urea and carglumic acid

urea has been researched along with carglumic acid in 8 studies

Research

Studies (8)

TimeframeStudies, this research(%)All Research%
pre-19902 (25.00)18.7374
1990's0 (0.00)18.2507
2000's3 (37.50)29.6817
2010's2 (25.00)24.3611
2020's1 (12.50)2.80

Authors

AuthorsStudies
Costell, M; Grisolía, S; O'Connor, JE1
Grisolía, S; Jordá, A; O'Connor, JE1
Caldovic, L; Daikhin, Y; McCarter, RJ; Morizono, H; Nissim, I; Tuchman, M; Yudkoff, M1
Burton, B; Caldovic, L; Daikhin, Y; Horyn, O; Korson, M; Nissim, I; Tuchman, M; Yudkoff, M1
Ah Mew, N; Daikhin, Y; Nissim, I; Payan, I; Tuchman, M; Yudkoff, M1
Ah Mew, N; Daikhin, Y; McCarter, R; Nissim, I; Tuchman, M; Yudkoff, M1
Ah Mew, N; Daikhin, Y; Lichter-Konecki, U; McCarter, R; Nissim, I; Tuchman, M; Yudkoff, M1
Caldovic, L; Haskins, N; McNutt, M; Morizono, H; Senkevitch, E; Sonaimuthu, P; Tuchman, M; Uapinyoying, P1

Trials

4 trial(s) available for urea and carglumic acid

ArticleYear
N-carbamylglutamate markedly enhances ureagenesis in N-acetylglutamate deficiency and propionic acidemia as measured by isotopic incorporation and blood biomarkers.
    Pediatric research, 2008, Volume: 64, Issue:2

    Topics: Acetyl Coenzyme A; Adult; Amino Acids; Ammonia; Biomarkers; Carbon Dioxide; Carbon Isotopes; Child; Feasibility Studies; Female; Glutamates; Humans; Male; Metabolic Diseases; Middle Aged; Propionates; Urea

2008
Effects of a single dose of N-carbamylglutamate on the rate of ureagenesis.
    Molecular genetics and metabolism, 2009, Volume: 98, Issue:4

    Topics: Adult; Amino Acids; Blood Glucose; Carbon Dioxide; Carbon Isotopes; Demography; Dose-Response Relationship, Drug; Exhalation; Female; Glutamates; Health; Humans; Infusions, Intravenous; Male; Sodium Bicarbonate; Urea; Young Adult

2009
N-carbamylglutamate augments ureagenesis and reduces ammonia and glutamine in propionic acidemia.
    Pediatrics, 2010, Volume: 126, Issue:1

    Topics: Administration, Oral; Adolescent; Ammonia; Blood Chemical Analysis; Child; Child, Preschool; Confidence Intervals; Dose-Response Relationship, Drug; Drug Administration Schedule; Female; Follow-Up Studies; Glutamates; Glutamine; Humans; Infant; Male; Probability; Propionic Acidemia; Prospective Studies; Risk Assessment; Treatment Outcome; Urea

2010
Augmenting ureagenesis in patients with partial carbamyl phosphate synthetase 1 deficiency with N-carbamyl-L-glutamate.
    The Journal of pediatrics, 2014, Volume: 165, Issue:2

    Topics: Adolescent; Adult; Ammonia; Carbamoyl-Phosphate Synthase I Deficiency Disease; Child; Child, Preschool; Female; Glutamates; Glutamine; Humans; Linear Models; Male; Mass Spectrometry; Treatment Outcome; Urea; Young Adult

2014

Other Studies

4 other study(ies) available for urea and carglumic acid

ArticleYear
Carbamyl glutamate prevents the potentiation of ammonia toxicity by sodium benzoate.
    European journal of pediatrics, 1989, Volume: 148, Issue:6

    Topics: Ammonia; Animals; Benzoates; Benzoic Acid; Drug Synergism; Glutamates; Mice; Urea

1989
Acute and chronic effects of carbamyl glutamate on blood urea and ammonia.
    European journal of pediatrics, 1985, Volume: 143, Issue:3

    Topics: Ammonia; Animals; Glutamates; Male; Mice; Rats; Rats, Inbred Strains; Time Factors; Urea

1985
Restoration of ureagenesis in N-acetylglutamate synthase deficiency by N-carbamylglutamate.
    The Journal of pediatrics, 2004, Volume: 145, Issue:4

    Topics: Acetyltransferases; Adolescent; Adult; Amino-Acid N-Acetyltransferase; Ammonia; Ammonium Chloride; Blood Urea Nitrogen; Female; Glutamates; Glutamine; Humans; Nitrogen Isotopes; Urea

2004
Gene delivery corrects N-acetylglutamate synthase deficiency and enables insights in the physiological impact of L-arginine activation of N-acetylglutamate synthase.
    Scientific reports, 2021, 02-11, Volume: 11, Issue:1

    Topics: Amino-Acid N-Acetyltransferase; Animals; Arginine; Citrulline; Dependovirus; Disease Models, Animal; Gene Transfer Techniques; Glutamates; Humans; Hyperammonemia; Mice; Mice, Knockout; Mutant Proteins; Urea; Urea Cycle Disorders, Inborn

2021