Page last updated: 2024-08-17

pivalic acid and carnitine

pivalic acid has been researched along with carnitine in 50 studies

Research

Studies (50)

TimeframeStudies, this research(%)All Research%
pre-19904 (8.00)18.7374
1990's26 (52.00)18.2507
2000's15 (30.00)29.6817
2010's5 (10.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Nezu, JI; Ohashi, R; Oku, A; Sai, Y; Shimane, M; Tamai, I; Tsuji, A; Yabuuchi, H1
Hashimoto, H; Konishi, M1
Konishi, M; Shimizu, K; Totsuka, K; Yamamoto, S1
Matsuno, S; Mizojiri, K; Nakashima, M; Oguma, T; Uematsu, T; Yamamoto, S; Yoshida, T1
Holme, E; Jodal, U; Linstedt, S; Nordin, I1
Bianchi, PB; Davis, AT2
Greter, J; Holme, E; Jacobson, CE; Jodal, U; Kristiansson, B; Lindstedt, S; Nordin, I1
Melegh, B1
Bieber, LL; Kerner, J; Melegh, B1
Arison, BH; Duncan, CA; Flynn, H; Ramjit, HG; Smith, JL; Vickers, S; Walker, RW; White, SD1
Christos, SC; DiDomenico, DF; Morris, GS; Paulson, DJ; Shug, AL; Wolf, BA; Zhou, Q1
Brørs, O; Bøhmer, T; Diep, QN1
Abrahamsson, K; Holme, E; Jodal, U; Lindstedt, S; Nordin, I1
Broderick, TL; DiDomenico, D; Paulson, DJ; Shug, AL1
Broderick, TL; Christos, SC; DiDomenico, D; Paulson, DJ; Shug, AL; Wolf, BA1
Bøhmer, T; Diep, QN1
Bøhmer, T; Diep, QN; Skrede, S1
Abrahamsson, K; Eriksson, BO; Holme, E; Jodal, U; Lindstedt, S; Nordin, I1
Chiba, S; Fujii, R; Meguro, H; Mori, A; Mori, T; Numazaki, K; Satoh, Y; Sunakawa, K; Terashima, I; Toyonaga, Y1
Melegh, B; Sherry, AD; Sumegi, B1
Fujita, Y; Hiraga, Y; Inamatsu, T; Nishikawa, T; Ohmichi, M; Saito, A; Shimada, J; Shimada, K; Shimizu, K; Tanimura, M1
Davis, AT1
Abrahamsson, K; Eriksson, BO; Holme, E; Jodal, U; Jönsson, A; Lindstedt, S; Mellander, M1
Broderick, TL; DiDomenico, D; Gamble, J; Lopaschuk, GD; Panagakis, G; Paulson, DJ; Shug, AL1
Inoue, F; Kinugasa, A; Kizaki, Z; Kodo, N; Nakajima, H; Nukina, S; Sawada, T1
Bianchi, PB; Davis, AT; Lehotay, DC1
Abrahamsson, K; Eriksson, BO; Holme, E; Jodal, U; Jönsson, A; Lindstedt, S1
Cooper, TG; Lewin, LM; Wang, XS; Yeung, CH1
Cooper, T; Fournier-Delpech, S; Golan, R; Lewin, LM; Pholpramool, C; Shochat, L; Weissenberg, R1
Bröer, A; Bröer, S; Kaltenbach, S; Lang, F; Lükewille, U; Moschen, I; Risler, T; Wagner, CA1
Arrigoni-Martelli, E; Caso, V1
Fujigaki, M; Komiya, I; Nakayoshi, T; Okudaira, N; Sugiyama, Y1
Arduini, A; Carminati, P; Ricciolini, R; Scalibastri, M1
Brass, EP1
Stanley, CA1
Davis, AT; Monroe, TJ1
Nakajima, Y; Nakamura, Y; Yamaguchi, T1
Broderick, TL1
Hasegawa, H; Norikura, R; Ohnishi, S; Okamura, N; Shimaoka, H1
Doberenz, J; Eder, K; Hirche, F; Keller, U1
Ito, T; Koyama, N; Makino, Y; Sugiura, T; Sugiyama, N1
Baba, T; Hasegawa, H; Horie, K; Kanaoka, E; Norikura, R; Ohnishi, S; Okamura, N; Sakamoto, K; Sakamoto, S; Takahashi, K1
Bodmer, M; Häussinger, D; Krähenbühl, S; Todesco, L; Vonwil, K1
Ito, T1
Djurhuus, H; Køber, L; Lund, AM; Nielsen, OW; Rasmussen, J1
Boemer, F; de Halleux, V; Debray, FG; Kalenga, M; Schoos, R1
Boemer, F; Dayaldasani, A; Rueda, I; Yahyaoui, R1
Kubota, M; Nasu, T; Suzuki, M; Uetake, K1
Fuchigami, T; Ishige, M; Ishige, N; Nakazaki, K; Ogawa, E; Takahashi, S1

