carnitine and glycine

carnitine has been researched along with glycine in 95 studies

Research

Studies (95)

TimeframeStudies, this research(%)All Research%
pre-199020 (21.05)18.7374
1990's25 (26.32)18.2507
2000's14 (14.74)29.6817
2010's24 (25.26)24.3611
2020's12 (12.63)2.80

Authors

AuthorsStudies
Barnes, JC; Bradley, P; Day, NC; Fourches, D; Reed, JZ; Tropsha, A1
Henderson, LM; Hochalter, JB1
Orii, T; Previs, SF; Rinaldo, P; Shimizu, N; Yamaguchi, S1
Dan, M; Fujioka, M; Kanaoka, H; Kikawa, Y; Shigematsu, Y; Sudo, M1
Fellenius, E; Ichihara, K; Mjøs, OD; Myrmel, T; Neely, JR1
Gargus, JJ; O'Shea, JJ; Previs, SF; Rinaldo, P; Schmidt-Sommerfeld, E; Welch, RD; Zinn, AB1
Bennett, MJ; Coates, PM; Hale, DE; Millington, DS; Pollitt, RJ; Rinaldo, P; Roe, CR; Tanaka, K1
Africk, D; Blitzer, M; Mandel, H; Shapira, E1
Fennessey, PV; Goodman, SI; Hill, RE; Miller, LV; O'Shea, JJ; Rinaldo, P; Tanaka, K; Whelan, DT1
Amendt, BA; Armstrong, D; Inoue, F; Millington, DS; Rhead, WJ; Wood, PA1
Bartlett, K; Eyre, JA; Fisher, J; Gardner-Medwin, D; Johnson, MA; Turnbull, DM; Watmough, NJ1
Berry, GT; Segal, S; Yudkoff, M1
Hokland, B; Jodalen, H; Mjøs, OD; Moen, P; Ytrehus, K1
Liedtke, AJ; Molaparast-Saless, F; Nellis, SH1
Inoue, F; Maltby, DA; Millington, DS; Roe, CR1
Bielefeld, DR; Neely, JR; Vary, TC1
Bradley, D; Chalmers, RA; de Sousa, C; Stacey, TE; Tracey, BM; Weaver, C1
Bradley, D; Chalmers, RA; de Sousa, C; Stacey, TE; Tracey, BM; Weaver, CM1
McGroarty, E; Tolbert, NE1
Müller, DM; Strack, E1
Aurich, H; Kleber, HP3
Kleber, HP1
Bohan, TP; Roe, CR1
Bohan, TP; Kahler, SG; Maltby, DA; Millington, DS; Roe, CR1
Berry, GT; Millington, D; Rutledge, SL; Stanley, CA; van Hove, JL1
Madden, MC; McMillin, JB; Pike, MM; Pohost, GM; Wołkowicz, PE1
de Wet, WJ; Erasmus, E; Gibson, KM; Jooste, S; Mienie, LJ1
Barbato, R; Burlina, AB; De Tullio, R; Di Lisa, F; Menabŏ, R; Salamino, F; Siliprandi, N1
Corr, PB; Donahue, K; Kléber, AG; McHowat, J; Peirick, J; Yamada, KA; Yan, GX1
Heales, SJ; Leonard, JV; Posca, AP; Rinaldo, P; Schmidt-Sommerfeld, E; Woolf, DA1
Chiba, T; Ito, T; Kajita, M; Kidouchi, K; Niwa, T; Sugiyama, N; Wada, Y1
Berry, SA; Gage, DA; Huang, ZH; Iwamoto, T; Johnston, K; Millington, DS; Packman, S; Röschinger, W; Sweetman, L; Yano, S1
Brummond, MR; Kahler, SG; Kishnani, P; Lachiewicz, AM; Millington, DS; Muenzer, J; Summar, ML; Van Hove, JL; Wenstrup, RJ1
Bakkeren, J; Baumgartner, R; de Jong, J; Mourmans, J; Suormala, T; van Diggelen, OP; Wendel, U; Wevers, R1
Fries, MH; Jurecki, E; Packman, S; Rinaldo, P; Schmidt-Sommerfeld, E1
