propionic acid has been researched along with propionylcarnitine in 15 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 6 (40.00) | 18.7374 |
1990's | 4 (26.67) | 18.2507 |
2000's | 5 (33.33) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Jeffrey, FM; Malloy, CR; Rajagopal, A; Roby, RE; Sherry, AD | 1 |
Brass, EP; Fennessey, PV; Miller, LV | 1 |
Kamiya, K; Kawase, A; Morishita, H; Nagaya, S; Nakajima, T; Ohya, A; Sugiyama, N; Sugiyama, S; Togari, H; Watanabe, I | 1 |
Böhles, H; Lehnert, W | 1 |
Di Donato, S; Garavaglia, B; Rimoldi, M; Uziel, G | 1 |
Bohan, TP; Hoppel, CL; Maltby, DA; Millington, DS; Roe, CR | 1 |
Kidouchi, K; Kobayashi, M; Matsuda, I; Narisawa, K; Sugiyama, N; Wada, Y | 1 |
Barbato, R; Di Lisa, F; Menabò, R; Siliprandi, N | 1 |
Fujioka, M; Kikawa, Y; Liu, YY; Nakai, A; Shigematsu, Y; Sudo, M | 1 |
Hoppel, CL; Minkler, PE | 1 |
de Hoffmann, E; Libert, R; Nassogne, MC; Schanck, A; Thillaye, M; Van Hoof, F; Vincent, MF | 1 |
Chace, DH; DiPerna, JC; Johnson, RW; Kalas, TA; Naylor, EW | 1 |
Endo, F; Inoue, Y; Ishimatu, J; Kuhara, T; Mitsubuchi, H; Ohse, M; Sakura, N; Yorifuji, T | 1 |
Endo, F; Hirano, S; Kawai, M; Kuhara, T; Kurokawa, K; Mamada, M; Mitsubuchi, H; Muroi, J; Nakahata, T; Sakura, N; Shigematsu, Y; Yorifuji, T; Yoshida, I | 1 |
Barshop, BA; Gangoiti, JA; Siuzdak, G; Wikoff, WR | 1 |
15 other study(ies) available for propionic acid and propionylcarnitine
Article | Year |
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Propionate metabolism in the rat heart by 13C n.m.r. spectroscopy.
Topics: Animals; Carbon Isotopes; Carnitine; In Vitro Techniques; Magnetic Resonance Spectroscopy; Methylmalonic Acid; Myocardium; Perfusion; Propionates; Pyruvates; Pyruvic Acid; Rats | 1988 |
Inhibition of oxidative metabolism by propionic acid and its reversal by carnitine in isolated rat hepatocytes.
Topics: Animals; Carnitine; Drug Interactions; In Vitro Techniques; Liver; Male; Mass Spectrometry; Oxidation-Reduction; Palmitic Acid; Palmitic Acids; Propionates; Pyruvates; Pyruvic Acid; Rats; Rats, Inbred Strains; Starvation | 1986 |
Biochemical evidence of carnitine effect on propionate elimination.
Topics: Carboxy-Lyases; Carnitine; Fibroblasts; Humans; Infant; Methylmalonyl-CoA Decarboxylase; Propionates; Skin | 1984 |
The effect of intravenous L-carnitine on propionic acid excretion in acute propionic acidaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Female; Humans; Infant; Injections, Intravenous; Propionates | 1984 |
Propionylcarnitine excretion in propionic and methylmalonic acidurias: a cause of carnitine deficiency.
Topics: Carnitine; Child, Preschool; Humans; Infant; Infant, Newborn; Malonates; Metabolism, Inborn Errors; Methylmalonic Acid; Muscles; Propionates | 1984 |
L-carnitine enhances excretion of propionyl coenzyme A as propionylcarnitine in propionic acidemia.
