Page last updated: 2024-08-26

propionylcarnitine and acetylcarnitine

propionylcarnitine has been researched along with acetylcarnitine in 60 studies

*Acetylcarnitine: An acetic acid ester of CARNITINE that facilitates movement of ACETYL COA into the matrices of mammalian MITOCHONDRIA during the oxidation of FATTY ACIDS. [MeSH]

*Acetylcarnitine: An acetic acid ester of CARNITINE that facilitates movement of ACETYL COA into the matrices of mammalian MITOCHONDRIA during the oxidation of FATTY ACIDS. [MeSH]

Research

Studies (60)

TimeframeStudies, this research(%)All Research%
pre-199011 (18.33)18.7374
1990's26 (43.33)18.2507
2000's9 (15.00)29.6817
2010's13 (21.67)24.3611
2020's1 (1.67)2.80

Authors

AuthorsStudies
Bertelli, A; Ronca-Testoni, S; Spaggiari, PG; Zucchi, R1
Sakuma, T; Sugiyama, N; Wada, Y1
Arrigoni Martelli, E; Bassani, E; Cardace, G; Corbelleta, C; Marzo, A; Morabito, E1
Arrigoni Martelli, E; Bassani, E; Cardace, G; Corbelletta, C; Mancinelli, A; Marzo, A; Solbiati, M1
Dhalla, NS; Ferrari, R; Kolár, F; Shah, KR1
Sakuma, T1
Brass, EP; Gandour, RD; Griffith, OW1
Boraso, A; Condorelli, E; Ferrari, R; Lisciani, R; Marzo, A; Pasini, E; Visiou, O1
Paulson, D; Regitz, V; Shug, A; Subramanian, R1
Scheffer, MA; van Hinsbergh, VW1
Arrigoni Martelli, E; Cardace, G; Esposito, G; Lindi, C; Marciani, P; Marzo, A1
Bonta, IL; Elliott, GR; Lauwen, AP1
Beyerinck, RA; Brass, EP1
Bieber, LL; Jakobs, C; Penn, D; Schmidt-Sommerfeld, E1
Brass, EP; Stabler, SP1
Kidouchi, K; Morishita, H; Nagai, S; Sakakibara, J; Sugiyama, N; Wada, Y1
Bremer, J; Hokland, BM1
Noonan, J; Paulson, DJ; Schmidt, M; Shug, AL; Traxler, J1
Okuyama, M; Yamaguchi, S; Yamamoto, H1
Liberato, DJ; Millington, DS; Yergey, AL1
Chalmers, RA; Hoppel, CL; Millington, DS; Roe, CR; Stacey, TE; Tracey, BM1
Bremer, J; Davis, EJ; Spydevold, O1
Kato, T; Kotaka, K; Miyazaki, Y; Ozawa, T; Sugiyama, S; Suzuki, S1
Cameron, NE; Cotter, MA; Dines, KC; Keegan, A1
Bartlett, K; Bhuiyan, AK; Seccombe, D1
Albano, O; Antonica, G; Berardi, E; Brevetti, G; Buonamico, P; Ferraioli, G; Godi, L; Sabbá, C1
Bonta, IL; Elliott, GR; Garrelds, IM; Zijlstra, FJ1
De Maria, P; Fontana, A; Frascari, S; Gargaro, G; Spinelli, D; Tinti, MO1
Cattapan, F; Magnanimi, L; Peschechera, A; Tassani, V1
Amico-Roxas, M; Caruso, A; Cutuli, VM; de Bernardis, E; Leonardi, G1
Hoppel, CL; Minkler, PE1
Arduini, A; Arrigoni-Martelli, E; Dottori, S; Federici, G; Gorbunov, N; Molajoni, F; Russo, F1
Bruno, G; Curti, S; Longo, A; Mancinelli, A; Miotto, G1
Capecchi, PL; Di Perri, T; Laghi Pasini, F; Quartarolo, E1
