Page last updated: 2024-08-21

isovaleric acid and valerates

isovaleric acid has been researched along with valerates in 56 studies

Research

Studies (56)

TimeframeStudies, this research(%)All Research%
pre-199050 (89.29)18.7374
1990's2 (3.57)18.2507
2000's2 (3.57)29.6817
2010's1 (1.79)24.3611
2020's1 (1.79)2.80

Authors

AuthorsStudies
Kodama, H; Uasa, S1
Glassberg, R; Ikeda, Y; Ito, M; Matsubara, Y; Satyabhama, S; Tanaka, K1
Tanaka, K1
Ackman, RG1
Jourdan, F; Royet, JP; Sicard, G1
Aiello, RJ; Armentano, LE; Bertics, SJ; Murphy, AT1
Dembure, P; Elsas, L; Madsen, K; Naglak, M; Salvo, R1
Gerdes, AM; Gregersen, N; Güttler, F; Lúdvigsson, P1
Heimler, R; Hennes, H; Khayata, S; Matalon, R; Sasidharan, P1
Elsas, LJ; Naglak, M1
Ikeda, Y; Tanaka, K1
Hyman, D; Ikeda, Y; Matsubara, Y; Tanaka, K1
Hyman, DB; Ikeda, Y; Matsubara, Y; Tanaka, K1
Buchanan, DN; Thoene, JG1
Ruchim, MA; Zarling, EJ1
Pollitt, RJ1
Goodman, SI; Hack, AM; Hine, DG; Tanaka, K1
Hyman, DB; Tanaka, K1
Ikeda, Y; Keese, SM; Tanaka, K1
Gottschild, C; Gründel, G; Kolb, E; Müller, I; Said, A; Schineff, C; Schmidt, U; Vallentin, G1
Bradley, D; Chalmers, RA; de Sousa, C; Stacey, TE; Tracey, BM; Weaver, C1
Bradley, D; Chalmers, RA; de Sousa, C; Stacey, TE; Tracey, BM; Weaver, CM1
Deetz, LE; Preston, RL; Pritchard, RH; Richardson, CR1
Lehnert, W3
Arnetoli, G; Boncinelli, L; Campostrini, R; Paganini, M; Zaccara, G; Zappoli, R1
Audenaert, SM; Squillaro, EJ; Wilson, WG1
Bumack, C; Burke, D; Danks, DM; Haan, EA; Halpern, B; Hammond, J; Hick, L; Malegan, D; McCairns, E; Nyhan, WL; Sims, P; Sweetman, L; Tanaka, K; Truscott, RJ1
Bohan, TP; Kahler, SG; Maltby, DA; Millington, DS; Roe, CR1
Edwall, L; Mejàre, B; Panopoulos, P1
Burke, DG; Danks, D; Halpern, B; Malegan, D; McCairns, E; Schlesinger, P; Wilken, B1
Duran, M; Houstková, H; Hyánek, J; Kozich, V; Pĕtová, J; Pisacka, M; Rubín, A; Wadman, SK; Zapadlo, M; Zeman, J1
Dabrowski, C; Dubiel, B; Tanaka, K; Wetts, R1
Coude, FX; Grimber, G; Parvy, P; Rabier, D1
Bruinvis, L; Dorland, L; Duran, M; Ketting, D; Niederwieser, A; Wadman, SK1
Britz, ML; Wilkinson, RG1
Liehr, JG; Mendiola, J; Robotham, JL; Williams, JC1
Kikawa, Y; Kikuchi, K; Ohta, S; Okamoto, M; Shigematsu, Y; Sudo, M1
Brenner, RR; Juárez, P1
Hillman, RE; Peden, VH; Williams, KM1
Batenburg-Plenter, AM; Bruinvis, L; Duran, M; Ketting, D; van Pelt, BC; Wadman, SK1
French, NP; Grauaug, A; Wysocki, SJ1
Mori, M; Tatibana, M; Uchiyama, C; Yamashita, F; Yoshida, I; Yoshino, M1
Charpentier, C; Coude, FX; Grimber, G; Ogier, H; Parvy, P; Pham Dinh, D; Saudubray, JM1
Bergen, BJ; Eguren, LA; Haas, R; Parks, JK; Stumpf, DA1
Inoue, Y; Kameyama, J; Momoi, T; Shigematsu, Y; Sudo, M; Suzuki, Y1
Bakkeren, JA; Houben, ML; Ruitenbeek, W; Sengers, RC; Trijbels, JM; Van der Zeè, SP1
Burton, BK; Challa, VR; Fischer, AQ; McLean, WT1
Aburada, M; Endo, T; Takeda, S; Yuasa, K1
Al-Bassam, SS; Sherratt, HS1
August, CS; Cohn, RM; Hutchinson, R; Kelleher, JF; Yudkoff, M1
Angelidaki, I; Batstone, DJ; Pind, PF1
Drouillard, JS; Gibson, ML; Karges, KK; May, ML; Murray, L; Quinn, MJ; Reinhardt, CD1
Centrella, W; Deliephan, A; Fuller, JC; Huss, AR; Jones, CK; Marshall, DL1
Gao, R; Li, Z1

