ornithine has been researched along with orotic acid in 48 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 36 (75.00) | 18.7374 |
1990's | 8 (16.67) | 18.2507 |
2000's | 3 (6.25) | 29.6817 |
2010's | 1 (2.08) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
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DeMars, R; LeVan, SL; Russell, LB; Trend, BL | 1 |
Alfant, M; Crandall, DE; Knott, CE; Tremblay, GS | 1 |
Gerok, W; Keppler, DO; Pausch, JG | 1 |
Visek, WJ | 1 |
Ha, YH; Milner, JA | 1 |
Hatchwell, LC; Milner, JA | 1 |
Glasgow, AM | 1 |
Brandt, JT; Fausto, N; Kesner, L | 1 |
Milner, JA; Visek, WJ | 1 |
Beaudry, MA; Collu, R; Dallairf, L; Ducharme, JR; Leboeuf, G; Letarte, J; Melancon, SB | 1 |
Daune, G; Gerhart, F; Grauffel, C; Seiler, N | 1 |
Alonso, E; Rubio, V | 1 |
Maswoswe, SM; Tremblay, GC | 1 |
Zieve, L | 1 |
Bachmann, C; Colombo, JP; Dionisi Vici, C; Gambarara, M; Sabetta, G | 1 |
Barth, CA; de Vrese, M | 1 |
Morris, JG | 1 |
Clow, CL; Mackenzie, S; Scriver, CR; Simell, O | 1 |
Ord, MG; Stocken, LA | 1 |
Dallman, PR; Siimes, MA | 1 |
Cihak, A; Pitot, HC; Wilkinson, D | 1 |
Szám, I | 1 |
Fausto, N | 2 |
Ord, MG; Stocken, LA; Thrower, S | 1 |
Freeman, JM; Levy, HL; Lindenbaum, JE; Sunshine, P | 1 |
Anakura, M; Arashima, S; Matsuda, I; Nambu, H; Takekoshi, Y | 1 |
Cerra, FB; Goodman, MW; Konstantinides, FN; Zieve, L | 1 |
Baker, DH; Czarnecki, GL | 1 |
Blanding, JH; Tremblay, GC; Wendler, PA | 1 |
Kubota, K; Murakami, T; Yamashita, F; Yoshida, I; Yoshino, M | 1 |
Daune-Anglard, G; Grauffel, C; Knödgen, B; Sarhan, S; Seiler, N | 1 |
Hartman, WJ; Prior, RL; Torre, PM | 1 |
Nelson, J; Qureshi, IA; Sarma, DS; Vasudevan, S | 1 |
Donati, MA; Filippi, L; Resti, M; Zammarchi, E | 1 |
de Martinville, B; Demmer, LA; Dowton, SB; Kim, JM | 1 |
Fukushige, T; Kakinoki, H; Kobayashi, K; Saheki, T | 1 |
Celli, M; Crifò, C; D'Eufemia, P; Finocchiaro, R; Giardini, O; Salerno, C | 1 |
Sass, JO; Skladal, D | 1 |
AMSTEY, M; BROWN, O; MCCARTY, KS; WOODSON, B | 1 |
NOVELLI, GD; TAYLOR, WH | 1 |
PERAINO, C; PITOT, HC | 1 |
KESNER, L | 1 |
COHEN, PP; KIM, S | 1 |
Berger, R; Besley, GT; Cleary, MA; de Koning, TJ; Dorland, L; Duran, M; Mandell, R; Olpin, SE; Poll-The, BT; Shih, VE | 1 |
Blanke, CD; Chan, JS; Harding, CO | 1 |
Amaral, AU; Dutra Filho, CS; Ferreira, Gda C; Knebel, LA; Schuck, PF; Tonin, AM; Viegas, CM; Wajner, M; Wannmacher, CM; Zanatta, A | 1 |
Auray-Blais, C; Lavoie, P; Maranda, B | 1 |
4 review(s) available for ornithine and orotic acid
Article | Year |
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Ammonia metabolism, urea cycle capacity and their biochemical assessment.
