isovaleric acid has been researched along with methylmalonic acid in 14 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 6 (42.86) | 18.7374 |
| 1990's | 3 (21.43) | 18.2507 |
| 2000's | 5 (35.71) | 29.6817 |
| 2010's | 0 (0.00) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Chalmers, RA; Hind, AJ; Iles, RA | 1 |
| Algert, S; Kelts, DG; Nyhan, WL; Prodanos, C; Wolff, JA | 1 |
| Guibaud, P; Rousson, R | 1 |
| Charpentier, C; Coudé, FX; Depondt, E; Frézal, J; Mitchell, G; Munnich, A; Ogier, H; Rey, F; Rey, J; Saudubray, JM | 1 |
| Chalmers, RA; Hoppel, CL; Roe, CR; Stacey, TE | 1 |
| Briand, P; Cathelineau, L; Charpentier, C; Coudé, FX; Ogier, H; Saudubray, JM | 1 |
| Bennett, MJ; Berry, GT; Hale, DE; Stanley, CA; Treem, WR; Willi, SM | 1 |
| Hoppel, CL; Minkler, PE | 1 |
| Chalmers, RA; Down, S; Halket, JM; Mallard, WG; Przyborowska, A; Stein, SE | 1 |
| Blau, N; Bonafé, L; Burlina, AB; Chamoles, NA; Heizmann, CW; Kuster, T; Troxler, H | 1 |
| Ogier de Baulny, H; Saudubray, JM | 1 |
| Kim, KR; Lee, HJ; Paik, MJ | 1 |
| Gao, XL; Gu, XF; Han, LS; Qiu, WJ; Ye, J | 1 |
| Fuller, GG; Hsu, TT; Nishimura, S; Sonner, JM; Weng, Y; Zhao, J | 1 |
1 review(s) available for isovaleric acid and methylmalonic acid
| Article | Year |
|---|---|
Branched-chain organic acidurias.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Diagnosis, Differential; Glycine; Hemiterpenes; Humans; Infant, Newborn; Malonates; Maple Syrup Urine Disease; Methylmalonic Acid; Pentanoic Acids; Prognosis; Propionates | 2002 |
13 other study(ies) available for isovaleric acid and methylmalonic acid
| Article | Year |
|---|---|
Use of proton nuclear magnetic resonance spectroscopy in detection and study of organic acidurias.
Topics: Amino Acid Metabolism, Inborn Errors; Carboxylic Acids; Child, Preschool; Glutarates; Hemiterpenes; Humans; Magnetic Resonance Spectroscopy; Male; Maple Syrup Urine Disease; Methylmalonic Acid; Pentanoic Acids; Propionates; Protons | 1985 |
Alanine decreases the protein requirements of infants with inborn errors of amino acid metabolism.
Topics: Alanine; Amino Acid Metabolism, Inborn Errors; Amino Acids; Body Weight; Dietary Proteins; Female; Hemiterpenes; Humans; Infant; Male; Methylmalonic Acid; Ornithine Carbamoyltransferase Deficiency Disease; Pentanoic Acids; Propionates; Proteins | 1985 |
Long term outcome of organic acidurias: survey of 105 French cases (1967-1983).
Topics: Acids; Adolescent; Child; Child, Preschool; France; Hemiterpenes; Humans; Infant; Infant, Newborn; Maple Syrup Urine Disease; Metabolism, Inborn Errors; Methylmalonic Acid; Pentanoic Acids; Prognosis; Propionates; Time Factors | 1984 |
Hudson memorial lecture. Neonatal management of organic acidurias. Clinical update.
Topics: Acids; Amino Acid Metabolism, Inborn Errors; Diuresis; Exchange Transfusion, Whole Blood; Hemiterpenes; Humans; Infant, Newborn; Maple Syrup Urine Disease; Methylmalonic Acid; Pentanoic Acids; Peritoneal Dialysis; Propionates | 1984 |
Urinary excretion of l-carnitine and acylcarnitines by patients with disorders of organic acid metabolism: evidence for secondary insufficiency of l-carnitine.
