glutaric acid has been researched along with riboflavin in 19 studies
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 5 (26.32) | 18.7374 |
1990's | 4 (21.05) | 18.2507 |
2000's | 10 (52.63) | 29.6817 |
2010's | 0 (0.00) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Bennett, MJ; Goodman, SI; Hale, DE; Pollitt, RJ; Vamecq, J | 1 |
Bell, RB; Brownell, AK; Engel, AG; Frerman, FE; Goodman, SI; Roe, CR; Seccombe, DW; Snyder, FF | 1 |
Iafolla, AK; Kahler, SG | 1 |
Divry, P; Gregersen, N; Mathieu, M; Vianey-Liaud, C | 1 |
Bartlett, K; Eyre, JA; Fisher, J; Gardner-Medwin, D; Johnson, MA; Turnbull, DM; Watmough, NJ | 1 |
Bolhuis, PA; de Visser, M; Luyt-Houwen, IE; Oey, PL; Scholte, HR; Schutgens, RB; Vaandrager-Verduin, MH; Veder, HA | 1 |
Blom, W; Giesberts, MA; Mooy, PD; Przyrembel, H; Scholte, HR; van Gelderen, HH | 1 |
Rohr, F; Warman, ML; Yannicelli, S | 1 |
Ciceri, E; Garavaglia, B; Moroni, I; Rimoldi, M; Uziel, G | 1 |
Gunji, T; Koga, Y; Nonaka, I; Shimizu, N; Tojo, M; Yamaguchi, S | 1 |
Corral, I; Gimeno, A; Martínez Castrillo, JC; Martínez-Pardo, M | 1 |
Christensen, E; de Koning, TJ; Dorland, L; Hoffmann, GF; Knerr, I; Müller, P; Rascher, W; Trautmann, U; Trefz, FK; Wündisch, GF; Zschocke, J | 1 |
Liang, Y; Liu, L; Luo, XP; Wang, MT; Wei, H | 1 |
Luo, F; Sun, JP; Yang, YJ; Yu, XH; Zhong, L | 1 |
Chen, LH; Jong, YJ; Lai, CL; Liang, WC; Tsai, KB | 1 |
Garcia-Segura, JM; Merinero, B; Pascual-Castroviejo, I; Pascual-Pascual, SI; Ugarte, M; Velazquez, R; Viaño, J | 1 |
Garcia Pérez, A; Martínez Granero, MA; Martínez-Pardo, M; Parra, E | 1 |
Bain, MD; Chalmers, RA; Zschocke, J | 1 |
Berger, R; de Sain-van der Velden, MG; Dorland, L; Ruiter, JP; Spliet, WG; Testerink, N; van der Kolk, JH; Votion, DM; Wanders, RJ; Westermann, CM; Wijnberg, ID | 1 |
2 review(s) available for glutaric acid and riboflavin
Article | Year |
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The inborn errors of mitochondrial fatty acid oxidation.
Topics: Carnitine; Diagnosis, Differential; Electron-Transferring Flavoproteins; Fatty Acid Desaturases; Fatty Acids; Flavoproteins; Glutarates; Humans; Iron-Sulfur Proteins; Lipid Metabolism, Inborn Errors; Microbodies; Mitochondria; Multienzyme Complexes; Oxidation-Reduction; Oxidoreductases Acting on CH-NH Group Donors; Riboflavin | 1987 |
Nutrition support for glutaric acidemia type I.
Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Child, Preschool; Dietary Proteins; Female; Food, Formulated; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Infant; Infant, Newborn; Lysine; Male; Mitochondria; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Riboflavin; Tryptophan | 1994 |
17 other study(ies) available for glutaric acid and riboflavin
Article | Year |
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Atypical riboflavin-responsive glutaric aciduria, and deficient peroxisomal glutaryl-CoA oxidase activity: a new peroxisomal disorder.
Topics: Acyl-CoA Oxidase; Cells, Cultured; Child, Preschool; Fatty Acids; Female; Fibroblasts; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Lysine; Microbodies; Oxidation-Reduction; Oxidoreductases; Riboflavin | 1991 |
Electron transfer flavoprotein: ubiquinone oxidoreductase (ETF:QO) deficiency in an adult.
Topics: Acidosis; Adult; Carnitine; Electron-Transferring Flavoproteins; Fatty Acid Desaturases; Female; Glutarates; Humans; Iron-Sulfur Proteins; Lipid Metabolism, Inborn Errors; Multienzyme Complexes; Muscular Diseases; Oxidoreductases Acting on CH-NH Group Donors; Reye Syndrome; Riboflavin | 1990 |
Megalencephaly in the neonatal period as the initial manifestation of glutaric aciduria type I.
Topics: Amino Acid Metabolism, Inborn Errors; Brain; Carnitine; Female; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Infant, Newborn; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Riboflavin | 1989 |
Lipid storage myopathy due to glutaric aciduria type II: treatment of a potentially fatal myopathy.
