meglutol has been researched along with beta-hydroxyisovaleric acid in 11 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 3 (27.27) | 18.7374 |
| 1990's | 2 (18.18) | 18.2507 |
| 2000's | 4 (36.36) | 29.6817 |
| 2010's | 2 (18.18) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Chalmers, RA; Halliday, D; Thompson, GN | 1 |
| Buchanan, DN; Muenzer, J; Thoene, JG | 1 |
| Cann, HM; Gibson, KM; Greene, CL; Holm, J; Nyhan, WL; Robinson, BH; Sweetman, L | 1 |
| Beemer, FA; Bruinvis, L; Duran, M; Ketting, D; Tibosch, AS; Wadman, SK | 1 |
| Berry, HK; Denton, MD; Norman, EJ | 1 |
| Brandis, M; Ensenauer, R; Gibson, KM; Lehnert, W; Müller, CB; Schwab, KO | 1 |
| Engelke, UF; Kluijtmans, LA; Kremer, B; Loss, S; Loupatty, FJ; Morava, E; Moskau, D; van den Bergh, E; van der Graaf, M; Wanders, RJ; Wevers, RA | 1 |
| Amaral, AU; de Bortoli, G; Latini, A; Leipnitz, G; Schuck, PF; Seminotti, B; Solano, A; Wajner, M; Wannmacher, CM; Wyse, AT | 1 |
| Amaral, AU; Beskow, AP; da Silva, Lde B; Fernandes, CG; Leipnitz, G; Ribeiro, CA; Seminotti, B; Vargas, CR; Wajner, M; Zanatta, A | 1 |
| Hickmann, FH; Ribeiro, CA; Wajner, M | 1 |
| Acquaviva-Bourdain, C; Briand, G; Dobbelaere, D; Fontaine, M; Jissendi-Tchofo, P; Mention, K; Roland, D; Ultré, V; Vamecq, J | 1 |
11 other study(ies) available for meglutol and beta-hydroxyisovaleric acid
| Article | Year |
|---|---|
The contribution of protein catabolism to metabolic decompensation in 3-hydroxy-3-methylglutaric aciduria.
Topics: Amino Acid Metabolism, Inborn Errors; Child; Diseases in Twins; Female; Glutarates; Humans; Leucine; Male; Meglutol; Oxo-Acid-Lyases; Phenylalanine; Proteins; Valerates | 1990 |
Positive-ion thermospray liquid chromatography-mass spectrometry: detection of organic acidurias.
Topics: Argininosuccinic Acid; Carboxylic Acids; Chromatography, Thin Layer; Female; Humans; Infant; Infant, Newborn; Male; Mass Spectrometry; Meglutol; Metabolism, Inborn Errors; Methylmalonic Acid; Sensitivity and Specificity; Valerates | 1990 |
3-Hydroxy-3-methylglutaric aciduria.
Topics: Cells, Cultured; Female; Fibroblasts; Follow-Up Studies; Glutarates; Humans; Infant, Newborn; Leucine; Meglutol; Oxo-Acid-Lyases; Skin; Valerates | 1984 |
Inherited 3-methylglutaconic aciduria in two brothers--another defect of leucine metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Glutarates; Humans; Hydro-Lyases; Leucine; Male; Meglutol; Speech Disorders; Valerates | 1982 |
Gas-chromatographic/mass spectrometric detection of 3-hydroxy-3-methylglutaryl-CoA lyase deficiency in double first cousins.
Topics: Amino Acid Metabolism, Inborn Errors; Female; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Hydroxy Acids; Infant; Leucine; Male; Meglutol; Oxo-Acid-Lyases; Valerates | 1982 |
3-Methylglutaconyl-CoA hydratase deficiency: a new patient with speech retardation as the leading sign.
Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Diet, Protein-Restricted; Fibroblasts; Glutarates; Humans; Hydro-Lyases; Meglutol; Speech Disorders; Valerates | 2000 |
NMR spectroscopic studies on the late onset form of 3-methylglutaconic aciduria type I and other defects in leucine metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Brain; Female; Glutarates; Humans; Leucine; Magnetic Resonance Spectroscopy; Meglutol; Middle Aged; Valerates | 2006 |
Induction of oxidative stress by the metabolites accumulating in 3-methylglutaconic aciduria in cerebral cortex of young rats.
Topics: Animals; Antioxidants; Cerebral Cortex; Glutarates; Glutathione; Lipid Peroxidation; Meglutol; Mitochondria; Molecular Structure; Oxidants; Oxidative Stress; Protein Carbonylation; Rats; Rats, Wistar; Superoxides; Thiobarbituric Acid Reactive Substances; Valerates | 2008 |
Striatum is more vulnerable to oxidative damage induced by the metabolites accumulating in 3-hydroxy-3-methylglutaryl-CoA lyase deficiency as compared to liver.
Topics: Animals; Corpus Striatum; Glutarates; Glutathione; Glycine; Humans; Liver; Male; Meglutol; Oxidative Stress; Oxo-Acid-Lyases; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances; Valerates | 2009 |
Neurochemical evidence that 3-methylglutaric acid inhibits synaptic Na+,K+-ATPase activity probably through oxidative damage in brain cortex of young rats.
Topics: Animals; Cerebral Cortex; Glutarates; Humans; Male; Meglutol; Mitochondria; Oxidation-Reduction; Oxidative Stress; Rats; Rats, Wistar; Sodium-Potassium-Exchanging ATPase; Synaptic Membranes; Valerates | 2011 |
Coupled brain and urine spectroscopy - in vivo metabolomic characterization of HMG-CoA lyase deficiency in 5 patients.
Topics: Acetyl-CoA C-Acetyltransferase; Amino Acid Metabolism, Inborn Errors; Brain; Brain Chemistry; Cerebellum; Child; Child, Preschool; Female; Humans; Hydrogen-Ion Concentration; Infant; Infant, Newborn; Magnetic Resonance Imaging; Male; Meglutol; Metabolomics; Proton Magnetic Resonance Spectroscopy; Urine; Valerates; White Matter | 2017 |