succinic semialdehyde and sodium oxybate

succinic semialdehyde has been researched along with sodium oxybate in 17 studies

Research

Studies (17)

TimeframeStudies, this research(%)All Research%
pre-199010 (58.82)18.7374
1990's2 (11.76)18.2507
2000's3 (17.65)29.6817
2010's2 (11.76)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Kaufman, EE; Nelson, T2
Hechler, V; Maitre, M; Mandel, P; Vayer, P1
Kaufman, EE; Miller, D; Nelson, T; Stadlan, N1
Gibson, KM; Nyhan, WL; Pattarelli, PP1
Fales, HM; Kaufman, EE; Levin, DM; Nelson, T1
Brown, GK; Danks, DM; Gibson, KM; Haan, EA; Jansen, I; Nyhan, WL; Sweetman, L1
Divry, P; Hanefeld, F; Hermier, M; Jakobs, C; Kneer, J; Rating, D; Siemes, H1
Divry, P; Hanefeld, F; Hermier, M; Jakobs, C; Kneer, J; Rating, D1
Bojasch, M; Hanefeld, F; Jakobs, C; Mönch, E; Rating, D; Siemes, H1
Rivett, AJ; Smith, IL; Tipton, KF1
Cho, SW; Choi, EY; Choi, SY; Hong, JW; Jang, SH; Lee, JE; Park, KA; Suk, JW; Yoo, BK1
Crouch, DH; Hayes, JD; Kelly, VP; Sherratt, PJ1
Gibson, KM; Hoffmann, GF; Jakobs, C; Kölker, S; Okun, JG; Sauer, SW; Ten Brink, HJ1
Kakazu, Y; Kochi, H; Matsuo, G; Robert, M; Saito, N; Soga, T; Tomita, M1
Adam-Vizi, V; Chinopoulos, C; Fodor, V; Horvath, K; Kacso, G; Ravasz, D1
Capo, C; Ciminelli, BM; Donati, MA; Falconi, M; Funghini, S; Iacovelli, F; Leo, S; Malaspina, P; Menduti, G; Rossi, L1

Reviews

2 review(s) available for succinic semialdehyde and sodium oxybate

ArticleYear
An overview of gamma-hydroxybutyrate catabolism: the role of the cytosolic NADP(+)-dependent oxidoreductase EC 1.1.1.19 and of a mitochondrial hydroxyacid-oxoacid transhydrogenase in the initial, rate-limiting step in this pathway.
    Neurochemical research, 1991, Volume: 16, Issue:9

    Topics: Alcohol Oxidoreductases; Animals; Carbohydrate Dehydrogenases; Carbon; Catalysis; Cytosol; gamma-Aminobutyric Acid; Hydroxybutyrate Dehydrogenase; Ketoglutaric Acids; Kinetics; Mitochondria; Mitochondrial Proteins; Oxidation-Reduction; Sodium Oxybate

1991
Function of gamma-hydroxybutyrate: a putative neurotransmitter.
    Biochemical Society transactions, 1987, Volume: 15, Issue:2

    Topics: Animals; Binding Sites; Brain; gamma-Aminobutyric Acid; Humans; Hydroxybutyrates; Neurotransmitter Agents; Sodium Oxybate

1987

Other Studies

15 other study(ies) available for succinic semialdehyde and sodium oxybate

ArticleYear
Evidence for the participation of a cytosolic NADP+-dependent oxidoreductase in the catabolism of gamma-hydroxybutyrate in vivo.
    Journal of neurochemistry, 1987, Volume: 48, Issue:6

    Topics: Animals; Brain; GABA Antagonists; gamma-Aminobutyric Acid; Glucuronates; Hydroxybutyrate Dehydrogenase; Hydroxybutyrates; Keto Acids; Kidney; Male; Muscles; Phenylacetates; Rats; Rats, Inbred Strains; Sodium Oxybate; Sodium Salicylate; Valproic Acid