Reviews

5 review(s) available for pivalic acid and carnitine

ArticleYear
Carnitine protects mitochondria and removes toxic acyls from xenobiotics.
    Drugs under experimental and clinical research, 2001, Volume: 27, Issue:1

    Topics: Acyl Coenzyme A; Ammonia; Animals; Anti-Bacterial Agents; Anti-HIV Agents; Antineoplastic Agents; Bacterial Toxins; Carnitine; Humans; Mitochondria; Pentanoic Acids; Peroxisome Proliferators; Valproic Acid; Xenobiotics

2001
Pivalate-generating prodrugs and carnitine homeostasis in man.
    Pharmacological reviews, 2002, Volume: 54, Issue:4

    Topics: Animals; Carnitine; Homeostasis; Humans; Pentanoic Acids; Prodrugs; Tissue Distribution

2002
Carnitine deficiency disorders in children.
    Annals of the New York Academy of Sciences, 2004, Volume: 1033

    Topics: Anti-Bacterial Agents; Carnitine; Child, Preschool; Fatty Acids; Humans; Mutation; Organic Cation Transport Proteins; Oxidation-Reduction; Pentanoic Acids; Solute Carrier Family 22 Member 5

2004
Hypocarnitinaemia induced by sodium pivalate in the rat is associated with left ventricular dysfunction and impaired energy metabolism.
    Drugs in R&D, 2006, Volume: 7, Issue:3

    Topics: Animals; Carnitine; Energy Metabolism; Models, Animal; Myocardium; Pentanoic Acids; Rats; Ventricular Dysfunction, Left

2006
Children's toxicology from bench to bed--Liver injury (1): Drug-induced metabolic disturbance--toxicity of 5-FU for pyrimidine metabolic disorders and pivalic acid for carnitine metabolism.
    The Journal of toxicological sciences, 2009, Volume: 34 Suppl 2

    Topics: Amidohydrolases; Animals; Anti-Bacterial Agents; Antineoplastic Agents; Carnitine; Cephalosporins; Child; Dihydropyrimidine Dehydrogenase Deficiency; Female; Fluorouracil; Humans; Intestinal Absorption; Pentanoic Acids; Purine-Pyrimidine Metabolism, Inborn Errors; Pyrimidines; Rats

2009

Trials

2 trial(s) available for pivalic acid and carnitine

ArticleYear
Phase I clinical studies of S-1108: safety and pharmacokinetics in a multiple-administration study with special emphasis on the influence on carnitine body stores.
    Antimicrobial agents and chemotherapy, 1992, Volume: 36, Issue:4

    Topics: Adult; Carnitine; Cephalosporins; Drug Administration Schedule; Drug Evaluation; Humans; Male; Pentanoic Acids; Tablets

1992
Impaired ketogenesis in carnitine depletion caused by short-term administration of pivalic acid prodrug.
    Biochemical medicine and metabolic biology, 1994, Volume: 52, Issue:1

