cystine and penicillamine

cystine has been researched along with penicillamine in 79 studies

Research

Studies (79)

Timeframe	Studies, this research(%)	All Research%
pre-1990	58 (73.42)	18.7374
1990's	7 (8.86)	18.2507
2000's	9 (11.39)	29.6817
2010's	3 (3.80)	24.3611
2020's	2 (2.53)	2.80

Authors

Authors	Studies
Brimacombe, KR; Dulcey, AE; Goldsborough, AS; Gottesman, MM; Griffiths, G; Hall, MD; Handley, MD; Kannan, P; Pluchino, KM	1
Frohmüller, H	1
François, J	1
Cambie, E; François, J	1
Neuhann, T; Nover, A; Sommer, G	1
Jaffe, IA	1
Jeppsson, JO; Laurell, CB; Wollheim, FA	1
Harmison, GG; Rafter, GW	1
Alexander, CS; DeMaster, EG; Goon, DJ; Nagasawa, HT	1
Hutchins, D; Kendall, PA	1
Hautmann, R; Lutzeyer, W; Stuhlsatz, HW; Terhorst, B	1
Armstrong, DA; Gaucher, GM; Lal, M; Lin, WS	1
Schulman, JD	1
Furlong, TJ; Posen, S	1
Drummer, OH; Henry, PJ; Horowitz, JD	1
Chang, R; Marshall, FF; Singh, A	1
Adams, BV; Fuller, C; Pak, CY; Sakhaee, K; Zerwekh, JE	1
Gasset, AR; Hood, CI; Zimmerman, TJ	1
Furlong, CE; Oshima, RG; Schneider, JA; Willis, RC	1
Mauermayer, W; Wenzl, H	1
Cambie, E; Feher, J; Francois, J; Van Den Eeckhout, E	1
Kallistratos, G; Malorny, G	1
Mrskos, A; Podhradská, O; Pospísil, R; Saxl, O	1
Planas-Bohne, F	1
Ozog, LS; Tomskey, GC	1
Mastropaolo, D; Potenza, J; Schugar, HJ; Thich, JA	1
Harbro, J	1
Coryell, ME; Roesel, RA	1
Crawhall, JC; Watts, RW	1
Bradley, KH; Schulman, JD	2
Melchior, H; Terhorst, B	1
Casey, JP; Martin, RB	1
Christensen, MF; Henriksen, O; Nielsen, JA	1
Bacon, VA; Halpern, B; Jellum, E; Patton, W; Pereira, W	1
Revúsová, V; Zvara, V	1
Vergis, JG; Walker, BR	1
Deutz, H	1
Kludas, M; Wenzl, H	1
Crawhall, JC; Lietman, PS; Schneider, JA; Seegmiller, JE	1
Hutchison, AG	1
Dworschak, W; Haschek, H	1
Bradley, KH; Crawhall, JC; Thompson, CJ	1
Antener, I; Bauer, B	1
Crawhall, JC; Scowen, EF; Thompson, CJ; Watts, RW	1
Earll, JM; Kolb, FO	1
Dal Forno, S; De Dominicis, C; Franco, G; Gallucci, M; Iori, F; Laurenti, C	1
Bec, P; Lacombe, JL; Malha, F; Pujo, JM	1
Denneberg, T; Jeppsson, JO; Stenberg, P	1
Asper, R; Schmucki, O	1
Castro, JE; Chaudary, M; Williams, G	1
Savir, A; Stark, H	1
Persu, A; Pirson, Y	1
Guo, Z; Hou, Y; Li, J; Wang, PG	1
Deltas, CC; Pierides, AM	1
Akakura, K; Egoshi, K; Ito, H; Kotake, T; Masai, M; Nozumi, K; Ueda, T	1
Li, H; Marshall, ZM; Whorton, AR	1
Demedts, M; Hoet, PH; Nemery, B; van Klaveren, RJ	1
Buckley, BJ; Whorton, AR	1
Bridges, CC; Ganapathy, V; Huang, W; Kekuda, R; Mehta, P; Prasad, PD; Smith, SB; Wang, H	1
Choi, EJ; Kang, SI; Kim, IY; Kim, JY; Park, HS	1
Gukasyan, HJ; Kannan, R; Kim, KJ; Lee, VH	1
LEVINE, BB	1
MUELLER, OH	1
ELDJARN, L; HAMBRAEUS, L	1
ANTENER, I; BERGER, H; BRECHBUEHLER, T; STALDER, G	1
AKERFELDT, S; LOEVGREN, G	1
CRAWHALL, JC; THOMPSON, CJ	1
COLLINI, WR; HARRIS, RC; MATTERN, SR; SHAPIRO, P; ZINSSER, HH	1
PATRICK, AD	1
Denneberg, T; Fjellstedt, E; Harnevik, L; Jeppsson, JO; Söderkvist, P; Tiselius, HG	1
Galande, AK; Spatola, AF; Trent, JO	1
Dziarmaga, A; Goodyer, P; Parvex, P; Rozen, R	1
Dello Strologo, L; Laurenzi, C; Legato, A; Pastore, A	1
Jalilehvand, F; Leung, BO; Pettersson, LG; Risberg, ED; Sandström, M	1
Desai, D; Parr, JM; Winkle, D	1
Asplin, JR; Enders, FT; Goldfarb, DS; Malieckal, DA; Mara, K; Modersitzki, F	1
Henderickx, MM; Homan van der Heide, JJ; Kamphuis, GM; Melessen, IM; Merkx, MM; van Etten-Jamaludin, FS	1
Courbebaisse, M; Daudon, M; Defazio, J; Dousseaux, MP; Knebelmann, B; Prot-Bertoye, C; Tostivint, I; Traxer, O	1