1987
Oxidation of gamma-hydroxybutyrate to succinic semialdehyde by a mitochondrial pyridine nucleotide-independent enzyme.
    Journal of neurochemistry, 1988, Volume: 51, Issue:4

    Topics: Animals; Brain; Carbon Dioxide; Cytosol; gamma-Aminobutyric Acid; Hydroxybutyrate Dehydrogenase; Hydroxybutyrates; Immunoassay; Kidney; Male; Mitochondria; NAD; NADP; Oxidation-Reduction; Rats; Rats, Inbred Strains; Sodium Oxybate; Valproic Acid

1988
Oxidation of [U-14C]succinic semialdehyde in cultured human lymphoblasts: measurement of residual succinic semialdehyde dehydrogenase activity in 11 patients with 4-hydroxybutyric aciduria.
    Pediatric research, 1988, Volume: 24, Issue:4

    Topics: Aldehyde Oxidoreductases; Carbon Dioxide; Cells, Cultured; Child; Child, Preschool; Female; gamma-Aminobutyric Acid; Humans; Hydroxybutyrates; Infant; Kinetics; Lactates; Lactic Acid; Lymphocytes; Male; Malonates; Oxidation-Reduction; Sodium Oxybate; Succinate-Semialdehyde Dehydrogenase; Succinates; Succinic Acid; Valproic Acid

1988
Isolation and characterization of a hydroxyacid-oxoacid transhydrogenase from rat kidney mitochondria.
    The Journal of biological chemistry, 1988, Nov-15, Volume: 263, Issue:32

    Topics: 3-Hydroxybutyric Acid; Animals; Chromatography, Paper; gamma-Aminobutyric Acid; Gas Chromatography-Mass Spectrometry; Glutarates; Hydrogen-Ion Concentration; Hydroxybutyrates; Kidney; Kinetics; Mitochondria; NAD; NADP; Rats; Sodium Oxybate; Time Factors

1988
Properties of succinic semialdehyde dehydrogenase in cultured human lymphoblasts.
    Journal of neurogenetics, 1985, Volume: 2, Issue:2

    Topics: Cell-Free System; gamma-Aminobutyric Acid; Humans; Hydrogen-Ion Concentration; Hydroxybutyrate Dehydrogenase; Hydroxybutyrates; Lymphocytes; NAD; Sodium Oxybate; Temperature

1985
4-Hydroxybutyric aciduria: a new inborn error of metabolism. I. Clinical review.
    Journal of inherited metabolic disease, 1984, Volume: 7 Suppl 1

    Topics: Adolescent; Ataxia; Child; Female; gamma-Aminobutyric Acid; Humans; Hydroxybutyrate Dehydrogenase; Hydroxybutyrates; Male; Metabolism, Inborn Errors; Sodium Oxybate

1984
4-Hydroxybutyric aciduria: a new inborn error of metabolism. II. Biochemical findings.
    Journal of inherited metabolic disease, 1984, Volume: 7 Suppl 1

    Topics: Adolescent; Child; Female; gamma-Aminobutyric Acid; Humans; Hydroxybutyrates; Male; Metabolism, Inborn Errors; Sodium Oxybate

1984
Urinary excretion of gamma-hydroxybutyric acid in a patient with neurological abnormalities. The probability of a new inborn error of metabolism.
    Clinica chimica acta; international journal of clinical chemistry, 1981, Apr-09, Volume: 111, Issue:2-3

    Topics: Fatty Acids, Nonesterified; gamma-Aminobutyric Acid; Gas Chromatography-Mass Spectrometry; Humans; Hydroxybutyrate Dehydrogenase; Hydroxybutyrates; Infant; Male; Nervous System Diseases; Sodium Oxybate

1981
The enzymes catalysing succinic semialdehyde reduction in rat brain.
    Biochemical pharmacology, 1981, Apr-01, Volume: 30, Issue:7

    Topics: Animals; Barbital; Brain; gamma-Aminobutyric Acid; Hydroxybutyrate Dehydrogenase; Hydroxybutyrates; In Vitro Techniques; Kinetics; NAD; NADP; Rats; Sodium Oxybate

