isoleucine and carnitine

isoleucine has been researched along with carnitine in 16 studies

Research

Studies (16)

TimeframeStudies, this research(%)All Research%
pre-19903 (18.75)18.7374
1990's0 (0.00)18.2507
2000's5 (31.25)29.6817
2010's3 (18.75)24.3611
2020's5 (31.25)2.80

Authors

AuthorsStudies
Isselbacher, KJ; Miller, EM; Tanaka, K1
Bohmer, T2
Brivet, M; Roe, CR; Roe, DS; Sweetman, L1
Burlingame, TG; Gibson, KM; Hogema, B; Jakobs, C; Kiss, D; Linck, L; Millington, D; Pohowalla, P; Rinaldo, P; Roe, CR; Roe, DS; Sacks, M; Schutgens, RB; Steiner, RD; Sweetman, L; Vockley, J1
Atri, S; Jagannathan, NR; Sarkar, C; Sharma, MC; Sharma, U1
Andresen, BS; Berry, SA; He, M; Lussky, RC; Madsen, PP; Matern, D; Rinaldo, P; van Calcar, SC; Vockley, J; Whitley, CB; Wolff, JA1
Fukao, T; Hazama, A; Kohno, Y; Kondo, M; Kondo, N; Kubo, T; Matsuo, N; Sakura, N; Shigematsu, Y; Yamaga, H; Yamaguchi, S; Zhang, GX1
Aranibar, N; Cherrington, NJ; Lake, AD; Lehman-McKeeman, LD; Novak, P; Reily, MD; Robertson, DG; Shipkova, P; Vaillancourt, RR1
Artigas, A; Brunelli, L; Ferrer, R; Goma, G; Navas, A; Pastorelli, R; Ribas Ripoll, V; Romay, E1
Al-Majdoub, M; Ali, A; Carstensen, B; RidderstrÄle, M; Safai, N; Spégel, P; Suvitaival, T; Vestergaard, H1
Cowan, TM; Le, A; Mak, J1
Adams-Huet, B; Devaraj, S; Jialal, I; Patel, A1
Berman, LM; Brown, LD; Hendricks, AE; Krebs, NF; Tang, M; Weaver, NE1
Jacobs, A; Jansen Van Vuren, E; Kruger, R; Louw, R; Mels, C; Strauss-Kruger, M1
Chen, H; Cross, JR; DeVita, RJ; Dodatko, T; Dwyer, W; Houten, SM; Leandro, J; Stauffer, B; Vaz, FM; Violante, S; Yu, C1

Reviews

1 review(s) available for isoleucine and carnitine

ArticleYear
Prospective diagnosis of 2-methylbutyryl-CoA dehydrogenase deficiency in the Hmong population by newborn screening using tandem mass spectrometry.
    Pediatrics, 2003, Volume: 112, Issue:1 Pt 1

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Diagnosis, Differential; Diet, Protein-Restricted; DNA Mutational Analysis; Ethnicity; Exons; Female; Genetic Testing; Humans; Infant, Newborn; Intellectual Disability; Isoleucine; Male; Mass Spectrometry; Neonatal Screening; Oxidoreductases Acting on CH-CH Group Donors; Sequence Deletion; Treatment Outcome

2003

Trials

2 trial(s) available for isoleucine and carnitine

ArticleYear
Effect of metformin on plasma metabolite profile in the Copenhagen Insulin and Metformin Therapy (CIMT) trial.
    Diabetic medicine : a journal of the British Diabetic Association, 2018, Volume: 35, Issue:7

    Topics: Aged; Carnitine; Chromatography, Liquid; Diabetes Mellitus, Type 2; Female; Follow-Up Studies; Glycated Hemoglobin; Humans; Hypoglycemic Agents; Insulin Resistance; Isoleucine; Leucine; Lysophospholipids; Male; Mass Spectrometry; Metabolome; Metabolomics; Metformin; Middle Aged; Mitochondria; Tyrosine; Valine

2018
Different Blood Metabolomics Profiles in Infants Consuming a Meat- or Dairy-Based Complementary Diet.
    Nutrients, 2021, Jan-27, Volume: 13, Issue:2

    Topics: Amino Acids, Branched-Chain; Amino Acids, Essential; Carnitine; Dairy Products; Diet; Follow-Up Studies; Humans; Infant; Infant Nutritional Physiological Phenomena; Isoleucine; Leucine; Meat; Metabolomics; Phenylalanine; Valine

2021

Other Studies

13 other study(ies) available for isoleucine and carnitine

ArticleYear
Hypoglycin A: a specific inhibitor of isovaleryl CoA dehydrogenase.
    Proceedings of the National Academy of Sciences of the United States of America, 1971, Volume: 68, Issue:1

    Topics: Acidosis; Alanine; Amino Acid Metabolism, Inborn Errors; Animals; Butyrates; Caproates; Carbon Dioxide; Carbon Isotopes; Carnitine; Chromatography, Gas; Coenzyme A; Cyclopropanes; In Vitro Techniques; Isoleucine; Leucine; Male; Oxidoreductases; Plant Poisoning; Rats; Valerates; Vomiting

1971
The conversion of valine to propionylcarnitine in isolated rat liver mitochondria.
    Biochimica et biophysica acta, 1970, Apr-14, Volume: 208, Issue:1

    Topics: Animals; Carbon Isotopes; Carnitine; Dinitrophenols; Glucose; Hexokinase; Isoleucine; Mitochondria, Liver; Propionates; Rats; Tritium; Uncoupling Agents; Valerates; Valine

