isovaleric acid has been researched along with glycine in 22 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 11 (50.00) | 18.7374 |
| 1990's | 7 (31.82) | 18.2507 |
| 2000's | 3 (13.64) | 29.6817 |
| 2010's | 1 (4.55) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Corbella, L; Depetris de Boldini, C; Dodelson de Kremer, R; Hliba, E; Paschini de Capra, A | 1 |
| Dan, M; Fujioka, M; Kanaoka, H; Kikawa, Y; Shigematsu, Y; Sudo, M | 1 |
| Caruso, U; Cerone, R; Pesce, F; Romano, C | 1 |
| Dembure, P; Elsas, L; Madsen, K; Naglak, M; Salvo, R | 1 |
| Elsas, LJ; Naglak, M | 1 |
| Goodman, SI; Hack, AM; Hine, DG; Tanaka, K | 1 |
| Bradley, D; Chalmers, RA; de Sousa, C; Stacey, TE; Tracey, BM; Weaver, C | 1 |
| Bradley, D; Chalmers, RA; de Sousa, C; Stacey, TE; Tracey, BM; Weaver, CM | 1 |
| Audenaert, SM; Squillaro, EJ; Wilson, WG | 1 |
| Bohan, TP; Kahler, SG; Maltby, DA; Millington, DS; Roe, CR | 1 |
| Batenburg-Plenter, AM; Bruinvis, L; Duran, M; Ketting, D; van Pelt, BC; Wadman, SK | 1 |
| Inoue, Y; Kameyama, J; Momoi, T; Shigematsu, Y; Sudo, M; Suzuki, Y | 1 |
| Bakkeren, JA; Houben, ML; Ruitenbeek, W; Sengers, RC; Trijbels, JM; Van der Zeè, SP | 1 |
| Al-Bassam, SS; Sherratt, HS | 1 |
| Barbato, R; Burlina, AB; De Tullio, R; Di Lisa, F; Menabŏ, R; Salamino, F; Siliprandi, N | 1 |
| Chiba, T; Ito, T; Kajita, M; Kidouchi, K; Niwa, T; Sugiyama, N; Wada, Y | 1 |
| Fries, MH; Jurecki, E; Packman, S; Rinaldo, P; Schmidt-Sommerfeld, E | 1 |
| Ito, T; Itoh, T; Kidouchi, K; Mizuguchi, K; Ohba, S; Sugiyama, N; Yamaguchi, S | 1 |
| Blau, N; Bonafé, L; Burlina, AB; Chamoles, NA; Heizmann, CW; Kuster, T; Troxler, H | 1 |
| Ogier de Baulny, H; Saudubray, JM | 1 |
| Amaral, AU; De Bortoli, GM; Dutra-Filho, CS; Fernandes, CG; Latini, AS; Leipnitz, G; Seminotti, B; Solano, AF; Wajner, M | 1 |
| Aldamiz-Echevarría, L; Barros, P; Belanger-Quintana, A; Blasco, J; Bueno, MA; Couce, ML; Fernández-Marmiesse, A; García-Silva, MT; Márquez-Armenteros, AM; Navarrete, R; Pérez, B; Pérez-Cerdá, C; Vitoria, I; Vives, I | 1 |
1 review(s) available for isovaleric acid and glycine
| Article | Year |
|---|---|
Branched-chain organic acidurias.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Diagnosis, Differential; Glycine; Hemiterpenes; Humans; Infant, Newborn; Malonates; Maple Syrup Urine Disease; Methylmalonic Acid; Pentanoic Acids; Prognosis; Propionates | 2002 |
21 other study(ies) available for isovaleric acid and glycine
| Article | Year |
|---|---|
[Phenotypic expression variation of isovaleric acidemia in Argentinian patients. A long term follow-up].
Topics: Acidosis; Brain; Child, Preschool; Chromatography, Thin Layer; Family; Female; Follow-Up Studies; Glycine; Hemiterpenes; Humans; Infant; Isovaleryl-CoA Dehydrogenase; Liver; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Phenotype | 1992 |
Prenatal diagnosis of isovaleric acidemia by fast atom bombardment and tandem mass spectrometry.
Topics: Amniotic Fluid; Carnitine; Female; Fetal Diseases; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Spectrometry, Mass, Fast Atom Bombardment | 1991 |
Acute neonatal isovaleric acidaemia presented without acidosis or ketonuria.
Topics: Acidosis; Dietary Proteins; Female; Glycine; Hemiterpenes; Humans; Infant; Ketones; Male; Metabolism, Inborn Errors; Pentanoic Acids | 1991 |
The treatment of isovaleric acidemia with glycine supplement.
Topics: Carbon Dioxide; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates | 1988 |
Acute and chronic-intermittent isovaleric acidemia: diagnosis and glycine therapy.
