citrulline has been researched along with ammonium hydroxide in 319 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 186 (58.31) | 18.7374 |
| 1990's | 70 (21.94) | 18.2507 |
| 2000's | 33 (10.34) | 29.6817 |
| 2010's | 22 (6.90) | 24.3611 |
| 2020's | 8 (2.51) | 2.80 |
| Authors | Studies |
|---|---|
| Derr, RF; Zieve, L | 1 |
| Townsend, R | 1 |
| Meijer, AJ; van Woerkom, GM | 1 |
| Allen, MM; Chee, HL; Weathers, PJ | 1 |
| Chase, HP; Glasgow, AM | 1 |
| Gatfield, PD; Haust, MD; Taller, E; Wolfe, DM | 1 |
| Gatfield, PD; Haust, MD | 1 |
| Chien, WS; Lockau, W; Meeks, JC; Schilling, N; Shaffer, PW; Wolk, CP | 1 |
| Hensgens, HE; Meijer, AJ | 1 |
| Bryła, J; Niedźwiecka, A | 1 |
| Freedland, RA; Story, DL; Triebwasser, KC | 1 |
| Akaboshi, I; Arashima, S; Imanishi, Y; Matsuda, I; Nagata, N; Shinozuka, S; Yamamoto, J | 1 |
| Ha, YH; Milner, JA | 1 |
| Fell, V; Pollitt, RJ | 1 |
| Camargo, EP; Yoshida, N | 1 |
| Katsunuma, T; Ohkubo, T; Saheki, T | 1 |
| Gatfield, PD; Gordon, BA; Taller, E | 1 |
| Freedland, RA; Triebwasser, KC | 1 |
| Nakao, T; Oyanagi, K; Sogawa, H | 1 |
| Brusso, T; Spate, M; Whelan, DT | 1 |
| Shih, VE | 3 |
| Briggs, S; Freedland, RA | 1 |
| Noda, K | 1 |
| Milner, JA; Visek, WJ | 1 |
| Deleeuw, GA; Gimpel, JA; Meijer, AJ; Tager, JM; Williamson, JR | 1 |
| Awrich, AE; Cantrell, JE; Patterson, JH; Rudman, D; Stackhouse, WJ | 1 |
| Anakura, M; Arashima, S; Matsuda, I; Oka, Y; Saito, Y | 1 |
| Goto, I; Kobayashi, T; Shigeto, H; Yamada, T | 1 |
| Shiro, Y; Yabuki, S | 1 |
| Ban, S; Ishii, A; Ohkoshi, N; Oka, Y; Takahashi, A | 1 |
| Boal, TR; Cardillo, TS; Lichtman, MA; Murant, FG; Segel, GB; Sherman, F | 1 |
| Shimizu, H | 1 |
| Arbour, JF; Dubé, J; Flessas, J; Laberge, M; Lafleur, L; Lambert, MA; Lemay, JF; Mitchell, GA; Valle, D; Vanasse, M | 1 |
| Laframboise, R; Mandell, R; Pichette, J; Shih, VE | 1 |
| Russell, WC; Smith, DG; Thirkell, D | 1 |
| Brochu, P; Jasmin, G; Lambert, MA; Qureshi, IA; Seidman, EG; Smith, L | 1 |
| Hatase, O; Hosokawa, K; Itano, T; Janjua, NA; Kugoh, T; Matsui, H; Tokuda, M | 1 |
| Geiger, R; Maurer, H; Murr, C; Sailer, M; Schmoigl, C; Sperl, W; Steichen-Gersdorf, E | 1 |
| Chung, HJ; Clancy, RR | 1 |
| Hommes, FA; Koch, R; Pandya, AL; Williams, JC | 1 |
| Kaneko, K; Miyatake, T; Ohno, T; Yanagisawa, K; Yuki, N | 1 |
| Azuma, T; Higa, S; Kishimoto, S; Sakoda, S; Suzuki, T; Tsujino, S | 1 |
| Ichiki, H; Kobayashi, K; Nukada, O; Saheki, T; Ubuka, S; Uchiyama, C; Yoda, T | 1 |
| Shindo, K; Shiozawa, Z; Tsunoda, S | 1 |
| Bellet, H; Callis, A; Magnan de Bornier, B; Saumade, R; Serrano, JJ | 1 |
| Batshaw, ML; Berry, GT | 1 |
| Knopman, DS; Shih, VE; Tuchman, M | 1 |
| Brusilow, SW; Elliott, GR; Johnston, K; Rubenstein, JL | 1 |
| Eto, Y; Maekawa, K; Shimizu, H | 1 |
| Gale, DS; Iafolla, AK; Roe, CR | 1 |
| Nagata, S; Senshu, T | 1 |
| Hibbs, JB; Taintor, RR; Vavrin, Z | 1 |
| Botschner, J; Scriver, CR; Simell, O; Smith, DW | 1 |
| Alonso, E; García-España, A; Girbés, J; Rubio, V | 1 |
| Ambani, LM; Apte, BN; Balsekar, MV; Bhatia, RS; Shah, SB | 1 |
| Bartmann, P; Gortner, L; Leupold, D; Pohlandt, F | 1 |
| Bachmann, C; Baerlocher, K; Hochreutener, H; Issakainen, J | 1 |
| Azorín, I; Felipo, V; Grisolía, S; Miñana, MD | 1 |
| Coleman, AE; Cooper, AJ; Filc-DeRicco, S; Gelbard, AS; Nieves, E | 1 |
| Buttrose, M; McKellar, D; Welbourne, TC | 1 |
| Bonnefont, JP; Chadefaux, B; Kamoun, P; Rabier, D; Saudubray, JM; Shih, VE | 1 |
| Applegarth, DA; Davidson, AG; Dimmick, JE; Norman, MG; Pirie, G; Toone, JR; Wong, J; Wong, LT | 1 |
| Zieve, L | 1 |
| Alme, A; Broch, H; Gjessing, LR; Lie, SO; Lunde, HA; Undrum, T | 1 |
| Shibata, K; Watanabe, T | 1 |
| Alvarez, L; Coude, FX; Fabregas, I; Fernandez Alvarez, E; Grimber, G; Pineda, M; Ribes, A; Rodes, M | 1 |
| Kato, T; Mizutani, N; Sano, M | 1 |
| Bachmann, C; Colombo, JP; Dionisi Vici, C; Gambarara, M; Sabetta, G | 1 |
| Coskun, T; Kneer, J; Mönch, S; Ozalp, I | 1 |
| Bachmann, C; Grossschädl, F; Roscher, A; Stöckler, S | 1 |
| Girgis, N; Herrin, J; McGravey, V; Shah, BL; Shih, VE | 1 |
| Inoue, I; Kayanuma, K; Koike, R; Koura, M; Miyatake, T; Nakajima, M; Saheki, T; Takeshita, K; Uono, M; Yuasa, T | 1 |
| Ameen, M; Oberholzer, VG; Palmer, T | 1 |
| Kurihara, T; Matsukura, S; Shioya, K; Yamamura, Y | 1 |
| Aida, M; Matsoo, M; Matsuo, T; Nakamura, H; Takemine, H | 1 |
| de Parscau, L; Divry, P; Guibaud, P; Hermier, M; Vianey-Liaud, C | 1 |
| Soeters, PB; van Berlo, CL; van Leeuwen, PA | 1 |
| Oyanagi, K | 1 |
| Inoue, I; Kobayashi, K; Saheki, T | 1 |
| Inoue, I; Kayanuma, K; Koike, R; Miyatake, T; Nakajima, M; Saheki, T; Sakoda, K; Takeshita, K; Uono, M; Yuasa, T | 1 |
| Anttila, S; Manninen, A; Savolainen, H | 1 |
| Hashiba, M; Noguchi, R; Shimoji, K; Tomita, Y | 1 |
| Batshaw, ML; Coyle, JT; Hyman, SL; Mellits, ED; Quaskey, S; Qureshi, IA; Robinson, MB | 1 |
| Akiyoshi, H; Ichihara, K; Inoue, I; Ishii, S; Mito, T; Nakajima, M; Saheki, T; Takakura, H; Takashima, S; Takeshita, K | 1 |
| Hasegawa, T; Iwashima, A; Wakabayashi, Y; Yamada, RH | 1 |
| Gordon, BA; Haust, MD | 2 |
| Fujimori, K; Koike, R; Miyatake, T; Yuasa, T | 1 |
| Gatfield, DP; Gordon, BA; Haust, MD | 1 |
| Fujimori, K; Inoue, I; Koike, R; Miyatake, T; Saheki, T; Yuasa, T | 1 |
| Akamatsu, K; Kimura, H; Murase, M; Ochi, M; Ohta, Y; Okubo, H; Onji, M; Shoda, T; Takeuchi, N | 1 |
| Biscoping, J; Hempelmann, G; Michaelis, G | 1 |
| Anderson, PM | 1 |
| Dyken, PR; Hartlage, PL; Hommes, FA; Metoki, K; Roesel, RA | 1 |
| Rogers, QR; Visek, WJ | 1 |
| Buist, NR; Engel, RC | 1 |
| Cheung, CW; Cohen, NS; Kyan, FS; Kyan, SS; Raijman, L | 1 |
| Meijer, AJ | 1 |
| Clow, CL; Mackenzie, S; Scriver, CR; Simell, O | 1 |
| Charles, R | 1 |
| Hsia, YE | 1 |
| Brenton, DP; Cusworth, DC; Hartley, S; Kuzemko, JA; Lumley, S | 1 |
| Bryla, J | 1 |
| Asafov, GB; Ekisenina, NI; Ivanova, LM; Lumel'skiĭ, VIa; Smagin, VG | 1 |
| Schwarz, E | 1 |
| Cohen, PP; Reddy, MK; Wixom, RL | 1 |
| Causa, P; Perri, GC | 1 |
| Nordmann, J; Nordmann, R; Petit, MA | 1 |
| Gamble, JG; Lehninger, AL | 1 |
| Pollitt, R; Wright, T | 1 |
| Horne, FR | 1 |
| Cedrola, G; Guazzi, GC; Ragonese, G; Striano, S; Tancredi, F | 1 |
| Cohen, HP; Lin, S | 1 |
| Bradford, NM; Chappell, JB; Crompton, M; McGivan, JD | 1 |
| Bryla, J; Kubica, A; Zaleski, J | 1 |
| Bachmann, C; Baumgartner, R; Brechbühler, T; Colombo, JP; Mihatsch, MJ; Ohnacker, H; Wick, H; Wiesmann, U | 1 |
| Bergman, EN; Kaufman, CF; Williams, HH; Wolff, JE | 1 |
| Fell, V; Pollitt, RJ; Sampson, GA; Wright, T | 1 |
| Buist, NR; Hepburn, CA; Kennaway, NG; Ramberg, DA; Strandholm, JJ | 1 |
| Burgess, EA; Butler, LJ; Levin, B; Oberholzer, VG; Palmer, T | 1 |
| Danks, DM; Tippett, P; Zentner, G | 1 |
| Menne, F | 1 |
| Colombo, JP | 1 |
| Levin, B | 1 |
| Hager, SE; Jones, ME | 2 |
| O'Reilly, S | 1 |
| Barrio, A; Carlisky, NJ | 1 |
| Higgins, JV; Kohrman, AF; Scott-Emuakpor, A | 1 |
| Gerok, W; Haag, G; Holldorf, AW | 1 |
| Hornig, D; Weber, F; Wiss, O | 1 |
| Dietz, RW; Flipse, RJ | 1 |
| Schulman, JD; Shih, VE | 1 |
| Ballan, P; Beylot, J; Broustet, A; Ferrer, J; Moretti, G; Roques, JC; Staeffen, J | 1 |
| Mille, T; Pastorino, G | 1 |
| DeHackbeil, KF; Lis, AW; Lis, EW | 1 |
| Buniatian, HCh; Egian, VB; Hagopian, GE; Turshian, GA | 1 |
| Ito, K; Nakanishi, S; Tatibana, M; Terada, M | 1 |
| Badonnel, Y; Dautrevaux, M; Gelot, S; Levin, B; Neimann, N; Paysant, P; Pierson, M; Vidailhet, M | 1 |
| Miller, DL; Rodwell, VW | 1 |
| Kloss, G; Schwarz, E | 1 |
| Konttinen, A | 2 |
| Berger, R; Broyer, M | 1 |
| Charbonneau, R; Roberge, A | 2 |
| Read, LJ | 1 |
| Nordmann, R | 1 |
| Charles, R; De Haan, EJ; Hoek, JB; Tager, JM | 1 |
| Efron, ML; Moser, HW; Shih, VE | 1 |
| Mitsutsuka, K; Miyakoshi, T; Takahashi, T; Wada, T | 1 |
| Dolan, TF; Nelligan, DJ; Shih, VE; Solitare, GB | 1 |
| McMurray, WC; Mohyuddin, F; Rathbun, JC | 1 |
| Morrow, G | 1 |
| Brown, H; Diamond, R; Efron, ML; Moser, HW; Neumann, CG | 1 |
| Hirasawa, T; Saheki, T; Yajima, Y | 2 |
| Gray, RG; Hill, SE; Pollitt, RJ | 2 |
| Zollner, H | 1 |
| Anderson, PM; Casey, CA | 1 |
| Itakura, Y; Nakao, T; Oyanagi, K; Sakamoto, S; Sogawa, H; Tsuchiyama, A; Wagatsuma, K; Yachi, A | 1 |
| Hommes, FA; Metoki, K | 1 |
| Bennett, MJ; Dear, PR; Gray, RG; McGinlay, JM | 1 |
| Dyken, P; Hommes, FA; Kelloes, C; Metoki, K; Trefz, J | 1 |
| Cerra, FB; Goodman, MW; Konstantinides, FN; Zieve, L | 1 |
| Bachmann, C | 1 |
| Hayasaka, S; Nomura, H; Ohmura, M; Takase, S; Yabata, K | 1 |
| Batshaw, ML | 1 |
| Harada, T; Hisauchi, T; Kawano, M; Maehara, M; Ohrui, M; Sugaya, H; Sugita, T | 1 |
| Ali, R; Ansari, AS | 1 |
| Blankenship, PR; Coryell, ME; Hommes, FA; Roesel, RA | 1 |
| Nakajima, H; Ogura, N; Ohtake, A; Takayanagi, M | 1 |
| Baker, DH; Czarnecki, GL | 1 |
| Carter, AL; Eller, AG; Evans, BA; Hommes, FA | 1 |
| Meijer, AJ; Van Roermund, CW; Wanders, RJ | 1 |
| Herzfeld, A; Mandell, R; Shih, VE | 2 |
| Charpentier, C; Coude, FX; Marsac, C; Munnich, A; Ogier, H; Saudubray, JM | 1 |
| Cathelineau, L; Coudé, FX; Grimber, G; Kamoun, P; Parvy, P; Rabier, D | 1 |
| Glasgow, AM | 1 |
| Cerdan, S; Corkey, BE; Martin-Requero, A; Parrilla, RL; Walajtys-Rode, E; Williamson, JR | 1 |
| Cohen, PP | 1 |
| DeLong, GR; Glick, TH | 2 |
| Akerboom, TP; Groen, AK; Meijer, AJ; Tager, JM; van der Meer, R; Wanders, RJ | 1 |
| Batshaw, ML; Blom, W; Brubakk, AM; Brusilow, S; Burton, BK; Cann, HM; Kerr, D; Mamunes, P; Matalon, R; Myerberg, D; Schafer, IA; Waber, L | 1 |
| Berger, R; Blom, W; Brubakk, AM; Teijema, LL | 1 |
| Canosa, C; Grisolia, S; Gutierez, F; Jordá, A; Nyhan, WL; Rubio, V | 1 |
| Altman, RP; Glasgow, AM; Schulman, JD; Stolar, CJ | 1 |
| Parks, JK; Stumpf, DA | 1 |
| Yajima, Y | 1 |
| Gatfield, PD; Gordon, BA; Haust, MD | 1 |
| Batshaw, ML; Brusilow, SW; Thomas, GH | 1 |
| Carter, M; Donnel, GN; Koch, R; McLaren, J; Ng, WG; Oizumi, J; Shaw, KN | 1 |
| Batshaw, M; Stewart, PM; Valle, D; Walser, M | 1 |
| Freund, RK; Jacobson, DB; Prescott, LM; Rector, JT | 1 |
| Hoek, JB; Tager, JM; Wanders, RJ | 1 |
| Bachmann, C; Colombo, JP | 1 |
| Batshaw, ML; Brusilow, S; Painter, MJ; Schafer, IA; Sproul, GT; Thomas, GH | 1 |
| Gray, RG; Green, A; Hall, S; McKeown, C | 1 |
| Gillardin, JM; Heulard, I; Levy, RH; Stephens, JR; Verleye, M | 1 |
| Igarashi, M; Iwasaki, H; Kawana, S; Namiki, A | 1 |
| Dejong, CH; Deutz, NE; Soeters, PB | 1 |
| Hartman, WJ; Prior, RL; Torre, PM | 1 |
| Bébin, B; Candito, M; Chambon, P; Chazalette, JP; Ferraci, JP; Mathieu, M; Sebag, F; Vianey-Saban, C | 1 |
| Elzalabany, MM; Madina, H; Morsy, MR; Ramadan, MA; Sharaf, SA; Soliman, AT | 1 |
| Beringer, A; Hubert, P; Jan, D; Jouvet, P; Laurent, J; Poggi, F; Rabier, D; Revillon, Y; Saudubray, JM | 1 |
| Ishizaki, T; Kubota, K | 1 |
| Flynn, NE; Knabe, DA; Wu, G | 1 |
| Beaudet, AL; Bradley, A; O'Brien, WE; Patejunas, G | 1 |
| Fukuda, K; Inui, Y; Ishiguro, H; Kakimoto, H; Kawata, S; Kono, N; Matsuzawa, Y; Namba, M; Tamura, S | 1 |
| Brosnan, JT; Ewart, HS | 1 |
| Henry, BW; Lange, C; Matalon, R; Melnyk, AR; Zeller, WP | 1 |
| Beliveau Carey, G; Brusilow, S; Cheung, CW; Cohen, NS; Raijman, L | 1 |
| Gunasekaran, M; Gunasekaran, S; Imbayagwo, M; Manavathu, E; McDonald, L | 1 |
| Wu, G | 1 |
| Bervoets, K; Böhles, H; Förster, H; Renner, C; Sewell, AC | 1 |
| Donati, MA; Filippi, L; Resti, M; Zammarchi, E | 1 |
| Dewar, RA; Gatfield, DP; Gordon, BA; Haust, MD | 1 |
| Bardet, J; Cadoudal, M; Drouin, V; Kuchler, G; Meyer-Gast, D; Poggi-Travert, F; Rabier, D; Saudubray, JM | 1 |
