propionic acid and propionylcarnitine

propionic acid has been researched along with propionylcarnitine in 15 studies

Research

Studies (15)

TimeframeStudies, this research(%)All Research%
pre-19906 (40.00)18.7374
1990's4 (26.67)18.2507
2000's5 (33.33)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Jeffrey, FM; Malloy, CR; Rajagopal, A; Roby, RE; Sherry, AD1
Brass, EP; Fennessey, PV; Miller, LV1
Kamiya, K; Kawase, A; Morishita, H; Nagaya, S; Nakajima, T; Ohya, A; Sugiyama, N; Sugiyama, S; Togari, H; Watanabe, I1
Böhles, H; Lehnert, W1
Di Donato, S; Garavaglia, B; Rimoldi, M; Uziel, G1
Bohan, TP; Hoppel, CL; Maltby, DA; Millington, DS; Roe, CR1
Kidouchi, K; Kobayashi, M; Matsuda, I; Narisawa, K; Sugiyama, N; Wada, Y1
Barbato, R; Di Lisa, F; Menabò, R; Siliprandi, N1
Fujioka, M; Kikawa, Y; Liu, YY; Nakai, A; Shigematsu, Y; Sudo, M1
Hoppel, CL; Minkler, PE1
de Hoffmann, E; Libert, R; Nassogne, MC; Schanck, A; Thillaye, M; Van Hoof, F; Vincent, MF1
Chace, DH; DiPerna, JC; Johnson, RW; Kalas, TA; Naylor, EW1
Endo, F; Inoue, Y; Ishimatu, J; Kuhara, T; Mitsubuchi, H; Ohse, M; Sakura, N; Yorifuji, T1
Endo, F; Hirano, S; Kawai, M; Kuhara, T; Kurokawa, K; Mamada, M; Mitsubuchi, H; Muroi, J; Nakahata, T; Sakura, N; Shigematsu, Y; Yorifuji, T; Yoshida, I1
Barshop, BA; Gangoiti, JA; Siuzdak, G; Wikoff, WR1

Other Studies

15 other study(ies) available for propionic acid and propionylcarnitine

ArticleYear
Propionate metabolism in the rat heart by 13C n.m.r. spectroscopy.
    The Biochemical journal, 1988, Sep-01, Volume: 254, Issue:2

    Topics: Animals; Carbon Isotopes; Carnitine; In Vitro Techniques; Magnetic Resonance Spectroscopy; Methylmalonic Acid; Myocardium; Perfusion; Propionates; Pyruvates; Pyruvic Acid; Rats

1988
Inhibition of oxidative metabolism by propionic acid and its reversal by carnitine in isolated rat hepatocytes.
    The Biochemical journal, 1986, May-15, Volume: 236, Issue:1

    Topics: Animals; Carnitine; Drug Interactions; In Vitro Techniques; Liver; Male; Mass Spectrometry; Oxidation-Reduction; Palmitic Acid; Palmitic Acids; Propionates; Pyruvates; Pyruvic Acid; Rats; Rats, Inbred Strains; Starvation

1986
Biochemical evidence of carnitine effect on propionate elimination.
    Journal of inherited metabolic disease, 1984, Volume: 7, Issue:3

    Topics: Carboxy-Lyases; Carnitine; Fibroblasts; Humans; Infant; Methylmalonyl-CoA Decarboxylase; Propionates; Skin

1984
The effect of intravenous L-carnitine on propionic acid excretion in acute propionic acidaemia.
    European journal of pediatrics, 1984, Volume: 143, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Female; Humans; Infant; Injections, Intravenous; Propionates

1984
Propionylcarnitine excretion in propionic and methylmalonic acidurias: a cause of carnitine deficiency.
    Clinica chimica acta; international journal of clinical chemistry, 1984, May-16, Volume: 139, Issue:1

    Topics: Carnitine; Child, Preschool; Humans; Infant; Infant, Newborn; Malonates; Metabolism, Inborn Errors; Methylmalonic Acid; Muscles; Propionates

1984
L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia.
    The Journal of clinical investigation, 1984, Volume: 73, Issue:6

    Topics: Acyl Coenzyme A; Adolescent; Carboxy-Lyases; Carnitine; Child; Child, Preschool; Humans; Infant; Male; Mass Spectrometry; Metabolism, Inborn Errors; Methylmalonyl-CoA Decarboxylase; Propionates