Topics: Amino Acids; Ammonia; Animals; Arginine; Brain; Citric Acid Cycle; Humans; Nutritional Requirements; Ornithine; Orotic Acid; Polyamines; Quaternary Ammonium Compounds; Urea | 1979 |
Conditional deficiencies of ornithine or arginine.
Topics: Amino Acids; Amino Acids, Branched-Chain; Ammonia; Animals; Arginine; Citrulline; Female; Glycine; Hepatic Encephalopathy; Humans; Liver Cirrhosis; Lysine; Models, Biological; Ornithine; Orotic Acid; Pregnancy; Protein Deficiency; Urease | 1986 |
The effect of pyrimidine analogues and tryptophan on enzyme synthesis and degradation in rat liver.
Topics: Adrenalectomy; Animals; Carbon Isotopes; Caseins; Centrifugation, Density Gradient; Cortisone; Cytidine; Dactinomycin; Enzyme Induction; Fluorine; L-Serine Dehydratase; Leucine; Liver; Lyases; Male; Nucleoproteins; Nucleosides; Ornithine; Orotic Acid; Phenylpyruvic Acids; Protein Hydrolysates; Pyrimidines; Rats; Ribosomes; RNA; Time Factors; Transaminases; Triazines; Tritium; Tryptophan; Tryptophan Oxygenase; Tyrosine Transaminase | 1970 |
[Hyperammoniemia and its treatment].
Topics: Ammonia; Arginine; Aspartic Acid; Humans; Ketoglutaric Acids; Liver; Malates; Metabolism, Inborn Errors; Ornithine; Orotic Acid | 1973 |
44 other study(ies) available for ornithine and orotic acid
Article | Year |
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Abnormal ornithine carbamoyltransferase in mice having the sparse-fur mutation.
Topics: Alleles; Animals; Female; Genes; Genetic Linkage; Heterozygote; Hydrogen-Ion Concentration; Male; Mice; Mutation; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Phenotype; Sex Chromosomes; Urinary Bladder Calculi | 1976 |
Orotic acid biosynthesis in rat liver: studies on the source of carbamoylphosphate.
Topics: Ammonia; Ammonium Chloride; Animals; Bicarbonates; Carbamates; Carbamoyl-Phosphate Synthase (Ammonia); Carbamyl Phosphate; Carbon Radioisotopes; Glutamine; Liver; Mitochondria, Liver; Ornithine; Orotic Acid; Phosphotransferases; Putrescine; Rats | 1977 |
Increased de novo pyrimidine nucleotide synthesis in liver induced by ammonium ions in amounts surpassing the urea cycle capacity.
Topics: Animals; Azauridine; Carbamoyl-Phosphate Synthase (Ammonia); Carbamoyl-Phosphate Synthase (Glutamine-Hydrolyzing); Carcinoma, Hepatocellular; Cytosine Nucleotides; Dose-Response Relationship, Drug; Female; Liver; Liver Neoplasms; Mitochondria, Liver; Models, Biological; Ornithine; Orotic Acid; Pyrimidine Nucleotides; Quaternary Ammonium Compounds; Rats; Uracil Nucleotides; Urea; Uridine Diphosphate Glucose | 1977 |
Urea cycle operation in the arginine deficient rat.
Topics: Ammonia; Animals; Arginase; Arginine; Argininosuccinate Lyase; Argininosuccinate Synthase; Carbamoyl-Phosphate Synthase (Glutamine-Hydrolyzing); Citrulline; Liver; Male; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Rats; Urea | 1979 |
Amino acid induced orotic aciduria.
Topics: Amino Acids; Ammonia; Animal Nutritional Physiological Phenomena; Animals; Arginine; Fasting; Male; Ornithine; Orotic Acid; Quaternary Ammonium Compounds; Rats; Urea; Urease | 1978 |
Potential hazard of therapy for Reye's syndrome with urea cycle intermediates.
