glutaric acid and lysine

glutaric acid has been researched along with lysine in 29 studies

Research

Studies (29)

TimeframeStudies, this research(%)All Research%
pre-19903 (10.34)18.7374
1990's4 (13.79)18.2507
2000's9 (31.03)29.6817
2010's8 (27.59)24.3611
2020's5 (17.24)2.80

Authors

AuthorsStudies
Bennett, MJ; Goodman, SI; Hale, DE; Pollitt, RJ; Vamecq, J1
Horn, L; Jellum, E; Kvittingen, EA; Nilsen, E; Seip, R; Stokke, O; Thoresen, O1
Bennett, MJ; Curnock, DA; Engel, PC; Gray, RG; Hull, D; Patrick, AD; Pollitt, RJ; Shaw, L1
Rohr, F; Warman, ML; Yannicelli, S1
Dalton, RN; Howard, RS; Olpin, SE; Prevett, MC1
Emons, D; Haverkamp, F; Kreft, B; Woelfle, J1
Crnic, LS; Koeller, DM; Woontner, M1
Manoj, N; Saraswathi, NT; Vijayan, M1
Prats Viñas, J1
Christensen, E; de Koning, TJ; Dorland, L; Hoffmann, GF; Knerr, I; Müller, P; Rascher, W; Trautmann, U; Trefz, FK; Wündisch, GF; Zschocke, J1
Andresen, BS; Campistol, J; Curcoy, A; Gregersen, N; Olsen, RK; Osorio, JH; Ribes, A; Trenchs, V; Vilaseca, MA1
HAIGHT, RD; MATTOON, JR1
Alderson, NL; Baynes, JW; Januszewski, AS; Jenkins, AJ; Thorpe, SR1
Antonetti, DA; Cheng, KC; Connor, JR; Goodman, SI; Lazovic, J; Smith, MB; Wolpert, EB; Woontner, M; Zinnanti, WJ1
Hoffmann, GF; Koeller, DM; Kölker, S; Okun, JG; Sauer, SW1
Cheng, KC; Connor, JR; Goodman, SI; Housman, C; Jacobs, RE; LaNoue, K; Lazovic, J; O'Callaghan, JP; Simpson, I; Woontner, M; Zinnanti, WJ1
Blank, AE; Burgard, P; Koeller, DM; Kölker, S; Komatsuzaki, S; Mittelbronn, M; Okun, JG; Opp, S; Sauer, SW1
Huang, H; Li, Q; Wang, G; Xie, J; Xie, L; Yu, Z; Zhou, M1
Cho, JS; Choi, JW; Jeong, KJ; Joo, JC; Lee, MH; Lee, SY; Oh, YH; Park, SH; Park, SJ; Shin, JH; Yu, J1
Assmann, B; Boy, N; Burgard, P; Dixon, M; Fleissner, S; Greenberg, CR; Harting, I; Heringer, J; Hoffmann, GF; Karall, D; Koeller, DM; Kölker, S; Krawinkel, MB; Maier, EM; Mühlhausen, C; Okun, JG; Opladen, T; Posset, R; Sahm, K; Zschocke, J1
He, JJ; Ju, Z1
Baritugo, KA; Hyun, SM; Joo, JC; Jung, SH; Kang, KH; Khang, TU; Kim, GB; Kim, HT; Kim, HU; Lee, SY; Oh, MK; Park, K; Park, SJ; Song, BK1
Ahn, JO; Bhatia, SK; Choi, TR; Hong, YG; Joo, JC; Jung, HR; Kim, YG; Lee, YK; Moon, YM; Park, K; Yang, SY; Yang, YH1
Hsu, JB; Huang, KY; Kao, HJ; Lee, TY; Weng, SL1
Bhatia, SK; Choi, TR; Choi, YK; Gurav, R; Han, YH; Kim, HJ; Kim, W; Park, K; Park, SH; Park, YL; Song, HS; Yang, YH1
Ahmad, MW; Arafat, ME; Dehzangi, A; Dipta, SR; Hasan, MAM; Sharma, A; Shatabda, S; Shovan, SM; Taherzadeh, G1
Bouchereau, J; Schiff, M1
Han, T; Kim, GB; Lee, SY1
Argmann, C; Bender, A; Dodatko, T; Houten, SM; Leandro, J; Yu, C1

Reviews

3 review(s) available for glutaric acid and lysine

ArticleYear
Nutrition support for glutaric acidemia type I.
    Journal of the American Dietetic Association, 1994, Volume: 94, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Child, Preschool; Dietary Proteins; Female; Food, Formulated; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Infant; Infant, Newborn; Lysine; Male; Mitochondria; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Riboflavin; Tryptophan

