valerates has been researched along with 3-methylglutaconic acid in 13 studies
| Studies (valerates) | Trials (valerates) | Recent Studies (post-2010) (valerates) | Studies (3-methylglutaconic acid) | Trials (3-methylglutaconic acid) | Recent Studies (post-2010) (3-methylglutaconic acid) |
|---|---|---|---|---|---|
| 2,251 | 294 | 457 | 136 | 1 | 25 |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 4 (30.77) | 18.7374 |
| 1990's | 1 (7.69) | 18.2507 |
| 2000's | 6 (46.15) | 29.6817 |
| 2010's | 2 (15.38) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Chalmers, RA; Halliday, D; Thompson, GN | 1 |
| Beemer, FA; Bruinvis, L; Duran, M; Ketting, D; Tibosch, AS; Wadman, SK | 1 |
| Ransnäs, L; Steen, G | 1 |
| Berry, HK; Denton, MD; Norman, EJ | 1 |
| Kuhara, T; Matsumoto, I; Matsuo, M; Shinka, T | 1 |
| Brandis, M; Ensenauer, R; Gibson, KM; Lehnert, W; Müller, CB; Schwab, KO | 1 |
| Das, AM; Gibson, KM; Illsinger, S; Lücke, T; Zschocke, J | 1 |
| de Koning, T; Engelke, U; Huizing, M; Kluijtmans, LA; Loupatty, FJ; Morava, E; Rodenburg, RJ; Smeitink, JA; Wevers, R; Wortmann, S | 1 |
| Engelke, UF; Kluijtmans, LA; Kremer, B; Loss, S; Loupatty, FJ; Morava, E; Moskau, D; van den Bergh, E; van der Graaf, M; Wanders, RJ; Wevers, RA | 1 |
| Amaral, AU; de Bortoli, G; Latini, A; Leipnitz, G; Schuck, PF; Seminotti, B; Solano, A; Wajner, M; Wannmacher, CM; Wyse, AT | 1 |
| Amaral, AU; Beskow, AP; da Silva, Lde B; Fernandes, CG; Leipnitz, G; Ribeiro, CA; Seminotti, B; Vargas, CR; Wajner, M; Zanatta, A | 1 |
| Hickmann, FH; Ribeiro, CA; Wajner, M | 1 |
| Antonetti, G; Boenzi, S; Carrozzo, R; Catesini, G; Diodato, D; Dionisi-Vici, C; Martinelli, D; Olivieri, G; Rizzo, C; Sacchetti, E; Semeraro, M | 1 |
13 other study(ies) available for valerates and 3-methylglutaconic acid
| Article | Year |
|---|---|
The contribution of protein catabolism to metabolic decompensation in 3-hydroxy-3-methylglutaric aciduria.
Topics: Amino Acid Metabolism, Inborn Errors; Child; Diseases in Twins; Female; Glutarates; Humans; Leucine; Male; Meglutol; Oxo-Acid-Lyases; Phenylalanine; Proteins; Valerates | 1990 |
Inherited 3-methylglutaconic aciduria in two brothers--another defect of leucine metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Glutarates; Humans; Hydro-Lyases; Leucine; Male; Meglutol; Speech Disorders; Valerates | 1982 |
Organic acids or urine in multiple sclerosis.
Topics: Aconitic Acid; Adipates; Carboxylic Acids; Fatty Acids, Monounsaturated; Fatty Acids, Unsaturated; Female; Glutarates; Humans; Lactates; Lactic Acid; Male; Multiple Sclerosis; Succinates; Succinic Acid; Terpenes; Valerates | 1983 |
Gas-chromatographic/mass spectrometric detection of 3-hydroxy-3-methylglutaryl-CoA lyase deficiency in double first cousins.
Topics: Amino Acid Metabolism, Inborn Errors; Female; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Hydroxy Acids; Infant; Leucine; Male; Meglutol; Oxo-Acid-Lyases; Valerates | 1982 |
Increased excretion of lactate, glutarate, 3-hydroxyisovalerate and 3-methylglutaconate during clinical episodes of propionic acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Carboxy-Lyases; Female; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Infant, Newborn; Lactates; Lactic Acid; Methylmalonyl-CoA Decarboxylase; Propionates; Valerates | 1982 |
3-Methylglutaconyl-CoA hydratase deficiency: a new patient with speech retardation as the leading sign.
Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Diet, Protein-Restricted; Fibroblasts; Glutarates; Humans; Hydro-Lyases; Meglutol; Speech Disorders; Valerates | 2000 |
3-methylglutaconic aciduria type I in a boy with fever-associated seizures.
Topics: Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Diagnosis, Differential; DNA Mutational Analysis; Enoyl-CoA Hydratase; Fibroblasts; Follow-Up Studies; Glutarates; Heterozygote; Homozygote; Humans; Hydro-Lyases; Introns; Male; Phenotype; Recurrence; RNA Splice Sites; RNA-Binding Proteins; Seizures, Febrile; Valerates | 2004 |
Association of 3-methylglutaconic aciduria with sensori-neural deafness, encephalopathy, and Leigh-like syndrome (MEGDEL association) in four patients with a disorder of the oxidative phosphorylation.
Topics: Adolescent; Brain Diseases, Metabolic; Child; Child, Preschool; Consanguinity; Fatal Outcome; Female; Glutarates; Hearing Loss, Sensorineural; Humans; Infant, Newborn; Leigh Disease; Male; Mitochondrial Diseases; Oxidative Phosphorylation; Syndrome; Valerates | 2006 |
NMR spectroscopic studies on the late onset form of 3-methylglutaconic aciduria type I and other defects in leucine metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Brain; Female; Glutarates; Humans; Leucine; Magnetic Resonance Spectroscopy; Meglutol; Middle Aged; Valerates | 2006 |
Induction of oxidative stress by the metabolites accumulating in 3-methylglutaconic aciduria in cerebral cortex of young rats.
Topics: Animals; Antioxidants; Cerebral Cortex; Glutarates; Glutathione; Lipid Peroxidation; Meglutol; Mitochondria; Molecular Structure; Oxidants; Oxidative Stress; Protein Carbonylation; Rats; Rats, Wistar; Superoxides; Thiobarbituric Acid Reactive Substances; Valerates | 2008 |
Striatum is more vulnerable to oxidative damage induced by the metabolites accumulating in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency as compared to liver.
Topics: Animals; Corpus Striatum; Glutarates; Glutathione; Glycine; Humans; Liver; Male; Meglutol; Oxidative Stress; Oxo-Acid-Lyases; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances; Valerates | 2009 |
Neurochemical evidence that 3-methylglutaric acid inhibits synaptic Na+,K+-ATPase activity probably through oxidative damage in brain cortex of young rats.
Topics: Animals; Cerebral Cortex; Glutarates; Humans; Male; Meglutol; Mitochondria; Oxidation-Reduction; Oxidative Stress; Rats; Rats, Wistar; Sodium-Potassium-Exchanging ATPase; Synaptic Membranes; Valerates | 2011 |
The urinary organic acids profile in single large-scale mitochondrial DNA deletion disorders.
Topics: 3-Hydroxybutyric Acid; Acyl-CoA Dehydrogenase, Long-Chain; Adolescent; Child; Child, Preschool; Congenital Bone Marrow Failure Syndromes; DNA, Mitochondrial; Fumarates; Glutarates; Humans; Hydroxybutyrates; Infant; Kearns-Sayre Syndrome; Lactic Acid; Lipid Metabolism, Inborn Errors; Mitochondrial Diseases; Muscular Diseases; Pyruvic Acid; Retrospective Studies; Valerates | 2018 |