Topics: Ammonia; Humans; Ornithine; Orotic Acid; Reye Syndrome; Urea | 1977 |
Possible interactions between the urea cycle and synthesis of pyrimidines and polyamines in regenerating liver.
Topics: Adrenalectomy; Ammonia; Animals; Bicarbonates; Carbon Radioisotopes; Carboxy-Lyases; Hepatectomy; Liver; Liver Regeneration; Male; Ornithine; Orotic Acid; Polyamines; Pyrimidines; Rats; Urea; Urease | 1975 |
Urinary metabolites characteristic of urea-cycle amino acid deficiency.
Topics: Amino Acids; Amino Acids, Essential; Ammonia; Animal Nutritional Physiological Phenomena; Animals; Arginine; Biotransformation; Body Weight; Carbamyl Phosphate; Citrates; Citrulline; Deficiency Diseases; Diet; Male; Nitrogen; Ornithine; Orotic Acid; Pyrimidines; Rats; Urea | 1975 |
[Chronic hyperammonemia with orotic aciduria: evidence of pyrimidine pathway stimulation (author's transl)].
Topics: Alanine; Amino Acids; Ammonia; Child, Preschool; Dietary Proteins; Erythrocytes; Growth Disorders; Humans; Intellectual Disability; Leukocytes; Ornithine; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Orotate Phosphoribosyltransferase; Orotic Acid; Orotidine-5'-Phosphate Decarboxylase; Purine-Pyrimidine Metabolism, Inborn Errors; Pyrimidines; Seizures; Syndrome; Urea | 1975 |
Ornithine aminotransferase activity, liver ornithine concentration and acute ammonia intoxication.
Topics: Acetates; Administration, Oral; Ammonia; Animals; Arginine; Creatinine; Eflornithine; Female; Injections, Intraperitoneal; Liver; Mice; Ornithine; Ornithine-Oxo-Acid Transaminase; Orotic Acid; Transaminases; Urea | 1989 |
Orotic aciduria due to arginine deprivation: changes in the levels of carbamoyl phosphate and of other urea cycle intermediates in mouse liver.
Topics: Animals; Arginine; Body Weight; Carbamates; Carbamyl Phosphate; Citrulline; Diet; Glutamates; Liver; Male; Mice; Mice, Inbred Strains; Ornithine; Orotic Acid | 1989 |
Biosynthesis of hippurate, urea and pyrimidines in the fatty liver: studies with rats fed orotic acid or a diet deficient in choline and inositol, and with genetically obese (Zucker) rats.
Topics: Ammonium Chloride; Animals; Benzoates; Choline Deficiency; Diet; Fatty Liver; Gluconeogenesis; Hippurates; Inositol; Liver; Obesity; Ornithine; Orotic Acid; Pyrimidines; Rats; Rats, Inbred Strains; Rats, Zucker; Urea | 1989 |
Hyperornithinemia-hyperammonemia-homocitrullinuria syndrome: low creatine excretion and effect of citrulline, arginine, or ornithine supplement.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Child, Preschool; Citrulline; Creatine; Female; Humans; Lysine; Male; Ornithine; Orotic Acid; Syndrome | 1987 |
Influence of lysine on urea cycle activity and orotate formation in the isolated perfused rat liver.
Topics: Ammonia; Animals; In Vitro Techniques; Kinetics; Liver; Lysine; Male; Ornithine; Orotic Acid; Perfusion; Rats; Rats, Inbred Strains; Urea | 1985 |
Nutritional and metabolic responses to arginine deficiency in carnivores.
Topics: Aging; Animal Nutritional Physiological Phenomena; Animals; Arginine; Carnivora; Cats; Citrulline; Dogs; Glutamine; Intestinal Mucosa; Kidney; Liver; Muscles; Nutritional Requirements; Ornithine; Ornithine-Oxo-Acid Transaminase; Orotic Acid; Rats; Species Specificity; Urea | 1985 |
Ornithine loading did not prevent induced hyperammonemia in a patient with hyperornithinemia-hyperammonemia-homocitrullinuria syndrome.