    Topics: Adult; Amdinocillin Pivoxil; Carnitine; Fatty Acids; Fatty Acids, Nonesterified; Humans; Ketone Bodies; Liver; Male; Muscle, Skeletal; Oxidation-Reduction; Pentanoic Acids; Prodrugs

1994

Other Studies

43 other study(ies) available for pivalic acid and carnitine

ArticleYear
Na(+)-dependent carnitine transport by organic cation transporter (OCTN2): its pharmacological and toxicological relevance.
    The Journal of pharmacology and experimental therapeutics, 1999, Volume: 291, Issue:2

    Topics: Biological Transport, Active; Carnitine; Carrier Proteins; Cations; Cells, Cultured; Dose-Response Relationship, Drug; Embryo, Mammalian; Humans; Hydrogen-Ion Concentration; Kidney; Membrane Proteins; Organic Cation Transport Proteins; Sodium; Solute Carrier Family 22 Member 5; Stereoisomerism

1999
Determination of pivaloylcarnitine in human plasma and urine by high-performance liquid chromatography with fluorescence detection.
    Journal of pharmaceutical sciences, 1992, Volume: 81, Issue:10

    Topics: Calibration; Carnitine; Cephalosporins; Chromatography, High Pressure Liquid; Drug Stability; Humans; Pentanoic Acids; Prodrugs; Quinoxalines; Sensitivity and Specificity; Spectrometry, Fluorescence

1992
Metabolism of S-1108, a new oral cephem antibiotic, and metabolic profiles of its metabolites in humans.
    Antimicrobial agents and chemotherapy, 1992, Volume: 36, Issue:4

    Topics: Administration, Oral; Adult; Anti-Bacterial Agents; Carnitine; Cephalosporins; Humans; Male; Pentanoic Acids

1992
Effects of pivalic acid-containing prodrugs on carnitine homeostasis and on response to fasting in children.
    Scandinavian journal of clinical and laboratory investigation, 1992, Volume: 52, Issue:5

    Topics: Amdinocillin Pivoxil; Carnitine; Child; Child, Preschool; Fasting; Female; Homeostasis; Humans; Muscles; Pentanoic Acids; Pivampicillin; Prodrugs; Reference Values

1992
Sodium pivalate treatment reduces tissue carnitines and enhances ketosis in rats.
    The Journal of nutrition, 1991, Volume: 121, Issue:12

    Topics: Animals; Carnitine; Chromatography, High Pressure Liquid; Ketosis; Liver; Male; Pentanoic Acids; Rats; Rats, Inbred Strains; Tissue Distribution

1991
Carnitine deficiency induced by pivampicillin and pivmecillinam therapy.
    Lancet (London, England), 1989, Aug-26, Volume: 2, Issue:8661

    Topics: Adolescent; Adult; Amdinocillin; Amdinocillin Pivoxil; Ampicillin; Carnitine; Child; Child, Preschool; Chromatography, Gas; Chromatography, High Pressure Liquid; Drug Administration Schedule; Drug Evaluation; Drug Therapy, Combination; Female; Humans; Infant; Male; Mass Spectrometry; Muscles; Pentanoic Acids; Pivampicillin; Time Factors; Urinary Tract Infections

1989
Carnitine supplementation in pivampicillin treatment.
    Lancet (London, England), 1989, Nov-04, Volume: 2, Issue:8671

    Topics: Ampicillin; Carnitine; Child; Humans; Pentanoic Acids; Pivampicillin

1989
Pivampicillin-promoted excretion of pivaloylcarnitine in humans.
    Biochemical pharmacology, 1987, Oct-15, Volume: 36, Issue:20

    Topics: Acetylcarnitine; Adolescent; Ampicillin; Carnitine; Child; Female; Humans; Kidney; Male; Pentanoic Acids; Pivampicillin

1987
Carnitine and glucuronic acid conjugates of pivalic acid.
    Xenobiotica; the fate of foreign compounds in biological systems, 1985, Volume: 15, Issue:6