1994
Proposed recommendations for diagnosing and managing individuals with glutaric aciduria type I: second revision.
    Journal of inherited metabolic disease, 2017, Volume: 40, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Brain Diseases, Metabolic; Dietary Supplements; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Lysine

2017
Inherited Disorders of Lysine Metabolism: A Review.
    The Journal of nutrition, 2020, 10-01, Volume: 150, Issue:Suppl 1

    Topics: 2-Aminoadipic Acid; Aldehyde Dehydrogenase; Amino Acid Metabolism, Inborn Errors; Arginine; Brain; Brain Diseases, Metabolic; Brain Diseases, Metabolic, Inborn; Carnitine; Epilepsy; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Lysine; Metabolic Diseases; Pyridoxal Phosphate; Pyridoxine

2020

Other Studies

26 other study(ies) available for glutaric acid and lysine

ArticleYear
Atypical riboflavin-responsive glutaric aciduria, and deficient peroxisomal glutaryl-CoA oxidase activity: a new peroxisomal disorder.
    Journal of inherited metabolic disease, 1991, Volume: 14, Issue:2

    Topics: Acyl-CoA Oxidase; Cells, Cultured; Child, Preschool; Fatty Acids; Female; Fibroblasts; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Lysine; Microbodies; Oxidation-Reduction; Oxidoreductases; Riboflavin

1991
Advances in the use of computerized gas chromatography-mass spectrometry and high-performance liquid chromatography with rapid scanning detection for clinical diagnosis.
    Journal of chromatography, 1989, May-12, Volume: 468

    Topics: Acids; Alkaptonuria; Child; Chromatography, High Pressure Liquid; Clinical Laboratory Techniques; Female; Gas Chromatography-Mass Spectrometry; Glutarates; Humans; Infant; Lysine; Pharmaceutical Preparations

1989
Glutaric aciduria type II: biochemical investigation and treatment of a child diagnosed prenatally.
    Journal of inherited metabolic disease, 1984, Volume: 7, Issue:2

    Topics: Adipates; Carbon Dioxide; Fatty Acid Desaturases; Fatty Acids; Female; Fibroblasts; Glutarates; Humans; Infant, Newborn; Liver; Lysine; Pregnancy; Prenatal Diagnosis; Sarcosine

1984
Glutaric aciduria type 1 in adulthood.
    Journal of neurology, neurosurgery, and psychiatry, 1996, Volume: 60, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Dystonia; Female; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Lysine; Middle Aged; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Tryptophan

1996
Subdural hemorrhage as an initial sign of glutaric aciduria type 1: a diagnostic pitfall.
    Pediatric radiology, 1996, Volume: 26, Issue:11

    Topics: Amino Acid Metabolism, Inborn Errors; Atrophy; Cisterna Magna; Developmental Disabilities; Diagnosis, Differential; Female; Frontal Lobe; Glutarates; Glutaryl-CoA Dehydrogenase; Hematoma, Subdural; Humans; Infant; Lysine; Magnetic Resonance Imaging; Movement Disorders; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Psychomotor Performance; Temporal Lobe; Tomography, X-Ray Computed; Tryptophan

1996
Analysis of the expression of murine glutaryl-CoA dehydrogenase: in vitro and in vivo studies.
    Molecular genetics and metabolism, 2000, Volume: 69, Issue:2

    Topics: 3T3 Cells; 5' Untranslated Regions; Animals; Base Sequence; Blotting, Western; Brain; Glutarates; Glutaryl-CoA Dehydrogenase; Kidney; Liver; Lysine; Mice; Mice, Inbred C57BL; Molecular Sequence Data; Organ Specificity; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Promoter Regions, Genetic; Reverse Transcriptase Polymerase Chain Reaction; Sequence Alignment; Transfection

2000
X-ray studies on crystalline complexes involving amino acids and peptides. XXXVII. Novel aggregation patterns and effect of chirality in the complexes of DL- and L-lysine with glutaric acid.
    Acta crystallographica. Section B, Structural science, 2001, Volume: 57, Issue:Pt 3

    Topics: Crystallography, X-Ray; Electrochemistry; Glutarates; Lysine; Macromolecular Substances; Models, Molecular; Stereoisomerism

2001
[Glutaric aciduria type I: an organic acidemia without acidosis with severe movement disorders].
    Neurologia (Barcelona, Spain), 2001, Volume: 16, Issue:8