Reviews

3 review(s) available for isovaleric acid and valerates

ArticleYear
Birthweights in the Faroe Islands: possible role of isovaleric acid.
    Journal of internal medicine, 1989, Volume: 225, Issue:2

    Topics: Birth Weight; Denmark; Feeding Behavior; Female; Hemiterpenes; Humans; Pentanoic Acids; Pregnancy; Valerates

1989
Molecular basis of isovaleric acidemia and the study of the acyl-CoA dehydrogenase family.
    Advances in neurology, 1988, Volume: 48

    Topics: Acyl-CoA Dehydrogenases; Animals; DNA; Hemiterpenes; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Leucine; Mitochondria, Liver; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Phenotype; Protein Biosynthesis; Protein Processing, Post-Translational; Rats; Valerates

1988
Molecular basis of isovaleric acidemia and medium-chain acyl-CoA dehydrogenase deficiency.
    Enzyme, 1987, Volume: 38, Issue:1-4

    Topics: Acyl-CoA Dehydrogenases; Amino Acid Sequence; Base Sequence; DNA, Circular; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Metabolism, Inborn Errors; Molecular Sequence Data; Mutation; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Protein Biosynthesis; Sequence Homology, Nucleic Acid; Valerates

1987

Other Studies

53 other study(ies) available for isovaleric acid and valerates

ArticleYear
Isotachophoretic analysis of isovalerylglycine in urine of a patient with isovaleric acidemia.
    Journal of chromatography, 1979, Jul-21, Volume: 163, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Dipeptides; Electrophoresis; Hemiterpenes; Humans; Pentanoic Acids; Valerates

1979
Nucleotide sequence of messenger RNA encoding human isovaleryl-coenzyme A dehydrogenase and its expression in isovaleric acidemia fibroblasts.
    The Journal of clinical investigation, 1990, Volume: 85, Issue:4

    Topics: Amino Acid Sequence; Animals; Base Sequence; DNA; Fatty Acid Desaturases; Fibroblasts; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Molecular Sequence Data; Mutation; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Rats; RNA, Messenger; Valerates

1990
Isovaleric acidemia: personal history, clinical survey and study of the molecular basis.
    Progress in clinical and biological research, 1990, Volume: 321

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Cell Line; Child, Preschool; Female; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Prognosis; Valerates

1990
A comparative study of 2-deoxyglucose patterns of glomerular activation in the olfactory bulbs of C57 BL/6J and AKR/J mice.
    Brain research, 1989, Mar-06, Volume: 481, Issue:2

    Topics: Action Potentials; Animals; Deoxy Sugars; Deoxyglucose; Hemiterpenes; Mice; Mice, Inbred AKR; Mice, Inbred C57BL; Olfactory Bulb; Pentanoic Acids; Pentanols; Valerates

1989
Volatile fatty acid uptake and propionate metabolism in ruminant hepatocytes.
    Journal of dairy science, 1989, Volume: 72, Issue:4

    Topics: Animals; Butyrates; Cattle; Fatty Acids, Volatile; Female; Gluconeogenesis; Goats; Hemiterpenes; Liver; Male; Pentanoic Acids; Propionates; Time Factors; Valerates

