methylmalonic acid and ammonium hydroxide

methylmalonic acid has been researched along with ammonium hydroxide in 26 studies

Research

Studies (26)

Timeframe	Studies, this research(%)	All Research%
pre-1990	15 (57.69)	18.7374
1990's	3 (11.54)	18.2507
2000's	2 (7.69)	29.6817
2010's	5 (19.23)	24.3611
2020's	1 (3.85)	2.80

Authors

Authors	Studies
Mahoney, MJ	1
Hsia, YE; Mahoney, MJ; Packman, S; Tanaka, K	1
Akaboshi, I; Hattori, S; Matsuda, I; Nagata, N; Oka, Y; Shinozuka, S; Terashima, T; Yamamoto, J	1
Hill, R; Hurley, RM; Morris, M; Ryan, E; Spate, M; Whelan, DT	1
Amédée-Manesme, O; Besson-Leaud, M; Charpentier, C; Checouri, A; Coude, FX; Ferre, P; Lavaud, J; Leraillez, J; Mselati, JC; Ogier, H; Saudubray, JM	1
Coude, FX; Nyhan, WL; Sweetman, L	1
Danks, DM; Haan, EA; Hoogenraad, NJ; Rogers, JG	1
Chase, HP; Glasgow, AM	1
Ledley, FD; Levy, HL; Rosenblatt, DS; Shapira, SK	1
Carter, RJ; Parsons, HG; Snyder, FF; Unrath, M	1
Rosenberg, LE	1
Batshaw, ML; Cohen, SR; Mahoney, MJ; Matalon, R; Thomas, GH	1
Burgess, EA; Mantagos, S; Oberholzer, VG; Palmer, T	1
Krieger, IE; Nigro, M; Sarnaik, A; Taqi, Q	1
Jaquotot, C; Prats, JM; Rodríguez Soriano, J; Sanjurjo, P; Ugarte, M; Uriarte, R; Vallo, A	1
Briand, P; Cathelineau, L; Charpentier, C; Coudé, FX; Ogier, H; Saudubray, JM	2
Stewart, PM; Walser, M	1
Bonini, JS; Brenner, GM; Dutra-Filho, CS; Lima, TT; Mann, KC; Marisco, Pda C; Mello, CF; Ribeiro, MC	1
Carayannopoulos, MO; Dietzen, DJ; Landt, M; Reddy, L; Smith, CH; Wilhite, TR	1
Donati, MA; Filippi, L; Fiorini, P; Gozzini, E; la Marca, G; Malvagia, S	1
Chen, YJ; Cheng, KH; Chiang, CC; Ho, HJ; Hsiao, KJ; Huang, CH; Hung, PY; Hwu, WL; Kao, CH; Lee, NC; Lin, HY; Lin, JL; Lin, SP; Liu, MY; Liu, TT; Niu, DM	1
de Oliveira, FH; Grings, M; Hickmann, FH; Leipnitz, G; Monteiro, WO; Sitta, Â; Soares, LE; Viegas, CM; Wajner, M; Zanatta, Â	1
Braga, DV; da Silva, AM; da Silva, LR; da Silveira Junior, ME; de Oliveira Ferreira, AP; Della-Pace, ID; Dobrachinski, F; Fighera, MR; Furian, AF; Gabbi, P; Grisólia, AB; Marchesan, S; Oliveira, MS; Ribeiro, LR; Rodrigues, FS; Royes, LF; Soares, FA	1
Baumgartner, MR; Burda, P; Devuyst, O; Fingerhut, R; Forny, P; Froese, DS; Heeren, J; Hornemann, T; Kölker, S; Langhans, CD; Mathis, D; Mustedanagic, M; Nägele, N; Peters, HL; Scheja, L; Schumann, A; Thony, B; Wulf, MA; Zhakupova, A	1
Choi, J; Kim, JH	1

Reviews

2 review(s) available for methylmalonic acid and ammonium hydroxide

Article	Year
Organic acidemias. Clinics in perinatology, 1976, Volume: 3, Issue:1 Topics: Acidosis, Renal Tubular; Acids; Amino Acid Metabolism, Inborn Errors; Amino Acids, Essential; Ammonia; Child; Diagnosis, Differential; Glutarates; Humans; Hydrogen-Ion Concentration; Infant; Infant, Newborn; Leucine; Ligases; Methylmalonic Acid; Prenatal Diagnosis; Propionates; Pyruvates; Urea; Valerates	1976
Treating genetic diseases: lessons from three children. Pediatric research, 1990, Volume: 27, Issue:6 Suppl Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Genetic Diseases, Inborn; Genetic Therapy; Humans; Infant; Infant, Newborn; Male; Methylmalonic Acid; Ornithine Carbamoyltransferase Deficiency Disease; Transplantation	1990