| Haust, MD | 1 |
| Chow, WC; Ng, HS; Tan, IK; Thum, TY | 1 |
| Hayashi, Y; Hiroi, M; Ohta, N; Saito, H; Saito, T; Sakai, N | 1 |
| Brosnan, JT; Nissim, I; Yudkoff, M | 1 |
| Ahrens, MJ; Berry, SA; Markowitz, DJ; Plante, RJ; Tuchman, M; Whitley, CB | 1 |
| Matìjèková, A; Sychrová, H | 1 |
| Kawata, A; Suda, M; Tanabe, H | 1 |
| Bonocore, G; Buonocore, G; Ciani, F; Donati, MA; Pasquini, E; Shih, VE; Zammarchi, E | 1 |
| Fukushige, T; Kakinoki, H; Kobayashi, K; Saheki, T | 1 |
| Akatsu, T; Kawamoto, S; Kerlin, P; Kobayashi, K; Lynch, SV; Matsunami, H; Nakagawa, S; Saheki, T; Steadman, C; Strong, RW | 1 |
| Nagao, M; Oyanagi, K | 1 |
| Alonso, EM; Boyle, JT; Emond, JC; Millis, JM; Molleston, JP; Rosenthal, P; Whitington, PF | 1 |
| Beaudet, AL; Dennis, JA; Frazer, M; Healy, PJ; Lee, B; Mull, B; O'Brien, WE; Patejunas, G; Reeds, PJ; Warman, AW; Yu, H | 1 |
| Leonard, JV; Morris, AA; Oddie, SJ; Pourfarzam, M; Richmond, SW; Worthington, V | 1 |
| Futamura, A; Hirade, S; Inoue, H; Ogawa, K; Takashima, S; Ueno, H | 1 |
| Aguilar-Cordova, E; Beaudet, AL; Dennis, JA; Healy, PJ; Lee, B; Mull, B; O'Brien, W; Pastore, L; Reeds, P; Yu, H | 1 |
| Blachier, F; Guihot-Joubrel, G; Morel, E; Mouillé, B; Robert, V | 1 |
| Arena, ME; Manca de Nadra, MC; Saguir, FM | 1 |
| Bauder-Gross, D; Hartmann, F; Plauth, M; Raible, A; Vieillard-Baron, D | 1 |
| Hartmann, F; Plauth, M; Raible, A; Schneider, BH | 1 |
| Almashanu, S; Biery, B; Camacho, JA; Casey, R; Goodman, BK; Hu, CA; Lambert, M; Mitchell, GA; Obie, C; Steel, G; Valle, D | 1 |
| Brosnan, JT; Brosnan, ME; Nissim, I; Yudkoff, M | 1 |
| Fukushige, T; Kobayashi, K; Li, MX; Nakajima, T; Saheki, T; Seiler, N | 1 |
| Celli, M; Crifò, C; D'Eufemia, P; Finocchiaro, R; Giardini, O; Salerno, C | 1 |
| Eto, Y; Kanazawa, N; Kira, J; Ohashi, T; Saito, T; Tsujino, S; Yamada, T | 1 |
| Clemmesen, JO; Kondrup, J; Ott, P | 1 |
| Iwata, K; Kajimura, M; Sakamoto, T | 1 |
| Kobayashi, K; Maruyama, H; Nishio, T; Ogawa, M; Saheki, T; Sunohara, N | 1 |
| Chou, SP; Hu, YH; Hwu, WL; Kobayashi, K; Saheki, T; Wang, JH; Yamaguchi, N | 1 |
| Bauer, MF; Bieger, I; Gempel, K; Gerbitz, KD; Hofmann, S; Pontz, BF; Stadler, S | 1 |
| Hashikura, Y; Ikeda, S; Ikegami, T; Iwai, M; Kawasaki, S; Kobayashi, K; Saheki, T; Takei, Y; Yazaki, M | 1 |
| Kanazawa, N; Miyamoto, T; Tsujino, S | 1 |
| Dehne, MG; Fuchs, M; Hempelmann, G; Mühling, J; Sablotzki, A; Spatz, J; Weiss, S | 1 |
| Iseki, K; Kobayashi, K; Kochinda, T; Komine, Y; Muratani, H; Oshiro, S; Saheki, T; Takishita, S; Tana, T; Yamazato, M | 1 |
| Deutz, NE; Hallemeesch, MM; Soeters, PB | 1 |
| Doutreleau, S; Geny, B; Lampert, E; Lonsdorfer, J; Mettauer, B; Piquard, F; Schaefer, A | 1 |
| Costa Rosa, LF; Lancha, AH; Mendonça, JR; Meneguello, MO | 1 |
| Bracht, A; Bracht, L; Ishii-Iwamoto, EL; Kelmer-Bracht, AM; Lousano, SH; Yassuda Filho, P | 1 |
| Antonelli, AC; dos Santos Michima, LE; Kitamura, SS; Maruta, CA; Mori, CS; Ortolani, EL; Sucupira, MC | 1 |
| Au, WL; Koh, PL; Lim, MS; Lim, TC; Loh, NK; Seow, DC; Tan, IK; Yee, WC | 1 |
| Aalto, M; Lukkarinen, M; Näntö-Salonen, K; Pulkki, K; Simell, O | 1 |
| CAMPBELL, JW | 1 |
| GERSHENOVITCH, ZS; KRICHEVSKAYA, AA; SHUGALEI, WS | 1 |
| GIULIANI, V | 1 |
| CAMERON, JA; VINCENT, WF | 1 |
| KESNER, L | 1 |
| Beneduce, L; Chieppa, G; Massa, S; Spano, G | 1 |
| BURRIS, RH; COHEN, PP; GRISOLIA, S | 1 |
| Yazaki, M | 1 |
| Blachier, F; Mouillé, B; Robert, V | 1 |
| Baldwin, RL; Bequette, BJ; Oba, M; Owens, SL | 2 |
| Govindasamy, C; Nadiger, HA; Sirajudeen, KN; Swamy, M; Zakaria, AZ | 1 |
| Berger, R; Besley, GT; Cleary, MA; de Koning, TJ; Dorland, L; Duran, M; Mandell, R; Olpin, SE; Poll-The, BT; Shih, VE | 1 |
| Daikhin, Y; Horyn, O; Luhovyy, B; Nissim, I; Wehrli, SL; Yudkoff, M | 1 |
| Dutra Filho, CS; Pederzolli, CD; Prestes, CC; Sgaravatti, AM; Sgarbi, MB; Wajner, M; Wannmacher, CM; Wyse, AT; Zorzi, GK | 1 |
| Al-Dirbashi, OY; Al-Hassnan, ZN; Rashed, MS | 1 |
| Djais, A; Hoshino, E; Sato, N; Uematsu, H | 1 |
| Huoponen, K; Näntö-Salonen, K; Niinikoski, H; Simell, O; Tanner, LM | 1 |
| Au, WL; Lim, CC; Wong, YC; Xu, M; Ye, J | 1 |
| Castillo, L; Erez, A; Lee, B; Marini, JC | 1 |
| Biswas, K; Kharbuli, ZY; Saha, N | 1 |
| Chang, CK; Chiang, CW; Liu, TH; Lo, YW; Tseng, HF; Wu, CL | 1 |
| Castillo, L; Didelija, IC; Lee, B; Marini, JC | 1 |
| Bhatia, M; Causey, CP; Dreyton, CJ; Jones, JE; Knuckley, B; Osborne, TC; Takahara, H; Thompson, PR | 1 |
| Deutz, NE; Hayes, PC; Jalan, R; Lee, A; Olde Damink, SW; Redhead, DN; Ter Steege, JC | 1 |
| Aires, CC; de Almeida, IT; Duran, M; Ijlst, L; Silva, MF; van Cruchten, A; Wanders, RJ | 1 |
| Baruteau, J; de Baulny, HO; Faghfoury, H; Häberle, J; Schulze, A | 1 |
| Kohara, A; Machida, M; Omi, N; Takeda, K; Takemasa, T | 1 |
| Choi, DE; Lee, KW; Na, KR; Shin, YT | 1 |
| Busanello, EN; Grings, M; Knebel, LA; Leipnitz, G; Lobato, VA; Moura, AP; Pettenuzzo, LF; Ritter, L; Tonin, AM; Vargas, CR; Viegas, CM; Wajner, M; Zanatta, A | 1 |
| Go, H; Hashimoto, K; Hosoya, M; Imamura, T; Momoi, N; Ogasawara, K; Sakamoto, O; Takubo, N | 1 |
| Busanello, EN; Fernandes, CG; Leipnitz, G; Moura, AP; Seminotti, B; Tonin, AM; Viegas, CM; Wajner, M; Zanatta, A | 1 |
| de Nadra, MC; Saguir, FM; Sánchez, LA; Savino, MJ | 1 |
| Chandler, RJ; Cusmano-Ozog, K; McGuire, PJ; Sun, Q; Sutton, VR; Tarasenko, TN; Venditti, CP | 1 |
| DU, K; Jin, HY; Liu, WP; Luan, Z; Qu, SQ; Wang, ZY; Yang, H; Yang, YX | 1 |
| Arnoux, JB; Barbier, V; Barouki, R; Bonnefont, JP; Brassier, A; De Lonlay, P; Dubois, S; Dupic, L; Gobin, S; Habarou, F; Kossorotoff, M; Lesage, F; Ottolenghi, C; Servais, A; Touati, G; Valayannopoulos, V | 1 |
| Arslan, N; Bulbul, S; Gunduz, M; Häberle, J; Kose, E; Unal, O | 1 |
| Fernie, AR; Joshi, V | 1 |
| Burgard, P; Cederbaum, S; Cuthbertson, D; Holbert, A; McCarter, R; Waisbren, SE | 1 |
| Hua, Q; Liu, L; Liu, Y; Nie, X; Yang, C; Zhang, H; Zhao, GP | 1 |
| Cant, JP; de Lange, CFM; Htoo, JK; Mansilla, WD; Nyachoti, CM; Silva, KE; Zhu, C | 1 |
| Balikci, C; Erdogan, H; Gultekin, G; Gultekin, M; Ural, K; Voyvoda, H | 1 |
| Eto, K; Funahashi, A; Furuie, S; Furukawa, T; Gao, Q; Horiuchi, M; Kadowaki, T; Kuroda, E; Moriyama, M; Nakamura, Y; Saheki, T; Setogawa, Y; Sinasac, DS; Tai, YH; Takano, K; Ushikai, M; Yamamura, KI; Yasuda, I | 1 |
| Bazer, FW; Gilbreath, KR; Nawaratna, GI; Satterfield, MC; Wickersham, TA; Wu, G | 2 |
| Bazer, FW; Cleere, JJ; Gilbreath, KR; Satterfield, MC; Wu, G | 1 |
| Delmônego, L; Delwing-Dal Magro, D; Delwing-de Lima, D; Lima, AB; Maia, TP; Pscheidt, LC; Vincenzi, KL | 1 |
| Delmonego, L; Delwing-Dal Magro, D; Delwing-de Lima, D; Eger, L; Lima, AB; Maia, TP; Pscheidt, LC; Vincenzi, KL | 1 |
| Chen, C; Chen, J; Cui, Q; Deng, J; Huang, B; Li, Y; Liu, J; Liu, S; Lu, S; Lv, J; Ma, J; Tang, K; Wang, D; Yang, Z; Zhang, H | 1 |
| Chen, Y; Wang, G; Wang, Z; Yan, X; Zhang, L; Zhao, F; Zhou, M | 1 |
| Arnoux, JB; Benoist, JF; Bérat, CM; Bouchereau, J; Brassier, A; de Lonlay, P; Imbard, A; Josse, C; Montestruc, F; Pontoizeau, C; Schiff, M | 1 |
| Li, Y; Liu, XF; Lu, JJ; Qiang, JW; Yang, XY | 1 |
19 review(s) available for citrulline and ammonium hydroxide
| Article | Year |
|---|---|
[A case of ornithine transcarbamylase deficiency presenting severe symptoms in adulthood].
Topics: Adult; Ammonia; Arginine; Citrulline; Consciousness Disorders; Female; Glycine; Humans; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid | 1992 |
Hyperornithinemia, hyperammonemia, homocitrullinuria (HHH) syndrome: presentation as acute liver disease with coagulopathy.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Blood Coagulation Disorders; Child, Preschool; Citrulline; Female; Humans; Liver Diseases; Liver Function Tests; Ornithine; Syndrome | 1992 |
[Adverse effects of branched chain amino acid transfusion on type-II citrullinemia--report of an adult case].
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Ammonia; Argininosuccinate Synthase; Citrulline; Humans; Infusions, Intravenous; Liver; Male; Urea | 1991 |
Conditional deficiencies of ornithine or arginine.
Topics: Amino Acids; Amino Acids, Branched-Chain; Ammonia; Animals; Arginine; Citrulline; Female; Glycine; Hepatic Encephalopathy; Humans; Liver Cirrhosis; Lysine; Models, Biological; Ornithine; Orotic Acid; Pregnancy; Protein Deficiency; Urease | 1986 |
Hereditary disorders of the urea cycle in man: biochemical and molecular approaches.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinate Synthase; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Female; Humans; Hyperargininemia; Ornithine Carbamoyltransferase Deficiency Disease; Pregnancy; Prenatal Diagnosis; RNA, Messenger; Urea | 1987 |
Inherited hyperammonemic syndromes.
Topics: Acidosis; Amino Acids; Ammonia; Animals; Arginine; Brain; Brain Diseases; Chemical and Drug Induced Liver Injury; Citrulline; Dementia; Homeostasis; Humans; Infant, Newborn; Liver; Lysine; Metabolism, Inborn Errors; Ornithine Carbamoyltransferase; Phosphotransferases; Succinates; Syndrome; Urea; Urease | 1974 |
Arginnosuccinic aciduria.
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Arginine; Blood Urea Nitrogen; Child, Preschool; Citrulline; Humans; Intellectual Disability; Lyases; Rats; Succinates | 1967 |
[Feeble mindedness caused by genetic disorders of amino acid metabolism].
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Glycine; Hartnup Disease; Histidine; Homocystinuria; Humans; Hydroxyproline; Intellectual Disability; Lysine; Maple Syrup Urine Disease; Methionine; Phenylketonurias; Proline; Sarcosine; Succinates; Transferases; Tryptophan; Valine | 1968 |
[Hereditary enzyme defects of the urea cycle].
Topics: Adult; Ammonia; Arginase; Arginine; Child; Child, Preschool; Citrulline; Enzymes; Female; Humans; Infant; Infant, Newborn; Ligases; Lyases; Male; Metabolism, Inborn Errors; Ornithine; Ornithine Carbamoyltransferase; Phosphotransferases; Succinates; Transaminases; Urea | 1971 |
Hereditary metabolic disorders of the urea cycle.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginase; Arginine; Aspartic Acid; Carbamates; Citrulline; Humans; Ligases; Liver; Lyases; Models, Chemical; Ornithine Carbamoyltransferase; Phosphotransferases; Succinates; Urea | 1971 |
The ornithine-urea cycle: biosynthesis and regulation of carbamyl phosphate synthetase I and ornithine transcarbamylase.
Topics: Ammonia; Animals; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Dietary Proteins; Glutamates; Kinetics; Ligases; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase; Urea | 1981 |
Regulation of ornithine metabolism.
Topics: Ammonia; Animals; Biological Transport; Citrulline; Cytosol; Fibroblasts; Humans; Mitochondria; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase; Urea | 1981 |
Encephalopathy of Reye's syndrome: a review of pathogenetic hypotheses.
Topics: Acidosis; Ammonia; Animals; Brain; Citrulline; Fatty Acids, Nonesterified; Glucose; Humans; Insulin; Intracranial Pressure; Lactates; Mitochondria; Mitochondria, Liver; Nitrogen; Ornithine; Rabbits; Reye Syndrome | 1982 |
Control mechanisms of energy-dependent metabolic pathways in hepatocytes.
Topics: Adenosine Triphosphate; Ammonia; Animals; Bicarbonates; Citrulline; Energy Metabolism; Gluconeogenesis; Glucose; Lactates; Liver; Mitochondria, Liver; Oxidative Phosphorylation; Oxygen Consumption; Pyruvates; Rats | 1981 |
[Hyperornithinemia-hyperammonemia-homocitrullinuria (H.H.H.) syndrome].