1989
The treatment of isovaleric acidemia with glycine supplement.
    Pediatric research, 1988, Volume: 24, Issue:1

    Topics: Carbon Dioxide; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1988
A Scandinavian case of isovaleric acidaemia.
    Journal of inherited metabolic disease, 1988, Volume: 11, Issue:2

    Topics: Child, Preschool; Denmark; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1988
Isovaleric acidaemia in a premature infant: diagnosis and treatment.
    Journal of inherited metabolic disease, 1988, Volume: 11, Issue:3

    Topics: Amino Acids; Hemiterpenes; Humans; Infant, Newborn; Infant, Premature, Diseases; Isovaleryl-CoA Dehydrogenase; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1988
Acute and chronic-intermittent isovaleric acidemia: diagnosis and glycine therapy.
    Acta paediatrica Japonica : Overseas edition, 1988, Volume: 30, Issue:4

    Topics: Acute Disease; Child; Child, Preschool; Chronic Disease; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1988
[Isovaleric acidemia].
    Tanpakushitsu kakusan koso. Protein, nucleic acid, enzyme, 1988, Volume: 33, Issue:5

    Topics: Animals; Cloning, Molecular; DNA; Fibroblasts; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Mutation; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1988
Early identification of isovaleric aciduria using photodiode array detection for liquid chromatographic profiling of urinary carboxylic acids.
    Biomedical chromatography : BMC, 1986, Volume: 1, Issue:1

    Topics: Carboxylic Acids; Chromatography, High Pressure Liquid; Hemiterpenes; Humans; Mass Spectrometry; Pentanoic Acids; Spectrophotometry, Ultraviolet; Valerates

1986
Protein origin of the volatile fatty acids isobutyrate and isovalerate in human stool.
    The Journal of laboratory and clinical medicine, 1987, Volume: 109, Issue:5

    Topics: Albumins; Butyrates; Fatty Acids, Volatile; Feces; Hemiterpenes; Humans; Hydrogen-Ion Concentration; Isobutyrates; Leucine; Male; Pentanoic Acids; Proteins; Valerates; Valine

1987
Endogenous catabolism as source of toxic metabolites in isovaleric acidemia.
    The Journal of pediatrics, 1987, Volume: 111, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Dietary Proteins; Hemiterpenes; Humans; Leucine; Pentanoic Acids; Valerates

1987
Stable isotope dilution analysis of isovalerylglycine in amniotic fluid and urine and its application for the prenatal diagnosis of isovaleric acidemia.
    Pediatric research, 1986, Volume: 20, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Amniotic Fluid; Female; Gas Chromatography-Mass Spectrometry; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Risk; Valerates

1986
Isovaleryl-CoA dehydrogenase activity in isovaleric acidemia fibroblasts using an improved tritium release assay.
    Pediatric research, 1986, Volume: 20, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Fibroblasts; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Kinetics; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Skin; Tritium; Valerates

1986
Molecular heterogeneity of variant isovaleryl-CoA dehydrogenase from cultured isovaleric acidemia fibroblasts.
    Proceedings of the National Academy of Sciences of the United States of America, 1985, Volume: 82, Issue:20

    Topics: Amino Acid Metabolism, Inborn Errors; Electrophoresis, Polyacrylamide Gel; Fibroblasts; Genetic Carrier Screening; Genetic Variation; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Methionine; Molecular Weight; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1985
[Effect of the intravenous infusion of butyrate, isobutyrate and isovalerate on the blood serum levels of glucose, insulin, free fatty acids and total alpha-amino-N in sheep under conditions of adequate feeding and after an 8-day fast].
    Archiv fur experimentelle Veterinarmedizin, 1985, Volume: 39, Issue:1

    Topics: Amino Acids; Animal Feed; Animals; Blood Glucose; Butyrates; Fasting; Fatty Acids, Nonesterified; Hemiterpenes; Infusions, Parenteral; Insulin; Isobutyrates; Nitrogen; Pentanoic Acids; Sheep; Time Factors; Valerates

1985
L-carnitine and glycine therapy in isovaleric acidaemia.
    Journal of inherited metabolic disease, 1985, Volume: 8 Suppl 2

