methylmalonic acid has been researched along with valine in 21 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 13 (61.90) | 18.7374 |
1990's | 4 (19.05) | 18.2507 |
2000's | 2 (9.52) | 29.6817 |
2010's | 2 (9.52) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Lebowitz, J; Morrow, G; Revsin, B | 1 |
Porath, U; Schreier, K | 1 |
Davies, G; Taylor, W; Westwood, A | 1 |
Armitage, IM; Hsia, YE; Lipsky, SR; Ramsdell, HS; Rosenberg, LE; Tanaka, K | 1 |
Jacob, F; Siddons, RC | 1 |
Dayan, AD; Siddons, RC; Spence, JA | 1 |
Blomquist, GJ; Lok, JB; Major, MA | 1 |
Blomquist, GJ; Kearney, GP | 1 |
Chetty, N; Metz, J; Reavis, SC; Vieira-Makings, E | 1 |
Carter, RJ; Parsons, HG; Snyder, FF; Unrath, M | 1 |
Bartlett, K; Halliday, D; Leonard, JV; Thompson, GN; Walter, JH | 1 |
Rasmussen, K | 1 |
Blomquist, GJ; Halarnkar, PP; Heisler, CR; Nelson, JH | 1 |
Crout, DH; Lloyd, EJ; Singh, J | 1 |
Aberhart, DJ; Amster, JI; Hsu, CT; Jenkins, EE; Tanaka, K | 1 |
De Meirleir, L; De Raeve, L; Gerlo, E; Ramet, J; Vandenplas, Y | 1 |
Berrios, M; Crawford, D; Frieden, IJ; Goodman, SI; Hart, K; Howard, R; Levy, ML; McCalmont, T; Ohnstad, C; Packman, S; Rosenblatt, DS; Sweetman, L | 1 |
Hong, M; Yao, X | 1 |
Masumoto, K; Ogita, K; Suita, S; Taguchi, T; Takada, N | 1 |
Dalmau Serra, J; Vitoria Miñana, I | 1 |
Ahmadi, KR; Andrew, T; Dalmia, A; Dib, MJ; Harrington, DJ; Maude, H; Sobczyńska-Malefora, A | 1 |
2 review(s) available for methylmalonic acid and valine
Article | Year |
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[Congenital metabolic acidosis in the postnatal period].
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Fructose-1,6-Diphosphatase Deficiency; Glutarates; Glycogen Storage Disease Type I; Humans; Hyperglycemia; Infant, Newborn; Isoleucine; Ketosis; Lactates; Leucine; Leukoencephalitis, Acute Hemorrhagic; Methylmalonic Acid; Propionates; Syndrome; Thiamine; Valerates; Valine | 1978 |
Methylmalonic acidemia, cobalamin C type, presenting with cutaneous manifestations.
Topics: Acrodermatitis; Amino Acid Metabolism, Inborn Errors; Biopsy; Cheilitis; Female; Humans; Infant, Newborn; Isoleucine; Methylmalonic Acid; Skin; Skin Diseases, Metabolic; Valine; Vitamin B 12 Deficiency | 1997 |
19 other study(ies) available for methylmalonic acid and valine
Article | Year |
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Effect of valine on propionate metabolism in control and hyperglycinemic fibroblasts and in rat liver.
Topics: Carboxy-Lyases; Fibroblasts; Glycine; Humans; In Vitro Techniques; Isoleucine; Metabolism, Inborn Errors; Methylmalonic Acid; Methylmalonyl-CoA Mutase; Propionates; Valine | 1977 |
Colorimetric method for determination of urinary methylmalonic acid.
Topics: Colorimetry; Humans; Indicators and Reagents; Malonates; Methylmalonic Acid; Spectrophotometry; Valine | 1979 |
[13C]Valine metabolism in methylmalonicacidemia using nuclear magnetic resonance: propinonate as an obligate intermediate.
Topics: Amino Acid Metabolism, Inborn Errors; Child; Coenzyme A; Humans; Magnetic Resonance Spectroscopy; Male; Malonates; Methylmalonic Acid; Propionates; Valine | 1975 |
Vitamin B12 nutrition and metabolism in the baboon (Papio cynocephalus).
Topics: Animal Nutritional Physiological Phenomena; Animals; Blood Proteins; Cobalt Radioisotopes; Diet, Vegetarian; Intestinal Absorption; Intestine, Small; Liver; Male; Methylmalonic Acid; Nutritional Requirements; Papio; Propionates; Protein Binding; Species Specificity; Stereoisomerism; Valine; Vitamin B 12; Vitamin B 12 Deficiency | 1975 |
Experimental vitamin B12 deficiency in the baboon.
Topics: Animals; Bacteria; Biopsy; Blood Cell Count; Brain Chemistry; Cerebral Cortex; Folic Acid; Formiminoglutamic Acid; Hemoglobins; Histidine; Intestines; Liver; Methylmalonic Acid; Papio; Spinal Cord; Valine; Vitamin B 12; Vitamin B 12 Deficiency | 1975 |
Biosynthesis of 3-methylpentacosane in the cockroach Periplaneta americana.