Ito, T; Itoh, T; Kidouchi, K; Mizuguchi, K; Ohba, S; Sugiyama, N; Yamaguchi, S1
Kanazu, T; Yamaguchi, T1
Davis, JA; Roeser, NF; Venkatachalam, MA; Weinberg, JM1
Jiménez, C; Lluch-Fernández, MD; Marchante-Serrano, C; Navarro-Quesada, FJ; Vaquero-Abellán, M1
Bykov, IL; Shigematsu, E1
Carregal, M; Dalamon, V; Savino, EA; Testoni, G; Varela, A1
Artuch, R; Lambruschini, N; Moyano, D; Vilaseca, MA1
Felipo, V; Llansola, M1
de Hoffmann, E; Libert, R; Nassogne, MC; Schanck, A; Stroobant, V; Thillaye, M; Van Hoof, F; Vincent, MF1
Sachan, DS; Yatim, AM1
Albers, S; Irons, M; Levy, HL; Marsden, D; Strauss, AW1
Kong, JY; Rabkin, SW1
Borovoy, J; Korson, MS; Nurko, S; Prasad, C1
Andresen, BS; Angel, L; Bennetts, B; Carpenter, K; Waddell, L; Wilcken, B; Wiley, V1
Benet, LZ; Bjørnsdottir, I; Hansen, SH; Li, C; Olsen, J; Sidenius, U1
Chace, DH; Kohli, R; Wainwright, MS; Whitington, PF1
Bodamer, OA; Heinze, G; Holub, M; Mühl, A; Ratschmann, R; Sperl, W; Strnadová, KA; Tuschl, K1
Asakura, H; Igimi, S; Makino, S; Okada, N; Okada, Y; Yamamoto, S1
Bennett, MJ1
Ganapathy, V; Prasad, PD; Shekhawat, PS; Srinivas, SR; Umapathy, NS1
Bloomer, RJ; Fry, AC; Smith, WA; Tschume, LC1
Baumgartner, MR; Biberoglu, G; Demir, E; Eminoglu, FT; Hasanoglu, A; Okur, I; Ozcelik, AA; Tumer, L1
Bloomer, RJ; Smith, WA; Tschume, LC1
Deigner, HP; Enot, D; Keller, M; Koal, T; Saugstad, OD; Scholl-Bürgi, S; Solberg, R1
Gavrilov, D; Highsmith, WE; Matern, D; McHugh, D; Oglesbee, D; Raymond, K; Rinaldo, P; Smith, EH; Thomas, C; Tortorelli, S1
Hata, I; Shigematsu, Y; Tajima, G1
Arica, SG; Arica, V; Dag, H; Gülbayzar, S; Obut, O; Onur, H1
Adamski, J; Gieger, C; Illig, T; Kronenberg, F; Krumsiek, J; Meitinger, T; Mittelstrass, K; Peters, A; Polonikov, A; Prehn, C; Ried, JS; Roemisch-Margl, W; Suhre, K; Theis, FJ; Wang-Sattler, R; Weidinger, S; Wichmann, HE; Yu, Z1
Baumgartner, MR; Burda, P; Bürer, C; Fowler, B; Grünert, SC; Morscher, RJ; Suormala, T1
Fong, BM; Leung, KS; Tam, S1
Carland, JE; Mansfield, RE; Ryan, RM; Vandenberg, RJ1
Igarashi, K; Katsumi, T; Nishise, Y; Okumoto, K; Saito, K; Saito, T; Sato, C; Shao, L; Soga, T; Sugimoto, M; Tomita, K; Tomita, M; Ueno, Y; Watanabe, H1
Boix, H; Knaepper-Martin, S1
Abdin, MZ; Ahad, A; Farooqi, H; Ganai, AA; Jahan, S1
Cedazo-Mínguez, Á; Cifuentes, A; Ibáñez, C; Lodeiro, M; Simó, C1
Amaral, AF1
Bousquet, J; Loureiro, CC; Rocha, SM; Todo Bom, A1
Akiba, K; Aoyama, Y; Fukao, T; Goto, M; Hasegawa, Y; Hashimoto, T; Hori, T; Kuwayama, N; Morita, M; Moriyama, Y; Murayama, K; Ohtake, A; Shigematsu, Y; Usuda, N; Venkatesan, R; Wierenga, R1
