methylmalonic acid and glutaric acid

methylmalonic acid has been researched along with glutaric acid in 11 studies

Research

Studies (11)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's4 (36.36)18.2507
2000's4 (36.36)29.6817
2010's3 (27.27)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Allen, JC; Bonham, JR; Carpenter, KH; Downing, M; Manning, NJ; Olpin, SE; Pollitt, RJ; Worthy, E1
Aguilar, R; Barbas, C; Castro, M; García, A1
Chalmers, RA; Down, S; Halket, JM; Mallard, WG; Przyborowska, A; Stein, SE1
Evans, JE; Hagen, T; Korson, MS; Sakamoto, M1
Barbas, C; García, A1
Hasegawa, Y; Iga, M; Kimura, M; Shigematsu, Y; Yamaguchi, S1
Gao, XL; Gu, XF; Han, LS; Qiu, WJ; Ye, J1
Deng, C; Li, N; Zhang, X1
Fricker, G; Kamiński, MM; Kölker, S; Mahringer, A; Morath, MA; Okun, JG; Opp, S; Sauer, SW; Thiel, C1
Colín-González, AL; Leipnitz, G; Paz-Loyola, AL; Ribeiro, CA; Santamaría, A; Seminotti, B; Serratos, I; Souza, DO; Wajner, M1
Colín-González, AL; Leipnitz, G; Paz-Loyola, AL; Ribeiro, CA; Santamaría, A; Seminotti, B; Serratos, IN; Souza, DO; Wajner, M1

Reviews

1 review(s) available for methylmalonic acid and glutaric acid

ArticleYear
Capillary electrophoresis for the determination of organic acidurias in body fluids: a review.
    Clinical chemistry and laboratory medicine, 2003, Volume: 41, Issue:6

    Topics: Carboxylic Acids; Electrophoresis, Capillary; Glutarates; Humans; Infant, Newborn; Lactates; Lactic Acid; Metabolism, Inborn Errors; Methylmalonic Acid; Spectrophotometry, Ultraviolet; Time Factors

2003

Other Studies

10 other study(ies) available for methylmalonic acid and glutaric acid

ArticleYear
Quality assessment of urinary organic acid analysis.
    Annals of clinical biochemistry, 1994, Volume: 31 ( Pt 2)

    Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Carboxylic Acids; Chromatography, Gas; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Metabolism, Inborn Errors; Methylmalonic Acid; Quality Control; Sodium Oxybate; United Kingdom

1994
Capillary electrophoresis for rapid profiling of organic acidurias.
    Clinical chemistry, 1998, Volume: 44, Issue:9

    Topics: Carboxylic Acids; Electrophoresis, Capillary; Glutarates; Humans; Infant; Infant, Newborn; Metabolism, Inborn Errors; Methylmalonic Acid; Pyrrolidonecarboxylic Acid

1998
Deconvolution gas chromatography/mass spectrometry of urinary organic acids--potential for pattern recognition and automated identification of metabolic disorders.
    Rapid communications in mass spectrometry : RCM, 1999, Volume: 13, Issue:4

    Topics: Acyl-CoA Dehydrogenase; Autoanalysis; Child, Preschool; Dicarboxylic Acids; Fatty Acid Desaturases; Gas Chromatography-Mass Spectrometry; Glutarates; Hemiterpenes; Humans; Infant; Meglutol; Metabolism, Inborn Errors; Methylmalonic Acid; Pattern Recognition, Automated; Pentanoic Acids; Propionates

1999
A GC/MS/MS screening method for multiple organic acidemias from urine specimens.
    Clinica chimica acta; international journal of clinical chemistry, 1999, Volume: 283, Issue:1-2

    Topics: Acids; Adipates; Automation; Biomarkers; Caprylates; Decanoic Acids; Dicarboxylic Acids; Fumarates; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Keto Acids; Mass Screening; Metabolism, Inborn Errors; Methylmalonic Acid; Reference Values; Sensitivity and Specificity; Urinalysis

1999
Prenatal diagnosis for organic acid disorders using two mass spectrometric methods, gas chromatography mass spectrometry and tandem mass spectrometry.
    Journal of chromatography. B, Analytical technologies in the biomedical and life sciences, 2005, Aug-25, Volume: 823, Issue:1

    Topics: Amniotic Fluid; Carboxylic Acids; Carnitine; Female; Fetal Diseases; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Mass Spectrometry; Metabolism, Inborn Errors; Methylmalonic Acid; Pregnancy; Prenatal Diagnosis; Propionates; Reproducibility of Results; Sensitivity and Specificity; Spectrometry, Mass, Electrospray Ionization; Temperature

2005
[Application of tandem mass spectrometry in diagnosis of organic acidemias].
    Zhonghua er ke za zhi = Chinese journal of pediatrics, 2005, Volume: 43, Issue:5

    Topics: Adolescent; Child; Child, Preschool; Female; Filtration; Gas Chromatography-Mass Spectrometry; Glutarates; Hemiterpenes; Humans; Infant; Male; Metabolism, Inborn Errors; Methylmalonic Acid; Pentanoic Acids; Propionic Acidemia; Tandem Mass Spectrometry

2005
Determination of methylmalonic acid and glutaric acid in urine by aqueous-phase derivatization followed by headspace solid-phase microextraction and gas chromatography-mass spectrometry.
    Journal of separation science, 2007, Volume: 30, Issue:2

    Topics: Chromatography, Ion Exchange; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Methylmalonic Acid; Solid Phase Microextraction; Temperature

2007
Glutaric aciduria type I and methylmalonic aciduria: simulation of cerebral import and export of accumulating neurotoxic dicarboxylic acids in in vitro models of the blood-brain barrier and the choroid plexus.
    Biochimica et biophysica acta, 2010, Volume: 1802, Issue:6

    Topics: Animals; Base Sequence; Blood-Brain Barrier; Brain; Cells, Cultured; Choroid Plexus; Dicarboxylic Acid Transporters; Dicarboxylic Acids; DNA Primers; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; In Vitro Techniques; Metabolism, Inborn Errors; Methylmalonic Acid; Methylmalonyl-CoA Mutase; Models, Biological; Neurotoxins; RNA, Messenger; Swine

2010
Toxic synergism between quinolinic acid and organic acids accumulating in glutaric acidemia type I and in disorders of propionate metabolism in rat brain synaptosomes: Relevance for metabolic acidemias.
    Neuroscience, 2015, Nov-12, Volume: 308

    Topics: Amino Acid Metabolism, Inborn Errors; Animals; Brain; Brain Diseases, Metabolic; Disease Models, Animal; Glutarates; Glutaryl-CoA Dehydrogenase; Lipid Peroxidation; Male; Methylmalonic Acid; Neuroprotective Agents; Oxidative Stress; Propionates; Quinolinic Acid; Rats, Wistar; Reactive Oxygen Species; Synaptosomes

2015
The effect of WIN 55,212-2 suggests a cannabinoid-sensitive component in the early toxicity induced by organic acids accumulating in glutaric acidemia type I and in related disorders of propionate metabolism in rat brain synaptosomes.
    Neuroscience, 2015, Dec-03, Volume: 310

    Topics: Acids, Acyclic; Amino Acid Metabolism, Inborn Errors; Animals; Benzoxazines; Brain; Brain Diseases, Metabolic; Cannabinoid Receptor Agonists; Glutarates; Glutaryl-CoA Dehydrogenase; Lipid Peroxidation; Male; Methylmalonic Acid; Mitochondria; Morpholines; Naphthalenes; Oxidative Stress; Propionates; Rats; Rats, Wistar; Reactive Oxygen Species; Synaptosomes

2015