isovaleric acid has been researched along with leucine in 39 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 18 (46.15) | 18.7374 |
1990's | 4 (10.26) | 18.2507 |
2000's | 11 (28.21) | 29.6817 |
2010's | 3 (7.69) | 24.3611 |
2020's | 3 (7.69) | 2.80 |
Authors | Studies |
---|---|
Tanaka, K | 1 |
Dembure, P; Elsas, L; Madsen, K; Naglak, M; Salvo, R | 1 |
Elsas, LJ; Naglak, M | 1 |
Hyman, D; Ikeda, Y; Matsubara, Y; Tanaka, K | 1 |
Ruchim, MA; Zarling, EJ | 1 |
Pollitt, RJ | 1 |
Hyman, DB; Tanaka, K | 1 |
Hagberg, B; Hjalmarson, O; Lindstedt, S; Ransnäs, L; Steen, G | 1 |
Allison, MJ; Baetz, AL; Wiegel, J | 1 |
Duran, M; Houstková, H; Hyánek, J; Kozich, V; Pĕtová, J; Pisacka, M; Rubín, A; Wadman, SK; Zapadlo, M; Zeman, J | 1 |
Britz, ML; Wilkinson, RG | 3 |
French, NP; Grauaug, A; Wysocki, SJ | 1 |
Inoue, Y; Kameyama, J; Momoi, T; Shigematsu, Y; Sudo, M; Suzuki, Y | 1 |
Bakkeren, JA; Houben, ML; Ruitenbeek, W; Sengers, RC; Trijbels, JM; Van der Zeè, SP | 1 |
August, CS; Cohn, RM; Hutchinson, R; Kelleher, JF; Yudkoff, M | 1 |
Fries, MH; Jurecki, E; Packman, S; Rinaldo, P; Schmidt-Sommerfeld, E | 1 |
Ito, T; Itoh, T; Kidouchi, K; Mizuguchi, K; Ohba, S; Sugiyama, N; Yamaguchi, S | 1 |
Chalmers, RA; Harrison, EL; Jones, MG; Lee, PJ; Leonard, JV; Whipp, BJ | 1 |
Vockley, J; Volchenboum, SL | 1 |
Maillard, MB; Thierry, A; Yvon, M | 1 |
Yang, CM | 1 |
Ikeda, Y; Kondo, S; Naganawa, H; Umezawa, K | 1 |
WOOLF, LI | 1 |
ACHENBACH, H; GRISEBACH, H | 1 |
Acun, C; Aktuglu, C; Aydin, K; Demirel, F; Sogut, A; Tomac, N; Tomsac, N | 1 |
Beck, HC; Hansen, AM; Lauritsen, FR | 1 |
Berry, SA; Burton, BK; Edland, SD; Ensenauer, R; Grünert, S; Hahn, S; Huey, JC; Koch, HG; Marquardt, I; Matern, D; Rinaldo, P; Santer, R; Sass, JO; Vockley, J; Willard, JM | 1 |
Gnau, V; Höschle, B; Jendrossek, D | 1 |
Aguilar, JA; Campos-García, J; Cervantes, C; Díaz-Pérez, AL; Díaz-Pérez, C; Zavala, AN | 1 |
Armbruster, W; Bott, M; Förster-Fromme, K; Höschle, B; Jendrossek, D; Mack, C | 1 |
Antuzzi, D; Castorina, M; Ricci, R; Rigante, D; Sciascia Cannizzaro, G | 1 |
Ishida, Y; Kuroyanagi, M; Nakane, T; Sekita, S; Shirota, O; Someya, K; Tokita, F | 1 |
Corsetti, A; Ehrmann, M; Guerzoni, ME; Ndagijimana, M; Sado-Kamdem, SL; Serrazanetti, DI; Vogel, RF | 1 |
Ching, CB; Mishra, P; Yuan, J | 1 |
Gao, R; Li, Z | 1 |
Hazenkamp, M; Kluttig, M; Mayer, S; Ochs, D | 1 |
He, A; Shen, X; Shi, C; Wan, Y; Wu, X; Yang, J; Zhou, Y; Zhu, X | 1 |
1 review(s) available for isovaleric acid and leucine
Article | Year |
---|---|
Molecular basis of isovaleric acidemia and the study of the acyl-CoA dehydrogenase family.