Topics: Acetates; Alkanes; Animals; Carbon Radioisotopes; Chromatography, Gas; Cockroaches; Isoleucine; Lactones; Methionine; Methylmalonic Acid; Mevalonic Acid; Propionates; Tritium; Valine | 1975 |
Biosynthesis of internally branched monomethylalkanes in the cockroach Periplaneta fuliginosa.
Topics: Acetates; Alkanes; Animals; Chromatography, Gas; Cockroaches; Glucose; Isoleucine; Methionine; Methylmalonic Acid; Propionates; Skin; Valine | 1976 |
Methylmalonic acid metabolism and nervous-system fatty acids in cobalamin-deficient fruit bats receiving supplements of methionine, valine and isoleucine.
Topics: Amino Acids; Animals; Brain; Chiroptera; Fatty Acids; Isoleucine; Liver; Methionine; Methylmalonic Acid; Methylmalonyl-CoA Mutase; Nervous System; Nervous System Diseases; Spinal Cord; Valine; Vitamin B 12 Deficiency | 1991 |
Evaluation of branched-chain amino acid intake in children with maple syrup urine disease and methylmalonic aciduria.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Ammonia; Body Weight; Child, Preschool; Creatinine; Dietary Proteins; Female; Food, Formulated; Growth; Humans; Infant; Infant, Newborn; Isoleucine; Leucine; Male; Malonates; Maple Syrup Urine Disease; Methylmalonic Acid; Nutritional Requirements; Valine | 1990 |
Contribution of aminoacid catabolism to propionate production in methylmalonic acidaemia.
Topics: Acyl Coenzyme A; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Child; Humans; Isoleucine; Kinetics; Leucine; Malonates; Methionine; Methylmalonic Acid; Phenylalanine; Threonine; Time Factors; Valine | 1989 |
Studies on methylmalonic acid in humans. I. Concentrations in serum and urinary excretion in normal subjects after feeding and during fasting, and after loading with protein, fat, sugar, isoleucine, and valine.
Topics: Adult; Dietary Carbohydrates; Dietary Fats; Dietary Proteins; Eating; Fasting; Female; Humans; Isoleucine; Male; Malonates; Methylmalonic Acid; Middle Aged; Monitoring, Physiologic; Stress, Physiological; Valine; Vitamin B 12; Vitamin B 12 Deficiency | 1989 |
Metabolism of propionate to acetate in the cockroach Periplaneta americana.
Topics: Acetates; Animals; Biotransformation; Chemical Phenomena; Chemistry; Chromatography, High Pressure Liquid; Cockroaches; Fat Body; In Vitro Techniques; Magnetic Resonance Spectroscopy; Methylmalonic Acid; Mitochondria; Propionates; Valine | 1985 |
Metabolism of methyl methacrylate: evidence for metabolism by the valine pathway of catabolism in rat and in man.
Topics: Animals; Gas Chromatography-Mass Spectrometry; Humans; Methylmalonic Acid; Methylmethacrylate; Methylmethacrylates; Rats; Species Specificity; Valine | 1982 |
Metabolism of valine chirally labeled with carbon 13 and deuterium in vitamin B12-folate-deficient rats in vivo. Studies on the physiological role of keto-enol tautomerization.
Topics: Animals; Butyrates; Carbon Isotopes; Deuterium; Folic Acid Deficiency; Isobutyrates; Isomerism; Isotope Labeling; Male; Methylmalonic Acid; Rats; Valine; Vitamin B 12 Deficiency | 1980 |
Acrodermatitis enteropathica-like cutaneous lesions in organic aciduria.
Topics: Acrodermatitis; Amino Acid Metabolism, Inborn Errors; Female; Humans; Infant; Infant, Newborn; Isoleucine; Leucine; Male; Methylmalonic Acid; Microscopy, Electron; Propionates; Skin; Valine | 1994 |
Determination of calpha chemical shift tensor orientation in peptides by dipolar-modulated chemical shift recoupling NMR spectroscopy.
Topics: Anisotropy; Carbon Isotopes; Glycine; Methylmalonic Acid; Models, Molecular; Nitrogen Isotopes; Nuclear Magnetic Resonance, Biomolecular; Peptides; Protein Structure, Secondary; Valine | 2002 |
Effect of a valine-rich diet on a rat model of short bowel syndrome.
Topics: Adaptation, Physiological; Animals; Disease Models, Animal; Male; Methylmalonic Acid; Rats; Rats, Inbred Lew; Regeneration; Short Bowel Syndrome; Valine | 2005 |
[Enteropathic acrodermatitis-like lesions in valine deficiency methylmalonic acidaemia].
Topics: Acrodermatitis; Amino Acid Metabolism, Inborn Errors; Female; Humans; Infant; Intestinal Diseases; Methylmalonic Acid; Valine | 2010 |
A genetic epidemiological study in British adults and older adults shows a high heritability of the combined indicator of vitamin B
Topics: Adult; Aged; Aged, 80 and over; Alkyl and Aryl Transferases; Biomarkers; Energy Metabolism; Female; Ferredoxin-NADP Reductase; Genome-Wide Association Study; Homocysteine; Humans; Male; Metabolism, Inborn Errors; Methylmalonic Acid; Methylmalonyl-CoA Mutase; Middle Aged; Mitochondria; Molecular Epidemiology; Polymorphism, Single Nucleotide; Thiolester Hydrolases; Transcobalamins; Valine; Vitamin B 12 | 2019 |