Chen, J; Conway, SJ; Ganapathy, V; Huang, W; Leibach, FH; Prasad, PD; Rajan, DP; Seth, P; Wu, X1
Grommisch, J; Gründer, W; Keller, T; Löster, H1
Iacobazzi, V; Lasorsa, FM; Palmieri, F; Palmieri, L; Runswick, MJ; Walker, JE1
Carter, AL; Ganapathy, ME; Ganapathy, V; Huang, W; Iseki, K; Leibach, FH; Rajan, DP; Sugawara, M1
Evans, AM; Longo, A; Pace, S; Rolan, P; Toon, S1
Evans, AM; Longo, A; Mancinelli, A; Nation, RL1
Arafa, HM; Sayed-Ahmed, MM1
Bertelli, A; Cui, J; Das, DK; Tosaki, A1
Cavallini, G; Koverech, A; Modenini, F; Vitali, G1
Al-Majed, AA; Al-Omar, FA; Al-Shabanah, OA; Al-Yahya, AA; Aleisa, AM; Sayed-Ahmed, MM1
Barshop, BA; Gangoiti, JA; Siuzdak, G; Wikoff, WR1
Cao, Y; Han, ZW; Liu, CJ; Wang, CB; Wang, LX; Wang, YX1
Chen, YJ; Cheng, KH; Chiang, CC; Ho, HJ; Hsiao, KJ; Huang, CH; Hung, PY; Hwu, WL; Kao, CH; Lee, NC; Lin, HY; Lin, JL; Lin, SP; Liu, MY; Liu, TT; Niu, DM1
Alvarez de Sotomayor, M; Herrera, MD; Justo, ML; Mingorance, C; Rodríguez-Rodríguez, R1
Malaguarnera, M1
Donzelli, M; Fischer-Barnicol, D; Krähenbühl, S; Morand, R; Mullen, PJ; Todesco, L1
Gao, XL; Gu, XF; Han, LS; Li, XY; Qiu, WJ; Wang, Y; Wu, SN; Xu, H; Ye, J; Zhang, HW1
Auriola, S; Hanhineva, K; Huotari, A; Keski-Rahkonen, P; Kolehmainen, M; Lehtonen, M; Mykkänen, H; Olli, K; Pekkinen, J; Poutanen, K; Tiihonen, K1
Bouitbir, J; Felser, A; Frank, S; Handschin, C; Hench, J; Krähenbühl, S; Morand, R1
Baumgartner, MR; Blom, HJ; Huemer, M; Kožich, V; Merinero, B; Pasquini, E; Ribes, A; Rinaldo, P1
Dayaldasani, A; Pérez-Valero, V; Rodríguez-Espinosa, M; Rueda, I; Ruiz-Escalera, J; Yahyaoui, R1
Gao, X; Gong, Z; Gu, X; Han, L; Jin, J; Qiu, W; Wang, Y; Wu, S; Ye, J; Zhang, H1
Al-Dirbashi, OY; Chakraborty, P; McIntosh, N1
Deng, Z; Jiang, Q; Li, C; Wang, C; Wang, M; Wang, Q; Xue, C; Xue, L1
Barić, I; Bártl, J; Baumgartner, MR; Ben-Omran, T; Blasco-Alonso, J; Blom, HJ; Bueno Delgado, MA; Carducci, C; Cassanello, M; Cerone, R; Chrastina, P; Couce, ML; Crushell, E; Delgado Pecellin, C; Dionisi-Vici, C; Dulin, E; Espada, M; Ferino, G; Fingerhut, R; Garcia Jimenez, I; Gleich, F; Gonzalez Gallego, I; González-Irazabal, Y; Gouveia, S; Gramer, G; Huemer, M; Juan Fita, MJ; Karg, E; Keller, R; Klein, J; Kölker, S; Konstantopoulou, V; Kožich, V; la Marca, G; Leão Teles, E; Leuzzi, V; Lilliu, F; Lopez, RM; Lund, AM; Mayne, P; Meavilla, S; Moat, SJ; Morris, AA; Okun, JG; Pasquini, E; Pavlíková, M; Pedron-Giner, CC; Racz, GZ; Ribes, A; Ruiz Gomez, MA; Vilarinho, L; Yahyaoui, R; Zerjav Tansek, M; Zetterström, RH; Zeyda, M1
Águas, R; Mota, SI; Pereira, FC; Pita, I; Rego, AC; Tagorti, S; Virmani, A1