    Topics: Animals; Carnitine; Chromatography, Thin Layer; Glucuronates; Glucuronic Acid; Humans; Hydrolysis; Macaca fascicularis; Male; Methyldopa; Pentanoic Acids; Scintillation Counting; Spectrum Analysis; Valerates

1985
Sodium pivalate reduces cardiac carnitine content and increases glucose oxidation without affecting cardiac functional capacity.
    Life sciences, 1995, Volume: 57, Issue:24

    Topics: 3-Hydroxyacyl CoA Dehydrogenases; Animals; Carnitine; Citrate (si)-Synthase; Glucose; Heart; Hexokinase; Isoenzymes; Male; Myocardium; Myosins; Oxidation-Reduction; Pentanoic Acids; Rats; Rats, Sprague-Dawley

1995
Formation of pivaloylcarnitine in isolated rat heart cells.
    Biochimica et biophysica acta, 1995, Nov-16, Volume: 1259, Issue:2

    Topics: Acetylcarnitine; Animals; Betaine; Carnitine; Cells, Cultured; Kinetics; Myocardium; Pentanoic Acids; Pivampicillin; Rats; Rats, Wistar

1995
Effect of short-term treatment with pivalic acid containing antibiotics on serum carnitine concentration--a risk irrespective of age.
    Biochemical and molecular medicine, 1995, Volume: 55, Issue:1

    Topics: Adolescent; Adult; Age Factors; Aged; Amdinocillin Pivoxil; Carnitine; Female; Humans; Male; Middle Aged; Norfloxacin; Penicillins; Pentanoic Acids; Prodrugs; Risk Factors; Time Factors; Urinary Tract Infections

1995
L-propionylcarnitine effects on cardiac carnitine content and function in secondary carnitine deficiency.
    Canadian journal of physiology and pharmacology, 1995, Volume: 73, Issue:4

    Topics: Animals; Aorta; Blood Pressure; Cardiotonic Agents; Carnitine; Heart; Heart Rate; In Vitro Techniques; Male; Myocardium; Pentanoic Acids; Perfusion; Rats; Rats, Sprague-Dawley

1995
Fatty acid oxidation and cardiac function in the sodium pivalate model of secondary carnitine deficiency.
    Metabolism: clinical and experimental, 1995, Volume: 44, Issue:4

    Topics: Adenosine Triphosphate; Animals; Blood Glucose; Carnitine; Esters; Fatty Acids; Glucose; Heart; Lipids; Male; Myocardium; Oxidation-Reduction; Palmitates; Pentanoic Acids; Rats; Rats, Sprague-Dawley

1995
Increased pivaloylcarnitine in the liver of the sodium pivalate treated rat exposed to clofibrate.
    Biochimica et biophysica acta, 1995, May-17, Volume: 1256, Issue:2

    Topics: Adipose Tissue, Brown; Animals; Carnitine; Carnitine O-Acetyltransferase; Clofibrate; Heart; Liver; Male; Pentanoic Acids; Rats; Rats, Wistar; Triglycerides

1995
Formation of pivaloylcarnitine in heart and brown adipose tissue in the rat.
    Biochimica et biophysica acta, 1995, Jan-18, Volume: 1243, Issue:1

    Topics: Adipose Tissue, Brown; Animals; Carbon Radioisotopes; Carnitine; Chromatography, Gas; Isotope Labeling; Male; Myocardium; Pentanoic Acids; Rats; Rats, Wistar; Tissue Distribution

1995
[Effect of cefditoren pivoxil on carnitine metabolism in pediatric patients].
    The Japanese journal of antibiotics, 1993, Volume: 46, Issue:10

    Topics: Bacterial Infections; Carnitine; Cephalosporins; Child; Child, Preschool; Female; Humans; Infant; Male; Pentanoic Acids

1993
Preferential elimination of pivalate with supplemental carnitine via formation of pivaloylcarnitine in man.
    Xenobiotica; the fate of foreign compounds in biological systems, 1993, Volume: 23, Issue:11

    Topics: Adolescent; Carnitine; Child; Chromatography, Gas; Drug Interactions; Esters; Female; Humans; Magnetic Resonance Spectroscopy; Male; Pentanoic Acids; Pivampicillin

