carnitine and leucine

carnitine has been researched along with leucine in 59 studies

Research

Studies (59)

Timeframe	Studies, this research(%)	All Research%
pre-1990	14 (23.73)	18.7374
1990's	13 (22.03)	18.2507
2000's	8 (13.56)	29.6817
2010's	12 (20.34)	24.3611
2020's	12 (20.34)	2.80

Authors

Authors	Studies
Glatz, JF; Van Hinsbergh, VW; Veerkamp, JH	1
Adibi, SA; Paul, HS	1
Van Hinsbergh, VM; Veerkamp, JH; Zuurveld, JG	1
Engelen, PJ; Ghijsen, WJ; Van Hinsbergh, VW; Veerkamp, JH	1
Gibson, KM; Lee, CF; Wappner, RS	1
Khurana, KK; Miotto, G; Mortimore, GE; Siliprandi, N; Venerando, R	1
Bertelli, A; Conte, A; Giovannini, L; Palmieri, L; Ronca, G	1
Tanaka, K	1
Buchanan, D; Dasouki, M; Gibson, KM; Mercer, N; Thoene, J	1
Bowyer, BA; Fleming, CR; Haymond, MW; Miles, JM	1
Miotto, G; Siliprandi, N; Venerando, R	1
Horecker, BL; Melloni, E; Michetti, M; Pontremoli, S; Salamino, F; Siliprandi, N; Sparatore, B	1
Inoue, F; Maltby, DA; Millington, DS; Roe, CR	1
Burton, AF; Turnell, RW	1
Brendel, K; Bressler, R; Corredor, C	1
Isselbacher, KJ; Miller, EM; Tanaka, K	1
Massaro, D; Simon, MR; Steinkamp, H	1
Cordewener, JH; van Hinsbergh, VW; Veerkamp, JH	1
Granchelli, JA; Gregorio, CC; Hudecki, MS; Pollina, CM; Povoski, SP	1
Bain, MS; Burns, SP; Chalmers, RA; Holmes, HC; Iles, RA	1
Kahler, SG; Millington, DS; Nada, MA; Rutledge, SL; van Hove, JL	1
Fries, MH; Jurecki, E; Packman, S; Rinaldo, P; Schmidt-Sommerfeld, E	1
Ito, T; Itoh, T; Kidouchi, K; Mizuguchi, K; Ohba, S; Sugiyama, N; Yamaguchi, S	1
Bennett, MJ; Gibson, KM; Morton, DH; Naylor, EW	1
Chalmers, RA; Harrison, EL; Jones, MG; Lee, PJ; Leonard, JV; Whipp, BJ	1
Baumgartner, ER; Duran, M; Fingerhut, R; Kohlschütter, A; Lehnert, W; Steen, C; Stehn, M; Suormala, T	1
de Almeida, IT; Duran, M; Maya, M; Overmars, H; Selhorst, J; Silva, MF; van Gennip, AH; Wanders, RJ	1
Amat di San Filippo, C; Longo, N; Wang, Y	1
Irokawa, M; Kobayashi, D; Maeda, T; Tamai, I; Tsuji, A	1
Bodamer, OA; Hussein, K; Langhans, CD; Leonard, JV; Mayatepek, E; Morris, AA; Rating, D	1
Barazzoni, R; Bianco, F; Biolo, G; Guarnieri, G; Mengozzi, G; Panzetta, G; Stulle, M; Vasile, A	1
Arnold, GL; Barshop, B; Braverman, N; Burton, B; Cederbaum, S; Fiegenbaum, A; Garganta, C; Gibson, J; Goodman, SI; Harding, C; Kahler, S; Koeberl, DD; Kronn, D; Longo, N; Matern, D	1
León-Ruiz, EN; Robbins, KA	1
Berezowski, V; Cecchelli, R; Czeredys, M; Kulikova, N; Mysiorek, C; Nałecz, KA; Samluk, Ł	1
Acquaviva, C; Caruba, C; Giudicelli, H; Khalfi, A; Moreigne, M; Pierron, S; Rolland, MO; Touati, G	1
Chace, DH; De Jesús, VR; Hannon, WH; Lim, TH; Mei, JV	1
Hu, W; Li, JM; Liao, XB; Peng, YQ; Song, FL; Tang, SY; Xie, H; Xiong, SY; Yang, B; Yuan, LQ; Zhou, K; Zhou, XM	1
Bogusiewicz, A; Boysen, G; Dawson, AM; Henrich, CL; Horvath, TD; Matthews, NI; Mock, DM; Moran, JH; Owen, SN; Spencer, HJ; Stratton, SL	1
Adams, SH; Hoppel, CL; Inukai, A; Kadota, Y; Kawamata, Y; Lang, CH; Lynch, CJ; Matsumoto, H; Olson, KC; Sakai, R; She, P; Shimomura, Y	1
Dutra-Filho, CS; Guerreiro, G; Manfredini, V; Mescka, CP; Vargas, CR; Wayhs, CA	1
Caudill, MA; Gayle, A; Jiang, X; Lucas, LK; Malysheva, O; Perry, CA; West, AA; Yan, J	1
Aranibar, N; Cherrington, NJ; Lake, AD; Lehman-McKeeman, LD; Novak, P; Reily, MD; Robertson, DG; Shipkova, P; Vaillancourt, RR	1
Jung, S; Kim, M; Lee, JH; Lee, SH	1
Bernstone, L; Hall, SK; Lawson, AJ	1
Moazzami, AA; Müllner, E; Mykkänen, H; Poutanen, K; Shrestha, A	1
Al-Majdoub, M; Ali, A; Carstensen, B; Ridderstråle, M; Safai, N; Spégel, P; Suvitaival, T; Vestergaard, H	1
Antoniazzi, S; Bertino, E; Cavallarin, L; Cesare Marincola, F; Corbu, S; Coscia, A; Cresi, F; Fanos, V; Giribaldi, M; Maiocco, G; Moro, GE; Peila, C; Sottemano, S	1
Holeček, M; Vodeničarovová, M	1
Berman, LM; Brown, LD; Hendricks, AE; Krebs, NF; Tang, M; Weaver, NE	1
Bararpour, N; Darrous, L; Froguel, P; Gasser, M; Gilardi, F; Kutalik, Z; Marques-Vidal, P; Porcu, E; Thomas, A; Waeber, G; Yengo, L	1
Feng, X; Hou, L; Jiang, Y; Li, X; Meng, X; Niu, J; Wang, Y; Wu, J; Xu, G; Zhao, X	1
Melander, O; Ottosson, F; Smith, E; Yan, Y	1
Jacobs, A; Jansen Van Vuren, E; Kruger, R; Louw, R; Mels, C; Strauss-Kruger, M	1
Dan, XG; Guan, GQ; Li, X; Liu, JL; Zhao, HX	1
Brzeska, B; Jaworska, J; Olek, RA; Radkiewicz, M; Sabisz, A; Samborowska, E; Sawicka, AK; Szarmach, A; Szurowska, E; Winklewski, PJ	1
Olek, RA; Samborowska, E	1
Abi-Rached, ZH; Jennings, EA; Jones, DE; Ryan, RO	1
Bertinato, J; Hendry, A; Kenney, L; Xiao, CW	1

