n-isovalerylglycine has been researched along with glycine in 19 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 10 (52.63) | 18.7374 |
1990's | 5 (26.32) | 18.2507 |
2000's | 1 (5.26) | 29.6817 |
2010's | 2 (10.53) | 24.3611 |
2020's | 1 (5.26) | 2.80 |
Authors | Studies |
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Dan, M; Fujioka, M; Kanaoka, H; Kikawa, Y; Shigematsu, Y; Sudo, M | 1 |
Dembure, P; Elsas, L; Madsen, K; Naglak, M; Salvo, R | 1 |
Goodman, SI; Hack, AM; Hine, DG; Tanaka, K | 1 |
Inoue, F; Maltby, DA; Millington, DS; Roe, CR | 1 |
Christensen, E; Gregersen, N; Kølvraa, S | 1 |
Audenaert, SM; Squillaro, EJ; Wilson, WG | 1 |
Hine, DG; Tanaka, K | 1 |
Batenburg-Plenter, AM; Bruinvis, L; Duran, M; Ketting, D; van Pelt, BC; Wadman, SK | 1 |
Inoue, Y; Kameyama, J; Momoi, T; Shigematsu, Y; Sudo, M; Suzuki, Y | 1 |
Bakkeren, JA; Houben, ML; Ruitenbeek, W; Sengers, RC; Trijbels, JM; Van der Zeè, SP | 1 |
Brandt, NJ; Gregersen, N; Kølvraa, S | 1 |
Chiba, T; Ito, T; Kajita, M; Kidouchi, K; Niwa, T; Sugiyama, N; Wada, Y | 1 |
Fries, MH; Jurecki, E; Packman, S; Rinaldo, P; Schmidt-Sommerfeld, E | 1 |
Bykov, IL; Shigematsu, E | 1 |
Kimura, M; Yamaguchi, S | 1 |
Amaral, AU; De Bortoli, GM; Dutra-Filho, CS; Fernandes, CG; Latini, AS; Leipnitz, G; Seminotti, B; Solano, AF; Wajner, M | 1 |
Hata, I; Shigematsu, Y; Tajima, G | 1 |
Aldamiz-Echevarría, L; Barros, P; Belanger-Quintana, A; Blasco, J; Bueno, MA; Couce, ML; Fernández-Marmiesse, A; García-Silva, MT; Márquez-Armenteros, AM; Navarrete, R; Pérez, B; Pérez-Cerdá, C; Vitoria, I; Vives, I | 1 |
Bansal, N; Chen, Y; Feldman, HI; Go, AS; Heckbert, SR; Hoofnagle, AN; Hsu, CY; Huber, MP; Kestenbaum, BR; Lash, JP; Mehta, RC; Paranji, RK; Porter, AC; Raj, DS; Seliger, SL; Srivastava, A; Waikar, SS; Wang, K; Weiss, NS; Zelnick, LR | 1 |
19 other study(ies) available for n-isovalerylglycine and glycine
Article | Year |
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Prenatal diagnosis of isovaleric acidemia by fast atom bombardment and tandem mass spectrometry.
Topics: Amniotic Fluid; Carnitine; Female; Fetal Diseases; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Spectrometry, Mass, Fast Atom Bombardment | 1991 |
The treatment of isovaleric acidemia with glycine supplement.
Topics: Carbon Dioxide; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates | 1988 |
Stable isotope dilution analysis of isovalerylglycine in amniotic fluid and urine and its application for the prenatal diagnosis of isovaleric acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Amniotic Fluid; Female; Gas Chromatography-Mass Spectrometry; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Risk; Valerates | 1986 |
Endogenous catabolism is the major source of toxic metabolites in isovaleric acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Dietary Proteins; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates | 1987 |
In vivo studies on the metabolic derangement in a patient with D-glyceric acidaemia and hyperglycinaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Carbohydrate Dehydrogenases; Child, Preschool; Diet; Fructose; Glyceric Acids; Glycine; Humans; Male; Proline; Propionates; Riboflavin; Serine | 1984 |
Hyperammonaemia in a preterm infant with isovaleric acidaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Female; Glycine; Hemiterpenes; Humans; Infant, Newborn; Infant, Premature; Pentanoic Acids; Valerates | 1984 |
The identification and the excretion pattern of isovaleryl glucuronide in the urine of patients with isovaleric acidemia.
Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Chromatography, Gas; Gas Chromatography-Mass Spectrometry; Glucuronates; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates | 1984 |
Isovaleric acidaemia presenting with dwarfism, cataract and congenital abnormalities.
Topics: Abnormalities, Multiple; Amino Acid Metabolism, Inborn Errors; Cataract; Child; Dwarfism; Female; Glycine; Hemiterpenes; Humans; Intellectual Disability; Pentanoic Acids; Valerates | 1982 |
Changing plasma and urinary organic acid levels in a patient with isovaleric acidemia during an attack.
Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Hydroxybutyrates; Leucine; Pentanoic Acids; Valerates | 1982 |
[Isovaleric acidemia: identical biochemical picture in 3 patients with variable clinical manifestations].
Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Oxidation-Reduction; Pentanoic Acids; Valerates | 1982 |
Excretion of short-chain N-acylglycines in the urine of a patient with D-glyceric acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Butyrates; Caproates; Caprylates; Child, Preschool; Glyceric Acids; Glycine; Humans; Hydrolysis; Models, Chemical | 1980 |
Liquid chromatographic-atmospheric pressure chemical ionization mass spectrometric analysis of glycine conjugates and urinary isovalerylglycine in isovaleric acidemia.
Topics: Acidosis; Administration, Oral; Carnitine; Child, Preschool; Chromatography, Liquid; Female; Glucuronates; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Male; Mass Spectrometry; Pentanoic Acids | 1995 |
Isovaleric acidemia: response to a leucine load after three weeks of supplementation with glycine, L-carnitine, and combined glycine-carnitine therapy.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids | 1996 |
[Effect of l-carnitine on the expression of glycine conjugates in rats in experimental B2-hypovitaminosis].
Topics: Animals; Carnitine; Glycine; Rats; Rats, Wistar; Riboflavin Deficiency | 1997 |
Screening for fatty acid beta oxidation disorders. Acylglycine analysis by electron impact ionization gas chromatography-mass spectrometry.
Topics: Dicarboxylic Acids; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Lipid Metabolism, Inborn Errors; Reference Standards | 1999 |
Induction of oxidative stress by the metabolites accumulating in isovaleric acidemia in brain cortex of young rats.
Topics: Animals; Cerebral Cortex; Free Radical Scavengers; Glutathione; Glycine; Hemiterpenes; Lipid Peroxidation; Metabolism, Inborn Errors; Mitochondria; Oxidative Stress; Pentanoic Acids; Protein Carbonylation; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances | 2008 |
Useful second-tier tests in expanded newborn screening of isovaleric acidemia and methylmalonic aciduria.
Topics: Amino Acid Metabolism, Inborn Errors; Biomarkers; Blood Specimen Collection; Carnitine; Case-Control Studies; Chromatography, Liquid; False Positive Reactions; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Japan; Lactic Acid; Metabolism, Inborn Errors; Methylmalonic Acid; Neonatal Screening; Pilot Projects; Predictive Value of Tests; Retrospective Studies; Severity of Illness Index; Tandem Mass Spectrometry | 2010 |
Genotype and phenotype characterization in a Spanish cohort with isovaleric acidemia.
Topics: Acute Disease; Amino Acid Metabolism, Inborn Errors; Asymptomatic Diseases; Carnitine; Child; Child, Preschool; Chronic Disease; Creatinine; Female; Fibroblasts; Gene Expression; Genetic Association Studies; Genotype; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Male; Mutation; Neonatal Screening; Pentanoic Acids; Phenotype; Prevalence; Spain | 2017 |
Association Between Kidney Clearance of Secretory Solutes and Cardiovascular Events: The Chronic Renal Insufficiency Cohort (CRIC) Study.
Topics: Aged; Albuminuria; Chromatography, Liquid; Cohort Studies; Cresols; Female; Glomerular Filtration Rate; Glycine; Heart Failure; Humans; Incidence; Indican; Kidney Tubules; Kynurenic Acid; Male; Middle Aged; Myocardial Infarction; Organic Anion Transporters; Proportional Hazards Models; Prospective Studies; Pyridoxic Acid; Renal Insufficiency, Chronic; Ribonucleosides; Stroke; Sulfuric Acid Esters; Tandem Mass Spectrometry; Xanthines | 2021 |