Topics: Alanine; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Child; Citrulline; Cytoplasm; Humans; Male; Ornithine; Orotic Acid; Syndrome | 1985 |
Uptake of amino acids and nucleic acid precursors by regenerating rat liver.
Topics: Adenine; Adrenalectomy; Amino Acids; Animals; Dactinomycin; Hepatectomy; Liver; Liver Regeneration; Lysine; Male; Ornithine; Orotic Acid; Phenylalanine; Rats; RNA; Thymidine; Tritium; Tyrosine; Uridine; Valine | 1972 |
Nucleic acid and polyamine synthesis in the rat during short-term protein deficiency: responsiveness of the liver to partial hepatectomy.
Topics: Animal Nutritional Physiological Phenomena; Animals; Bone Marrow; Carbon Radioisotopes; Carboxy-Lyases; Dietary Proteins; DNA; Female; Hepatectomy; Liver; Liver Regeneration; Organ Size; Ornithine; Orotic Acid; Phosphotransferases; Polyamines; Protein Deficiency; Rats; RNA; Thymidine Kinase; Time Factors; Tritium; Uridine | 1974 |
RNA metabolism in isolated perfused normal and regenerating livers: polyamine effects.
Topics: Amino Acids; Animals; Carbon Isotopes; Carboxy-Lyases; Cell Nucleus; Centrifugation, Density Gradient; Cytoplasm; Enzyme Activation; Hepatectomy; In Vitro Techniques; Liver; Liver Regeneration; Ornithine; Orotic Acid; Perfusion; Polyribosomes; Rats; RNA; Spermidine | 1972 |
Effects of phenoxybenzamine on early stages of liver regeneration in partially hepatectomized rats.
Topics: Adrenal Glands; Adrenalectomy; Animals; Carboxy-Lyases; Cell Nucleus; DNA; Enzyme Induction; Hepatectomy; Histones; Hydrogen-Ion Concentration; Liver; Liver Regeneration; Male; Ornithine; Orotic Acid; Phenoxybenzamine; Phosphorus Radioisotopes; Protein Kinase Inhibitors; Rats; RNA, Messenger; Thymidine; Time Factors; Transcription, Genetic | 1973 |
Hyperammonemia due to a defect in hepatic ornithine transcarbamylase.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Central Nervous System Diseases; Child; Child Behavior Disorders; Citrates; Coma; Diet Therapy; Dietary Proteins; Female; Gastrointestinal Diseases; Guanidines; Humans; Liver; Male; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Succinates; Urea | 1972 |
Hyperammonemia due to a mutant enzyme of ornithine transcarbamylase.
Topics: Amino Acids; Ammonia; Animals; Autopsy; Clinical Enzyme Tests; Culture Techniques; Female; Humans; Infant; Liver; Metabolism, Inborn Errors; Mutation; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Phosphotransferases; Rats; Threonine; Urea | 1971 |
Studies on ornithine decarboxylase activity in normal and regenerating livers.
Topics: Acetates; Amides; Amino Acids; Animals; Carbon Dioxide; Carbon Isotopes; Carboxy-Lyases; Caseins; Dactinomycin; Hepatectomy; Liver; Liver Regeneration; Male; Ornithine; Orotic Acid; Puromycin; Radiation Effects; Rats; Ribosomes; RNA; Time Factors | 1969 |
Mechanism of arginine protection against ammonia intoxication in the rat.
Topics: Acetyltransferases; Amino-Acid N-Acetyltransferase; Ammonia; Animals; Arginine; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Male; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Rats; Rats, Inbred Strains; Urea | 1984 |
Urea cycle function in the dog with emphasis on the role of arginine.
Topics: Age Factors; Ammonia; Animals; Arginine; Blood Glucose; Citrulline; Dogs; Ornithine; Orotic Acid; Urea; Vomiting | 1984 |
Interaction between the urea cycle and the orotate pathway: studies with isolated hepatocytes.