Reviews

2 review(s) available for carnitine and leucine

Article	Year
Hypoglycin and hypoglycin-like compounds. Pharmacological reviews, 1969, Volume: 21, Issue:2 Topics: Amino Acids; Animals; Blood Glucose; Carnitine; Chemical Phenomena; Chemistry; Cholesterol; Coenzyme A; Columbidae; Cyclohexanes; Fatty Acids; Fruit; Gluconeogenesis; Glucose; Glycolysis; Hypoglycemia; Hypoglycemic Agents; In Vitro Techniques; Leucine; Mice; Propionates; Rabbits; Rats; Toxins, Biological; Transferases; Vomiting	1969
3-Methylglutarylcarnitine: A biomarker of mitochondrial dysfunction. Clinica chimica acta; international journal of clinical chemistry, 2023, Nov-01, Volume: 551 Topics: Biomarkers; Carnitine; Humans; Leucine; Mitochondria	2023

Article

Year

Hypoglycin and hypoglycin-like compounds.

Pharmacological reviews, 1969, Volume: 21, Issue:2

Topics: Amino Acids; Animals; Blood Glucose; Carnitine; Chemical Phenomena; Chemistry; Cholesterol; Coenzyme A; Columbidae; Cyclohexanes; Fatty Acids; Fruit; Gluconeogenesis; Glucose; Glycolysis; Hypoglycemia; Hypoglycemic Agents; In Vitro Techniques; Leucine; Mice; Propionates; Rabbits; Rats; Toxins, Biological; Transferases; Vomiting

1969

3-Methylglutarylcarnitine: A biomarker of mitochondrial dysfunction.