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Valerates

1985
The response to L-carnitine and glycine therapy in isovaleric acidaemia.
    European journal of pediatrics, 1986, Volume: 144, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Carboxylic Acids; Carnitine; Child, Preschool; Combined Modality Therapy; Drug Therapy, Combination; Female; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Valerates

1986
Feedlot performance and carcass characteristics of steers fed diets containing ammonium salts of the branched-chain fatty acids and valeric acid.
    Journal of animal science, 1985, Volume: 61, Issue:6

    Topics: Animals; Body Composition; Body Weight; Butyrates; Cattle; Diet; Fatty Acids, Volatile; Hemiterpenes; Isobutyrates; Pentanoic Acids; Quaternary Ammonium Compounds; Valerates

1985
N-Isovalerylalanine and N-isovalerylsarcosine: two new minor metabolites in isovaleric acidemia.
    Clinica chimica acta; international journal of clinical chemistry, 1983, Oct-31, Volume: 134, Issue:1-2

    Topics: Alanine; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Pentanoic Acids; Sarcosine; Valerates

1983
Treatment of epileptic patients with valproic acid does not modify plasma and urine short-chain-fatty acids.
    Acta neurologica Scandinavica, 1983, Volume: 68, Issue:4

    Topics: Adolescent; Adult; Ammonia; Brain Diseases; Butyrates; Epilepsy; Fatty Acids; Female; Hemiterpenes; Humans; Isobutyrates; Male; Pentanoic Acids; Propionates; Reye Syndrome; Valerates; Valproic Acid

1983
Hyperammonaemia in a preterm infant with isovaleric acidaemia.
    Journal of inherited metabolic disease, 1984, Volume: 7, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Female; Glycine; Hemiterpenes; Humans; Infant, Newborn; Infant, Premature; Pentanoic Acids; Valerates

1984
New metabolites in isovaleric acidemia.
    Clinica chimica acta; international journal of clinical chemistry, 1981, Mar-05, Volume: 110, Issue:2-3

    Topics: 4-Butyrolactone; Chemical Phenomena; Chemistry; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Infant, Newborn; Male; Maleates; Metabolism, Inborn Errors; Pentanoic Acids; Valerates

1981
L-carnitine therapy in isovaleric acidemia.
    The Journal of clinical investigation, 1984, Volume: 74, Issue:6

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Chromatography, Ion Exchange; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Male; Mass Spectrometry; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1984
Effects of ammonia and organic acids on the intradental sensory nerve activity.
    Acta odontologica Scandinavica, 1983, Volume: 41, Issue:4

    Topics: Acetates; Acetic Acid; Ammonia; Animals; Butyrates; Cats; Cuspid; Dental Caries; Female; Hemiterpenes; Isobutyrates; Lactates; Male; Neural Conduction; Pentanoic Acids; Pyruvates; Tooth; Valerates

1983
Profiles of urinary volatiles from metabolic disorders characterized by unusual odors.
    Clinical chemistry, 1983, Volume: 29, Issue:10

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Chromatography, Gas; Flame Ionization; Hemiterpenes; Humans; Infant, Newborn; Maple Syrup Urine Disease; Methylamines; Pentanoic Acids; Phenylketonurias; Valerates

1983
[Isovaleric aciduria].
    Casopis lekaru ceskych, 1983, Sep-02, Volume: 122, Issue:35

    Topics: Amino Acid Metabolism, Inborn Errors; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Pentanoic Acids; Valerates

1983
Complementation studies of isovaleric acidemia and glutaric aciduria type II using cultured skin fibroblasts.
    The Journal of clinical investigation, 1983, Volume: 72, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Carbon Radioisotopes; Cell Fusion; Cell Line; Fibroblasts; Glutarates; Hemiterpenes; Humans; Oxidation-Reduction; Pentanoic Acids; Polyethylene Glycols; Valerates

1983
Role of N-acetylglutamate and acetyl-CoA in the inhibition of ureagenesis by isovaleric acid in isolated rat hepatocytes.
    Biochimica et biophysica acta, 1983, Nov-22, Volume: 761, Issue:1

    Topics: Acetyl Coenzyme A; Alanine; Animals; Glutamates; Hemiterpenes; In Vitro Techniques; Liver; Male; Ornithine; Pentanoic Acids; Rats; Rats, Inbred Strains; Urea; Valerates

