Page last updated: 2024-08-16

succinylacetone and phenylalanine

succinylacetone has been researched along with phenylalanine in 8 studies

Research

Studies (8)

TimeframeStudies, this research(%)All Research%
pre-19901 (12.50)18.7374
1990's3 (37.50)18.2507
2000's1 (12.50)29.6817
2010's3 (37.50)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Hjalmarson, O; Holme, E; Lindstedt, S; Lock, EA; Strandvik, B1
Bain, MD; Bingham, P; Chalmers, RA; Jones, M; Purkiss, P; Stacey, TE1
Fällström, SP; Lindblad, B; Steen, G1
Fernández-Cañón, JM; Peñalva, MA1
Anders, MW; Blackburn, AC; Board, PG; Dahlstrom, JE; Davis, RP; Koina, ME; Lim, CE; Matthaei, KI1
Jitraruch, S; Leelaudomlipi, S; Sornmayura, P; Sriphojanart, S; Teeraratkul, S; Treepongkaruna, S; Viengteerawat, S; Wattanasirichaigoon, D1
Boenzi, S; Della Bona, ML; Dionisi-Vici, C; la Marca, G; Malvagia, S; Martinelli, D; Materazzi, S1
Burgerhof, JGM; Daly, A; de Blaauw, P; Heiner-Fokkema, MR; Kienstra, NS; MacDonald, A; Rodenburg, IL; Santra, S; van de Krogt, J; van Ginkel, WG; van Reemst, HE; van Spronsen, FJ1

Other Studies

8 other study(ies) available for succinylacetone and phenylalanine

ArticleYear
Treatment of hereditary tyrosinaemia type I by inhibition of 4-hydroxyphenylpyruvate dioxygenase.
    Lancet (London, England), 1992, Oct-03, Volume: 340, Issue:8823

    Topics: 4-Hydroxyphenylpyruvate Dioxygenase; Acetoacetates; alpha-Fetoproteins; Amino Acid Metabolism, Inborn Errors; Aminolevulinic Acid; Child; Child, Preschool; Cyclohexanones; Erythrocytes; Heptanoates; Humans; Hydroxybenzoates; Infant; Kidney Tubules; Liver; Nitrobenzoates; Phenylalanine; Phosphates; Porphobilinogen Synthase; Proteinuria; Tyrosine

1992
Dietary treatment eliminates succinylacetone from the urine of a patient with tyrosinaemia type 1.
    European journal of pediatrics, 1990, Volume: 149, Issue:9

    Topics: Amino Acid Metabolism, Inborn Errors; Female; Heme; Heptanoates; Heptanoic Acids; Humans; Infant; Methionine; Phenylalanine; Tyrosine

1990
On the renal tubular damage in hereditary tyrosinemia and on the formation of succinylacetoacetate and succinylacetone.
    Acta paediatrica Scandinavica, 1981, Volume: 70, Issue:3

    Topics: Acetoacetates; Amino Acid Metabolism, Inborn Errors; Aminolevulinic Acid; Child; Heptanoates; Homogentisic Acid; Humans; Infant; Keto Acids; Kidney Diseases; Kidney Tubules; Male; Phenylalanine; Proteinuria; Tyrosine

1981
Fungal metabolic model for human type I hereditary tyrosinaemia.
    Proceedings of the National Academy of Sciences of the United States of America, 1995, Sep-26, Volume: 92, Issue:20

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acid Sequence; Aspergillus nidulans; Chromatography, High Pressure Liquid; Dioxygenases; Enzyme Inhibitors; Gas Chromatography-Mass Spectrometry; Genes, Fungal; Heptanoates; Homogentisate 1,2-Dioxygenase; Humans; Hydrolases; Models, Genetic; Molecular Sequence Data; Mutation; Open Reading Frames; Oxygenases; Phenylalanine; Restriction Mapping; Sequence Homology, Amino Acid; Tyrosine

1995
Mice deficient in glutathione transferase zeta/maleylacetoacetate isomerase exhibit a range of pathological changes and elevated expression of alpha, mu, and pi class glutathione transferases.
    The American journal of pathology, 2004, Volume: 165, Issue:2

    Topics: Acetone; Animals; cis-trans-Isomerases; Diet; Female; Glutathione S-Transferase pi; Glutathione Transferase; Hepatitis; Heptanoates; Isoenzymes; Kidney; Leukocytes; Liver; Male; Maleates; Mice; Mice, Inbred BALB C; Mice, Inbred C57BL; Mice, Knockout; Models, Animal; NAD(P)H Dehydrogenase (Quinone); Phenylalanine; Spleen; Up-Regulation

2004
Long-term outcome of living donor liver transplantation in a Thai boy with hereditary tyrosinemia type I: a case report.
    Journal of the Medical Association of Thailand = Chotmaihet thangphaet, 2011, Volume: 94, Issue:10

    Topics: Asian People; Diet Therapy; Heptanoates; Humans; Hydrolases; Infant; Liver Failure; Liver Transplantation; Living Donors; Male; Mutation; Phenylalanine; Thailand; Treatment Outcome; Tyrosine; Tyrosinemias

2011
LC-MS/MS method for simultaneous determination on a dried blood spot of multiple analytes relevant for treatment monitoring in patients with tyrosinemia type I.
    Analytical chemistry, 2012, Jan-17, Volume: 84, Issue:2

    Topics: 4-Hydroxyphenylpyruvate Dioxygenase; Adolescent; Biomarkers; Child; Child, Preschool; Chromatography, Liquid; Cyclohexanones; Diet, Protein-Restricted; Drug Monitoring; Enzyme Inhibitors; Heptanoates; Humans; Infant; Infant, Newborn; Kidney; Liver; Methionine; Nitrobenzoates; Phenylalanine; Tandem Mass Spectrometry; Tyrosine; Tyrosinemias

2012
The Effect of Various Doses of Phenylalanine Supplementation on Blood Phenylalanine and Tyrosine Concentrations in Tyrosinemia Type 1 Patients.
    Nutrients, 2019, Nov-18, Volume: 11, Issue:11

    Topics: Adolescent; Adult; Child; Cyclohexanones; Dietary Supplements; Enzyme Inhibitors; Female; Heptanoates; Humans; Linear Models; Male; Nitrobenzoates; Phenylalanine; Tyrosine; Tyrosinemias; Young Adult

2019