pyridoxine and cystathionine

pyridoxine has been researched along with cystathionine in 54 studies

Research

Studies (54)

TimeframeStudies, this research(%)All Research%
pre-199039 (72.22)18.7374
1990's10 (18.52)18.2507
2000's1 (1.85)29.6817
2010's3 (5.56)24.3611
2020's1 (1.85)2.80

Authors

AuthorsStudies
Plöchl, E2
Dow, MJ; Kokkeler, SC; Miller, LT1
Bremer, HJ; Endres, W; Riegel, KP; Vogt, R1
Láhoda, F1
Anand, CR; Brown, RR; Leklem, JE; Linkswiler, HM; Rose, DP1
Ota, K1
Conerly, EB; Edwards, WA; Mudd, SH; Poole, JR1
Brown, RR; Leklem, JE; Linkswiler, HM; Rose, DP2
Beratis, NG; Gaull, GE; Gillam, BM; Hirschhorn, K; Pascal, TA; Tallan, HH1
Frimpter, GW; Horwith, M; Kozlowski, KK1
Morino, Y; Tanase, S1
Borud, O; Gjessing, L; Hestnes, A; Lunde, H1
Borud, O; Gjessing, LR; Hestnes, A; Lunde, H1
Zakim, D1
Krishnaswamy, K2
Linkswiler, HM; Shin, HK1
Fleisher, LD; Gaull, GE1
Bremer, HJ; Endres, W1
Coignet, J; Laurent, B1
Bittles, AH; Carson, NA1
Cohen, PA; Gaull, GE; Ginsberg-Fellner, F; Knittle, J; Schneidman, K; Sturman, JA1
Frimpter, GW1
Yoshida, T1
AvRuskin, TW; Kang, ES1
Gaull, G; Schaffner, F; Sturman, JA1
Hirayama, K; Ikegami, T; Kodama, H; Mizuhara, S1
Brown, FC; DeFoor, M1
Brill, PW; Gaull, GE; Mitty, HA1
Kanfer, JN; Kurtz, DJ; Levy, H1
Appleyard, JG; Stanley, DA1
Gaull, GE1
Kashiwamata, S1
Arafa, AM; Hussein, L1
Beratis, NG; Gaull, GE; Guarini, L; Pascal, TA1
Endres, W1
Allen, RH; Joosten, E; Lindenbaum, J; Naurath, HJ; Riezler, R; Stabler, SP1
Glueck, CJ; Lang, JE; Shaw, P; Sieve-Smith, L; Tracy, T; Wang, Y1
Alonso Fernández, JR; Alonso Martín, A; Bravo Mata, M; Escribano Rey, MD1
Allen, RH; Delport, R; Riezler, R; Stabler, SP; Ubbink, JB; van der Merwe, A; Vermaak, WJ1
Asagi, K; Awata, S; Kobayashi, M; Kodama, H; Nakayama, K; Nakayama, M1
Cardesa García, JJ; Remón Alvarez-Arenas, J; Ruiz García, V; Sánchez Alarcón, J; Val Sánchez de León, JM; Vaquerizo Madrid, J1
Cole, DE; Donovan, SM; Howell, DS; Mahuren, JD; Massé, PG; Yamauchi, M; Ziv, I1
Hamano, H; Takizawa, S1
Bai, SC; Morris, JG; Rogers, QR; Sampson, DA; Wong, DL1
Bodis, M; Geisel, J; Herrmann, W; Knapp, JP; Müller, A; Schorr, H; Stein, G1
HOPE, DB2
Aliani, M; House, JD; Mayengbam, S; Raposo, S2
Chi, YY; Coats, B; Gregory, JF; Midttun, Ø; Ralat, M; Rios-Avila, L; Stacpoole, PW; Ueland, PM1
Aghalarov, M; Aktuglu-Zeybek, C; Cansever, MS; Kıykım, E; Uygur, E; Zubarioglu, T1

Reviews

5 review(s) available for pyridoxine and cystathionine

ArticleYear
[Vitamin dependency].
    Horumon to rinsho. Clinical endocrinology, 1975, Volume: 23, Issue:9

