tiglylglycine has been researched along with propionic-acid* in 1 studies
1 other study(ies) available for tiglylglycine and propionic-acid
Article | Year |
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Late onset type of propionic acidaemia: case report and biochemical studies.
A late-onset case of propionic acidaemia with favourable response to restriction of dietary protein is described. During a keto-acidotic crisis, this patient demonstrated unexpectedly low concentrations of propionic acid and glycine in blood and urine but increased urinary output of some secondary metabolites. Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Carbon-Carbon Ligases; Female; Glycine; Humans; Hydroxybutyrates; Infant; Ketosis; Ligases; Propionates | 1981 |