Topics: Acyl-CoA Dehydrogenases; Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Carnitine; Child; Child, Preschool; Female; Hemiterpenes; Humans; Infant; Infant, Newborn; Lysine; Male; Methylmalonic Acid; Middle Aged; Pentanoic Acids; Propionates | 1984 |
Hyperammonemia secondary to hereditary organic acidurias: a study of 29 cases.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Hemiterpenes; Humans; Infant, Newborn; Methylmalonic Acid; Pentanoic Acids; Propionates; Urea | 1982 |
Renal handling of carnitine in secondary carnitine deficiency disorders.
Topics: Acyl Coenzyme A; Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenase, Long-Chain; Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Child, Preschool; Female; Hemiterpenes; Humans; Infant; Kidney; Male; Methylmalonic Acid; Mitochondria; Oxidation-Reduction; Pentanoic Acids | 1993 |
Quantification of carnitine and specific acylcarnitines by high-performance liquid chromatography: application to normal human urine and urine from patients with methylmalonic aciduria, isovaleric acidemia or medium-chain acyl-CoA dehydrogenase deficiency
Topics: Acetophenones; Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Chromatography, High Pressure Liquid; Female; Hemiterpenes; Humans; Indicators and Reagents; Infant; Methylmalonic Acid; Pentanoic Acids | 1993 |
Deconvolution gas chromatography/mass spectrometry of urinary organic acids--potential for pattern recognition and automated identification of metabolic disorders.
Topics: Acyl-CoA Dehydrogenase; Autoanalysis; Child, Preschool; Dicarboxylic Acids; Fatty Acid Desaturases; Gas Chromatography-Mass Spectrometry; Glutarates; Hemiterpenes; Humans; Infant; Meglutol; Metabolism, Inborn Errors; Methylmalonic Acid; Pattern Recognition, Automated; Pentanoic Acids; Propionates | 1999 |
Evaluation of urinary acylglycines by electrospray tandem mass spectrometry in mitochondrial energy metabolism defects and organic acidurias.
Topics: Acyl-CoA Dehydrogenase; Adolescent; Adult; Amidohydrolases; Biotinidase; Carbon-Nitrogen Ligases; Child; Child, Preschool; Fatty Acid Desaturases; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Mass Spectrometry; Meglutol; Metabolism, Inborn Errors; Methylmalonic Acid; Mitochondria; Pentanoic Acids; Propionates | 2000 |
Simultaneous retention index analysis of urinary amino acids and carboxylic acids for graphic recognition of abnormal state.
Topics: Acetamides; Amino Acids; Carboxylic Acids; Child; Child, Preschool; Chromatography, Gas; Fluoroacetates; Hemiterpenes; Humans; Hydroxylamines; Infant; Maple Syrup Urine Disease; Metabolism, Inborn Errors; Methylmalonic Acid; Organosilicon Compounds; Pentanoic Acids; Phenylketonurias; Trifluoroacetic Acid | 2005 |
[Application of tandem mass spectrometry in diagnosis of organic acidemias].
Topics: Adolescent; Child; Child, Preschool; Female; Filtration; Gas Chromatography-Mass Spectrometry; Glutarates; Hemiterpenes; Humans; Infant; Male; Metabolism, Inborn Errors; Methylmalonic Acid; Pentanoic Acids; Propionic Acidemia; Tandem Mass Spectrometry | 2005 |
Isovaleric, methylmalonic, and propionic acid decrease anesthetic EC50 in tadpoles, modulate glycine receptor function, and interact with the lipid 1,2-dipalmitoyl-Sn-glycero-3-phosphocholine.
Topics: 1,2-Dipalmitoylphosphatidylcholine; Anesthetics, Inhalation; Animals; Cell Membrane; Chlorides; Dose-Response Relationship, Drug; Female; Hemiterpenes; Isoflurane; Larva; Membrane Potentials; Methylmalonic Acid; Mutation; Pentanoic Acids; Pressure; Propionates; Receptors, GABA-A; Receptors, Glycine; Surface Properties; Xenopus laevis | 2009 |