Page last updated: 2024-08-23

miglustat and migalastat

miglustat has been researched along with migalastat in 10 studies

Research

Studies (10)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's2 (20.00)18.2507
2000's4 (40.00)29.6817
2010's3 (30.00)24.3611
2020's1 (10.00)2.80

Authors

AuthorsStudies
Aerts, JM; Bijl, N; Boot, RG; Copeland, D; Ghauharali, K; Groen, AK; Groener, JE; Liu, H; Meijer, AJ; O'Shea, TJ; Ottenhoff, R; Overkleeft, HS; Song, H; van den Berg, RJ; van der Marel, GA; van Eijk, M; Wennekes, T; Yew, N1
Benjamin, ER; Boyd, RE; Khanna, R; Lee, G; Rybczynski, P; Valenzano, KJ; Wustman, BA1
Block, T; Butters, T; Dwek, R; Lu, X; Mehta, A1
Butters, TD; Dwek, RA; Karlsson, GB; Neises, GR; Platt, FM1
Andersson, U; Butters, TD; Dwek, RA; Platt, FM1
Butters, TD; Dwek, RA; Platt, FM; Suganuma, R; van der Spoel, AC; Walden, CM; Yanagimachi, R1
Brady, RO1
Butters, TD; d'Azzo, A; Dwek, RA; Elliot-Smith, E; Jeyakumar, M; Lloyd-Evans, E; Platt, FM; Smith, DA; Speak, AO; van der Spoel, AC1
Andreotti, G; Cubellis, MV; Monticelli, M1
D'Alonzo, D; Dechecchi, MC; Esposito, A; Fenza, M; Gregorio, E; Guaragna, A; Lippi, G; Tamanini, A1

Reviews

3 review(s) available for miglustat and migalastat

ArticleYear
Pharmacological chaperones as therapeutics for lysosomal storage diseases.
    Journal of medicinal chemistry, 2013, Apr-11, Volume: 56, Issue:7

    Topics: Cell Line; Glycolipids; Humans; Lysosomal Storage Diseases; Molecular Chaperones; Structure-Activity Relationship

2013
Emerging strategies for the treatment of hereditary metabolic storage disorders.
    Rejuvenation research, 2006,Summer, Volume: 9, Issue:2

    Topics: 1-Deoxynojirimycin; Bone Marrow Transplantation; Enzyme Inhibitors; Fabry Disease; Gangliosidosis, GM1; Gaucher Disease; Genetic Therapy; Humans; Imino Sugars; Piperidines

2006
Synthesis and Therapeutic Applications of Iminosugars in Cystic Fibrosis.
    International journal of molecular sciences, 2020, May-09, Volume: 21, Issue:9

    Topics: 1-Deoxynojirimycin; Anti-Inflammatory Agents; Cystic Fibrosis; Cystic Fibrosis Transmembrane Conductance Regulator; Glycoside Hydrolases; Glycosyltransferases; Heterocyclic Compounds, 1-Ring; Humans; Imino Pyranoses; Inflammation; Molecular Structure; Mutation; Sequence Deletion; Tartrates

2020

Other Studies

7 other study(ies) available for miglustat and migalastat

ArticleYear
Dual-action lipophilic iminosugar improves glycemic control in obese rodents by reduction of visceral glycosphingolipids and buffering of carbohydrate assimilation.
    Journal of medicinal chemistry, 2010, Jan-28, Volume: 53, Issue:2

    Topics: Absorption; Animals; Blood Glucose; Carbohydrate Metabolism; Glycated Hemoglobin; Glycosphingolipids; Imino Sugars; Mice; Mice, Obese; Obesity; Rats; Rats, Zucker; Structure-Activity Relationship; Viscera

2010
Evidence that N-linked glycosylation is necessary for hepatitis B virus secretion.
    Virology, 1995, Nov-10, Volume: 213, Issue:2

    Topics: 1-Deoxynojirimycin; alpha-Glucosidases; Base Sequence; DNA Primers; Enzyme Inhibitors; Glycoside Hydrolase Inhibitors; Glycosylation; Hepatitis B Surface Antigens; Hepatitis B virus; Humans; Molecular Sequence Data; Tumor Cells, Cultured; Tunicamycin; Viral Envelope Proteins; Virion

1995
N-butyldeoxygalactonojirimycin inhibits glycolipid biosynthesis but does not affect N-linked oligosaccharide processing.
    The Journal of biological chemistry, 1994, Oct-28, Volume: 269, Issue:43

    Topics: 1-Deoxynojirimycin; alpha-Glucosidases; Animals; Cells, Cultured; Disease Models, Animal; Gaucher Disease; Glucosylceramidase; Glucosyltransferases; Glycolipids; Humans; Mice; Oligosaccharides; Structure-Activity Relationship

1994
N-butyldeoxygalactonojirimycin: a more selective inhibitor of glycosphingolipid biosynthesis than N-butyldeoxynojirimycin, in vitro and in vivo.
    Biochemical pharmacology, 2000, Apr-01, Volume: 59, Issue:7

    Topics: 1-Deoxynojirimycin; Animals; Carbon Radioisotopes; Cell Division; Disaccharidases; Enzyme Inhibitors; Female; Glycogen; Glycosphingolipids; Humans; Liver; Lymphocytes; Mice; Mice, Inbred C57BL; Tissue Distribution

2000
Alkylated imino sugars, reversible male infertility-inducing agents, do not affect the genetic integrity of male mouse germ cells during short-term treatment despite induction of sperm deformities.
    Biology of reproduction, 2005, Volume: 72, Issue:4

    Topics: 1-Deoxynojirimycin; Alkylation; Animals; Carbohydrates; Contraceptive Agents, Male; Disulfides; Female; Fertility; Fertilization in Vitro; Imines; Infertility, Male; Male; Mice; Mice, Inbred C57BL; Mice, Inbred DBA; Pregnancy; Pregnancy Outcome; Protamines; Spermatozoa; Sphingolipids

2005
Beneficial effects of substrate reduction therapy in a mouse model of GM1 gangliosidosis.
    Molecular genetics and metabolism, 2008, Volume: 94, Issue:2

    Topics: 1-Deoxynojirimycin; Animals; beta-Galactosidase; Brain; Disease Models, Animal; Enzyme Inhibitors; Feces; Gangliosidosis, GM1; Glucosyltransferases; Glycosphingolipids; Humans; Macrophage Activation; Mice; Mice, Knockout; Motor Activity; Protein Transport

2008
Looking for protein stabilizing drugs with thermal shift assay.
    Drug testing and analysis, 2015, Volume: 7, Issue:9

    Topics: 1-Deoxynojirimycin; alpha-Galactosidase; Drug Evaluation, Preclinical; Enzyme Stability; Fabry Disease; Glycogen Storage Disease Type II; High-Throughput Screening Assays; Humans; Temperature

2015