miglustat has been researched along with isofagomine in 6 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 0 (0.00) | 18.2507 |
2000's | 2 (33.33) | 29.6817 |
2010's | 3 (50.00) | 24.3611 |
2020's | 1 (16.67) | 2.80 |
Authors | Studies |
---|---|
Blériot, Y; Davies, GJ; Dumon, C; Gilbert, HJ; Gratien, J; Heck, MP; Morland, C; Offen, WA; Smith, NL; Stick, RV; Tailford, LE; Vasella, A | 1 |
Allman, S; Butters, TD; Jensen, HH; Rasmussen, TS; Twigg, G | 1 |
Benjamin, ER; Boyd, RE; Khanna, R; Lee, G; Rybczynski, P; Valenzano, KJ; Wustman, BA | 1 |
Fleet, GWJ; Jia, YM; Kato, A; Kise, M; Li, YX; Shimadate, Y; Wang, JZ; Yu, CY | 1 |
Chung, S; Do, H; Kornfeld, S; Lee, WS; Pine, CW; Steet, R | 1 |
Kaminsky, P; Lidove, O | 1 |
2 review(s) available for miglustat and isofagomine
Article | Year |
---|---|
Pharmacological chaperones as therapeutics for lysosomal storage diseases.
Topics: Cell Line; Glycolipids; Humans; Lysosomal Storage Diseases; Molecular Chaperones; Structure-Activity Relationship | 2013 |
[Current therapeutic strategies in lysosomal disorders].
Topics: 1-Deoxynojirimycin; Codon, Nonsense; Codon, Terminator; Cystine Depleting Agents; Enzyme Inhibitors; Enzyme Replacement Therapy; Gene Expression Regulation; Hematopoietic Stem Cell Transplantation; Humans; Imino Pyranoses; Lysosomal Storage Diseases; Mutant Proteins; Renal Insufficiency | 2014 |
4 other study(ies) available for miglustat and isofagomine
Article | Year |
---|---|
Structural and biochemical evidence for a boat-like transition state in beta-mannosidases.
Topics: beta-Mannosidase; Enzyme Inhibitors; Hydrolysis; Molecular Mimicry; Protein Conformation | 2008 |
Synthesis of N-alkylated noeurostegines and evaluation of their potential as treatment for Gaucher's disease.
Topics: Enzyme Assays; Gaucher Disease; Glucosylceramidase; Humans; Inhibitory Concentration 50; Nortropanes | 2011 |
trans, trans-2-C-Aryl-3,4-dihydroxypyrrolidines as potent and selective β-glucosidase inhibitors: Pharmacological chaperones for Gaucher disease.
Topics: beta-Glucosidase; Enzyme Inhibitors; Gaucher Disease; Glucosylceramidase; Humans; Molecular Docking Simulation; Pyrrolidines | 2022 |
Selective action of the iminosugar isofagomine, a pharmacological chaperone for mutant forms of acid-beta-glucosidase.
Topics: 1-Deoxynojirimycin; alpha-Glucosidases; Cell Proliferation; Cells, Cultured; Disaccharidases; Gaucher Disease; Glucosylceramidase; Glucosyltransferases; Glycoside Hydrolases; Humans; Imino Pyranoses; Lysosomes; Mutation; Oligosaccharides; Piperidines | 2007 |