glutaric acid has been researched along with s-adenosylmethionine in 10 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 0 (0.00) | 18.7374 |
1990's | 1 (10.00) | 18.2507 |
2000's | 7 (70.00) | 29.6817 |
2010's | 2 (20.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Bonham, JR; Downing, M; Edwards, RG; Manning, NJ; Olpin, SE; Pollitt, RJ; Pourfarzam, M; Sharrard, MJ; Tanner, MS | 1 |
al-Essa, MA; Bakheet, SM; Ozand, PT; Patay, ZJ; Rashed, MS | 1 |
Bain, MD; Baric, I; Chalmers, RA; Feyh, P; Hoffmann, GF; Jakobs, C; Jeffrey, I; Kölker, S; Okun, JG; Pourfarzam, M; Schor, DS; Wagner, L; Zschocke, J | 1 |
Lai, CC; Lee, CC; Lin, WD; Tsai, FJ; Wang, CH | 1 |
Liu, A; Pasquali, M | 1 |
Beresford, MW; Davidson, JE; Pourfarzam, M; Turnbull, DM | 1 |
Crnic, LR; Fricker, G; Goodman, SI; Harding, CO; Hoffmann, GF; Hörster, F; Koeller, DM; Kölker, S; Mahringer, A; Mühlhausen, C; Müller, I; Okun, JG; Sauer, SW | 1 |
Berger, R; de Sain-van der Velden, MG; Dorland, L; Ruiter, JP; Spliet, WG; Testerink, N; van der Kolk, JH; Votion, DM; Wanders, RJ; Westermann, CM; Wijnberg, ID | 1 |
da Silva, JM; de Moura Coelho, D; Deon, M; Ribas, GS; Sitta, A; Vargas, CR; Wajner, M | 1 |
Liu, H; Miao, JK; Wan, KX; Wang, DJ; Yang, J; Yu, CW; Yuan, ZJ; Zeng, Y; Zhang, J; Zou, L | 1 |
10 other study(ies) available for glutaric acid and s-adenosylmethionine
Article | Year |
---|---|
Normal acylcarnitines in maternal urine during a pregnancy affected by glutaric aciduria type II.
Topics: Acidosis, Renal Tubular; Carnitine; Female; Glutarates; Humans; Infant, Newborn; Male; Pregnancy | 1999 |
Glutaric aciduria type II: observations in seven patients with neonatal- and late-onset disease.
Topics: Acidosis; Age of Onset; Brain; Carnitine; Child; Consanguinity; Female; Glutarates; Humans; Infant; Infant, Newborn; Magnetic Resonance Imaging; Male; Mass Spectrometry; Metabolism, Inborn Errors; Tomography, Emission-Computed | 2000 |
Glutaryl-CoA dehydrogenase deficiency: region-specific analysis of organic acids and acylcarnitines in post mortem brain predicts vulnerability of the putamen.
Topics: Acidosis; Acute Disease; Adolescent; Anticonvulsants; Atrophy; Brain; Carnitine; DNA Mutational Analysis; Fatal Outcome; Gas Chromatography-Mass Spectrometry; Gene Expression; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Male; Muscle Hypotonia; N-Methylaspartate; Oxidoreductases Acting on CH-CH Group Donors; Point Mutation; Putamen; Spasm; Vigabatrin | 2003 |
Genetic and biochemical study in a patient with glutaric acidemia type I.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Male; Mutation; Oxidoreductases Acting on CH-CH Group Donors | 2004 |
Acidified acetonitrile and methanol extractions for quantitative analysis of acylcarnitines in plasma by stable isotope dilution tandem mass spectrometry.
Topics: Acetonitriles; Carnitine; Chemical Fractionation; Glutarates; Humans; Isotope Labeling; Mass Spectrometry; Metabolism, Inborn Errors; Methanol; Reproducibility of Results | 2005 |
So doctor, what exactly is wrong with my muscles? Glutaric aciduria type II presenting in a teenager.
Topics: Acyl-CoA Dehydrogenase; Adolescent; Carnitine; DNA Mutational Analysis; Electron-Transferring Flavoproteins; Female; Glutarates; Humans; Iron-Sulfur Proteins; Metabolism, Inborn Errors; Muscular Diseases; Oxidoreductases Acting on CH-NH Group Donors | 2006 |
Intracerebral accumulation of glutaric and 3-hydroxyglutaric acids secondary to limited flux across the blood-brain barrier constitute a biochemical risk factor for neurodegeneration in glutaryl-CoA dehydrogenase deficiency.
Topics: Amino Acids; Animals; Biological Transport; Blood-Brain Barrier; Blotting, Western; Brain; Carnitine; Cells, Cultured; Dicarboxylic Acids; Disease Models, Animal; Endothelial Cells; Glucose; Glutarates; Glutaryl-CoA Dehydrogenase; Heart; Liver; Mice; Mice, Inbred C57BL; Mice, Knockout; Models, Biological; Muscles; Neurodegenerative Diseases; Risk Factors; Statistics, Nonparametric; Swine; Time Factors; Tissue Distribution | 2006 |
Acquired multiple Acyl-CoA dehydrogenase deficiency in 10 horses with atypical myopathy.
Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Animals; Butyric Acid; Butyryl-CoA Dehydrogenase; Carnitine; Chromatography, High Pressure Liquid; Female; Gas Chromatography-Mass Spectrometry; Glutarates; Horse Diseases; Horses; Isovaleryl-CoA Dehydrogenase; Lactic Acid; Male; Microscopy, Electron; Microscopy, Fluorescence; Muscles; Muscular Diseases; Riboflavin | 2008 |
Selective Screening of Fatty Acids Oxidation Defects and Organic Acidemias by Liquid Chromatography/tandem Mass Spectrometry Acylcarnitine Analysis in Brazilian Patients.
Topics: Acyl-CoA Dehydrogenase; Amino Acid Metabolism, Inborn Errors; Brain Diseases, Metabolic; Brazil; Carnitine; Child, Preschool; Chromatography, Liquid; Fatty Acids; Female; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Infant, Newborn; Lipid Metabolism, Inborn Errors; Male; Mass Screening; Oxidation-Reduction; Prevalence; Tandem Mass Spectrometry; Young Adult | 2018 |
Severe clinical manifestation of mitochondrial 3-hydroxy-3-methylglutaryl-CoA synthase deficiency associated with two novel mutations: a case report.
Topics: Acidosis; Acyl Coenzyme A; Adipates; Carnitine; Diarrhea; Dicarboxylic Acids; Exome Sequencing; Fatal Outcome; Frameshift Mutation; Glutarates; Humans; Hydroxymethylglutaryl-CoA Synthase; Infant; Male; Mitochondria; Multiple Organ Failure; Mutation; Respiratory Tract Infections | 2019 |