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Diagnosis, Differential; Humans; Infant, Newborn; Ornithine; Ornithine-Oxo-Acid Transaminase; Syndrome | 1998 |
[Adult-onset type II citrullinemia in a patient undergoing continuous ambulatory peritoneal dialysis].
Topics: Ammonia; Argininosuccinate Synthase; Citrulline; Hepatic Encephalopathy; Humans; Liver; Male; Middle Aged; Peritoneal Dialysis, Continuous Ambulatory | 1998 |
[Molecular genetic studies of mitochondrial ornithine transporter deficiency (HHH syndrome)].
Topics: Amino Acid Transport Systems, Basic; Ammonia; Animals; Base Sequence; Carrier Proteins; Citrulline; Humans; Membrane Transport Proteins; Mitochondria; Molecular Sequence Data; Mutation; Nervous System Diseases; Ornithine; Syndrome | 2001 |
[Adult-onset type II citrullinemia].
Topics: Adult; Ammonia; Arginine; Brain; Calcium-Binding Proteins; Citrulline; Citrullinemia; Female; Humans; Liver; Liver Transplantation; Magnetic Resonance Imaging; Male; Middle Aged; Organic Anion Transporters | 2003 |
Citrulline metabolism in plants.
Topics: Adaptation, Physiological; Amino Acid Transport Systems; Ammonia; Animals; Arabidopsis; Argininosuccinate Synthase; Bacteria; Biological Transport; Carbamyl Phosphate; Citrulline; Cucurbitaceae; Fungi; Gene Expression Regulation, Plant; Humans; Ornithine; Ornithine Carbamoyltransferase; Stress, Physiological | 2017 |
5 trial(s) available for citrulline and ammonium hydroxide
| Article | Year |
|---|---|
Activity of citrulline malate on acid-base balance and blood ammonia and amino acid levels. Study in the animal and in man.
Topics: Acid-Base Equilibrium; Adult; Amino Acids; Ammonia; Animals; Citrulline; Double-Blind Method; Female; Humans; Kidney; Liver; Malates; Male; Rats; Rats, Inbred Strains | 1991 |
L-arginine reduces exercise-induced increase in plasma lactate and ammonia.
Topics: Adult; Ammonia; Arginine; Citrulline; Double-Blind Method; Exercise; Humans; Lactates; Male; Muscle, Skeletal; Nitric Oxide; Ornithine | 2002 |
No effect of short-term arginine supplementation on nitric oxide production, metabolism and performance in intermittent exercise in athletes.
Topics: Ammonia; Arginine; Citrulline; Cross-Over Studies; Exercise; Humans; Lactates; Male; Martial Arts; Nitric Oxide; Placebos; Young Adult | 2009 |
Ammonia-Nitrogen Added to Low-Crude-Protein Diets Deficient in Dispensable Amino Acid-Nitrogen Increases the Net Release of Alanine, Citrulline, and Glutamate Post-Splanchnic Organ Metabolism in Growing Pigs.
Topics: Alanine; Amino Acids; Ammonia; Animal Feed; Animal Nutritional Physiological Phenomena; Animals; Citrulline; Diet; Dietary Proteins; Gastrointestinal Tract; Liver; Male; Nitrogen; Swine | 2018 |
Ruminal microbes of adult sheep do not degrade extracellular l-citrulline.
Topics: Ammonia; Animal Feed; Animals; Arginine; Bacteria; Citrulline; Diet; Dietary Supplements; Female; Glutamic Acid; Glutamine; Ornithine; Proline; Rumen; Sheep; Urea | 2020 |
295 other study(ies) available for citrulline and ammonium hydroxide
| Article | Year |
|---|---|
Effect of fatty acids on the disposition of ammonia.
Topics: Ammonia; Animals; Brain; Caprylates; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Fatty Acids; Glutamate Dehydrogenase; Glutamate-Ammonia Ligase; In Vitro Techniques; Liver; Male; Rats; Urea | 1976 |
Arginine metabolism by spiroplasma citri.
Topics: Ammonia; Arginine; Citrulline; Fructose; Glucose; Hydrogen-Ion Concentration; Ornithine; Spiroplasma | 1976 |
Relationship between intramitochondrial citrate and the activity of carbamoyl-phosphate synthase (ammonia).
Topics: Adenosine Triphosphate; Ammonia; Animals; Calcimycin; Carbamoyl-Phosphate Synthase (Ammonia); Citrates; Citrulline; Glutamates; Hydrogen-Ion Concentration; Magnesium; Malates; Mitochondria, Liver; Ornithine; Phosphotransferases; Rats | 1977 |
Arginine catabolism in Aphanocapsa 6308.
Topics: Adenosine Triphosphate; Aerobiosis; Ammonia; Arginase; Arginine; Carbon Dioxide; Citrulline; Cyanobacteria; Hydrolases; Ornithine; Urea; Urease | 1978 |
Inhibition of urea synthesis by 4-pentenoic acid.
Topics: Ammonia; Animals; Aspartic Acid; Citrulline; Fatty Acids, Monounsaturated; Fatty Acids, Unsaturated; Glutamates; Liver; Ornithine; Phosphotransferases; Rats; Transferases; Urea; Valerates | 1975 |
Hyperornithinemia, hyperammonemia, and homocitrullinuria associated with decreased carbamyl phosphate synthetase I activity.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Biopsy; Carbamoyl-Phosphate Synthase (Ammonia); Child; Child, Preschool; Citrulline; Dietary Proteins; Female; Humans; Leukocytes; Liver; Lysine; Male; Microscopy, Electron; Mitochondria, Liver; Ornithine; Phosphotransferases | 1975 |
Proceedings: Hepatic ultrastructure in a child with carbamyl phosphate synthetase deficiency, hyperornithinaemia, hyperammonaemia, and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Carbamoyl-Phosphate Synthase (Ammonia); Child; Citrulline; Humans; Liver; Male; Ornithine; Phosphotransferases | 1975 |
Pathways of assimilation of [13N]N2 and 13NH4+ by cyanobacteria with and without heterocysts.
Topics: Alanine; Ammonia; Citrulline; Cyanobacteria; Glutamates; Glutamine; Methionine Sulfoximine; Nitrogen Fixation; Species Specificity | 1978 |
The interrelationship between ureogenesis and protein synthesis in isolated rat-liver cells.
Topics: Amino Acids; Aminooxyacetic Acid; Ammonia; Animals; Arginine; Citrulline; Cycloheximide; Glucose; Leucine; Liver; Male; Protein Biosynthesis; Rats; Urea; Valine | 1979 |
Relationship between pyruvate carboxylation and citrulline synthesis in rat liver mitochondria: the effect of ammonia and energy.
Topics: Ammonia; Animals; Citrulline; Energy Metabolism; Male; Mitochondria, Liver; Oleic Acids; Pyruvate Carboxylase; Rats | 1979 |
The effect of dietary o,p'-DDT on ureagenesis from ammonia by isolated rat hepatocytes.
Topics: Ammonia; Animals; Citrulline; DDT; In Vitro Techniques; Lactates; Liver; Male; Mitochondria, Liver; Ornithine; Rats; Urea | 1979 |
Lysine intolerance in a variant form of citrullinemia.
Topics: Adolescent; Adult; Amino Acids; Ammonia; Citrulline; Cystine; Female; Humans; Lysine | 1979 |
Urea cycle operation in the arginine deficient rat.
Topics: Ammonia; Animals; Arginase; Arginine; Argininosuccinate Lyase; Argininosuccinate Synthase; Carbamoyl-Phosphate Synthase (Glutamine-Hydrolyzing); Citrulline; Liver; Male; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Rats; Urea | 1979 |
3-Aminopiperid-2-one, an unusual metabolite in the urine of a patient with hyperammonaemia, hyperornithinaemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Chromatography, Gas; Chromatography, Ion Exchange; Citrulline; Electrophoresis; Humans; Mass Spectrometry; Ornithine; Piperidines; Piperidones | 1978 |
Ureotelism and ammonotelism in trypanosomatids.
Topics: Ammonia; Animals; Arginine; Citrulline; Crithidia; Culture Media; Eukaryota; Leishmania; Species Specificity; Trypanosoma; Urea | 1978 |
Regulation of urea synthesis in rat liver. Increase in the concentrations of ornithine and acetylglutamate in rat liver in response to urea synthesis stimulated by the injection of an ammonium salt.
Topics: Ammonia; Animals; Citrulline; Glutamates; Kinetics; Liver; Male; Ornithine; Quaternary Ammonium Compounds; Rats; Urea | 1978 |
Ornithine methyl ester. An unusual metabolite encountered in the urine of patients with a urea cycle disorder characterized by hyperammonemia, hyperornithinemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Chromatography; Citrulline; Dansyl Compounds; Humans; Ornithine | 1977 |
The effect of glucagon on ureagenesis from ammonia by isolated rat hepatocytes.
Topics: Ammonia; Animals; Citrulline; Glucagon; In Vitro Techniques; Kinetics; Liver; Male; Mitochondria, Liver; Ornithine; Rats; Urea | 1977 |
Periodic hyperammonemia, hyperlysinemia, and homocitrullinuria associated with decreased argininosuccinate synthetase and arginase activities.
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginase; Arginine; Argininosuccinate Synthase; Citrulline; Humans; Hyperargininemia; Intellectual Disability; Ligases; Liver; Lysine; Male | 1977 |
Citrullinemia: phenotypic variations.
Topics: Amino Acids; Ammonia; Argininosuccinate Synthase; Blood Urea Nitrogen; Citrulline; Female; Humans; Infant; Orotic Acid; Phenotype | 1976 |
Congenital hyperammonemic syndromes.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinate Synthase; Argininosuccinic Aciduria; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Diagnosis, Differential; Humans; Hyperargininemia; Infant, Newborn; Infant, Newborn, Diseases; Lysine; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Syndrome; Urea | 1976 |
Effect of ornithine and lactate on urea synthesis in isolated hepatocytes.
Topics: Ammonia; Animals; Butyrates; Citrulline; In Vitro Techniques; Kinetics; Lactates; Liver; Male; Oleic Acids; Ornithine; Pyruvates; Rats; Starvation; Stimulation, Chemical; Urea | 1976 |
Possible effect of blood ammonia on food intake of rats fed amino acid imbalanced diets.
Topics: Amino Acids; Ammonia; Animal Nutritional Physiological Phenomena; Animals; Arginine; Aspartic Acid; Body Weight; Citrulline; Histidine; Ligases; Liver; Male; Nutrition Disorders; Perfusion; Protein Deficiency; Quaternary Ammonium Compounds; Rats; Structure-Activity Relationship; Succinates; Tryptophan | 1975 |
Urinary metabolites characteristic of urea-cycle amino acid deficiency.
Topics: Amino Acids; Amino Acids, Essential; Ammonia; Animal Nutritional Physiological Phenomena; Animals; Arginine; Biotransformation; Body Weight; Carbamyl Phosphate; Citrates; Citrulline; Deficiency Diseases; Diet; Male; Nitrogen; Ornithine; Orotic Acid; Pyrimidines; Rats; Urea | 1975 |
Role of anion translocation across the mitochondrial membrane in the regulation of urea synthesis from ammonia by isolated rat hepatocytes.
Topics: Acetoacetates; Adenosine Triphosphate; Aminooxyacetic Acid; Ammonia; Animals; Biological Transport, Active; Citrulline; Cycloserine; Hydroxybutyrates; In Vitro Techniques; Kinetics; Liver; Male; Malonates; Membranes; Mitochondria, Liver; Models, Biological; Perfusion; Rats; Urea | 1975 |
Hyperdibasicaminoaciduria, hyperammonemia, and growth retardation: Treatment with arginine, lysine, and citrulline.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Child; Citrulline; Female; Growth Disorders; Humans; Lysine | 1975 |
A variant form of citrullinemia.
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinate Synthase; Citrulline; Female; Humans; Liver | 1976 |
[A case of hyperornithinemia-hyperammonemia-homocitrullinuria (HHH) syndrome with spastic paraparesis and severe distal muscle atrophy of lower limbs].
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Electromyography; Humans; Leg; Male; Muscular Atrophy; Ornithine; Paraparesis, Tropical Spastic; Spinal Cord; Syndrome | 1992 |
[A case of citrullinemia associated with isolated ACTH deficiency, rapidly developing coma].
Topics: Adrenal Cortex; Adrenocorticotropic Hormone; Adult; Ammonia; Argininosuccinate Synthase; Citrulline; Coma; Humans; Hydrocortisone; Liver; Male | 1992 |
Isolation of a gene encoding a chaperonin-like protein by complementation of yeast amino acid transport mutants with human cDNA.
Topics: Amino Acid Sequence; Ammonia; Base Sequence; Biological Transport; Blotting, Southern; Chaperonins; Citrulline; Cloning, Molecular; DNA; Genes; Genetic Complementation Test; Histidine; Humans; Molecular Sequence Data; Proteins; Restriction Mapping; RNA, Messenger; Saccharomyces cerevisiae; Sequence Alignment | 1992 |
[The dibasic amino acid metabolic disorders].
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Blood Transfusion; Citrulline; Humans; Hyperargininemia; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Renal Dialysis | 1992 |
Hyperammonemia-hyperornithinemia-homocitrullinuria syndrome: neurologic, ophthalmologic, and neuropsychologic examination of six patients.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Child, Preschool; Citrulline; Eye Diseases; Female; Humans; Male; Nervous System Diseases; Neuropsychological Tests; Ornithine; Psychomotor Performance | 1992 |
Neonatal form of the hyperornithinaemia, hyperammonaemia, and homocitrullinuria (HHH) syndrome and prenatal diagnosis.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Cells, Cultured; Citrulline; Female; Gestational Age; Hepatitis B Surface Antigens; Humans; Hyaline Membrane Disease; Infant, Newborn; Male; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Ornithine-Oxo-Acid Transaminase; Pregnancy; Pregnancy Outcome; Prenatal Diagnosis; Syndrome | 1992 |
Urea-hydrolysis-dependent citrulline synthesis by Ureaplasma urealyticum.
Topics: Ammonia; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Hydrolysis; Ornithine Carbamoyltransferase; Urea; Ureaplasma | 1992 |
Plasma urea and ammonia in epileptic patients and their relatives.
Topics: Adolescent; Adult; Amino Acids; Ammonia; Child; Citrulline; Epilepsy; Family; Female; Humans; Male; Middle Aged; Ornithine; Urea | 1992 |
Continuous arteriovenous haemofiltration in a neonate with hyperammonaemic coma due to citrullinaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Coma; Hemofiltration; Humans; Infant, Newborn; Male | 1992 |
EEG changes during recovery from acute severe neonatal citrullinemia.
Topics: Ammonia; Brain; Brain Diseases; Citrulline; Electroencephalography; Humans; Infant, Newborn; Male; Metabolism, Inborn Errors | 1991 |
N-acetylglutamate synthetase deficiency: clinical and laboratory observations.
Topics: Acetyltransferases; Amino-Acid N-Acetyltransferase; Ammonia; Arginine; Benzoates; Benzoic Acid; Citrulline; Dietary Proteins; Humans; Infant; Infant, Newborn; Liver; Male; Phenylacetates | 1991 |
[The correlation of consciousness level and the concentration of CSF ammonia in a patient with adult-type citrullinemia].
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Astrocytes; Circadian Rhythm; Citrulline; Consciousness; Glutamine; Humans; Hydrocortisone; Male; Receptors, Glucocorticoid | 1991 |
Hyperornithinemia, hyperammonemia and homocitrullinuria--a case report and study of ornithine metabolism using in vivo deuterium labelling.
Topics: Adult; Ammonia; Arginine; Chromatography, Liquid; Citrulline; Deuterium; Humans; Male; Mass Spectrometry; Ornithine | 1991 |
A case of citrullinemia with abnormal messenger RNA for argininosuccinate synthetase.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinate Synthase; Citrulline; Humans; Infant, Newborn; Male; Pedigree; RNA, Messenger | 1991 |
Use of citrulline as a diagnostic marker in the prospective treatment of urea cycle disorders.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Biomarkers; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Humans; Infant, Newborn; Male; Urea | 1991 |
Episodic hyperammonemia in adult siblings with hyperornithinemia, hyperammonemia, and homocitrullinuria syndrome.
Topics: Adult; Ammonia; Citrulline; Female; Fibroblasts; Glutamine; Humans; Leucine; Male; Metabolism, Inborn Errors; Ornithine; Phenylbutyrates; Recurrence; Syndrome; Urea | 1990 |
Haloperidol-induced hyperammonaemia in a child with citrullinaemia.
Topics: Ammonia; Attention Deficit Disorder with Hyperactivity; Child, Preschool; Citrulline; Haloperidol; Humans; Intellectual Disability; Male; Metabolism, Inborn Errors | 1990 |
Abnormal urinary excretion of polyamines in HHH syndrome (hyperornithinemia associated with hyperammonemia and homocitrullinuria).
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Biogenic Polyamines; Citrulline; Diet; Humans; Male; Ornithine; Syndrome | 1990 |
Citrate therapy in argininosuccinate lyase deficiency.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Argininosuccinic Acid; Argininosuccinic Aciduria; Aspartic Acid; Child; Citrates; Citric Acid; Citrulline; Female; Humans; Infant; Lyases | 1990 |
Peptidylarginine deiminase in rat and mouse hemopoietic cells.
Topics: Ammonia; Animals; Arginine; Blotting, Western; Bone Marrow; Bone Marrow Cells; Citrulline; Female; Hydrolases; Immunosorbent Techniques; Macrophages; Mice; Mice, Inbred C57BL; Monocytes; Neutrophils; Peritoneal Cavity; Protein-Arginine Deiminase Type 4; Protein-Arginine Deiminases; Rats; Rats, Inbred Strains; Spleen | 1990 |
Macrophage cytotoxicity: role for L-arginine deiminase and imino nitrogen oxidation to nitrite.
