glutaric acid and glutaconic acid

glutaric acid has been researched along with glutaconic acid in 5 studies

Research

Studies (5)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's1 (20.00)18.2507
2000's3 (60.00)29.6817
2010's1 (20.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Christensen, E; Deufel, T; Falter, C; Fautek, JD; Fingerhut, R; Flott-Rahmel, B; Jakobs, C; Ludolph, A; Musshoff, U; Schluff, P; Ullrich, K1
Frederick, CB; Palmeira, CM; Rana, MI; Wallace, KB1
Christensen, E; Kristensen, AS; Lund, AM; Lund, TM; Schousboe, A1
Bührer, C; Gerstner, B; Gratopp, A; Marcinkowski, M; Obladen, M; Sifringer, M1
Assmann, B; Boy, N; Burgard, P; Dixon, M; Fleissner, S; Greenberg, CR; Harting, I; Heringer, J; Hoffmann, GF; Karall, D; Koeller, DM; Kölker, S; Krawinkel, MB; Maier, EM; Mühlhausen, C; Okun, JG; Opladen, T; Posset, R; Sahm, K; Zschocke, J1

Reviews

1 review(s) available for glutaric acid and glutaconic acid

ArticleYear
Proposed recommendations for diagnosing and managing individuals with glutaric aciduria type I: second revision.
    Journal of inherited metabolic disease, 2017, Volume: 40, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Brain Diseases, Metabolic; Dietary Supplements; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Lysine

2017

Other Studies

4 other study(ies) available for glutaric acid and glutaconic acid

ArticleYear
Nerve cell lesions caused by 3-hydroxyglutaric acid: a possible mechanism for neurodegeneration in glutaric acidaemia I.
    Journal of inherited metabolic disease, 1997, Volume: 20, Issue:3

    Topics: Adenosine Triphosphate; Amino Acid Metabolism, Inborn Errors; Animals; Electrophysiology; Glutarates; Hippocampus; Nerve Degeneration; Nervous System Diseases; Neurons; Organ Culture Techniques; Rats

1997
Induction of the mitochondrial permeability transition in vitro by short-chain carboxylic acids.
    Biochemical and biophysical research communications, 2000, Jun-07, Volume: 272, Issue:2

    Topics: Acrylates; Animals; Calcium; Carboxylic Acids; Crotonates; Cyclosporine; Dose-Response Relationship, Drug; Fatty Acids, Monounsaturated; Glutarates; Kinetics; Male; Mitochondria, Liver; Mitochondrial Swelling; Molecular Weight; Pentanoic Acids; Permeability; Propionates; Rats; Rats, Sprague-Dawley

2000
On the neurotoxicity of glutaric, 3-hydroxyglutaric, and trans-glutaconic acids in glutaric acidemia type 1.
    Journal of neuroscience research, 2004, Jul-01, Volume: 77, Issue:1

    Topics: Animals; Brain Diseases, Metabolic, Inborn; Cell Death; Cells, Cultured; Cerebral Cortex; Corpus Striatum; Fetus; Glutarates; Glutaryl-CoA Dehydrogenase; Membrane Potentials; Mice; Nerve Degeneration; Neurons; Neurotoxins; Oocytes; Oxidoreductases Acting on CH-CH Group Donors; Rats; Receptors, N-Methyl-D-Aspartate; Xenopus

2004
Glutaric acid and its metabolites cause apoptosis in immature oligodendrocytes: a novel mechanism of white matter degeneration in glutaryl-CoA dehydrogenase deficiency.
    Pediatric research, 2005, Volume: 57, Issue:6

    Topics: Amino Acid Chloromethyl Ketones; Animals; Apoptosis; Base Sequence; Brain Diseases, Metabolic, Inborn; Caspase Inhibitors; Cell Differentiation; Cell Line; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Nerve Degeneration; Oligodendroglia; Oxidoreductases Acting on CH-CH Group Donors; Rats; Receptors, Glutamate; RNA, Messenger

2005