Page last updated: 2024-08-21

isovaleric acid and leucine

isovaleric acid has been researched along with leucine in 39 studies

Research

Studies (39)

TimeframeStudies, this research(%)All Research%
pre-199018 (46.15)18.7374
1990's4 (10.26)18.2507
2000's11 (28.21)29.6817
2010's3 (7.69)24.3611
2020's3 (7.69)2.80

Authors

AuthorsStudies
Tanaka, K1
Dembure, P; Elsas, L; Madsen, K; Naglak, M; Salvo, R1
Elsas, LJ; Naglak, M1
Hyman, D; Ikeda, Y; Matsubara, Y; Tanaka, K1
Ruchim, MA; Zarling, EJ1
Pollitt, RJ1
Hyman, DB; Tanaka, K1
Hagberg, B; Hjalmarson, O; Lindstedt, S; Ransnäs, L; Steen, G1
Allison, MJ; Baetz, AL; Wiegel, J1
Duran, M; Houstková, H; Hyánek, J; Kozich, V; Pĕtová, J; Pisacka, M; Rubín, A; Wadman, SK; Zapadlo, M; Zeman, J1
Britz, ML; Wilkinson, RG3
French, NP; Grauaug, A; Wysocki, SJ1
Inoue, Y; Kameyama, J; Momoi, T; Shigematsu, Y; Sudo, M; Suzuki, Y1
Bakkeren, JA; Houben, ML; Ruitenbeek, W; Sengers, RC; Trijbels, JM; Van der Zeè, SP1
August, CS; Cohn, RM; Hutchinson, R; Kelleher, JF; Yudkoff, M1
Fries, MH; Jurecki, E; Packman, S; Rinaldo, P; Schmidt-Sommerfeld, E1
Ito, T; Itoh, T; Kidouchi, K; Mizuguchi, K; Ohba, S; Sugiyama, N; Yamaguchi, S1
Chalmers, RA; Harrison, EL; Jones, MG; Lee, PJ; Leonard, JV; Whipp, BJ1
Vockley, J; Volchenboum, SL1
Maillard, MB; Thierry, A; Yvon, M1
Yang, CM1
Ikeda, Y; Kondo, S; Naganawa, H; Umezawa, K1
WOOLF, LI1
ACHENBACH, H; GRISEBACH, H1
Acun, C; Aktuglu, C; Aydin, K; Demirel, F; Sogut, A; Tomac, N; Tomsac, N1
Beck, HC; Hansen, AM; Lauritsen, FR1
Berry, SA; Burton, BK; Edland, SD; Ensenauer, R; Grünert, S; Hahn, S; Huey, JC; Koch, HG; Marquardt, I; Matern, D; Rinaldo, P; Santer, R; Sass, JO; Vockley, J; Willard, JM1
Gnau, V; Höschle, B; Jendrossek, D1
Aguilar, JA; Campos-García, J; Cervantes, C; Díaz-Pérez, AL; Díaz-Pérez, C; Zavala, AN1
Armbruster, W; Bott, M; Förster-Fromme, K; Höschle, B; Jendrossek, D; Mack, C1
Antuzzi, D; Castorina, M; Ricci, R; Rigante, D; Sciascia Cannizzaro, G1
Ishida, Y; Kuroyanagi, M; Nakane, T; Sekita, S; Shirota, O; Someya, K; Tokita, F1
Corsetti, A; Ehrmann, M; Guerzoni, ME; Ndagijimana, M; Sado-Kamdem, SL; Serrazanetti, DI; Vogel, RF1
Ching, CB; Mishra, P; Yuan, J1
Gao, R; Li, Z1
Hazenkamp, M; Kluttig, M; Mayer, S; Ochs, D1
He, A; Shen, X; Shi, C; Wan, Y; Wu, X; Yang, J; Zhou, Y; Zhu, X1

Reviews

1 review(s) available for isovaleric acid and leucine

ArticleYear
Molecular basis of isovaleric acidemia and the study of the acyl-CoA dehydrogenase family.
    Advances in neurology, 1988, Volume: 48

    Topics: Acyl-CoA Dehydrogenases; Animals; DNA; Hemiterpenes; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Leucine; Mitochondria, Liver; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Phenotype; Protein Biosynthesis; Protein Processing, Post-Translational; Rats; Valerates

1988

Other Studies

38 other study(ies) available for isovaleric acid and leucine

ArticleYear
Isovaleric acidemia: personal history, clinical survey and study of the molecular basis.
    Progress in clinical and biological research, 1990, Volume: 321

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Cell Line; Child, Preschool; Female; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Prognosis; Valerates