1983
Isovalerylglucuronide, a new urinary metabolite in isovaleric acidemia. Identification problems due to rearrangement reactions.
    Clinica chimica acta; international journal of clinical chemistry, 1983, Oct-31, Volume: 134, Issue:1-2

    Topics: Amino Acid Metabolism, Inborn Errors; Chromatography, Gas; Glucuronates; Hemiterpenes; Humans; Hydrogen-Ion Concentration; Pentanoic Acids; Valerates

1983
Partial purification and characterization of two enzymes involved in isovaleric acid synthesis in Clostridium bifermentans.
    Journal of general microbiology, 1983, Volume: 129, Issue:10

    Topics: Carboxy-Lyases; Chromatography, Gel; Chromatography, Ion Exchange; Clostridium; Deamination; Flavin-Adenine Dinucleotide; Hemiterpenes; Hydrogen-Ion Concentration; Keto Acids; Leucine; Molecular Weight; Pentanoic Acids; Transaminases; Valerates

1983
Neonatal lethargy due to isovaleric acidemia and hyperammonemia.
    Texas medicine, 1984, Volume: 80, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Hemiterpenes; Humans; Infant, Newborn; Male; Pentanoic Acids; Sleep Stages; Valerates

1984
A simple method of determining 4-hydroxyisovaleric acid and its level in a patient with isovaleric acidemia.
    Clinica chimica acta; international journal of clinical chemistry, 1984, Apr-27, Volume: 138, Issue:3

    Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Ketosis; Pentanoic Acids; Valerates

1984
[Biochemistry of the evolutive cycle of Triatoma infestans (vinchuca). V. Volatile fatty acids emission].
    Acta physiologica latino americana, 1981, Volume: 31, Issue:2

    Topics: Acetates; Animals; Butyrates; Caproates; Caprylates; Fatty Acids, Volatile; Female; Hemiterpenes; Isobutyrates; Male; Pentanoic Acids; Propionates; Triatoma; Triatominae; Valerates

1981
Isovalericacidemia appearing as diabetic ketoacidosis.
    American journal of diseases of children (1960), 1981, Volume: 135, Issue:11

    Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Diabetic Ketoacidosis; Diagnosis, Differential; Hemiterpenes; Humans; Hyperglycemia; Pentanoic Acids; Valerates

1981
Isovaleric acidaemia presenting with dwarfism, cataract and congenital abnormalities.
    Journal of inherited metabolic disease, 1982, Volume: 5, Issue:2

    Topics: Abnormalities, Multiple; Amino Acid Metabolism, Inborn Errors; Cataract; Child; Dwarfism; Female; Glycine; Hemiterpenes; Humans; Intellectual Disability; Pentanoic Acids; Valerates

1982
Organic aciduria associated with isovaleric acidemia.
    Clinical chemistry, 1983, Volume: 29, Issue:5

    Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Infant; Leucine; Pentanoic Acids; Valerates

1983
Neonatal isovaleric acidemia associated with hyperammonemia.
    Advances in experimental medicine and biology, 1982, Volume: 153

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Female; Hemiterpenes; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Liver; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Urea; Valerates

1982
Correlation between blood ammonia concentration and organic acid accumulation in isovaleric and propionic acidemia.
    Pediatrics, 1982, Volume: 69, Issue:1

    Topics: Acid-Base Imbalance; Ammonia; Hemiterpenes; Humans; Pentanoic Acids; Propionates; Valerates

1982
A mechanism of toxicity of isovaleric acid in rat liver mitochondria.
    Biochemical medicine, 1982, Volume: 27, Issue:2

    Topics: Animals; Hemiterpenes; In Vitro Techniques; Kinetics; Mitochondria, Liver; Oxidative Phosphorylation; Oxygen Consumption; Pentanoic Acids; Rats; Rats, Inbred Strains; Valerates

1982
Changing plasma and urinary organic acid levels in a patient with isovaleric acidemia during an attack.
    Pediatric research, 1982, Volume: 16, Issue:9

    Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Hydroxybutyrates; Leucine; Pentanoic Acids; Valerates