1993
Carnitine status and safety after administration of S-1108, a new oral cephem, to patients.
    Antimicrobial agents and chemotherapy, 1993, Volume: 37, Issue:5

    Topics: Administration, Oral; Adult; Aged; Aged, 80 and over; Bacterial Infections; Carnitine; Cephalosporins; Female; Humans; Kidney Diseases; Male; Middle Aged; Pentanoic Acids; Prodrugs

1993
Carnitine depletion in rat pups of lactating mothers given sodium pivalate.
    Biology of the neonate, 1995, Volume: 68, Issue:3

    Topics: Animals; Carnitine; Female; Lactation; Liver; Milk; Myocardium; Pentanoic Acids; Pregnancy; Rats; Rats, Sprague-Dawley; Tissue Distribution

1995
Transient reduction of human left ventricular mass in carnitine depletion induced by antibiotics containing pivalic acid.
    British heart journal, 1995, Volume: 74, Issue:6

    Topics: Adolescent; Adult; Amdinocillin Pivoxil; Anti-Bacterial Agents; Carnitine; Echocardiography; Female; Heart Septum; Humans; Male; Middle Aged; Muscle, Skeletal; Myocardium; Pentanoic Acids; Time Factors

1995
L-carnitine improvement of cardiac function is associated with a stimulation in glucose but not fatty acid metabolism in carnitine-deficient hearts.
    Cardiovascular research, 1995, Volume: 30, Issue:5

    Topics: Animals; Carnitine; Fatty Acids; Glucose; Glycolysis; Male; Myocardium; Oxidation-Reduction; Pentanoic Acids; Perfusion; Rats; Rats, Sprague-Dawley; Stimulation, Chemical

1995
Pivalate affects carnitine status but causes no severe metabolic changes in rat liver.
    The Journal of nutrition, 1996, Volume: 126, Issue:6

    Topics: 3-Hydroxybutyric Acid; Animals; Carnitine; Fatty Acids, Nonesterified; Gluconeogenesis; Heart; Hydroxybutyrates; Ketone Bodies; Lactates; Lactic Acid; Liver; Male; Muscles; Myocardium; Pentanoic Acids; Pyruvates; Pyruvic Acid; Rats; Rats, Wistar

1996
beta-Hydroxybutyrate oxidation is reduced and hepatic balance of ketone bodies and free fatty acids is unaltered in carnitine-depleted, pivalate-treated rats.
    The Journal of nutrition, 1996, Volume: 126, Issue:11

    Topics: 3-Hydroxybutyric Acid; Animals; Body Weight; Carbon Dioxide; Carbon Radioisotopes; Carnitine; Fatty Acids, Nonesterified; Female; Hydroxybutyrates; Ketone Bodies; Ketones; Liver; Male; Oxidation-Reduction; Pentanoic Acids; Rats; Rats, Sprague-Dawley

1996
Carnitine supplementation ameliorates the steatosis and ketosis induced by pivalate in rats.
    The Journal of nutrition, 1996, Volume: 126, Issue:11

    Topics: 3-Hydroxybutyric Acid; Animals; Carbonates; Carnitine; Dicarboxylic Acids; Fatty Acids; Food, Fortified; Hydroxybutyrates; Ketones; Lipid Metabolism; Liver; Male; Muscle, Skeletal; Myocardium; Oxidation-Reduction; Pentanoic Acids; Rats; Rats, Sprague-Dawley; Triglycerides; Weight Gain

1996
Pivalic acid-induced carnitine deficiency and physical exercise in humans.
    Metabolism: clinical and experimental, 1996, Volume: 45, Issue:12

    Topics: Adolescent; Adult; Amdinocillin Pivoxil; Blood Glucose; Carnitine; Exercise; Fatty Acids, Nonesterified; Female; Glycogen; Humans; Male; Middle Aged; Pentanoic Acids; Pivampicillin; Triglycerides