Topics: Ammonia; Animals; Cells, Cultured; Citrulline; Cytotoxicity, Immunologic; Homoarginine; Hydrolases; Macrophage Activation; Macrophages; Mice; Nitrates; Nitrites | 1987 |
Comparison of ornithine metabolism in hyperornithinaemia-hyperammonaemia-homocitrullinuria syndrome, lysinuric protein intolerance and gyrate atrophy fibroblasts.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Fibroblasts; Heterozygote; Homozygote; Humans; Lysine; Ornithine; Ornithine-Oxo-Acid Transaminase; Oxidation-Reduction; Proteins; Syndrome | 1989 |
Changes in urea cycle-related metabolites in the mouse after combined administration of valproic acid and an amino acid load.
Topics: Amino Acids; Ammonia; Animals; Carbamoyl-Phosphate Synthase (Glutamine-Hydrolyzing); Citrulline; Glutamates; Glutamine; Liver; Mice; Ornithine; Urea; Valproic Acid | 1989 |
Citrullinemia: early diagnosis & successful management of an otherwise lethal disorder.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Argininosuccinate Synthase; Citrulline; Female; Humans; India; Infant, Newborn | 1989 |
Peritoneal dialysis in the treatment of metabolic crises caused by inherited disorders of organic and amino acid metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Creatinine; Female; Humans; Infant, Newborn; Male; Maple Syrup Urine Disease; Peritoneal Dialysis; Propionates; Tyrosine | 1989 |
[Carbamyl phosphate synthase deficiency: clinical symptoms, diagnosis and dietary-medicamentous treatment in the neonatal period and infancy].
Topics: Amino Acids; Ammonia; Arginine; Benzoates; Benzoic Acid; Carbamoyl-Phosphate Synthase (Ammonia); Carnitine; Citrulline; Combined Modality Therapy; Dietary Proteins; Female; Fetal Growth Retardation; Humans; Infant, Newborn; Male; Pregnancy | 1989 |
A simple animal model of hyperammonemia.
Topics: Acetates; Ammonia; Animals; Citrulline; Disease Models, Animal; Glutamate Dehydrogenase; Liver; Male; Orotic Acid; Rats; Rats, Inbred Strains; Urea | 1989 |
Short-term metabolic fate of [13N]ammonia in rat liver in vivo.
Topics: Alanine Transaminase; Amino Acids; Ammonia; Animals; Aspartate Aminotransferases; Carbamyl Phosphate; Chromatography, High Pressure Liquid; Citrulline; Cytoplasm; Glutamate-Ammonia Ligase; Glutamates; Glutamic Acid; Hepatic Veins; Kinetics; Liver; Male; Mitochondria, Liver; Portal Vein; Rats; Rats, Inbred Strains; Urea | 1987 |
Gut-liver interaction in glutamine homeostasis: portal ammonia role in uptake and metabolism.
Topics: Acid-Base Equilibrium; Alanine; Ammonia; Animals; Carbonates; Citrulline; Digestive System Physiological Phenomena; Glutamates; Glutamic Acid; Glutamine; Homeostasis; Liver; Male; Mitochondria, Liver; Portal Vein; Rats; Rats, Inbred Strains | 1987 |
Potential for the prenatal diagnosis of hyperornithinemia, hyperammonemia, and homocitrullinuria syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Chorionic Villi Sampling; Citrulline; Female; Humans; Ornithine; Pregnancy; Pregnancy Trimester, First; Prenatal Diagnosis | 1989 |
Biochemical and histologic pathology in an infant with cross-reacting material (negative) pyruvate carboxylase deficiency.
Topics: Acidosis; Amino Acids; Ammonia; Biopsy; Citrulline; Cross Reactions; Glutamine; Humans; Infant, Newborn; Lactates; Liver; Liver Function Tests; Lysine; Male; Pyruvate Carboxylase Deficiency Disease | 1986 |
A new patient with hyperornithinaemia, hyperammonaemia and homocitrullinuria treated early with low protein diet.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Citrulline; Dietary Proteins; Glutamine; Humans; Infant; Male; Ornithine; Pyrimidines | 1986 |
Carboxypeptidase activity in human mycoplasmas.
Topics: Adenosine Triphosphate; Ammonia; Arginine; Carboxypeptidases; Citrulline; Humans; Lysine Carboxypeptidase; Mycoplasma; Mycoplasma pneumoniae | 1986 |
A new family affected by the syndrome of hyperornithinaemia, hyperammonaemia and homocitrullinuria.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Citrulline; Female; Humans; Male; Ornithine; Syndrome | 1987 |
Inhibitory effect of intravenous lysine infusion on urea cycle metabolism.
Topics: Adolescent; Amino Acids; Ammonia; Child; Citric Acid Cycle; Citrulline; Depression, Chemical; Female; Humans; Infusions, Intravenous; Lysine; Male; Orotic Acid; Putrescine; Urea | 1987 |
Hyperornithinemia-hyperammonemia-homocitrullinuria syndrome: low creatine excretion and effect of citrulline, arginine, or ornithine supplement.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Child, Preschool; Citrulline; Creatine; Female; Humans; Lysine; Male; Ornithine; Orotic Acid; Syndrome | 1987 |
Lethal hyperammonaemic coma due to ornithine transcarbamylase deficiency presenting as brain stem encephalitis in a previously asymptomatic ten-year-old boy.
Topics: Ammonia; Brain Stem; Child; Citrulline; Coma; Diagnosis, Differential; Encephalitis; Humans; Male; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid | 1987 |
Ornithine transcarbamylase variant in a male patient.
Topics: Amino Acids; Ammonia; Citrulline; Dietary Proteins; Genetic Variation; Humans; Hydrogen-Ion Concentration; Infant; Liver; Male; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid | 1987 |
Lethal ornithine transcarbamylase deficiency in a female neonate.
Topics: Ammonia; Arginine; Citrulline; Coma; Female; Humans; Infant, Newborn; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Peritoneal Dialysis; Stevens-Johnson Syndrome | 1987 |
Abnormality of citrulline synthesis in liver mitochondria from patients with hyperornithinaemia, hyperammonaemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Humans; Kinetics; Mitochondria, Liver; Ornithine | 1987 |
Inhibition of bovine liver lysine-ketoglutarate reductase by urea cycle metabolites and saccharopine.
Topics: Ammonia; Animals; Cattle; Citrulline; Humans; Lysine; Mitochondria, Liver; Oxidoreductases Acting on CH-NH Group Donors; Rats; Saccharopine Dehydrogenases; Species Specificity | 1987 |
[A case of combined lysinuric protein intolerance and hypoactivity of argininosuccinate synthetase (citrullinemia)].
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Ammonium Chloride; Citrulline; Female; Humans; Lysine; Renal Tubular Transport, Inborn Errors | 1988 |
Serum arginine level in neonatal citrullinaemia.
Topics: Ammonia; Arginine; Citrulline; Humans; Infant, Newborn | 1988 |
[Protein intolerance with lysinuria. Value of orotic aciduria in adjusting treatment with citrulline].
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Amino Acids; Amino Acids, Diamino; Ammonia; Biological Transport; Cell Membrane; Citrulline; Consanguinity; Dietary Proteins; Humans; Lysine; Male; Orotic Acid; Osteoporosis | 1988 |
Porcine intestinal ammonia liberation. Influence of food intake, lactulose and neomycin treatment.
Topics: Alanine; Amino Acids; Ammonia; Animals; Blood Flow Velocity; Citrulline; Disaccharides; Eating; Female; Glutamates; Glutamine; Intestinal Mucosa; Lactulose; Neomycin; Swine; Urea | 1988 |
[Hyperornithinemia, hyperammonemia and homocitrullinuria due to a defect of mitochondrial membrane transport].
Topics: Amino Acids; Ammonia; Biological Transport; Cells, Cultured; Citrulline; Fibroblasts; Humans; Mitochondria, Liver; Ornithine; Skin | 1988 |
Biochemical analysis of decreased ornithine transport activity in the liver mitochondria from patients with hyperornithinemia, hyperammonemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Biological Transport; Citrulline; Humans; Kinetics; Mitochondria, Liver; Ornithine | 1988 |
Rat metabolic adaptation to ammonia inhalation.
Topics: Absorption; Administration, Inhalation; Ammonia; Animals; Blood Urea Nitrogen; Brain Chemistry; Citrulline; Female; Hydrogen-Ion Concentration; Liver; Lung; Rats; Rats, Inbred Strains | 1988 |
[Anesthesia for a patient with the hyperornithinemia-hyperammonemia-homocitrullinuria (HHH) syndrome].
Topics: Adult; Ammonia; Anesthesia; Citrulline; Humans; Male; Ornithine; Syndrome | 1988 |
Effect of sodium benzoate and sodium phenylacetate on brain serotonin turnover in the ornithine transcarbamylase-deficient sparse-fur mouse.
Topics: Administration, Oral; Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Benzoates; Benzoic Acid; Brain; Child; Citrulline; Humans; Injections, Intraperitoneal; Male; Mice; Mice, Mutant Strains; Ornithine Carbamoyltransferase Deficiency Disease; Phenylacetates; Serotonin | 1988 |
Clinical, biochemical and ultrastructural study on the pathogenesis of hyperornithinemia-hyperammonemia-homocitrullinuria syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Brain; Child; Citrulline; Endoplasmic Reticulum; Humans; Liver Glycogen; Male; Mitochondria, Liver; Ornithine; Tomography, X-Ray Computed | 1988 |
Citrulline accumulation in mice induced by administration of L-hydrazinosuccinate.
Topics: Amino Acids; Ammonia; Animals; Aspartate Aminotransferases; Aspartic Acid; Citrulline; Corticosterone; Hydrazines; Liver; Male; Mice; Succinates | 1988 |
Possible pathogenetic mechanism in hyperornithinemia, hyperammonemia, and homocitrullinuria syndrome.
Topics: Ammonia; Citrulline; Growth Disorders; Humans; Intellectual Disability; Liver; Lymphocytes; Mitochondria; Ornithine; Syndrome | 1987 |
[Hyperornithinemia, hyperammonemia and homocitrullinuria syndrome in a family].
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Electroencephalography; Humans; Male; Mitochondria; Ornithine; Syndrome | 1987 |
The hyperornithinemia, hyperammonemia, homocitrullinuria syndrome: an ornithine transport defect remediable with ornithine supplements.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Citrulline; Dietary Proteins; Fibroblasts; Humans; In Vitro Techniques; Male; Mitochondria; Ornithine; Oxidation-Reduction; Syndrome | 1987 |
Hyperornithinemia, hyperammonemia, and homocitrullinuria: case report and biochemical study.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Citrulline; Fibroblasts; Humans; Liver; Male; Ornithine; Reference Values; Skin | 1987 |
[Changes in the electroencephalogram, cerebral visual evoked potential and plasma NH3 levels in adult type citrullinemia].
Topics: Adult; Ammonia; Citrulline; Electroencephalography; Evoked Potentials, Visual; Humans; Male; Telencephalon | 1986 |
[H-H-H syndrome: a rare disease also relevant in anesthesiology].
Topics: Adolescent; Ammonia; Anesthesia, General; Citrulline; Femoral Fractures; Fracture Fixation, Internal; Humans; Male; Ornithine; Postoperative Complications; Syndrome; Wound Healing | 1986 |
Support of respiration and citrulline synthesis by isolated hepatic mitochondria from Squalus acanthias by acyl-CoAs and other nitrogen-donating substrates.
Topics: Acyl Coenzyme A; Amino Acids; Ammonia; Animals; Bicarbonates; Citrulline; Dogfish; Glutamine; Kinetics; Mitochondria, Liver; Ornithine; Oxygen Consumption; Sharks | 1986 |
Studies on a case of HHH-syndrome (hyperammonemia, hyperornithinemia, homocitrullinuria).
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Biological Transport; Child, Preschool; Citrulline; Fibroblasts; Follow-Up Studies; Humans; Kinetics; Male; Ornithine; Psychomotor Disorders; Seizures; Syndrome | 1986 |
Metabolic role of urea cycle intermediates: nutritional and clinical aspects. Introduction.
Topics: Ammonia; Animals; Arginine; Body Weight; Citrulline; Intestine, Small; Kidney; Liver; Nutritional Physiological Phenomena; Ornithine; Proline; Rats; Urea | 1985 |
The EEGs of infants with citrullinemia.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Electroencephalography; Female; Humans; Infant, Newborn | 1985 |
The apparent Km of ammonia for carbamoyl phosphate synthetase (ammonia) in situ.
Topics: Ammonia; Animals; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Hydrogen-Ion Concentration; Kinetics; Ligases; Male; Mitochondria, Liver; Rats; Rats, Inbred Strains | 1985 |
Channeling of ammonia from glutaminase to carbamoyl-phosphate synthetase in liver mitochondria.
Topics: Ammonia; Animals; Carbamoyl-Phosphate Synthase (Glutamine-Hydrolyzing); Citrulline; Glutamine; Ligases; Male; Mitochondria, Liver; Rats; Rats, Inbred Strains; Succinates; Succinic Acid | 1985 |
Ornithine loading did not prevent induced hyperammonemia in a patient with hyperornithinemia-hyperammonemia-homocitrullinuria syndrome.
Topics: Alanine; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Child; Citrulline; Cytoplasm; Humans; Male; Ornithine; Orotic Acid; Syndrome | 1985 |
Biochemical aspects of metamorphosis: a study of the isolation of intact frog-liver mitochondria.
Topics: Adenosine Triphosphatases; Ammonia; Animals; Anura; Cell Differentiation; Citrulline; Glutamates; Liver; Metamorphosis, Biological; Mitochondria, Liver; Ornithine; Oxygen Consumption | 1971 |
Argininosuccinicaciduria: clinical, metabolic and dietary study.
Topics: Affective Symptoms; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginase; Arginine; Ataxia; Child; Citrulline; Dietary Proteins; Electroencephalography; Epilepsy; Female; Humans; Intellectual Disability; Intelligence Tests; Male; Ornithine; Phenobarbital; Seizures; Succinates; Tremor | 1974 |
Role of fatty acids in regulation of phosphoenolpyruvate and citrulline synthesis in rabbit liver mitochondria.
Topics: Acetates; Adenosine Triphosphate; Ammonia; Animals; Caprylates; Carnitine; Citrulline; Cyanides; Fatty Acids, Nonesterified; Glutamates; Hydrazones; Hydroxylamines; Male; Mitochondria, Liver; Oleic Acids; Oligomycins; Phosphoenolpyruvate; Rabbits; Rotenone | 1974 |
[Amino acid levels in the blood serum of patients with chronic colitis].
Topics: Adult; Alanine; Amino Acids; Ammonia; Arginine; Aspartic Acid; Betaine; Chronic Disease; Citrulline; Colitis; Glutamates; Glutamine; Glycine; Histidine; Humans; Middle Aged; Ornithine; Phenylalanine; Proline; Serine; Taurine; Threonine; Tryptophan; Tyrosine; Urea | 1974 |
[Biochemical stigmas of human skin surface in old age (author's transl)].
Topics: Adult; Aged; Aging; Alanine; Amino Acids; Ammonia; Citrulline; Glutamates; Glycine; Histidine; Humans; Lactates; Pyrrolidonecarboxylic Acid; Skin; Surface Properties; Sweating; Threonine; Urea; Valine | 1974 |
A concerted response of the enzymes of urea biosynthesis during thyroxine-induced metamorphosis of Rana catesbeiana.
Topics: Adenosine Triphosphate; Ammonia; Animals; Anura; Arginase; Arginine; Aspartic Acid; Carbon Dioxide; Citrulline; Larva; Ligases; Liver; Lyases; Metamorphosis, Biological; Mitochondria, Liver; Organ Size; Ornithine; Ornithine Carbamoyltransferase; Phosphotransferases; Rana catesbeiana; Subcellular Fractions; Succinates; Thyroxine; Urea | 1972 |
[Experimental study of synergism and antagonism between the amino acids of the Krebs-Henseleit cycle].
Topics: Amino Acids; Ammonia; Animals; Arginine; Citric Acid Cycle; Citrulline; Drug Antagonism; Drug Interactions; Drug Synergism; Female; Male; Mice; Ornithine; Poisoning | 1972 |
[Mechanism of intrahepatic accumulation of dicarboxylic amino acids during ammonia poisoning].
Topics: Alanine; Amino Acids; Ammonia; Animals; Arginine; Aspartic Acid; Citrates; Citrulline; Dicarboxylic Acids; Glutamates; Glutaminase; Glutamine; Liver; Malates; Ornithine; Pyruvates; Rats; Seizures; Urea | 1972 |
Transport of ornithine and citrulline across the mitochondrial membrane.
Topics: Ammonia; Animals; Biological Transport, Active; Carbamates; Carbon Isotopes; Citrulline; Electron Transport; In Vitro Techniques; Membrane Potentials; Mitochondria; Mitochondria, Liver; Mitochondria, Muscle; Mitochondrial Swelling; Myocardium; Oligomycins; Organ Specificity; Ornithine; Ornithine Carbamoyltransferase; Osmosis; Oxygen Consumption; Phosphotransferases; Rats; Uncoupling Agents; Valinomycin | 1973 |
Psychomotor retardation, epileptic and stuporous attacks, irritability and ataxia associated with ammonia intoxication, high blood ornithine levels and increased homocitruline in the urine.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Ataxia; Citrulline; Epilepsy; Female; Humans; Ornithine; Paralysis; Psychomotor Disorders | 1973 |
Urea metabolism in an estivating terrestrial snail Bulimulus dealbatus.