1982
[Isovaleric acidemia: identical biochemical picture in 3 patients with variable clinical manifestations].
    Tijdschrift voor kindergeneeskunde, 1982, Volume: 50, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Oxidation-Reduction; Pentanoic Acids; Valerates

1982
Cerebellar hemorrhage complicating isovaleric acidemia: a case report.
    Neurology, 1981, Volume: 31, Issue:6

    Topics: Acidosis; Cerebellar Diseases; Cerebral Hemorrhage; Female; Hemiterpenes; Humans; Infant, Newborn; Pentanoic Acids; Valerates

1981
Pharmacological studies on iridoid compounds. II. Relationship between structures and choleretic actions of iridoid compound.
    Journal of pharmacobio-dynamics, 1980, Volume: 3, Issue:10

    Topics: Animals; Bile; Cholagogues and Choleretics; Glucosides; Glycosides; Hemiterpenes; Hydrolysis; Iridoids; Male; Pentanoic Acids; Pyrans; Rats; Structure-Activity Relationship; Time Factors; Valerates

1980
3-Hydroxyisoheptanoic acid: a new metabolite in isovaleric acidemia.
    Clinica chimica acta; international journal of clinical chemistry, 1981, Jun-02, Volume: 113, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Child; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Heptanoic Acids; Humans; Magnetic Resonance Spectroscopy; Pentanoic Acids; Valerates

1981
Excretion of N-isovalerylglutamic acid in isovaleric acidemia.
    Clinica chimica acta; international journal of clinical chemistry, 1981, Oct-26, Volume: 116, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Gas Chromatography-Mass Spectrometry; Glutamates; Hemiterpenes; Humans; Pentanoic Acids; Valerates

1981
The antagonism of the toxicity of hypoglycin by glycine.
    Biochemical pharmacology, 1981, Volume: 30, Issue:20

    Topics: Animals; Blood Glucose; Body Temperature; Cyclopropanes; Fatty Acids, Volatile; Gluconeogenesis; Glycine; Hemiterpenes; Hypoglycins; Kinetics; Liver; Male; Pentanoic Acids; Rats; Rats, Inbred Strains; Valerates

1981
The pancytopenia of isovaleric acidemia.
    Pediatrics, 1980, Volume: 65, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Bone Marrow Examination; Female; Hematopoietic Stem Cells; Hemiterpenes; Humans; Infant, Newborn; Leucine; Male; Pancytopenia; Pentanoic Acids; Valerates

1980
Kinetics of thermophilic, anaerobic oxidation of straight and branched chain butyrate and valerate.
    Biotechnology and bioengineering, 2003, Oct-20, Volume: 84, Issue:2

    Topics: Acetates; Amino Acids; Anaerobiosis; Animals; Bacteria, Anaerobic; Biodegradation, Environmental; Butyrates; Catalysis; Cattle; Hemiterpenes; Isobutyrates; Kinetics; Manure; Models, Chemical; Oxidation-Reduction; Pentanoic Acids; Propionates; Proteins; Valerates

2003
Effects of dry-rolled or steam-flaked corn finishing diets with or without twenty-five percent dried distillers grains on ruminal fermentation and apparent total tract digestion.
    Journal of animal science, 2009, Volume: 87, Issue:11

    Topics: Animal Feed; Animals; Butyrates; Cattle; Digestion; Edible Grain; Feces; Fermentation; Food Handling; Gastric Juice; Hemiterpenes; Isobutyrates; Lactic Acid; Male; Pentanoic Acids; Valerates; Zea mays

2009
Mitigation of Salmonella on Pet Food Kibbles by Using Liquid and Powdered 3-Hydroxy-3-Methylbutyric Acid.
    Journal of food protection, 2017, Volume: 80, Issue:7

    Topics: Animals; Colony Count, Microbial; Dogs; Food Contamination; Food Handling; Food Microbiology; Hemiterpenes; Humans; Pentanoic Acids; Salmonella enteritidis; Valerates

2017
Biosynthesis of 3-Hydroxy-3-Methylbutyrate from l-Leucine by Whole-Cell Catalysis.
    Journal of agricultural and food chemistry, 2021, Mar-31, Volume: 69, Issue:12

    Topics: Biocatalysis; Hemiterpenes; Leucine; Pentanoic Acids; Valerates

2021