Bo, R; Hasegawa, Y; Ishige, N; Kobayashi, H; Nakamura, M; Takahashi, T; Yamada, K; Yamaguchi, S1
Aadland, EK; Bertram, HC; Clausen, MR; Eng, Ø; Graff, IE; Holthe, A; Jacques, H; Lavigne, C; Liaset, B; Mellgren, G; Schmedes, M; Sundekilde, UK; Young, JF1
Farooqi, H; Ganai, AA; Ganaie, IA; Verma, N1
Aldamiz-Echevarría, L; Barros, P; Belanger-Quintana, A; Blasco, J; Bueno, MA; Couce, ML; Fernández-Marmiesse, A; García-Silva, MT; Márquez-Armenteros, AM; Navarrete, R; Pérez, B; Pérez-Cerdá, C; Vitoria, I; Vives, I1
Appelblom, H; Gissler, M; Nevalainen, J; Ryynänen, M; Sairanen, M; Timonen, S1
Alarcón Riquelme, ME; Beretta, L; Borrás-Linares, I; Fernández-Ochoa, Á; Gemperline, D; Quirantes-Piné, R; Segura-Carretero, A1
Iloki-Assanga, S; Lujany, LML; McCarty, MF1
He, R; Jin, Y; Kang, L; Li, Y; Liu, Y; Luo, L; Shen, M; Song, J; Yang, Y1
Arning, E; Ashcraft, P; Bottiglieri, T; Brown, M; Gibson, KM; Jansen, E; Kirby, T; Rinaldo, P; Roullet, JB; Salomons, GS; Turgeon, C; Walters, DC1
Holeček, M; Vodeničarovová, M1
Beger, RD; Cao, Z; Nakamura, N; Pence, LM1
Agnoli, C; Allen, N; Amiano, P; Biessy, C; Christakoudi, S; Colorado-Yohar, SM; Crous-Bou, M; Dimou, N; Dossus, L; Fortner, R; Gram, IT; Gunter, MJ; Gurrea, AB; Heath, AK; Kaaks, R; Keun, HC; Kouloura, E; Lécuyer, L; Mattiello, A; Merritt, MA; Nøst, TH; Palli, D; Rinaldi, S; Rothwell, JA; Sacerdote, C; Sánchez, MJ; Schmidt, JA; Schulze, MB; Severi, G; Siskos, AP; Travis, RC; Tsilidis, KK; Tumino, R; Vermeulen, R; Viallon, V; Weiderpass, E1
Agudo, A; Aleksandrova, K; Amos, CI; Barranco, MR; Barricarte, A; Bochers, CH; Brennan, P; Cerani, A; Chirlaque-López, MD; Gram, IT; Grankvist, K; Guida, F; Han, J; Hung, RJ; Imaz, L; Johansson, M; Kaaks, R; Kühn, T; Martin, RM; McKay, JD; Nøst, TH; Pala, V; Richards, JB; Robbins, HA; Sandanger, TM; Schibli, D; Schulze, MB; Smith-Byrne, K; Travis, RC; Vineis, P; Weiderpass, E; Zhou, S1
Gu, S; Liu, D; Ma, Z; Wang, J; Xiao, L; Zhou, Z; Zuo, H1
Brumarová, R; Dobešová, D; Friedecký, D; Jahn, P; Kopecká, A; Tóthová, K1
De Grassi, A; Giangregorio, N; Incampo, G; Indiveri, C; Pierri, CL; Tonazzi, A; Tragni, V1
Canizales-Quinteros, S; Flores, YN; Ibarra-González, I; León-Reyes, G; Palacios-González, B; Rivera-Paredez, B; Salmerón, J; Vela-Amieva, M; Velázquez-Cruz, R1
Aon, J; Luo, Y; Orzechowski, K; Patel, P; Sevin, D; Vappiani, J1
Kraemer, T; Steuer, AE; Steuer, C; Sutter, L1
Bavato, F; Bosch, OG; Dornbierer, DA; Kraemer, T; Quednow, BB; Schnider, LK; Seifritz, E; Steuer, AE; Steuer, C1