    Topics: Anemia, Sideroblastic; Animals; Biotin; Crotonates; Cystathionine; gamma-Aminobutyric Acid; Glutamate Decarboxylase; Glycine; Humans; Infant; Infant, Newborn; Maple Syrup Urine Disease; Methylmalonic Acid; Mice; Pyridoxine; Vitamin B 6 Deficiency; Vitamin D Deficiency; Xanthurenates

1975
Biochemical foundations of preventive medicine: the study of abnormal enzymes.
    Horizons in biochemistry and biophysics, 1974, Volume: 1

    Topics: Amino Acid Metabolism, Inborn Errors; Cystathionine; Cystathionine gamma-Lyase; Erythrocytes; Genes, Recessive; Genetic Variation; Glucosephosphate Dehydrogenase Deficiency; Glucuronosyltransferase; Glycogen Storage Disease Type I; Humans; Isoenzymes; Kinetics; Metabolism, Inborn Errors; Methylmalonic Acid; Orotic Acid; Purine-Pyrimidine Metabolism, Inborn Errors; Pyridoxine

1974
Methionine metabolism in man: development and deficiencies.
    Clinics in endocrinology and metabolism, 1974, Volume: 3, Issue:1

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Cystathionine; Female; Fetus; Heterozygote; Homocystinuria; Homozygote; Humans; Liver; Lyases; Male; Methionine; Methyltransferases; Microscopy, Electron; Mitochondria, Liver; Oxidoreductases; Phenotype; Pregnancy; Pyridoxine; Sulfites; Tetrahydrofolates

1974
[Congenital cystathioninuria. B6-dependent].
    Anales espanoles de pediatria, 1993, Volume: 39, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Cystathionine; Female; Humans; Pyridoxine; Remission Induction

1993
[Methylenetetrahydrofolate reductase deficiency].
    Ryoikibetsu shokogun shirizu, 1998, Issue:19 Pt 2

    Topics: Biomarkers; Child, Preschool; Cystathionine; Folic Acid; Genes, Recessive; Humans; Infant; Infant, Newborn; Methionine; Methylenetetrahydrofolate Reductase (NADPH2); Mutation; Oxidoreductases Acting on CH-NH Group Donors; Pyridoxine; Vitamin B 12

1998

Trials

2 trial(s) available for pyridoxine and cystathionine

ArticleYear
Vitamin B6 requirements of women using oral contraceptives.
    The American journal of clinical nutrition, 1975, Volume: 28, Issue:5

    Topics: Adult; Alanine Transaminase; Aspartate Aminotransferases; Contraceptives, Oral; Contraceptives, Oral, Hormonal; Cystathionine; Female; Humans; Methionine; Nutritional Requirements; Pyridoxal Phosphate; Pyridoxic Acid; Pyridoxine; Tryptophan; Vitamin B 6 Deficiency

1975
Effects of vitamin B12, folate, and vitamin B6 supplements in elderly people with normal serum vitamin concentrations.
    Lancet (London, England), 1995, Jul-08, Volume: 346, Issue:8967

    Topics: Aged; Aged, 80 and over; Avitaminosis; Citrates; Cystathionine; Double-Blind Method; Female; Folic Acid; Follow-Up Studies; Homocysteine; Humans; Injections, Intramuscular; Male; Methylmalonic Acid; Placebos; Prospective Studies; Pyridoxine; Vitamin B 12; Vitamin B 12 Deficiency

1995

Other Studies

47 other study(ies) available for pyridoxine and cystathionine

ArticleYear
[Genetic and biochemical studies on familial neuroblastoma].
    Fortschritte der Medizin, 1979, Sep-13, Volume: 97, Issue:34

    Topics: Adrenal Gland Neoplasms; Coenzymes; Cystathionine; Cystathionine gamma-Lyase; Humans; Infant, Newborn; Mutation; Nervous System Neoplasms; Neuroblastoma; Oxamic Acid; Pyridoxine; Sympathetic Nervous System

