carnitine and isobutyryl-1-carnitine

carnitine has been researched along with isobutyryl-1-carnitine in 10 studies

Research

Studies (10)

TimeframeStudies, this research(%)All Research%
pre-19902 (20.00)18.7374
1990's2 (20.00)18.2507
2000's2 (20.00)29.6817
2010's1 (10.00)24.3611
2020's3 (30.00)2.80

Authors

AuthorsStudies
Bieber, LL; Choi, YR; Clarke, PR1
Ichiki, T; Kobayashi, M; Nohara, D; Sakuma, T; Sugiyama, N; Wada, Y1
Miotto, G; Siliprandi, N; Venerando, R1
Cederbaum, SD; Galindo, A; Mardach, R; Roe, CR; Roe, DS; Sweetman, L1
An, Y; Bali, D; Benjamin, DK; Chaing, SH; Chen, YT; Gregersen, NS; Kishnani, PS; Koeberl, DD; McDonald, MT; Millington, DS; Smith, WE; Vockley, J; Weavil, SD; Young, SP1
Belanger-Quintana, A; Bischoff, C; de la Mota, JL; Ferrer, I; García, MJ; Gregersen, N; Martin-Hernández, E; Martínez Pardo, M; Merinero, B; Pérez-Cerdá, C; Ruiz Sala, P; Ugarte, M; Vianey-Saban, C1
Forni, S; Fu, X; Palmer, SE; Sweetman, L1
Costales, C; Holliman, CL; Horlbogen, L; Luo, L; Mathialagan, S; Ramanathan, R; Rodrigues, AD; Vourvahis, M1
Amano, I; Hatanaka, Y; Ikuno, M; Matsuzawa, SI; Takahashi, R; Uemura, N; Yamakado, H1
Brose, SA; Hobert, JA; Pasquali, M1

Other Studies

10 other study(ies) available for carnitine and isobutyryl-1-carnitine

ArticleYear
Studies on the oxidation of isobutyrylcarnitine by beef and rat liver mitochondria.
    The Journal of biological chemistry, 1979, Jul-10, Volume: 254, Issue:13

    Topics: Animals; Carnitine; Cattle; Kinetics; Mitochondria, Liver; Oxidation-Reduction; Rats; Species Specificity

1979
Analysis of acylcarnitines in maternal urine for prenatal diagnosis of glutaric aciduria type 2.
    Prenatal diagnosis, 1991, Volume: 11, Issue:2

    Topics: Abortion, Induced; Amino Acid Metabolism, Inborn Errors; Amniotic Fluid; Carnitine; Female; Glutarates; Humans; Pregnancy; Prenatal Diagnosis

1991
Inhibitory action of isovaleryl-L-carnitine on proteolysis in perfused rat liver.
    Biochemical and biophysical research communications, 1989, Feb-15, Volume: 158, Issue:3

    Topics: Animals; Carnitine; Dose-Response Relationship, Drug; Leucine; Liver; Male; Peptide Hydrolases; Proteins; Rats; Rats, Inbred Strains

1989
Isolated isobutyryl-CoA dehydrogenase deficiency: an unrecognized defect in human valine metabolism.
    Molecular genetics and metabolism, 1998, Volume: 65, Issue:4

    Topics: Cardiomyopathies; Carnitine; Child, Preschool; Female; Fibroblasts; Humans; Infant; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Palmitic Acids; Substrate Specificity; Valine

1998
Rare disorders of metabolism with elevated butyryl- and isobutyryl-carnitine detected by tandem mass spectrometry newborn screening.
    Pediatric research, 2003, Volume: 54, Issue:2

    Topics: Butyryl-CoA Dehydrogenase; Carnitine; Cells, Cultured; Fibroblasts; Humans; Infant, Newborn; Mass Spectrometry; Metabolism, Inborn Errors; Neonatal Screening; Oxidoreductases Acting on CH-CH Group Donors

2003
Persistent increase of plasma butyryl/isobutyrylcarnitine concentrations as marker of SCAD defect and ethylmalonic encephalopathy.
    Journal of inherited metabolic disease, 2006, Volume: 29, Issue:5

    Topics: Brain Diseases; Butyryl-CoA Dehydrogenase; Carnitine; Humans; Malonates; Mitochondrial Proteins; Nervous System Diseases; Nucleocytoplasmic Transport Proteins

2006
Rapid determination of C4-acylcarnitine and C5-acylcarnitine isomers in plasma and dried blood spots by UPLC-MS/MS as a second tier test following flow-injection MS/MS acylcarnitine profile analysis.
    Molecular genetics and metabolism, 2010, Volume: 101, Issue:1

    Topics: Carnitine; Chromatography, Liquid; Humans; Infant, Newborn; Isomerism; Neonatal Screening; Tandem Mass Spectrometry

2010
A Multiplexed HILIC-MS/HRMS Assay for the Assessment of Transporter Inhibition Biomarkers in Phase I Clinical Trials: Isobutyryl-Carnitine as an Organic Cation Transporter (OCT1) Biomarker.
    Analytical chemistry, 2020, 07-21, Volume: 92, Issue:14

    Topics: Biomarkers; Carnitine; Clinical Trials, Phase I as Topic; Drug Interactions; Enzyme Inhibitors; Humans; Metformin; Organic Cation Transport Proteins; Organic Cation Transporter 1; Organic Cation Transporter 2

2020
Mitochondrial dysfunction in a mouse model of prodromal Parkinson's disease: A metabolomic analysis.
    Neuroscience letters, 2021, 11-20, Volume: 765

    Topics: Animals; Biomarkers; Carnitine; Disease Models, Animal; Metabolomics; Mice; Mitochondria; Parkinsonian Disorders; Prodromal Symptoms

2021
Quantitation of Butyrylcarnitine, Isobutyrylcarnitine, and Glutarylcarnitine in Urine Using Ultra-Performance Liquid Chromatography-Tandem Mass Spectrometry (UPLC-MS/MS).
    Methods in molecular biology (Clifton, N.J.), 2022, Volume: 2546

    Topics: Carnitine; Chromatography, High Pressure Liquid; Chromatography, Liquid; Coenzyme A; Fatty Acids; Tandem Mass Spectrometry

2022