Reviews

3 review(s) available for propionylcarnitine and acetylcarnitine

ArticleYear
Critical update for the clinical use of L-carnitine analogs in cardiometabolic disorders.
    Vascular health and risk management, 2011, Volume: 7

    Topics: Acetylcarnitine; Animals; Cardiovascular Agents; Cardiovascular Diseases; Carnitine; Diabetes Mellitus, Type 2; Evidence-Based Medicine; Humans; Hypoglycemic Agents; Insulin Resistance; Treatment Outcome

2011
Carnitine derivatives: clinical usefulness.
    Current opinion in gastroenterology, 2012, Volume: 28, Issue:2

    Topics: Acetylcarnitine; Cardiotonic Agents; Cardiovascular Diseases; Carnitine; Cognition Disorders; Depression; Diabetes Mellitus; Humans; Liver Cirrhosis; Nervous System Diseases; Nootropic Agents

2012
Newborn screening for homocystinurias and methylation disorders: systematic review and proposed guidelines.
    Journal of inherited metabolic disease, 2015, Volume: 38, Issue:6

    Topics: Acetylcarnitine; Betaine; Carnitine; Homocystinuria; Humans; Infant, Newborn; Methionine; Methylation; Methylenetetrahydrofolate Reductase (NADPH2); Methylmalonic Acid; Neonatal Screening; Practice Guidelines as Topic

2015

Trials

3 trial(s) available for propionylcarnitine and acetylcarnitine

ArticleYear
Comparison between the effect of L-propionylcarnitine, L-acetylcarnitine and nitroglycerin in chronic peripheral arterial disease: a haemodynamic double blind echo-Doppler study.
    European heart journal, 1994, Volume: 15, Issue:10

    Topics: Acetylcarnitine; Blood Flow Velocity; Cardiotonic Agents; Carnitine; Child, Preschool; Cross-Over Studies; Double-Blind Method; Femoral Artery; Hemodynamics; Humans; Male; Middle Aged; Nitroglycerin; Peripheral Vascular Diseases; Ultrasonography, Doppler, Pulsed

1994
Pharmacokinetics of propionyl-L-carnitine in humans: evidence for saturable tubular reabsorption.
    British journal of clinical pharmacology, 2000, Volume: 50, Issue:5

    Topics: Absorption; Acetylcarnitine; Adolescent; Adult; Cardiotonic Agents; Carnitine; Creatinine; Dose-Response Relationship, Drug; Double-Blind Method; Humans; Infusions, Intravenous; Kidney Tubules; Male; Middle Aged; Placebos

2000
Acetyl-L-carnitine plus propionyl-L-carnitine improve efficacy of sildenafil in treatment of erectile dysfunction after bilateral nerve-sparing radical retropubic prostatectomy.
    Urology, 2005, Volume: 66, Issue:5

    Topics: Acetylcarnitine; Carnitine; Drug Therapy, Combination; Erectile Dysfunction; Humans; Male; Middle Aged; Piperazines; Prospective Studies; Prostate; Prostatectomy; Purines; Sildenafil Citrate; Sulfones

2005

Other Studies

54 other study(ies) available for propionylcarnitine and acetylcarnitine

ArticleYear
Adenosine and carnitine derivatives and calcium movements in rat heart sarcoplasmic reticulum.
    International journal of tissue reactions, 1992, Volume: 14, Issue:1

    Topics: Acetylcarnitine; Adenosine; Animals; Calcium; Carnitine; Heart; In Vitro Techniques; Male; Myocardium; Perfusion; Rats; Rats, Sprague-Dawley; Sarcoplasmic Reticulum

1992
The urinary acylcarnitine profile in three cases of transient hyperammonemia of the newborn.
    Acta paediatrica (Oslo, Norway : 1992), 1992, Volume: 81, Issue:5

    Topics: Acetylcarnitine; Ammonia; Carnitine; Hippurates; Humans; Infant, Newborn; Male; Time Factors

1992
Homeostatic equilibrium of L-carnitine family before and after i.v. administration of propionyl-L-carnitine in humans, dogs and rats.
    European journal of drug metabolism and pharmacokinetics, 1991, Volume: Spec No 3

    Topics: Acetylcarnitine; Animals; Carnitine; Dogs; Female; Homeostasis; Humans; Injections, Intravenous; Male; Rats; Rats, Inbred Strains; Stereoisomerism

1991
Protein binding of L-carnitine family components.
    European journal of drug metabolism and pharmacokinetics, 1991, Volume: Spec No 3

    Topics: Acetylcarnitine; Animals; Blood Proteins; Carnitine; Chromatography, Gel; Dogs; Humans; Palmitoylcarnitine; Protein Binding; Rats; Serum Albumin; Ultrafiltration

1991
Effects of some L-carnitine derivatives on heart membrane ATPases.
    Cardiovascular drugs and therapy, 1991, Volume: 5 Suppl 1

    Topics: Acetylcarnitine; Animals; Ca(2+) Mg(2+)-ATPase; Calcium-Transporting ATPases; Carnitine; Cell Membrane; Cells, Cultured; Male; Rats; Sarcoplasmic Reticulum; Sodium-Potassium-Exchanging ATPase

1991
Alteration of urinary carnitine profile induced by benzoate administration.
    Archives of disease in childhood, 1991, Volume: 66, Issue:7

    Topics: Acetylcarnitine; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Carnitine; Child, Preschool; Dose-Response Relationship, Drug; Hippurates; Humans; Male

1991
Effect of carnitine acetyltransferase inhibition on rat hepatocyte metabolism.
    Biochimica et biophysica acta, 1991, Oct-16, Volume: 1095, Issue:1