Reviews

7 review(s) available for cystine and penicillamine

Article	Year
Cystinosis--a review. Scottish medical journal, 1975, Volume: 20, Issue:1 Topics: Animals; Birds; Cystine; Cystinosis; Dimercaprol; Homocystine; Humans; Hydrogen Sulfide; Kidney Transplantation; Lysosomes; Mammals; Methionine; Organoids; Penicillamine; S-Adenosylmethionine; Thiosulfates; Transplantation, Homologous	1975
"Adolescent" cystinosis. A case presentation and review of the recent literature. Archives of ophthalmology (Chicago, Ill. : 1960), 1974, Volume: 92, Issue:3 Topics: Adolescent; Biopsy; Bone Marrow; Chromosomes; Conjunctiva; Cornea; Cystine; Cystinosis; Diet Therapy; Female; Genes, Recessive; Humans; Kidney; Kidney Transplantation; Liver; Lymph Nodes; Mononuclear Phagocyte System; Nephrectomy; Penicillamine; Retinal Hemorrhage; Sclera; Scotoma; Spleen; Staining and Labeling; Uvea	1974
Cystinuria. The American journal of medicine, 1968, Volume: 45, Issue:5 Topics: Adolescent; Adult; Arginine; Biological Transport; Chemical Phenomena; Chemistry; Cystine; Cystinuria; Female; Heterozygote; Homocysteine; Homozygote; Humans; Jejunum; Kidney Tubules; Lysine; Male; Middle Aged; Ornithine; Penicillamine; Piperidines; Pyrrolidines	1968
[Current aspects of the medical treatment of cystinuria]. Acta urologica Belgica, 1994, Volume: 62, Issue:2 Topics: Ascorbic Acid; Captopril; Cystine; Cystinuria; Humans; Hydrogen-Ion Concentration; Penicillamine; Solubility; Tiopronin; Urine	1994
POLAROGRAPHIC ANALYSIS OF PROTEINS, AMINO ACIDS, AND OTHER COMPOUNDS BY MEANS OF THE BRDI CKA REACTION. Methods of biochemical analysis, 1963, Volume: 11 Topics: Amino Acids; Aminobutyrates; Animals; Cattle; Cobalt; Cysteine; Cystine; gamma-Globulins; Penicillamine; Pepsin A; Polarography; Proteins; Research; Serum Albumin; Serum Albumin, Bovine; Sulfhydryl Compounds; Trypsin	1963
The effect of additional drug therapy as metaphylaxis in patients with cystinuria: a systematic review. Minerva urologica e nefrologica = The Italian journal of urology and nephrology, 2020, Volume: 72, Issue:4 Topics: Captopril; Cystine; Cystinuria; Drug Therapy, Combination; Evidence-Based Medicine; Female; Humans; Male; Penicillamine; Tiopronin	2020
[Cystinuria]. Nephrologie & therapeutique, 2021, Volume: 17S Topics: Cystine; Cystinuria; Humans; Kidney Calculi; Penicillamine; Tiopronin	2021

Trials

3 trial(s) available for cystine and penicillamine

Article	Year
Management of cystine nephrolithiasis with alpha-mercaptopropionylglycine. The Journal of urology, 1986, Volume: 136, Issue:5 Topics: Adolescent; Adult; Aged; Amino Acids, Sulfur; Child; Clinical Trials as Topic; Cystine; Cystinuria; Female; Humans; Kidney Calculi; Male; Middle Aged; Penicillamine; Time Factors; Tiopronin	1986
Cystinuria in children and young adults: success of monitoring free-cystine urine levels. Pediatric nephrology (Berlin, Germany), 2007, Volume: 22, Issue:11 Topics: Adolescent; Adult; Alkalies; Chelating Agents; Child; Child, Preschool; Cystine; Cystinuria; Diuretics; Drug Monitoring; Humans; Infant; Penicillamine; Potassium Citrate; Prospective Studies; Sodium Bicarbonate; Tiopronin; Urinary Calculi	2007
Effect of increasing doses of cystine-binding thiol drugs on cystine capacity in patients with cystinuria. Urolithiasis, 2019, Volume: 47, Issue:6 Topics: Adolescent; Adult; Aged; Aged, 80 and over; Cross-Over Studies; Cystine; Cystinuria; Dose-Response Relationship, Drug; Female; Humans; Male; Middle Aged; Penicillamine; Solubility; Tiopronin; Young Adult	2019