Clinica chimica acta; international journal of clinical chemistry, 2023, Nov-01, Volume: 551

Topics: Biomarkers; Carnitine; Humans; Leucine; Mitochondria

2023

Trials

5 trial(s) available for carnitine and leucine

Article	Year
Insulin action on glucose and protein metabolism during L-carnitine supplementation in maintenance haemodialysis patients. Nephrology, dialysis, transplantation : official publication of the European Dialysis and Transplant Association - European Renal Association, 2008, Volume: 23, Issue:3 Topics: Aged; Carnitine; Double-Blind Method; Female; Glucose; Humans; Injections, Intravenous; Insulin; Insulin Resistance; Kidney Failure, Chronic; Leucine; Male; Middle Aged; Proteins; Renal Dialysis	2008
Pregnancy and lactation alter biomarkers of biotin metabolism in women consuming a controlled diet. The Journal of nutrition, 2014, Volume: 144, Issue:12 Topics: Adult; Biomarkers; Biotin; Carbon-Carbon Ligases; Carnitine; Choline; Chromatography, Liquid; Diet; Dietary Supplements; Female; Humans; Lactation; Leucine; Milk, Human; New York; Patient Compliance; Pregnancy; Tandem Mass Spectrometry; Valerates; Young Adult	2014
Effect of metformin on plasma metabolite profile in the Copenhagen Insulin and Metformin Therapy (CIMT) trial. Diabetic medicine : a journal of the British Diabetic Association, 2018, Volume: 35, Issue:7 Topics: Aged; Carnitine; Chromatography, Liquid; Diabetes Mellitus, Type 2; Female; Follow-Up Studies; Glycated Hemoglobin; Humans; Hypoglycemic Agents; Insulin Resistance; Isoleucine; Leucine; Lysophospholipids; Male; Mass Spectrometry; Metabolome; Metabolomics; Metformin; Middle Aged; Mitochondria; Tyrosine; Valine	2018
Urinary Metabolomic Profile of Preterm Infants Receiving Human Milk with Either Bovine or Donkey Milk-Based Fortifiers. Nutrients, 2020, Jul-27, Volume: 12, Issue:8 Topics: Animals; Carnitine; Cattle; Choline; Enteral Nutrition; Equidae; Female; Food, Fortified; Galactose; Humans; Infant, Newborn; Infant, Premature; Leucine; Lysine; Male; Metabolome; Milk, Human; Nutritional Status	2020
Different Blood Metabolomics Profiles in Infants Consuming a Meat- or Dairy-Based Complementary Diet. Nutrients, 2021, Jan-27, Volume: 13, Issue:2 Topics: Amino Acids, Branched-Chain; Amino Acids, Essential; Carnitine; Dairy Products; Diet; Follow-Up Studies; Humans; Infant; Infant Nutritional Physiological Phenomena; Isoleucine; Leucine; Meat; Metabolomics; Phenylalanine; Valine	2021

