phenylacetic acid and urea

phenylacetic acid has been researched along with urea in 16 studies

Research

Studies (16)

TimeframeStudies, this research(%)All Research%
pre-19904 (25.00)18.7374
1990's3 (18.75)18.2507
2000's7 (43.75)29.6817
2010's2 (12.50)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Barnes, JC; Bradley, P; Day, NC; Fourches, D; Reed, JZ; Tropsha, A1
Brusilow, SW1
Brusilow, SW; Rajantie, J; Simell, O; Sipilä, I; Valle, DL1
Batshaw, M; Brusilow, SW; Burton, B; Danney, M; Levitsky, L; McKeethren, C; Roth, K; Waber, LJ; Ward, J1
Batshaw, ML; Brusilow, SW1
Feillet, F; Leonard, JV1
Thoene, JG1
Boyadjiev, SA; Brusilow, SW; Geraghty, MT; Praphanphoj, V; Waber, LJ1
Summar, M1
Batshaw, ML; MacArthur, RB; Tuchman, M1
Shi, D; Thompson, MM; Tuchman, M; Yu, X1
CHITI, W; SELLERI, R1
Carter, S; Lee, B; O'Brien, WE; Scaglia, F1
Berry, GT; Berry, SA; Brusilow, SW; Enns, GM; Hamosh, A; Rhead, WJ1
Shih, VE1
Akula, VP; Alcorn, D; Benitz, WE; Bernstein, JA; Berquist, WE; Blumenfeld, YJ; Castillo, RO; Concepcion, W; Cowan, TM; Cox, KL; Cusmano, K; Enns, GM; Esquivel, CO; Hintz, SR; Homeyer, M; Hudgins, L; Hurwitz, M; Lyell, DJ; Palma, JP; Schelley, S; Summar, ML; Wilnai, Y1

Reviews

3 review(s) available for phenylacetic acid and urea

ArticleYear
Alternative pathway therapy for urea cycle disorders.
    Journal of inherited metabolic disease, 1998, Volume: 21 Suppl 1

    Topics: Amino Acid Metabolism, Inborn Errors; Animals; Arginine; Benzoates; Benzoic Acid; Child; Citrulline; Combined Modality Therapy; Female; Humans; Male; Nitrogen; Phenylacetates; Phenylbutyrates; Urea

1998
Treatment of urea cycle disorders.
    The Journal of pediatrics, 1999, Volume: 134, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Antimetabolites; Child, Preschool; Drug Combinations; Humans; Infant; Infant, Newborn; Ornithine Carbamoyltransferase Deficiency Disease; Phenylacetates; Sodium Benzoate; Urea

1999
Alternative pathway therapy for urea cycle disorders: twenty years later.
    The Journal of pediatrics, 2001, Volume: 138, Issue:1 Suppl

    Topics: Amino Acid Metabolism, Inborn Errors; Animals; Arginine; Humans; Hyperammonemia; Phenylacetates; Phenylbutyrates; Sodium Benzoate; Urea

2001

Trials

1 trial(s) available for phenylacetic acid and urea

ArticleYear
Survival after treatment with phenylacetate and benzoate for urea-cycle disorders.
    The New England journal of medicine, 2007, May-31, Volume: 356, Issue:22

    Topics: Adolescent; Adult; Age Factors; Age of Onset; Amino Acid Metabolism, Inborn Errors; Ammonia; Carbamoyl-Phosphate Synthase I Deficiency Disease; Child; Child, Preschool; Citrullinemia; Female; Humans; Hyperammonemia; Infant; Infant, Newborn; Male; Ornithine Carbamoyltransferase Deficiency Disease; Phenylacetates; Sodium Benzoate; Survival Analysis; Urea

2007

Other Studies

12 other study(ies) available for phenylacetic acid and urea

ArticleYear
Cheminformatics analysis of assertions mined from literature that describe drug-induced liver injury in different species.
    Chemical research in toxicology, 2010, Volume: 23, Issue:1

    Topics: Animals; Chemical and Drug Induced Liver Injury; Cluster Analysis; Databases, Factual; Humans; MEDLINE; Mice; Models, Chemical; Molecular Conformation; Quantitative Structure-Activity Relationship

2010
Phenylacetylglutamine may replace urea as a vehicle for waste nitrogen excretion.
    Pediatric research, 1991, Volume: 29, Issue:2