Other Studies

24 other study(ies) available for methylmalonic acid and ammonium hydroxide

Article	Year
Severe hyperammonemia in a newborn infant with methylmalonyl-CoA mutase deficiency. The Journal of pediatrics, 1978, Volume: 92, Issue:5 Topics: Ammonia; Humans; Infant, Newborn; Infant, Newborn, Diseases; Isomerases; Liver; Male; Methylmalonic Acid; Methylmalonyl-CoA Mutase	1978
Methylmalonic acidemia. European journal of pediatrics, 1978, Jul-03, Volume: 128, Issue:3 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Ammonia; Female; Glycine; Humans; Hypoglycemia; Infant; Isomerases; Malonates; Methylmalonic Acid; Methylmalonyl-CoA Mutase; Uric Acid	1978
Methylmalonic acidemia: 6 years' clinical experience with two variants unresponsive to vitamin B12 therapy. Canadian Medical Association journal, 1979, May-19, Volume: 120, Issue:10 Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Child, Preschool; Female; Humans; Infant; Infant, Newborn; Male; Malonates; Methylmalonic Acid; Methylmalonyl-CoA Mutase; Uric Acid; Vitamin B 12	1979
[Emergency treatment of inborn amino errors of amino acid metabolism detected in the neonatal period]. Archives francaises de pediatrie, 1979, Volume: 36, Issue:10 Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Diuretics, Osmotic; Emergencies; Enteral Nutrition; Exchange Transfusion, Whole Blood; Humans; Infant, Newborn; Leucine; Methylmalonic Acid; Peritoneal Dialysis; Propionates; Valerates	1979
Inhibition by propionyl-coenzyme A of N-acetylglutamate synthetase in rat liver mitochondria. A possible explanation for hyperammonemia in propionic and methylmalonic acidemia. The Journal of clinical investigation, 1979, Volume: 64, Issue:6 Topics: Acetyl Coenzyme A; Acetyltransferases; Acidosis; Acyl Coenzyme A; Ammonia; Animals; Glutamates; Kinetics; Malonates; Methylmalonic Acid; Mitochondria, Liver; Propionates; Rats; Substrate Specificity	1979
Hereditary hyperammonaemic syndromes--a six year experience. Australian paediatric journal, 1979, Volume: 15, Issue:3 Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Child, Preschool; Female; Humans; Infant; Infant, Newborn; Male; Methylmalonic Acid; Ornithine Carbamoyltransferase Deficiency Disease; Syndrome	1979
Effect of propionic acid on fatty acid oxidation and ureagenesis. Pediatric research, 1976, Volume: 10, Issue:7 Topics: Ammonia; Animals; Carbon Dioxide; Fatty Acids; Fatty Liver; Fibroblasts; Liver; Methylmalonic Acid; Oxidation-Reduction; Palmitates; Pentetic Acid; Propionates; Rats; Reye Syndrome; Urea	1976
Ketoacidotic crisis as a presentation of mild ("benign") methylmalonic acidemia. The Journal of pediatrics, 1991, Volume: 119, Issue:1 Pt 1 Topics: Acidosis; Amino Acids; Ammonia; Child, Preschool; Female; Fibroblasts; Humans; Ketones; Ketosis; Metabolism, Inborn Errors; Methylmalonic Acid; Oxidation-Reduction; Vitamin B 12	1991
Evaluation of branched-chain amino acid intake in children with maple syrup urine disease and methylmalonic aciduria. Journal of inherited metabolic disease, 1990, Volume: 13, Issue:2 Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Ammonia; Body Weight; Child, Preschool; Creatinine; Dietary Proteins; Female; Food, Formulated; Growth; Humans; Infant; Infant, Newborn; Isoleucine; Leucine; Male; Malonates; Maple Syrup Urine Disease; Methylmalonic Acid; Nutritional Requirements; Valine	1990
Treatment of the cbl B form of methylmalonic acidaemia with adenosylcobalamin. Journal of inherited metabolic disease, 1984, Volume: 7, Issue:2 Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Bicarbonates; Child, Preschool; Cobamides; Female; Glycine; Humans; Malonates; Methylmalonic Acid; Vitamin B 12	1984
Three instances of neonatal death with hyperammonaemia, each resulting from a different cause. Journal of inherited metabolic disease, 1980, Volume: 3, Issue:3 Topics: Amino Acids; Ammonia; Autopsy; Female; Humans; Infant, Newborn; Infant, Newborn, Diseases; Lactates; Male; Methylmalonic Acid; Urea	1980
Screening of high risk infants for metabolic disease in a metropolitan hospital. Journal of inherited metabolic disease, 1981, Volume: 4, Issue:2 Topics: Amino Acids; Ammonia; Carboxylic Acids; Humans; Infant, Newborn; Infant, Newborn, Diseases; Lactates; Lactic Acid; Metabolism, Inborn Errors; Methylmalonic Acid; Pyruvates; Pyruvic Acid	1981