1981
Distribution of succinic semialdehyde reductase in rat brain.
    Molecules and cells, 1997, Feb-28, Volume: 7, Issue:1

    Topics: Animals; Antibodies, Monoclonal; Brain; Cattle; gamma-Aminobutyric Acid; Hydroxybutyrate Dehydrogenase; Immunoenzyme Techniques; Limbic System; Microscopy, Immunoelectron; Rats; Reticular Formation; Sodium Oxybate; Tissue Distribution

1997
Novel homodimeric and heterodimeric rat gamma-hydroxybutyrate synthases that associate with the Golgi apparatus define a distinct subclass of aldo-keto reductase 7 family proteins.
    The Biochemical journal, 2002, Sep-15, Volume: 366, Issue:Pt 3

    Topics: Alcohol Oxidoreductases; Aldehyde Reductase; Aldo-Keto Reductases; Amino Acid Sequence; Animals; Base Sequence; Blotting, Western; Catalysis; Cells, Cultured; Chromatography, Ion Exchange; Cloning, Molecular; Cytosol; Dimerization; DNA, Complementary; Female; gamma-Aminobutyric Acid; Golgi Apparatus; Humans; Immunoblotting; Immunohistochemistry; Kinetics; Liver; Male; Mice; Microscopy, Fluorescence; Molecular Sequence Data; Protein Binding; Protein Structure, Tertiary; Rats; Rats, Inbred F344; Rats, Sprague-Dawley; Sequence Homology, Amino Acid; Sodium Oxybate; Subcellular Fractions; Substrate Specificity

2002
Enzymatic and metabolic evidence for a region specific mitochondrial dysfunction in brains of murine succinic semialdehyde dehydrogenase deficiency (Aldh5a1-/- mice).
    Neurochemistry international, 2007, Volume: 50, Issue:4

    Topics: Animals; Brain; Brain Diseases, Metabolic, Inborn; Citric Acid Cycle; Disease Models, Animal; Electron Transport; Energy Metabolism; gamma-Aminobutyric Acid; Glutathione; Mice; Mice, Knockout; Mitochondria; Mitochondrial Diseases; Oxidative Stress; Sodium Oxybate; Subcellular Fractions; Succinate-Semialdehyde Dehydrogenase

2007
Metabolite profiling reveals YihU as a novel hydroxybutyrate dehydrogenase for alternative succinic semialdehyde metabolism in Escherichia coli.
    The Journal of biological chemistry, 2009, Jun-12, Volume: 284, Issue:24

    Topics: Alcohol Oxidoreductases; Amino Acid Sequence; Arabidopsis; Enzyme Activation; Escherichia coli K12; Escherichia coli Proteins; gamma-Aminobutyric Acid; Hydroxybutyrate Dehydrogenase; Metabolome; Molecular Sequence Data; Sequence Homology, Amino Acid; Sodium Oxybate; Stress, Physiological; Succinate-Semialdehyde Dehydrogenase

2009
Catabolism of GABA, succinic semialdehyde or gamma-hydroxybutyrate through the GABA shunt impair mitochondrial substrate-level phosphorylation.
    Neurochemistry international, 2017, Volume: 109

    Topics: Adjuvants, Anesthesia; Animals; Female; gamma-Aminobutyric Acid; Male; Metabolism; Mice; Mice, Inbred C57BL; Mitochondria; Phosphorylation; Sodium Oxybate; Substrate Specificity

2017
SSADH deficiency in an Italian family: a novel ALDH5A1 gene mutation affecting the succinic semialdehyde substrate binding site.
    Metabolic brain disease, 2017, Volume: 32, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Binding Sites; Computer Simulation; Developmental Disabilities; DNA; Female; gamma-Aminobutyric Acid; HEK293 Cells; Heterozygote; Humans; Infant; Models, Molecular; Mutation; Mutation, Missense; Pedigree; Sodium Oxybate; Succinate-Semialdehyde Dehydrogenase

2017