Other Studies

69 other study(ies) available for cystine and penicillamine

Article	Year
Collateral sensitivity of multidrug-resistant cells to the orphan drug tiopronin. Journal of medicinal chemistry, 2011, Jul-28, Volume: 54, Issue:14 Topics: Antineoplastic Agents; ATP Binding Cassette Transporter, Subfamily B; ATP Binding Cassette Transporter, Subfamily B, Member 1; Cell Line, Tumor; Doxorubicin; Drug Resistance, Multiple; Drug Resistance, Neoplasm; Drug Screening Assays, Antitumor; HEK293 Cells; Humans; Multidrug Resistance-Associated Proteins; Orphan Drug Production; Paclitaxel; RNA Stability; RNA, Messenger; Structure-Activity Relationship; Tiopronin	2011
[Recent advances in the treatment of nephrolithiasis (author's transl)]. Aktuelle Gerontologie, 1979, Volume: 9, Issue:12 Topics: Calcium; Cystine; Fluid Therapy; Humans; Kidney Calculi; Methods; Penicillamine; Uric Acid	1979
The Seventh Frederick H. Verhoeff Lecture. Collagenase and collagenase inhibitors. Transactions of the American Ophthalmological Society, 1977, Volume: 75 Topics: Animals; Burns, Chemical; Collagen; Cystine; Edetic Acid; Eye Diseases; Humans; Keratitis; Microbial Collagenase; Penicillamine; Rabbits; Zinc	1977
[Collagenase inhibitors]. L'Annee therapeutique et clinique en ophtalmologie, 1976, Volume: 27 Topics: Animals; Corneal Ulcer; Cystine; Humans; Keratitis; Keratitis, Dendritic; Microbial Collagenase; Penicillamine; Rabbits	1976
[Collagenase inhibition: an experiment in the treatment of scleromalacia perforans (author's transl)]. Klinische Monatsblatter fur Augenheilkunde, 1979, Volume: 175, Issue:5 Topics: Aged; Cystine; Enzyme Inhibitors; Eye Diseases; Female; Humans; Microbial Collagenase; Penicillamine; Sclera	1979
Penicillamine in rheumatoid arthritis: clinical pharmacology and biochemical properties. Scandinavian journal of rheumatology. Supplement, 1979, Issue:28 Topics: Arthritis, Rheumatoid; Autoimmune Diseases; Collagen; Cystine; Drug Evaluation; Humans; Penicillamine; Pyridoxine	1979
D-penicillamine treatment in rheumatoid arthritis monitored by plasma alfa-1-antitrypsin-IgA complexes and plasma and urinary sulphur containing aminoacids. Scandinavian journal of rheumatology. Supplement, 1979, Issue:28 Topics: alpha 1-Antitrypsin; Amino Acids, Sulfur; Arthritis, Rheumatoid; Collagen; Cystine; Humans; Immunoglobulin A; Penicillamine	1979
Disulfide-disulfide interchange catalyzed by a liver supernatant enzyme. Biochimica et biophysica acta, 1979, Mar-16, Volume: 567, Issue:1 Topics: Animals; Cystine; Disulfides; Glutathione; Isomerases; Liver; Penicillamine; Rabbits; Substrate Specificity	1979
Lowering of ethanol-derived circulating blood acetaldehyde in rats by D-penicillamine. Life sciences, 1977, Jan-01, Volume: 20, Issue:1 Topics: Acetaldehyde; Animals; Breath Tests; Cysteine; Cystine; Ethanol; Male; Penicillamine; Rats	1977
The effect of thiol compounds on lymphocytes stimulated in culture. Immunology, 1978, Volume: 35, Issue:1 Topics: Animals; Cells, Cultured; Culture Media; Cystine; Lymphocyte Activation; Mice; Penicillamine; Sulfhydryl Compounds; Time Factors	1978
Mercaptopropionylglycine: a progress in cystine stone therapy. The Journal of urology, 1977, Volume: 117, Issue:5 Topics: Adult; Amino Acids, Sulfur; Cystine; Cystinuria; Female; Follow-Up Studies; Humans; Male; Penicillamine; Tiopronin; Urinary Calculi	1977
The repair, protection and sensitization of papain with respect to inactivation by H2O2 and OH: effects of dithiothreitol, penicillamine, cystine and penicillamine disulphide. International journal of radiation biology and related studies in physics, chemistry, and medicine, 1975, Volume: 28, Issue:6 Topics: Cystine; Disulfides; Dithiothreitol; Hydroxylation; Penicillamine; Peroxides; Radiation-Protective Agents; Sulfhydryl Compounds	1975
D-penicillamine and the transport of L-cystine by rat and human renal cortical brush-border membrane vesicles. The American journal of physiology, 1990, Volume: 258, Issue:2 Pt 2 Topics: Amino Acids; Animals; Biological Transport; Cystine; Diamide; Dithiothreitol; Glucose; Humans; Kidney Cortex; Male; Microvilli; Penicillamine; Rats; Rats, Inbred Strains; Sodium	1990