Topics: Acyl-CoA Dehydrogenases; Animals; DNA; Hemiterpenes; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Leucine; Mitochondria, Liver; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Phenotype; Protein Biosynthesis; Protein Processing, Post-Translational; Rats; Valerates | 1988 |
38 other study(ies) available for isovaleric acid and leucine
Article | Year |
---|---|
Isovaleric acidemia: personal history, clinical survey and study of the molecular basis.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Cell Line; Child, Preschool; Female; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Prognosis; Valerates | 1990 |
The treatment of isovaleric acidemia with glycine supplement.
Topics: Carbon Dioxide; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates | 1988 |
Acute and chronic-intermittent isovaleric acidemia: diagnosis and glycine therapy.
Topics: Acute Disease; Child; Child, Preschool; Chronic Disease; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates | 1988 |
Protein origin of the volatile fatty acids isobutyrate and isovalerate in human stool.
Topics: Albumins; Butyrates; Fatty Acids, Volatile; Feces; Hemiterpenes; Humans; Hydrogen-Ion Concentration; Isobutyrates; Leucine; Male; Pentanoic Acids; Proteins; Valerates; Valine | 1987 |
Endogenous catabolism as source of toxic metabolites in isovaleric acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Dietary Proteins; Hemiterpenes; Humans; Leucine; Pentanoic Acids; Valerates | 1987 |
Isovaleryl-CoA dehydrogenase activity in isovaleric acidemia fibroblasts using an improved tritium release assay.
Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Fibroblasts; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Kinetics; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Skin; Tritium; Valerates | 1986 |
3-Methylglutaconic aciduria in two infants.
Topics: Creatinine; Female; Fibroblasts; Glutarates; Hemiterpenes; Humans; Hydroxymethylglutaryl-CoA Synthase; Infant; Leucine; Leukocytes; Meglutol; Metabolism, Inborn Errors; Pentanoic Acids | 1983 |
Alternative pathways for biosynthesis of leucine and other amino acids in Bacteroides ruminicola and Bacteroides fragilis.
Topics: 2-Isopropylmalate Synthase; Amino Acids; Animals; Bacteroides; Bacteroides fragilis; Carbon Dioxide; Carbon Radioisotopes; Hemiterpenes; Leucine; Pentanoic Acids; Rumen | 1984 |
[Isovaleric aciduria].
Topics: Amino Acid Metabolism, Inborn Errors; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Pentanoic Acids; Valerates | 1983 |
Partial purification and characterization of two enzymes involved in isovaleric acid synthesis in Clostridium bifermentans.
Topics: Carboxy-Lyases; Chromatography, Gel; Chromatography, Ion Exchange; Clostridium; Deamination; Flavin-Adenine Dinucleotide; Hemiterpenes; Hydrogen-Ion Concentration; Keto Acids; Leucine; Molecular Weight; Pentanoic Acids; Transaminases; Valerates | 1983 |
Leucine dissimilation to isovaleric and isocaproic acids by cell suspensions of amino acid fermenting anaerobes: the Stickland reaction revisited.
Topics: Amino Acids; Caproates; Carbon Dioxide; Clostridium; Clostridium botulinum; Glucose; Hemiterpenes; Hydrogen-Ion Concentration; Kinetics; Leucine; Pentanoic Acids; Peptostreptococcus; Quaternary Ammonium Compounds | 1982 |
Organic aciduria associated with isovaleric acidemia.
Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Infant; Leucine; Pentanoic Acids; Valerates | 1983 |
Subcellular location of enzymes involved in leucine dissimilation in Clostridium bifermentans.
Topics: Caproates; Clostridium; Hemiterpenes; Leucine; Molecular Weight; Pentanoic Acids | 1983 |
Changing plasma and urinary organic acid levels in a patient with isovaleric acidemia during an attack.
Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Hydroxybutyrates; Leucine; Pentanoic Acids; Valerates | 1982 |
[Isovaleric acidemia: identical biochemical picture in 3 patients with variable clinical manifestations].
Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Oxidation-Reduction; Pentanoic Acids; Valerates | 1982 |
The pancytopenia of isovaleric acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Bone Marrow Examination; Female; Hematopoietic Stem Cells; Hemiterpenes; Humans; Infant, Newborn; Leucine; Male; Pancytopenia; Pentanoic Acids; Valerates | 1980 |
Isovaleric acidemia: response to a leucine load after three weeks of supplementation with glycine, L-carnitine, and combined glycine-carnitine therapy.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids | 1996 |
Effect of carnitine administration on glycine metabolism in patients with isovaleric acidemia: significance of acetylcarnitine determination to estimate the proper carnitine dose.
Topics: Acetylcarnitine; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biomarkers; Carnitine; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Leucine; Male; Pentanoic Acids | 1996 |
Improvement in exercise tolerance in isovaleric acidaemia with L-carnitine therapy.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Exercise; Female; Hemiterpenes; Humans; Leucine; Pentanoic Acids | 1998 |
Mitochondrial import and processing of wild type and type III mutant isovaleryl-CoA dehydrogenase.
Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Amino Acid Sequence; Biological Transport; Enzyme Stability; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Mitochondria; Models, Molecular; Molecular Sequence Data; Mutation; Open Reading Frames; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Protein Conformation; Protein Processing, Post-Translational; Sequence Homology, Amino Acid | 2000 |
Conversion of L-leucine to isovaleric acid by Propionibacterium freudenreichii TL 34 and ITGP23.
Topics: Cheese; Culture Media; Hemiterpenes; Keto Acids; Leucine; Pentanoic Acids; Propionibacterium | 2002 |
Response of forage fiber degradation by ruminal microorganisms to branched-chain volatile fatty acids, amino acids, and dipeptides.
Topics: Amino Acids; Animal Feed; Animals; Bacteria; Butyrates; Cattle; Dietary Fiber; Digestion; Dipeptides; Fatty Acids, Volatile; Hemiterpenes; Isobutyrates; Kinetics; Leucine; Male; Medicago sativa; Pentanoic Acids; Poaceae; Rumen; Silage; Valine | 2002 |
Biosynthesis of the lipophilic side chain in the cyclic hexadepsipeptide antibiotic IC101.
Topics: Acetates; Anti-Bacterial Agents; Fermentation; Hemiterpenes; Leucine; Models, Molecular; Molecular Structure; Pentanoic Acids; Peptides; Peptides, Cyclic; Streptomyces; Structure-Activity Relationship | 2002 |
The hypoglycaemic effect of leucine and isovaleric acid.
Topics: Blood Glucose; Fatty Acids; Hemiterpenes; Humans; Hypoglycemic Agents; Leucine; Pentanoic Acids | 1960 |
[On the origin of isovaleric acid in magnamycin].
Topics: Hemiterpenes; Humans; Hypnotics and Sedatives; Leucine; Leucomycins; Pentanoic Acids; Valerian | 1963 |
Isovaleric acidaemia: cranial CT and MRI findings.
Topics: Amino Acid Metabolism, Inborn Errors; Brain; Female; Hemiterpenes; Humans; Infant; Isovaleryl-CoA Dehydrogenase; Leucine; Magnetic Resonance Imaging; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Tomography, X-Ray Computed | 2004 |
Catabolism of leucine to branched-chain fatty acids in Staphylococcus xylosus.
Topics: Cell Membrane; Chromatography; Culture Media; Fatty Acids; Flavoring Agents; Food Microbiology; Glucose; Hemiterpenes; Isoleucine; Keto Acids; Leucine; Meat Products; Oxidation-Reduction; Pentanoic Acids; Pyruvic Acid; Staphylococcus; Valine | 2004 |
A common mutation is associated with a mild, potentially asymptomatic phenotype in patients with isovaleric acidemia diagnosed by newborn screening.
