citrulline and lysine

citrulline has been researched along with lysine in 153 studies

Research

Studies (153)

TimeframeStudies, this research(%)All Research%
pre-199096 (62.75)18.7374
1990's17 (11.11)18.2507
2000's23 (15.03)29.6817
2010's12 (7.84)24.3611
2020's5 (3.27)2.80

Authors

AuthorsStudies
Bonini, BM; Thevelein, JM; Van Zeebroeck, G; Versele, M1
Gatfield, PD; Haust, MD; Taller, E; Wolfe, DM1
Chakrabarty, S; Duerre, JA1
Akaboshi, I; Arashima, S; Imanishi, Y; Matsuda, I; Nagata, N; Shinozuka, S; Yamamoto, J1
Bantzer, P; Jäkel, A; Liappis, N1
Batshaw, M; Brusilow, S; Kulovich, S; Nyhan, W; Spector, E; Thoene, J; Walser, M1
Nakao, T; Oyanagi, K; Sogawa, H1
Shih, VE1
Nakao, T; Orii, T; Oyanagi, K; Sato, S; Sogawa, H1
Clara, R; Mardens, Y; Strauven, T; Terheggen, H1
Counahan, R; Cox, BD; El-Bishti, M; Ogg, CS1
Awrich, AE; Cantrell, JE; Patterson, JH; Rudman, D; Stackhouse, WJ1
Harding, HW; Rogers, GE1
Imanari, T; Koshiishi, I1
Hayakawa, C; Kato, T; Mizutani, N; Sano, M1
Kato, T; Mizutani, N; Sano, M2
Bey, P; Mehdi, S; Skoog, MT; Wiseman, JS1
Botschner, J; Scriver, CR; Simell, O; Smith, DW1
Applegarth, DA; Davidson, AG; Dimmick, JE; Norman, MG; Pirie, G; Toone, JR; Wong, J; Wong, LT1
Zieve, L1
Cheung, CW; Cohen, NS; Raijman, L1
Thompson, J1
Bachmann, C; Colombo, JP; Dionisi Vici, C; Gambarara, M; Sabetta, G1
Ameen, M; Oberholzer, VG; Palmer, T1
Kurihara, T; Matsukura, S; Shioya, K; Yamamura, Y1
de Parscau, L; Divry, P; Guibaud, P; Hermier, M; Vianey-Liaud, C1
Anast, CS; Carpenter, TO; Holtrop, ME; Levy, HL; Shih, VE1
Martinez, L; Mora, J; Sanchez, S1
Hsia, YE1
Cybis, JJ; Davis, RH1
Scott-Emuakpor, AB1
Levin, B; Oberholzer, VG; Palmer, T2
Cathelineau, L; Charpentier, C; Polonovski, C; Saudubray, JM1
Jäkel, A; Liappis, N1
Eddy, AA; Inkson, C; Seaston, A1
Frimpter, GW1
Carson, NA1
Coulson, RA; Herbert, JD1
Fifkova, E; Van Harreveld, A1
Deetjen, P; Silbernagl, S1
Herbert, JD1
Teijema, HL; van Gelderen, HH1
Carson, NA; Fellows, FC1
De la Llosa, P; Durosay, M; Jutisz, M; Tertrin-Clary, C1
Fell, V; Pollitt, RJ; Sampson, GA; Wright, T1
Burgess, EA; Butler, LJ; Levin, B; Oberholzer, VG; Palmer, T1
Menne, F1
Holden, JT; Wilson, OH1
Cahill, CF; Felig, P; Marliss, E; Ohman, JL1
Colley, L; Dicker, SE; Elliott, AB; Huggins, AK; Rowe, WC1
Donner, M; Simell, O; Visakorpi, JK1
Higgins, JV; Kohrman, AF; Scott-Emuakpor, A1
Campbell, DJ; Reid, DW; Yakymyshyn, LY1
Seydoux, F; Yon, J1
Hornig, D; Weber, F; Wiss, O1
Geisler, C; Höcker, P; Stacher, A; Wiser, M1
Meyer, ME2
Bechet, J; Ramos, F; Thuriaux, P; Wiame, JM1
Gordon, WG; Hipp, NJ; Pepper, L1
Fishman, W; Sie, HG1
Badonnel, Y; Dautrevaux, M; Gelot, S; Levin, B; Neimann, N; Paysant, P; Pierson, M; Vidailhet, M1
Ogata, K; Yorifuji, T1
Anfinsen, CB; Chaiken, IM1
Evered, DF; Nunn, PB1
Frahn, JL; Mills, JA1
Hein, GE; Sanborn, BM1
Carré, LJ; Carson, NA; Neill, DW; Scally, BG1
Landau, RL; Lugibihl, K2
Efron, ML; Moser, HW; Shih, VE1
Felber, JP; Robinson, JL1
Jirgl, V1
Armstrong, MD; Robinow, M1
Ong, EB; Woody, NC1
Perheentupa, J; Rajantie, J; Simell, O5
Ishikawa, Y; Kaiser-Kupfer, MI; Kuwabara, T1
Crozier, GL; Freedland, RA; Hicks, BL; Meijer, AJ1
Eller, AG; Hommes, FA; Kitchings, L1
Behbehani, AW; Gahr, M; Schröter, W1
Carter, AL; Eller, AG; Hommes, FA; Metoki, K; Rufo, S1
Ameen, M; Palmer, T1
Perheentupa, J; Rajantie, J; Rapola, J; Simell, O1
Morimoto, K; Sato, M; Tanaka, A; Yamaha, T1
Karube, K; Minami, R; Nakao, T; Oyanagi, K; Sogawa, H; Tsugawa, S1
Kato, T; Sano, M1
Indiveri, C; Palmieri, F; Palmieri, L1
Gross, KL; Prior, RL1
Bébin, B; Candito, M; Chambon, P; Chazalette, JP; Ferraci, JP; Mathieu, M; Sebag, F; Vianey-Saban, C1
Donati, MA; Filippi, L; Resti, M; Zammarchi, E1
Aarsen, M; De Vries, PM; Donker, AJ; Smulders, RA; Stehouwer, CD; Teerlink, T; Van Kamp, GJ1
Matìjèková, A; Sychrová, H1
Kubín, J; Opekarová, M1
Belousova, AK; Shulepova, TS1
Dick, JM; Lefebvre, RA1
Ash, DE; Dismukes, GC; Khangulov, SV; Sossong, TM1
Chen, MC; Eizirik, DL; Flodström, M; Pipeleers, DG; Schuit, F; Smismans, A1
Ball, AK; Koeberle, PD1
Folkerts, G; Hammermann, R; Hey, C; Hirschmann, J; Mössner, J; Nijkamp, FP; Racké, K; Wessler, I1
Inoue, S; Kawata, S; Kayanoki, Y; Kiso, S; Matsuzawa, Y; Tamura, S; Taniguchi, N; Yamasaki, E1
Almeida, A; Bolaños, JP; Heales, SJ; Medina, JM; Vega-Agapito, V1
Cholewa, B; Mattson, DL; Wu, F1
Fathman, CG; Kim, DT; Mitchell, DJ; Rothbard, JB; Steinman, L1
Gauthier, S; Law, A; Quirion, R1
Donabedian, M; Hare, JM; Rosas, GO; Vandegaer, K; Zieman, SJ1
Casanello, P; Sobrevia, L1
Kueh, R; Merican, AF; Rahman, NA1
Chibber, R; Ferro, A; Kohner, E; Ritter, J; Ruggerio, D; Ruggiero, D; Xu, B1
David, L; Dionisi-Vici, C; Dolce, V; Fiermonte, G; Palmieri, F; Santorelli, FM; Walker, JE1
Aalto, M; Lukkarinen, M; Näntö-Salonen, K; Pulkki, K; Simell, O1
STEWART, I1
RYAN, WL; WELLS, IC1
CRAFT, MK; DEWALD, HA; NICOLAIDES, ED1
KIM, S; PAIK, WK1
BAUERLE, RH; GARNER, HR1
ALLISON, F; LANCASTER, MG1
LEWANDOWSKI, V; MAXWELL, RE; NICKEL, VS1
Evans, RW; Fernstrom, JD; Kuller, LH; Morris, SM; Thompson, J1
Haginaka, J; Honda, C; Hoshina, K; Ogawa, T; Tanimoto, T; Uchida, T1
Bachmann, C; Boulat, O; Carrozzo, R; Dionisi-Vici, C; Emma, F; Mannucci, L; Markert, M; Rizzoni, G1
Giangregorio, N; Indiveri, C; Palmieri, F; Tonazzi, A1
Angrand, PO; Vandamme, J1
Costello, AL; Fast, W; Stone, EM; Tierney, DL1
Brunini, TM; Ellory, JC; Mann, GE; Mendes Ribeiro, AC; Moss, MB; Roberts, NB; Siqueira, MA; Yaqoob, MM1
Huoponen, K; Näntö-Salonen, K; Niinikoski, H; Simell, O; Tanner, LM1
Helanterä, A; Huoponen, K; Jahnukainen, T; Kananen, K; Keskinen, P; Linnanvuo, M; Metso, M; Näntö-Salonen, K; Niinikoski, H; Saha, H; Simell, O; Tanner, LM1
Elkabes, S; Grant, JE; Hu, J; Jain, MR; Li, H; Liu, T1
Huoponen, K; Kotilainen, S; Näntö-Salonen, K; Niinikoski, H; Simell, O; Tanner, LM; Venetoklis, J1
Ischiropoulos, H; Rader, DJ1
Brennan, DM; Cho, L; Hazen, SL; Tang, WH; Wang, Z1
Chen, G; Doret, P; Hao, G; Li, P; Qiu, H; Shen, Q; Wang, D; Wang, Y; Yao, H; Zhang, X1
Dietzen, DJ; Shinawi, M; Sprietsma, L; Weymann, A; White, FV1
Delporte, C; Desmet, JM; Dufour, D; Franck, T; Madhoun, P; Moguilevsky, N; Nève, J; Nortier, J; Noyon, C; Raes, M; Rousseau, A; Serteyn, D; Van Antwerpen, P; Vanhaeverbeek, M; Vanhamme, L; Zouaoui Boudjeltia, K1
Rubio-Texeira, M; Schothorst, J; Thevelein, JM; Van Zeebroeck, G1
Bergum, B; Bielecka, E; Binder, V; Blom, AM; Brun, JG; Dahl-Knudsen, A; Enghild, JJ; Hellvard, A; Jonsson, R; Koro, C; Mydel, P; Potempa, J; Scavenius, C1
Elferink, CJ; Joshi, AD; Lichti, CF; Mustafa, MG1
Alten, R; Bang, H; Cobra, JF; Englbrecht, M; Feuchtenberger, M; Figueiredo, CP; Finzel, S; Fleck, M; Haschka, J; Henes, J; Hueber, AJ; Kleinert, S; Kleyer, A; Krueger, K; Lorenz, HM; Manger, B; Manger, K; Nuesslein, H; Ochs, W; Rech, J; Reiser, M; Ronneberger, M; Schett, G; Schmitt-Haendle, M; Schuch, F; Tony, HP; Wendler, J1
Cheng, J; Li, N; Shen, J; Song, Q; Zhang, X1
Aliani, M; Hanson, M; Taylor, CG; Zahradka, P1
Chen, L; Chen, SL; Cui, D; Hu, YH; Liao, JX; Shen, D; Tang, G1
Bollenbach, A; Brunner, G; Hanff, E; Tsikas, D1
Auge, D; Chafai, A; Fromm, MF; Gessner, A; Maas, R; Mieth, M; Müller, F1
Atabani, S; Boocock, D; Brentville, VA; Choudhury, RH; Cook, KW; Coveney, C; Daniels, I; Durrant, LG; Gijon, M; Metheringham, RL; Miles, AK; Shah, S; Symonds, P; Vaghela, P; Weston, D; Xue, W1
Beckmann, B; Blau, LS; Dimina, L; Finkel, A; Jantz, M; Lützow, M; Maassen, N; Mariotti, F; Röhrig, MA; Shushakov, V; Thorns, A; Tsikas, D1
Chen, Y; Wang, G; Wang, Z; Yan, X; Zhang, L; Zhao, F; Zhou, M1
Ban, Q; Hou, YY; Huang, T; Ma, B; Shi, L; Zhang, ML; Zhang, Q; Zhou, YF1
Elango, R1