Topics: Ammonia; Animals; Carbamoyl-Phosphate Synthase (Ammonia); Catalysis; In Vitro Techniques; Ligases; Liver; Male; Ornithine; Orotic Acid; Pyrimidines; Rats; Rats, Inbred Strains; Urea | 1983 |
Argininemia: report of a new case and mechanisms of orotic aciduria and hyperammonemia.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Child, Preschool; Female; Humans; Hyperargininemia; Ornithine; Orotic Acid; Purine-Pyrimidine Metabolism, Inborn Errors; Urea | 1982 |
Decreased hyperammonaemia and orotic aciduria due to inactivation of ornithine aminotransferase in mice with a hereditary abnormal ornithine carbamoyltransferase.
Topics: Amino Acids; Ammonia; Animals; Behavior, Animal; Female; Male; Metabolism, Inborn Errors; Mice; Mice, Mutant Strains; Mutation; Ornithine; Ornithine Carbamoyltransferase; Ornithine-Oxo-Acid Transaminase; Orotic Acid | 1994 |
Dietary citrulline but not ornithine counteracts dietary arginine deficiency in rats by increasing splanchnic release of citrulline.
Topics: Alanine; Amino Acids; Ammonia; Animals; Arginine; Blood Flow Velocity; Body Weight; Citrulline; Creatinine; Diet; Food; Glutamic Acid; Glutamine; Male; Ornithine; Orotic Acid; Proline; Rats; Rats, Sprague-Dawley; Splanchnic Circulation; Urea | 1994 |
The effects of various inhibitors on the regulation of orotic acid excretion in sparse-fur mutant mice (spf/Y) deficient in ornithine transcarbamylase.
Topics: Adenine; Animals; Antimetabolites; Aspartic Acid; Creatinine; Cycloheximide; Injections, Intraperitoneal; Isoxazoles; Liver; Male; Mice; Mice, Mutant Strains; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Phosphonoacetic Acid | 1993 |
Cryptogenic hepatitis masking the diagnosis of ornithine transcarbamylase deficiency.
Topics: Absorption; Ammonia; Arginine; Child, Preschool; Citrulline; Diagnosis, Differential; Dietary Proteins; Female; Glutamine; Hepatitis; Humans; Infant; Lysine; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Urea | 1996 |
A novel missense mutation in the exon containing the putative ornithine-binding domain of the OTC enzyme in a female.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Binding Sites; Child, Preschool; Codon, Terminator; DNA Probes; Exons; Female; Humans; Mutation; Ornithine; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid | 1996 |
No increase of ornithine concentration in the liver of ornithine transcarbamylase-deficient spf-ash mice following intraperitoneal injection of ammonium chloride.
Topics: Ammonia; Ammonium Chloride; Animals; Arginine; Citrulline; Liver; Mice; Mice, Inbred Strains; Mice, Transgenic; Ornithine; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Peptones | 1997 |
Determination of urinary orotic acid and uracil by capillary zone electrophoresis.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Borates; Buffers; Citrulline; Dietary Proteins; Electrophoresis, Capillary; Humans; Hydrogen-Ion Concentration; Infant; Male; Ornithine; Orotic Acid; Syndrome; Uracil | 1999 |
Plasma concentrations and renal clearance of orotic acid in argininosuccinic acid synthetase deficiency.
Topics: Amino Acids; Arginine; Child; Chromatography, Gas; Citrulline; Citrullinemia; Creatinine; Glutamine; Humans; Male; Ornithine; Orotic Acid; Quaternary Ammonium Compounds; Time Factors | 1999 |
ARGININE AS A PRECURSOR OF PYRIMIDINES IN STRAIN L-929 FIBROBLASTS INFECTED WITH PLEUROPNEUMONIA-LIKE ORGANISMS.