1996
Successful lowering of epididymal carnitine by administration of pivalate to rats.
    International journal of andrology, 1997, Volume: 20, Issue:3

    Topics: Animals; Carnitine; Epididymis; Female; Fertility; Kidney; Liver; Male; Myocardium; Ovariectomy; Pentanoic Acids; Rats; Sperm Motility; Time Factors; Water Supply

1997
Effects of pivalic acid and sodium pivalate on L-carnitine concentrations in the cauda epididymidis and on male fertility in the hamster.
    Reproduction, fertility, and development, 1997, Volume: 9, Issue:4

    Topics: Animals; Carnitine; Chromatin; Cricetinae; Epididymis; Fertility; Male; Mesocricetus; Pentanoic Acids; Sperm Motility

1997
Functional and pharmacological characterization of human Na(+)-carnitine cotransporter hOCTN2.
    American journal of physiology. Renal physiology, 2000, Volume: 279, Issue:3

    Topics: Amino Acids; Animals; Betaine; Biological Transport; Carnitine; Carrier Proteins; Emetine; Enzyme Inhibitors; Humans; Hydrogen-Ion Concentration; Lipotropic Agents; Membrane Potentials; Membrane Proteins; Microinjections; Oocytes; Organic Cation Transport Proteins; Patch-Clamp Techniques; Pentanoic Acids; Protein Synthesis Inhibitors; RNA, Complementary; Sodium; Solute Carrier Family 22 Member 5; Tetraethylammonium; Tritium; Valproic Acid; Xenopus laevis

2000
Up-regulation of carnitine transporters helps maintain tissue carnitine levels in carnitine deficiency induced by pivalic acid.
    Pharmaceutical research, 2001, Volume: 18, Issue:4

    Topics: Animals; Carnitine; Carrier Proteins; Injections, Intra-Arterial; Injections, Intravenous; Male; Organic Cation Transport Proteins; Pentanoic Acids; Rats; Rats, Sprague-Dawley; Solute Carrier Family 22 Member 5; Tissue Distribution; Up-Regulation

2001
The effect of pivalate treatment of pregnant rats on body mass and insulin levels in the adult offspring.
    Life sciences, 2001, Aug-31, Volume: 69, Issue:15

    Topics: 3-Hydroxybutyric Acid; Animals; Animals, Newborn; Blood Glucose; Carnitine; Female; Hyperinsulinism; Insulin; Insulin Resistance; Lactation; Male; Maternal-Fetal Exchange; Obesity; Pentanoic Acids; Pregnancy; Prodrugs; Rats; Triglycerides

2001
Carnitine deficiency and supplementation do not affect the gene expression of carnitine biosynthetic enzymes in rats.
    The Journal of nutrition, 2005, Volume: 135, Issue:4

    Topics: Animals; Carnitine; Dietary Supplements; gamma-Butyrobetaine Dioxygenase; Gene Expression Regulation; Kidney; Liver; Lysine; Male; Mixed Function Oxygenases; Pentanoic Acids; Rats; RNA, Messenger

2005
Possible mechanism for species difference on the toxicity of pivalic acid between dogs and rats.
    Toxicology and applied pharmacology, 2006, Jul-01, Volume: 214, Issue:1

    Topics: Acyl Coenzyme A; Animals; Anti-Bacterial Agents; Carnitine; Dogs; In Vitro Techniques; Kidney; Male; Mitochondria; Muscle, Skeletal; Pentanoic Acids; Rabbits; Rats; Rats, Sprague-Dawley; Species Specificity

2006
Involvement of recognition and interaction of carnitine transporter in the decrease of L-carnitine concentration induced by pivalic acid and valproic acid.
    Pharmaceutical research, 2006, Volume: 23, Issue:8

    Topics: Acetylcarnitine; Algorithms; Amino Acid Transport Systems, Basic; Animals; Biological Transport, Active; Carnitine; Carrier Proteins; Enzyme Inhibitors; LLC-PK1 Cells; Pentanoic Acids; Swine; Valproic Acid