1990
The treatment of isovaleric acidemia with glycine supplement.
    Pediatric research, 1988, Volume: 24, Issue:1

    Topics: Carbon Dioxide; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1988
Acute and chronic-intermittent isovaleric acidemia: diagnosis and glycine therapy.
    Acta paediatrica Japonica : Overseas edition, 1988, Volume: 30, Issue:4

    Topics: Acute Disease; Child; Child, Preschool; Chronic Disease; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1988
Protein origin of the volatile fatty acids isobutyrate and isovalerate in human stool.
    The Journal of laboratory and clinical medicine, 1987, Volume: 109, Issue:5

    Topics: Albumins; Butyrates; Fatty Acids, Volatile; Feces; Hemiterpenes; Humans; Hydrogen-Ion Concentration; Isobutyrates; Leucine; Male; Pentanoic Acids; Proteins; Valerates; Valine

1987
Endogenous catabolism as source of toxic metabolites in isovaleric acidemia.
    The Journal of pediatrics, 1987, Volume: 111, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Dietary Proteins; Hemiterpenes; Humans; Leucine; Pentanoic Acids; Valerates

1987
Isovaleryl-CoA dehydrogenase activity in isovaleric acidemia fibroblasts using an improved tritium release assay.
    Pediatric research, 1986, Volume: 20, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Fibroblasts; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Kinetics; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Skin; Tritium; Valerates

1986
3-Methylglutaconic aciduria in two infants.
    Clinica chimica acta; international journal of clinical chemistry, 1983, Oct-31, Volume: 134, Issue:1-2

    Topics: Creatinine; Female; Fibroblasts; Glutarates; Hemiterpenes; Humans; Hydroxymethylglutaryl-CoA Synthase; Infant; Leucine; Leukocytes; Meglutol; Metabolism, Inborn Errors; Pentanoic Acids

1983
Alternative pathways for biosynthesis of leucine and other amino acids in Bacteroides ruminicola and Bacteroides fragilis.
    Applied and environmental microbiology, 1984, Volume: 48, Issue:6

    Topics: 2-Isopropylmalate Synthase; Amino Acids; Animals; Bacteroides; Bacteroides fragilis; Carbon Dioxide; Carbon Radioisotopes; Hemiterpenes; Leucine; Pentanoic Acids; Rumen

1984
[Isovaleric aciduria].
    Casopis lekaru ceskych, 1983, Sep-02, Volume: 122, Issue:35

    Topics: Amino Acid Metabolism, Inborn Errors; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Pentanoic Acids; Valerates

1983
Partial purification and characterization of two enzymes involved in isovaleric acid synthesis in Clostridium bifermentans.
    Journal of general microbiology, 1983, Volume: 129, Issue:10

    Topics: Carboxy-Lyases; Chromatography, Gel; Chromatography, Ion Exchange; Clostridium; Deamination; Flavin-Adenine Dinucleotide; Hemiterpenes; Hydrogen-Ion Concentration; Keto Acids; Leucine; Molecular Weight; Pentanoic Acids; Transaminases; Valerates

1983
Leucine dissimilation to isovaleric and isocaproic acids by cell suspensions of amino acid fermenting anaerobes: the Stickland reaction revisited.
    Canadian journal of microbiology, 1982, Volume: 28, Issue:3

    Topics: Amino Acids; Caproates; Carbon Dioxide; Clostridium; Clostridium botulinum; Glucose; Hemiterpenes; Hydrogen-Ion Concentration; Kinetics; Leucine; Pentanoic Acids; Peptostreptococcus; Quaternary Ammonium Compounds

1982
Organic aciduria associated with isovaleric acidemia.
    Clinical chemistry, 1983, Volume: 29, Issue:5

    Topics: Acidosis; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Infant; Leucine; Pentanoic Acids; Valerates

1983
Subcellular location of enzymes involved in leucine dissimilation in Clostridium bifermentans.
    Canadian journal of microbiology, 1983, Volume: 29, Issue:4

    Topics: Caproates; Clostridium; Hemiterpenes; Leucine; Molecular Weight; Pentanoic Acids

1983
Changing plasma and urinary organic acid levels in a patient with isovaleric acidemia during an attack.
    Pediatric research, 1982, Volume: 16, Issue:9

    Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Hydroxybutyrates; Leucine; Pentanoic Acids; Valerates

1982
[Isovaleric acidemia: identical biochemical picture in 3 patients with variable clinical manifestations].
    Tijdschrift voor kindergeneeskunde, 1982, Volume: 50, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Oxidation-Reduction; Pentanoic Acids; Valerates

1982
The pancytopenia of isovaleric acidemia.
    Pediatrics, 1980, Volume: 65, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Bone Marrow Examination; Female; Hematopoietic Stem Cells; Hemiterpenes; Humans; Infant, Newborn; Leucine; Male; Pancytopenia; Pentanoic Acids; Valerates

