meglutol and carnitine

meglutol has been researched along with carnitine in 9 studies

Research

Studies (9)

TimeframeStudies, this research(%)All Research%
pre-19903 (33.33)18.7374
1990's3 (33.33)18.2507
2000's0 (0.00)29.6817
2010's2 (22.22)24.3611
2020's1 (11.11)2.80

Authors

AuthorsStudies
Gibson, KM; Lee, CF; Wappner, RS1
Chalmers, RA; Davies, SE; Iles, RA; Stacey, TE1
Buchanan, D; Dasouki, M; Gibson, KM; Mercer, N; Thoene, J1
Foster, DW; McGarry, JD1
Chalmers, RA; de Sousa, C; Hoppel, CL; Millington, DS; Roe, CR; Stacey, TE; Tracey, BM1
Castro-Gago, M; Eirís, J; Fernández-Prieto, R; Ribes, A; Rodríguez-García, J; Rodríguez-Segade, S1
Acquaviva, C; Caruba, C; Giudicelli, H; Khalfi, A; Moreigne, M; Pierron, S; Rolland, MO; Touati, G1
Balbueno Guerreiro, GB; de Moura Coelho, D; Delgado, CA; Diaz Jacques, CE; Manfredini, V; Sitta, A; Vargas, CR; Wajner, M1
Gornbein, JA; Koos, BJ1

Reviews

1 review(s) available for meglutol and carnitine

ArticleYear
Regulation of hepatic fatty acid oxidation and ketone body production.
    Annual review of biochemistry, 1980, Volume: 49

    Topics: Acetyl Coenzyme A; Adipose Tissue; Animals; Carnitine; Carnitine Acyltransferases; Fatty Acids; Fatty Acids, Nonesterified; Glucagon; Glycogen; Insulin; Ketone Bodies; Liver; Malonyl Coenzyme A; Meglutol; Models, Biological; Triglycerides

1980

Other Studies

8 other study(ies) available for meglutol and carnitine

ArticleYear
3-Methylglutaconyl-coenzyme-A hydratase deficiency: a new case.
    Journal of inherited metabolic disease, 1992, Volume: 15, Issue:3

    Topics: Carnitine; Diseases in Twins; Fibroblasts; Glutarates; Humans; Hydro-Lyases; Infant; Leucine; Lymphocytes; Male; Meglutol

1992
Creatine metabolism during metabolic perturbations in patients with organic acidurias.
    Clinica chimica acta; international journal of clinical chemistry, 1990, Dec-24, Volume: 194, Issue:2-3

    Topics: 3-Hydroxybutyric Acid; Carnitine; Child; Child, Preschool; Creatine; Creatinine; Female; Humans; Hydroxybutyrates; Infant; Lactates; Lactic Acid; Magnetic Resonance Spectroscopy; Male; Meglutol; Metabolism, Inborn Errors; Methylmalonic Acid; Vitamin B 12

1990
3-Hydroxy-3-methylglutaric aciduria: response to carnitine therapy and fat and leucine restriction.
    Journal of inherited metabolic disease, 1987, Volume: 10, Issue:2

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Carnitine; Dietary Fats; Dietary Proteins; Female; Glutarates; Humans; Infant, Newborn; Leucine; Meglutol; Oxo-Acid-Lyases

1987
L-Carnitine insufficiency in disorders of organic acid metabolism: response to L-carnitine by patients with methylmalonic aciduria and 3-hydroxy-3-methylglutaric aciduria.
    Journal of inherited metabolic disease, 1984, Volume: 7 Suppl 2

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Glutarates; Humans; Malonates; Meglutol; Methylmalonic Acid

1984
[3-hydroxy-3-methylglutaric aciduria and recurrent Reye-like syndrome].
    Revista de neurologia, 1998, Volume: 26, Issue:154

    Topics: Acidosis; Adolescent; Apnea; Carnitine; Coma; Diagnosis, Differential; Fatty Liver; Female; Fibroblasts; Hepatomegaly; Humans; Hypoglycemia; Meglutol; Oxo-Acid-Lyases; Phenotype; Recurrence; Reye Syndrome

1998
[Late onset 3-HMG-CoA lyase deficiency: a rare but treatable disorder].
    Archives de pediatrie : organe officiel de la Societe francaise de pediatrie, 2010, Volume: 17, Issue:1

    Topics: Alleles; Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Chromosome Aberrations; Combined Modality Therapy; Diet, Protein-Restricted; DNA Mutational Analysis; Exons; Genes, Recessive; Humans; Hypoglycemia; Leucine; Male; Meglutol; Oxo-Acid-Lyases; Polymerase Chain Reaction; Rare Diseases; Sequence Analysis, DNA

2010
Prevention by L-carnitine of DNA damage induced by 3-hydroxy-3-methylglutaric and 3-methylglutaric acids and experimental evidence of lipid and DNA damage in patients with 3-hydroxy-3-methylglutaric aciduria.
    Archives of biochemistry and biophysics, 2019, 06-15, Volume: 668

    Topics: 8-Hydroxy-2'-Deoxyguanosine; Acetyl-CoA C-Acetyltransferase; Adolescent; Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Child, Preschool; Dinoprost; DNA Damage; Guanine; Guanosine; Humans; Infant; Lipid Peroxidation; Meglutol

2019
Early pregnancy metabolites predict gestational diabetes mellitus: implications for fetal programming.
    American journal of obstetrics and gynecology, 2021, Volume: 224, Issue:2

    Topics: Adult; Alanine; Arginine; Carnitine; Case-Control Studies; Diabetes, Gestational; Diet Therapy; Dopamine; Early Diagnosis; Epigenesis, Genetic; Female; Fetal Development; Gestational Age; Glucose Tolerance Test; Glucuronides; Humans; Hypoglycemic Agents; Lactones; Lysine; Meglutol; Metabolomics; Neopterin; Orotic Acid; Phenols; Pregnancy; Ribonucleosides; Sulfides

2021