Reviews

3 review(s) available for carnitine and glycine

ArticleYear
Enzymes in peroxisomes.
    The journal of histochemistry and cytochemistry : official journal of the Histochemistry Society, 1973, Volume: 21, Issue:11

    Topics: Acyltransferases; Alcohol Oxidoreductases; Carnitine; Chloroplasts; Fatty Acids; Glyceric Acids; Glycerolphosphate Dehydrogenase; Glycine; Glycolates; Glyoxylates; Kidney; L-Lactate Dehydrogenase; Liver; Malate Dehydrogenase; Malates; Microbodies; Organoids; Plant Cells; Plants; Serine

1973
Assays of fatty acid beta-oxidation activity.
    Methods in cell biology, 2007, Volume: 80

    Topics: Acids; Biological Transport, Active; Carnitine; Fatty Acids; Glycine; Humans; Lipid Metabolism; Mitochondria; Models, Biological; Oxidation-Reduction

2007
[Amplitude-integrated electroencephalography in non-ketotic hyperglycinaemia].
    Revista de neurologia, 2014, Jan-01, Volume: 58, Issue:1

    Topics: Carnitine; Consanguinity; Dextromethorphan; Drug Therapy, Combination; Early Diagnosis; Electroencephalography; Fatal Outcome; Glycine; Humans; Hyperglycinemia, Nonketotic; Infant, Newborn; Monitoring, Physiologic; Myoclonus; Sodium Benzoate; Treatment Failure

2014

Trials

4 trial(s) available for carnitine and glycine

ArticleYear
Effect of glycine propionyl-L-carnitine on aerobic and anaerobic exercise performance.
    International journal of sport nutrition and exercise metabolism, 2008, Volume: 18, Issue:1

    Topics: Adolescent; Adult; Carnitine; Dietary Supplements; Double-Blind Method; Exercise; Female; Glycine; Humans; Male; Muscle, Skeletal; Oxygen Consumption; Physical Endurance

2008
Glycine propionyl-L-carnitine modulates lipid peroxidation and nitric oxide in human subjects.
    International journal for vitamin and nutrition research. Internationale Zeitschrift fur Vitamin- und Ernahrungsforschung. Journal international de vitaminologie et de nutrition, 2009, Volume: 79, Issue:3

    Topics: Adolescent; Adult; Blood Cell Count; Blood Chemical Analysis; Carnitine; Cholesterol; Double-Blind Method; Exercise; Glycine; Humans; Lipid Metabolism; Malondialdehyde; Nitric Oxide; Triglycerides; Young Adult

2009
Dynamics of serum metabolites in patients with chronic hepatitis C receiving pegylated interferon plus ribavirin: a metabolomics analysis.
    Metabolism: clinical and experimental, 2013, Volume: 62, Issue:11

    Topics: Adult; Aged; Antiviral Agents; Area Under Curve; Betaine; Carnitine; Chromatography, Liquid; Drug Therapy, Combination; Female; Glycine; Hepatitis C, Chronic; Humans; Interferons; Male; Metabolomics; Middle Aged; Polyethylene Glycols; Principal Component Analysis; Ribavirin; Tandem Mass Spectrometry; Treatment Outcome; Tryptophan; Viral Load