    Topics: Adolescent; Child; Child, Preschool; Female; Glutamine; Humans; Infant; Male; Metabolism, Inborn Errors; Nitrogen; Phenylacetates; Phenylbutyrates; Urea

1991
Waste nitrogen excretion via amino acid acylation: benzoate and phenylacetate in lysinuric protein intolerance.
    Pediatric research, 1986, Volume: 20, Issue:11

    Topics: Acylation; Alanine; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Benzoates; Benzoic Acid; Child; Child, Preschool; Creatinine; Glutamine; Hippurates; Humans; Lysine; Nitrogen; Orotic Acid; Phenylacetates; Urea

1986
Treatment of episodic hyperammonemia in children with inborn errors of urea synthesis.
    The New England journal of medicine, 1984, Jun-21, Volume: 310, Issue:25

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Argininosuccinate Synthase; Benzoates; Benzoic Acid; Carbamoyl-Phosphate Synthase (Ammonia); Drug Administration Schedule; Humans; Infant; Injections, Intravenous; Male; Ornithine Carbamoyltransferase Deficiency Disease; Parenteral Nutrition, Total; Phenylacetates; Renal Dialysis; Urea

1984
Evidence of lack of toxicity of sodium phenylacetate and sodium benzoate in treating urea cycle enzymopathies.
    Journal of inherited metabolic disease, 1981, Volume: 4, Issue:4

    Topics: Benzoates; Benzoic Acid; Child, Preschool; Female; Humans; Male; Metabolism, Inborn Errors; Phenylacetates; Urea

1981
Three cases of intravenous sodium benzoate and sodium phenylacetate toxicity occurring in the treatment of acute hyperammonaemia.
    Journal of inherited metabolic disease, 2000, Volume: 23, Issue:2

    Topics: Child; Child, Preschool; Drug Overdose; Fatal Outcome; Female; Humans; Injections, Intravenous; Male; Metabolism, Inborn Errors; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Phenylacetates; Quaternary Ammonium Compounds; Sodium Benzoate; Urea

2000
Current strategies for the management of neonatal urea cycle disorders.
    The Journal of pediatrics, 2001, Volume: 138, Issue:1 Suppl

    Topics: Algorithms; Amino Acid Metabolism, Inborn Errors; Antimetabolites, Antineoplastic; Arginine; Dialysis; Extracorporeal Membrane Oxygenation; Humans; Hyperammonemia; Infant, Newborn; Phenylacetates; Sodium Benzoate; Urea

2001
Quantification of benzoic, phenylacetic, and phenylbutyric acids from filter-paper blood spots by gas chromatography--mass spectrometry with stable isotope dilution.
    Clinical chemistry, 2001, Volume: 47, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Benzoic Acid; Blood Specimen Collection; Deuterium; Gas Chromatography-Mass Spectrometry; Humans; Indicator Dilution Techniques; Paper; Phenylacetates; Phenylbutyrates; Propionates; Urea

2001
[Relation between chemical structure and local anesthetic action; tertiary alkylamine derivatives of barbituric acid, urea & phenyl-ethylacetic acid].
    Il Farmaco; edizione scientifica, 1957, Volume: 12, Issue:7

    Topics: Analgesia; Anesthesia; Anesthesia and Analgesia; Anesthesia, Local; Anesthetics, Local; Barbiturates; Phenylacetates; Urea

1957
Effect of alternative pathway therapy on branched chain amino acid metabolism in urea cycle disorder patients.
    Molecular genetics and metabolism, 2004, Volume: 81 Suppl 1

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Citrullinemia; Drug Therapy, Combination; Female; Humans; Male; Ornithine Carbamoyltransferase Deficiency Disease; Phenylacetates; Phenylbutyrates; Retrospective Studies; Sodium Benzoate; Time Factors; Urea

2004
Alternative-pathway therapy for hyperammonemia.
    The New England journal of medicine, 2007, May-31, Volume: 356, Issue:22

    Topics: Amino Acid Metabolism, Inborn Errors; Humans; Hyperammonemia; Phenylacetates; Sodium Benzoate; Urea

2007
Prenatal treatment of ornithine transcarbamylase deficiency.
    Molecular genetics and metabolism, 2018, Volume: 123, Issue:3

    Topics: Ammonia; Drug Combinations; Female; Glutamine; Humans; Hyperammonemia; Infant, Newborn; Male; Mutation; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Phenylacetates; Pregnancy; Prenatal Care; Prenatal Diagnosis; Sodium Benzoate; Treatment Outcome; Urea

2018