Other Studies

52 other study(ies) available for carnitine and leucine

Article	Year
4-Methyl-2-oxopentanoate oxidation by rat skeletal-muscle mitochondria. The Biochemical journal, 1979, Aug-15, Volume: 182, Issue:2 Topics: Animals; Caproates; Carnitine; Coenzyme A; Decarboxylation; In Vitro Techniques; Keto Acids; Kinetics; Leucine; Mitochondria, Muscle; Models, Biological; Oxidation-Reduction; Rats	1979
Effect of carnitine on branched-chain amino acid oxidation by liver and skeletal muscle. The American journal of physiology, 1978, Volume: 234, Issue:5 Topics: Amino Acids; Animals; Caproates; Carnitine; Carnitine Acyltransferases; Diabetes Mellitus, Experimental; In Vitro Techniques; Leucine; Liver; Male; Muscles; Oxidation-Reduction; Rats; Starvation	1978
Role of carnitine in leucine oxidation by mitochondria of rat muscle. FEBS letters, 1978, Aug-01, Volume: 92, Issue:1 Topics: Animals; Biological Transport, Active; Caproates; Carnitine; In Vitro Techniques; Leucine; Male; Mitochondria, Muscle; Oxidation-Reduction; Rats	1978
Effect of L-carnitine on the oxidation of leucine and valine by rat skeletal muscle. Biochemical medicine, 1978, Volume: 20, Issue:1 Topics: Animals; Caproates; Carnitine; Coenzyme A; Keto Acids; Ketoglutaric Acids; Leucine; Male; Mitochondria, Muscle; Muscles; Oxidation-Reduction; Pyruvates; Rats; Valine	1978
3-Methylglutaconyl-coenzyme-A hydratase deficiency: a new case. Journal of inherited metabolic disease, 1992, Volume: 15, Issue:3 Topics: Carnitine; Diseases in Twins; Fibroblasts; Glutarates; Humans; Hydro-Lyases; Infant; Leucine; Lymphocytes; Male; Meglutol	1992
Control of hepatic proteolysis by leucine and isovaleryl-L-carnitine through a common locus. Evidence for a possible mechanism of recognition at the plasma membrane. The Journal of biological chemistry, 1992, Nov-05, Volume: 267, Issue:31 Topics: Alanine; Animals; Biological Transport; Carnitine; Cell Membrane; Glutamine; Kinetics; Leucine; Liver; Proteins; Rats	1992
Synergic and complementary effects of L-carnitine and coenzyme Q on long-chain fatty acid metabolism and on protection against anthracycline damage. International journal of tissue reactions, 1990, Volume: 12, Issue:3 Topics: Animals; Antibiotics, Antineoplastic; Carbon Radioisotopes; Carnitine; Cattle; Doxorubicin; Drug Synergism; Fatty Acids; In Vitro Techniques; Leucine; Mitochondria, Heart; Oxidation-Reduction; Oxidoreductases; Oxygen Consumption; Ubiquinone	1990
Metabolic effects of carnitine supplementation in subjects with low plasma carnitine levels. Nutrition reviews, 1990, Volume: 48, Issue:3 Topics: Blood Glucose; Carnitine; Humans; Leucine; Palmitates; Palmitic Acids	1990
Isovaleric acidemia: personal history, clinical survey and study of the molecular basis. Progress in clinical and biological research, 1990, Volume: 321 Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Cell Line; Child, Preschool; Female; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Prognosis; Valerates	1990
3-Hydroxy-3-methylglutaric aciduria: response to carnitine therapy and fat and leucine restriction. Journal of inherited metabolic disease, 1987, Volume: 10, Issue:2 Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Carnitine; Dietary Fats; Dietary Proteins; Female; Glutarates; Humans; Infant, Newborn; Leucine; Meglutol; Oxo-Acid-Lyases	1987
L-carnitine: effect of intravenous administration on fuel homeostasis in normal subjects and home-parenteral-nutrition patients with low plasma carnitine concentrations. The American journal of clinical nutrition, 1989, Volume: 49, Issue:4 Topics: Acetoacetates; Blood Glucose; Carnitine; Fatty Acids; Glucagon; Home Care Services; Homeostasis; Humans; Ketone Bodies; Leucine; Oxidation-Reduction; Palmitates; Parenteral Nutrition	1989