2006
Pivalate lowers litter sizes and weights in female rats independent of its effect on carnitine status.
    Reproductive toxicology (Elmsford, N.Y.), 2007, Volume: 24, Issue:1

    Topics: Animals; Animals, Newborn; Body Weight; Carnitine; Female; Fertilization; Litter Size; Pentanoic Acids; Pregnancy; Rats; Rats, Sprague-Dawley; Vitamin B Deficiency

2007
Carnitine-associated encephalopathy caused by long-term treatment with an antibiotic containing pivalic acid.
    Pediatrics, 2007, Volume: 120, Issue:3

    Topics: Acidosis; Anti-Bacterial Agents; Brain Diseases, Metabolic; Carnitine; Cephalosporins; Humans; Hypoglycemia; Infant; Infusions, Intravenous; Male; Otitis Media; Pentanoic Acids; Seizures; Unconsciousness; Vitamin B Complex

2007
Role of Na+/L-carnitine transporter (OCTN2) in renal handling of pivaloylcarnitine and valproylcarnitine formed during pivalic acid-containing prodrugs and valproic acid treatment.
    Drug metabolism and pharmacokinetics, 2008, Volume: 23, Issue:4

    Topics: Animals; Carnitine; CHO Cells; Cricetinae; Cricetulus; Humans; Kidney; Male; Organic Cation Transport Proteins; Pentanoic Acids; Prodrugs; Rats; Rats, Sprague-Dawley; Sodium; Solute Carrier Family 22 Member 5; Valproic Acid

2008
Interaction between pivaloylcarnitine and L-carnitine transport into L6 cells overexpressing hOCTN2.
    Chemico-biological interactions, 2009, Aug-14, Volume: 180, Issue:3

    Topics: Animals; Biological Transport; Carnitine; Cell Line; Humans; Kinetics; Organic Cation Transport Proteins; Pentanoic Acids; Rats; Solute Carrier Family 22 Member 5

2009
Primary carnitine deficiency and pivalic acid exposure causing encephalopathy and fatal cardiac events.
    Journal of inherited metabolic disease, 2013, Volume: 36, Issue:1

    Topics: Adult; Anti-Bacterial Agents; Arrhythmias, Cardiac; Cardiomyopathies; Carnitine; Child, Preschool; Death, Sudden, Cardiac; Female; Humans; Hyperammonemia; Infant; Muscular Diseases; Pentanoic Acids; Retrospective Studies

2013
Surprising causes of C5-carnitine false positive results in newborn screening.
    Molecular genetics and metabolism, 2014, Volume: 111, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Belgium; Carnitine; False Positive Reactions; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Mass Spectrometry; Neonatal Screening; Ointments; Pentanoic Acids; Prodrugs; Risk Factors

2014
[C5-carnitine false positive results in newborn screening: what is the cause?].
    Medicina clinica, 2015, Feb-20, Volume: 144, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Biotransformation; Breast Feeding; Carnitine; Coenzyme A Ligases; Cosmetics; False Positive Reactions; Female; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Maternal-Fetal Exchange; Neonatal Screening; Ointments; Pentanoic Acids; Pregnancy; Tandem Mass Spectrometry

2015
Newborn hypocarnitinemia due to long-term transplacental pivalic acid passage.
    Pediatrics international : official journal of the Japan Pediatric Society, 2014, Volume: 56, Issue:5

    Topics: Carnitine; Female; Humans; Infant, Newborn; Male; Maternal-Fetal Exchange; Metabolism, Inborn Errors; Pentanoic Acids; Pregnancy; Time Factors

2014
Hypocarnitinemia Observed in an Infant Treated with Short-Term Administration of Antibiotic Containing Pivalic Acid.
    The Tohoku journal of experimental medicine, 2018, Volume: 244, Issue:4

    Topics: Anti-Bacterial Agents; Carbon; Carnitine; Humans; Hypoglycemia; Infant; Male; Metabolic Diseases; Oxygen; Pentanoic Acids; Tandem Mass Spectrometry

2018