Page last updated: 2024-08-26

propionyl-coenzyme a and methylmalonic acid

propionyl-coenzyme a has been researched along with methylmalonic acid in 6 studies

Research

Studies (6)

TimeframeStudies, this research(%)All Research%
pre-19901 (16.67)18.7374
1990's4 (66.67)18.2507
2000's1 (16.67)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Chalmers, RA; Davies, SE; de Sousa, C; Iles, RA; Stacey, TE1
Baumgartner, R; Spaapen, LJ; van der Meer, SB; Wendel, U1
Bartlett, K; Halliday, D; Leonard, JV; Thompson, GN; Walter, JH1
Leupold, D; Wendel, U; Zass, R1
Kennedy, DG; Kennedy, S; Young, PB1
Hinz, A; Hoffmann, GF; Hörster, F; Kölker, S; Mayatepek, E; Okun, JG; Sauer, S; Schwab, M; Smeitink, JA; Wolf, NI1

Other Studies

6 other study(ies) available for propionyl-coenzyme a and methylmalonic acid

ArticleYear
Carnitine therapy and metabolism in the disorders of propionyl-CoA metabolism studied using 1H-NMR spectroscopy.
    Clinica chimica acta; international journal of clinical chemistry, 1991, Dec-31, Volume: 204, Issue:1-3

    Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Infant, Newborn; Kinetics; Magnetic Resonance Spectroscopy; Male; Methylmalonic Acid; Propionates

1991
Accumulation of odd-numbered long-chain fatty acids in fetuses and neonates with inherited disorders of propionate metabolism.
    Pediatric research, 1991, Volume: 29, Issue:4 Pt 1

    Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Fatty Acids; Female; Fetus; Humans; Infant, Newborn; Male; Metabolism, Inborn Errors; Methylmalonic Acid; Pregnancy; Propionates; Vitamin B 12

1991
Contribution of aminoacid catabolism to propionate production in methylmalonic acidaemia.
    Lancet (London, England), 1989, Jun-10, Volume: 1, Issue:8650

    Topics: Acyl Coenzyme A; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Child; Humans; Isoleucine; Kinetics; Leucine; Malonates; Methionine; Methylmalonic Acid; Phenylalanine; Threonine; Time Factors; Valine

1989
Contribution of odd-numbered fatty acid oxidation to propionate production in neonates with methylmalonic and propionic acidaemias.
    European journal of pediatrics, 1993, Volume: 152, Issue:12

    Topics: Acyl Coenzyme A; Adipose Tissue; Amino Acid Metabolism, Inborn Errors; Fatty Acids; Humans; Infant, Newborn; Methylmalonic Acid; Mitochondria; Oxidation-Reduction; Propionates

1993
Effects of low concentrations of dietary cobalt on rumen succinate concentration in sheep.
    International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition, 1996, Volume: 66, Issue:1

    Topics: Acyl Coenzyme A; Animals; Cobalt; Diet; Liver; Methylmalonic Acid; Methylmalonyl-CoA Mutase; Propionates; Rumen; Sheep; Succinates; Succinic Acid; Vitamin B 12

1996
Methylmalonic acid, a biochemical hallmark of methylmalonic acidurias but no inhibitor of mitochondrial respiratory chain.
    The Journal of biological chemistry, 2003, Nov-28, Volume: 278, Issue:48

    Topics: Acyl Coenzyme A; Adenosine Triphosphate; Aging; Amino Acid Metabolism, Inborn Errors; Animals; Cattle; Citrates; Citric Acid Cycle; Dose-Response Relationship, Drug; Electron Transport; Female; Hydrogen-Ion Concentration; Male; Malonates; Methylmalonic Acid; Mice; Mice, Inbred C57BL; Mitochondria; Mitochondrial Diseases; Muscles; Myocardium; Oxygen; Phosphorylation; Pyruvates; Spectrophotometry; Time Factors

2003