Reviews

6 review(s) available for citrulline and lysine

ArticleYear
Conditional deficiencies of ornithine or arginine.
    Journal of the American College of Nutrition, 1986, Volume: 5, Issue:2

    Topics: Amino Acids; Amino Acids, Branched-Chain; Ammonia; Animals; Arginine; Citrulline; Female; Glycine; Hepatic Encephalopathy; Humans; Liver Cirrhosis; Lysine; Models, Biological; Ornithine; Orotic Acid; Pregnancy; Protein Deficiency; Urease

1986
Inherited hyperammonemic syndromes.
    Gastroenterology, 1974, Volume: 67, Issue:2

    Topics: Acidosis; Amino Acids; Ammonia; Animals; Arginine; Brain; Brain Diseases; Chemical and Drug Induced Liver Injury; Citrulline; Dementia; Homeostasis; Humans; Infant, Newborn; Liver; Lysine; Metabolism, Inborn Errors; Ornithine Carbamoyltransferase; Phosphotransferases; Succinates; Syndrome; Urea; Urease

1974
Aminoacidurias due to inherited disorders of metabolism. 2.
    The New England journal of medicine, 1973, Oct-25, Volume: 289, Issue:17

    Topics: Acidosis; Alanine; Amino Acid Metabolism, Inborn Errors; Arginase; Arginine; Carbamates; Citrulline; Dipeptides; Glutarates; Glycine; Histidine; Humans; Hydroxyproline; Hyperglycemia; Infant, Newborn; Keto Acids; Lysine; Malonates; Maple Syrup Urine Disease; Ornithine Carbamoyltransferase; Phosphotransferases; Proline; Sarcosine; Succinates; Urea; Valine

1973
Metabolic errors in lysine degradation.
    Clinics in endocrinology and metabolism, 1974, Volume: 3, Issue:1

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Child; Child, Preschool; Citrulline; Collagen; Electroencephalography; Female; Fibroblasts; Humans; Hydroxylysine; Lysine; Male; Oxidoreductases; Pipecolic Acids

1974
[Feeble mindedness caused by genetic disorders of amino acid metabolism].
    Hippokrates, 1968, May-31, Volume: 39, Issue:10

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Glycine; Hartnup Disease; Histidine; Homocystinuria; Humans; Hydroxyproline; Intellectual Disability; Lysine; Maple Syrup Urine Disease; Methionine; Phenylketonurias; Proline; Sarcosine; Succinates; Transferases; Tryptophan; Valine

1968
Tolerable Upper Intake Level for Individual Amino Acids in Humans: A Narrative Review of Recent Clinical Studies.
    Advances in nutrition (Bethesda, Md.), 2023, Volume: 14, Issue:4

    Topics: Aged; Arginine; Citrulline; Histidine; Humans; Leucine; Lysine; Methionine; Ornithine; Phenylalanine; Serine; Tryptophan

2023

Trials

2 trial(s) available for citrulline and lysine

ArticleYear
Haemodynamic and biochemical responses to L-arginine and L-lysine infusions in normal subjects: L-arginine-induced vasodilatation cannot be explained by non-specific effects of cationic amino acids.
    Clinical science (London, England : 1979), 1997, Volume: 92, Issue:4

    Topics: Adult; Arginine; Atrial Natriuretic Factor; Blood Pressure; Citrulline; Cyclic GMP; Electrolytes; Extracellular Space; Female; Heart Rate; Humans; Lysine; Male; Nitric Oxide; Vascular Resistance; Vasodilation

1997
Short-Term Supplementation of Sodium Nitrate vs. Sodium Chloride Increases Homoarginine Synthesis in Young Men Independent of Exercise.
    International journal of molecular sciences, 2022, Sep-13, Volume: 23, Issue:18

    Topics: Arginine; Citrulline; Creatine; Creatinine; Dietary Supplements; Glutamates; Glutamine; Glycine; Homoarginine; Humans; Lysine; Male; Malondialdehyde; Methyltransferases; Nitrates; Nitrites; Ornithine; Phenylalanine; Sarcosine; Sodium Chloride; Tryptophan; Tyrosine

2022

Other Studies

145 other study(ies) available for citrulline and lysine

ArticleYear
Transport and signaling via the amino acid binding site of the yeast Gap1 amino acid transceptor.
    Nature chemical biology, 2009, Volume: 5, Issue:1

    Topics: Amino Acid Transport Systems; Amino Acids; Biological Transport; Catalytic Domain; Dipeptides; Gene Expression Regulation, Fungal; Mutagenesis; Protein Conformation; Protein Structure, Tertiary; Saccharomyces cerevisiae; Saccharomyces cerevisiae Proteins; Signal Transduction

2009
Hyperornithinemia, hyperammonemia, and homocitrullinuria associated with decreased carbamyl phosphate synthetase I activity.
    Pediatric research, 1975, Volume: 9, Issue:5

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Biopsy; Carbamoyl-Phosphate Synthase (Ammonia); Child; Child, Preschool; Citrulline; Dietary Proteins; Female; Humans; Leukocytes; Liver; Lysine; Male; Microscopy, Electron; Mitochondria, Liver; Ornithine; Phosphotransferases

1975
l-amino acid oxidases of Proteus rettgeri.
    Journal of bacteriology, 1975, Volume: 121, Issue:2

    Topics: Amino Acid Oxidoreductases; Amino Acids; Arginine; Carbon Radioisotopes; Cell Fractionation; Cell-Free System; Centrifugation, Density Gradient; Chelating Agents; Citrulline; Deamination; Histidine; Hot Temperature; Hydrogen-Ion Concentration; Isoenzymes; Kinetics; Lysine; Ornithine; Oxygen Consumption; Proteus; Pyruvates; Stereoisomerism

1975
Lysine intolerance in a variant form of citrullinemia.
    Pediatric research, 1979, Volume: 13, Issue:10

    Topics: Adolescent; Adult; Amino Acids; Ammonia; Citrulline; Cystine; Female; Humans; Lysine

1979
[Normal range of free amino acids in cerebrospinal fluid of children (author's transl)].
    Klinische Padiatrie, 1977, Volume: 189, Issue:2

    Topics: Adolescent; Age Factors; Amino Acids; Aspartic Acid; Child; Child, Preschool; Citrulline; Female; Histidine; Humans; Infant; Lysine; Male; Methods; Serine; Sex Factors; Threonine; Tyrosine

1977
Neonatal citrllinemia: treatment with keto-analogues of essential amino acids.
    The Journal of pediatrics, 1977, Volume: 90, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Essential; Arginine; Argininosuccinate Synthase; Citrulline; Fibroblasts; Histidine; Humans; Infant; Infant, Newborn; Isoleucine; Leucine; Lysine; Male; Methionine; Phenylalanine; Threonine; Tryptophan; Valine

1977
Periodic hyperammonemia, hyperlysinemia, and homocitrullinuria associated with decreased argininosuccinate synthetase and arginase activities.
    Pediatric research, 1977, Volume: 11, Issue:9 Pt 1

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginase; Arginine; Argininosuccinate Synthase; Citrulline; Humans; Hyperargininemia; Intellectual Disability; Ligases; Liver; Lysine; Male

1977
Congenital hyperammonemic syndromes.
    Clinics in perinatology, 1976, Volume: 3, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinate Synthase; Argininosuccinic Aciduria; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Diagnosis, Differential; Humans; Hyperargininemia; Infant, Newborn; Infant, Newborn, Diseases; Lysine; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Syndrome; Urea

1976
Clinical and biochemical studies on periodic hyperammonemia with hyperlysinemia and homocitrullinuria.
    The Tohoku journal of experimental medicine, 1976, Volume: 120, Issue:2

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Amino Acids; Anorexia; Arginase; Arginine; Citrulline; Erythrocytes; Growth Disorders; Humans; Intellectual Disability; Lysine; Male

1976
Intravenous loading with arginine-hydrochloride and ornithine-aspartate in siblings of two families, presenting a familial neurological syndrome associated with cystinuria.
    Biomedicine / [publiee pour l'A.A.I.C.I.G.], 1976, Volume: 24, Issue:3

    Topics: Amino Acids; Arginine; Aspartic Acid; Child; Citrulline; Cystinuria; Glutamine; Humans; Hyperargininemia; Lysine; Ornithine

1976
Plasma amino acids in children and adolescents on hemodialysis.
    Kidney international, 1976, Volume: 10, Issue:6

    Topics: Adolescent; Amino Acids; Child; Child Nutritional Physiological Phenomena; Citrulline; Diet; Female; Glycine; Growth; Histidine; Humans; Isoleucine; Leucine; Lysine; Male; Methylhistidines; Nutritional Physiological Phenomena; Proline; Renal Dialysis; Serine; Tyrosine; Valine