Topics: Algorithms; DNA Primers; Genotype; Hemiterpenes; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Leucine; Mass Spectrometry; Metabolism, Inborn Errors; Mutation; Neonatal Screening; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Restriction Mapping | 2004 |
Methylcrotonyl-CoA and geranyl-CoA carboxylases are involved in leucine/isovalerate utilization (Liu) and acyclic terpene utilization (Atu), and are encoded by liuB/liuD and atuC/atuF, in Pseudomonas aeruginosa.
Topics: Acyclic Monoterpenes; Bacterial Proteins; Biotin; Carbon-Carbon Ligases; Culture Media; Hemiterpenes; Leucine; Monoterpenes; Multigene Family; Pentanoic Acids; Pseudomonas aeruginosa; Terpenes | 2005 |
The atu and liu clusters are involved in the catabolic pathways for acyclic monoterpenes and leucine in Pseudomonas aeruginosa.
Topics: Acyclic Monoterpenes; Bacterial Proteins; Carbon-Carbon Ligases; Evolution, Molecular; Hemiterpenes; Leucine; Monoterpenes; Multigene Family; Mutation; Pentanoic Acids; Phylogeny; Pseudomonas aeruginosa; Sequence Analysis, DNA | 2006 |
Identification of genes and proteins necessary for catabolism of acyclic terpenes and leucine/isovalerate in Pseudomonas aeruginosa.
Topics: Acyclic Monoterpenes; Bacterial Proteins; Blotting, Western; Carbon-Carbon Ligases; DNA Transposable Elements; Electrophoresis, Gel, Two-Dimensional; Hemiterpenes; Leucine; Monoterpenes; Multigene Family; Mutagenesis, Insertional; Pentanoic Acids; Pseudomonas aeruginosa; Terpenes | 2006 |
Different outcome in isovaleric acidemia might be related to unsatisfactory diet compliance.
Topics: Amino Acid Metabolism, Inborn Errors; Child; Diet, Protein-Restricted; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Patient Compliance; Pentanoic Acids | 2008 |
Polyprenylated benzoylphloroglucinol-type derivatives including novel cage compounds from Hypericum erectum.
Topics: Corynebacterium; Cyclization; Hemiterpenes; Hypericum; Leucine; Molecular Conformation; Pentanoic Acids; Phloroglucinol; Stereoisomerism | 2010 |
Acid stress-mediated metabolic shift in Lactobacillus sanfranciscensis LSCE1.
Topics: Amino Acids, Branched-Chain; Butyrates; Carbohydrate Metabolism; Chromatography, Gas; Gas Chromatography-Mass Spectrometry; Gene Expression; Hemiterpenes; Hydrogen-Ion Concentration; Lactobacillus; Leucine; Pentanoic Acids; Reverse Transcriptase Polymerase Chain Reaction; Stress, Physiological | 2011 |
Engineering the leucine biosynthetic pathway for isoamyl alcohol overproduction in Saccharomyces cerevisiae.
Topics: 1-Butanol; Biosynthetic Pathways; Butanols; Cytosol; Genetic Engineering; Hemiterpenes; Hydro-Lyases; Leucine; Metabolic Networks and Pathways; Pentanoic Acids; Pentanols; Plasmids; Polymerase Chain Reaction; Proteins; RNA; Saccharomyces cerevisiae | 2017 |
Biosynthesis of 3-Hydroxy-3-Methylbutyrate from l-Leucine by Whole-Cell Catalysis.
Topics: Biocatalysis; Hemiterpenes; Leucine; Pentanoic Acids; Valerates | 2021 |
Inhibition of microbial production of the malodorous substance isovaleric acid by 4,4' dichloro 2-hydroxydiphenyl ether (DCPP).
Topics: Anti-Infective Agents; Corynebacterium; Hemiterpenes; Humans; Laundering; Leucine; Odorants; Oligopeptides; Pentanoic Acids; Proline; Pyridines; Skin; Staphylococcus aureus; Textiles | 2021 |
Urinary metabolites associate with the presence of diabetic kidney disease in type 2 diabetes and mediate the effect of inflammation on kidney complication.
Topics: Biomarkers; Diabetes Mellitus, Type 2; Diabetic Nephropathies; Humans; Inflammation; Interleukin-18; Kidney; Leucine | 2023 |