    Topics: Acetylcarnitine; Animals; Carnitine; Carnitine O-Acetyltransferase; Cell Separation; Liver; Male; Morpholines; Oxidation-Reduction; Propionates; Pyruvates; Pyruvic Acid; Rats; Rats, Inbred Strains

1991
Effect of propionyl-L-carnitine on mechanical function of isolated rabbit heart.
    Cardiovascular drugs and therapy, 1991, Volume: 5 Suppl 1

    Topics: Acetylcarnitine; Animals; Carnitine; Electric Stimulation; Heart; Injections, Intraperitoneal; Male; Myocardial Contraction; Rabbits

1991
Protective effects of propionyl-L-carnitine during ischemia and reperfusion.
    Cardiovascular drugs and therapy, 1991, Volume: 5 Suppl 1

    Topics: Acetylcarnitine; Acyl Coenzyme A; Animals; Carnitine; Coronary Disease; Hemodynamics; Male; Myocardial Reperfusion; Rats; Rats, Inbred Strains

1991
Effect of propionyl-L-carnitine on human endothelial cells.
    Cardiovascular drugs and therapy, 1991, Volume: 5 Suppl 1

    Topics: Acetylcarnitine; Calcium; Carnitine; Cells, Cultured; Endothelium, Vascular; Humans; Lipoproteins, LDL

1991
L-carnitine and carnitine ester transport in the rat small intestine.
    Pharmacological research, 1991, Volume: 23, Issue:2

    Topics: Acetylcarnitine; Animals; Carnitine; Ether; Intestinal Absorption; Jejunum; Male; Potassium; Rats; Rats, Inbred Strains

1991
The effect of acute feeding of carnitine, acetyl carnitine and propionyl carnitine on basal and A23187-stimulated eicosanoid release from rat carrageenan-elicited peritoneal macrophages.
    The British journal of nutrition, 1990, Volume: 64, Issue:2

    Topics: 6-Ketoprostaglandin F1 alpha; Acetylcarnitine; Animals; Calcimycin; Carnitine; Dinoprostone; Eicosanoic Acids; Leukotriene B4; Macrophages; Male; Rats; Rats, Inbred Strains; Thromboxane B2

1990
Interactions of propionate and carnitine metabolism in isolated rat hepatocytes.
    Metabolism: clinical and experimental, 1987, Volume: 36, Issue:8

    Topics: Acetylcarnitine; Animals; Carbon Dioxide; Carnitine; Glucose; In Vitro Techniques; Liver; Male; Propionates; Rats; Rats, Inbred Strains

1987
Amniotic fluid propionylcarnitine in methylmalonic aciduria.
    Journal of inherited metabolic disease, 1987, Volume: 10, Issue:4

    Topics: Acetylcarnitine; Amino Acid Metabolism, Inborn Errors; Amniotic Fluid; Carnitine; Chromatography, High Pressure Liquid; Female; Humans; Malonates; Methylmalonic Acid

1987
Carnitine metabolism in the vitamin B-12-deficient rat.
    The Biochemical journal, 1988, Oct-01, Volume: 255, Issue:1

    Topics: Acetylcarnitine; Animals; Body Weight; Carnitine; Fasting; Male; Methylmalonic Acid; Rats; Vitamin B 12 Deficiency

1988
Analytical method for urinary glutarylcarnitine, acetylcarnitine and propionylcarnitine with a carboxylic acid analyser and a reversed-phase column.
    Journal of chromatography, 1987, Dec-25, Volume: 423

    Topics: Acetylcarnitine; Adolescent; Carboxylic Acids; Carnitine; Child, Preschool; Chromatography, High Pressure Liquid; Female; Humans; Magnetic Resonance Spectroscopy; Male; Mass Spectrometry

1987
Metabolism and excretion of carnitine and acylcarnitines in the perfused rat kidney.
    Biochimica et biophysica acta, 1986, Apr-29, Volume: 886, Issue:2

    Topics: Absorption; Acetylcarnitine; Albumins; Animals; Carnitine; Kidney; Male; Metabolic Clearance Rate; Perfusion; Rats; Rats, Inbred Strains

1986
Protection of the ischaemic myocardium by L-propionylcarnitine: effects on the recovery of cardiac output after ischaemia and reperfusion, carnitine transport, and fatty acid oxidation.
    Cardiovascular research, 1986, Volume: 20, Issue:7

    Topics: Acetylcarnitine; Adenosine Triphosphate; Animals; Blood Pressure; Cardiac Output; Carnitine; Coronary Disease; Fatty Acids; Male; Myocardial Contraction; Myocardium; Oxidation-Reduction; Palmitic Acid; Palmitic Acids; Phosphocreatine; Rats; Rats, Inbred Strains