1979
Methionine metabolism and vitamin B6 status in women using oral contraceptives.
    The American journal of clinical nutrition, 1978, Volume: 31, Issue:4

    Topics: Adult; Alanine Transaminase; Aspartate Aminotransferases; Contraceptives, Oral; Contraceptives, Oral, Combined; Cystathionine; Female; Homocysteine; Humans; Methionine; Pyridoxine; Taurine

1978
[Biochemical studies on familial neuroblastoma].
    Padiatrie und Padologie, 1978, Volume: 13, Issue:2

    Topics: Adult; Child; Cystathionine; Female; Humans; Male; Mutation; Neuroblastoma; Oxalates; Pedigree; Pyridoxine; Vitamin B Deficiency

1978
The influence of vitamin B-6 on cystathioninuria in premature infants.
    Clinica chimica acta; international journal of clinical chemistry, 1978, May-16, Volume: 86, Issue:1

    Topics: Birth Weight; Cystathionine; Female; Gestational Age; Humans; Infant, Newborn; Infant, Premature; Male; Methionine; Proteins; Pyridoxine; Time Factors

1978
[Disorders of methionine metabolism in polyneuropathies].
    MMW, Munchener medizinische Wochenschrift, 1976, Dec-17, Volume: 118, Issue:51

    Topics: Adult; Alcoholism; Cystathionine; Diabetic Neuropathies; Female; Humans; Male; Metabolic Diseases; Methionine; Middle Aged; Neurologic Manifestations; Pyridoxine; Vitamin B 6 Deficiency

1976
Metabolism of methionine in oral contraceptive users and control women receiving controlled intakes of vitamin B6.
    The American journal of clinical nutrition, 1977, Volume: 30, Issue:7

    Topics: Adult; Contraceptives, Oral; Contraceptives, Oral, Combined; Contraceptives, Oral, Hormonal; Cystathionine; Dose-Response Relationship, Drug; Female; Humans; Methionine; Pyridoxine; Sulfinic Acids; Taurine; Vitamin B 6 Deficiency

1977
Homocystinuria due to cystathionine synthase deficiency. Studies of nitrogen balance and sulfur excretion.
    The Journal of clinical investigation, 1975, Volume: 55, Issue:5

    Topics: Adolescent; Adult; Amino Acids; Child; Cystathionine; Cystine; Diet; Female; Homocystinuria; Humans; Hydro-Lyases; Male; Methionine; Nitrogen; Pyridoxine; Sulfur

1975
Vitamin B6-responsive and -unresponsive cystathioninuria: two variant molecular forms.
    Science (New York, N.Y.), 1975, Dec-19, Volume: 190, Issue:4220

    Topics: Amino Acid Metabolism, Inborn Errors; Cell Line; Cross Reactions; Cystathionine; Cystathionine gamma-Lyase; Dose-Response Relationship, Drug; Enzyme Activation; Humans; Lyases; Mutation; Pyridoxal Phosphate; Pyridoxine

1975
Effects of oral contraceptives on tryptophan metabolism and vitamin B6 requirements in women.
    Acta vitaminologica et enzymologica, 1975, Volume: 29, Issue:1-6

    Topics: Adult; Contraceptives, Oral; Cystathionine; Female; Humans; Kynurenine; Methionine; Pyridoxal Phosphate; Pyridoxine; Sex Factors; Tryptophan; Vitamin B 6 Deficiency

1975
Distribution of sulfur in urine of patients with cystathioninuria before and during administration of pyridoxine.
    Metabolism: clinical and experimental, 1976, Volume: 25, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Cystathionine; Humans; Male; Pyridoxine; Sulfates; Sulfur

1976
[Vitamin B6 dependency syndrome].
    Nihon rinsho. Japanese journal of clinical medicine, 1992, Volume: 50, Issue:7

    Topics: Amino Acid Metabolism, Inborn Errors; Aspartate Aminotransferases; Cystathionine; Homocystinuria; Humans; Hyperoxaluria; Ornithine; Pyridoxal Phosphate; Pyridoxine