2013
Lean-seafood intake decreases urinary markers of mitochondrial lipid and energy metabolism in healthy subjects: Metabolomics results from a randomized crossover intervention study.
    Molecular nutrition & food research, 2016, Volume: 60, Issue:7

    Topics: Adolescent; Adult; Aged; Biomarkers; Carnitine; Cross-Over Studies; Diet; Dietary Proteins; Energy Metabolism; Female; Glycine; Healthy Volunteers; Humans; Lipid Metabolism; Male; Metabolomics; Methylamines; Methylhistidines; Middle Aged; Mitochondria; Pyridones; Seafood; Young Adult

2016

Other Studies

88 other study(ies) available for carnitine and glycine

ArticleYear
Cheminformatics analysis of assertions mined from literature that describe drug-induced liver injury in different species.
    Chemical research in toxicology, 2010, Volume: 23, Issue:1

    Topics: Animals; Chemical and Drug Induced Liver Injury; Cluster Analysis; Databases, Factual; Humans; MEDLINE; Mice; Models, Chemical; Molecular Conformation; Quantitative Structure-Activity Relationship

2010
Carnitine biosynthesis: the formation of glycine from carbons 1 and 2 of 6-N-trimethyl-L-lysine.
    Biochemical and biophysical research communications, 1976, May-17, Volume: 70, Issue:2

    Topics: Animals; Carnitine; Glycine; Hippurates; Lysine; Male; Rats

1976
Mass spectrometric analysis of metabolite excretion in five Japanese patients with the late-onset form of glutaric aciduria type II.
    Biological mass spectrometry, 1991, Volume: 20, Issue:8

    Topics: Acids; Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Female; Gas Chromatography-Mass Spectrometry; Glutarates; Glycine; Humans; Infant; Japan; Male; Phenotype; Spectrometry, Mass, Fast Atom Bombardment

1991
Prenatal diagnosis of isovaleric acidemia by fast atom bombardment and tandem mass spectrometry.
    Clinica chimica acta; international journal of clinical chemistry, 1991, Dec-16, Volume: 203, Issue:2-3

    Topics: Amniotic Fluid; Carnitine; Female; Fetal Diseases; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Pregnancy; Prenatal Diagnosis; Spectrometry, Mass, Fast Atom Bombardment

1991
Fatty acids suppress recovery of heart function after hypothermic perfusion.
    The Annals of thoracic surgery, 1991, Volume: 52, Issue:4

    Topics: Acyl Coenzyme A; Adenosine Triphosphate; Animals; Calcium; Carnitine; Coronary Circulation; Fatty Acids; Glycine; Heart Arrest, Induced; Hypothermia, Induced; In Vitro Techniques; Male; Myocardial Reperfusion Injury; Myocardium; Palmitates; Phosphocreatine; Rats; Rats, Inbred Strains; Ventricular Function, Left; Verapamil

1991
Ethylmalonic/adipic aciduria: effects of oral medium-chain triglycerides, carnitine, and glycine on urinary excretion of organic acids, acylcarnitines, and acylglycines.
    Pediatric research, 1991, Volume: 30, Issue:3

    Topics: Acylation; Adipates; Administration, Oral; Carnitine; Child; Electron-Transferring Flavoproteins; Fatty Acid Desaturases; Female; Glycine; Humans; Iron-Sulfur Proteins; Malonates; Metabolism, Inborn Errors; Multienzyme Complexes; Oxidoreductases Acting on CH-NH Group Donors; Triglycerides

1991
Analysis of abnormal urinary metabolites in the newborn period in medium-chain acyl-CoA dehydrogenase deficiency.
    Journal of inherited metabolic disease, 1990, Volume: 13, Issue:5

    Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Carnitine; Child, Preschool; Creatinine; Dicarboxylic Acids; Gas Chromatography-Mass Spectrometry; Genetic Markers; Glycine; Humans; Infant, Newborn; Male; Trimethylsilyl Compounds

1990
The importance of recognizing secondary carnitine deficiency in organic acidaemias: case report in glutaric acidaemia type II.
    Journal of inherited metabolic disease, 1988, Volume: 11, Issue:4

