homogentisic acid and phenylalanine

homogentisic acid has been researched along with phenylalanine in 18 studies

Research

Studies (18)

TimeframeStudies, this research(%)All Research%
pre-199013 (72.22)18.7374
1990's1 (5.56)18.2507
2000's1 (5.56)29.6817
2010's1 (5.56)24.3611
2020's2 (11.11)2.80

Authors

AuthorsStudies
Lähdesmäki, P; Oja, SS; Vanhatalo, A1
Hannus, ML; Lähdesmäki, P1
Athar, HS; Hasnain, SN1
Angsusingha, K; Punnakanta, L; Tuchinda, C1
Dickens, G; Guroff, G; Letendre, CH1
Lähdesmäki, P; Oja, SS1
Iijima, S; Ishii, A; Miyakoshi, T; Musha, M; Odaira, T1
Räihä, NC1
Adolphsen, P; Lenz, H; Siegenthaler, W; Zimmermann, KG1
Fisher, MJ; Pogson, CI1
Lähdesmäki, P1
Morrissey, JH1
Fällström, SP; Lindblad, B; Steen, G1
Takita, H1
Arias-Barrau, E; Díaz, E; Fernández, C; Galán, B; García, JL; Luengo, JM; Miñambres, B; Olivera, ER1
Cox, TF; Davison, AS; Gallagher, JA; Hughes, AT; Khedr, M; Milan, AM; Psarelli, EE; Ranganath, LR; Rhodes, NP; Rovensky, J1
Arnoux, JB; Braconi, D; Bygott, H; Davison, AS; Fitzgerald, R; Gallagher, JA; Genovese, F; Glasova, H; Hughes, AT; Hughes, JH; Imrich, R; Jarvis, JC; Khedr, M; Laan, D; Le Quan Sang, KH; Luangrath, E; Mankowitz, L; Milan, AM; Norman, BP; Olsson, B; Psarelli, EE; Ranganath, LR; Rhodes, NP; Rudebeck, M; Santucci, A; Shweihdi, E; Sireau, N; Stančík, R; van Kan, C; Zatkova, A1
Arnoux, JB; Bou-Gharios, G; Davison, AS; Gallagher, JA; Hughes, AT; Imrich, R; M, K; Milan, AM; Norman, BP; Olsson, B; Ranganath, LR; Rudebeck, M1

Reviews

2 review(s) available for homogentisic acid and phenylalanine

ArticleYear
Biochemical basis for nutritional management of preterm infants.
    Pediatrics, 1974, Volume: 53, Issue:2

    Topics: Acetoacetates; Adenosine Triphosphate; Amino Acids; Animals; Brain; Cyclic AMP; Cystathionine; Cystine; Enzyme Induction; Female; Fumarates; Homogentisic Acid; Humans; Hydro-Lyases; Infant Nutritional Physiological Phenomena; Infant, Newborn; Infant, Premature; Liver; Lyases; Maternal-Fetal Exchange; Methionine; Oxidoreductases; Phenylalanine; Phenylalanine Hydroxylase; Phenylpyruvic Acids; Pregnancy; S-Adenosylmethionine; Transferases; Tyrosine; Tyrosine Transaminase

1974
[Alkaptonuria (homogentisic aciduria)].
    Ryoikibetsu shokogun shirizu, 1998, Issue:18 Pt 1

    Topics: Alkaptonuria; Arthritis; Diagnosis, Differential; Dioxygenases; Homogentisate 1,2-Dioxygenase; Homogentisic Acid; Humans; Ochronosis; Oxygenases; Phenylalanine; Tyrosine

1998

Trials

1 trial(s) available for homogentisic acid and phenylalanine

ArticleYear
Quantification of the flux of tyrosine pathway metabolites during nitisinone treatment of Alkaptonuria.
    Scientific reports, 2019, 07-11, Volume: 9, Issue:1

    Topics: Adult; Alkaptonuria; Cyclohexanones; Female; Homogentisic Acid; Humans; Male; Middle Aged; Nitrobenzoates; Phenylalanine; Pigments, Biological; Tandem Mass Spectrometry; Tyrosine

2019

Other Studies

15 other study(ies) available for homogentisic acid and phenylalanine

ArticleYear
Effect of phenylpyruvate and homogentisate on the formation of aromatic aminoacyl-tRNAs.
    FEBS letters, 1977, Sep-01, Volume: 81, Issue:1

    Topics: Animals; Brain; Cattle; Depression, Chemical; Homogentisic Acid; Phenylalanine; Phenylpyruvic Acids; RNA, Transfer; RNA, Transfer, Amino Acyl; Tryptophan; Tyrosine

1977
Effect of aromatic acids on the influx of aromatic amino acids in rat brain slices.
    Experimental brain research, 1977, Dec-19, Volume: 30, Issue:4

    Topics: Animals; Brain; Dose-Response Relationship, Drug; Homogentisic Acid; In Vitro Techniques; Kinetics; Phenylalanine; Phenylpyruvic Acids; Rats; Tryptophan; Tyrosine

1977
Enzyme abnormalities in man and the role of their identification in preventive medicine.
    JPMA. The Journal of the Pakistan Medical Association, 1976, Volume: 26, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Clinical Enzyme Tests; Cystathionine; Homogentisic Acid; Humans; Metabolism, Inborn Errors; Phenylalanine; Propionates

1976
Intermittent alcaptonuria.
    Journal of the Medical Association of Thailand = Chotmaihet thangphaet, 1975, Volume: 58, Issue:5

