n-isovalerylglycine has been researched along with valerates in 8 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 8 (100.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 0 (0.00) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Dembure, P; Elsas, L; Madsen, K; Naglak, M; Salvo, R | 1 |
Goodman, SI; Hack, AM; Hine, DG; Tanaka, K | 1 |
Inoue, F; Maltby, DA; Millington, DS; Roe, CR | 1 |
Audenaert, SM; Squillaro, EJ; Wilson, WG | 1 |
Hine, DG; Tanaka, K | 1 |
Batenburg-Plenter, AM; Bruinvis, L; Duran, M; Ketting, D; van Pelt, BC; Wadman, SK | 1 |
Inoue, Y; Kameyama, J; Momoi, T; Shigematsu, Y; Sudo, M; Suzuki, Y | 1 |
Bakkeren, JA; Houben, ML; Ruitenbeek, W; Sengers, RC; Trijbels, JM; Van der Zeè, SP | 1 |
8 other study(ies) available for n-isovalerylglycine and valerates
Article | Year |
---|---|
The treatment of isovaleric acidemia with glycine supplement.
Topics: Carbon Dioxide; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates | 1988 |
Stable isotope dilution analysis of isovalerylglycine in amniotic fluid and urine and its application for the prenatal diagnosis of isovaleric acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Amniotic Fluid; Female; Gas Chromatography-Mass Spectrometry; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Risk; Valerates | 1986 |
Endogenous catabolism is the major source of toxic metabolites in isovaleric acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Dietary Proteins; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates | 1987 |
Hyperammonaemia in a preterm infant with isovaleric acidaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Female; Glycine; Hemiterpenes; Humans; Infant, Newborn; Infant, Premature; Pentanoic Acids; Valerates | 1984 |
The identification and the excretion pattern of isovaleryl glucuronide in the urine of patients with isovaleric acidemia.
Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Chromatography, Gas; Gas Chromatography-Mass Spectrometry; Glucuronates; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates | 1984 |
Isovaleric acidaemia presenting with dwarfism, cataract and congenital abnormalities.
Topics: Abnormalities, Multiple; Amino Acid Metabolism, Inborn Errors; Cataract; Child; Dwarfism; Female; Glycine; Hemiterpenes; Humans; Intellectual Disability; Pentanoic Acids; Valerates | 1982 |
Changing plasma and urinary organic acid levels in a patient with isovaleric acidemia during an attack.
Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Hydroxybutyrates; Leucine; Pentanoic Acids; Valerates | 1982 |
[Isovaleric acidemia: identical biochemical picture in 3 patients with variable clinical manifestations].
Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Oxidation-Reduction; Pentanoic Acids; Valerates | 1982 |