1980
Isovaleric acidemia: response to a leucine load after three weeks of supplementation with glycine, L-carnitine, and combined glycine-carnitine therapy.
    The Journal of pediatrics, 1996, Volume: 129, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids

1996
Effect of carnitine administration on glycine metabolism in patients with isovaleric acidemia: significance of acetylcarnitine determination to estimate the proper carnitine dose.
    The Tohoku journal of experimental medicine, 1996, Volume: 179, Issue:2

    Topics: Acetylcarnitine; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biomarkers; Carnitine; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Leucine; Male; Pentanoic Acids

1996
Improvement in exercise tolerance in isovaleric acidaemia with L-carnitine therapy.
    Journal of inherited metabolic disease, 1998, Volume: 21, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Exercise; Female; Hemiterpenes; Humans; Leucine; Pentanoic Acids

1998
Mitochondrial import and processing of wild type and type III mutant isovaleryl-CoA dehydrogenase.
    The Journal of biological chemistry, 2000, Mar-17, Volume: 275, Issue:11

    Topics: Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Amino Acid Sequence; Biological Transport; Enzyme Stability; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Mitochondria; Models, Molecular; Molecular Sequence Data; Mutation; Open Reading Frames; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Protein Conformation; Protein Processing, Post-Translational; Sequence Homology, Amino Acid

2000
Conversion of L-leucine to isovaleric acid by Propionibacterium freudenreichii TL 34 and ITGP23.
    Applied and environmental microbiology, 2002, Volume: 68, Issue:2

    Topics: Cheese; Culture Media; Hemiterpenes; Keto Acids; Leucine; Pentanoic Acids; Propionibacterium

2002
Response of forage fiber degradation by ruminal microorganisms to branched-chain volatile fatty acids, amino acids, and dipeptides.
    Journal of dairy science, 2002, Volume: 85, Issue:5

    Topics: Amino Acids; Animal Feed; Animals; Bacteria; Butyrates; Cattle; Dietary Fiber; Digestion; Dipeptides; Fatty Acids, Volatile; Hemiterpenes; Isobutyrates; Kinetics; Leucine; Male; Medicago sativa; Pentanoic Acids; Poaceae; Rumen; Silage; Valine

2002
Biosynthesis of the lipophilic side chain in the cyclic hexadepsipeptide antibiotic IC101.
    Journal of natural products, 2002, Volume: 65, Issue:12

    Topics: Acetates; Anti-Bacterial Agents; Fermentation; Hemiterpenes; Leucine; Models, Molecular; Molecular Structure; Pentanoic Acids; Peptides; Peptides, Cyclic; Streptomyces; Structure-Activity Relationship

2002
The hypoglycaemic effect of leucine and isovaleric acid.
    Clinica chimica acta; international journal of clinical chemistry, 1960, Volume: 5

    Topics: Blood Glucose; Fatty Acids; Hemiterpenes; Humans; Hypoglycemic Agents; Leucine; Pentanoic Acids

1960
[On the origin of isovaleric acid in magnamycin].
    Experientia, 1963, Jan-15, Volume: 19

    Topics: Hemiterpenes; Humans; Hypnotics and Sedatives; Leucine; Leucomycins; Pentanoic Acids; Valerian

1963
Isovaleric acidaemia: cranial CT and MRI findings.
    Pediatric radiology, 2004, Volume: 34, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Brain; Female; Hemiterpenes; Humans; Infant; Isovaleryl-CoA Dehydrogenase; Leucine; Magnetic Resonance Imaging; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Tomography, X-Ray Computed

2004
Catabolism of leucine to branched-chain fatty acids in Staphylococcus xylosus.
    Journal of applied microbiology, 2004, Volume: 96, Issue:5

    Topics: Cell Membrane; Chromatography; Culture Media; Fatty Acids; Flavoring Agents; Food Microbiology; Glucose; Hemiterpenes; Isoleucine; Keto Acids; Leucine; Meat Products; Oxidation-Reduction; Pentanoic Acids; Pyruvic Acid; Staphylococcus; Valine

2004
A common mutation is associated with a mild, potentially asymptomatic phenotype in patients with isovaleric acidemia diagnosed by newborn screening.
    American journal of human genetics, 2004, Volume: 75, Issue:6

    Topics: Algorithms; DNA Primers; Genotype; Hemiterpenes; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Leucine; Mass Spectrometry; Metabolism, Inborn Errors; Mutation; Neonatal Screening; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Restriction Mapping