1992
Cystathioninuria in Down's syndrome.
    Journal of mental deficiency research, 1989, Volume: 33 ( Pt 3)

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Cystathionine; Down Syndrome; Female; Humans; Pyridoxine

1989
Cystathioninuria in a profoundly mentally retarded woman with spastic tetraplegia, deafness and abnormal liver function tests.
    Journal of mental deficiency research, 1987, Volume: 31 ( Pt 3)

    Topics: Cystathionine; Deafness; Female; Humans; Intellectual Disability; Liver Function Tests; Middle Aged; Pyridoxine; Quadriplegia

1987
Methionine metabolism in pyridoxine deficiency.
    Nutrition and metabolism, 1974, Volume: 17, Issue:1

    Topics: Adult; Aspartate Aminotransferases; Cystathionine; Cysteine; Erythrocytes; Humans; Lyases; Male; Methionine; Middle Aged; Nutritional Physiological Phenomena; Peripheral Nervous System Diseases; Pyridoxine; Reflex; Sulfinic Acids; Vitamin B 6 Deficiency

1974
Tryptophan and methionine metabolism of adult females as affected by vitamin B-6 deficiency.
    The Journal of nutrition, 1974, Volume: 104, Issue:10

    Topics: Adult; Body Weight; Cystathionine; Cysteine; Dietary Proteins; Female; Homocystine; Humans; Kynurenic Acid; Kynurenine; Methionine; Nutritional Physiological Phenomena; Pyridoxine; Sulfinic Acids; Taurine; Tryptophan; Vitamin B 6 Deficiency; Xanthurenates

1974
Primary cystathioninuria. Methionine load tests and response to pyridoxine.
    Helvetica paediatrica acta, 1972, Volume: 27, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Child; Cystathionine; Female; Humans; Methionine; Pyridoxine

1972
[Cystathionuria and defective enzyme regulation].
    Clinica chimica acta; international journal of clinical chemistry, 1973, Jan-24, Volume: 43, Issue:2

    Topics: Administration, Oral; Amino Acid Metabolism, Inborn Errors; Child; Chromatography, Ion Exchange; Chromatography, Paper; Cystathionine; Cysteine; Electrophoresis, Paper; Female; Homocysteine; Homocystine; Homoserine; Humans; Hydro-Lyases; Hydrocortisone; Liver; Lyases; Methionine; Pyridoxine; Sulfur

1973
Tissue culture techniques as an aid to prenatal diagnosis and genetic counselling in homocystinuria.
    Journal of medical genetics, 1973, Volume: 10, Issue:2

    Topics: Adult; Biopsy; Clinical Enzyme Tests; Culture Techniques; Cystathionine; Female; Fibroblasts; Genetic Counseling; Heterozygote; Homocystinuria; Humans; Infant, Newborn; Pregnancy; Prenatal Diagnosis; Pyridoxine; Tryptophanase

1973
High pyridoxine diet in the rat: possible implications for megavitamin therapy.
    The Journal of nutrition, 1973, Volume: 103, Issue:1

    Topics: Adipose Tissue; Animal Nutritional Physiological Phenomena; Animals; Body Weight; Cell Count; Cystathionine; Epididymis; Homocystinuria; Humans; Hydro-Lyases; L-Serine Dehydratase; Lipid Metabolism; Liver; Male; Protein Biosynthesis; Proteins; Pyridoxine; Rats; Structure-Activity Relationship; Sulfur Isotopes

1973
Recurrent urinary tract calculi possibly due to inherited cystathioninuria.
    Aerospace medicine, 1973, Volume: 44, Issue:11

    Topics: Adult; Aerospace Medicine; Chronic Disease; Cystathionine; Humans; Male; Metabolism, Inborn Errors; Pyridoxine; Urinary Calculi

1973
[Vitamin B 6 dependency].
    Nihon rinsho. Japanese journal of clinical medicine, 1973, Aug-10, Volume: 31, Issue:8

    Topics: Child; Cystathionine; Female; Homocystinuria; Humans; Infant; Male; Metabolism, Inborn Errors; Pyridoxine; Xanthurenates

