isovaleric acid and carnitine

Topics: Amniotic Fluid; Carnitine; Female; Fetal Diseases; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Spectrometry, Mass, Fast Atom Bombardment

Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Cell Line; Child, Preschool; Female; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Prognosis; Valerates

Topics: Carnitine; Chromatography, Liquid; Fatty Acid Desaturases; Hemiterpenes; Humans; Pentanoic Acids; Propionates; Spectrometry, Mass, Fast Atom Bombardment

Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Valerates

Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Carboxylic Acids; Carnitine; Child, Preschool; Combined Modality Therapy; Drug Therapy, Combination; Female; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Valerates

Topics: Acyl-CoA Dehydrogenases; Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Carnitine; Child; Child, Preschool; Female; Hemiterpenes; Humans; Infant; Infant, Newborn; Lysine; Male; Methylmalonic Acid; Middle Aged; Pentanoic Acids; Propionates

Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Chromatography, Ion Exchange; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Male; Mass Spectrometry; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

Topics: Calpain; Carnitine; Child; Erythrocytes; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids

Topics: Acetylcarnitine; Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Female; Hemiterpenes; Humans; Injections, Intravenous; Lipid Metabolism, Inborn Errors; Pentanoic Acids; Safety

Topics: Acyl Coenzyme A; Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenase, Long-Chain; Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Child, Preschool; Female; Hemiterpenes; Humans; Infant; Kidney; Male; Methylmalonic Acid; Mitochondria; Oxidation-Reduction; Pentanoic Acids

Topics: Acetophenones; Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Chromatography, High Pressure Liquid; Female; Hemiterpenes; Humans; Indicators and Reagents; Infant; Methylmalonic Acid; Pentanoic Acids

Topics: Acidosis; Administration, Oral; Carnitine; Child, Preschool; Chromatography, Liquid; Female; Glucuronates; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Male; Mass Spectrometry; Pentanoic Acids

Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids

Topics: Acetylcarnitine; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biomarkers; Carnitine; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Leucine; Male; Pentanoic Acids

Topics: Acyl-CoA Dehydrogenase, Long-Chain; Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Fatty Acid Desaturases; Female; Glutarates; Hemiterpenes; Humans; Infant; Male; Pentanoic Acids

Topics: Acidosis; Adolescent; Anesthesia, General; Anesthesia, Local; Anesthetics, Local; Bupivacaine; Carnitine; Electrocardiography; Female; Hemiterpenes; Humans; Intraoperative Complications; Lipectomy; Pentanoic Acids; Ventricular Dysfunction

Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Exercise; Female; Hemiterpenes; Humans; Leucine; Pentanoic Acids

Topics: Carnitine; False Positive Reactions; Female; Gas Chromatography-Mass Spectrometry; Hemiterpenes; Humans; Infant, Newborn; Mass Spectrometry; Metabolism, Inborn Errors; Neonatal Screening; Pentanoic Acids; Sulbactam; Urinary Tract Infections

Topics: Adult; Carnitine; Child; Child, Preschool; Female; Hemiterpenes; Humans; Infant; Isovaleryl-CoA Dehydrogenase; Male; Metabolism, Inborn Errors; Mutation; Pentanoic Acids; Polymorphism, Genetic; Spectrometry, Mass, Electrospray Ionization; Taiwan

Topics: Acidosis; Carnitine; Diet, Protein-Restricted; Female; Graves Disease; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Pentanoic Acids; Vitamin B Complex; Young Adult

Topics: Acute Disease; Amino Acid Metabolism, Inborn Errors; Asymptomatic Diseases; Carnitine; Child; Child, Preschool; Chronic Disease; Creatinine; Female; Fibroblasts; Gene Expression; Genetic Association Studies; Genotype; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Male; Mutation; Neonatal Screening; Pentanoic Acids; Phenotype; Prevalence; Spain

Topics: Acetates; Animals; Apolipoproteins E; Atherosclerosis; Atorvastatin; beta-Glucans; Butyrates; Cardiovascular Diseases; Carnitine; Cholesterol; Cholesterol, Dietary; Diet, High-Fat; Dietary Supplements; Feces; Gastrointestinal Microbiome; Hemiterpenes; Limosilactobacillus reuteri; Male; Metabolome; Mice; Obesity; Pentanoic Acids; Probiotics