Topics: Acute Disease; Child; Child, Preschool; Chronic Disease; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates | 1988 |
Stable isotope dilution analysis of isovalerylglycine in amniotic fluid and urine and its application for the prenatal diagnosis of isovaleric acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Amniotic Fluid; Female; Gas Chromatography-Mass Spectrometry; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Risk; Valerates | 1986 |
L-carnitine and glycine therapy in isovaleric acidaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Valerates | 1985 |
The response to L-carnitine and glycine therapy in isovaleric acidaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Carboxylic Acids; Carnitine; Child, Preschool; Combined Modality Therapy; Drug Therapy, Combination; Female; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Valerates | 1986 |
Hyperammonaemia in a preterm infant with isovaleric acidaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Female; Glycine; Hemiterpenes; Humans; Infant, Newborn; Infant, Premature; Pentanoic Acids; Valerates | 1984 |
L-carnitine therapy in isovaleric acidemia.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Chromatography, Ion Exchange; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Male; Mass Spectrometry; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates | 1984 |
Isovaleric acidaemia presenting with dwarfism, cataract and congenital abnormalities.
Topics: Abnormalities, Multiple; Amino Acid Metabolism, Inborn Errors; Cataract; Child; Dwarfism; Female; Glycine; Hemiterpenes; Humans; Intellectual Disability; Pentanoic Acids; Valerates | 1982 |
Changing plasma and urinary organic acid levels in a patient with isovaleric acidemia during an attack.
Topics: Amino Acid Metabolism, Inborn Errors; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Hydroxybutyrates; Leucine; Pentanoic Acids; Valerates | 1982 |
[Isovaleric acidemia: identical biochemical picture in 3 patients with variable clinical manifestations].
Topics: Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Child; Child, Preschool; Female; Fibroblasts; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Leucine; Male; Oxidation-Reduction; Pentanoic Acids; Valerates | 1982 |
The antagonism of the toxicity of hypoglycin by glycine.
Topics: Animals; Blood Glucose; Body Temperature; Cyclopropanes; Fatty Acids, Volatile; Gluconeogenesis; Glycine; Hemiterpenes; Hypoglycins; Kinetics; Liver; Male; Pentanoic Acids; Rats; Rats, Inbred Strains; Valerates | 1981 |
Involvement of erythrocyte calpain in glycine- and carnitine-treated isovaleric acidemia.
Topics: Calpain; Carnitine; Child; Erythrocytes; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids | 1994 |
Liquid chromatographic-atmospheric pressure chemical ionization mass spectrometric analysis of glycine conjugates and urinary isovalerylglycine in isovaleric acidemia.
Topics: Acidosis; Administration, Oral; Carnitine; Child, Preschool; Chromatography, Liquid; Female; Glucuronates; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Male; Mass Spectrometry; Pentanoic Acids | 1995 |
Isovaleric acidemia: response to a leucine load after three weeks of supplementation with glycine, L-carnitine, and combined glycine-carnitine therapy.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids | 1996 |
Effect of carnitine administration on glycine metabolism in patients with isovaleric acidemia: significance of acetylcarnitine determination to estimate the proper carnitine dose.
Topics: Acetylcarnitine; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biomarkers; Carnitine; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Leucine; Male; Pentanoic Acids | 1996 |
Evaluation of urinary acylglycines by electrospray tandem mass spectrometry in mitochondrial energy metabolism defects and organic acidurias.
Topics: Acyl-CoA Dehydrogenase; Adolescent; Adult; Amidohydrolases; Biotinidase; Carbon-Nitrogen Ligases; Child; Child, Preschool; Fatty Acid Desaturases; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Mass Spectrometry; Meglutol; Metabolism, Inborn Errors; Methylmalonic Acid; Mitochondria; Pentanoic Acids; Propionates | 2000 |
Induction of oxidative stress by the metabolites accumulating in isovaleric acidemia in brain cortex of young rats.
Topics: Animals; Cerebral Cortex; Free Radical Scavengers; Glutathione; Glycine; Hemiterpenes; Lipid Peroxidation; Metabolism, Inborn Errors; Mitochondria; Oxidative Stress; Pentanoic Acids; Protein Carbonylation; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances | 2008 |
Genotype and phenotype characterization in a Spanish cohort with isovaleric acidemia.
Topics: Acute Disease; Amino Acid Metabolism, Inborn Errors; Asymptomatic Diseases; Carnitine; Child; Child, Preschool; Chronic Disease; Creatinine; Female; Fibroblasts; Gene Expression; Genetic Association Studies; Genotype; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Male; Mutation; Neonatal Screening; Pentanoic Acids; Phenotype; Prevalence; Spain | 2017 |