1986
Pitfalls in the assay of acylcarnitine.
    Clinical chemistry, 1986, Volume: 32, Issue:2

    Topics: Acetylcarnitine; Carnitine; Humans; Hydrogen-Ion Concentration; Hydrolysis; Radiochemistry

1986
Thermospray liquid chromatography/mass spectrometry for the analysis of L-carnitine and its short-chain acyl derivatives.
    Analytical biochemistry, 1984, Volume: 139, Issue:2

    Topics: Acetylcarnitine; Carnitine; Chromatography, High Pressure Liquid; Hot Temperature; Mass Spectrometry

1984
Metabolic response to carnitine in methylmalonic aciduria. An effective strategy for elimination of propionyl groups.
    Archives of disease in childhood, 1983, Volume: 58, Issue:11

    Topics: Acetylcarnitine; Amino Acid Metabolism, Inborn Errors; Carnitine; Female; Humans; Infant; Malonates; Methylmalonic Acid

1983
Pyruvate carboxylase and propionyl-CoA carboxylase as anaplerotic enzymes in skeletal muscle mitochondria.
    European journal of biochemistry, 1980, Volume: 110, Issue:1

    Topics: Acetylcarnitine; Adenosine Triphosphate; Animals; Bicarbonates; Carbon Dioxide; Carbon-Carbon Ligases; Carnitine; Citric Acid Cycle; Ligases; Mitochondria, Heart; Mitochondria, Muscle; Pyruvate Carboxylase; Pyruvates; Rats

1980
Mechanism of free fatty acid-induced arrhythmias.
    Journal of electrocardiology, 1982, Volume: 15, Issue:3

    Topics: Acetylcarnitine; Acyl Coenzyme A; Animals; Arrhythmias, Cardiac; Calcium; Carnitine; Dogs; Fatty Acids, Nonesterified; Heart; Mitochondria, Heart

1982
Effects of acetyl- and proprionyl-L-carnitine on peripheral nerve function and vascular supply in experimental diabetes.
    Metabolism: clinical and experimental, 1995, Volume: 44, Issue:9

    Topics: Acetylcarnitine; Action Potentials; Animals; Blood Flow Velocity; Blood Glucose; Body Weight; Carnitine; Diabetes Mellitus, Experimental; Kinetics; Male; Neural Conduction; Peripheral Nerves; Rats; Rats, Sprague-Dawley; Sciatic Nerve

1995
Production of acyl-carnitines from the metabolism of [U-14C]3-methyl-2-oxopentanoate by rat liver and skeletal muscle mitochondria.
    Clinical and investigative medicine. Medecine clinique et experimentale, 1995, Volume: 18, Issue:2

    Topics: Acetylcarnitine; Amino Acids, Branched-Chain; Animals; Carnitine; Chromatography, High Pressure Liquid; Keto Acids; Kinetics; Male; Mitochondria, Liver; Mitochondria, Muscle; Oxidation-Reduction; Rats; Rats, Wistar

1995
Effects of short- and long-term feeding of L-carnitine and congeners on the production of eicosanoids from rat peritoneal leucocytes.
    The British journal of nutrition, 1994, Volume: 72, Issue:5

    Topics: 6-Ketoprostaglandin F1 alpha; Acetylcarnitine; Animals; Carnitine; Cell Count; Eicosanoids; In Vitro Techniques; Leukotriene B4; Macrophages, Peritoneal; Male; Rats; Rats, Wistar; Time Factors

1994
Effect of the addition of electrolytes on the partition coefficients, activity coefficients, and acid dissociation constants of carnitine and its acetyl and propionyl derivatives.
    Journal of pharmaceutical sciences, 1994, Volume: 83, Issue:5

    Topics: 1-Octanol; Acetylcarnitine; Biological Transport; Carnitine; Cations; Chemical Phenomena; Chemistry, Physical; Electrolytes; Kinetics; Metals; Octanols; Osmolar Concentration; Solubility; Thermodynamics; Water

1994
Anaplerotic effect of propionyl carnitine in rat heart mitochondria.
    Biochemical and biophysical research communications, 1994, Mar-15, Volume: 199, Issue:2

    Topics: Acetylcarnitine; Animals; Carbon Dioxide; Cardiotonic Agents; Carnitine; Male; Malonates; Mitochondria, Heart; Mitochondria, Liver; Oxygen Consumption; Pyruvates; Rats; Rats, Wistar

1994
Inhibitory effects of propionyl-L-carnitine on plasma extravasation induced by irritants in rodents.
    Drugs under experimental and clinical research, 1993, Volume: 19, Issue:5