1973
Cystathioninuria, mental retardation, and juvenile diabetes mellitus.
    American journal of diseases of children (1960), 1974, Volume: 127, Issue:2

    Topics: Adolescent; Child; Consanguinity; Cystathionine; Diabetes Mellitus; Diabetes Mellitus, Type 1; Homozygote; Humans; Intellectual Disability; Male; Methionine; Pyridoxine; Vitamin B 6 Deficiency

1974
Homocystinuria due to cystathionine synthase deficiency: enzymatic and ultrastructural studies.
    The Journal of pediatrics, 1974, Volume: 84, Issue:3

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Biopsy, Needle; Child; Child, Preschool; Cystathionine; Female; Heterozygote; Homocysteine; Homocystinuria; Humans; Hydro-Lyases; Liver; Male; Methionine; Mitochondria, Liver; Pyridoxine; Transferases; Transketolase

1974
Effect of pyridoxine treatment of a cystathioninuric patient on the urinary excretion of some unusual sulfur-containing amino acids.
    Clinica chimica acta; international journal of clinical chemistry, 1974, Feb-28, Volume: 51, Issue:1

    Topics: Acetamides; Amino Acid Metabolism, Inborn Errors; Amino Acids, Sulfur; Autoanalysis; Chromatography, Ion Exchange; Cystathionine; Cysteine; Electrophoresis, Paper; Female; Homocysteine; Homocystine; Humans; Pyridoxine; Time Factors

1974
Trans-sulfuration in rat brain--effects of 3,4-dihydroxyphenylalanine (L-dopa).
    Biochemical pharmacology, 1974, Mar-15, Volume: 23, Issue:6

    Topics: Animals; Brain; Cystathionine; Dihydroxyphenylalanine; Kidney; Liver; Male; Nitro Compounds; Pyridoxine; Rats; S-Adenosylmethionine; Sulfur

1974
Homocystinuria due to cystathionine synthase deficiency: clinical-roentgenologic correlations.
    The American journal of roentgenology, radium therapy, and nuclear medicine, 1974, Volume: 121, Issue:1

    Topics: Adult; Bone Diseases; Child; Child, Preschool; Cystathionine; Eye Manifestations; Female; Homocystinuria; Humans; Hydro-Lyases; Male; Pyridoxine; Radiography

1974
Cerebral lipids and amino acids in the vitamin B 6 -deficient suckling rat.
    The Journal of nutrition, 1972, Volume: 102, Issue:2

    Topics: Amino Acids; Animal Nutritional Physiological Phenomena; Animals; Animals, Newborn; Body Weight; Brain; Carbon Isotopes; Cerebrosides; Cystathionine; Female; Gangliosides; Lipid Metabolism; Organ Size; Phospholipids; Plasmalogens; Pregnancy; Pyridoxine; Rats; Sphingolipids; Sphingomyelins; Sulfoglycosphingolipids; Tyrosine; Tyrosine Decarboxylase; Vitamin B 6 Deficiency

1972
The evaluation of the vitamin B 6 status in children with convulsions.
    Medical laboratory technology, 1972, Volume: 29, Issue:2

    Topics: Child; Cystathionine; Humans; Infant; Pyridoxine; Saccharomyces; Seizures; Vitamin B 6 Deficiency

1972
Methionine load test in pyridoxine deficiency.
    International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition, 1972, Volume: 42, Issue:3

    Topics: Aspartate Aminotransferases; Cystathionine; Cysteine; Erythrocytes; Female; Humans; Hydro-Lyases; Methionine; Mouth Diseases; Pregnancy; Pregnancy Complications; Pyridoxine; Sulfinic Acids; Taurine; Vitamin B 6 Deficiency

1972
Homocystinuria, vitamin B 6 , and folate: metabolic interrelationships and clinical significance.
    The Journal of pediatrics, 1972, Volume: 81, Issue:5

    Topics: Alcohol Oxidoreductases; Cystathionine; Folic Acid; Glycine; Homocystine; Homocystinuria; Humans; L-Serine Dehydratase; Metabolic Diseases; Methionine; Methyltransferases; Pyridoxine; Tetrahydrofolates; Transferases; Vitamin B 12

