Compounds > isoleucine

isoleucine and 2-methylbutyrylglycine

isoleucine has been researched along with 2-methylbutyrylglycine in 4 studies

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19901 (25.00)18.7374
1990's1 (25.00)18.2507
2000's2 (50.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
de Céspedes, C; Estrada, Y; Loria, AR; Nyhan, WL; Sweetman, L; Weyler, W1
Clarke, JT; Fisher, L; Lehotay, DC; Nowaczyk, MJ; Phillips, H; Platt, BA; Tan, R1
Andresen, BS; Boneh, A; Gutman, A; Korman, SH; Pitt, JJ; Zeharia, A1
Andresen, BS; Engel, K; Ensenauer, R; Häberle, J; Lehnert, W; Mégarbané, A; Reich, H; Röschinger, W; Sass, JO; Schirrmacher, O; Steuerwald, U; Zschocke, J1

Other Studies

4 other study(ies) available for isoleucine and 2-methylbutyrylglycine

ArticleYear
Abnormal metabolites of isoleucine in a patient with propionyl-CoA carboxylase deficiency.
    Biomedical mass spectrometry, 1978, Volume: 5, Issue:3

    Topics: Acetoacetates; Carboxy-Lyases; Child, Preschool; Consanguinity; Female; Glycine; Humans; Hydroxy Acids; Hydroxybutyrates; Isoleucine; Keto Acids; Pentanoic Acids; Propionates

1978
Ethylmalonic and methylsuccinic aciduria in ethylmalonic encephalopathy arise from abnormal isoleucine metabolism.
    Metabolism: clinical and experimental, 1998, Volume: 47, Issue:7

    Topics: Administration, Oral; Brain; Cells, Cultured; Child, Preschool; Female; Fibroblasts; Glycine; Humans; Isoleucine; Malonates; Metabolism, Inborn Errors; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Succinates

1998
2-ethylhydracrylic aciduria in short/branched-chain acyl-CoA dehydrogenase deficiency: application to diagnosis and implications for the R-pathway of isoleucine oxidation.
    Clinical chemistry, 2005, Volume: 51, Issue:3

    Topics: Biomarkers; Butyrates; Butyryl-CoA Dehydrogenase; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Infant, Newborn; Isoleucine; Mutation; Oxidation-Reduction; Stereoisomerism; Valerates

2005
2-Methylbutyryl-coenzyme A dehydrogenase deficiency: functional and molecular studies on a defect in isoleucine catabolism.
    Molecular genetics and metabolism, 2008, Volume: 93, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Butyryl-CoA Dehydrogenase; Cells, Cultured; Child; Child, Preschool; Female; Genotype; Glycine; Humans; Infant; Isoleucine; Male; Metabolism; Valerates

2008