    Topics: Acetylcarnitine; Animals; Anti-Inflammatory Agents, Non-Steroidal; Capillary Permeability; Carnitine; Carrageenan; Dermatitis; Edema; Exudates and Transudates; Gossypium; Granuloma; Irritants; Male; Mice; Peritonitis; Rats; Rats, Sprague-Dawley

1993
Quantification of free carnitine, individual short- and medium-chain acylcarnitines, and total carnitine in plasma by high-performance liquid chromatography.
    Analytical biochemistry, 1993, Aug-01, Volume: 212, Issue:2

    Topics: Acetylcarnitine; Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Acylation; Carnitine; Chromatography, High Pressure Liquid; Humans; Methylmalonic Acid; Molecular Weight; Propionates; Reference Standards; Reproducibility of Results

1993
Effects of L-carnitine and its acetate and propionate esters on the molecular dynamics of human erythrocyte membrane.
    Biochimica et biophysica acta, 1993, Mar-14, Volume: 1146, Issue:2

    Topics: Acetylcarnitine; Carnitine; Diphenylhexatriene; Electron Spin Resonance Spectroscopy; Erythrocyte Membrane; Esters; Humans; Membrane Fluidity; Membrane Proteins; Palmitoylcarnitine; Pyrimidinones; Spin Labels

1993
Determination of L-carnitine, acetyl-L-carnitine and propionyl-L-carnitine in human plasma by high-performance liquid chromatography after pre-column derivatization with 1-aminoanthracene.
    Journal of chromatography. B, Biomedical applications, 1996, Nov-15, Volume: 686, Issue:2

    Topics: Acetylcarnitine; Anthracenes; Carnitine; Chromatography, High Pressure Liquid; Fluorescent Dyes; Humans; Reproducibility of Results; Sensitivity and Specificity; Spectrometry, Fluorescence

1996
Carnitines increase plasma levels of adenosine and ATP in humans.
    Vascular medicine (London, England), 1997, Volume: 2, Issue:2

    Topics: Acetylcarnitine; Adenosine; Adenosine Triphosphate; Aged; Analysis of Variance; Cardiotonic Agents; Carnitine; Female; Humans; Infusions, Intravenous; Inosine; Intermittent Claudication; Male

1997
Functional characteristics and tissue distribution pattern of organic cation transporter 2 (OCTN2), an organic cation/carnitine transporter.
    The Journal of pharmacology and experimental therapeutics, 1999, Volume: 290, Issue:3

    Topics: Acetylcarnitine; Animals; Biological Transport, Active; Carnitine; Carrier Proteins; Humans; In Situ Hybridization; Kidney; Membrane Proteins; Mice; Myocardium; Organ Specificity; Organic Cation Transport Proteins; Placenta; Rats; RNA, Messenger; Solute Carrier Family 22 Member 5; Tetraethylammonium

1999
Effects of L-carnitine and its acetyl and propionyl esters on ATP and PCr levels of isolated rat hearts perfused without fatty acids and investigated by means of 31P-NMR spectroscopy.
    Molecular and cellular biochemistry, 1999, Volume: 200, Issue:1-2

    Topics: Acetylcarnitine; Adenosine Triphosphate; Animals; Carnitine; Energy Metabolism; Female; Heart; In Vitro Techniques; Magnetic Resonance Spectroscopy; Myocardial Ischemia; Myocardial Reperfusion Injury; Myocardium; Perfusion; Phosphates; Phosphocreatine; Rats; Rats, Wistar

1999
Identification of the mitochondrial carnitine carrier in Saccharomyces cerevisiae.
    FEBS letters, 1999, Dec-03, Volume: 462, Issue:3

    Topics: Acetylcarnitine; Amino Acid Transport Systems; Carnitine; Carrier Proteins; Chromatography, Affinity; Kinetics; Mitochondria; Mitochondrial Proteins; Molecular Sequence Data; Recombinant Proteins; Saccharomyces cerevisiae; Saccharomyces cerevisiae Proteins; Substrate Specificity; Time Factors

1999
beta-lactam antibiotics as substrates for OCTN2, an organic cation/carnitine transporter.
    The Journal of biological chemistry, 2000, Jan-21, Volume: 275, Issue:3

    Topics: Acetylcarnitine; Animals; Anti-Bacterial Agents; Carnitine; Carrier Proteins; Cefadroxil; Cefepime; Cephaloridine; Cephalosporins; Dose-Response Relationship, Drug; HeLa Cells; Humans; Kinetics; Membrane Proteins; Nitrogen; Organic Cation Transport Proteins; Rats; Sodium; Solute Carrier Family 22 Member 5; Tumor Cells, Cultured