1976
Hyperdibasicaminoaciduria, hyperammonemia, and growth retardation: Treatment with arginine, lysine, and citrulline.
    The Journal of pediatrics, 1975, Volume: 87, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Child; Citrulline; Female; Growth Disorders; Humans; Lysine

1975
Isolation of peptides containing citrulline and the cross-link, epsilon-(gamma-glutamyl)lysine, from hair medulla protein.
    Biochimica et biophysica acta, 1976, Mar-18, Volume: 427, Issue:1

    Topics: Amino Acids; Binding Sites; Citrulline; Glutamates; Hair; Lysine; Macromolecular Substances; Peptide Fragments; Protein Binding; Protein Conformation; Proteins; Thermolysin; Trypsin

1976
State analysis of endogenous cyanate ion in human plasma.
    Journal of pharmacobio-dynamics, 1990, Volume: 13, Issue:4

    Topics: Adult; Aged; Blood Proteins; Carbamates; Citrulline; Cyanates; Erythrocytes; Female; Humans; Lysine; Male; Middle Aged; Renal Dialysis; Sulfhydryl Compounds; Urea

1990
Homocitrullinuria and homoargininuria in hyperargininaemia.
    Journal of inherited metabolic disease, 1988, Volume: 11, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Child; Child, Preschool; Citrulline; Homoarginine; Humans; Lysine; Male

1988
Homocitrullinuria and homoargininuria in lysinuric protein intolerance.
    Journal of inherited metabolic disease, 1989, Volume: 12, Issue:2

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Arginine; Child; Citrulline; Female; Homoarginine; Humans; Kidney; Lysine; Male; Ornithine

1989
The specificity of two proteinases that cleave adjacent to arginine, C1 esterase and acrosin, for peptide p-nitroanilide substrates.
    Biochimica et biophysica acta, 1989, Jun-13, Volume: 996, Issue:1-2

    Topics: Acrosin; Anilides; Arginine; Binding Sites; Citrulline; Complement Activating Enzymes; Complement C1s; Humans; In Vitro Techniques; Kinetics; Lysine; Peptides; Serine Endopeptidases; Substrate Specificity

1989
Comparison of ornithine metabolism in hyperornithinaemia-hyperammonaemia-homocitrullinuria syndrome, lysinuric protein intolerance and gyrate atrophy fibroblasts.
    Journal of inherited metabolic disease, 1989, Volume: 12, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Fibroblasts; Heterozygote; Homozygote; Humans; Lysine; Ornithine; Ornithine-Oxo-Acid Transaminase; Oxidation-Reduction; Proteins; Syndrome

1989
Biochemical and histologic pathology in an infant with cross-reacting material (negative) pyruvate carboxylase deficiency.
    Pediatric research, 1986, Volume: 20, Issue:3

    Topics: Acidosis; Amino Acids; Ammonia; Biopsy; Citrulline; Cross Reactions; Glutamine; Humans; Infant, Newborn; Lactates; Liver; Liver Function Tests; Lysine; Male; Pyruvate Carboxylase Deficiency Disease

1986
Channeling of extramitochondrial ornithine to matrix ornithine transcarbamylase.
    The Journal of biological chemistry, 1987, Jan-05, Volume: 262, Issue:1

    Topics: Amino Acid Transport Systems, Basic; Animals; Biological Transport; Carbamoyl-Phosphate Synthase (Ammonia); Carrier Proteins; Citrulline; Kinetics; Lysine; Male; Membrane Transport Proteins; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase; Rats; Rats, Inbred Strains; Urea

1987
Inhibitory effect of intravenous lysine infusion on urea cycle metabolism.
    European journal of pediatrics, 1987, Volume: 146, Issue:1

    Topics: Adolescent; Amino Acids; Ammonia; Child; Citric Acid Cycle; Citrulline; Depression, Chemical; Female; Humans; Infusions, Intravenous; Lysine; Male; Orotic Acid; Putrescine; Urea

1987
Ornithine transport and exchange in Streptococcus lactis.
    Journal of bacteriology, 1987, Volume: 169, Issue:9

    Topics: Amino Acids; Biological Transport; Chromatography, Thin Layer; Citrulline; Kinetics; Lactococcus lactis; Lysine; Ornithine

1987
Hyperornithinemia-hyperammonemia-homocitrullinuria syndrome: low creatine excretion and effect of citrulline, arginine, or ornithine supplement.
    Pediatric research, 1987, Volume: 22, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Child, Preschool; Citrulline; Creatine; Female; Humans; Lysine; Male; Ornithine; Orotic Acid; Syndrome

1987
Inhibition of bovine liver lysine-ketoglutarate reductase by urea cycle metabolites and saccharopine.
    Biochemistry international, 1987, Volume: 14, Issue:4

    Topics: Ammonia; Animals; Cattle; Citrulline; Humans; Lysine; Mitochondria, Liver; Oxidoreductases Acting on CH-NH Group Donors; Rats; Saccharopine Dehydrogenases; Species Specificity

1987
[A case of combined lysinuric protein intolerance and hypoactivity of argininosuccinate synthetase (citrullinemia)].
    Nihon Naika Gakkai zasshi. The Journal of the Japanese Society of Internal Medicine, 1988, Volume: 77, Issue:5

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Ammonium Chloride; Citrulline; Female; Humans; Lysine; Renal Tubular Transport, Inborn Errors

1988
[Protein intolerance with lysinuria. Value of orotic aciduria in adjusting treatment with citrulline].
    Archives francaises de pediatrie, 1988, Volume: 45, Issue:10

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Amino Acids; Amino Acids, Diamino; Ammonia; Biological Transport; Cell Membrane; Citrulline; Consanguinity; Dietary Proteins; Humans; Lysine; Male; Orotic Acid; Osteoporosis

1988
Lysinuric protein intolerance presenting as childhood osteoporosis. Clinical and skeletal response to citrulline therapy.
    The New England journal of medicine, 1985, Jan-31, Volume: 312, Issue:5

    Topics: Alanine; Amino Acid Metabolism, Inborn Errors; Arginine; Bone Development; Child, Preschool; Citrulline; Female; Humans; Lysine; Osteogenesis; Osteoporosis

1985
Interactions between amino acid transport systems in Neurospora crassa.
    Journal of bacteriology, 1972, Volume: 112, Issue:1

    Topics: Amino Acids; Arginine; Biological Transport, Active; Canavanine; Carbon Isotopes; Cell-Free System; Chromatography, Paper; Citrulline; Drug Resistance, Microbial; Genetics, Microbial; Lysine; Membrane Transport Proteins; Mutation; Neurospora; Neurospora crassa; Stereoisomerism; Tryptophan

1972
Acetylglutamate kinase: a feedback-sensitive enzyme of arginine biosynthesis in Neurospora.
    Biochemical and biophysical research communications, 1974, Sep-23, Volume: 60, Issue:2

    Topics: Arginine; Carbon Radioisotopes; Chromatography, Gel; Chromatography, Ion Exchange; Citrulline; Enzyme Activation; Feedback; Glutamates; Hydroxylamines; Kinetics; Lysine; Magnesium; Neurospora; Neurospora crassa; Ornithine; Phosphotransferases

1974
Letter: On a late developing urea cycle.
    Pediatric research, 1974, Volume: 8, Issue:10

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Citrulline; Humans; Ligases; Lysine; Ornithine Carbamoyltransferase; Succinates; Urea

1974
Letter: The high levels of lysine, homocitrulline, and homoarginine found in argininosuccinate synthetase deficiency.
    Pediatric research, 1974, Volume: 8, Issue:10

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Citrulline; Humans; Ligases; Lysine; Succinates

1974
Letter: The presence of the homoanalogues of substrates of the urea cycle in the presence of argininosuccinate synthetase deficiency.
    Pediatric research, 1974, Volume: 8, Issue:10

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Citrulline; Diet; Humans; Ligases; Lysine; Ornithine Carbamoyltransferase; Succinates

1974
[Free amino acids in the 24 h urine of healthy children (author's transl)].
    Monatsschrift fur Kinderheilkunde, 1974, Volume: 122, Issue:9

    Topics: Adolescent; Age Factors; Alanine; Amino Acids; Aminobutyrates; Carnosine; Child; Chromatography, Ion Exchange; Citrulline; Female; Glycine; Histidine; Humans; Isoleucine; Lysine; Male; Methionine; Ornithine; Phenylalanine; Serine; Sex Factors; Threonine; Tyrosine; Valine

1974
The absorption of protons with specific amino acids and carbohydrates by yeast.
    The Biochemical journal, 1973, Volume: 134, Issue:4

    Topics: Amino Acids; Arginine; Canavanine; Carbohydrate Metabolism; Carbon Radioisotopes; Citrulline; Glycine; Lactose; Lysine; Maltose; Methionine; Mutation; Proline; Protons; Saccharomyces; Saccharomyces cerevisiae; Sucrose

1973
Amino acid metabolism in chameleon liver.
    Comparative biochemistry and physiology. B, Comparative biochemistry, 1972, Jul-15, Volume: 42, Issue:3

    Topics: Alanine; Amino Acids; Animals; Arginine; Aspartic Acid; Carbon Isotopes; Citrulline; Female; Glutamates; Glutamine; Glycine; Histidine; Keto Acids; Liver; Lizards; Lysine; Male; Methionine; Ornithine; Phenylalanine; Pyruvates; Serine; Threonine; Tryptophan

1972
Effects of amino acids on the isolated chicken retina, and on its response to glutamate stimulation.
    Journal of neurochemistry, 1973, Volume: 20, Issue:4

    Topics: Amino Acids; Aminobutyrates; Animals; Arginine; Carbon Isotopes; Chickens; Chromatography, Paper; Citrulline; Cortical Spreading Depression; Glutamates; Glutarates; In Vitro Techniques; Isoleucine; Leucine; Lysine; Methionine; Ornithine; Perfusion; Phenylalanine; Retina; Sclera; Taurine; Tryptophan; Tyrosine

1973
Citrullinemia and an alternative urea cycle.
    Pediatric research, 1973, Volume: 7, Issue:8

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Citrulline; Humans; Infant; Lysine; Urea

1973
Molecular specificity of the L-arginine reabsorption mechanism. Microperfusion studies in the proximal tubule of rat kidney.
    Pflugers Archiv : European journal of physiology, 1973, Jun-04, Volume: 340, Issue:4