Inhibitory action of isovaleryl-L-carnitine on proteolysis in perfused rat liver. Biochemical and biophysical research communications, 1989, Feb-15, Volume: 158, Issue:3 Topics: Animals; Carnitine; Dose-Response Relationship, Drug; Leucine; Liver; Male; Peptide Hydrolases; Proteins; Rats; Rats, Inbred Strains	1989
Isovalerylcarnitine is a specific activator of calpain of human neutrophils. Biochemical and biophysical research communications, 1987, Nov-13, Volume: 148, Issue:3 Topics: Calcium; Calpain; Carnitine; Cytoskeletal Proteins; Enzyme Activation; Humans; Leucine; Neutrophils	1987
Endogenous catabolism is the major source of toxic metabolites in isovaleric acidemia. The Journal of pediatrics, 1987, Volume: 110, Issue:1 Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Dietary Proteins; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates	1987
Studies on the mechanism of resistance to lymphocytolysis induced by corticosteroids. Cancer research, 1974, Volume: 34, Issue:1 Topics: Animals; Carnitine; Cell Line; Cell Nucleus; Drug Resistance; Fatty Acids, Nonesterified; Glucose; Hydrocortisone; Leucine; Leukemia L1210; Leukemia, Experimental; Leukemia, Lymphoid; Lymphoma, Non-Hodgkin; Mice; Oxidation-Reduction; Sarcoma, Experimental; Thymidine; Thymus Gland; Uridine	1974
Hypoglycin A: a specific inhibitor of isovaleryl CoA dehydrogenase. Proceedings of the National Academy of Sciences of the United States of America, 1971, Volume: 68, Issue:1 Topics: Acidosis; Alanine; Amino Acid Metabolism, Inborn Errors; Animals; Butyrates; Caproates; Carbon Dioxide; Carbon Isotopes; Carnitine; Chromatography, Gas; Coenzyme A; Cyclopropanes; In Vitro Techniques; Isoleucine; Leucine; Male; Oxidoreductases; Plant Poisoning; Rats; Valerates; Vomiting	1971
Metabolic factors affecting protein synthesis by lung in vitro. Journal of applied physiology, 1971, Volume: 30, Issue:1 Topics: Albumins; Aminobutyrates; Animals; Carbon Dioxide; Carbon Isotopes; Carnitine; Citric Acid Cycle; Glucose; Hypoxia; In Vitro Techniques; Leucine; Lung; Male; Malonates; Oxidation-Reduction; Palmitic Acids; Protein Biosynthesis; Rabbits	1971
Degradation of branched-chain amino acids and 2-oxo acids in human and rat muscle. Biochemical medicine, 1980, Volume: 24, Issue:2 Topics: Amino Acids, Branched-Chain; Animals; Carnitine; Hemiterpenes; Humans; Keto Acids; Leucine; Liver; Male; Mitochondria, Muscle; Muscles; Oxidation-Reduction; Rats; Valine	1980
Efficacy of drug regimen exceeds electrostimulation in treatment of avian muscular dystrophy. Journal of applied physiology (Bethesda, Md. : 1985), 1995, Volume: 78, Issue:6 Topics: Age Factors; Animals; Carnitine; Chickens; Cinanserin; Drug Combinations; Electric Stimulation Therapy; Glucose; Injections, Intraperitoneal; Insulin; Leucine; Muscular Dystrophy, Animal; Stanozolol	1995
Ketogenic flux from lipids and leucine, assessment in 3-hydroxy-3-methylglutaryl CoA lyase deficiency. Biochemical Society transactions, 1995, Volume: 23, Issue:3 Topics: Carnitine; Child; Humans; Ketone Bodies; Leucine; Lipid Metabolism; Magnetic Resonance Spectroscopy; Male; Oxo-Acid-Lyases; Valerates	1995
3-Hydroxyisovalerylcarnitine in 3-methylcrotonyl-CoA carboxylase deficiency. Journal of inherited metabolic disease, 1995, Volume: 18, Issue:5 Topics: Carbon-Carbon Ligases; Carnitine; Deuterium; Female; Fibroblasts; Gas Chromatography-Mass Spectrometry; Humans; Infant; Leucine; Ligases; Mass Spectrometry	1995
Isovaleric acidemia: response to a leucine load after three weeks of supplementation with glycine, L-carnitine, and combined glycine-carnitine therapy. The Journal of pediatrics, 1996, Volume: 129, Issue:3 Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids	1996
Effect of carnitine administration on glycine metabolism in patients with isovaleric acidemia: significance of acetylcarnitine determination to estimate the proper carnitine dose. The Tohoku journal of experimental medicine, 1996, Volume: 179, Issue:2 Topics: Acetylcarnitine; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biomarkers; Carnitine; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Leucine; Male; Pentanoic Acids	1996