1984
Urinary propionylcarnitine analysis for monitoring carnitine supplementation in inherited disorders of propionate metabolism.
    Journal of inherited metabolic disease, 1994, Volume: 17, Issue:5

    Topics: Adolescent; Carnitine; Child; Child, Preschool; Female; Humans; Infant; Male; Metabolism, Inborn Errors; Propionates

1994
Contrasting effects of propionate and propionyl-L-carnitine on energy-linked processes in ischemic hearts.
    The American journal of physiology, 1994, Volume: 267, Issue:2 Pt 2

    Topics: Animals; Cardiotonic Agents; Carnitine; Coenzyme A; Energy Metabolism; Esters; In Vitro Techniques; Male; Mitochondria, Heart; Myocardial Contraction; Myocardial Ischemia; Myocardial Reperfusion; Myocardium; Propionates; Rats; Rats, Wistar

1994
Free carnitine and short-chain acylcarnitines in cerebrospinal fluid of patients with disorders of propionate metabolism determined by fast atom bombardment and tandem mass spectrometry.
    Acta paediatrica Japonica : Overseas edition, 1994, Volume: 36, Issue:1

    Topics: Adolescent; Carnitine; Female; Humans; Infant; Mass Spectrometry; Metabolic Diseases; Propionates; Spectrometry, Mass, Fast Atom Bombardment

1994
Quantification of free carnitine, individual short- and medium-chain acylcarnitines, and total carnitine in plasma by high-performance liquid chromatography.
    Analytical biochemistry, 1993, Aug-01, Volume: 212, Issue:2

    Topics: Acetylcarnitine; Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Acylation; Carnitine; Chromatography, High Pressure Liquid; Humans; Methylmalonic Acid; Molecular Weight; Propionates; Reference Standards; Reproducibility of Results

1993
Identification of undescribed medium-chain acylcarnitines present in urine of patients with propionic and methylmalonic acidemias.
    Clinica chimica acta; international journal of clinical chemistry, 2000, Volume: 295, Issue:1-2

    Topics: Adult; Carboxy-Lyases; Carnitine; Case-Control Studies; Gas Chromatography-Mass Spectrometry; Humans; Infant; Lipid Metabolism, Inborn Errors; Male; Methylmalonic Acid; Methylmalonyl-CoA Decarboxylase; Propionates; Spectrometry, Mass, Fast Atom Bombardment

2000
Rapid diagnosis of methylmalonic and propionic acidemias: quantitative tandem mass spectrometric analysis of propionylcarnitine in filter-paper blood specimens obtained from newborns.
    Clinical chemistry, 2001, Volume: 47, Issue:11

    Topics: Amino Acid Metabolism, Inborn Errors; Blood Specimen Collection; Carnitine; False Positive Reactions; Humans; Infant, Newborn; Methylmalonic Acid; Paper; Propionates; Spectrometry, Mass, Electrospray Ionization

2001
Gas chromatographic-mass spectrometric newborn screening for propionic acidaemia by targeting methylcitrate in dried filter-paper urine samples.
    Journal of inherited metabolic disease, 2002, Volume: 25, Issue:2

    Topics: Carboxy-Lyases; Carnitine; Citrates; DNA Mutational Analysis; Gas Chromatography-Mass Spectrometry; Homozygote; Humans; Infant, Newborn; Male; Mass Spectrometry; Methylmalonyl-CoA Decarboxylase; Mutation, Missense; Neonatal Screening; Paper; Propionates

2002
Unexpectedly high prevalence of the mild form of propionic acidemia in Japan: presence of a common mutation and possible clinical implications.
    Human genetics, 2002, Volume: 111, Issue:2

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Carboxy-Lyases; Carnitine; Child, Preschool; Citrates; DNA Mutational Analysis; DNA Primers; Exons; Humans; Infant; Japan; Methylmalonyl-CoA Decarboxylase; Mutation; Polymerase Chain Reaction; Polymorphism, Single-Stranded Conformational; Prevalence; Propionates; RNA, Messenger

2002
Metabolomics identifies perturbations in human disorders of propionate metabolism.
    Clinical chemistry, 2007, Volume: 53, Issue:12

    Topics: Acetylcarnitine; Adult; Amino Acid Metabolism, Inborn Errors; Betaine; Biomarkers; Carnitine; Child; Chromatography, High Pressure Liquid; Humans; Methylmalonic Acid; Plasma; Propionates; Spectrometry, Mass, Electrospray Ionization

2007