    Topics: Absorption; Aminobutyrates; Animals; Arginine; Canavanine; Citrulline; Guanidines; Homoserine; Kidney Tubules; Kidney Tubules, Proximal; Lysine; Ornithine; Perfusion; Propionates; Rats; Structure-Activity Relationship

1973
Amino acid metabolism in chameleon tissues.
    Comparative biochemistry and physiology. B, Comparative biochemistry, 1973, Oct-15, Volume: 46, Issue:2

    Topics: Alanine; Amino Acids; Animals; Arginine; Aspartic Acid; Brain; Citrulline; Glutamates; Glutamine; Glycine; Histidine; Ketoglutaric Acids; Kidney; Liver; Lysine; Muscles; Myocardium; Ornithine; Oxaloacetates; Proline; Pyruvates; Reptiles; Serine; Tryptophan

1973
Hyperlysinaemia. Harmless inborn error of metabolism?
    Archives of disease in childhood, 1973, Volume: 48, Issue:11

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Body Height; Carbon Isotopes; Child; Citrulline; Cystine; Fibroblasts; Humans; Ketone Oxidoreductases; Lysine; Male; Ornithine

1973
Enzyme studies in a patient with saccharopinuria: a defect of lysine metabolism.
    Pediatric research, 1974, Volume: 8, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Carbon Radioisotopes; Cells, Cultured; Chromatography, Paper; Citrulline; Electrophoresis; Enzyme Induction; Fibroblasts; Glutarates; Humans; In Vitro Techniques; Ketoglutaric Acids; Lysine; Mitochondria; Oxidoreductases; Skin

1974
Chemical modification of lysine residues in ovine luteinizing hormone. Effect on biological activity.
    Biochimica et biophysica acta, 1974, Mar-14, Volume: 342, Issue:1

    Topics: Alkylation; Animals; Arginine; Ascorbic Acid; Binding Sites; Biological Assay; Borohydrides; Carbamates; Chromatography, Gel; Citrulline; Cyanogen Bromide; Female; Formaldehyde; Guanidines; Luteinizing Hormone; Lysine; Methylation; Ovary; Oxidation-Reduction; Protein Binding; Protein Conformation; Sheep; Structure-Activity Relationship

1974
Ornithinemia, hyperammonemia, and homocitrullinuria. A disease associated with mental retardation and possibly caused by defective mitochondrial transport.
    American journal of diseases of children (1960), 1974, Volume: 127, Issue:5

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Dietary Proteins; Female; Humans; Intellectual Disability; Lysine; Mitochondria; Ornithine; Ornithine Carbamoyltransferase; Proline; Transaminases

1974
Hyperammonaemia in 20 families. Biochemical and genetical survey, including investigations in 3 new families.
    Archives of disease in childhood, 1974, Volume: 49, Issue:6

    Topics: Alanine; Ammonia; Arginine; Child, Preschool; Citrulline; Female; Genes, Dominant; Genetic Linkage; Glutamates; Glutamine; Glycine; Humans; Leucine; Liver; Lysine; Male; Metabolism, Inborn Errors; Ornithine; Ornithine Carbamoyltransferase; Sex Chromosomes

1974
Arginine transport and metabolism in osmotically shocked and unshocked cells of Escherichia coli W.
    The Journal of biological chemistry, 1969, May-25, Volume: 244, Issue:10

    Topics: Acetates; Arginine; Biological Transport; Canavanine; Carbon Isotopes; Carboxy-Lyases; Citrulline; Cold Temperature; Escherichia coli; Glutamates; Guanidines; Hydrochloric Acid; Leucine; Lysine; Ornithine; Osmolar Concentration; Proline; Tromethamine; Urea

1969
Plasma amino acid levels in diabetic ketoacidosis.
    Diabetes, 1970, Volume: 19, Issue:10

    Topics: Adolescent; Adult; Aged; Alanine; Amino Acids; Arginine; Butyrates; Child; Citrulline; Cystine; Diabetic Ketoacidosis; Female; Glycine; Histidine; Humans; Insulin; Isoleucine; Leucine; Lysine; Male; Methionine; Middle Aged; Ornithine; Phenylalanine; Proline; Serine; Threonine; Tyrosine; Valine

1970
The effect of short-term changes in the external salinity on the levels of the non-protein nitrogenous compounds and the ornithine-urea cycle enzymes in Rana cancrivora.
    Comparative biochemistry and physiology. B, Comparative biochemistry, 1972, Feb-15, Volume: 41, Issue:2

    Topics: Amino Acids; Animals; Anura; Arginase; Aspartic Acid; Carbamates; Choline; Citrulline; Female; Hypertonic Solutions; Ligases; Liver; Lysine; Male; Mannitol; Muscles; Ornithine Carbamoyltransferase; Phosphotransferases; Potassium; Ranidae; Sodium; Sucrose; Urea; Water-Electrolyte Balance

1972
Saccharopinuria.
    Archives of disease in childhood, 1972, Volume: 47, Issue:251

    Topics: Adipates; Amino Acid Metabolism, Inborn Errors; Amino Acids; Child, Preschool; Chromatography, Paper; Citrulline; Dipeptides; Female; Humans; Lysine; Muscle Spasticity

1972
Citrullinemia: a new case, with implications concerning adaptation to defective urea synthesis.
    Pediatric research, 1972, Volume: 6, Issue:7

    Topics: Adult; Amino Acids; Ammonia; Citrulline; Dietary Proteins; Fibroblasts; Humans; Intellectual Disability; Ligases; Lysine; Male; Metabolism, Inborn Errors; Urea

1972
Quantitative amino acids in amniotic fluid and maternal plasma in early and late pregnancy. Preliminary report.
    American journal of obstetrics and gynecology, 1971, Sep-15, Volume: 111, Issue:2

    Topics: Alanine; Amino Acids; Aminobutyrates; Amniotic Fluid; Arginine; Aspartic Acid; Citrulline; Cystine; Female; Gestational Age; Glutamates; Glycine; Histidine; Humans; Isoleucine; Leucine; Lysine; Methionine; Ornithine; Phenylalanine; Pregnancy; Proline; Serine; Threonine; Tyrosine; Valine

1971
On the specificity of tryptic catalysis.
    Biochemical and biophysical research communications, 1971, Aug-06, Volume: 44, Issue:3

    Topics: 1-Propanol; Acetates; Acylation; Arginine; Benzoates; Catalysis; Chemical Phenomena; Chemistry; Citrulline; Esters; Glycine; Kinetics; Lysine; Methanol; Models, Biological; Ornithine; Phenylalanine; Protein Binding; Sulfonic Acids; Thermodynamics; Toluene; Trypsin; Tyrosine

1971
The effect of vitamin C depletion on the free amino acid content in blood plasma of the guinea pig.
    International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition, 1971, Volume: 41, Issue:1

    Topics: Alanine; Amino Acids; Ammonia; Animals; Arginine; Ascorbic Acid Deficiency; Aspartic Acid; Citrulline; Cysteine; Glutamates; Glycine; Guinea Pigs; Histidine; Isoleucine; Lysine; Male; Methionine; Ornithine; Phenylalanine; Proline; Serine; Threonine; Time Factors; Tyrosine; Valine

1971
[Distribution of free amino acids in plasma in patients with a chronic lymphatic and acute leukemia].
    Wiener klinische Wochenschrift, 1971, Apr-09, Volume: 83, Issue:14

    Topics: Alanine; Amino Acids; Arginine; Aspartic Acid; Citrulline; Cystine; Glutamates; Glutamine; Glycine; Histidine; Humans; Isoleucine; Leucine; Leukemia, Lymphoid; Lysine; Methionine; Ornithine; Phenylalanine; Prednisolone; Proline; Serine; Threonine; Triethylenemelamine; Tyrosine; Valine; Vincristine

1971
Brucella organisms isolated from dogs: comparison of characteristics of members of the genus Brucella.
    American journal of veterinary research, 1969, Volume: 30, Issue:10

    Topics: Abortion, Veterinary; Alanine; Animals; Arabinose; Arginine; Asparagine; Brucella; Brucellosis; Citrulline; Culture Media; Dog Diseases; Dogs; Female; Galactose; Glutamates; Hematoma; Humans; Lysine; Ornithine; Pregnancy; Ribose; Xylose

1969
The participation of ornithine and citrulline in the regulation of arginine metabolism in Saccharomyces cerevisiae.
    European journal of biochemistry, 1970, Volume: 12, Issue:1

    Topics: Amino Acids; Arginine; Carbon Isotopes; Citrulline; Culture Media; Depression, Chemical; Enzyme Repression; Glutamates; Lysine; Models, Biological; Mutation; Ornithine; Ornithine Carbamoyltransferase; Quaternary Ammonium Compounds; Saccharomyces; Species Specificity; Time Factors

1970
Effects of modification of episilon-amino groups on the interaction of kappa- and alpha-S1-caseins.
    Biochimica et biophysica acta, 1970, May-26, Volume: 207, Issue:2

    Topics: Arginine; Calcium; Carbamates; Caseins; Chemical Phenomena; Chemistry; Citrulline; Formaldehyde; Lysine; Ultracentrifugation

1970
L-homoarginine; an inhibitor of serum "bone and liver" alkaline phosphatase.
    Clinica chimica acta; international journal of clinical chemistry, 1970, Volume: 29, Issue:2

    Topics: Alkaline Phosphatase; Arginine; Bone and Bones; Canavanine; Citrulline; Electrophoresis; Female; Guanidines; Humans; Isoenzymes; Liver; Lysine; Organ Specificity; Placenta; Pregnancy

1970
[Citrullinemia].
    Archives francaises de pediatrie, 1971, Volume: 28, Issue:5

    Topics: Alanine; Amino Acid Metabolism, Inborn Errors; Ammonia; Autopsy; Chromatography; Citrulline; Humans; Infant; Lysine; Male; Urea

1971
Arginine racemase of Pseudomonas graveolens. I. Purification, crystallization, and properties.
    The Journal of biological chemistry, 1971, Aug-25, Volume: 246, Issue:16

    Topics: Alcohols; Amides; Aminobutyrates; Arginine; Boron Compounds; Catalysis; Chemical Precipitation; Chromatography, DEAE-Cellulose; Chromatography, Gel; Chromatography, Ion Exchange; Citrulline; Crystallization; Drug Stability; Ethionine; Glutamates; Hot Temperature; Hydrogen-Ion Concentration; Hydroxylamines; Isomerases; Kinetics; Light; Lysine; Molecular Weight; Ornithine; Oxidation-Reduction; Penicillamine; Phenylhydrazines; Protein Binding; Pseudomonas; Pyridoxal Phosphate; Quaternary Ammonium Compounds; Rotation; Spectrophotometry; Sulfates; Ultracentrifugation