Topics: Adaptation, Physiological; Ammonia; Animals; Arginase; Arginine; Bicarbonates; Carbon Dioxide; Carbon Isotopes; Citrulline; Estivation; Ornithine Carbamoyltransferase; Phosphotransferases; Snails; Urea; Urease | 1973 |
[Argininosuccinic aciduria with and without hyperammoniemia. Study of 2 cases].
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Child; Child Behavior Disorders; Child, Preschool; Chromosome Aberrations; Citrulline; Dietary Proteins; Electrocardiography; Electroencephalography; Hepatomegaly; Humans; Intellectual Disability; Male; Movement Disorders; Seizures; Speech Disorders | 1973 |
Crayfish ventral nerve cord and hemolymph: content of free amino acids and other metabolites.
Topics: Amino Acids; Aminobutyrates; Ammonia; Animals; Asparagine; Astacoidea; Chromatography, Ion Exchange; Citrulline; Female; Glucose; Glutamates; Glutamine; Hemolymph; In Vitro Techniques; Male; Neurons; Sex Factors; Tryptophan; Urea | 1973 |
Effect of L-leucine on the nitrogen metabolism of isolated rat liver mitochondria.
Topics: Ammonia; Ammonium Chloride; Animals; Biological Transport; Carbon Isotopes; Citrulline; Enzyme Activation; Glutamate Dehydrogenase; Isoleucine; Ketoglutaric Acids; Kinetics; Leucine; Membranes; Mitochondria; Mitochondria, Liver; Rats; Spectrophotometry, Ultraviolet; Time Factors | 1973 |
Competition for energy between phosphoenolpyruvate and citrulline synthesis in guinea-pig liver mitochondria.
Topics: Acetates; Ammonia; Animals; Aspartate Aminotransferases; Citrulline; Energy Transfer; Glucosephosphates; Glutamates; Guinea Pigs; Hydrazones; Hydrocarbons, Fluorinated; Hydroxylamines; Kinetics; Mitochondria, Liver; Nitriles; Oligomycins; Oxidative Phosphorylation; Phosphoenolpyruvate; Phosphoenolpyruvate Carboxykinase (GTP); Uncoupling Agents | 1973 |
Variants of citrullinaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Brain; Chromatography; Citrulline; Dyspnea; Edema; Electrophoresis; Humans; Infant, Newborn; Infant, Newborn, Diseases; Liver; Lung; Male; Microscopy, Electron; Spasm; Urea | 1973 |
Renal metabolism of amino acids and ammonia in fed and fasted pregnant sheep.
Topics: Acidosis; Alanine; Amino Acids; Ammonia; Animals; Arginine; Aspartic Acid; Catheterization; Citrulline; Fasting; Female; Glutamates; Glutamine; Glycine; Hypoglycemia; Kidney; Pregnancy; Pregnancy, Animal; Regional Blood Flow; Renal Artery; Serine; Sheep | 1974 |
Ornithinemia, hyperammonemia, and homocitrullinuria. A disease associated with mental retardation and possibly caused by defective mitochondrial transport.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Dietary Proteins; Female; Humans; Intellectual Disability; Lysine; Mitochondria; Ornithine; Ornithine Carbamoyltransferase; Proline; Transaminases | 1974 |
Citrullinemia: investigation and treatment over a four-year period.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Arginine; Child, Preschool; Citrulline; Dietary Proteins; Dipeptides; Female; Fibroblasts; Follow-Up Studies; Guanidines; Humans; Infant; Infant, Newborn; Orotic Acid; Peptide Synthases; Urea; Uric Acid | 1974 |
Hyperammonaemia in 20 families. Biochemical and genetical survey, including investigations in 3 new families.
Topics: Alanine; Ammonia; Arginine; Child, Preschool; Citrulline; Female; Genes, Dominant; Genetic Linkage; Glutamates; Glutamine; Glycine; Humans; Leucine; Liver; Lysine; Male; Metabolism, Inborn Errors; Ornithine; Ornithine Carbamoyltransferase; Sex Chromosomes | 1974 |
Severe neonatal citrullinaemia.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Arginine; Citrulline; Dietary Carbohydrates; Dietary Proteins; Glucose; Humans; Infant Nutritional Physiological Phenomena; Infant, Newborn; Infant, Newborn, Diseases; Male; Seizures; Urea | 1974 |
Letter: Citrulline for Reye's syndrome.
Topics: Ammonia; Brain Diseases; Citrulline; Fatty Liver; Reye Syndrome | 1974 |
Initial steps in pyrimidine synthesis in Ehrlich ascites carcinoma in vitro. II. The synthesis of carbamyl phosphate by a soluble, glutamine-dependent carbamyl phosphate synthetase.
Topics: Adenosine Triphosphate; Ammonia; Ammonium Chloride; Animals; Bicarbonates; Carbon Isotopes; Carcinoma, Ehrlich Tumor; Citrulline; Enterococcus faecalis; Glutamine; In Vitro Techniques; Magnesium; Ornithine; Ornithine Carbamoyltransferase; Phosphotransferases; Pyrimidines; Streptococcus; Time Factors | 1967 |
Neurologic disorders and liver disease.
Topics: Adipose Tissue; Ammonia; Brain Diseases; Citrulline; Fatty Liver; Galactosemias; Hepatic Encephalopathy; Hepatitis; Hepatolenticular Degeneration; Humans; Hyperbilirubinemia, Hereditary; Kidney Diseases; Liver; Liver Diseases; Metabolism, Inborn Errors; Mucopolysaccharidoses; Nervous System Diseases; Neurologic Manifestations; Paraplegia; Phenylketonurias; Quadriplegia; Urea | 1971 |
Early dietary management in an infant with argininosuccinase deficiency: preliminary report.
Topics: Ammonia; Arginine; Blood Urea Nitrogen; Child Development; Child, Preschool; Citrulline; Diet Therapy; Dietary Proteins; Female; Growth; Humans; Infant; Lyases; Metabolism, Inborn Errors; Succinates | 1972 |
Nitrogen metabolism of the South American lungfish Lepidosiren paradoxa.
Topics: Acetates; Ammonia; Animals; Arginine; Aspartic Acid; Bicarbonates; Carbon Isotopes; Citrulline; Climate; Fasting; Fishes; Glutamates; Guanidines; Leucine; Liver; Manganese; Ornithine; Serine; Stereoisomerism; Urea | 1972 |
Citrullinemia: a new case, with implications concerning adaptation to defective urea synthesis.
Topics: Adult; Amino Acids; Ammonia; Citrulline; Dietary Proteins; Fibroblasts; Humans; Intellectual Disability; Ligases; Lysine; Male; Metabolism, Inborn Errors; Urea | 1972 |
[Activity of liver argininosuccinate synthetase in chronic hepatic disease].
Topics: Ammonia; Animals; Arginine; Chronic Disease; Citrulline; Hepatitis; Hypoxanthines; Ligases; Liver Cirrhosis; Liver Diseases; Lung; Rabbits; Succinates | 1972 |
The effect of vitamin C depletion on the free amino acid content in blood plasma of the guinea pig.
Topics: Alanine; Amino Acids; Ammonia; Animals; Arginine; Ascorbic Acid Deficiency; Aspartic Acid; Citrulline; Cysteine; Glutamates; Glycine; Guinea Pigs; Histidine; Isoleucine; Lysine; Male; Methionine; Ornithine; Phenylalanine; Proline; Serine; Threonine; Time Factors; Tyrosine; Valine | 1971 |
Metabolism of bovine semen. XX. Role of ammonia in interactions between the citric acid and urea cycles.
Topics: Amino Acids; Ammonia; Animals; Arginase; Arginine; Carbamates; Carbon Dioxide; Carbon Isotopes; Cattle; Cell Fractionation; Citric Acid Cycle; Citrulline; Male; Ornithine; Ornithine Carbamoyltransferase; Oxygen Consumption; Phosphotransferases; Proline; Pyruvates; Rabbits; Semen; Spermatozoa; Urea; Valerates | 1969 |
Ornithine-ketoacid transaminase activity in human skin and amniotic fluid cell culture.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Amniotic Fluid; Biopsy; Cell Line; Citrulline; Culture Techniques; Humans; Keto Acids; Ornithine; Skin; Transaminases | 1970 |
[Simple and quick technic of determination of ornithine-carbamoyl transferase in the serum. Value and limitations].
Topics: Adolescent; Adult; Ammonia; Arsenic; Child; Child, Preschool; Citrulline; Female; Humans; Indicators and Reagents; Infant; Liver; Liver Function Tests; Male; Methods; Ornithine Carbamoyltransferase | 1970 |
[The use of a detoxicant drug in the treatment of alcoholic toxicosis].
Topics: Adult; Alcoholic Intoxication; Alcoholism; Ammonia; Arginine; Citrulline; Female; Humans; Liver Function Tests; Male; Middle Aged; Nitrogen; Ornithine; Psychoses, Alcoholic; Transaminases | 1970 |
Ultraviolet-absorbing components of urine from mentally retarded children. 3.
Topics: Adolescent; Adult; Ammonia; Autistic Disorder; Central Nervous System Diseases; Child; Child, Preschool; Chromatography, Ion Exchange; Chromatography, Paper; Citrulline; Creatinine; Dialysis; Humans; Hypnotics and Sedatives; Intellectual Disability; Male; Nephrectomy; Orotic Acid; RNA, Messenger; Sleep; Tranquilizing Agents; Ultraviolet Rays | 1970 |
[Changes in carbohydrate and amino acid metabolism in dog brain in experimental alloxan diabetes. 2].
Topics: Ammonia; Animals; Arteries; Aspartic Acid; Blood Glucose; Citrulline; Diabetes Mellitus, Experimental; Dogs; Glutamates; Glutamine; Glutathione; Ketoglutaric Acids; Male; Pyruvates; Urea; Veins | 1970 |
Control of pyrimidine biosynthesis in mammalian tissues. II. Glutamine-utilizing carbamoyl phosphate synthetase of various experimental tumors: distribution, purification and characterization.
Topics: Adenosine Triphosphate; Ammonia; Animals; Antigen-Antibody Reactions; Apatites; Carbamates; Carbon Isotopes; Carcinoma 256, Walker; Carcinoma, Ehrlich Tumor; Cattle; Centrifugation, Density Gradient; Chemical Phenomena; Chemistry; Chromatography; Citrulline; Quaternary Ammonium Compounds | 1970 |
[Citrullinemia].
Topics: Alanine; Amino Acid Metabolism, Inborn Errors; Ammonia; Autopsy; Chromatography; Citrulline; Humans; Infant; Lysine; Male; Urea | 1971 |
Metabolism of basic amino acids in Pseudomonas putida. Intermediates in L-arginine catabolism.
Topics: Amides; Aminobutyrates; Ammonia; Arginine; Butyrates; Canavanine; Carbon Isotopes; Chemical Phenomena; Chemistry; Chromatography, Paper; Chromatography, Thin Layer; Citrulline; Computers; Drug Stability; Electrophoresis; Enzyme Induction; Guanidines; Hot Temperature; Hydrogen-Ion Concentration; Keto Acids; Kinetics; Malates; Paper; Pseudomonas; Tritium; Urea | 1971 |
[Free amino acids and other ninhydrin-positive substances in the normal horny layer and in psoriasis scales].
Topics: Alanine; Amino Acids; Ammonia; Asparagine; Chromatography; Citrulline; Cysteine; Glycine; Histidine; Humans; Imidazoles; Phenylalanine; Proline; Psoriasis; Serine; Skin; Taurine; Threonine; Urea | 1967 |
A glutamine-dependent enzyme for the synthesis of carbamyl phosphate for pyrimidine biosynthesis in fetal rat liver.
Topics: Adenosine Triphosphate; Ammonia; Ammonium Chloride; Animals; Animals, Newborn; Bicarbonates; Carbon Isotopes; Carcinoma, Ehrlich Tumor; Chickens; Citrulline; Columbidae; Fetus; Gestational Age; Glutamine; Hydrogen-Ion Concentration; In Vitro Techniques; Liver; Liver Extracts; Magnesium; Mitochondria, Liver; Organ Size; Ornithine Carbamoyltransferase; Phosphotransferases; Proteins; Pyrimidines; Rats; Transferases | 1967 |
A further simplified method of ornithine carbomoyltransferase measurement.
Topics: Ammonia; Arsenic; Chemical Phenomena; Chemistry; Citrulline; Colorimetry; Humans; Hydrogen-Ion Concentration; Indicators and Reagents; Liver Diseases; Liver Function Tests; Methods; Ornithine Carbamoyltransferase | 1968 |
[Hereditary anomalies of the urea cycle].
Topics: Ammonia; Arginine; Citrulline; Humans; Ligases; Lyases; Metabolism, Inborn Errors; Ornithine Carbamoyltransferase; Phosphotransferases; Succinates; Urea | 1968 |
Metabolism of ammonia. I. Biochemical aspect of ammonia intoxication.
Topics: Ammonia; Animals; Arginine; Ascorbic Acid; Autoradiography; Bicarbonates; Blood-Brain Barrier; Carbon Isotopes; Chickens; Citrulline; Hydrogen-Ion Concentration; Injections, Intraperitoneal; Male; Mice; Ornithine; Phosphates; Poisoning; Rats; Sulfates; Time Factors | 1968 |
A study of ammonia and urea production and excretion in the fresh-water-adapted form of the Pacific lempry, Entosphenus tridentatus.
Topics: Ammonia; Animals; Arginase; Biological Evolution; Carbamates; Citrulline; Fishes; Gills; Hydrogen-Ion Concentration; Kidney; Kinetics; Liver; Manganese; Ornithine; Phosphotransferases; Seawater; Urea | 1968 |
[Therapy of hyperammoniemia].
Topics: Adenosine Triphosphate; Ammonia; Anti-Bacterial Agents; Arginine; Aspartic Acid; Citrulline; Dietary Proteins; Hepatic Encephalopathy; Humans; Intestines; Malates; Ornithine | 1969 |
Glutamate oxidation in rat-liver homogenate.
Topics: Adenine Nucleotides; Ammonia; Animals; Arginine; Aspartic Acid; Citrulline; Glutamates; Glutaminase; Glutamine; Kinetics; Liver; Nitrogen; Rats; Urea; Urease | 1969 |
Hyperornithinemia, hyperammonemia, and homocitrullinuria. A new disorder of amino acid metabolism associated with myoclonic seizures and mental retardation.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Ataxia; Child, Preschool; Citrulline; Diet Therapy; Humans; Intellectual Disability; Lysine; Male; Myoclonus; Ornithine; Ornithine Carbamoyltransferase; Seizures | 1969 |
[Metabolism of ammonia. 3. Effect in vitro of arginine on the physiological activity of the urea cycle enzymes during ammonia poisoning].
Topics: Ammonia; Animals; Arginase; Arginine; Citrulline; Epinephrine; Hormones; In Vitro Techniques; Ligases; Liver; Norepinephrine; Ornithine; Rats; Transferases; Urea | 1969 |
[Treatment of a consciousness disorder seizure specific to hepato-encephalopathy (Inose type)--trial use of gamma-hydroxy-beta-aminobutyric acid].
Topics: Adult; Aminobutyrates; Ammonia; Brain Diseases; Citrulline; Coma; Electroencephalography; Female; Humans; Hydroxybutyrates; Injections, Intravenous; Liver Cirrhosis; Liver Diseases; Liver Function Tests; Unconsciousness | 1969 |
Argininosuccinic aciduria: clinical, biochemical, anatomical and neuropathological observations.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Arginine; Aspartic Acid; Brain; Cerebellum; Citrulline; Female; Humans; Infant; Intellectual Disability; Liver; Lyases; Myelin Sheath; Neuroglia; Succinates | 1969 |
Studies on amino acid metabolism in citrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Blood Chemical Analysis; Caseins; Child; Citrulline; Diet Therapy; Humans; Infant; Intellectual Disability; Ligases; Male; Neomycin; Urea | 1967 |
Citrullinemia. A preliminary case report.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Blood Chemical Analysis; Citrulline; Diet Therapy; Female; Humans; Infant; Ligases; Pyridoxine; Triiodothyronine; Urea | 1967 |
Argininosuccinic aciduria. Report of two new cases and demonstration of intermittent elevation of blood ammonia.
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Arginine; Chromatography, Paper; Citrulline; Electroencephalography; Electrophoresis; Female; Humans; Intellectual Disability; Male; Microchemistry; Succinates | 1967 |
Simple method for determination of ornithine transcarbamylase activity in serum.
Topics: Ammonia; Arsenic; Citrulline; Humans; Indophenol; Infrared Rays; Liver Diseases; Methods; Ornithine Carbamoyltransferase; Spectrum Analysis; Statistics as Topic | 1967 |
Treatment of adult-type citrullinemia with administration of citrate.
Topics: Amino Acids; Ammonia; Circadian Rhythm; Citrates; Citric Acid; Citrulline; Glutamates; Glutamic Acid; Humans; Lactulose; Male; Middle Aged; Urea | 1981 |
Reduced ornithine catabolism in cultured fibroblasts and phytohaemagglutinin-stimulated lymphocytes from a patient with hyperornithinaemia, hyperammonaemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Aspartate Ammonia-Lyase; Cells, Cultured; Citrulline; Fibroblasts; Glutamates; Glutamic Acid; Humans; Lymphocyte Activation; Lymphocytes; Ornithine; Phytohemagglutinins; Proline | 1982 |
Regulation of the n-acetylglutamate content of rat hepatocytes by the glutamate concentration.
