Page last updated: 2024-08-26

n-isovalerylglycine and glycine

n-isovalerylglycine has been researched along with glycine in 19 studies

Research

Studies (19)

TimeframeStudies, this research(%)All Research%
pre-199010 (52.63)18.7374
1990's5 (26.32)18.2507
2000's1 (5.26)29.6817
2010's2 (10.53)24.3611
2020's1 (5.26)2.80

Authors

AuthorsStudies
Dan, M; Fujioka, M; Kanaoka, H; Kikawa, Y; Shigematsu, Y; Sudo, M1
Dembure, P; Elsas, L; Madsen, K; Naglak, M; Salvo, R1
Goodman, SI; Hack, AM; Hine, DG; Tanaka, K1
Inoue, F; Maltby, DA; Millington, DS; Roe, CR1
Christensen, E; Gregersen, N; Kølvraa, S1
Audenaert, SM; Squillaro, EJ; Wilson, WG1
Hine, DG; Tanaka, K1
Batenburg-Plenter, AM; Bruinvis, L; Duran, M; Ketting, D; van Pelt, BC; Wadman, SK1
Inoue, Y; Kameyama, J; Momoi, T; Shigematsu, Y; Sudo, M; Suzuki, Y1
Bakkeren, JA; Houben, ML; Ruitenbeek, W; Sengers, RC; Trijbels, JM; Van der Zeè, SP1
Brandt, NJ; Gregersen, N; Kølvraa, S1
Chiba, T; Ito, T; Kajita, M; Kidouchi, K; Niwa, T; Sugiyama, N; Wada, Y1
Fries, MH; Jurecki, E; Packman, S; Rinaldo, P; Schmidt-Sommerfeld, E1
Bykov, IL; Shigematsu, E1
Kimura, M; Yamaguchi, S1
Amaral, AU; De Bortoli, GM; Dutra-Filho, CS; Fernandes, CG; Latini, AS; Leipnitz, G; Seminotti, B; Solano, AF; Wajner, M1
Hata, I; Shigematsu, Y; Tajima, G1
Aldamiz-Echevarría, L; Barros, P; Belanger-Quintana, A; Blasco, J; Bueno, MA; Couce, ML; Fernández-Marmiesse, A; García-Silva, MT; Márquez-Armenteros, AM; Navarrete, R; Pérez, B; Pérez-Cerdá, C; Vitoria, I; Vives, I1
Bansal, N; Chen, Y; Feldman, HI; Go, AS; Heckbert, SR; Hoofnagle, AN; Hsu, CY; Huber, MP; Kestenbaum, BR; Lash, JP; Mehta, RC; Paranji, RK; Porter, AC; Raj, DS; Seliger, SL; Srivastava, A; Waikar, SS; Wang, K; Weiss, NS; Zelnick, LR1

Other Studies

19 other study(ies) available for n-isovalerylglycine and glycine

ArticleYear
Prenatal diagnosis of isovaleric acidemia by fast atom bombardment and tandem mass spectrometry.
    Clinica chimica acta; international journal of clinical chemistry, 1991, Dec-16, Volume: 203, Issue:2-3

    Topics: Amniotic Fluid; Carnitine; Female; Fetal Diseases; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Spectrometry, Mass, Fast Atom Bombardment

1991
The treatment of isovaleric acidemia with glycine supplement.
    Pediatric research, 1988, Volume: 24, Issue:1

    Topics: Carbon Dioxide; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1988
Stable isotope dilution analysis of isovalerylglycine in amniotic fluid and urine and its application for the prenatal diagnosis of isovaleric acidemia.
    Pediatric research, 1986, Volume: 20, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Amniotic Fluid; Female; Gas Chromatography-Mass Spectrometry; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Risk; Valerates

1986
Endogenous catabolism is the major source of toxic metabolites in isovaleric acidemia.
    The Journal of pediatrics, 1987, Volume: 110, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Dietary Proteins; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates

1987
In vivo studies on the metabolic derangement in a patient with D-glyceric acidaemia and hyperglycinaemia.
    Journal of inherited metabolic disease, 1984, Volume: 7, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Carbohydrate Dehydrogenases; Child, Preschool; Diet; Fructose; Glyceric Acids; Glycine; Humans; Male; Proline; Propionates; Riboflavin; Serine

1984
Hyperammonaemia in a preterm infant with isovaleric acidaemia.
    Journal of inherited metabolic disease, 1984, Volume: 7, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Female; Glycine; Hemiterpenes; Humans; Infant, Newborn; Infant, Premature; Pentanoic Acids; Valerates

1984
The identification and the excretion pattern of isovaleryl glucuronide in the urine of patients with isovaleric acidemia.
    Pediatric research, 1984, Volume: 18, Issue:6

    Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Chromatography, Gas; Gas Chromatography-Mass Spectrometry; Glucuronates; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates

1984
Isovaleric acidaemia presenting with dwarfism, cataract and congenital abnormalities.
    Journal of inherited metabolic disease, 1982, Volume: 5, Issue:2