Topics: Arginase; Arginine; Aspartic Acid; Carbamates; Carbon Isotopes; Connective Tissue; Fibroblasts; Glutamine; Ligases; Metabolism; Mycoplasma; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Phosphates; Phosphotransferases; Proline; Proteins; Pyrimidines; Research; Thymidine; Tissue Culture Techniques; Uracil; Urea; Ureohydrolases | 1964 |
ENZYMES OF THE PYRIMIDINE PATHWAY IN ESCHERICHIA COLI. I. SYNTHESIS BY CELLS AND SPHEROPLASTS.
Topics: Amino Acids; Chloramphenicol; Edetic Acid; Escherichia coli; Nucleotides; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Oxidoreductases; Pharmacology; Pyrimidines; Research; Spheroplasts; Sucrose; Transferases; Uracil | 1964 |
STUDIES ON THE INDUCTION AND REPRESSION OF ENZYMES IN RAT LIVER. I. INDUCTION OF THREONINE DEHYDRASE AND ORNITHINE-DELTA-TRANSAMINASE BY ORAL INTUBATION OF CASEIN HYDROLYSATE.
Topics: Adrenalectomy; Caseins; Dactinomycin; Hydro-Lyases; Intubation; Liver; Ornithine; Orotic Acid; Pharmacology; Protein Hydrolysates; Puromycin; Rats; Research; Threonine; Threonine Dehydratase; Transaminases | 1964 |
THE EFFECT OF AMMONIA ADMINISTRATION ON OROTIC ACID EXCRETION IN RATS.
Topics: Ammonia; Ammonium Chloride; Antimetabolites; Arginine; Chromatography; Citrulline; Diet; Glutamine; Ornithine; Orotic Acid; Pharmacology; Rats; Research; Succinates; Urine | 1965 |
TRANSCARBAMYLASE ACTIVITY IN FETAL LIVER AND IN LIVER OF PARTIALLY HEPATECTOMIZED PARABIOTIC RATS.
Topics: Cell Division; Enzyme Precursors; Erythrocyte Count; Fetus; Guinea Pigs; Hepatectomy; Ligases; Liver; Liver Diseases; Liver Regeneration; Nucleosides; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Parabiosis; Pyrimidines; Rats; Research; Transferases; Uracil; Urea; Uridine | 1965 |
Ornithine aminotransferase deficiency: diagnostic difficulties in neonatal presentation.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Diagnosis, Differential; Female; Fibroblasts; Glutamine; Humans; Hyperammonemia; Infant, Newborn; Male; Mutation; Neonatal Screening; Ornithine; Ornithine-Oxo-Acid Transaminase; Orotic Acid | 2005 |
Postchemotherapy hyperammonemic encephalopathy emulating ornithine transcarbamoylase (OTC) deficiency.
Topics: Adult; Arginine; Carcinoma, Hepatocellular; Citrulline; Female; Glutamine; Hepatic Encephalopathy; Humans; Hyperammonemia; Liver Neoplasms; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Polymorphism, Single-Stranded Conformational; Syndrome | 2008 |
Experimental evidence that ornithine and homocitrulline disrupt energy metabolism in brain of young rats.
Topics: Analysis of Variance; Animals; Cerebral Cortex; Citric Acid Cycle; Citrulline; Creatine Kinase; Cytosol; Electron Transport Chain Complex Proteins; In Vitro Techniques; Mitochondria; Ornithine; Orotic Acid; Oxygen Consumption; Rats; Sodium-Potassium-Exchanging ATPase; Spectrophotometry; Synaptic Membranes | 2009 |
High-throughput tandem mass spectrometry multiplex analysis for newborn urinary screening of creatine synthesis and transport disorders, Triple H syndrome and OTC deficiency.
Topics: Biomarkers; Creatine; Creatinine; Filtration; Glycine; Humans; Hyperammonemia; Infant, Newborn; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Paper; Reference Values; Reproducibility of Results; Tandem Mass Spectrometry; Uracil; Urea Cycle Disorders, Inborn; Urinalysis | 2014 |