S-nitrosothiols as vasodilators: implications regarding tolerance to nitric oxide-containing vasodilators. British journal of pharmacology, 1989, Volume: 98, Issue:3 Topics: Acetylcysteine; Animals; Ascorbic Acid; Cattle; Chromatography, High Pressure Liquid; Coronary Vessels; Cystine; Drug Tolerance; In Vitro Techniques; Methylene Blue; Muscle Relaxation; Muscle, Smooth, Vascular; Nitric Oxide; Nitroglycerin; Penicillamine; S-Nitroso-N-Acetylpenicillamine; Vasodilator Agents	1989
Cystine calculi: clinical management and in vitro observations. Urology, 1988, Volume: 31, Issue:3 Topics: Acetylcysteine; Adult; Ascorbic Acid; Bicarbonates; Cystine; Cystinuria; Female; Homozygote; Humans; Kidney Calculi; Male; Middle Aged; Penicillamine; Sodium; Sodium Bicarbonate; Tromethamine	1988
Binding assays for amino acids. The utilization of a cystine binding protein from Escherichia coli for the determination of acid-soluble cystine in small physiological samples. The Journal of biological chemistry, 1974, Oct-10, Volume: 249, Issue:19 Topics: Amino Acids; Amino Acids, Diamino; Bacterial Proteins; Binding Sites; Binding, Competitive; Carbon Radioisotopes; Chromatography, DEAE-Cellulose; Chromatography, Ion Exchange; Cystathionine; Cystine; Cystinosis; Disulfides; Edetic Acid; Escherichia coli; Ethylmaleimide; Fibroblasts; Humans; Hydrogen-Ion Concentration; Isomerism; Kinetics; Lanthanum; Magnesium; Methods; Osmolar Concentration; Penicillamine; Pimelic Acids; Protein Binding; Radioligand Assay; Receptors, Drug; Sodium Chloride	1974
[Satisfactory prophylaxis of urinary lithiasis with D-penicillamine in cystinuria]. La semaine des hopitaux : organe fonde par l'Association d'enseignement medical des hopitaux de Paris, 1970, Apr-08, Volume: 46, Issue:17 Topics: Adult; Cysteine; Cystine; Cystinuria; Diet Therapy; Female; Humans; Penicillamine; Urinary Calculi	1970
Collagenase inhibitors (penicillamine). Annals of ophthalmology, 1973, Volume: 5, Issue:4 Topics: Adult; Alkalies; Animals; Arginine; Bacitracin; Burns, Chemical; Cicatrix; Contact Lenses, Hydrophilic; Cornea; Corneal Ulcer; Cystamine; Cysteine; Cystine; Edetic Acid; Eye Burns; Female; Fibroblasts; Glutathione; Humans; Leukocytes; Magnesium Sulfate; Male; Methods; Microbial Collagenase; Middle Aged; Penicillamine; Rabbits; Spectrophotometry, Atomic	1973
[Experimental studies on the chemical dissolution of cystine stones]. Arzneimittel-Forschung, 1972, Volume: 22, Issue:9 Topics: Animals; Cysteamine; Cysteine; Cystine; Disulfides; Dithiothreitol; Glutathione; Glycine; Isomerism; Kidney Calculi; Lethal Dose 50; Mercaptopurine; Mice; Penicillamine; Rabbits; Rats; Solubility; Spectrophotometry, Infrared; Sulfhydryl Compounds; Water	1972
[Cystinuria: influence of D-penicillamine on the concentration of cystine in serum and urine]. Ceskoslovenska pediatrie, 1973, Volume: 28, Issue:2 Topics: Cystine; Cystinuria; Female; Humans; Infant; Penicillamine	1973
[Studies on the formation of mixed disulfides between D-penicillamine and serum proteins (author's transl)]. Research in experimental medicine. Zeitschrift fur die gesamte experimentelle Medizin einschliesslich experimenteller Chirurgie, 1973, Nov-23, Volume: 161, Issue:4 Topics: Animals; Blood Proteins; Cysteine; Cystine; Disulfides; Ethylmaleimide; Male; Penicillamine; Protein Binding; Rats; Serum Albumin	1973
Diagnosis and treatment of cystinuria. Urology, 1974, Volume: 3, Issue:2 Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Bicarbonates; Biological Transport; Coloring Agents; Crystallization; Cystine; Cystinuria; Diet Therapy; Female; Humans; Kidney Calculi; Middle Aged; Penicillamine; Ureteral Obstruction; Water; X-Ray Diffraction	1974
Crystal and molecular structure of bis(copper(II) D-penicillamine disulfide) nonahydrate, a derivative of copper(II) cystinate. Journal of the American Chemical Society, 1974, Feb-06, Volume: 96, Issue:3 Topics: Copper; Cystine; Disulfides; Methods; Molecular Conformation; Organometallic Compounds; Penicillamine; Solubility; Water; X-Ray Diffraction	1974