    Topics: Abnormalities, Multiple; Amino Acid Metabolism, Inborn Errors; Cataract; Child; Dwarfism; Female; Glycine; Hemiterpenes; Humans; Intellectual Disability; Pentanoic Acids; Valerates

1982
Changing plasma and urinary organic acid levels in a patient with isovaleric acidemia during an attack.
    Pediatric research, 1982, Volume: 16, Issue:9

    Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Hydroxybutyrates; Leucine; Pentanoic Acids; Valerates

1982
[Isovaleric acidemia: identical biochemical picture in 3 patients with variable clinical manifestations].
    Tijdschrift voor kindergeneeskunde, 1982, Volume: 50, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Oxidation-Reduction; Pentanoic Acids; Valerates

1982
Excretion of short-chain N-acylglycines in the urine of a patient with D-glyceric acidemia.
    Clinica chimica acta; international journal of clinical chemistry, 1980, Sep-25, Volume: 106, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Butyrates; Caproates; Caprylates; Child, Preschool; Glyceric Acids; Glycine; Humans; Hydrolysis; Models, Chemical

1980
Liquid chromatographic-atmospheric pressure chemical ionization mass spectrometric analysis of glycine conjugates and urinary isovalerylglycine in isovaleric acidemia.
    Journal of chromatography. B, Biomedical applications, 1995, Aug-18, Volume: 670, Issue:2

    Topics: Acidosis; Administration, Oral; Carnitine; Child, Preschool; Chromatography, Liquid; Female; Glucuronates; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Male; Mass Spectrometry; Pentanoic Acids

1995
Isovaleric acidemia: response to a leucine load after three weeks of supplementation with glycine, L-carnitine, and combined glycine-carnitine therapy.
    The Journal of pediatrics, 1996, Volume: 129, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids

1996
[Effect of l-carnitine on the expression of glycine conjugates in rats in experimental B2-hypovitaminosis].
    Voprosy pitaniia, 1997, Issue:6

    Topics: Animals; Carnitine; Glycine; Rats; Rats, Wistar; Riboflavin Deficiency

1997
Screening for fatty acid beta oxidation disorders. Acylglycine analysis by electron impact ionization gas chromatography-mass spectrometry.
    Journal of chromatography. B, Biomedical sciences and applications, 1999, Aug-06, Volume: 731, Issue:1

    Topics: Dicarboxylic Acids; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Lipid Metabolism, Inborn Errors; Reference Standards

1999
Induction of oxidative stress by the metabolites accumulating in isovaleric acidemia in brain cortex of young rats.
    Free radical research, 2008, Volume: 42, Issue:8

    Topics: Animals; Cerebral Cortex; Free Radical Scavengers; Glutathione; Glycine; Hemiterpenes; Lipid Peroxidation; Metabolism, Inborn Errors; Mitochondria; Oxidative Stress; Pentanoic Acids; Protein Carbonylation; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances

2008
Useful second-tier tests in expanded newborn screening of isovaleric acidemia and methylmalonic aciduria.
    Journal of inherited metabolic disease, 2010, Volume: 33, Issue:Suppl 2

    Topics: Amino Acid Metabolism, Inborn Errors; Biomarkers; Blood Specimen Collection; Carnitine; Case-Control Studies; Chromatography, Liquid; False Positive Reactions; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Japan; Lactic Acid; Metabolism, Inborn Errors; Methylmalonic Acid; Neonatal Screening; Pilot Projects; Predictive Value of Tests; Retrospective Studies; Severity of Illness Index; Tandem Mass Spectrometry

2010
Genotype and phenotype characterization in a Spanish cohort with isovaleric acidemia.
    Journal of human genetics, 2017, Volume: 62, Issue:3

    Topics: Acute Disease; Amino Acid Metabolism, Inborn Errors; Asymptomatic Diseases; Carnitine; Child; Child, Preschool; Chronic Disease; Creatinine; Female; Fibroblasts; Gene Expression; Genetic Association Studies; Genotype; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Male; Mutation; Neonatal Screening; Pentanoic Acids; Phenotype; Prevalence; Spain

2017
Association Between Kidney Clearance of Secretory Solutes and Cardiovascular Events: The Chronic Renal Insufficiency Cohort (CRIC) Study.
    American journal of kidney diseases : the official journal of the National Kidney Foundation, 2021, Volume: 78, Issue:2

    Topics: Aged; Albuminuria; Chromatography, Liquid; Cohort Studies; Cresols; Female; Glomerular Filtration Rate; Glycine; Heart Failure; Humans; Incidence; Indican; Kidney Tubules; Kynurenic Acid; Male; Middle Aged; Myocardial Infarction; Organic Anion Transporters; Proportional Hazards Models; Prospective Studies; Pyridoxic Acid; Renal Insufficiency, Chronic; Ribonucleosides; Stroke; Sulfuric Acid Esters; Tandem Mass Spectrometry; Xanthines

2021