2004
Methylcrotonyl-CoA and geranyl-CoA carboxylases are involved in leucine/isovalerate utilization (Liu) and acyclic terpene utilization (Atu), and are encoded by liuB/liuD and atuC/atuF, in Pseudomonas aeruginosa.
    Microbiology (Reading, England), 2005, Volume: 151, Issue:Pt 11

    Topics: Acyclic Monoterpenes; Bacterial Proteins; Biotin; Carbon-Carbon Ligases; Culture Media; Hemiterpenes; Leucine; Monoterpenes; Multigene Family; Pentanoic Acids; Pseudomonas aeruginosa; Terpenes

2005
The atu and liu clusters are involved in the catabolic pathways for acyclic monoterpenes and leucine in Pseudomonas aeruginosa.
    Applied and environmental microbiology, 2006, Volume: 72, Issue:3

    Topics: Acyclic Monoterpenes; Bacterial Proteins; Carbon-Carbon Ligases; Evolution, Molecular; Hemiterpenes; Leucine; Monoterpenes; Multigene Family; Mutation; Pentanoic Acids; Phylogeny; Pseudomonas aeruginosa; Sequence Analysis, DNA

2006
Identification of genes and proteins necessary for catabolism of acyclic terpenes and leucine/isovalerate in Pseudomonas aeruginosa.
    Applied and environmental microbiology, 2006, Volume: 72, Issue:7

    Topics: Acyclic Monoterpenes; Bacterial Proteins; Blotting, Western; Carbon-Carbon Ligases; DNA Transposable Elements; Electrophoresis, Gel, Two-Dimensional; Hemiterpenes; Leucine; Monoterpenes; Multigene Family; Mutagenesis, Insertional; Pentanoic Acids; Pseudomonas aeruginosa; Terpenes

2006
Different outcome in isovaleric acidemia might be related to unsatisfactory diet compliance.
    Scandinavian journal of gastroenterology, 2008, Volume: 43, Issue:6

    Topics: Amino Acid Metabolism, Inborn Errors; Child; Diet, Protein-Restricted; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Patient Compliance; Pentanoic Acids

2008
Polyprenylated benzoylphloroglucinol-type derivatives including novel cage compounds from Hypericum erectum.
    Chemical & pharmaceutical bulletin, 2010, Volume: 58, Issue:3

    Topics: Corynebacterium; Cyclization; Hemiterpenes; Hypericum; Leucine; Molecular Conformation; Pentanoic Acids; Phloroglucinol; Stereoisomerism

2010
Acid stress-mediated metabolic shift in Lactobacillus sanfranciscensis LSCE1.
    Applied and environmental microbiology, 2011, Volume: 77, Issue:8

    Topics: Amino Acids, Branched-Chain; Butyrates; Carbohydrate Metabolism; Chromatography, Gas; Gas Chromatography-Mass Spectrometry; Gene Expression; Hemiterpenes; Hydrogen-Ion Concentration; Lactobacillus; Leucine; Pentanoic Acids; Reverse Transcriptase Polymerase Chain Reaction; Stress, Physiological

2011
Engineering the leucine biosynthetic pathway for isoamyl alcohol overproduction in Saccharomyces cerevisiae.
    Journal of industrial microbiology & biotechnology, 2017, Volume: 44, Issue:1

    Topics: 1-Butanol; Biosynthetic Pathways; Butanols; Cytosol; Genetic Engineering; Hemiterpenes; Hydro-Lyases; Leucine; Metabolic Networks and Pathways; Pentanoic Acids; Pentanols; Plasmids; Polymerase Chain Reaction; Proteins; RNA; Saccharomyces cerevisiae

2017
Biosynthesis of 3-Hydroxy-3-Methylbutyrate from l-Leucine by Whole-Cell Catalysis.
    Journal of agricultural and food chemistry, 2021, Mar-31, Volume: 69, Issue:12

    Topics: Biocatalysis; Hemiterpenes; Leucine; Pentanoic Acids; Valerates

2021
Inhibition of microbial production of the malodorous substance isovaleric acid by 4,4' dichloro 2-hydroxydiphenyl ether (DCPP).
    MicrobiologyOpen, 2021, Volume: 10, Issue:2

    Topics: Anti-Infective Agents; Corynebacterium; Hemiterpenes; Humans; Laundering; Leucine; Odorants; Oligopeptides; Pentanoic Acids; Proline; Pyridines; Skin; Staphylococcus aureus; Textiles

2021
Urinary metabolites associate with the presence of diabetic kidney disease in type 2 diabetes and mediate the effect of inflammation on kidney complication.
    Acta diabetologica, 2023, Volume: 60, Issue:9

    Topics: Biomarkers; Diabetes Mellitus, Type 2; Diabetic Nephropathies; Humans; Inflammation; Interleukin-18; Kidney; Leucine

2023