Excerpts from the casebook of Jason Harbro, M.D., AME. Aerospace medicine, 1974, Volume: 45, Issue:3 Topics: Adult; Aerospace Medicine; Cystine; Cystinuria; Deafness; Female; Hearing Tests; Humans; Male; Middle Aged; Penicillamine	1974
Determination of cystine excretion by the nitroprusside method during drug therapy of cystinuria. Clinica chimica acta; international journal of clinical chemistry, 1974, May-17, Volume: 52, Issue:3 Topics: Amino Acids, Sulfur; Cystine; Cystinuria; Electrophoresis, Paper; Evaluation Studies as Topic; Ferricyanides; Glycine; Humans; Indicators and Reagents; Methods; Penicillamine; Time Factors	1974
Cystinosis: selective induction of vacuolation in fibroblasts by L-cysteine-D-penicillamine disulfide. Science (New York, N.Y.), 1970, Aug-07, Volume: 169, Issue:3945 Topics: Biological Transport; Culture Techniques; Cysteine; Cystine; Cystinosis; Cytoplasm; Fibroblasts; Humans; Lysosomes; Microscopy, Phase-Contrast; Penicillamine; Sulfides	1970
[Drug therapy in urinary calculi. II. Peroral litholysis and prevention]. Urologia internationalis, 1972, Volume: 27, Issue:3 Topics: Administration, Oral; Allopurinol; Cystine; Humans; Magnesium; Oxalates; Penicillamine; Phosphates; Pyridoxine; Quaternary Ammonium Compounds; Urinary Calculi	1972
Disulfide stereochemistry. Conformations and chiroptical properties of L-Cystine derivatives. Journal of the American Chemical Society, 1972, Aug-23, Volume: 94, Issue:17 Topics: Chemical Phenomena; Chemistry; Circular Dichroism; Cystine; Disulfides; Magnetic Resonance Spectroscopy; Methylation; Penicillamine; Peptides; Protein Conformation; Spectrum Analysis; Ultraviolet Rays	1972
Treatment of cystinosis with a diet poor in cystine and methionine. Acta paediatrica Scandinavica, 1970, Volume: 59, Issue:6 Topics: Amino Acids; Body Height; Body Weight; Child; Child, Preschool; Cysteine; Cystine; Cystinosis; Cystinuria; Diet Therapy; Dwarfism; Ergocalciferols; Female; Humans; Ketoglutaric Acids; Male; Methionine; Pedigree; Penicillamine; Pyruvates; Renal Tubular Transport, Inborn Errors	1970
Quantitative determination of biologically important thiols and disulfides by gas-liquid chromatography. Analytical biochemistry, 1969, Oct-01, Volume: 31, Issue:1 Topics: Aldehydes; Chromatography, Gas; Cystamine; Cysteamine; Cysteine; Cystine; Homocysteine; Homocystine; Hot Temperature; Hydrogen-Ion Concentration; Lactones; Methionine; Methods; Penicillamine; Sulfhydryl Compounds; Sulfides	1969
[Problems in the therapy of cystine urolithiasis using penicillamine]. Bratislavske lekarske listy, 1970, Volume: 53, Issue:3 Topics: Adolescent; Cystine; Female; Humans; Male; Penicillamine; Proteinuria; Urinary Calculi	1970
Cystinuria, hyperuricemia and uric acid nephrolithiasis. Case report. Nephron, 1970, Volume: 7, Issue:6 Topics: Adult; Allopurinol; Cystine; Cystinuria; Female; Glycine; Humans; Kidney Calculi; Penicillamine; Uric Acid; Urine	1970
[Preoperative diagnosis and postoperative treatment of cystine calculi]. Zeitschrift fur Urologie und Nephrologie, 1970, Volume: 63, Issue:12 Topics: Adult; Cystine; Cystinuria; Diet Therapy; Female; Humans; Hydrogen-Ion Concentration; Kidney Calculi; Middle Aged; Penicillamine; Postoperative Care	1970
[Therapeutic problems during D-penicillamine treatment of patients with cystine calculi]. Munchener medizinische Wochenschrift (1950), 1970, Nov-27, Volume: 112, Issue:48 Topics: Adolescent; Adult; Albuminuria; Copper; Cystine; Cystinuria; Female; Humans; Kidney Calculi; Penicillamine; Pregnancy; Pregnancy Complications; Proteinuria	1970
Cystinosis: therapeutic implications of in vitro studies of cultured fibroblasts. The Journal of pediatrics, 1971, Volume: 78, Issue:5 Topics: Biopsy; Child; Chromatography; Culture Techniques; Cystine; Cystinosis; Diet Therapy; Fibroblasts; Glomerulonephritis; Humans; Penicillamine; Skin; Sulfur Isotopes	1971
