monomethyl succinate has been researched along with ethylmalonic acid in 12 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 3 (25.00) | 18.7374 |
| 1990's | 3 (25.00) | 18.2507 |
| 2000's | 2 (16.67) | 29.6817 |
| 2010's | 3 (25.00) | 24.3611 |
| 2020's | 1 (8.33) | 2.80 |
| Authors | Studies |
|---|---|
| Amendt, BA; Cloherty, J; Greene, C; Moon, A; Rhead, WJ; Shih, V; Sweetman, L; Teel, L | 1 |
| Mamer, OA; Montgomery, JA; Scriver, CR | 1 |
| Cyr, D; Giguère, R; Leblanc, D; Mitchell, G; Qureshi, IA | 1 |
| Blaser, SI; Clarke, JT; Nowaczyk, MJ | 1 |
| Clarke, JT; Fisher, L; Lehotay, DC; Nowaczyk, MJ; Phillips, H; Platt, BA; Tan, R | 1 |
| Balestri, P; Berardi, R; Dionisi-Vici, C; Farnetani, MA; Grosso, S; Molinelli, M; Morgese, G; Mostardini, R; Rizzo, C | 1 |
| Gordon, N | 1 |
| Bierau, J; Dorland, L; Schoonderwoerd, K; van der Kolk, JH; van Diggelen, OP; Waterham, HR; Westermann, CM | 1 |
| Abdenur, JE; Barshop, BA; Cederbaum, SD; Chang, E; Deignan, JL; Dorrani, N; Feuchtbaum, L; Gallant, NM; Leydiker, K; Lorey, F; Neidich, J; Puckett, R; Tang, H; Wang, RY | 1 |
| Cheon, CK; Kim, GH; Kim, YM; Ko, JM; Lee, KA; Park, KH; Park, S; Yoo, HW | 1 |
| Friss, T; Gray, K; Guven, A; Kellogg, MD; Kiebish, MA; Klotz, A; Narain, NR; Peng, KW; Ravipaty, S; Sarangarajan, R; Tolstikov, V | 1 |
| Amendt, BA; Armstrong, D; Inoue, F; Millington, DS; Rhead, WJ; Wood, PA | 1 |
12 other study(ies) available for monomethyl succinate and ethylmalonic acid
| Article | Year |
|---|---|
Short-chain acyl-coenzyme A dehydrogenase deficiency. Clinical and biochemical studies in two patients.
Topics: 3-Hydroxybutyric Acid; Acyl-CoA Dehydrogenases; Adipates; Adult; Butyrates; Butyric Acid; Female; Fibroblasts; Humans; Hydroxybutyrates; Lactates; Lactic Acid; Lipid Metabolism, Inborn Errors; Malonates; Succinates | 1987 |
Metabolism of ethylmalonate to mesaconate in the rat. Evidence for trans-dehydrogenation of methylsuccinate.
Topics: Animals; Chemical Phenomena; Chemistry; Maleates; Malonates; Rats; Rats, Inbred Strains; Succinates | 1983 |
Breeding experiments to combine the X-linked sparse-fur (spf) mutation with the autosomal recessive BALB/cByJ strain: testing the biochemical phenotype of double-mutant mice as a model for ammonia: fatty acyl CoA synergism.
Topics: Acyl Coenzyme A; Acyl-CoA Dehydrogenases; Ammonia; Animals; Butyryl-CoA Dehydrogenase; Crosses, Genetic; Female; Genes, Recessive; Genetic Linkage; Glycine; Hair; Male; Malonates; Mice; Mice, Inbred BALB C; Mice, Mutant Strains; Mutation; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Phenotype; Succinates; X Chromosome | 1993 |
Central nervous system malformations in ethylmalonic encephalopathy.
Topics: Abnormalities, Multiple; Brain; Child, Preschool; Female; Growth Disorders; Humans; Magnetic Resonance Imaging; Male; Malonates; Metabolism, Inborn Errors; Spine; Succinates | 1998 |
Ethylmalonic and methylsuccinic aciduria in ethylmalonic encephalopathy arise from abnormal isoleucine metabolism.
Topics: Administration, Oral; Brain; Cells, Cultured; Child, Preschool; Female; Fibroblasts; Glycine; Humans; Isoleucine; Malonates; Metabolism, Inborn Errors; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Succinates | 1998 |
Ethylmalonic encephalopathy: further clinical and neuroradiological characterization.
Topics: Brain Diseases, Metabolic, Inborn; Female; Humans; Infant; Magnetic Resonance Imaging; Malonates; Muscles; Prostaglandin-Endoperoxide Synthases; Radiography; Succinates | 2002 |
Acyl-CoA dehydrogenase deficiency: varieties with neurological involvement.
Topics: Acyl-CoA Dehydrogenase; Carnitine; Child; Child, Preschool; Chromosome Aberrations; Developmental Disabilities; Diagnosis, Differential; Electron-Transferring Flavoproteins; Female; Genes, Recessive; Genetic Variation; Humans; Hypoglycemia; Infant; Infant, Newborn; Male; Malonates; Mass Spectrometry; Metabolism, Inborn Errors; Neonatal Screening; Nervous System Diseases; Pregnancy; Prenatal Diagnosis; Prognosis; Succinates; Sudden Infant Death | 2005 |
Decreased oxidative phosphorylation and PGAM deficiency in horses suffering from atypical myopathy associated with acquired MADD.
Topics: Animals; Aspartate Aminotransferases; Base Sequence; Creatine; Creatine Kinase; DNA Primers; Female; Horse Diseases; Horses; L-Lactate Dehydrogenase; Malonates; Mitochondrial Proton-Translocating ATPases; Molecular Sequence Data; Multiple Acyl Coenzyme A Dehydrogenase Deficiency; Oxidative Phosphorylation; Phosphoglycerate Mutase; Physical Conditioning, Animal; Rhabdomyolysis; Sequence Analysis, DNA; Succinates; Uric Acid | 2011 |
Biochemical, molecular, and clinical characteristics of children with short chain acyl-CoA dehydrogenase deficiency detected by newborn screening in California.
Topics: Acyl Coenzyme A; Acyl-CoA Dehydrogenase; California; Carnitine; Female; Follow-Up Studies; Humans; Infant, Newborn; Lipid Metabolism, Inborn Errors; Male; Malonates; Neonatal Screening; Sequence Deletion; Succinates | 2012 |
Novel and Recurrent ACADS Mutations and Clinical Manifestations Observed in Korean Patients with Short-chain Acyl-coenzyme a Dehydrogenase Deficiency.
Topics: Acyl-CoA Dehydrogenase; Asian People; Child; Child, Preschool; Disease Progression; Female; Follow-Up Studies; Humans; Infant; Lipid Metabolism, Inborn Errors; Male; Malonates; Mutation; Republic of Korea; Succinates; Treatment Outcome | 2016 |
Multiplexed LC-MS/MS analysis of methylsuccinic acid, ethylmalonic acid, and glutaric acid in plasma and urine.
Topics: Chromatography, Liquid; Glutarates; Malonates; Spectrometry, Mass, Electrospray Ionization; Succinates; Tandem Mass Spectrometry | 2022 |
Short-chain acyl-coenzyme A dehydrogenase deficiency in mice.
Topics: Acyl-CoA Dehydrogenase; Animals; Carnitine; Disease Models, Animal; Fatty Acid Desaturases; Fatty Acids; Fatty Acids, Volatile; Gas Chromatography-Mass Spectrometry; Glycine; Malonates; Mice; Mice, Inbred BALB C; Oxidation-Reduction; Succinates | 1989 |