Page last updated: 2024-08-24

homocitrulline and arginine

homocitrulline has been researched along with arginine in 12 studies

Research

Studies (12)

TimeframeStudies, this research(%)All Research%
pre-19904 (33.33)18.7374
1990's5 (41.67)18.2507
2000's2 (16.67)29.6817
2010's1 (8.33)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Shimizu, H1
Azuma, T; Higa, S; Kishimoto, S; Sakoda, S; Suzuki, T; Tsujino, S1
Hayakawa, C; Kato, T; Mizutani, N; Sano, M1
Kato, T; Mizutani, N; Sano, M1
Bachmann, C; Colombo, JP; Dionisi Vici, C; Gambarara, M; Sabetta, G1
Akiyoshi, H; Ichihara, K; Inoue, I; Ishii, S; Mito, T; Nakajima, M; Saheki, T; Takakura, H; Takashima, S; Takeshita, K1
Donati, MA; Filippi, L; Resti, M; Zammarchi, E1
Lee, SC; Marekov, LN; Mei, G; Melino, G; Steinert, PM; Tarcsa, E1
Boucher, JL; Mansuy, D; Moali, C; Sari, MA; Stuehr, DJ1
David, L; Dionisi-Vici, C; Dolce, V; Fiermonte, G; Palmieri, F; Santorelli, FM; Walker, JE1
Andria, G; Carbone, MT; Correra, A; Della Casa, R; Dionisi-Vici, C; Fecarotta, S; Parenti, G; Riva, S; Santorelli, FM; Torre, G; Vajro, P; Zuppaldi, A1
Becker, T; Hanff, E; Tsikas, D1

Other Studies

12 other study(ies) available for homocitrulline and arginine

ArticleYear
[The dibasic amino acid metabolic disorders].
    Nihon rinsho. Japanese journal of clinical medicine, 1992, Volume: 50, Issue:7

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Blood Transfusion; Citrulline; Humans; Hyperargininemia; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Renal Dialysis

1992
Hyperornithinemia, hyperammonemia and homocitrullinuria--a case report and study of ornithine metabolism using in vivo deuterium labelling.
    Clinica chimica acta; international journal of clinical chemistry, 1991, Sep-14, Volume: 201, Issue:1-2

    Topics: Adult; Ammonia; Arginine; Chromatography, Liquid; Citrulline; Deuterium; Humans; Male; Mass Spectrometry; Ornithine

1991
Homocitrullinuria and homoargininuria in hyperargininaemia.
    Journal of inherited metabolic disease, 1988, Volume: 11, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Child; Child, Preschool; Citrulline; Homoarginine; Humans; Lysine; Male

1988
Homocitrullinuria and homoargininuria in lysinuric protein intolerance.
    Journal of inherited metabolic disease, 1989, Volume: 12, Issue:2

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Arginine; Child; Citrulline; Female; Homoarginine; Humans; Kidney; Lysine; Male; Ornithine

1989
Hyperornithinemia-hyperammonemia-homocitrullinuria syndrome: low creatine excretion and effect of citrulline, arginine, or ornithine supplement.
    Pediatric research, 1987, Volume: 22, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Child, Preschool; Citrulline; Creatine; Female; Humans; Lysine; Male; Ornithine; Orotic Acid; Syndrome

1987
Clinical, biochemical and ultrastructural study on the pathogenesis of hyperornithinemia-hyperammonemia-homocitrullinuria syndrome.
    Brain & development, 1988, Volume: 10, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Brain; Child; Citrulline; Endoplasmic Reticulum; Humans; Liver Glycogen; Male; Mitochondria, Liver; Ornithine; Tomography, X-Ray Computed

1988
Cryptogenic hepatitis masking the diagnosis of ornithine transcarbamylase deficiency.
    Journal of pediatric gastroenterology and nutrition, 1996, Volume: 22, Issue:4

    Topics: Absorption; Ammonia; Arginine; Child, Preschool; Citrulline; Diagnosis, Differential; Dietary Proteins; Female; Glutamine; Hepatitis; Humans; Infant; Lysine; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Urea

1996
Protein unfolding by peptidylarginine deiminase. Substrate specificity and structural relationships of the natural substrates trichohyalin and filaggrin.
    The Journal of biological chemistry, 1996, Nov-29, Volume: 271, Issue:48

    Topics: Amino Acid Sequence; Animals; Arginine; Circular Dichroism; Citrulline; Filaggrin Proteins; Humans; Hydrolases; Intermediate Filament Proteins; Mice; Molecular Sequence Data; Peptides; Protein Denaturation; Protein Precursors; Protein Structure, Secondary; Protein-Arginine Deiminase Type 4; Protein-Arginine Deiminases; Skin; Spectrometry, Fluorescence; Substrate Specificity

1996
Substrate specificity of NO synthases: detailed comparison of L-arginine, homo-L-arginine, their N omega-hydroxy derivatives, and N omega-hydroxynor-L-arginine.
    Biochemistry, 1998, Jul-21, Volume: 37, Issue:29

    Topics: Animals; Arginine; Catalysis; Cattle; Citrulline; Homoarginine; Kinetics; NADP; Nitric Oxide Synthase; Nitrites; Oxidation-Reduction; Oxygen; Substrate Specificity

1998
The mitochondrial ornithine transporter. Bacterial expression, reconstitution, functional characterization, and tissue distribution of two human isoforms.
    The Journal of biological chemistry, 2003, Aug-29, Volume: 278, Issue:35

    Topics: Amino Acid Transport Systems, Basic; Arginine; Biological Transport; Carrier Proteins; Citrulline; DNA, Complementary; Electrophoresis, Polyacrylamide Gel; Humans; Hyperammonemia; Kinetics; Liposomes; Liver; Lysine; Malates; Membrane Transport Proteins; Mitochondria; Models, Biological; Mutation; Ornithine; Phosphates; Protein Folding; Protein Isoforms; Recombinant Proteins; Reverse Transcriptase Polymerase Chain Reaction; Substrate Specificity; Time Factors; Tissue Distribution; Transcription, Genetic

2003
HHH syndrome (hyperornithinaemia, hyperammonaemia, homocitrullinuria), with fulminant hepatitis-like presentation.
    Journal of inherited metabolic disease, 2006, Volume: 29, Issue:1

    Topics: Alanine Transaminase; Amino Acid Transport Systems, Basic; Arginine; Aspartate Aminotransferases; Child, Preschool; Citrulline; Diet, Protein-Restricted; Hepatitis; Humans; Hyperammonemia; Liver; Male; Metabolism, Inborn Errors; Mitochondrial Membrane Transport Proteins; Ornithine; Proteins; Syndrome

2006
Drastic decrease of global l-arginine bioavailability during orthotopic liver transplantation: A matter of ATP deficiency of the graft?
    Nitric oxide : biology and chemistry, 2018, 02-28, Volume: 73

    Topics: Adenosine Triphosphate; Arginine; Biological Availability; Citrulline; Humans; Liver Transplantation; Ornithine

2018