    Topics: Carnitine; Electron-Transferring Flavoproteins; Fatty Acid Desaturases; Female; Fibroblasts; Glutarates; Glycine; Humans; Infant; Iron-Sulfur Proteins; Multienzyme Complexes; Oxidoreductases Acting on CH-NH Group Donors; Sarcosine

1988
Comparison of urinary acylglycines and acylcarnitines as diagnostic markers of medium-chain acyl-CoA dehydrogenase deficiency.
    Journal of inherited metabolic disease, 1989, Volume: 12 Suppl 2

    Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Acylation; Biomarkers; Carnitine; Glycine; Humans; Lipid Metabolism, Inborn Errors; Reference Values

1989
Short-chain acyl-coenzyme A dehydrogenase deficiency in mice.
    Pediatric research, 1989, Volume: 25, Issue:1

    Topics: Acyl-CoA Dehydrogenase; Animals; Carnitine; Disease Models, Animal; Fatty Acid Desaturases; Fatty Acids; Fatty Acids, Volatile; Gas Chromatography-Mass Spectrometry; Glycine; Malonates; Mice; Mice, Inbred BALB C; Oxidation-Reduction; Succinates

1989
Lipid storage myopathy due to glutaric aciduria type II: treatment of a potentially fatal myopathy.
    Developmental medicine and child neurology, 1988, Volume: 30, Issue:5

    Topics: Carnitine; Female; Glutarates; Glutaryl-CoA Dehydrogenase; Glycine; Humans; Infant; Lipid Metabolism; Metabolic Diseases; Muscles; Muscular Diseases; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Riboflavin

1988
Isovaleric acidemia: medical and neurodevelopmental effects of long-term therapy.
    The Journal of pediatrics, 1988, Volume: 113, Issue:1 Pt 1

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child Development; Dietary Proteins; Female; Glycine; Growth; Humans; Infant; Infant, Newborn; Intelligence; Isovaleryl-CoA Dehydrogenase; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors

1988
Oxfenicine-induced accumulation of lipid in the rat myocardium.
    Journal of molecular and cellular cardiology, 1988, Volume: 20, Issue:3

    Topics: Acyl Coenzyme A; Animals; Carnitine; Coenzyme A; Drug Synergism; Fatty Acids, Nonesterified; Glycine; Heart; Isoproterenol; Male; Myocardium; Rats; Rats, Inbred Strains; Sodium Chloride; Triglycerides

1988
Effects of the fatty acid blocking agents, oxfenicine and 4-bromocrotonic acid, on performance in aerobic and ischemic myocardium.
    Journal of molecular and cellular cardiology, 1987, Volume: 19, Issue:5

    Topics: Aerobiosis; Animals; Butyrates; Carnitine; Carnitine O-Palmitoyltransferase; Coronary Disease; Crotonates; Fatty Acids; Glycine; Heart; Myocardium; Oxidation-Reduction; Palmitates; Perfusion; Swine

1987
Endogenous catabolism is the major source of toxic metabolites in isovaleric acidemia.
    The Journal of pediatrics, 1987, Volume: 110, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Dietary Proteins; Glycine; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Male; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Valerates

1987
Inhibition of carnitine palmitoyl-CoA transferase activity and fatty acid oxidation by lactate and oxfenicine in cardiac muscle.
    Journal of molecular and cellular cardiology, 1985, Volume: 17, Issue:6

    Topics: Acyl Coenzyme A; Acyltransferases; Animals; Carbon Dioxide; Carnitine; Carnitine O-Palmitoyltransferase; Energy Metabolism; Glycine; Lactates; Lactic Acid; Male; Myocardium; Palmitates; Rats; Rats, Inbred Strains; Triglycerides

1985
L-carnitine and glycine therapy in isovaleric acidaemia.
    Journal of inherited metabolic disease, 1985, Volume: 8 Suppl 2