    Topics: Alkaptonuria; Child; Homogentisic Acid; Humans; Male; Oxygenases; Phenylalanine; Tyrosine

1975
Phenylalanine hydroxylase from Pseudomonas sp. (ATCC 11299a). Purification, molecular weight, and influence of tyrosine metabolites on activation and hydroxylation.
    The Journal of biological chemistry, 1975, Sep-10, Volume: 250, Issue:17

    Topics: Enzyme Activation; Homogentisic Acid; Iron; Kinetics; Molecular Weight; Phenylacetates; Phenylalanine; Phenylalanine Hydroxylase; Phenylpyruvic Acids; Pseudomonas; Tyrosine

1975
Effect of aromatic acids on protein synthesis in subcellular preparations from the rat brain.
    Journal of neurobiology, 1975, Volume: 6, Issue:3

    Topics: Animals; Benzoates; Brain; Cell-Free System; Depression, Chemical; Homogentisic Acid; In Vitro Techniques; Nerve Tissue Proteins; Phenylacetates; Phenylalanine; Phenylpyruvic Acids; Rats; Salicylates; Transfer RNA Aminoacylation; Tryptophan; Tyrosine

1975
Studies on the experimental phenylketonuria in rats.
    The Tohoku journal of experimental medicine, 1975, Volume: 117, Issue:2

    Topics: Amino Acids; Animals; Brain Chemistry; Female; Homogentisic Acid; Humans; Liver; Phenylalanine; Phenylalanine Hydroxylase; Phenylketonurias; Phenylpyruvic Acids; Pregnancy; Rats; Transaminases; Tyrosine

1975
[Alkaptonuria and ochronosis].
    Deutsche medizinische Wochenschrift (1946), 1972, Feb-18, Volume: 97, Issue:7

    Topics: Alkaptonuria; Chemical Phenomena; Chemistry; Diagnosis, Differential; Female; Germany, West; Homogentisic Acid; Humans; Male; Middle Aged; Ochronosis; Phenols; Phenylalanine; Radiography; Sex Factors; Spinal Diseases; Tyrosine

1972
The determination of flux through phenylalanine hydroxylase and homogentisate oxidase in isolated hepatocytes.
    Bioscience reports, 1984, Volume: 4, Issue:10

    Topics: Animals; Cells, Cultured; Dioxygenases; Homogentisate 1,2-Dioxygenase; Homogentisic Acid; Kinetics; Liver; Male; Oxygenases; Phenylalanine; Phenylalanine Hydroxylase; Rats; Rats, Inbred Strains; Tyrosine

1984
Inhibition of protein and aminoacyl-tRNA synthesis, and binding and transport sites for aromatic amino acids in the brain in vitro with aromatic acids.
    The International journal of neuroscience, 1984, Volume: 23, Issue:1

    Topics: Amino Acids; Animals; Brain; Brain Chemistry; Cattle; Homogentisic Acid; In Vitro Techniques; Nerve Tissue Proteins; Phenylalanine; Phenylpyruvic Acids; Rats; Rats, Inbred Strains; RNA, Transfer, Amino Acyl; Synaptic Membranes; Synaptosomes; Tritium; Tryptophan; Tyrosine

1984
Deficiency in homogentisic acid oxidase activity associated with the brown phenotype of Dictyostelium discoideum.
    Journal of general microbiology, 1983, Volume: 129, Issue:4

    Topics: Dictyostelium; Dioxygenases; Genotype; Homogentisate 1,2-Dioxygenase; Homogentisic Acid; Mutation; Oxygenases; Phenotype; Phenylalanine; Pigmentation; Ploidies; Suppression, Genetic; Tyrosine

1983
On the renal tubular damage in hereditary tyrosinemia and on the formation of succinylacetoacetate and succinylacetone.
    Acta paediatrica Scandinavica, 1981, Volume: 70, Issue:3

    Topics: Acetoacetates; Amino Acid Metabolism, Inborn Errors; Aminolevulinic Acid; Child; Heptanoates; Homogentisic Acid; Humans; Infant; Keto Acids; Kidney Diseases; Kidney Tubules; Male; Phenylalanine; Proteinuria; Tyrosine

1981
The homogentisate pathway: a central catabolic pathway involved in the degradation of L-phenylalanine, L-tyrosine, and 3-hydroxyphenylacetate in Pseudomonas putida.
    Journal of bacteriology, 2004, Volume: 186, Issue:15

    Topics: Bacterial Proteins; Base Sequence; Biodegradation, Environmental; Gene Expression Regulation, Bacterial; Homogentisic Acid; Molecular Sequence Data; Multigene Family; Phenylacetates; Phenylalanine; Pseudomonas putida; Sequence Analysis, DNA; Tyrosine

2004
Homogentisic acid is not only eliminated by glomerular filtration and tubular secretion but also produced in the kidney in alkaptonuria.
    Journal of inherited metabolic disease, 2020, Volume: 43, Issue:4

    Topics: Adult; Alkaptonuria; Case-Control Studies; Creatinine; Female; Glomerular Filtration Rate; Homogentisic Acid; Humans; Kidney; Linear Models; Male; Middle Aged; Ochronosis; Phenylalanine; Sex Factors; Tyrosine

2020
Determinants of tyrosinaemia during nitisinone therapy in alkaptonuria.
    Scientific reports, 2022, 09-27, Volume: 12, Issue:1

    Topics: Alkaptonuria; Brain Diseases, Metabolic, Inborn; Cyclohexanones; Homogentisic Acid; Humans; Nitrobenzoates; Phenylalanine; Phenylpropionates; Tyrosine; Tyrosinemias

2022