Page last updated: 2024-08-25

glutaconic acid and 3-hydroxyglutaric acid

glutaconic acid has been researched along with 3-hydroxyglutaric acid in 4 studies

Research

Studies (4)

TimeframeStudies, this research(%)All Research%
pre-19900 (0.00)18.7374
1990's1 (25.00)18.2507
2000's2 (50.00)29.6817
2010's1 (25.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Christensen, E; Deufel, T; Falter, C; Fautek, JD; Fingerhut, R; Flott-Rahmel, B; Jakobs, C; Ludolph, A; Musshoff, U; Schluff, P; Ullrich, K1
Christensen, E; Kristensen, AS; Lund, AM; Lund, TM; Schousboe, A1
Bührer, C; Gerstner, B; Gratopp, A; Marcinkowski, M; Obladen, M; Sifringer, M1
Assmann, B; Boy, N; Burgard, P; Dixon, M; Fleissner, S; Greenberg, CR; Harting, I; Heringer, J; Hoffmann, GF; Karall, D; Koeller, DM; Kölker, S; Krawinkel, MB; Maier, EM; Mühlhausen, C; Okun, JG; Opladen, T; Posset, R; Sahm, K; Zschocke, J1

Reviews

1 review(s) available for glutaconic acid and 3-hydroxyglutaric acid

ArticleYear
Proposed recommendations for diagnosing and managing individuals with glutaric aciduria type I: second revision.
    Journal of inherited metabolic disease, 2017, Volume: 40, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Brain Diseases, Metabolic; Dietary Supplements; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Lysine

2017

Other Studies

3 other study(ies) available for glutaconic acid and 3-hydroxyglutaric acid

ArticleYear
Nerve cell lesions caused by 3-hydroxyglutaric acid: a possible mechanism for neurodegeneration in glutaric acidaemia I.
    Journal of inherited metabolic disease, 1997, Volume: 20, Issue:3

    Topics: Adenosine Triphosphate; Amino Acid Metabolism, Inborn Errors; Animals; Electrophysiology; Glutarates; Hippocampus; Nerve Degeneration; Nervous System Diseases; Neurons; Organ Culture Techniques; Rats

1997
On the neurotoxicity of glutaric, 3-hydroxyglutaric, and trans-glutaconic acids in glutaric acidemia type 1.
    Journal of neuroscience research, 2004, Jul-01, Volume: 77, Issue:1

    Topics: Animals; Brain Diseases, Metabolic, Inborn; Cell Death; Cells, Cultured; Cerebral Cortex; Corpus Striatum; Fetus; Glutarates; Glutaryl-CoA Dehydrogenase; Membrane Potentials; Mice; Nerve Degeneration; Neurons; Neurotoxins; Oocytes; Oxidoreductases Acting on CH-CH Group Donors; Rats; Receptors, N-Methyl-D-Aspartate; Xenopus

2004
Glutaric acid and its metabolites cause apoptosis in immature oligodendrocytes: a novel mechanism of white matter degeneration in glutaryl-CoA dehydrogenase deficiency.
    Pediatric research, 2005, Volume: 57, Issue:6

    Topics: Amino Acid Chloromethyl Ketones; Animals; Apoptosis; Base Sequence; Brain Diseases, Metabolic, Inborn; Caspase Inhibitors; Cell Differentiation; Cell Line; Glutarates; Glutaryl-CoA Dehydrogenase; Humans; Nerve Degeneration; Oligodendroglia; Oxidoreductases Acting on CH-CH Group Donors; Rats; Receptors, Glutamate; RNA, Messenger

2005