Cystinosis. Plasma cystine and cysteine concentrations and the effect of D-penicillamine and dietary treatment. The American journal of medicine, 1968, Volume: 44, Issue:3 Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Blood Chemical Analysis; Cysteine; Cystine; Cystinosis; Cystinuria; Diet Therapy; Female; Humans; Infant; Male; Methionine; Nitrogen; Penicillamine; Pyruvates	1968
Cystine stones treated by surgery and D-penicillamine. Proceedings of the Royal Society of Medicine, 1968, Volume: 61, Issue:11 Part 1 Topics: Adolescent; Cystine; Cystinuria; England; Follow-Up Studies; Humans; Kidney Calculi; Male; Penicillamine; Scotland; United States; Urography	1968
[Conservative treatment of kidney calculi]. Medizinische Klinik, 1969, Feb-14, Volume: 64, Issue:7 Topics: Allopurinol; Calcium; Calcium Phosphates; Chemical Phenomena; Chemistry; Citrates; Cystine; Diagnosis, Differential; Diet Therapy; Humans; Kidney Calculi; Magnesium; Oxalates; Penicillamine; Phosphates; Quaternary Ammonium Compounds; Uric Acid; Xanthines	1969
Separation of cystine, penicillamine disulfide and cysteine-penicillamine mixed disulfide by automatic amino acid analysis. Analytical biochemistry, 1966, Volume: 14, Issue:3 Topics: Autoanalysis; Blood Chemical Analysis; Chemistry, Clinical; Chromatography, Ion Exchange; Cysteine; Cystine; Cystinuria; Humans; In Vitro Techniques; Penicillamine; Sulfides; Urine	1966
[An effective dietetic and medicinal treatment of cystinosis]. Helvetica paediatrica acta, 1966, Volume: 21, Issue:1 Topics: Amino Acids; Child, Preschool; Cystine; Cystinosis; Diet Therapy; Humans; Kidney Function Tests; Male; Methenolone; Penicillamine; Pyruvates; Vitamin D	1966
The renal clearance of amino acids in cystinuria. The Journal of clinical investigation, 1967, Volume: 46, Issue:7 Topics: Adolescent; Adult; Arginine; Child; Chromatography, Ion Exchange; Cystine; Cystinuria; Female; Glomerular Filtration Rate; Glycine; Humans; Inulin; Lysine; Male; Ornithine; Penicillamine	1967
Treatment of cystinuria and cystine stone disease. Modern treatment, 1967, Volume: 4, Issue:3 Topics: Cystine; Cystinuria; Humans; Penicillamine; Urinary Calculi	1967
[Medical treatment of cystine lithiasis in children]. Journal d'urologie, 1984, Volume: 90, Issue:2 Topics: Amino Acids, Sulfur; Child; Cystine; Female; Humans; Male; Penicillamine; Recurrence; Tiopronin; Urinary Calculi	1984
[Results of long-term treatment of cystine lithiasis with D-penicillamine]. Nephrologie, 1984, Volume: 5, Issue:5 Topics: Adult; Age Factors; Child, Preschool; Cystine; Cystinuria; Female; Humans; Kidney Calculi; Male; Middle Aged; Penicillamine	1984
Alternative treatment of cystinuria with alpha-merkaptopropionylglycine, Thiola. Proceedings of the European Dialysis and Transplant Association. European Dialysis and Transplant Association, 1983, Volume: 20 Topics: Adolescent; Adult; Aged; Amino Acids, Sulfur; Cystine; Cystinuria; Dipeptides; Female; Humans; Male; Middle Aged; Penicillamine; Tiopronin; Urinary Calculi	1983
[Cystinuria therapy by ascorbic acid (author's transl)]. Urologia internationalis, 1982, Volume: 37, Issue:2 Topics: Ascorbic Acid; Cysteine; Cystine; Cystinuria; Humans; Intestinal Absorption; Kidney; Penicillamine; Tiopronin	1982
Cystine stones. Urology, 1980, Volume: 16, Issue:4 Topics: Adolescent; Adult; Aged; Child, Preschool; Cystine; Cystinuria; Female; Humans; Male; Middle Aged; Penicillamine; Recurrence; Urinary Calculi	1980
Dissolution of cystine calculi by pelviocaliceal irrigation with D-penicillamine. The Journal of urology, 1980, Volume: 124, Issue:6 Topics: Adolescent; Cystine; Cystinuria; Female; Humans; Kidney Calculi; Patient Compliance; Penicillamine; Therapeutic Irrigation	1980
Seleno compounds and glutathione peroxidase catalyzed decomposition of S-nitrosothiols. Biochemical and biophysical research communications, 1996, Nov-01, Volume: 228, Issue:1 Topics: Catalysis; Cystamine; Cystine; Glutathione; Glutathione Peroxidase; Nitric Oxide; Nitroso Compounds; Organoselenium Compounds; Penicillamine; S-Nitroso-N-Acetylpenicillamine; S-Nitrosoglutathione; Sulfhydryl Compounds	1996
