Page last updated: 2024-08-26

n-isovalerylglycine and carnitine

n-isovalerylglycine has been researched along with carnitine in 7 studies

Research

Studies (7)

TimeframeStudies, this research(%)All Research%
pre-19901 (14.29)18.7374
1990's4 (57.14)18.2507
2000's0 (0.00)29.6817
2010's2 (28.57)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Dan, M; Fujioka, M; Kanaoka, H; Kikawa, Y; Shigematsu, Y; Sudo, M1
Inoue, F; Maltby, DA; Millington, DS; Roe, CR1
Chiba, T; Ito, T; Kajita, M; Kidouchi, K; Niwa, T; Sugiyama, N; Wada, Y1
Fries, MH; Jurecki, E; Packman, S; Rinaldo, P; Schmidt-Sommerfeld, E1
Bykov, IL; Shigematsu, E1
Hata, I; Shigematsu, Y; Tajima, G1
Aldamiz-Echevarría, L; Barros, P; Belanger-Quintana, A; Blasco, J; Bueno, MA; Couce, ML; Fernández-Marmiesse, A; García-Silva, MT; Márquez-Armenteros, AM; Navarrete, R; Pérez, B; Pérez-Cerdá, C; Vitoria, I; Vives, I1

Other Studies

7 other study(ies) available for n-isovalerylglycine and carnitine

ArticleYear
Prenatal diagnosis of isovaleric acidemia by fast atom bombardment and tandem mass spectrometry.
    Clinica chimica acta; international journal of clinical chemistry, 1991, Dec-16, Volume: 203, Issue:2-3

    Topics: Amniotic Fluid; Carnitine; Female; Fetal Diseases; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Spectrometry, Mass, Fast Atom Bombardment

1991
Endogenous catabolism is the major source of toxic metabolites in isovaleric acidemia.
    The Journal of pediatrics, 1987, Volume: 110, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Dietary Proteins; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates

1987
Liquid chromatographic-atmospheric pressure chemical ionization mass spectrometric analysis of glycine conjugates and urinary isovalerylglycine in isovaleric acidemia.
    Journal of chromatography. B, Biomedical applications, 1995, Aug-18, Volume: 670, Issue:2

    Topics: Acidosis; Administration, Oral; Carnitine; Child, Preschool; Chromatography, Liquid; Female; Glucuronates; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Male; Mass Spectrometry; Pentanoic Acids

1995
Isovaleric acidemia: response to a leucine load after three weeks of supplementation with glycine, L-carnitine, and combined glycine-carnitine therapy.
    The Journal of pediatrics, 1996, Volume: 129, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids

1996
[Effect of l-carnitine on the expression of glycine conjugates in rats in experimental B2-hypovitaminosis].
    Voprosy pitaniia, 1997, Issue:6

    Topics: Animals; Carnitine; Glycine; Rats; Rats, Wistar; Riboflavin Deficiency

1997
Useful second-tier tests in expanded newborn screening of isovaleric acidemia and methylmalonic aciduria.
    Journal of inherited metabolic disease, 2010, Volume: 33, Issue:Suppl 2

    Topics: Amino Acid Metabolism, Inborn Errors; Biomarkers; Blood Specimen Collection; Carnitine; Case-Control Studies; Chromatography, Liquid; False Positive Reactions; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Japan; Lactic Acid; Metabolism, Inborn Errors; Methylmalonic Acid; Neonatal Screening; Pilot Projects; Predictive Value of Tests; Retrospective Studies; Severity of Illness Index; Tandem Mass Spectrometry

2010
Genotype and phenotype characterization in a Spanish cohort with isovaleric acidemia.
    Journal of human genetics, 2017, Volume: 62, Issue:3

    Topics: Acute Disease; Amino Acid Metabolism, Inborn Errors; Asymptomatic Diseases; Carnitine; Child; Child, Preschool; Chronic Disease; Creatinine; Female; Fibroblasts; Gene Expression; Genetic Association Studies; Genotype; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Male; Mutation; Neonatal Screening; Pentanoic Acids; Phenotype; Prevalence; Spain

2017