2000
Disposition of L-carnitine and its short-chain esters, acetyl-L-carnitine and propionyl-L-carnitine, in the rat isolated perfused liver.
    Drug metabolism and disposition: the biological fate of chemicals, 2000, Volume: 28, Issue:12

    Topics: Acetylcarnitine; Animals; Area Under Curve; Biological Availability; Cardiotonic Agents; Carnitine; Half-Life; In Vitro Techniques; Liver; Male; Nootropic Agents; Rats; Rats, Sprague-Dawley

2000
Protective role of carnitine esters against alcohol-induced gastric lesions in rats.
    Pharmacological research, 2003, Volume: 48, Issue:3

    Topics: Acetylcarnitine; Administration, Oral; Animals; Carnitine; Catalase; Ethanol; Gastric Mucosa; Glutathione; Glutathione Transferase; Male; Mice; Rats; Stomach Ulcer; Superoxide Dismutase; Thiobarbituric Acid Reactive Substances

2003
Effects of L-carnitine and its derivatives on postischemic cardiac function, ventricular fibrillation and necrotic and apoptotic cardiomyocyte death in isolated rat hearts.
    Molecular and cellular biochemistry, 2003, Volume: 254, Issue:1-2

    Topics: Acetylcarnitine; Animals; Apoptosis; Cardiotonic Agents; Carnitine; Heart; Ischemia; Myocardium; Myocytes, Cardiac; Rats; Rats, Sprague-Dawley; Reperfusion Injury; Time Factors; Ventricular Fibrillation

2003
Carnitine esters prevent oxidative stress damage and energy depletion following transient forebrain ischaemia in the rat hippocampus.
    Clinical and experimental pharmacology & physiology, 2006, Volume: 33, Issue:8

    Topics: Acetylcarnitine; Adenosine Triphosphate; Animals; Carnitine; Disease Models, Animal; Energy Metabolism; Glutathione; Hippocampus; Ischemic Attack, Transient; Male; Nerve Degeneration; Neurons; Neuroprotective Agents; Nitrates; Nitrites; Oxidative Stress; Prosencephalon; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances

2006
Metabolomics identifies perturbations in human disorders of propionate metabolism.
    Clinical chemistry, 2007, Volume: 53, Issue:12

    Topics: Acetylcarnitine; Adult; Amino Acid Metabolism, Inborn Errors; Betaine; Biomarkers; Carnitine; Child; Chromatography, High Pressure Liquid; Humans; Methylmalonic Acid; Plasma; Propionates; Spectrometry, Mass, Electrospray Ionization

2007
Comparison of pharmacokinetics of L-carnitine, acetyl-L-carnitine and propionyl-L-carnitine after single oral administration of L-carnitine in healthy volunteers.
    Clinical and investigative medicine. Medecine clinique et experimentale, 2009, Feb-01, Volume: 32, Issue:1

    Topics: Acetylcarnitine; Administration, Oral; Adult; Area Under Curve; Carnitine; Chromatography, High Pressure Liquid; Female; Half-Life; Humans; Male; Reference Values

2009
Newborn screening for methylmalonic aciduria by tandem mass spectrometry: 7 years' experience from two centers in Taiwan.
    Journal of the Chinese Medical Association : JCMA, 2010, Volume: 73, Issue:6

    Topics: Acetylcarnitine; Ammonia; Carnitine; Humans; Infant, Newborn; Methylmalonic Acid; Neonatal Screening; Taiwan; Tandem Mass Spectrometry

2010
Effect of short- and long-term treatment with valproate on carnitine homeostasis in humans.
    Therapeutic drug monitoring, 2012, Volume: 34, Issue:4

    Topics: Acetylcarnitine; Adult; Betaine; Biological Transport; Carnitine; Cell Line; Drug Administration Schedule; Female; HEK293 Cells; Homeostasis; Humans; Kidney Tubules, Proximal; Organic Cation Transport Proteins; Solute Carrier Family 22 Member 5; Valproic Acid

2012
[Analysis of propionylcarnitine in blood and methylmalonic acid in urine of 162 patients with methylmalonic acidemia].
    Zhonghua yi xue za zhi, 2013, Feb-26, Volume: 93, Issue:8

    Topics: Acetylcarnitine; Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Carnitine; Case-Control Studies; Child; Child, Preschool; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Infant, Newborn; Male; Methylmalonic Acid; Tandem Mass Spectrometry; Young Adult

2013
Betaine supplementation causes increase in carnitine metabolites in the muscle and liver of mice fed a high-fat diet as studied by nontargeted LC-MS metabolomics approach.
    Molecular nutrition & food research, 2013, Volume: 57, Issue:11