3-Methylcrotonyl-coenzyme A carboxylase deficiency in Amish/Mennonite adults identified by detection of increased acylcarnitines in blood spots of their children. The Journal of pediatrics, 1998, Volume: 132, Issue:3 Pt 1 Topics: Adult; Amino Acid Metabolism, Inborn Errors; Carbon-Carbon Ligases; Carnitine; Child, Preschool; Christianity; Female; Humans; Infant, Newborn; Leucine; Mothers; Pennsylvania; Spectrometry, Mass, Fast Atom Bombardment	1998
Improvement in exercise tolerance in isovaleric acidaemia with L-carnitine therapy. Journal of inherited metabolic disease, 1998, Volume: 21, Issue:2 Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Exercise; Female; Hemiterpenes; Humans; Leucine; Pentanoic Acids	1998
Metabolic stroke in isolated 3-methylcrotonyl-CoA carboxylase deficiency. European journal of pediatrics, 1999, Volume: 158, Issue:9 Topics: Amino Acid Metabolism, Inborn Errors; Carbon-Carbon Ligases; Carnitine; Diet, Protein-Restricted; Failure to Thrive; Female; Gliosis; Hemiplegia; Humans; Infant; Intellectual Disability; Leucine; Seizures	1999
Characterization of plasma acylcarnitines in patients under valproate monotherapy using ESI-MS/MS. Clinical biochemistry, 2001, Volume: 34, Issue:8 Topics: Adolescent; Adult; Aged; Anticonvulsants; Carnitine; Female; Humans; Leucine; Male; Middle Aged; Mitochondrial Trifunctional Protein; Multienzyme Complexes; Spectrometry, Mass, Electrospray Ionization; Valerates; Valproic Acid	2001
Functional domains in the carnitine transporter OCTN2, defective in primary carnitine deficiency. The Journal of biological chemistry, 2003, Nov-28, Volume: 278, Issue:48 Topics: Amino Acid Sequence; Animals; Arginine; Binding Sites; Biological Transport; Carnitine; Carrier Proteins; CHO Cells; Cricetinae; DNA, Complementary; Dose-Response Relationship, Drug; Genetic Vectors; Humans; Kinetics; Leucine; Membrane Proteins; Membrane Transport Proteins; Models, Biological; Molecular Sequence Data; Mutagenesis, Site-Directed; Mutation; Organic Cation Transport Proteins; Protein Structure, Tertiary; Sodium; Solute Carrier Family 22 Member 5; Symporters; Threonine; Time Factors	2003
Carnitine/organic cation transporter OCTN2-mediated transport of carnitine in primary-cultured epididymal epithelial cells. Reproduction (Cambridge, England), 2005, Volume: 130, Issue:6 Topics: Acetylcarnitine; Amino Acid Transport Systems; Animals; Betaine; Biological Transport; Carnitine; Cells, Cultured; Dose-Response Relationship, Drug; Epididymis; Epithelial Cells; Leucine; Lysine; Male; Organic Cation Transport Proteins; Pyrilamine; Quinidine; Rats; Rats, Sprague-Dawley; Reverse Transcriptase Polymerase Chain Reaction; RNA; Sodium; Solute Carrier Family 22 Member 5; Time Factors	2005
Glucose and leucine kinetics in idiopathic ketotic hypoglycaemia. Archives of disease in childhood, 2006, Volume: 91, Issue:6 Topics: Alanine; Amino Acids, Branched-Chain; Basal Metabolism; Calorimetry, Indirect; Carnitine; Case-Control Studies; Child; Child, Preschool; Fasting; Female; Glucose; Humans; Hypoglycemia; Infant; Insulin; Ketosis; Leucine; Male	2006
A Delphi-based consensus clinical practice protocol for the diagnosis and management of 3-methylcrotonyl CoA carboxylase deficiency. Molecular genetics and metabolism, 2008, Volume: 93, Issue:4 Topics: Carbon-Carbon Ligases; Carnitine; Delphi Technique; Energy Intake; Humans; Infant, Newborn; Leucine; Metabolism, Inborn Errors; Mothers; Neonatal Screening	2008
Anesthetic management of a patient with 3-methylcrotonyl-CoA carboxylase deficiency. Anesthesia and analgesia, 2008, Volume: 107, Issue:2 Topics: Adult; Amino Acid Metabolism, Inborn Errors; Anesthesia, General; Carbon-Carbon Ligases; Cardiomyopathies; Carnitine; Female; Humans; Leucine	2008