Topics: Acyl Coenzyme A; Adolescent; Carboxy-Lyases; Carnitine; Child; Child, Preschool; Humans; Infant; Male; Mass Spectrometry; Metabolism, Inborn Errors; Methylmalonyl-CoA Decarboxylase; Propionates | 1984 |
Urinary propionylcarnitine analysis for monitoring carnitine supplementation in inherited disorders of propionate metabolism.
Topics: Adolescent; Carnitine; Child; Child, Preschool; Female; Humans; Infant; Male; Metabolism, Inborn Errors; Propionates | 1994 |
Contrasting effects of propionate and propionyl-L-carnitine on energy-linked processes in ischemic hearts.
Topics: Animals; Cardiotonic Agents; Carnitine; Coenzyme A; Energy Metabolism; Esters; In Vitro Techniques; Male; Mitochondria, Heart; Myocardial Contraction; Myocardial Ischemia; Myocardial Reperfusion; Myocardium; Propionates; Rats; Rats, Wistar | 1994 |
Free carnitine and short-chain acylcarnitines in cerebrospinal fluid of patients with disorders of propionate metabolism determined by fast atom bombardment and tandem mass spectrometry.
Topics: Adolescent; Carnitine; Female; Humans; Infant; Mass Spectrometry; Metabolic Diseases; Propionates; Spectrometry, Mass, Fast Atom Bombardment | 1994 |
Quantification of free carnitine, individual short- and medium-chain acylcarnitines, and total carnitine in plasma by high-performance liquid chromatography.
Topics: Acetylcarnitine; Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Acylation; Carnitine; Chromatography, High Pressure Liquid; Humans; Methylmalonic Acid; Molecular Weight; Propionates; Reference Standards; Reproducibility of Results | 1993 |
Identification of undescribed medium-chain acylcarnitines present in urine of patients with propionic and methylmalonic acidemias.
Topics: Adult; Carboxy-Lyases; Carnitine; Case-Control Studies; Gas Chromatography-Mass Spectrometry; Humans; Infant; Lipid Metabolism, Inborn Errors; Male; Methylmalonic Acid; Methylmalonyl-CoA Decarboxylase; Propionates; Spectrometry, Mass, Fast Atom Bombardment | 2000 |
Rapid diagnosis of methylmalonic and propionic acidemias: quantitative tandem mass spectrometric analysis of propionylcarnitine in filter-paper blood specimens obtained from newborns.
Topics: Amino Acid Metabolism, Inborn Errors; Blood Specimen Collection; Carnitine; False Positive Reactions; Humans; Infant, Newborn; Methylmalonic Acid; Paper; Propionates; Spectrometry, Mass, Electrospray Ionization | 2001 |
Gas chromatographic-mass spectrometric newborn screening for propionic acidaemia by targeting methylcitrate in dried filter-paper urine samples.
Topics: Carboxy-Lyases; Carnitine; Citrates; DNA Mutational Analysis; Gas Chromatography-Mass Spectrometry; Homozygote; Humans; Infant, Newborn; Male; Mass Spectrometry; Methylmalonyl-CoA Decarboxylase; Mutation, Missense; Neonatal Screening; Paper; Propionates | 2002 |
Unexpectedly high prevalence of the mild form of propionic acidemia in Japan: presence of a common mutation and possible clinical implications.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Carboxy-Lyases; Carnitine; Child, Preschool; Citrates; DNA Mutational Analysis; DNA Primers; Exons; Humans; Infant; Japan; Methylmalonyl-CoA Decarboxylase; Mutation; Polymerase Chain Reaction; Polymorphism, Single-Stranded Conformational; Prevalence; Propionates; RNA, Messenger | 2002 |
Metabolomics identifies perturbations in human disorders of propionate metabolism.
Topics: Acetylcarnitine; Adult; Amino Acid Metabolism, Inborn Errors; Betaine; Biomarkers; Carnitine; Child; Chromatography, High Pressure Liquid; Humans; Methylmalonic Acid; Plasma; Propionates; Spectrometry, Mass, Electrospray Ionization | 2007 |