[Combined exchange transfusion and peritoneal dialysis treatment in a neonatal case of methylmalonic acidemia with severe hyperammonemia]. Anales espanoles de pediatria, 1982, Volume: 17, Issue:4 Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Ammonia; Dietary Proteins; Exchange Transfusion, Whole Blood; Female; Humans; Infant, Newborn; Malonates; Methylmalonic Acid; Parenteral Nutrition; Peritoneal Dialysis	1982
Hyperammonemia secondary to hereditary organic acidurias: a study of 29 cases. Advances in experimental medicine and biology, 1982, Volume: 153 Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Hemiterpenes; Humans; Infant, Newborn; Methylmalonic Acid; Pentanoic Acids; Propionates; Urea	1982
Occurrence of hyperammonemia in the course of 17 cases of methylmalonic acidemia. The Journal of pediatrics, 1981, Volume: 99, Issue:2 Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Chromatography, Gas; Humans; Malonates; Methylmalonic Acid; Propionates	1981
Failure of the normal ureagenic response to amino acids in organic acid-loaded rats. Proposed mechanism for the hyperammonemia of propionic and methylmalonic acidemia. The Journal of clinical investigation, 1980, Volume: 66, Issue:3 Topics: Acyl Coenzyme A; Adenosine Triphosphate; Ammonia; Animals; Carbamoyl-Phosphate Synthase (Ammonia); Female; Glutamates; Kinetics; Liver; Malonates; Methylmalonic Acid; Ornithine Carbamoyltransferase; Propionates; Rats; Urea	1980
Ammonia potentiates methylmalonic acid-induced convulsions and TBARS production. Experimental neurology, 2003, Volume: 182, Issue:2 Topics: Acetates; Ammonia; Ammonium Chloride; Animals; Behavior, Animal; Corpus Striatum; Drug Synergism; Enzyme Activation; Enzyme Inhibitors; Male; Methylmalonic Acid; Rats; Rats, Wistar; Seizures; Succinate Dehydrogenase; Thiobarbituric Acid Reactive Substances	2003
Equimolar ammonia interference in potassium measurement on the Osmetech OPTI Critical Care Analyzer. Clinical chemistry, 2006, Volume: 52, Issue:8 Topics: Ammonia; Critical Care; False Positive Reactions; Humans; Infant; Methylmalonic Acid; Point-of-Care Systems; Potassium; Transportation of Patients	2006
N-carbamylglutamate in emergency management of hyperammonemia in neonatal acute onset propionic and methylmalonic aciduria. Neonatology, 2010, Volume: 97, Issue:3 Topics: Acute Disease; Amino Acid Metabolism, Inborn Errors; Ammonia; Emergency Medical Services; Female; Glutamates; Humans; Hyperammonemia; Infant, Newborn; Male; Methylmalonic Acid; Propionic Acidemia; Vitamin B 12 Deficiency	2010
Newborn screening for methylmalonic aciduria by tandem mass spectrometry: 7 years' experience from two centers in Taiwan. Journal of the Chinese Medical Association : JCMA, 2010, Volume: 73, Issue:6 Topics: Acetylcarnitine; Ammonia; Carnitine; Humans; Infant, Newborn; Methylmalonic Acid; Neonatal Screening; Taiwan; Tandem Mass Spectrometry	2010
Disruption of redox homeostasis and brain damage caused in vivo by methylmalonic acid and ammonia in cerebral cortex and striatum of developing rats. Free radical research, 2014, Volume: 48, Issue:6 Topics: Ammonia; Animals; Antioxidants; Catalase; Cerebral Cortex; Corpus Striatum; Fluoresceins; Glutathione; Glutathione Peroxidase; Glutathione Reductase; Homeostasis; Hyperammonemia; Infusions, Intraventricular; Male; Methylmalonic Acid; NG-Nitroarginine Methyl Ester; Nitrates; Nitrites; Oxidation-Reduction; Rats; Rats, Wistar; Sulfhydryl Compounds; Superoxide Dismutase; Urease	2014
A neuronal disruption in redox homeostasis elicited by ammonia alters the glycine/glutamate (GABA) cycle and contributes to MMA-induced excitability. Amino acids, 2016, Volume: 48, Issue:6 Topics: Ammonia; Animals; Cerebral Cortex; Cytokines; Electroencephalography; Glutamic Acid; Glycine; Homeostasis; Hyperammonemia; Membrane Potential, Mitochondrial; Methylmalonic Acid; Mice; Oxidation-Reduction; Seizures	2016
Novel Mouse Models of Methylmalonic Aciduria Recapitulate Phenotypic Traits with a Genetic Dosage Effect. The Journal of biological chemistry, 2016, 09-23, Volume: 291, Issue:39 Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Biomarkers; Brain; Carnitine; Dietary Proteins; Disease Models, Animal; Gene Dosage; Gene Knock-In Techniques; Kidney; Methylmalonic Acid; Methylmalonyl-CoA Mutase; Mice; Mice, Knockout; Phenotype; Quantitative Trait, Heritable	2016
Feline hyperammonemia associated with functional cobalamin deficiency: A case report. The Canadian veterinary journal = La revue veterinaire canadienne, 2023, Volume: 64, Issue:5 Topics: Amino Acids; Ammonia; Animals; Cat Diseases; Cats; Female; Hyperammonemia; Methylmalonic Acid; Urea; Vitamin B 12; Vitamin B 12 Deficiency	2023