1972
Brain cystathionine synthase: vitamin-B6 requirement for its enzymic reaction and changes in enzymic activity during early development of rats.
    Brain research, 1971, Jul-09, Volume: 30, Issue:1

    Topics: Amino Acids; Animals; Brain; Brain Chemistry; Cystathionine; Female; Liver; Lyases; Male; Pyridoxine; Rats

1971
The assessment of the vitamin B6 status among Egyptian school children by measuring the urinary cystathionine excretion.
    International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition, 1984, Volume: 54, Issue:4

    Topics: Adolescent; Child; Cystathionine; Egypt; Female; Humans; Male; Methionine; Pyridoxine; Vitamin B 6 Deficiency

1984
Studies with cystathionase-deficient lymphoid cell lines in culture.
    Enzyme, 1982, Volume: 27, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Cell Line; Cystathionine; Cystathionine gamma-Lyase; Humans; Leucine; Lyases; Lymphocytes; Pyridoxine

1982
[Various forms of cystathioninuria].
    Fortschritte der Medizin, 1982, Mar-18, Volume: 100, Issue:11

    Topics: Amino Acid Metabolism, Inborn Errors; Cystathionine; Humans; Infant, Newborn; Infant, Premature, Diseases; Pyridoxine

1982
Evidence that homocysteine is an independent risk factor for atherosclerosis in hyperlipidemic patients.
    The American journal of cardiology, 1995, Jan-15, Volume: 75, Issue:2

    Topics: Aged; Analysis of Variance; Arteriosclerosis; Coronary Disease; Cystathionine; Folic Acid; Homocysteine; Humans; Hyperlipidemias; Methylmalonic Acid; Middle Aged; Pyridoxine; Risk Factors

1995
The effect of a subnormal vitamin B-6 status on homocysteine metabolism.
    The Journal of clinical investigation, 1996, Jul-01, Volume: 98, Issue:1

    Topics: Administration, Oral; Adult; Asthma; Bronchodilator Agents; Cystathionine; Female; Homocysteine; Humans; Male; Methionine; Middle Aged; Pyridoxine; Theophylline; Vitamin B 6 Deficiency

1996
Content of sulfur amino acids and vitamin B6 and related enzyme activities in rats with chronic renal failure fed a high methionine diet.
    Nephron, 1996, Volume: 74, Issue:1

    Topics: Amino Acids, Sulfur; Animals; Blood Urea Nitrogen; Body Weight; Creatinine; Cystathionine; Cystathionine beta-Synthase; Cystathionine gamma-Lyase; Cysteine; Dietary Proteins; Glomerular Filtration Rate; Kidney Failure, Chronic; Liver; Male; Methionine; Nephrectomy; Pyridoxine; Rats; Rats, Wistar; Taurine; Uremia; Vitamin B 6 Deficiency

1996
[Cystathioninuria in two families: a clinical and biochemical follow-up].
    Anales espanoles de pediatria, 1997, Volume: 46, Issue:1

    Topics: Child; Child, Preschool; Cystathionine; Female; Humans; Male; Pyridoxine

1997
A cartilage matrix deficiency experimentally induced by vitamin B6 deficiency.
    Proceedings of the Society for Experimental Biology and Medicine. Society for Experimental Biology and Medicine (New York, N.Y.), 1998, Volume: 217, Issue:1

    Topics: Animals; Body Weight; Cartilage, Articular; Chickens; Cystathionine; Erythrocytes; Insulin-Like Growth Factor Binding Proteins; Insulin-Like Growth Factor I; Male; Osteoarthritis; Proteoglycans; Pyridoxal Phosphate; Pyridoxine; Sulfates; Synovial Fluid; Vitamin B 6 Deficiency

1998
Vitamin B-6 deficiency and level of dietary protein affect hepatic tyrosine aminotransferase activity in cats.
    The Journal of nutrition, 1998, Volume: 128, Issue:11