Topics: Ammonia; Animals; Aspartic Acid; Citrulline; Diet; Glutamates; Glutamic Acid; Liver; Ornithine; Rats; Urea | 1982 |
Glutamine-dependent synthesis of citrulline by isolated hepatic mitochondria from Squalus acanthias.
Topics: Ammonia; Ammonium Chloride; Animals; Citrulline; Dogfish; Glutamates; Glutamic Acid; Glutamine; Isoxazoles; Methionine Sulfoximine; Mitochondria, Liver | 1984 |
The mechanism of hyperammonaemia and hyperornithinaemia in the syndrome of hyperornithinaemia, hyperammonaemia with homocitrullinuria.
Topics: Ammonia; Citrulline; Fibroblasts; Humans; Liver; Male; Middle Aged; Mitochondria, Liver; Ornithine; Syndrome | 1983 |
Studies on the pathway from ornithine to proline in cultured skin fibroblasts with reference to the defect in hyperornithinaemia with hyperammonaemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Biological Transport; Cells, Cultured; Citrulline; Fibroblasts; Glutamine; Humans; Mitochondria; Ornithine; Proline; Proteins | 1983 |
The pH of mitochondria of fibroblasts from a hyperornithinaemia, hyperammonaemia, homocitrullinuria-syndrome patient.
Topics: Acid-Base Equilibrium; Ammonia; Citrulline; Cytosol; Fibroblasts; Humans; Hydrogen-Ion Concentration; Mitochondria; Ornithine; Syndrome | 1984 |
Acute neonatal citrullinaemia.
Topics: Ammonia; Argininosuccinate Synthase; Brain Stem; Citrulline; Fibroblasts; Humans; Infant, Newborn; Lactates; Lactic Acid; Ligases; Male; Phenylalanine | 1984 |
Ultrastructural changes in fibroblast mitochondria of a patient with HHH-syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Fibroblasts; Genes, Recessive; Humans; Intracellular Membranes; Microscopy, Electron; Mitochondria; Ornithine; Skin | 1984 |
Mechanism of arginine protection against ammonia intoxication in the rat.
Topics: Acetyltransferases; Amino-Acid N-Acetyltransferase; Ammonia; Animals; Arginine; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Male; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Rats; Rats, Inbred Strains; Urea | 1984 |
Treatment of congenital hyperammonemias.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Humans; Metabolism, Inborn Errors; Nitrogen; Serotonin; Urea | 1984 |
Papilloedema in late-onset citrullinaemia: report of second case.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Angiography; Argininosuccinate Synthase; Citrulline; Humans; Liver; Male; Papilledema; Tomography, X-Ray Computed | 1984 |
Hyperammonemia.
Topics: Acetyltransferases; Amino Acid Metabolism, Inborn Errors; Amino-Acid N-Acetyltransferase; Ammonia; Arginine; Argininosuccinate Synthase; Argininosuccinic Aciduria; Brain Edema; Carbamoyl-Phosphate Synthase (Ammonia); Child, Preschool; Citrulline; Diagnosis, Differential; Female; Humans; Hyperargininemia; Infant; Infant, Newborn; Leucine; Ornithine Carbamoyltransferase; Respiratory Distress Syndrome, Newborn; Urea | 1984 |
[A case of adult-type citrullinemia].
Topics: Adult; Amino Acids; Ammonia; Citrulline; Hepatic Encephalopathy; Humans; Male | 1984 |
Synergistic action of ultraviolet radiation and hydrogen peroxide on citrulline.
Topics: Amino Acids; Ammonia; Citrulline; Hydrogen Peroxide; Kinetics; Ultraviolet Rays; Urea | 1984 |
Gamma-glutamylornithine excretion in patients with hyperornithinemia.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Atrophy; Choroid; Chromatography; Citrulline; Dipeptides; Humans; Ornithine; Retina; Retinal Diseases; Syndrome; Uveal Diseases | 1984 |
A case of transient neonatal citrullinemia.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Diagnosis, Differential; Dietary Proteins; Humans; Infant; Infant, Newborn; Male | 1983 |
Urea cycle function in the dog with emphasis on the role of arginine.
Topics: Age Factors; Ammonia; Animals; Arginine; Blood Glucose; Citrulline; Dogs; Ornithine; Orotic Acid; Urea; Vomiting | 1984 |
Reconstitution of ornithine transport in liposomes with Lubrol extracts of mitochondria.
Topics: Amino Acid Transport Systems, Basic; Ammonia; Animals; Biological Transport, Active; Carrier Proteins; Cattle; Citrulline; Kinetics; Liposomes; Membrane Transport Proteins; Mitochondria, Liver; Ornithine; Polyethylene Glycols; Solubility; Syndrome | 1984 |
Analysis of the control of citrulline synthesis in isolated rat-liver mitochondria.
Topics: Acetazolamide; Ammonia; Animals; Bicarbonates; Carbamoyl-Phosphate Synthase (Ammonia); Carbamyl Phosphate; Citrulline; Male; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase; Rats; Rats, Inbred Strains; Valine | 1984 |
Defective ornithine metabolism in the syndrome of hyperornithinaemia, hyperammonaemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Fibroblasts; Humans; Ornithine; Pyrroline Carboxylate Reductases | 1981 |
Secondary citrullinemia with hyperammonemia in four neonatal cases of pyruvate carboxylase deficiency.
Topics: Ammonia; Citrulline; Humans; Infant, Newborn; Infant, Newborn, Diseases; Pyruvate Carboxylase Deficiency Disease | 1981 |
A mechanism for valproate-induced hyperammonemia.
Topics: Ammonia; Animals; Citrulline; Glutamates; Male; Mitochondria, Liver; Oxidation-Reduction; Rats; Rats, Inbred Strains; Urea; Valproic Acid | 1982 |
Hypoglycin toxicity: studies of ammonia metabolism.
Topics: Ammonia; Animals; Citrulline; Cyclopropanes; Disease Models, Animal; Humans; Hypoglycins; Liver; Nitrogen; Plant Poisoning; Rats; Rats, Inbred Strains; Urea | 1983 |
Interactions between alpha-ketoisovalerate metabolism and the pathways of gluconeogenesis and urea synthesis in isolated hepatocytes.
Topics: Ammonia; Animals; Citrulline; Gluconeogenesis; Hemiterpenes; In Vitro Techniques; Keto Acids; Kinetics; Lactates; Lactic Acid; Liver; Male; Myocardium; Pyruvate Dehydrogenase Complex; Pyruvates; Pyruvic Acid; Rats; Rats, Inbred Strains; Swine; Urea | 1983 |
Defective ornithine metabolism in cultured skin fibroblasts from patients with the syndrome of hyperornithinemia, hyperammonemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Cells, Cultured; Citrulline; Fibroblasts; Humans; Models, Chemical; Ornithine; Proteins; Skin | 1982 |
Ammonia metabolism in Reye syndrome and the effect of citrulline.
Topics: Ammonia; Child; Citrulline; Humans; Male; Metabolic Clearance Rate; Nitrogen; Reye Syndrome; Urea | 1982 |
Treatment of inborn errors of urea synthesis: activation of alternative pathways of waste nitrogen synthesis and excretion.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Essential; Ammonia; Arginine; Argininosuccinate Synthase; Argininosuccinic Aciduria; Benzoates; Benzoic Acid; Carbamoyl-Phosphate Synthase (Ammonia); Child, Preschool; Citrulline; Coma; Female; Humans; Infant; Infant, Newborn; Infusions, Parenteral; Male; Nitrogen; Ornithine Carbamoyltransferase Deficiency Disease; Urea | 1982 |
Successful treatment of severe OTC deficiency.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Benzoates; Benzoic Acid; Citrulline; Humans; Infant, Newborn; Male; Ornithine Carbamoyltransferase Deficiency Disease | 1982 |
Transient hyperammonemias in infants with and without organic acidemia.
Topics: Acetyltransferases; Amino Acid Metabolism, Inborn Errors; Amino-Acid N-Acetyltransferase; Ammonia; Arginine; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Humans; Infant, Newborn; Infant, Newborn, Diseases; Liver; Time Factors; Urea | 1982 |
Ammonia metabolism in dogs with portacaval shunts.
Topics: Ammonia; Animals; Arginine; Body Weight; Citrulline; Dogs; Female; Liver; Nitrogen; Organ Size; Orotic Acid; Portacaval Shunt, Surgical; Urea | 1982 |
Urea cycle regulation: I. Coupling of ornithine metabolism to mitochondrial oxidative phosphorylation.
Topics: Adenosine Triphosphate; Ammonia; Animals; Citric Acid Cycle; Citrulline; Glutamate Dehydrogenase; Ketoglutaric Acids; Mitochondria, Liver; Ornithine; Ornithine-Oxo-Acid Transaminase; Oxidative Phosphorylation; Rats; Reye Syndrome; Urea | 1980 |
[Hyperammonemic syndrome caused by abnormal urea cycle and its management].
Topics: Adolescent; Adult; Ammonia; Circadian Rhythm; Citrulline; Humans; Male; Middle Aged | 1982 |
Diurnal fluctuation of blood ammonia levels in adult-type citrullinemia.
Topics: Amino Acids; Ammonia; Circadian Rhythm; Citrulline; Fasting; Female; Humans; Liver Cirrhosis; Liver Diseases; Male; Middle Aged | 1982 |
Ultrastructural changes in the mitochondria in disorders in ornithine metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Humans; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease | 1980 |
Ultrastructure of hepatic mitochondria in a child with hyperornithinemia, hyperammonemia, and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Citrulline; Humans; Male; Microscopy, Electron; Mitochondria, Liver; Ornithine | 1981 |
New approaches to the diagnosis and treatment of inborn errors or urea synthesis.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinic Acid; Citrulline; Glutamine; Hippurates; Humans; Infant; Infant, Newborn; Phenylacetates; Urea | 1981 |
Carrier detection of urea cycle disorders.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinate Synthase; Citrulline; Female; Genetic Carrier Screening; Humans; Infant, Newborn; Male; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Pedigree; Pregnancy; Prenatal Diagnosis; Urea | 1981 |
Effects of arginine-free meals on ureagenesis in cats.
Topics: Acetyltransferases; Amino-Acid N-Acetyltransferase; Ammonia; Animals; Arginine; Cats; Citrulline; Food, Formulated; Kinetics; Liver; Mitochondria, Liver; Ornithine; Ornithine-Oxo-Acid Transaminase; Transaminases | 1981 |
Arginine synthesis and nitrogen excretion in the myxomycete Physarum polycephalum.
Topics: Ammonia; Arginine; Citrulline; Nitrogen; Physarum; Urea; Urease; Uric Acid | 1980 |
Origin of the ammonia found in protein-free extracts of rat-liver mitochondria and rat hepatocytes.
Topics: Ammonia; Animals; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Glutamate Dehydrogenase; Hydroxybutyrate Dehydrogenase; Liver; Lysosomes; Male; Mitochondria, Liver; Rats; Subcellular Fractions | 1980 |
Diagnostic value of orotic acid excretion in heritable disorders of the urea cycle and in hyperammonemia due to organic acidurias.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Child; Child, Preschool; Citrulline; Female; Humans; Infant; Infant, Newborn; Male; Metabolism, Inborn Errors; Middle Aged; Orotic Acid | 1980 |
Therapy of urea cycle enzymopathies: three case studies.
Topics: Ammonia; Arginine; Argininosuccinic Acid; Argininosuccinic Aciduria; Child, Preschool; Citrulline; Coma; Female; Humans; Infant; Infant, Newborn; Intellectual Disability; Lyases; Male; Ornithine Carbamoyltransferase Deficiency Disease; Urea | 1981 |
Prenatal exclusion of the HHH syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Amniotic Fluid; Cells, Cultured; Citrulline; Female; Humans; Ornithine; Pregnancy; Prenatal Diagnosis; Syndrome | 1995 |
Effects of citrulline malate on bacterial lipopolysaccharide induced endotoxemia in rats.
Topics: Ammonia; Animals; Body Temperature; Body Weight; Citrulline; Eating; Fatigue; Klebsiella pneumoniae; Lactates; Lipopolysaccharides; Male; Muscle, Skeletal; Rats; Rats, Wistar | 1995 |
[Anesthetic management for a patient with citrullinemia and liver cirrhosis].
Topics: Ammonia; Anesthesia, Spinal; Benzoates; Benzoic Acid; Citrulline; Female; Femoral Neck Fractures; Hepatic Encephalopathy; Hip Prosthesis; Humans; Liver Cirrhosis; Middle Aged; Preoperative Care | 1995 |
Intestinal glutamine and ammonia metabolism during chronic hyperammonaemia induced by liver insufficiency.
Topics: Alanine; Ammonia; Animals; Bile Ducts; Blood Flow Velocity; Body Weight; Chronic Disease; Citrulline; Diet; Glutamates; Glutamic Acid; Glutamine; Hepatic Encephalopathy; Jejunum; Ligation; Male; Neurotransmitter Agents; Portacaval Shunt, Surgical; Portal System; Rats; Rats, Wistar | 1993 |
Dietary citrulline but not ornithine counteracts dietary arginine deficiency in rats by increasing splanchnic release of citrulline.
Topics: Alanine; Amino Acids; Ammonia; Animals; Arginine; Blood Flow Velocity; Body Weight; Citrulline; Creatinine; Diet; Food; Glutamic Acid; Glutamine; Male; Ornithine; Orotic Acid; Proline; Rats; Rats, Sprague-Dawley; Splanchnic Circulation; Urea | 1994 |
Lysinuric protein intolerance. Urinary amino acid excretion at 2 and 9 days of age.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Arginine; Citrulline; Humans; Infant, Newborn; Lysine; Male; Ornithine | 1994 |
Hyperammonemia in Marasmic children.
Topics: Alanine Transaminase; Ammonia; Arginine; Aspartate Aminotransferases; Citrulline; Humans; Infant; Ornithine; Protein-Energy Malnutrition; Urea | 1994 |
Definitive cure of hyperammonemia by liver transplantation in urea cycle defects: report of three cases.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinate Synthase; Child; Citrulline; Humans; Liver Transplantation; Ornithine Carbamoyltransferase Deficiency Disease; Urea | 1994 |
Effect of single oral dose of sodium benzoate on ureagenesis in healthy men and two patients with late onset citrullinaemia.
Topics: Administration, Oral; Adult; Ammonia; Argininosuccinate Synthase; Benzoates; Benzoic Acid; Citrulline; Drug Administration Schedule; Humans; Male; Time Factors; Urea | 1993 |
Synthesis of citrulline from glutamine in pig enterocytes.
Topics: Ammonia; Animals; Carbon-Nitrogen Ligases; Citrulline; Female; Glutaminase; Glutamine; Jejunum; Ligases; Male; Ornithine; Ornithine Carbamoyltransferase; Ornithine-Oxo-Acid Transaminase; Proline; Swine | 1994 |
Generation of a mouse model for citrullinemia by targeted disruption of the argininosuccinate synthetase gene.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Animals; Argininosuccinate Synthase; Cells, Cultured; Citrulline; Disease Models, Animal; Heterozygote; Homozygote; Mice; Mice, Inbred BALB C; Mice, Mutant Strains; Plasmids; Recombination, Genetic; Stem Cells | 1994 |
Effects of glucagon on urinary excretion of urea and on plasma ammonia level in argininosuccinate synthetase deficiency.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinate Synthase; Citrulline; Female; Glucagon; Humans; Male; Urea | 1994 |
Rapid activation of hepatic glutaminase in rats fed on a single high-protein meal.
Topics: Ammonia; Animals; Citrulline; Dietary Proteins; Enzyme Activation; Glutaminase; Glutamine; Liver; Male; Mitochondria, Liver; Rats; Rats, Sprague-Dawley | 1993 |
Prospective management of a child with neonatal citrullinemia.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Argininosuccinate Synthase; Benzoates; Benzoic Acid; Child Development; Child, Preschool; Citrulline; Female; Humans; Infant; Infant, Newborn; Phenylacetates | 1993 |
Regulation of urea and citrulline synthesis under physiological conditions.
Topics: Amino Acids; Ammonia; Animals; Citrulline; Glutamates; Male; Mitochondria, Liver; Nitrogen; Ornithine; Rats; Rats, Sprague-Dawley; Urea | 1993 |
Influence of carbon and nitrogen sources on glutathione catabolic enzymes in Candida albicans during dimorphism.
Topics: Ammonia; Candida albicans; Citrulline; gamma-Glutamyltransferase; Glucose; Glutamic Acid; Glutathione; Glutathione Peroxidase; Glutathione Reductase; Glutathione Transferase; Sucrose | 1995 |
Urea synthesis in enterocytes of developing pigs.
Topics: Ammonia; Ammonium Chloride; Animals; Animals, Newborn; Animals, Suckling; Arginine; Argininosuccinate Lyase; Argininosuccinate Synthase; Carbamoyl-Phosphate Synthase (Ammonia); Carbamyl Phosphate; Chromatography, High Pressure Liquid; Citrulline; Glutamine; Intestinal Mucosa; Intestines; Ornithine; Ornithine Carbamoyltransferase; Swine; Urea; Weaning | 1995 |
Sodium citrate supplementation in inborn argininosuccinate lyase deficiency: a study in a 5-year-old patient under total parenteral nutrition.