1970
The formation of propionylcarnitine in isolated rat liver mitochondria.
    Biochimica et biophysica acta, 1968, Dec-18, Volume: 164, Issue:3

    Topics: Adenine Nucleotides; Amino Acids; Aminobutyrates; Animals; Bicarbonates; Butyrates; Carbon Dioxide; Carbon Isotopes; Carnitine; Citrates; Citric Acid Cycle; Coenzyme A; Depression, Chemical; Isoleucine; Keto Acids; Ketoglutaric Acids; Male; Mitochondria, Liver; Propionates; Rats; Stimulation, Chemical; Succinates; Tritium; Valerates; Valine

1968
Evidence for a short-chain carnitine-acylcarnitine translocase in mitochondria specifically related to the metabolism of branched-chain amino acids.
    Molecular genetics and metabolism, 2000, Volume: 69, Issue:1

    Topics: Amino Acids, Branched-Chain; Biological Transport; Carnitine; Carnitine Acyltransferases; Cells, Cultured; Child; Deuterium; Fibroblasts; Humans; Intracellular Membranes; Isoleucine; Mass Spectrometry; Metabolism, Inborn Errors; Mitochondria; Oxidation-Reduction

2000
2-Methylbutyryl-coenzyme A dehydrogenase deficiency: a new inborn error of L-isoleucine metabolism.
    Pediatric research, 2000, Volume: 47, Issue:6

    Topics: Amino Acid Metabolism, Inborn Errors; Base Sequence; Carnitine; DNA Primers; DNA, Complementary; Female; Humans; Infant; Isoleucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pregnancy; Prenatal Diagnosis

2000
Skeletal muscle metabolism in Duchenne muscular dystrophy (DMD): an in-vitro proton NMR spectroscopy study.
    Magnetic resonance imaging, 2003, Volume: 21, Issue:2

    Topics: Adolescent; Adult; Carnitine; Child; Child, Preschool; Humans; Immunohistochemistry; In Vitro Techniques; Isoleucine; Magnetic Resonance Spectroscopy; Male; Muscle, Skeletal; Muscular Dystrophy, Duchenne; Valine

2003
The mitochondrial acetoacetyl-CoA thiolase (T2) deficiency in Japanese patients: urinary organic acid and blood acylcarnitine profiles under stable conditions have subtle abnormalities in T2-deficient patients with some residual T2 activity.
    Journal of inherited metabolic disease, 2003, Volume: 26, Issue:5

    Topics: Acetoacetates; Acetyl-CoA C-Acetyltransferase; Amino Acid Metabolism, Inborn Errors; Carnitine; Humans; Hydroxybutyrates; Infant; Isoleucine; Ketone Bodies; Male; Mitochondria; Mutation

2003
Branched chain amino acid metabolism profiles in progressive human nonalcoholic fatty liver disease.
    Amino acids, 2015, Volume: 47, Issue:3

    Topics: Carnitine; Female; Gene Expression Profiling; Humans; Isoleucine; Leucine; Male; Metabolomics; Non-alcoholic Fatty Liver Disease; Signal Transduction; Valine

2015
Metabolite analysis in sepsis through conditional independence maps.
    Annual International Conference of the IEEE Engineering in Medicine and Biology Society. IEEE Engineering in Medicine and Biology Society. Annual International Conference, 2015, Volume: 2015

    Topics: Adult; Aged; Algorithms; Bayes Theorem; Biomarkers; Carnitine; Computer Graphics; Critical Care; Female; Humans; Intensive Care Units; Isoleucine; Length of Stay; Male; Markov Chains; Metabolomics; Middle Aged; Models, Statistical; Patient Discharge; Probability; Prospective Studies; Sepsis; Shock, Septic

2015
Metabolic profiling by reversed-phase/ion-exchange mass spectrometry.
    Journal of chromatography. B, Analytical technologies in the biomedical and life sciences, 2020, Apr-15, Volume: 1143

    Topics: Amino Acids; Bile Acids and Salts; Carnitine; Chromatography, High Pressure Liquid; Chromatography, Ion Exchange; Chromatography, Reverse-Phase; Hormones; Humans; Hydrophobic and Hydrophilic Interactions; Isoleucine; Metabolome; Metabolomics; Methylmalonic Acid; Nucleosides; Small Molecule Libraries; Succinic Acid; Tandem Mass Spectrometry; Vitamins

2020
Metabolites that activate the inflammasome in nascent metabolic syndrome.
    Journal of diabetes and its complications, 2021, Volume: 35, Issue:3

    Topics: Adult; Carnitine; Caspase 1; Diabetes Mellitus, Type 2; gamma-Aminobutyric Acid; Humans; Inflammasomes; Isoleucine; Metabolic Syndrome; NLR Family, Pyrin Domain-Containing 3 Protein

2021
Identifying a metabolomics profile associated with masked hypertension in two independent cohorts: Data from the African-PREDICT and SABPA studies.
    Hypertension research : official journal of the Japanese Society of Hypertension, 2022, Volume: 45, Issue:11

    Topics: Amino Acids; Carnitine; Humans; Isoleucine; Leucine; Masked Hypertension; Metabolomics; Methionine; Phenylalanine; Valine

2022
Acyl-CoA dehydrogenase substrate promiscuity: Challenges and opportunities for development of substrate reduction therapy in disorders of valine and isoleucine metabolism.
    Journal of inherited metabolic disease, 2023, Volume: 46, Issue:5

    Topics: 2-Methyl-4-chlorophenoxyacetic Acid; Acyl-CoA Dehydrogenase; Carnitine; HEK293 Cells; Humans; Isoleucine; Propionic Acidemia; Valine

2023