1971
Solic phase synthetic study of the active site region of staphylococcal nuclease-T'.
    The Journal of biological chemistry, 1971, Apr-10, Volume: 246, Issue:7

    Topics: Amides; Amino Acid Sequence; Arginine; Asparagine; Aspartic Acid; Binding Sites; Calcium; Chemical Phenomena; Chemistry; Chromatography, Paper; Citrulline; Deoxyribonucleases; Electrophoresis; Fluorescence; Glutamates; Lysine; Models, Structural; Peptides; Protein Binding; Ribonucleases; Spectrum Analysis; Staphylococcus; Trypsin

1971
Uptake of amino acids by mucosa of rat colon in vitro.
    European journal of biochemistry, 1968, Volume: 4, Issue:3

    Topics: Animals; Biological Transport; Carbon Isotopes; Citrulline; Colon; Cyanides; Depression, Chemical; Dinitrophenols; Glycine; Histidine; Intestinal Mucosa; Intestinal Secretions; Lysine; Male; Methionine; Rats; Serous Membrane; Valine

1968
Separation of basic amino acids by paper electrophoresis.
    Analytical biochemistry, 1968, Volume: 23, Issue:3

    Topics: Amino Acids; Arginine; Bicarbonates; Carbamates; Carbonates; Citrulline; Electrophoresis; Histidine; Hydrogen-Ion Concentration; Indicators and Reagents; Lysine; Methods; Paper; Quinolines; Temperature

1968
The interaction of trypsin with neutral substrates and modifiers.
    Biochemistry, 1968, Volume: 7, Issue:10

    Topics: Amino Acids; Arginine; Benzene Derivatives; Benzoates; Binding Sites; Chemical Phenomena; Chemistry; Citrulline; Esters; Guanidines; Hydrogen-Ion Concentration; Isoflurophate; Ketones; Kinetics; Lysine; Phenols; Quaternary Ammonium Compounds; Toluene; Trypsin; Urea

1968
Saccharopinuria: a new inborn error of lysine metabolism.
    Nature, 1968, May-18, Volume: 218, Issue:5142

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Animals; Chromatography, Ion Exchange; Chromatography, Paper; Citrulline; Female; Histidine; Humans; Lysine

1968
Effect of glucagon on concentration of several free amino acids in plasma.
    Metabolism: clinical and experimental, 1969, Volume: 18, Issue:4

    Topics: Alanine; Amino Acids; Arginine; Citrulline; Cystine; Depression, Chemical; Fasting; Female; Glucagon; Glycine; Histidine; Humans; Leucine; Liver; Lysine; Male; Methionine; Nitrogen; Phenylalanine; Progesterone; Proline; Serine; Threonine; Tyrosine; Valine

1969
Hyperornithinemia, hyperammonemia, and homocitrullinuria. A new disorder of amino acid metabolism associated with myoclonic seizures and mental retardation.
    American journal of diseases of children (1960), 1969, Volume: 117, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Ataxia; Child, Preschool; Citrulline; Diet Therapy; Humans; Intellectual Disability; Lysine; Male; Myoclonus; Ornithine; Ornithine Carbamoyltransferase; Seizures

1969
Phenotypic comparison of Brucella ovis to the DNA-homologous Brucella species.
    American journal of veterinary research, 1969, Volume: 30, Issue:10

    Topics: Alanine; Arabinose; Arginine; Asparagine; Brucella; Citrulline; Culture Media; DNA, Bacterial; Galactose; Glutamates; Lysine; Ornithine; Phenotype; Ribose; Xylose

1969
The absorption of dibasic amino-acids by rat intestinal slices.
    Biochemische Zeitschrift, 1965, Nov-05, Volume: 343, Issue:1

    Topics: Animals; Arginine; Biological Transport, Active; Buffers; Carbon Isotopes; Citrulline; Ethylmaleimide; Glucose; Intestinal Absorption; Intestinal Mucosa; Leucine; Lysine; Male; Methionine; Nitrophenols; Phlorhizin; Rats; Sodium

1965
Separation of basic amino acids. IV. Electrophoretic determination of L-arginine, L-citrulline, L-histidine, L-lysine, and L-ornithine.
    Analytical biochemistry, 1965, Volume: 13, Issue:3

    Topics: Arginine; Citrulline; Electrophoresis; Histidine; Lysine; Ornithine

1965
A case of hyperlysinemia: biochemical and clinical observations.
    Pediatrics, 1967, Volume: 39, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Autoanalysis; Child, Preschool; Chromatography, Paper; Citrulline; Humans; Intellectual Disability; Lysine; Male; Ornithine

1967
The effect of progesterone on the concentration of plasma amino acids in man.
    Metabolism: clinical and experimental, 1967, Volume: 16, Issue:12

    Topics: Acromegaly; Alanine; Amino Acids; Arginine; Citrulline; Cystine; Fasting; Glycine; Histidine; Humans; Isoleucine; Leucine; Liver; Lysine; Methionine; Ornithine; Phenylalanine; Progesterone; Proline; Proteins; Threonine; Tyrosine; Valine

1967
Paths of lysine degradation in patients with hyperlysinemia.
    Pediatrics, 1967, Volume: 40, Issue:6

    Topics: Arginine; Carbon Isotopes; Child; Child, Preschool; Chromatography, Paper; Citrulline; Female; Humans; Lysine

1967
Basolateral-membrane transport defect for lysine in lysinuric protein intolerance.
    Lancet (London, England), 1980, Jun-07, Volume: 1, Issue:8180

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Diamino; Biological Transport; Cell Membrane; Child; Child, Preschool; Citrulline; Female; Glycine; Humans; Infant; Intestinal Mucosa; Kidney; Liver; Lysine; Male

1980
Toxic effects of ornithine and its related compounds on the retina.
    Advances in experimental medicine and biology, 1982, Volume: 153

    Topics: Animals; Arginine; Citrulline; Glutamates; Glutamic Acid; Lysine; Ornithine; Pigment Epithelium of Eye; Proline; Putrescine; Rats; Rats, Inbred Strains; Retina

1982
Arginine uptake by isolated rat liver mitochondria.
    Biochimica et biophysica acta, 1984, Dec-20, Volume: 802, Issue:3

    Topics: Animals; Arginine; Citrulline; Glutamates; Glutamic Acid; Glutamine; Lysine; Male; Mitochondria, Heart; Mitochondria, Liver; Ornithine; Rats; Rats, Inbred Strains

1984
Oral administration of urea cycle intermediates in lysinuric protein intolerance: effect on plasma and urinary arginine and ornithine.
    Metabolism: clinical and experimental, 1983, Volume: 32, Issue:1

    Topics: Administration, Oral; Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Arginine; Child; Citrulline; Female; Humans; Intestinal Absorption; Lysine; Ornithine; Urea

1983
Oral administration of epsilon N-acetyllysine and homocitrulline in lysinuric protein intolerance.
    The Journal of pediatrics, 1983, Volume: 102, Issue:3

    Topics: Administration, Oral; Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Citrulline; Female; Humans; Lysine; Male

1983
"Basolateral" and mitochondrial membrane transport defect in the hepatocytes in lysinuric protein intolerance.
    Acta paediatrica Scandinavica, 1983, Volume: 72, Issue:1

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Arginine; Cell Membrane; Child; Citrulline; Female; Humans; Liver; Lysine; Male; Mitochondria, Liver; Ornithine

1983
The uptake of ornithine and lysine by rat liver mitochondria.
    Biochemical medicine, 1983, Volume: 30, Issue:3

    Topics: Animals; Arginine; Biological Transport; Citrulline; Female; In Vitro Techniques; Lysine; Mitochondria, Liver; Ornithine; Rats; Rats, Inbred Strains

1983
[Lysinuric protein intolerance].
    Monatsschrift Kinderheilkunde : Organ der Deutschen Gesellschaft fur Kinderheilkunde, 1983, Volume: 131, Issue:11

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Citrulline; Consanguinity; Dietary Proteins; Female; Ferritins; Humans; Infant; L-Lactate Dehydrogenase; Lysine; Ornithine; Turkey

1983
Further evidence for a separate enzymic entity for the synthesis of homocitrulline, distinct from the regular ornithine transcarbamylase.
    Enzyme, 1984, Volume: 32, Issue:1

    Topics: Animals; Citrulline; Female; Hydrogen-Ion Concentration; Kinetics; Lysine; Male; Mice; Mice, Mutant Strains; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase; Rats

1984
Enzyme inhibition as a possible cause of secondary increases in metabolite levels in patients with inborn errors of metabolism.
    Journal of inherited metabolic disease, 1980, Volume: 3, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonium Chloride; Ammonium Sulfate; Animals; Arginine; Argininosuccinate Lyase; Argininosuccinate Synthase; Argininosuccinic Acid; Cattle; Citrulline; Ligases; Liver; Lyases; Lysine; Rats; Swine

1980
Intestinal absorption in lysinuric protein intolerance: impaired for diamino acids, normal for citrulline.
    Gut, 1980, Volume: 21, Issue:6

    Topics: Adolescent; Adult; Amino Acids, Diamino; Citrulline; Female; Heterozygote; Homozygote; Humans; Infant; Intestinal Absorption; Lysine; Male; Renal Aminoacidurias

1980
Lysinuric protein intolerance: a two-year trial of dietary supplementation therapy with citrulline and lysine.
    The Journal of pediatrics, 1980, Volume: 97, Issue:6

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Arginine; Child; Child, Preschool; Citrulline; Complement C3; Female; Growth; Hemoglobins; Humans; Infant; Infant, Newborn; Lysine; Male; Serum Albumin

1980
Modification of poly-L-lysine by treatment with 1,1-ethylene-bis(1-nitrosourea) in vitro.
    Gan, 1981, Volume: 72, Issue:2

    Topics: Chemical Phenomena; Chemistry; Citrulline; Lysine; Nitrosourea Compounds; Polylysine

1981
A new transport interaction of dibasic amino acids and citrulline in human kidney.
    The Tohoku journal of experimental medicine, 1981, Volume: 134, Issue:1

    Topics: Amino Acids; Arginine; Biological Transport; Citrulline; Humans; Kidney; Lysine; Male; Ornithine

1981
Effect of ammonium chloride on homocitrulline and homoarginine synthesis from lysine.
    Journal of inherited metabolic disease, 1993, Volume: 16, Issue:5

    Topics: Adolescent; Ammonium Chloride; Child; Citrulline; Homoarginine; Humans; Lysine