A polarized localization of amino acid/carnitine transporter B(0,+) (ATB(0,+)) in the blood-brain barrier. Biochemical and biophysical research communications, 2008, Nov-14, Volume: 376, Issue:2 Topics: Amino Acid Transport System ASC; Amino Acid Transport Systems, Neutral; Amino Acids, Cyclic; Animals; Blood-Brain Barrier; Carnitine; Cattle; Leucine; Rats	2008
[Late onset 3-HMG-CoA lyase deficiency: a rare but treatable disorder]. Archives de pediatrie : organe officiel de la Societe francaise de pediatrie, 2010, Volume: 17, Issue:1 Topics: Alleles; Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Chromosome Aberrations; Combined Modality Therapy; Diet, Protein-Restricted; DNA Mutational Analysis; Exons; Genes, Recessive; Humans; Hypoglycemia; Leucine; Male; Meglutol; Oxo-Acid-Lyases; Polymerase Chain Reaction; Rare Diseases; Sequence Analysis, DNA	2010
Comparison of amino acids and acylcarnitines assay methods used in newborn screening assays by tandem mass spectrometry. Clinica chimica acta; international journal of clinical chemistry, 2010, May-02, Volume: 411, Issue:9-10 Topics: Amino Acids; Butanols; Carnitine; Humans; Infant, Newborn; Leucine; Metabolic Diseases; Methionine; Neonatal Screening; Palmitoylcarnitine; Phenylalanine; Quality Control; Tandem Mass Spectrometry	2010
L-carnitine and taurine synergistically inhibit the proliferation and osteoblastic differentiation of vascular smooth muscle cells. Acta pharmacologica Sinica, 2010, Volume: 31, Issue:3 Topics: Animals; Atherosclerosis; Calcium; Carnitine; Cell Differentiation; Cell Proliferation; Cells, Cultured; DNA; Gene Expression Regulation; Humans; Leucine; Membrane Glycoproteins; Membrane Transport Proteins; Muscle, Smooth, Vascular; Myocytes, Smooth Muscle; Osteoblasts; Rats; Taurine; Thymidine	2010
Urinary excretion of 3-hydroxyisovaleric acid and 3-hydroxyisovaleryl carnitine increases in response to a leucine challenge in marginally biotin-deficient humans. The Journal of nutrition, 2011, Volume: 141, Issue:11 Topics: Adult; Biotin; Carnitine; Cohort Studies; Female; Humans; Leucine; Male; Valerates	2011
Leucine and protein metabolism in obese Zucker rats. PloS one, 2013, Volume: 8, Issue:3 Topics: 3-Methyl-2-Oxobutanoate Dehydrogenase (Lipoamide); Adipose Tissue; Amino Acids, Branched-Chain; Animals; Biomarkers; Body Weight; Carbon Radioisotopes; Carnitine; Chromatography, Liquid; Creatinine; Leucine; Liver; Male; Metabolomics; Muscle, Skeletal; Obesity; Organ Size; Proteins; Rats; Rats, Zucker; Tandem Mass Spectrometry	2013
Prevention of DNA damage by L-carnitine induced by metabolites accumulated in maple syrup urine disease in human peripheral leukocytes in vitro. Gene, 2014, Sep-15, Volume: 548, Issue:2 Topics: Carnitine; Comet Assay; DNA Damage; Energy Metabolism; Humans; Keto Acids; Leucine; Leukocytes; Maple Syrup Urine Disease; Oxidative Stress; Vitamin B Complex	2014
Branched chain amino acid metabolism profiles in progressive human nonalcoholic fatty liver disease. Amino acids, 2015, Volume: 47, Issue:3 Topics: Carnitine; Female; Gene Expression Profiling; Humans; Isoleucine; Leucine; Male; Metabolomics; Non-alcoholic Fatty Liver Disease; Signal Transduction; Valine	2015
Association between arterial stiffness and serum L-octanoylcarnitine and lactosylceramide in overweight middle-aged subjects: 3-year follow-up study. PloS one, 2015, Volume: 10, Issue:3 Topics: Adult; Antigens, CD; Blood Pressure; Body Mass Index; Carnitine; Case-Control Studies; Humans; Lactosylceramides; Leucine; Middle Aged; Overweight; Vascular Stiffness	2015
Newborn screening blood spot analysis in the UK: influence of spot size, punch location and haematocrit. Journal of medical screening, 2016, Volume: 23, Issue:1 Topics: Amino Acids; Blood Specimen Collection; Carnitine; Dried Blood Spot Testing; Heel; Hematocrit; Humans; Infant, Newborn; Leucine; Linear Models; Methionine; Neonatal Screening; Phenylalanine; Thyrotropin; Trypsinogen; Tyrosine; United Kingdom	2016