Topics: Alkalosis; Ammonia; Argininosuccinic Acid; Argininosuccinic Aciduria; Child, Preschool; Citrates; Citric Acid; Citrulline; Female; Humans; Nitrogen; Parenteral Nutrition, Total | 1995 |
Cryptogenic hepatitis masking the diagnosis of ornithine transcarbamylase deficiency.
Topics: Absorption; Ammonia; Arginine; Child, Preschool; Citrulline; Diagnosis, Differential; Dietary Proteins; Female; Glutamine; Hepatitis; Humans; Infant; Lysine; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Urea | 1996 |
Hyperornithinemia-hyperammonemia-homocitrullinuria (HHH)-syndrome. Ultrastructural changes of mitochondria in cultured dermal fibroblasts of three patients.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Cells, Cultured; Child; Citrulline; Female; Fibroblasts; Humans; Male; Mitochondria; Ornithine; Skin; Syndrome | 1996 |
Therapeutic use of carbamylglutamate in the case of carbamoyl-phosphate synthetase deficiency.
Topics: Ammonia; Arginine; Carbamoyl-Phosphate Synthase (Ammonia); Child, Preschool; Citrulline; Glutamates; Glutamic Acid; Glutamine; Humans; Male | 1996 |
Ciliated cultured dermal fibroblasts in a patient with hyperornithinemia, hyperammonemia and homocitrullinuria (HHH) syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Cells, Cultured; Cilia; Citrulline; Endoplasmic Reticulum, Rough; Fibroblasts; Humans; Microscopy, Electron; Mitochondria; Ornithine; Skin; Syndrome; Urea | 1995 |
Case report: recurrent hyperammonaemic encephalopathy due to citrullinaemia in a 52 year old man.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinate Synthase; China; Citrulline; Hepatic Encephalopathy; Humans; Male; Middle Aged; Recurrence; Singapore | 1996 |
[A case of citrullinemia repeatedly induced by pregnancy].
Topics: Adult; Ammonia; Argininosuccinate Synthase; Citrulline; Female; Humans; Pregnancy; Pregnancy Complications, Hematologic; Pregnancy Outcome; Recurrence; Urea | 1996 |
Regulation of [15N]urea synthesis from [5-15N]glutamine. Role of pH, hormones, and pyruvate.
Topics: Amino Acids; Ammonia; Animals; Citric Acid Cycle; Citrulline; Gas Chromatography-Mass Spectrometry; Glucagon; Glutamates; Glutaminase; Glutamine; Hydrogen-Ion Concentration; Insulin; Liver; Male; Pyruvic Acid; Rats; Rats, Sprague-Dawley; Urea | 1996 |
Clinical and biochemical heterogeneity in females of a large pedigree with ornithine transcarbamylase deficiency due to the R141Q mutation.
Topics: Allopurinol; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Female; Glutamine; Heterozygote; Humans; Infant, Newborn; Male; Mutation; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Pedigree | 1996 |
Biogenesis of Candida albicans Can1 permease expressed in Saccharomyces cerevisiae.
Topics: Amino Acid Transport Systems; Ammonia; Arginine; Blotting, Western; Candida albicans; Citrulline; Cycloheximide; Epitopes; Fungal Proteins; Gene Expression; Histidine; Lysine; Membrane Transport Proteins; Mutation; Plasmids; Proline; Proto-Oncogene Proteins c-myc; Recombinant Proteins; Saccharomyces cerevisiae; Transformation, Genetic | 1997 |
Adult-onset type II citrullinemia: clinical pictures before and after liver transplantation.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Humans; Liver Transplantation; Magnetic Resonance Imaging; Male; Tomography, X-Ray Computed; Trypsin Inhibitor, Kazal Pancreatic | 1997 |
Neonatal onset of hyperornithinemia-hyperammonemia-homocitrullinuria syndrome with favorable outcome.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Carnitine; Citrulline; Diet, Protein-Restricted; Humans; Infant, Newborn; Male; Ornithine | 1997 |
No increase of ornithine concentration in the liver of ornithine transcarbamylase-deficient spf-ash mice following intraperitoneal injection of ammonium chloride.
Topics: Ammonia; Ammonium Chloride; Animals; Arginine; Citrulline; Liver; Mice; Mice, Inbred Strains; Mice, Transgenic; Ornithine; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Peptones | 1997 |
Orthotopic liver transplantation for adult-onset type II citrullinaemia.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids, Branched-Chain; Ammonia; Arginine; Argininosuccinate Synthase; Brain Edema; Cause of Death; Citrulline; Diet, Protein-Restricted; Disease Progression; Fatal Outcome; Glutamic Acid; Hepatic Encephalopathy; Humans; Immunohistochemistry; Liver; Liver Transplantation; Male; Prognosis; Referral and Consultation | 1997 |
Proceedings of a satellite meeting on advances in inherited urea cycle disorders. Vienna, 20-21 May 1997.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Genetic Therapy; Genome, Human; Humans; Nitrogen; Ornithine Carbamoyltransferase Deficiency Disease; Urea | 1998 |
Liver transplantation for the treatment of urea cycle disorders.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Canada; Carbamoyl-Phosphate Synthase (Ammonia); Child; Citrulline; Communication Disorders; Female; Graft Rejection; Humans; Intellectual Disability; Liver Transplantation; Male; Microcephaly; Ornithine Carbamoyltransferase Deficiency Disease; Treatment Outcome; United States; Urea | 1998 |
Evaluation of gene therapy for citrullinaemia using murine and bovine models.
Topics: Adenoviruses, Human; Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Arginine; Argininosuccinate Synthase; Benzoates; Benzoic Acid; Cattle; Citrulline; Disease Models, Animal; Evaluation Studies as Topic; Gene Transfer Techniques; Genetic Therapy; Genetic Vectors; Liver; Mice; Nitrogen; Treatment Outcome; Urea | 1998 |
N-acetylglutamate synthetase deficiency: favourable experience with carbamylglutamate.
Topics: Acetyltransferases; Amino-Acid N-Acetyltransferase; Ammonia; Citrulline; Consanguinity; Dietary Proteins; Female; Glutamates; Glutamine; Humans; Infant, Newborn; Mitochondria, Liver | 1998 |
Hepatocyte gene therapy in a large animal: a neonatal bovine model of citrullinemia.
Topics: Adenoviridae; Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Animals, Newborn; Argininosuccinate Synthase; Cattle; Cell Transplantation; Citrulline; Female; Genetic Therapy; Genetic Vectors; Glutamine; Heterozygote; Humans; Liver; Male | 1999 |
Metabolic capacity for L-citrulline synthesis from ammonia in rat isolated colonocytes.
Topics: Ammonia; Ammonium Chloride; Animals; Arginase; Arginine; Argininosuccinate Synthase; Cell Survival; Cells, Cultured; Citrulline; Colon; Ketoglutaric Acids; Male; Ornithine Carbamoyltransferase; Oxidation-Reduction; Rats; Rats, Inbred F344; Urea | 1999 |
Arginine dihydrolase pathway in Lactobacillus plantarum from orange.
Topics: Ammonia; Arginine; Beverages; Citrulline; Citrus; Colorimetry; Glucose; Hydrogen-Ion Concentration; Hydrolases; Lactobacillus; Ornithine; Spectrophotometry; Urea | 1999 |
Is glutamine essential for the maintenance of intestinal function? A study in the isolated perfused rat small intestine.
Topics: Alanine; Ammonia; Animals; Citrulline; Glutamate-Ammonia Ligase; Glutamine; In Vitro Techniques; Intestine, Small; Male; Perfusion; Rats; Rats, Sprague-Dawley | 1999 |
Effects of vascular or luminal administration and of simultaneous glucose availability on glutamine utilization by isolated rat small intestine.
Topics: Ammonia; Animals; Citrulline; Glucose; Glutamine; In Vitro Techniques; Intestinal Absorption; Intestinal Mucosa; Intestine, Small; Male; Perfusion; Rats; Rats, Sprague-Dawley | 1999 |
Hyperornithinaemia-hyperammonaemia-homocitrullinuria syndrome is caused by mutations in a gene encoding a mitochondrial ornithine transporter.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acid Sequence; Amino Acid Substitution; Amino Acid Transport Systems, Basic; Ammonia; Animals; Canada; Carrier Proteins; Chromosome Mapping; Chromosomes, Human, Pair 13; Citrulline; Female; France; Genetic Carrier Screening; Humans; Karyotyping; Male; Membrane Transport Proteins; Mice; Mitochondria; Mitochondrial Membrane Transport Proteins; Molecular Sequence Data; Neurospora crassa; Ornithine; Point Mutation; Saccharomyces cerevisiae; Sequence Alignment; Sequence Deletion; Sequence Homology, Amino Acid; Skin; Syndrome; Transfection | 1999 |
Studies of hepatic glutamine metabolism in the perfused rat liver with (15)N-labeled glutamine.
Topics: Ammonia; Animals; Aspartic Acid; Carbamyl Phosphate; Citrulline; Glucagon; Glutamates; Glutaminase; Glutamine; Insulin; Liver; Male; Nitrogen Isotopes; Oxygen Consumption; Perfusion; Rats; Rats, Sprague-Dawley; Urea | 1999 |
Aberrations of ammonia metabolism in ornithine carbamoyltransferase-deficient spf-ash mice and their prevention by treatment with urea cycle intermediate amino acids and an ornithine aminotransferase inactivator.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Ammonium Chloride; Animals; Arginine; Citrulline; Enzyme Inhibitors; Injections, Intraperitoneal; Liver; Male; Mice; Mice, Transgenic; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Perfusion; Urea | 1999 |
Determination of urinary orotic acid and uracil by capillary zone electrophoresis.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Borates; Buffers; Citrulline; Dietary Proteins; Electrophoresis, Capillary; Humans; Hydrogen-Ion Concentration; Infant; Male; Ornithine; Orotic Acid; Syndrome; Uracil | 1999 |
Three novel mutations (G27E, insAAC, R179X) in the ORNT1 gene of Japanese patients with hyperornithinemia, hyperammonemia, and homocitrullinuria syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acid Sequence; Ammonia; Asian People; Biological Transport; Carrier Proteins; Citrulline; DNA Mutational Analysis; Exons; Humans; Japan; Mitochondria; Molecular Sequence Data; Mutation; Ornithine; Reverse Transcriptase Polymerase Chain Reaction; Syndrome | 2000 |
Splanchnic and leg exchange of amino acids and ammonia in acute liver failure.
Topics: Adult; Alanine; Amino Acids; Ammonia; Blood Urea Nitrogen; Citrulline; Female; Femoral Artery; Femoral Vein; Fibrosis; Glutamine; Humans; Leg; Liver Failure, Acute; Male; Middle Aged; Predictive Value of Tests; Proline; Splanchnic Circulation; Urea | 2000 |
Functional ureogenesis in the gobiid fish Mugilogobius abei.
Topics: Amino Acid Sequence; Ammonia; Animals; Anti-Bacterial Agents; Carbon-Nitrogen Ligases; Citrulline; Female; Gills; Glutamate-Ammonia Ligase; Glutamine; Kinetics; Liver; Male; Molecular Sequence Data; Muscles; Nitrogen; Ornithine; Perciformes; RNA, Messenger; Seawater; Sequence Alignment; Skin; Urea; Uric Acid | 2000 |
Citrullinemia type II in a 64-year-old man with fluctuating serum citrulline levels.
Topics: Ammonia; Biomarkers; Brain; Cerebrovascular Circulation; Citrulline; Citrullinemia; Humans; Magnetic Resonance Imaging; Male; Middle Aged; Serine; Threonine; Trypsin Inhibitor, Kazal Pancreatic | 2001 |
A Chinese adult onset type II citrullinaemia patient with 851del4/1638ins23 mutations in the SLC25A13 gene.
Topics: Adult; Age of Onset; Ammonia; Calcium-Binding Proteins; China; Citrulline; Citrullinemia; DNA Mutational Analysis; Female; Humans; Kidney Failure, Chronic; Liver; Membrane Transport Proteins; Mitochondrial Membrane Transport Proteins; Mitochondrial Proteins; Mutagenesis, Insertional; Mutation; Sequence Deletion | 2001 |
Detection of neonatal argininosuccinate lyase deficiency by serum tandem mass spectrometry.
Topics: Amino Acid Sequence; Amino Acids; Ammonia; Arginine; Argininosuccinate Lyase; Argininosuccinic Acid; Argininosuccinic Aciduria; Base Sequence; Citrulline; Coma; Frameshift Mutation; Humans; Hyperammonemia; Infant, Newborn; Mass Spectrometry; Molecular Sequence Data; Neonatal Screening; Ornithine | 2001 |
Type II (adult onset) citrullinaemia: clinical pictures and the therapeutic effect of liver transplantation.
Topics: Adolescent; Adult; Ammonia; Brain; Brain Edema; Citrulline; Citrullinemia; Cognition Disorders; Coma; Consciousness Disorders; Electroencephalography; Female; Hepatic Encephalopathy; Humans; Liver Transplantation; Magnetic Resonance Imaging; Male; Middle Aged; Neuropsychological Tests; Severity of Illness Index; Tomography, Emission-Computed, Single-Photon; Tomography, X-Ray Computed; Treatment Outcome | 2001 |
Conscientious metabolic monitoring on a patient with hyperornithinemia-hyperammonemia-homocitrullinuria (HHH) syndrome undergoing anaesthesia.
Topics: Adult; Amino Acids; Ammonia; Anesthesia; Blood Coagulation Tests; Citrulline; Clinical Chemistry Tests; Female; Humans; Monitoring, Physiologic; Ornithine; Syndrome | 2001 |
A patient with adult-onset type II citrullinemia on long-term hemodialysis: reversal of clinical symptoms and brain MRI findings.
Topics: Adult; Ammonia; Brain; Citrulline; Citrullinemia; Diagnosis, Differential; Female; Humans; Magnetic Resonance Imaging; Polycystic Kidney Diseases; Renal Dialysis; Time Factors | 2002 |
Renal arginine and protein synthesis are increased during early endotoxemia in mice.
Topics: Amino Acids; Ammonia; Animals; Arginine; Citrulline; Endotoxemia; Female; Kidney; Lipopolysaccharides; Mice; Nitrates; Nitric Oxide; Protein Biosynthesis; Urea | 2002 |
Effect of arginine, ornithine and citrulline supplementation upon performance and metabolism of trained rats.
Topics: Ammonia; Animals; Arginine; Citrulline; Dietary Supplements; Glutamate-Ammonia Ligase; Glutamine; Glycogen; Liver; Male; Muscle, Skeletal; Ornithine; Rats; Rats, Wistar; Swimming; Urea | 2003 |
The urea cycle in the liver of arthritic rats.
Topics: Ammonia; Animals; Arthritis, Experimental; Aspartic Acid; Citrulline; Dose-Response Relationship, Drug; Glucose; Glutamic Acid; Kidney; Lactic Acid; Liver; Male; Models, Biological; Oxygen; Perfusion; Pyruvic Acid; Rats; Rats, Wistar; Time Factors; Urea | 2003 |
Treatment of ammonia intoxication in rats with urea cycle amino acids, furosemide and fluids.
Topics: Ammonia; Animals; Arginine; Citrulline; Diuretics; Fluid Therapy; Furosemide; Male; Ornithine; Poisoning; Rats; Rats, Wistar | 2003 |
Serial diffusion-weighted magnetic resonance imaging in adult-onset citrullinaemia.
Topics: Adult; Ammonia; Argininosuccinic Acid; Brain; Citrulline; Citrullinemia; Coma; Diagnosis, Differential; Disease Progression; Fatty Liver; Humans; Magnetic Resonance Imaging; Male; Recurrence; Remission, Spontaneous; Substance-Related Disorders; Ultrasonography | 2003 |
Oral supplementation corrects plasma lysine concentrations in lysinuric protein intolerance.
Topics: Absorption; Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Female; Humans; Intestinal Absorption; Kidney Tubules; Kinetics; Lysine; Male; Nitrogen; Ornithine; Reference Values; Urea | 2003 |
UREA FORMATION AND UREA CYCLE ENZYMES IN THE CESTODE, HYMENOLEPIS DIMINUTA.
Topics: Amino Acids; Ammonia; Animals; Arginase; Bicarbonates; Carbon Isotopes; Cestoda; Citrulline; Hymenolepis diminuta; Magnesium; Manganese; Metabolism; Ornithine; Research; Transferases; Urea | 1963 |
THE SYNTHESIS OF UREA IN THE BRAIN.
Topics: Alanine; Amino Acids; Aminobutyrates; Ammonia; Aspartic Acid; Brain; Carbon Isotopes; Citrulline; Ornithine; Proteins; Rats; Research; Tissue Culture Techniques; Urea | 1963 |
[INITIAL CLINICAL RESULTS FOLLOWING THE USE OF A NEW HEPATOPROTECTIVE AND ANTI-BLOOD AMMONIA PREPARATION].
Topics: Amino Acids; Ammonia; Arginine; Blood Chemical Analysis; Chemical and Drug Induced Liver Injury; Citrulline; Geriatrics; Hepatitis; Hepatitis A; Humans; Ornithine | 1963 |
MEASUREMENT OF TISSUE ORNITHINE CARBAMOYLTRANSFERASE.
Topics: Ammonia; Animals; Citrulline; Colorimetry; Hydroxides; Liver; Mice; Ornithine; Ornithine Carbamoyltransferase; Research; Transferases | 1964 |
THE EFFECT OF AMMONIA ADMINISTRATION ON OROTIC ACID EXCRETION IN RATS.