1993
Kinetic characterization of the reconstituted ornithine carrier from rat liver mitochondria.
    Biochimica et biophysica acta, 1994, Dec-30, Volume: 1188, Issue:3

    Topics: Animals; Biological Transport; Carrier Proteins; Citrulline; Hydrogen-Ion Concentration; Kinetics; Liposomes; Lysine; Mitochondria, Liver; Ornithine; Rats

1994
Dietary arginine deficiency and gut ammonium infusion alter flux of urea cycle intermediates across the portal-drained viscera of pigs.
    The Journal of nutrition, 1995, Volume: 125, Issue:2

    Topics: Alanine; Animals; Arginine; Citrulline; Diet; Digestive System; Glutamic Acid; Glutamine; Lysine; Ornithine; Portal Vein; Quaternary Ammonium Compounds; Regional Blood Flow; Swine; Urea; Viscera

1995
Lysinuric protein intolerance. Urinary amino acid excretion at 2 and 9 days of age.
    Journal of inherited metabolic disease, 1994, Volume: 17, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Arginine; Citrulline; Humans; Infant, Newborn; Lysine; Male; Ornithine

1994
Cryptogenic hepatitis masking the diagnosis of ornithine transcarbamylase deficiency.
    Journal of pediatric gastroenterology and nutrition, 1996, Volume: 22, Issue:4

    Topics: Absorption; Ammonia; Arginine; Child, Preschool; Citrulline; Diagnosis, Differential; Dietary Proteins; Female; Glutamine; Hepatitis; Humans; Infant; Lysine; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Urea

1996
Biogenesis of Candida albicans Can1 permease expressed in Saccharomyces cerevisiae.
    FEBS letters, 1997, May-12, Volume: 408, Issue:1

    Topics: Amino Acid Transport Systems; Ammonia; Arginine; Blotting, Western; Candida albicans; Citrulline; Cycloheximide; Epitopes; Fungal Proteins; Gene Expression; Histidine; Lysine; Membrane Transport Proteins; Mutation; Plasmids; Proline; Proto-Oncogene Proteins c-myc; Recombinant Proteins; Saccharomyces cerevisiae; Transformation, Genetic

1997
On the unidirectionality of arginine uptake in the yeast Saccharomyces cerevisiae.
    FEMS microbiology letters, 1997, Jul-15, Volume: 152, Issue:2

    Topics: Amino Acid Transport Systems; Arginine; Biological Transport; Citrulline; Fungal Proteins; Genes, Fungal; Lysine; Membrane Transport Proteins; Saccharomyces cerevisiae

1997
[Mechanism of the transport of novel nitrosoalkylurea derivative, nitrulline, into tumor and normal cells].
    Biulleten' eksperimental'noi biologii i meditsiny, 1996, Volume: 122, Issue:12

    Topics: Animals; Antineoplastic Agents; Biological Transport, Active; Cells, Cultured; Citrulline; Diffusion; Intestine, Small; Leukemia P388; Lysine; Male; Mice; Nitrosourea Compounds; Tumor Cells, Cultured

1996
Influence of different classes of NO synthase inhibitors in the pig gastric fundus.
    Naunyn-Schmiedeberg's archives of pharmacology, 1997, Volume: 356, Issue:4

    Topics: Animals; Biotin; Citrulline; Electric Stimulation; Enzyme Inhibitors; Gastric Fundus; In Vitro Techniques; Isothiuronium; Lysine; Male; Muscle Contraction; Muscle, Smooth; NG-Nitroarginine Methyl Ester; Nitric Oxide Synthase; Nitroarginine; Ornithine; Swine; Thiourea

1997
L-arginine binding to liver arginase requires proton transfer to gateway residue His141 and coordination of the guanidinium group to the dimanganese(II,II) center.
    Biochemistry, 1998, Jun-09, Volume: 37, Issue:23

    Topics: Animals; Arginase; Arginine; Asparagine; Binding Sites; Borates; Citrulline; Electron Spin Resonance Spectroscopy; Guanidine; Histidine; Hydrogen-Ion Concentration; Isoleucine; Liver; Lysine; Manganese; Mutagenesis, Site-Directed; Ornithine; Protons; Rats; Substrate Specificity

1998
Interleukin 1beta increases arginine accumulation and activates the citrulline-NO cycle in rat pancreatic beta cells.
    Cytokine, 1999, Volume: 11, Issue:6

    Topics: Amino Acid Transport Systems; Amino Acids; Animals; Arginine; Biological Transport; Carrier Proteins; Cells, Cultured; Citrulline; Interleukin-1; Islets of Langerhans; Lysine; Male; Nitric Oxide; Nitric Oxide Synthase; Nitric Oxide Synthase Type II; Rats; Rats, Wistar; Reverse Transcriptase Polymerase Chain Reaction

1999
Nitric oxide synthase inhibition delays axonal degeneration and promotes the survival of axotomized retinal ganglion cells.
    Experimental neurology, 1999, Volume: 158, Issue:2

    Topics: Animals; Axons; Axotomy; Cell Survival; Citrulline; Dihydrolipoamide Dehydrogenase; Enzyme Inhibitors; Female; Gene Expression Regulation, Enzymologic; Injections; Lysine; Nerve Degeneration; NG-Nitroarginine Methyl Ester; Nitric Oxide Synthase; Nitric Oxide Synthase Type I; Nitric Oxide Synthase Type II; Nitroarginine; Optic Nerve; Rats; Rats, Sprague-Dawley; Retinal Ganglion Cells; Thiourea; Time Factors

1999
Cationic proteins inhibit L-arginine uptake in rat alveolar macrophages and tracheal epithelial cells. Implications for nitric oxide synthesis.
    American journal of respiratory cell and molecular biology, 1999, Volume: 21, Issue:2

    Topics: Animals; Arginase; Arginine; Blood Proteins; Citrulline; Dose-Response Relationship, Drug; Eosinophil Granule Proteins; Epithelial Cells; Female; Fibrinolytic Agents; Gene Expression; Heparin; Lipopolysaccharides; Lung; Lysine; Macrophages, Alveolar; Male; Nitric Oxide; Nitrites; Rats; Rats, Sprague-Dawley; Ribonucleases; Time Factors; Trachea

1999
Reduced nitric oxide production by L-arginine deficiency in lysinuric protein intolerance exacerbates intravascular coagulation.
    Metabolism: clinical and experimental, 1999, Volume: 48, Issue:9

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Antithrombin III; Arginine; Blood Coagulation Disorders; Citrulline; Cyclic GMP; Humans; Lysine; Male; Nitric Oxide; Nitroglycerin; Ornithine; Peptide Hydrolases; Platelet Aggregation; Thrombosis

1999
Peroxynitrite anion stimulates arginine release from cultured rat astrocytes.
    Journal of neurochemistry, 1999, Volume: 73, Issue:4

    Topics: Animals; Animals, Newborn; Arginine; Astrocytes; Cells, Cultured; Citrulline; Glutamic Acid; Hydrogen Peroxide; Kinetics; Lysine; Nitrates; Nitric Oxide Donors; Oxidants; Rats; Rats, Wistar; Serine

1999
Characterization of L-arginine transporters in rat renal inner medullary collecting duct.
    American journal of physiology. Regulatory, integrative and comparative physiology, 2000, Volume: 278, Issue:6

    Topics: Amino Acid Transport Systems; Animals; Arginine; beta-Alanine; Biological Transport; Carrier Proteins; Cations; Citrulline; Enzyme Inhibitors; Gene Expression; Homeostasis; Kidney Medulla; Kidney Tubules, Collecting; Lysine; Male; NG-Nitroarginine Methyl Ester; Nitric Oxide Synthase; omega-N-Methylarginine; Ornithine; Rats; Rats, Sprague-Dawley; RNA, Messenger; Substrate Specificity; Tritium; Water-Electrolyte Balance

2000
Polyarginine enters cells more efficiently than other polycationic homopolymers.
    The journal of peptide research : official journal of the American Peptide Society, 2000, Volume: 56, Issue:5

    Topics: Biological Transport; Biopolymers; Cell Membrane Permeability; Citrulline; Cytosol; Endocytosis; Flow Cytometry; gamma-Aminobutyric Acid; Histidine; Humans; Jurkat Cells; Lysine; Microscopy, Confocal; Molecular Weight; Ornithine; Peptides; Polyamines; Polyelectrolytes; Sodium Azide; Temperature

2000
Neuroprotective and neurorescuing effects of isoform-specific nitric oxide synthase inhibitors, nitric oxide scavenger, and antioxidant against beta-amyloid toxicity.
    British journal of pharmacology, 2001, Volume: 133, Issue:7

    Topics: Amyloid beta-Peptides; Animals; Antioxidants; Benzoates; Cell Survival; Cells, Cultured; Cerebral Cortex; Chromans; Citrulline; Dose-Response Relationship, Drug; Enzyme Inhibitors; Imidazoles; Isoenzymes; Lysine; Neuroprotective Agents; Nitrates; Nitric Oxide; Nitric Oxide Synthase; Nitroarginine; Oxidants; Peptide Fragments; Rats; Rats, Sprague-Dawley; Thiourea; Time Factors

2001
Augmented age-associated innate immune responses contribute to negative inotropic and lusitropic effects of lipopolysaccharide and interferon gamma.
    Journal of molecular and cellular cardiology, 2001, Volume: 33, Issue:10

    Topics: Adrenergic beta-Agonists; Age Factors; Aging; Animals; Arginine; Blotting, Western; Citrulline; Cyclic AMP; Cytokines; Dose-Response Relationship, Drug; Enzyme Inhibitors; Immunity; Interferon-gamma; Isoproterenol; Lipopolysaccharide Receptors; Lipopolysaccharides; Lysine; Nitric Oxide; Rats; Rats, Wistar; Sepsis; Signal Transduction; Up-Regulation

2001
Intrauterine growth retardation is associated with reduced activity and expression of the cationic amino acid transport systems y+/hCAT-1 and y+/hCAT-2B and lower activity of nitric oxide synthase in human umbilical vein endothelial cells.
    Circulation research, 2002, Jul-26, Volume: 91, Issue:2

    Topics: Amino Acid Transport Systems, Basic; Arginine; Biological Transport; Cationic Amino Acid Transporter 1; Cationic Amino Acid Transporter 2; Cells, Cultured; Citrulline; Endothelium, Vascular; Ethylmaleimide; Female; Fetal Growth Retardation; Gene Expression Regulation; Humans; Lysine; Membrane Potentials; Nitric Oxide Synthase; Nitric Oxide Synthase Type III; Pregnancy; RNA, Messenger; Umbilical Veins