Metabolic changes in serum metabolome in response to a meal. European journal of nutrition, 2017, Volume: 56, Issue:2 Topics: Aged; Amino Acids; Blood Glucose; Bread; Carnitine; Dietary Carbohydrates; Dietary Fats; Dietary Fiber; Dietary Proteins; Energy Metabolism; Fasting; Female; Glycolysis; Humans; Insulin; Ketone Bodies; Leucine; Meals; Metabolome; Middle Aged; Phospholipids; Postmenopause; Postprandial Period; Triticum	2017
Effects of low and high doses of fenofibrate on protein, amino acid, and energy metabolism in rat. International journal of experimental pathology, 2020, Volume: 101, Issue:5 Topics: Amino Acids; Amino Acids, Branched-Chain; Animals; Carnitine; Energy Metabolism; Fenofibrate; Glycine; Hepatomegaly; Humans; Hypolipidemic Agents; Leucine; Liver; Lysine; Male; Methionine; Muscle, Skeletal; Oxidation-Reduction; Proteins; Rats; Rats, Wistar	2020
Triangulating evidence from longitudinal and Mendelian randomization studies of metabolomic biomarkers for type 2 diabetes. Scientific reports, 2021, 03-18, Volume: 11, Issue:1 Topics: Adult; Aged; Betaine; Biomarkers; Carnitine; Case-Control Studies; Diabetes Mellitus, Type 2; Early Diagnosis; Female; Genetic Predisposition to Disease; Glutamic Acid; Humans; Leucine; Lysine; Male; Mannose; Mendelian Randomization Analysis; Metabolome; Middle Aged; Valine	2021
How to Screen and Prevent Metabolic Syndrome in Patients of PCOS Early: Implications From Metabolomics. Frontiers in endocrinology, 2021, Volume: 12 Topics: Adolescent; Adult; Biomarkers; Carnitine; Female; Glutamic Acid; Humans; Leucine; Metabolic Syndrome; Metabolomics; Polycystic Ovary Syndrome; ROC Curve; Young Adult	2021
The association between plasma metabolites and future risk of all-cause mortality. Journal of internal medicine, 2022, Volume: 292, Issue:5 Topics: Biomarkers; Carnitine; Glutamates; Histidine; Humans; Leucine; Lysine; Metabolomics; Prospective Studies; Tryptophan; Valine	2022
Identifying a metabolomics profile associated with masked hypertension in two independent cohorts: Data from the African-PREDICT and SABPA studies. Hypertension research : official journal of the Japanese Society of Hypertension, 2022, Volume: 45, Issue:11 Topics: Amino Acids; Carnitine; Humans; Isoleucine; Leucine; Masked Hypertension; Metabolomics; Methionine; Phenylalanine; Valine	2022
Metabolomic profiling of bovine leucocytes transformed by Theileria annulata under BW720c treatment. Parasites & vectors, 2022, Oct-05, Volume: 15, Issue:1 Topics: Animals; Arginine; Carnitine; Cattle; Dimethyl Sulfoxide; Leucine; Naphthoquinones; Theileria; Theileria annulata; Theileriasis	2022
L-Carnitine Combined with Leucine Supplementation Does Not Improve the Effectiveness of Progressive Resistance Training in Healthy Aged Women. The journal of nutrition, health & aging, 2022, Volume: 26, Issue:10 Topics: Aged; Carnitine; Decorin; Dietary Supplements; Female; Humans; Insulin-Like Growth Factor I; Leucine; Middle Aged; Muscle Strength; Muscle, Skeletal; Myostatin; Resistance Training; Tartrates	2022
Twenty-Four Weeks of L-Carnitine Combined with Leucine Supplementation Does Not Increase the Muscle Carnitine Content in Healthy Active Subjects. Annals of nutrition & metabolism, 2023, Volume: 79, Issue:2 Topics: Carnitine; Dietary Supplements; Humans; Leucine; Muscle, Skeletal; Proto-Oncogene Proteins c-akt; TOR Serine-Threonine Kinases; Young Adult	2023
L-Lysine supplementation affects dietary protein quality and growth and serum amino acid concentrations in rats. Scientific reports, 2023, Nov-15, Volume: 13, Issue:1 Topics: Amino Acids; Animals; Asparagine; Carnitine; Caseins; Diet; Dietary Proteins; Dietary Supplements; Histidine; Leucine; Lysine; Male; Methionine; Ornithine; Racemethionine; Rats; Rats, Sprague-Dawley; Tryptophan; Valine; Weight Gain	2023