Topics: Ammonia; Ammonium Chloride; Antimetabolites; Arginine; Chromatography; Citrulline; Diet; Glutamine; Ornithine; Orotic Acid; Pharmacology; Rats; Research; Succinates; Urine | 1965 |
Expression analysis of putative arcA, arcB and arcC genes partially cloned from Lactobacillus plantarum isolated from wine.
Topics: Amino Acid Sequence; Ammonia; Arginine; Bacterial Outer Membrane Proteins; Citrulline; Cloning, Molecular; Escherichia coli Proteins; Fermentation; Gene Expression Regulation; Genes, Bacterial; Humans; Lactobacillus; Membrane Proteins; Molecular Sequence Data; Protein Kinases; Repressor Proteins; Reverse Transcriptase Polymerase Chain Reaction; Wine | 2004 |
Carbon dioxide and ammonia fixation in the biosynthesis of citrulline.
Topics: Ammonia; Carbon Dioxide; Citrulline | 1951 |
Adaptative increase of ornithine production and decrease of ammonia metabolism in rat colonocytes after hyperproteic diet ingestion.
Topics: Adaptation, Physiological; Ammonia; Ammonium Chloride; Animals; Arginine; Body Weight; Citrulline; Colon; Dietary Proteins; Dose-Response Relationship, Drug; Eating; Feces; Hydrogen-Ion Concentration; Intestines; Male; Ornithine; Osmolar Concentration; Polyamines; Quaternary Ammonium Compounds; Rats; Rats, Inbred F344; Veins | 2004 |
Urea synthesis by ruminal epithelial and duodenal mucosal cells from growing sheep.
Topics: Ammonia; Animals; Arginase; Arginine; Aspartic Acid; Carbamoyl-Phosphate Synthase (Ammonia); Cells, Cultured; Citrulline; Duodenum; Enzyme Activation; Epithelial Cells; Gastric Mucosa; Intestinal Mucosa; Ornithine; Rumen; Sheep; Urea | 2004 |
Effects of acute ammonia toxicity on nitric oxide (NO), citrulline-NO cycle enzymes, arginase and related metabolites in different regions of rat brain.
Topics: Amino Acids; Ammonia; Animals; Arginase; Argininosuccinate Lyase; Argininosuccinate Synthase; Brain; Citrulline; gamma-Aminobutyric Acid; Male; Nitrates; Nitric Oxide; Nitric Oxide Synthase; Nitrites; Rats; Rats, Sprague-Dawley | 2005 |
Ornithine aminotransferase deficiency: diagnostic difficulties in neonatal presentation.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Diagnosis, Differential; Female; Fibroblasts; Glutamine; Humans; Hyperammonemia; Infant, Newborn; Male; Mutation; Neonatal Screening; Ornithine; Ornithine-Oxo-Acid Transaminase; Orotic Acid | 2005 |
Metabolic fates of ammonia-N in ruminal epithelial and duodenal mucosal cells isolated from growing sheep.
Topics: Alanine; Ammonia; Animals; Arginine; Aspartic Acid; Citrulline; Duodenum; Epithelium; Gas Chromatography-Mass Spectrometry; Glutamic Acid; Intestinal Mucosa; Nitrogen; Nitrogen Isotopes; Rumen; Sheep; Urea | 2005 |
Agmatine stimulates hepatic fatty acid oxidation: a possible mechanism for up-regulation of ureagenesis.
Topics: Adenosine Diphosphate; Adenosine Monophosphate; Adenosine Triphosphate; Agmatine; Ammonia; Animals; Carbon Isotopes; Citrulline; Dose-Response Relationship, Drug; Fasting; Fatty Acids; Gas Chromatography-Mass Spectrometry; Glutamates; Ketone Bodies; Kinetics; Liver; Male; Mitochondria, Liver; Models, Biological; Nuclear Magnetic Resonance, Biomolecular; Oxidation-Reduction; Oxygen Consumption; Palmitic Acids; Perfusion; Rats; Rats, Sprague-Dawley; Up-Regulation; Urea | 2006 |
Citrulline and ammonia accumulating in citrullinemia reduces antioxidant capacity of rat brain in vitro.
Topics: Ammonia; Animals; Antioxidants; Catalase; Cerebral Cortex; Citrulline; Citrullinemia; Enzyme Activation; Glutathione Peroxidase; Hydrogen Peroxide; In Vitro Techniques; Lipid Peroxidation; Oxidative Stress; Rats; Rats, Wistar; Sulfhydryl Compounds; Superoxide Dismutase; Thiobarbituric Acid Reactive Substances | 2006 |
Determination of homocitrulline in urine of patients with HHH syndrome by liquid chromatography tandem mass spectrometry.
Topics: Ammonia; Chromatography, Liquid; Citrulline; Creatinine; Humans; Mass Spectrometry; Ornithine; Syndrome | 2006 |
Degradation of arginine by Slackia exigua ATCC 700122 and Cryptobacterium curtum ATCC 700683.
Topics: Ammonia; Arginine; Chromatography, High Pressure Liquid; Citrulline; Dental Pulp Necrosis; Eubacterium; Humans; Hydrolases; Ornithine; Periodontal Pocket | 2006 |
Long-term oral lysine supplementation in lysinuric protein intolerance.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Calcium; Child; Child, Preschool; Chromatography, Ion Exchange; Citrulline; Dietary Supplements; Female; Finland; Humans; Long-Term Care; Lysine; Male; Middle Aged; Phosphates | 2007 |
Magnetic resonance spectroscopy in adult-onset citrullinemia: elevated glutamine levels in comatose patients.
Topics: Adult; Ammonia; Biomarkers; Brain; Brain Mapping; Cerebral Cortex; Choline; Citrulline; Citrullinemia; Coma; Diffusion Magnetic Resonance Imaging; Disease Progression; Early Diagnosis; Fatal Outcome; Glutamic Acid; Glutamine; Gyrus Cinguli; Humans; Hyperammonemia; Inositol; Magnetic Resonance Spectroscopy; Male; Predictive Value of Tests | 2007 |
Interaction between murine spf-ash mutation and genetic background yields different metabolic phenotypes.
Topics: Alanine; Ammonia; Animals; Arginine; Citrulline; Disease Models, Animal; Female; Glycine; Injections, Intravenous; Intestinal Mucosa; Liver; Male; Mice; Mice, Inbred ICR; Mice, Inbred Strains; Mice, Mutant Strains; Models, Biological; Mutation; Nitric Oxide; Ornithine; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Phenotype; Phenylalanine; Urea | 2007 |
Mitochondrial citrulline synthesis from ammonia and glutamine in the liver of ureogenic air-breathing catfish, Clarias batrachus (Linnaeus).
Topics: Ammonia; Animals; Biosynthetic Pathways; Carbonic Anhydrases; Catfishes; Citrulline; Glutamine; Mitochondria; Succinic Acid; Urea | 2007 |
Glutamine: precursor or nitrogen donor for citrulline synthesis?
Topics: Ammonia; Animals; Arginine; Carbon Isotopes; Citrulline; Gastrointestinal Tract; Glutamine; Male; Mass Spectrometry; Mice; Mice, Inbred ICR; Nitrogen; Nitrogen Isotopes; Proline; Random Allocation; Specific Pathogen-Free Organisms | 2010 |
Substrate specificity and kinetic studies of PADs 1, 3, and 4 identify potent and selective inhibitors of protein arginine deiminase 3.
Topics: Amino Acid Sequence; Ammonia; Calcium; Catalysis; Citrulline; Enzyme Inhibitors; Humans; Hydrolases; Isoenzymes; Kinetics; Molecular Sequence Data; Protein-Arginine Deiminase Type 1; Protein-Arginine Deiminase Type 3; Protein-Arginine Deiminase Type 4; Protein-Arginine Deiminases; Substrate Specificity | 2010 |
Acute endotoxemia following transjugular intrahepatic stent-shunt insertion is associated with systemic and cerebral vasodilatation with increased whole body nitric oxide production in critically ill cirrhotic patients.
Topics: Acute Disease; Ammonia; Arginine; Cerebrovascular Circulation; Citrulline; Critical Illness; Cytokines; Endotoxemia; Female; Humans; Liver Cirrhosis; Male; Middle Aged; Neutrophils; Nitric Oxide; Portasystemic Shunt, Transjugular Intrahepatic; Vasodilation | 2011 |
New insights on the mechanisms of valproate-induced hyperammonemia: inhibition of hepatic N-acetylglutamate synthase activity by valproyl-CoA.
Topics: Acyl Coenzyme A; Amino-Acid N-Acetyltransferase; Ammonia; Animals; Anticonvulsants; Citrulline; Disease Models, Animal; Glutamates; Glutamine; Humans; Hyperammonemia; In Vitro Techniques; Liver; Male; Mice; Mice, Inbred C57BL; Models, Biological; Rats; Rats, Wistar; Urea; Valproic Acid | 2011 |
Transient fulminant liver failure as an initial presentation in citrullinemia type I.
Topics: Ammonia; Argininosuccinate Synthase; Base Sequence; Citrulline; Citrullinemia; Fatty Liver; Female; Humans; Infant; International Normalized Ratio; Liver; Liver Failure, Acute; Male; Molecular Sequence Data; Mutagenesis, Insertional; Mutation, Missense; RNA Splice Sites; Seizures; Transaminases; Ultrasonography; Vomiting | 2011 |
Effects of citrulline supplementation on fatigue and exercise performance in mice.
Topics: Ammonia; Animals; Citrulline; Dietary Supplements; Fatigue; Lactic Acid; Male; Mice; Mice, Inbred ICR; Physical Conditioning, Animal; Physical Endurance; Swimming | 2011 |
Hyperammonemia in a patient with late-onset ornithine carbamoyltransferase deficiency.
Topics: Age of Onset; Ammonia; Arginine; Citrulline; Humans; Hyperammonemia; Male; Middle Aged; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Pedigree; Renal Dialysis; Sodium Benzoate | 2012 |
Chronic postnatal ornithine administration to rats provokes learning deficit in the open field task.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Animals, Newborn; Avoidance Learning; Behavior, Animal; Citrulline; Cognition; Developmental Disabilities; Disease Models, Animal; Half-Life; Learning Disabilities; Maze Learning; Memory; Memory, Long-Term; Ornithine; Postural Balance; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances | 2012 |
Successful prospective management of neonatal citrullinemia.
Topics: Adult; Ammonia; Anti-Infective Agents; Argininosuccinate Synthase; Base Sequence; Benzoates; Citrulline; Citrullinemia; Disease Management; Female; Humans; Infant, Newborn; Injections, Intravenous; Molecular Sequence Data; Mutation; Pregnancy; Pregnancy Complications; Prenatal Diagnosis; Prognosis; Prospective Studies; Renal Dialysis; Sequence Homology, Nucleic Acid | 2012 |
Impairment of brain redox homeostasis caused by the major metabolites accumulating in hyperornithinemia-hyperammonemia-homocitrullinuria syndrome in vivo.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Antioxidants; Brain; Catalase; Citrulline; Glutathione Peroxidase; Homeostasis; Injections, Intraperitoneal; Injections, Intraventricular; Male; Nitric Oxide; Ornithine; Oxidation-Reduction; Oxidative Stress; Protein Carbonylation; Rats; Rats, Wistar; Sulfhydryl Compounds; Thiobarbituric Acid Reactive Substances; Urease | 2012 |
Lactic acid bacteria isolated from apples are able to catabolise arginine.
Topics: Ammonia; Arginine; Bacterial Load; Bacterial Typing Techniques; Citrulline; Culture Media; DNA, Bacterial; DNA, Ribosomal; Hydrogen-Ion Concentration; Lactobacillales; Malus; Molecular Sequence Data; RNA, Ribosomal, 16S; Sequence Analysis, DNA | 2012 |
Liver-directed adeno-associated virus serotype 8 gene transfer rescues a lethal murine model of citrullinemia type 1.
Topics: Ammonia; Animals; Argininosuccinate Synthase; Citrulline; Citrullinemia; Dependovirus; Disease Models, Animal; Genetic Therapy; Genetic Vectors; Humans; Liver; Mice; Organ Specificity; Phenotype; Thyroxine-Binding Globulin | 2013 |
[Clinical effect of stem cell transplantation via hepatic artery in the treatment of type II hyperammonemia: a report on 6 cases].
Topics: AC133 Antigen; Ammonia; Antigens, CD; Arginine; Citrulline; Female; Glycoproteins; Hepatic Artery; Humans; Hyperammonemia; Infant; Male; Peptides; Stem Cell Transplantation | 2013 |
Long-term outcomes in Ornithine Transcarbamylase deficiency: a series of 90 patients.
Topics: Adolescent; Adult; Ammonia; Child; Child, Preschool; Citrulline; Female; Glutamine; Humans; Infant; Male; Ornithine Carbamoyltransferase Deficiency Disease; Young Adult | 2015 |
Identification of three novel mutations in fourteen patients with citrullinemia type 1.
Topics: Age of Onset; Ammonia; Argininosuccinate Synthase; Child; Child, Preschool; Citrulline; Citrullinemia; Gene Expression; Genes, Recessive; Genotype; Heterozygote; Homozygote; Humans; Infant; Infant, Newborn; Mutation; Pedigree; Phenotype; Retrospective Studies | 2017 |
Biochemical markers and neuropsychological functioning in distal urea cycle disorders.
Topics: Adolescent; Adult; Ammonia; Arginine; Argininosuccinic Aciduria; Biomarkers; Child; Child, Preschool; Citrulline; Citrullinemia; Female; Glutamine; Humans; Hyperargininemia; Longitudinal Studies; Male; Middle Aged; Neuropsychological Tests; Young Adult | 2018 |
The cyanobacterial ornithine-ammonia cycle involves an arginine dihydrolase.
Topics: Ammonia; Arginine; Bacterial Proteins; Biomass; Carbon Dioxide; Citrulline; Cyanobacteria; Hydrolases; Mutation; Nitrogen; Nitrogen Isotopes; Ornithine; Oscillometry; Polyamines; Synechocystis; Urea | 2018 |
Plasma citrulline, arginine, nitric oxide, and blood ammonia levels in neonatal calves with acute diarrhea.
Topics: Ammonia; Animals; Animals, Newborn; Arginine; Case-Control Studies; Cattle; Cattle Diseases; Citrulline; Dehydration; Diarrhea; Nitric Oxide; Systemic Inflammatory Response Syndrome | 2019 |
Pivotal role of inter-organ aspartate metabolism for treatment of mitochondrial aspartate-glutamate carrier 2 (citrin) deficiency, based on the mouse model.
Topics: Amino Acids; Ammonia; Ammonium Chloride; Animals; Aspartic Acid; Citrulline; Citrullinemia; Disease Models, Animal; Glycerolphosphate Dehydrogenase; Hyperammonemia; Intestine, Small; Lactates; Liver; Mice, Inbred C57BL; Mice, Knockout; Mitochondrial Membrane Transport Proteins; Organ Specificity; Ornithine; Perfusion; Portal Vein; Pyruvic Acid; Urea | 2019 |
Ruminal microbes of adult steers do not degrade extracellular L-citrulline and have a limited ability to metabolize extracellular L-glutamate1,2.
Topics: Amino Acids; Ammonia; Animals; Arginine; Bacteria; Cattle; Citrulline; Glutamic Acid; Glutamine; Male; Ornithine; Proline; Rumen | 2019 |
Metabolic studies reveal that ruminal microbes of adult steers do not degrade rumen-protected or unprotected L-citrulline.
Topics: Ammonia; Animal Feed; Animals; Arginine; Cattle; Citrulline; Diet; Digestion; Edible Grain; Fermentation; Gastrointestinal Microbiome; Glutamic Acid; Glutamine; Male; Rumen | 2020 |
Effects of resveratrol on alterations in cerebrum energy metabolism caused by metabolites accumulated in type I citrullinemia in rats.
Topics: Ammonia; Animals; Cerebellum; Cerebral Cortex; Citrulline; Citrullinemia; Disease Models, Animal; Dose-Response Relationship, Drug; Energy Metabolism; Free Radical Scavengers; Hippocampus; Male; Rats; Rats, Wistar; Resveratrol | 2021 |
Protective effect of resveratrol on citrullinemia type I-induced brain oxidative damage in male rats.
Topics: Ammonia; Animals; Antioxidants; Brain; Citrulline; Citrullinemia; Dose-Response Relationship, Drug; Male; Neuroprotective Agents; Oxidative Stress; Rats; Rats, Wistar; Resveratrol | 2021 |
Ammonia detoxification promotes CD8
Topics: Ammonia; Arginase; Arginine; CD8-Positive T-Lymphocytes; Citrulline; Nitric Oxide; Urea | 2023 |
Metabolomic Analysis of Microcystis aeruginosa After Exposure to the Algicide L-Lysine.
Topics: Ammonia; Arginine; Citrulline; Cyanobacteria; Ecosystem; Herbicides; Humans; Lysine; Microcystins; Microcystis; Ornithine | 2022 |
Citrulline in the management of patients with urea cycle disorders.
Topics: Ammonia; Arginine; Citrulline; Drug-Related Side Effects and Adverse Reactions; Humans; Retrospective Studies; Urea; Urea Cycle Disorders, Inborn | 2023 |
The interaction of ammonia and manganese in abnormal metabolism of minimal hepatic encephalopathy: A comparison metabolomics study.
Topics: Alanine; Ammonia; Animals; Arginine; Brain; Citrulline; gamma-Aminobutyric Acid; Glutamic Acid; Glutamine; Hepatic Encephalopathy; Hyperammonemia; Inositol; Isoleucine; Lactic Acid; Leucine; Manganese; Metabolomics; Rats; Rats, Sprague-Dawley; Taurine | 2023 |