2002
Computational docking of L-arginine and its structural analogues to C-terminal domain of Escherichia coli arginine repressor protein (ArgRc).
    Journal of molecular modeling, 2003, Volume: 9, Issue:2

    Topics: Arginine; Binding Sites; Canavanine; Citrulline; Computer Simulation; Crystallization; Escherichia coli Proteins; Homoarginine; Lysine; Models, Molecular; Molecular Structure; Protein Binding; Protein Conformation; Repressor Proteins

2003
Impairment of vascular endothelial nitric oxide synthase activity by advanced glycation end products.
    FASEB journal : official publication of the Federation of American Societies for Experimental Biology, 2003, Volume: 17, Issue:10

    Topics: Animals; Antibodies; Aorta; Arginine; Blood Pressure; Cells, Cultured; Citrulline; Diabetes Mellitus; Endothelium, Vascular; Enzyme Inhibitors; Female; Femoral Artery; Glycation End Products, Advanced; Humans; In Vitro Techniques; Lysine; Male; Models, Biological; NG-Nitroarginine Methyl Ester; Nitric Oxide; Nitric Oxide Synthase; Nitric Oxide Synthase Type III; Rabbits; Receptor for Advanced Glycation End Products; Receptors, Immunologic; Vasodilation

2003
The mitochondrial ornithine transporter. Bacterial expression, reconstitution, functional characterization, and tissue distribution of two human isoforms.
    The Journal of biological chemistry, 2003, Aug-29, Volume: 278, Issue:35

    Topics: Amino Acid Transport Systems, Basic; Arginine; Biological Transport; Carrier Proteins; Citrulline; DNA, Complementary; Electrophoresis, Polyacrylamide Gel; Humans; Hyperammonemia; Kinetics; Liposomes; Liver; Lysine; Malates; Membrane Transport Proteins; Mitochondria; Models, Biological; Mutation; Ornithine; Phosphates; Protein Folding; Protein Isoforms; Recombinant Proteins; Reverse Transcriptase Polymerase Chain Reaction; Substrate Specificity; Time Factors; Tissue Distribution; Transcription, Genetic

2003
Oral supplementation corrects plasma lysine concentrations in lysinuric protein intolerance.
    Metabolism: clinical and experimental, 2003, Volume: 52, Issue:7

    Topics: Absorption; Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Female; Humans; Intestinal Absorption; Kidney Tubules; Kinetics; Lysine; Male; Nitrogen; Ornithine; Reference Values; Urea

2003
Determination of ornithine, lysine, arginine, citrulline and histidine.
    Journal of chromatography, 1963, Volume: 10

    Topics: Amino Acids; Arginine; Chromatography; Citrulline; Histidine; Lysine; Ornithine

1963
HOMOCITRULLINE AND HOMOARGININE SYNTHESIS FROM LYSINE.
    Science (New York, N.Y.), 1964, May-29, Volume: 144, Issue:3622

    Topics: Adult; Amino Acids; Body Fluids; Carbon Isotopes; Carbon Radioisotopes; Chromatography; Citrulline; Homoarginine; Humans; Kidney; Liver; Lysine; Male; Proteins; Rats; Research; Urine

1964
THE SYNTHESIS OF 1-LYSINE, 1-ORNITHINE, 1-CITRULLINE, 1-GLUTAMIC ACID, AND 1-DESARGININE BRADYKININ.
    Journal of medicinal chemistry, 1963, Volume: 6

    Topics: Blood Pressure; Bradykinin; Bronchi; Chemistry, Pharmaceutical; Citrulline; Glutamates; Glutamic Acid; Guinea Pigs; Lysine; Ornithine; Peptides; Pharmacology; Research

1963
ENZYMIC SYNTHESIS OF EPSILON-N-ACETYL-L-LYSINE.
    Archives of biochemistry and biophysics, 1964, Volume: 108

    Topics: Amino Acids; Animals; Calcium; Calcium, Dietary; Carbon Isotopes; Cattle; Citrulline; Hydrogen-Ion Concentration; Kinetics; Liver; Lysine; Magnesium; Ornithine; Ornithine Carbamoyltransferase; Phosphates; Research; Spectrophotometry; Temperature; Transferases

1964
THE ASSIMILATION OF ARGININE AND LYSINE IN CANAVANINE RESISTANT AND SENSITIVE STRAINS OF NEUROSPORA CRASSA.
    Biochimica et biophysica acta, 1964, Nov-08, Volume: 93

    Topics: Amino Acids; Arginine; Biochemical Phenomena; Canavanine; Carbon Isotopes; Citrulline; Lysine; Neurospora; Neurospora crassa; Ornithine; Research; Serine

1964
PATHOGENESIS OF ACUTE INFLAMMATION. VI. INFLUENCE OF OSMOLARITY AND CERTAIN METABOLIC ANTAGONISTS UPON PHAGOCYTOSIS AND ADHESIVENESS BY LEUCOCYTES RECOVERED FROM MAN.
    Proceedings of the Society for Experimental Biology and Medicine. Society for Experimental Biology and Medicine (New York, N.Y.), 1965, Volume: 119

    Topics: Adhesiveness; Aminocaproates; Aminocaproic Acid; Citrulline; Dinitrophenols; Edetic Acid; Glycine; Hypertonic Solutions; Inflammation; Isoflurophate; Leukocytes; Lysine; Neutrophils; Ornithine; Osmolar Concentration; Pathology; Phagocytosis; Pharmacology; Pralidoxime Compounds; Quinidine; Research

1965
EFFECTS OF SOME AMINO ACIDS ON THE INHIBITION OF PLASMIN BY ANTIPLASMIN.
    Biochimica et biophysica acta, 1965, May-18, Volume: 99

    Topics: Amino Acids; Aminobutyrates; Aminocaproates; Aminocaproic Acid; Antifibrinolytic Agents; Arginine; Citrulline; Enzyme Inhibitors; Fatty Acids; Fibrinolysin; Kinetics; Lysine; Ornithine; Research

1965
Biochemical responses of healthy subjects during dietary supplementation with L-arginine.
    The Journal of nutritional biochemistry, 2004, Volume: 15, Issue:9

    Topics: Arginine; Biological Availability; Blood; Blood Glucose; Citrulline; Cyclic GMP; Dietary Supplements; Dose-Response Relationship, Drug; Female; Glycine; Humans; Insulin; Lysine; Male; Ornithine

2004
Screening of bitterness-suppressing agents for quinine: the use of molecularly imprinted polymers.
    Journal of pharmaceutical sciences, 2005, Volume: 94, Issue:2

    Topics: Arginine; Chromatography, High Pressure Liquid; Citrulline; Drug Evaluation, Preclinical; Drug Interactions; Humans; Lysine; Models, Biological; Models, Molecular; Ornithine; Quinine; Reference Standards; Sweetening Agents; Taste; Taste Threshold

2005
Increased NO production in lysinuric protein intolerance.
    Journal of inherited metabolic disease, 2005, Volume: 28, Issue:2

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Amino Acid Transport System y+L; Cells, Cultured; Child; Citrulline; Fibroblasts; Fusion Regulatory Protein 1, Light Chains; Humans; Lysine; Nitrates; Nitric Oxide; Nitric Oxide Synthase; Nitric Oxide Synthase Type II; Nitrites

2005
Relationships of Cysteine and Lysine residues with the substrate binding site of the mitochondrial ornithine/citrulline carrier: an inhibition kinetic approach combined with the analysis of the homology structural model.
    Biochimica et biophysica acta, 2005, Dec-10, Volume: 1718, Issue:1-2

    Topics: 4-Acetamido-4'-isothiocyanatostilbene-2,2'-disulfonic Acid; 4,4'-Diisothiocyanostilbene-2,2'-Disulfonic Acid; Amino Acid Transport Systems, Basic; Animals; Binding Sites; Biological Transport; Citrulline; Cysteine; Lysine; Mutation; Ornithine; Protein Conformation; Pyridoxal Phosphate; Rats; Structural Homology, Protein; Sulfhydryl Reagents

2005
[Histone demethylation isn't what it used to be].
    Medecine sciences : M/S, 2006, Volume: 22, Issue:4

    Topics: Arginine; Citrulline; Dioxygenases; F-Box Proteins; Gene Expression Regulation; Histone Demethylases; Histone Methyltransferases; Histone-Lysine N-Methyltransferase; Histones; Humans; Hydrolases; Jumonji Domain-Containing Histone Demethylases; Lysine; Methylation; Oxidoreductases, N-Demethylating; Protein Methyltransferases; Protein Processing, Post-Translational; Protein-Arginine Deiminase Type 4; Protein-Arginine Deiminases

2006
Substrate-assisted cysteine deprotonation in the mechanism of dimethylargininase (DDAH) from Pseudomonas aeruginosa.
    Biochemistry, 2006, May-02, Volume: 45, Issue:17

    Topics: Amidohydrolases; Binding Sites; Citrulline; Cobalt; Cysteine; Hydrogen-Ion Concentration; Iodoacetamide; Kinetics; Lysine; Mass Spectrometry; Models, Chemical; omega-N-Methylarginine; Protons; Pseudomonas aeruginosa; Spectrophotometry, Ultraviolet; Spectrum Analysis; Thiourea; X-Rays; Zinc

2006
Characterization of cationic amino acid transport systems in rat erythrocytes: lack of effect of uraemia on L-arginine influx.
    Clinical and experimental pharmacology & physiology, 2006, Volume: 33, Issue:8

    Topics: Amino Acid Transport System y+; Amino Acid Transport System y+L; Animals; Arginine; Citrulline; Disease Models, Animal; Erythrocytes; Kinetics; Leucine; Lysine; Male; Nephrectomy; Ornithine; Rats; Rats, Wistar; Uremia

2006
Long-term oral lysine supplementation in lysinuric protein intolerance.
    Metabolism: clinical and experimental, 2007, Volume: 56, Issue:2

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Calcium; Child; Child, Preschool; Chromatography, Ion Exchange; Citrulline; Dietary Supplements; Female; Finland; Humans; Long-Term Care; Lysine; Male; Middle Aged; Phosphates

2007
Nephropathy advancing to end-stage renal disease: a novel complication of lysinuric protein intolerance.
    The Journal of pediatrics, 2007, Volume: 150, Issue:6