Topics: Carnitine; Female; Glutarates; Glutaryl-CoA Dehydrogenase; Glycine; Humans; Infant; Lipid Metabolism; Metabolic Diseases; Muscles; Muscular Diseases; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Riboflavin | 1988 |
Riboflavin-responsive lipid-storage myopathy and glutaric aciduria type II of early adult onset.
Topics: Adolescent; Carnitine; Child; Fatty Acids; Female; Fibroblasts; Glutarates; Humans; Infant; Lipid Metabolism; Metabolic Diseases; Mitochondria, Muscle; Muscular Diseases; Pedigree; Riboflavin | 1986 |
Glutaric aciduria type II: treatment with riboflavine, carnitine and insulin.
Topics: Biopsy; Carnitine; Fatty Acid Desaturases; Glutarates; Humans; Hypoglycemia; Infant; Insulin; Male; Metabolism, Inborn Errors; Muscle Hypotonia; Muscles; Riboflavin | 1984 |
Riboflavin-responsive glutaric aciduria type II presenting as a leukodystrophy.
Topics: Child, Preschool; Glutarates; Humans; Leukoencephalopathy, Progressive Multifocal; Magnetic Resonance Imaging; Male; Phenotype; Riboflavin | 1995 |
[A case of riboflavin-responsive multiple acyl-CoA dehydrogenase deficiency (glutaric aciduria type II)].
Topics: Acyl-CoA Dehydrogenases; Biomarkers; Carnitine; Child; Electron-Transferring Flavoproteins; Fatty Acids; Glutarates; Humans; Iron-Sulfur Proteins; Lipid Metabolism, Inborn Errors; Male; Multienzyme Complexes; Oxidoreductases Acting on CH-NH Group Donors; Riboflavin | 2000 |
[Glutaric aciduria type I: diagnosis in adulthood and phenotypic variability].
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Brain; Brain Diseases, Metabolic; Carnitine; Fibroblasts; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Infant; Magnetic Resonance Imaging; Movement Disorders; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Riboflavin; Tomography, X-Ray Computed | 2001 |
Glutaric aciduria type III: a distinctive non-disease?
Topics: Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Chromosome Deletion; Diarrhea; Fasting; Female; Glutarates; Humans; Liver; Lysine; Male; Pipecolic Acids; Riboflavin | 2002 |
[Late-onset riboflavin-responsive multiple acyl-CoA dehydrogenase deficiency (glutaric aciduria type II)].
Topics: Acyl-CoA Dehydrogenase; Adolescent; Age of Onset; Child; Female; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Metabolism, Inborn Errors; Photosensitizing Agents; Riboflavin; Treatment Outcome | 2003 |
[Glutaric aciduria type I: report of a case].
Topics: Amino Acid Metabolism, Inborn Errors; Diagnosis, Differential; Diet; Glutarates; Humans; Infant; Male; Riboflavin; Treatment Outcome | 2004 |
Riboflavin-responsive glutaric aciduria type II with recurrent pancreatitis.
Topics: Acyl-CoA Dehydrogenase; Adult; Female; Glutarates; Humans; Male; Metabolism, Inborn Errors; Pancreatitis; Pedigree; Recurrence; Riboflavin | 2004 |
[Glutaric aciduria type 1 with normal evolution: follow-up of one case until adult age].
Topics: Basal Ganglia; Brain; Brain Chemistry; Brain Diseases, Metabolic, Inborn; Carnitine; Cells, Cultured; Child Development; Child, Preschool; Chromosomes, Human, Pair 19; Corpus Callosum; Female; Fibroblasts; Follow-Up Studies; Glutarates; Glutaryl-CoA Dehydrogenase; Heterozygote; Humans; Intelligence; Lactic Acid; Magnetic Resonance Imaging; Mutation, Missense; Oxidoreductases Acting on CH-CH Group Donors; Riboflavin; Seizures; Sequence Deletion | 2005 |
[Macrocephaly the first manifestation of glutaric aciduria type I: the importance of early diagnosis].
Topics: Brain; Brain Diseases, Metabolic; Carnitine; Diagnosis, Differential; Glutarates; Humans; Infant; Magnetic Resonance Imaging; Male; Riboflavin; Time Factors | 2005 |
Riboflavin-responsive glutaryl CoA dehydrogenase deficiency.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Amino Acid Substitution; Child; Child, Preschool; Fatal Outcome; Female; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Infant; Male; Protein Structure, Quaternary; Riboflavin | 2006 |
Acquired multiple Acyl-CoA dehydrogenase deficiency in 10 horses with atypical myopathy.
Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Animals; Butyric Acid; Butyryl-CoA Dehydrogenase; Carnitine; Chromatography, High Pressure Liquid; Female; Gas Chromatography-Mass Spectrometry; Glutarates; Horse Diseases; Horses; Isovaleryl-CoA Dehydrogenase; Lactic Acid; Male; Microscopy, Electron; Microscopy, Fluorescence; Muscles; Muscular Diseases; Riboflavin | 2008 |