Clinical aspects of cystinuria. Contributions to nephrology, 1997, Volume: 122 Topics: Adolescent; Adult; Chelating Agents; Child; Child, Preschool; Cystine; Cystinuria; Diet; Female; Humans; Kidney Calculi; Male; Middle Aged; Pedigree; Penicillamine; Risk Factors; Solubility; Tiopronin	1997
The long-term outcome of cystinuria in Japan. Urologia internationalis, 1998, Volume: 61, Issue:2 Topics: Adult; Chelating Agents; Cystine; Cystinuria; Female; Follow-Up Studies; Humans; Hydrogen-Ion Concentration; Japan; Male; Penicillamine; Recurrence; Tiopronin; Treatment Outcome; Urinary Calculi	1998
Stimulation of cystine uptake by nitric oxide: regulation of endothelial cell glutathione levels. The American journal of physiology, 1999, Volume: 276, Issue:4 Topics: Animals; Aorta; Biological Transport; Cattle; Cells, Cultured; Cycloheximide; Cystine; Cytosol; Dactinomycin; Endothelium, Vascular; Glutamic Acid; Glutathione; Kinetics; Nitric Oxide; Penicillamine; S-Nitroso-N-Acetylpenicillamine; Time Factors	1999
Investigation of the transport of intact glutathione in human and rat type II pneumocytes. Free radical research, 1999, Volume: 30, Issue:5 Topics: Animals; Antimetabolites; Biological Transport; Cells, Cultured; Cystine; Glutathione; Humans; Isoxazoles; Lung; Male; Ouabain; Penicillamine; Rats; Rats, Wistar; Sulfhydryl Compounds	1999
Adaptive responses to peroxynitrite: increased glutathione levels and cystine uptake in vascular cells. American journal of physiology. Cell physiology, 2000, Volume: 279, Issue:4 Topics: Adaptation, Physiological; Animals; Cattle; Cells, Cultured; Cystine; Dose-Response Relationship, Drug; Endothelium, Vascular; Free Radical Scavengers; Glutamic Acid; Glutathione; Metalloporphyrins; Molsidomine; Muscle, Smooth, Vascular; Nitrates; Nitric Oxide Donors; Nucleic Acid Synthesis Inhibitors; Penicillamine; Protein Synthesis Inhibitors; S-Nitroso-N-Acetylpenicillamine; Sodium; Superoxide Dismutase	2000
Structure, function, and regulation of human cystine/glutamate transporter in retinal pigment epithelial cells. Investigative ophthalmology & visual science, 2001, Volume: 42, Issue:1 Topics: Amino Acid Sequence; Amino Acid Transport System y+; Carrier Proteins; Cells, Cultured; Cloning, Molecular; Cystine; DNA Primers; Eye Proteins; Gene Expression; Gene Library; Glutamic Acid; Glyceraldehyde-3-Phosphate Dehydrogenases; Humans; Molecular Sequence Data; Nitric Oxide; Penicillamine; Pigment Epithelium of Eye; Reverse Transcriptase Polymerase Chain Reaction; RNA, Messenger; Sequence Homology, Amino Acid; Structure-Activity Relationship; Substrate Specificity	2001
Redox regulation of cytosolic glycerol-3-phosphate dehydrogenase: Cys(102) is the target of the redox control and essential for the catalytic activity. Biochimica et biophysica acta, 2002, Jan-15, Volume: 1569, Issue:1-3 Topics: Animals; Binding Sites; Catalysis; CHO Cells; Cricetinae; Cysteine; Cystine; Cytosol; Ethylmaleimide; Glutathione; Glycerolphosphate Dehydrogenase; In Vitro Techniques; Nitric Oxide Donors; Oxidation-Reduction; Penicillamine; Sodium Selenite; Transfection	2002
Regulation of L-cystine transport and intracellular GSH level by a nitric oxide donor in primary cultured rabbit conjunctival epithelial cell layers. Investigative ophthalmology & visual science, 2003, Volume: 44, Issue:3 Topics: Animals; Biological Transport; Blotting, Western; Cells, Cultured; Conjunctiva; Cystine; Epithelial Cells; Glutamate-Cysteine Ligase; Glutathione; Male; Nitric Oxide Donors; Penicillamine; Permeability; Rabbits; Sodium	2003
Formation of D-penicillamine-cysteine mixed disulphide by reaction of D-benzylpenicilloic acid with cystine. Nature, 1960, Sep-10, Volume: 187 Topics: Cysteine; Cystine; Disulfides; Penicillamine; Penicillin G; Penicillins; Valine	1960
THE RATIONALE OF MIXED DISULPHIDES IN THE TREATMENT OF CYSTINURIA. Scandinavian journal of clinical and laboratory investigation, 1964, Volume: 16 Topics: Calculi; Cysteamine; Cystine; Cystinuria; Glutathione; Humans; Metabolism; Penicillamine	1964