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Brain Diseases, Metabolic; Carnitine; Child, Preschool; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Infant; Lysine; Movement Disorders; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Phenotype; Tryptophan

2001
Glutaric aciduria type III: a distinctive non-disease?
    Journal of inherited metabolic disease, 2002, Volume: 25, Issue:6

    Topics: Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Chromosome Deletion; Diarrhea; Fasting; Female; Glutarates; Humans; Liver; Lysine; Male; Pipecolic Acids; Riboflavin

2002
Late-onset form of beta-electron transfer flavoprotein deficiency.
    Molecular genetics and metabolism, 2003, Volume: 78, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Carnitine; Cysteine; DNA Mutational Analysis; Electron-Transferring Flavoproteins; Electrons; Exons; Female; Fibroblasts; Gas Chromatography-Mass Spectrometry; Gene Deletion; Glutarates; Humans; Infant, Newborn; Iron-Sulfur Proteins; Lysine; Mutation, Missense; Oxidoreductases Acting on CH-NH Group Donors; Oxygen; Phenotype

2003
Glutaric acid accumulation by a lysine-requiring yeast mutant.
    The Journal of biological chemistry, 1962, Volume: 237

    Topics: Glutarates; Humans; Lysine; Saccharomyces cerevisiae; Yeasts

1962
Chemical modification of proteins during peroxidation of phospholipids.
    Journal of lipid research, 2005, Volume: 46, Issue:7

    Topics: Adult; Blood Proteins; Catalysis; Copper Sulfate; Diabetes Mellitus, Type 1; Dicarboxylic Acids; Female; Glutarates; Glycation End Products, Advanced; Humans; Lipid Peroxidation; Lipoproteins, LDL; Lysine; Lysophosphatidylcholines; Male; Oxidation-Reduction; Phospholipids; Ribonuclease, Pancreatic

2005
A diet-induced mouse model for glutaric aciduria type I.
    Brain : a journal of neurology, 2006, Volume: 129, Issue:Pt 4

    Topics: Amino Acid Metabolism, Inborn Errors; Animals; Blood-Brain Barrier; Capillary Permeability; Corpus Striatum; Diet; Dietary Proteins; Disease Models, Animal; Female; Glutarates; Lysine; Magnetic Resonance Imaging; Male; Mice; Mice, Inbred C57BL; Neurons; Survival Analysis; Tissue Culture Techniques

2006
Lysine intake and neurotoxicity in glutaric aciduria type I: towards a rationale for therapy?
    Brain : a journal of neurology, 2006, Volume: 129, Issue:Pt 8

    Topics: Amino Acid Metabolism, Inborn Errors; Animals; Brain Diseases, Metabolic, Inborn; Diet; Disease Models, Animal; Glutarates; Lysine; Mice

2006
Mechanism of age-dependent susceptibility and novel treatment strategy in glutaric acidemia type I.
    The Journal of clinical investigation, 2007, Volume: 117, Issue:11

    Topics: Aging; Amino Acid Metabolism, Inborn Errors; Animals; Brain Diseases, Metabolic, Inborn; Child; Diet; Disease Models, Animal; gamma-Aminobutyric Acid; Genetic Predisposition to Disease; Glucose; Glutamic Acid; Glutarates; Glutaryl-CoA Dehydrogenase; Homoarginine; Humans; Lysine; Mice; Mice, Knockout; Mitochondria; Neurons; Nuclear Magnetic Resonance, Biomolecular; Tryptophan

2007
Multifactorial modulation of susceptibility to l-lysine in an animal model of glutaric aciduria type I.
    Biochimica et biophysica acta, 2015, Volume: 1852, Issue:5

    Topics: Aconitate Hydratase; Amino Acid Metabolism, Inborn Errors; Animals; Brain; Brain Diseases, Metabolic; Diet; Disease Models, Animal; Dose-Response Relationship, Drug; Energy Metabolism; Female; Genetic Predisposition to Disease; Glutarates; Glutaryl-CoA Dehydrogenase; Glyceraldehyde-3-Phosphate Dehydrogenases; Ketoglutarate Dehydrogenase Complex; Lysine; Male; Mice, 129 Strain; Mice, Inbred C57BL; Mice, Knockout; Risk Factors; Sex Factors; Spectrophotometry

2015
Proteome-wide Lysine Glutarylation Profiling of the Mycobacterium tuberculosis H37Rv.
    Journal of proteome research, 2016, Apr-01, Volume: 15, Issue:4