    Topics: Acetylcarnitine; Adipose Tissue; Adiposity; Animals; Betaine; Blood Glucose; Carnitine; Chromatography, Liquid; Diet, High-Fat; Dietary Supplements; Fasting; Glucans; Insulin; Leptin; Lipid Metabolism; Liver; Male; Mass Spectrometry; Metabolomics; Mice; Mice, Inbred C57BL; Muscle, Skeletal; Obesity; Triglycerides; Weight Gain

2013
Effect of carnitine, acetyl-, and propionylcarnitine supplementation on the body carnitine pool, skeletal muscle composition, and physical performance in mice.
    European journal of nutrition, 2014, Volume: 53, Issue:6

    Topics: Acetylcarnitine; Administration, Oral; Animals; Biological Availability; Biomarkers; Carnitine; Dietary Supplements; Energy Metabolism; Liver; Male; Mice; Mice, Inbred C57BL; Muscle, Skeletal; Oxidative Stress; Oxygen Consumption; Physical Conditioning, Animal

2014
Serum vitamin B12 levels during the first trimester of pregnancy correlate with newborn screening markers of vitamin B12 deficiency.
    International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition, 2014, Volume: 84, Issue:1-2

    Topics: Acetylcarnitine; Adolescent; Adult; Biomarkers; Carnitine; Diet; Female; Gestational Age; Humans; Infant, Newborn; Maternal Welfare; Meat; Neonatal Screening; Nutritional Status; Pregnancy; Pregnancy Complications; Pregnancy Trimester, Third; Smoking; Vitamin B 12; Vitamin B 12 Deficiency; Young Adult

2014
Biochemical, molecular and outcome analysis of eight chinese asymptomatic individuals with methyl malonic acidemia detected through newborn screening.
    American journal of medical genetics. Part A, 2015, Volume: 167A, Issue:10

    Topics: Acetylcarnitine; Acidosis; Asian People; Asymptomatic Diseases; Carboxy-Lyases; Carnitine; Carrier Proteins; Child; Citrates; Female; Gene Expression; Humans; Infant; Infant, Newborn; Male; Malonates; Malonyl Coenzyme A; Metabolism, Inborn Errors; Methylmalonic Acid; Methylmalonyl-CoA Mutase; Mutation; Neonatal Screening; Oxidoreductases

2015
Quantification of 2-methylcitric acid in dried blood spots improves newborn screening for propionic and methylmalonic acidemias.
    Journal of medical screening, 2017, Volume: 24, Issue:2

    Topics: Acetylcarnitine; Algorithms; Amino Acid Metabolism, Inborn Errors; Biomarkers; Carnitine; Chromatography, Liquid; Citrates; Dried Blood Spot Testing; False Positive Reactions; Humans; Infant, Newborn; Methylmalonic Acid; Neonatal Screening; Predictive Value of Tests; Reference Values; Referral and Consultation; Reproducibility of Results; Tandem Mass Spectrometry

2017
Changes in the levels of l-carnitine, acetyl-l-carnitine and propionyl-l-carnitine are involved in perfluorooctanoic acid induced developmental cardiotoxicity in chicken embryo.
    Environmental toxicology and pharmacology, 2016, Volume: 48

    Topics: Acetylcarnitine; Animals; Blotting, Western; Caprylates; Cardiotoxicity; Carnitine; Chick Embryo; Chickens; Chromatography, Liquid; Dose-Response Relationship, Drug; Electrocardiography; Environmental Pollutants; Fluorocarbons; Heart; Myocardium; Tandem Mass Spectrometry

2016
Newborn screening for homocystinurias: Recent recommendations versus current practice.
    Journal of inherited metabolic disease, 2019, Volume: 42, Issue:1

    Topics: Acetylcarnitine; Amino Acid Metabolism, Inborn Errors; Carnitine; Female; Glycine N-Methyltransferase; Homocysteine; Homocystinuria; Humans; Infant, Newborn; Male; Methionine; Methylenetetrahydrofolate Reductase (NADPH2); Methylmalonic Acid; Muscle Spasticity; Neonatal Screening; Phenylalanine; Psychotic Disorders

2019
Mechanistic perspectives on differential mitochondrial-based neuroprotective effects of several carnitine forms in Alzheimer's disease in vitro model.
    Archives of toxicology, 2021, Volume: 95, Issue:8

    Topics: Acetylcarnitine; Alzheimer Disease; Animals; Apoptosis; Carnitine; Cells, Cultured; Female; Hippocampus; Membrane Potential, Mitochondrial; Mitochondria; Neurons; Neuroprotective Agents; Oxygen Consumption; Rats; Rats, Wistar

2021