    Topics: Animals; Cats; Circadian Rhythm; Cystathionine; Dietary Proteins; Food Deprivation; Liver; Pyridoxal Phosphate; Pyridoxamine; Pyridoxine; Rats; Rats, Sprague-Dawley; Tyrosine; Tyrosine Transaminase; Vitamin B 6 Deficiency

1998
Role of homocysteine, cystathionine and methylmalonic acid measurement for diagnosis of vitamin deficiency in high-aged subjects.
    European journal of clinical investigation, 2000, Volume: 30, Issue:12

    Topics: Adult; Aged; Cystathionine; Female; Folic Acid; Folic Acid Deficiency; Homocysteine; Humans; Kidney; Male; Methylmalonic Acid; Middle Aged; Models, Chemical; Pyridoxine; Vitamin B 12; Vitamin B 12 Deficiency; Vitamin B 6 Deficiency

2000
L-cystathionine in the urine of pyridoxine-deficient rats.
    The Biochemical journal, 1957, Volume: 66, Issue:3

    Topics: Amino Acids; Animals; Cystathionine; Pyridoxine; Rats; Vitamin B 6 Deficiency

1957
CYSTATHIONINE ACCUMULATION IN THE BRAINS OF PYRIDOXINE-DEFICIENT RATS.
    Journal of neurochemistry, 1964, Volume: 11

    Topics: Amino Acids; Brain; Chromatography; Colorimetry; Cystathionine; Infrared Rays; Metabolism; Pyridoxine; Rats; Research; Spectrum Analysis; Spinal Cord; Vitamin B 6 Deficiency

1964
Oral exposure to the anti-pyridoxine compound 1-amino D-proline further perturbs homocysteine metabolism through the transsulfuration pathway in moderately vitamin B₆ deficient rats.
    The Journal of nutritional biochemistry, 2015, Volume: 26, Issue:3

    Topics: Animals; Asymptomatic Diseases; Biomarkers; Cystathionine; Cystathionine gamma-Lyase; Diet; Disease Models, Animal; Disease Progression; Flax; Homocysteine; Hyperhomocysteinemia; Liver; Male; Non-alcoholic Fatty Liver Disease; Proline; Pyridoxal Phosphate; Pyridoxine; Random Allocation; Rats, Sprague-Dawley; Seeds; Vitamin B 6; Vitamin B 6 Deficiency

2015
Pyridoxine supplementation does not alter in vivo kinetics of one-carbon metabolism but modifies patterns of one-carbon and tryptophan metabolites in vitamin B-6-insufficient oral contraceptive users.
    The American journal of clinical nutrition, 2015, Volume: 102, Issue:3

    Topics: 3-Hydroxyanthranilic Acid; Adult; Biomarkers; Carbon; Contraceptives, Oral; Cystathionine; Dietary Supplements; Female; Glycine; Homocysteine; Humans; Kynurenine; Leucine; Methionine; Methylamines; Multivariate Analysis; Pyridoxal Phosphate; Pyridoxine; Serine; Tryptophan; Vitamin B 6 Deficiency; Young Adult

2015
A Vitamin B-6 Antagonist from Flaxseed Perturbs Amino Acid Metabolism in Moderately Vitamin B-6-Deficient Male Rats.
    The Journal of nutrition, 2016, Volume: 146, Issue:1

    Topics: Amino Acids; Aminobutyrates; Animals; Cystathionine; Cystathionine beta-Synthase; Cystathionine gamma-Lyase; Diet; Disease Models, Animal; Flax; Glutamic Acid; Liver; Male; Proline; Pyridoxine; Rats; Vitamin B 6; Vitamin B 6 Deficiency

2016
A Methionine-Portioning-Based Medical Nutrition Therapy with Relaxed Fruit and Vegetable Consumption in Patients with Pyridoxine-Nonresponsive Cystathionine-β-Synthase Deficiency.
    Nutrients, 2023, Jul-11, Volume: 15, Issue:14

    Topics: Cystathionine; Cystathionine beta-Synthase; Diet, Protein-Restricted; Fruit; Homocysteine; Homocystinuria; Humans; Methionine; Pyridoxine; Racemethionine; Vegetables

2023