[CONTRIBUTION TO THE STUDY OF CYSTINOSIS. OBSERVATIONS ON THE DETERMINATION OF CYSTIN IN THE SERUM AND THERAPEUTIC RESULTS WITH PENICILLAMINE AND ANABOLIC STEROIDS]. Annales paediatrici. International review of pediatrics, 1964, Volume: 202 Topics: Amino Acids; Anabolic Agents; Blood; Cystine; Cystinosis; Drug Therapy; Humans; Infant; Penicillamine; Steroids; Testosterone Congeners; Urine; Vitamin D; Vitamins	1964
SPECTROPHOTOMETRIC DETERMINATION OF DISULFIDES, SULFINIC ACIDS, THIO ETHERS, AND THIOLS WITH THE PALLADIUM (II) ION. Analytical biochemistry, 1964, Volume: 8 Topics: Benzoates; Cysteamine; Cysteine; Cystine; Disulfides; Ethers; Glutathione; Homocysteine; Lactones; Methionine; Palladium; Penicillamine; Phosphates; Research; Spectrophotometry; Sulfhydryl Compounds; Sulfides; Sulfinic Acids; Sulfites; Thiosulfates	1964
CYSTINURIA: EFFECT OF D-PENICILLAMINE ON PLASMA AND URINARY CYSTINE CONCENTRATIONS. Science (New York, N.Y.), 1965, Mar-19, Volume: 147, Issue:3664 Topics: Arginine; Blood; Cysteine; Cystine; Cystinuria; Drug Therapy; Humans; Lysine; Penicillamine; Sulfides; Urine	1965
METHODS OF DIMINISHING CYSTINE EXCRETION IN CYSTINURIA. The Journal of urology, 1965, Volume: 93 Topics: Acetylcysteine; Amino Acids; Cysteine; Cystine; Cystinuria; Diet; Diet Therapy; Drug Therapy; Fluids and Secretions; Indoles; Oxandrolone; Penicillamine; Rats; Sulfur; Vitamin B 6 Deficiency	1965
DEFICIENCIES OF -SH-DEPENDENT ENZYMES IN CYSTINOSIS. Clinical science, 1965, Volume: 28 Topics: Alcohol Oxidoreductases; Alkaline Phosphatase; Child; Coenzyme A; Cysteine; Cystine; Cystinosis; Dimercaprol; Electron Transport Complex II; Enzymes; Glucose-6-Phosphatase; Glycerolphosphate Dehydrogenase; Hexokinase; Hydro-Lyases; Kidney; Leucyl Aminopeptidase; Liver; Muscles; Penicillamine; Pharmacology; Phosphogluconate Dehydrogenase; Succinate Dehydrogenase; Sulfhydryl Compounds; Tissue Extracts; Transaminases	1965
Urinary excretion of total cystine and the dibasic amino acids arginine, lysine and ornithine in relation to genetic findings in patients with cystinuria treated with sulfhydryl compounds. Urological research, 2003, Volume: 31, Issue:6 Topics: Adolescent; Adult; Aged; Aged, 80 and over; Alleles; Amino Acid Transport Systems, Basic; Amino Acids, Diamino; Arginine; Carrier Proteins; Cystine; Cystinuria; Female; Humans; Lysine; Male; Membrane Glycoproteins; Middle Aged; Mutation; Ornithine; Penicillamine; Sulfhydryl Compounds; Tiopronin	2003
Understanding base-assisted desulfurization using a variety of disulfide-bridged peptides. Biopolymers, 2003, Volume: 71, Issue:5 Topics: Cystine; Disulfides; Homocysteine; Penicillamine; Peptides; Protein Structure, Secondary; Sulfur; Temperature	2003
Studies of urinary cystine precipitation in vitro: ontogeny of cystine nephrolithiasis and identification of meso-2,3-dimercaptosuccinic acid as a potential therapy for cystinuria. Molecular genetics and metabolism, 2003, Volume: 80, Issue:4 Topics: Adolescent; Age Factors; Chemical Precipitation; Child; Child, Preschool; Cystine; Cystinuria; Dose-Response Relationship, Drug; Humans; Infant; Kidney Diseases; Lithiasis; Penicillamine; Reference Values; Succimer; Tiopronin; Urine	2003
Theoretical and experimental sulfur K-edge X-ray absorption spectroscopic study of cysteine, cystine, homocysteine, penicillamine, methionine and methionine sulfoxide. Dalton transactions (Cambridge, England : 2003), 2009, May-14, Issue:18 Topics: Cysteine; Cystine; Homocysteine; Hydrogen-Ion Concentration; Mercury; Methionine; Molecular Conformation; Nickel; Penicillamine; Protons; Spectrometry, X-Ray Emission; Sulfur Compounds; Water	2009
Natural history and quality of life in patients with cystine urolithiasis: a single centre study. BJU international, 2015, Volume: 116 Suppl 3 Topics: Adult; Aged; Australia; Chelating Agents; Cohort Studies; Cystine; Cystinuria; Female; Health Surveys; Humans; Male; Middle Aged; Penicillamine; Quality of Life; Surveys and Questionnaires; Urolithiasis; Urologic Surgical Procedures	2015