    Topics: Acetylation; Acyltransferases; Amino Acid Sequence; Antigens, Bacterial; Bacterial Proteins; Chromatography, Liquid; Escherichia coli; Escherichia coli Proteins; Gene Expression; Gene Expression Profiling; Glutarates; Lysine; Mass Spectrometry; Mycobacterium tuberculosis; Peptide Elongation Factor Tu; Protein Processing, Post-Translational; Proteome; Ribosomal Proteins; Succinic Acid

2016
Metabolic engineering of Corynebacterium glutamicum for enhanced production of 5-aminovaleric acid.
    Microbial cell factories, 2016, Oct-07, Volume: 15, Issue:1

    Topics: Amidohydrolases; Amino Acids, Neutral; Batch Cell Culture Techniques; Corynebacterium glutamicum; Escherichia coli; Fermentation; Glucose; Glutarates; Lysine; Metabolic Engineering; Mixed Function Oxygenases; Pseudomonas putida

2016
Prediction of lysine glutarylation sites by maximum relevance minimum redundancy feature selection.
    Analytical biochemistry, 2018, 06-01, Volume: 550

    Topics: Acylation; Glutarates; Lysine; Protein Processing, Post-Translational; Proteins; Sequence Analysis, Protein; Software; Support Vector Machine

2018
Metabolic engineering of Corynebacterium glutamicum for the production of glutaric acid, a C5 dicarboxylic acid platform chemical.
    Metabolic engineering, 2019, Volume: 51

    Topics: Codon; Corynebacterium glutamicum; Dicarboxylic Acids; DNA, Bacterial; Fermentation; Glucose; Glutarates; Lysine; Metabolic Engineering; Plasmids; Pseudomonas putida; Vasotocin

2019
Enhanced production of glutaric acid by NADH oxidase and GabD-reinforced bioconversion from l-lysine.
    Biotechnology and bioengineering, 2019, Volume: 116, Issue:2

    Topics: Bacillus subtilis; Biotransformation; Escherichia coli; Escherichia coli Proteins; Glutarates; Lysine; Metabolic Engineering; Multienzyme Complexes; NADH, NADPH Oxidoreductases; Recombinant Proteins; Succinate-Semialdehyde Dehydrogenase

2019
Characterization and identification of lysine glutarylation based on intrinsic interdependence between positions in the substrate sites.
    BMC bioinformatics, 2019, Feb-04, Volume: 19, Issue:Suppl 13

    Topics: Amino Acid Motifs; Amino Acid Sequence; Animals; Computational Biology; Databases, Protein; Glutarates; Lysine; Mice; Proteins; Reproducibility of Results; ROC Curve; Substrate Specificity; Support Vector Machine; User-Computer Interface

2019
Simultaneous monitoring of the bioconversion from lysine to glutaric acid by ethyl chloroformate derivatization and gas chromatography-mass spectrometry.
    Analytical biochemistry, 2020, 05-15, Volume: 597

    Topics: Chromatography, High Pressure Liquid; Fermentation; Formic Acid Esters; Gas Chromatography-Mass Spectrometry; Glutarates; Lysine; Molecular Structure

2020
Accurately Predicting Glutarylation Sites Using Sequential Bi-Peptide-Based Evolutionary Features.
    Genes, 2020, 08-31, Volume: 11, Issue:9

    Topics: Algorithms; Amino Acid Sequence; Animals; Computational Biology; Evolution, Molecular; Glutarates; Lysine; Machine Learning; Mice; Mycobacterium tuberculosis; Peptide Fragments; Protein Processing, Post-Translational; Proteins; Support Vector Machine

2020
Glutaric acid production by systems metabolic engineering of an l-lysine-overproducing
    Proceedings of the National Academy of Sciences of the United States of America, 2020, 12-01, Volume: 117, Issue:48

    Topics: Batch Cell Culture Techniques; Biosynthetic Pathways; Corynebacterium glutamicum; Fermentation; Glutarates; Lysine; Metabolic Engineering; Metabolic Flux Analysis; Systems Biology; Transcriptome

2020
Glutaric aciduria type 3 is a naturally occurring biochemical trait in inbred mice of 129 substrains.
    Molecular genetics and metabolism, 2021, Volume: 132, Issue:2

    Topics: Acyltransferases; Amino Acid Metabolism, Inborn Errors; Animals; Disease Models, Animal; Glutarates; Humans; Lysine; Metabolic Diseases; Mice; Mice, Inbred Strains; Oxidoreductases; Phenotype; Transferases

2021