    Topics: Adolescent; Adult; Amino Acid Transport Disorders, Inborn; Child; Child, Preschool; Citrulline; Creatinine; Cystatin C; Cystatins; Disease Progression; Female; Glomerular Filtration Rate; Humans; Infant; Kidney Diseases; Kidney Failure, Chronic; Kidney Transplantation; Lysine; Male; Middle Aged; Proteinuria

2007
Post-translational modifications in the rat lumbar spinal cord in experimental autoimmune encephalomyelitis.
    Journal of proteome research, 2007, Volume: 6, Issue:7

    Topics: Amino Acid Sequence; Animals; Arginine; Astrocytes; Citrulline; Encephalomyelitis, Autoimmune, Experimental; Glial Fibrillary Acidic Protein; Lumbar Vertebrae; Lysine; Methylation; Molecular Sequence Data; Multiple Sclerosis; Phosphorylation; Protein Processing, Post-Translational; Proteomics; Rats; Serine; Spinal Cord

2007
Nutrient intake in lysinuric protein intolerance.
    Journal of inherited metabolic disease, 2007, Volume: 30, Issue:5

    Topics: Adolescent; Adult; Aged; Amino Acid Metabolism, Inborn Errors; Child; Child, Preschool; Citrulline; Diet, Protein-Restricted; Dietary Supplements; Energy Intake; Female; Finland; Humans; Infant; Lysine; Male; Malnutrition; Middle Aged; Nutrition Assessment; Nutrition Policy; Nutritional Status; Phenylbutyrates; Sodium Benzoate

2007
'Multipurpose oxidase' in atherogenesis.
    Nature medicine, 2007, Volume: 13, Issue:10

    Topics: Animals; Apoptosis; Atherosclerosis; Carbamates; Cardiovascular Diseases; Cell Proliferation; Citrulline; Endothelial Cells; Humans; Inflammation; Lipoproteins, HDL; Lipoproteins, LDL; Lysine; Macrophages; Mice; Models, Biological; Muscle, Smooth; Oxidation-Reduction; Peroxidase; Scavenger Receptors, Class A; Smoking; Substrate Specificity; Thiocyanates

2007
Targeted metabolomic evaluation of arginine methylation and cardiovascular risks: potential mechanisms beyond nitric oxide synthase inhibition.
    Arteriosclerosis, thrombosis, and vascular biology, 2009, Volume: 29, Issue:9

    Topics: Aged; Arginine; Biomarkers; C-Reactive Protein; Cardiovascular Diseases; Chromatography, High Pressure Liquid; Citrulline; Coronary Artery Disease; Creatinine; Female; Humans; Lysine; Male; Metabolomics; Methylation; Middle Aged; Nitric Oxide Synthase; Odds Ratio; omega-N-Methylarginine; Ornithine; Prognosis; Prospective Studies; Protein Processing, Post-Translational; Risk Assessment; Risk Factors; Spectrometry, Mass, Electrospray Ionization; Tandem Mass Spectrometry; Time Factors

2009
Coordination of PAD4 and HDAC2 in the regulation of p53-target gene expression.
    Oncogene, 2010, May-27, Volume: 29, Issue:21

    Topics: Arginine; Cell Line, Tumor; Citrulline; Enzyme Inhibitors; Gene Expression Regulation, Neoplastic; Genes, p53; Histone Deacetylase 2; Histones; Humans; Hydrolases; Lysine; Protein-Arginine Deiminase Type 4; Protein-Arginine Deiminases; Tumor Suppressor Protein p53

2010
Early-onset hepatic fibrosis in lysinuric protein intolerance.
    Journal of pediatric gastroenterology and nutrition, 2011, Volume: 53, Issue:6

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acid Transport System y+L; Child, Preschool; Citrulline; Fusion Regulatory Protein 1, Light Chains; Humans; Liver; Liver Cirrhosis; Lysine; Male; Mutation; Treatment Outcome

2011
Simultaneous measurement of protein-bound 3-chlorotyrosine and homocitrulline by LC-MS/MS after hydrolysis assisted by microwave: application to the study of myeloperoxidase activity during hemodialysis.
    Talanta, 2012, Sep-15, Volume: 99

    Topics: Aged; Aged, 80 and over; Animals; Blood Chemical Analysis; Blood Proteins; Chromatography, Liquid; Citrulline; Female; Humans; Hydrolysis; Lysine; Male; Microwaves; Middle Aged; Peroxidase; Renal Dialysis; Tandem Mass Spectrometry; Time Factors; Tyrosine

2012
Specific analogues uncouple transport, signalling, oligo-ubiquitination and endocytosis in the yeast Gap1 amino acid transceptor.
    Molecular microbiology, 2014, Volume: 93, Issue:2

    Topics: Amino Acid Sequence; Amino Acid Transport Systems; Amino Acids; beta-Alanine; Binding Sites; Biological Transport; Citrulline; Endocytosis; Histidine; Lysine; Saccharomyces cerevisiae; Saccharomyces cerevisiae Proteins; Signal Transduction; Tryptophan; Ubiquitination

2014
Carbamylation of immunoglobulin abrogates activation of the classical complement pathway.
    European journal of immunology, 2014, Volume: 44, Issue:11

    Topics: Adhesins, Bacterial; Antibodies, Monoclonal, Murine-Derived; Antibody-Dependent Cell Cytotoxicity; Arthritis, Rheumatoid; Citrulline; Complement Activation; Complement C1q; Complement Pathway, Classical; Cyanates; Cysteine Endopeptidases; Gingipain Cysteine Endopeptidases; Humans; Immunoglobulin G; Immunologic Factors; Inflammation; Lysine; Mass Spectrometry; Protein Binding; Protein Processing, Post-Translational; Rituximab

2014
Homocitrullination Is a Novel Histone H1 Epigenetic Mark Dependent on Aryl Hydrocarbon Receptor Recruitment of Carbamoyl Phosphate Synthase 1.
    The Journal of biological chemistry, 2015, Nov-13, Volume: 290, Issue:46

    Topics: Animals; Base Sequence; Basic Helix-Loop-Helix Transcription Factors; Carbamoyl-Phosphate Synthase (Ammonia); Cells, Cultured; Chromatin; Citrulline; Epigenesis, Genetic; Female; Histones; Hydrolases; Lysine; Mice; Mice, Inbred C57BL; Nuclear Proteins; Polychlorinated Dibenzodioxins; Protein Binding; Protein Processing, Post-Translational; Protein Structure, Tertiary; Protein-Arginine Deiminases; Receptors, Aryl Hydrocarbon; Response Elements; Transcriptional Activation

2015
Antimodified protein antibody response pattern influences the risk for disease relapse in patients with rheumatoid arthritis tapering disease modifying antirheumatic drugs.
    Annals of the rheumatic diseases, 2017, Volume: 76, Issue:2

    Topics: Acetates; Acetylation; Antirheumatic Agents; Arthritis, Rheumatoid; Autoantibodies; Carbamates; Citrulline; Humans; Logistic Models; Lysine; Multivariate Analysis; Ornithine; Peptides; Peptides, Cyclic; Prognosis; Randomized Controlled Trials as Topic; Recurrence; Vimentin

2017
A propeptide-independent protease from Tannerella sp.6_1_58FAA_CT1 displays trypsin-like specificity.
    Journal of basic microbiology, 2017, Volume: 57, Issue:1

    Topics: Adhesins, Bacterial; Animals; Arginine; Bacteroidetes; Binding Sites; Cattle; Citrulline; Cysteine Endopeptidases; Cysteine Proteases; Gingipain Cysteine Endopeptidases; Kinetics; Lysine; Models, Molecular; Recombinant Proteins; Substrate Specificity; Swine; Tannerella forsythia; Trypsin

2017
Identification of urinary metabolites with potential blood pressure-lowering effects in lentil-fed spontaneously hypertensive rats.
    European journal of nutrition, 2018, Volume: 57, Issue:1

    Topics: Animals; Antihypertensive Agents; Blood Pressure; Citrulline; Diet; Hypertension; Lens Plant; Lysine; Male; Metabolomics; Pyridoxamine; Rats; Rats, Inbred SHR; Seeds

2018
[Clinical features of children with lysinuric protein intolerance and SLC7A7 gene mutation: an analysis of 3 cases].
    Zhongguo dang dai er ke za zhi = Chinese journal of contemporary pediatrics, 2019, Volume: 21, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acid Transport System y+L; Child; Citrulline; Fusion Regulatory Protein 1, Light Chains; Humans; Lysine; Mutation

2019
Asymmetric dimethylation and citrullination of proteinic arginine and homoarginine synthesis in human Helicobacter pylori infection.
    Amino acids, 2019, Volume: 51, Issue:6

    Topics: Adult; Aged; Aged, 80 and over; Arginine; Citrullination; Citrulline; Female; Gas Chromatography-Mass Spectrometry; Helicobacter Infections; Helicobacter pylori; Homoarginine; Humans; Lysine; Male; Methylation; Middle Aged; Nitric Oxide; Ornithine

2019
Establishment of reference values for the lysine acetylation marker N
    Amino acids, 2019, Volume: 51, Issue:9

    Topics: Adolescent; Adult; Arginine; Biomarkers; Cardiovascular Diseases; Carnitine; Chromatography, Liquid; Citrulline; Creatinine; Female; Homoarginine; Humans; Lysine; Male; Middle Aged; Ornithine; Reference Values; Renal Insufficiency, Chronic; Tandem Mass Spectrometry; Young Adult

2019
Homocitrullination of lysine residues mediated by myeloid-derived suppressor cells in the tumor environment is a target for cancer immunotherapy.
    Journal for immunotherapy of cancer, 2021, Volume: 9, Issue:7

    Topics: Animals; Cell Line, Tumor; Citrulline; Humans; Immunotherapy; Lysine; Mice; Myeloid-Derived Suppressor Cells; Tumor Microenvironment

2021
Metabolomic Analysis of Microcystis aeruginosa After Exposure to the Algicide L-Lysine.
    Bulletin of environmental contamination and toxicology, 2022, Dec-13, Volume: 110, Issue:1

    Topics: Ammonia; Arginine; Citrulline; Cyanobacteria; Ecosystem; Herbicides; Humans; Lysine; Microcystins; Microcystis; Ornithine

2022
Metabolomics profiling of seminal plasma in obesity-induced asthenozoospermia.
    Andrology, 2023, Volume: 11, Issue:7

    Topics: Aconitic Acid; Alanine; Asthenozoospermia; Citrulline; Glucose; Glutamic Acid; Glycine; Humans; Leucine; Lysine; Male; Metabolomics; Phenylalanine; Proline; Semen; Serine; Succinic Acid; Threonine; Tyrosine; Valine

2023