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Valerates

1985
The response to L-carnitine and glycine therapy in isovaleric acidaemia.
    European journal of pediatrics, 1986, Volume: 144, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Carboxylic Acids; Carnitine; Child, Preschool; Combined Modality Therapy; Drug Therapy, Combination; Female; Glycine; Hemiterpenes; Humans; Pentanoic Acids; Valerates

1986
[The binding energy of the ester group in O-acylcarnitines and some carboxyl derivatives, III. Hydrolysis enthalpy of O-acylcarnitines and betaine esters (author's transl)].
    Hoppe-Seyler's Zeitschrift fur physiologische Chemie, 1973, Volume: 354, Issue:9

    Topics: Acetates; Acetylcholine; Acylation; Betaine; Butyrates; Calorimetry; Carnitine; Esters; Glycine; Hydrogen-Ion Concentration; Hydrolysis; Kinetics; Structure-Activity Relationship; Temperature; Thermodynamics

1973
Evidence for an inducible active transport of carnitine in Pseudomonas aeruginosa.
    Biochemical and biophysical research communications, 1967, Feb-08, Volume: 26, Issue:3

    Topics: Antimetabolites; Azides; Betaine; Biological Transport, Active; Carnitine; Choline; Cyanides; Dinitrophenols; Edetic Acid; Glycine; Iodoacetates; Ouabain; Pseudomonas aeruginosa

1967
[Damped oscillations in the synthesis of carnitine dehydrogenase by Pseudomonas aeruginosa].
    Hoppe-Seyler's Zeitschrift fur physiologische Chemie, 1967, Volume: 348, Issue:12

    Topics: Betaine; Carnitine; Choline; Culture Media; Enzyme Repression; Galactosidases; Glucose; Glutamate Dehydrogenase; Glycine; Isocitrate Dehydrogenase; Oxidoreductases; Periodicity; Pseudomonas aeruginosa

1967
[Repression of the malic enzyme by carnitine metabolite in Pseudomonas aeruginosa].
    Acta biologica et medica Germanica, 1969, Volume: 23, Issue:1

    Topics: Acetates; Betaine; Carnitine; Choline; Culture Media; Enzyme Repression; Glucose; Glycine; Malate Dehydrogenase; Pseudomonas aeruginosa; Spectrophotometry; Succinates

1969
[Kinetics of active carnitine transport in Pseudomonas aeruginosa].
    Acta biologica et medica Germanica, 1970, Volume: 24, Issue:5

    Topics: Bacteriological Techniques; Betaine; Biological Transport, Active; Carnitine; Choline; Chromatography, Paper; Glucose; Glycine; Kinetics; Pseudomonas aeruginosa

1970
L-carnitine therapy in propionicacidaemia.
    Lancet (London, England), 1982, Jun-19, Volume: 1, Issue:8286

    Topics: Amino Acid Metabolism, Inborn Errors; Carboxy-Lyases; Carnitine; Glycine; Humans; Infant; Male; Methylmalonyl-CoA Decarboxylase; Propionates

1982
L-carnitine therapy in isovaleric acidemia.
    The Journal of clinical investigation, 1984, Volume: 74, Issue:6

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child, Preschool; Chromatography, Ion Exchange; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Male; Mass Spectrometry; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids; Valerates

1984
Glycine and L-carnitine therapy in 3-methylcrotonyl-CoA carboxylase deficiency.
    Journal of inherited metabolic disease, 1995, Volume: 18, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Carbon-Carbon Ligases; Carnitine; Child; Chromatography, Gas; Diet, Protein-Restricted; Female; Glycine; Humans; Ligases; Nutritional Status

1995
Acylcarnitine accumulation does not correlate with reperfusion recovery in palmitate-perfused rat hearts.
    The American journal of physiology, 1995, Volume: 268, Issue:6 Pt 2

    Topics: Acylation; Adenosine Triphosphate; Animals; Blood Pressure; Caproates; Carnitine; Carnitine O-Palmitoyltransferase; Energy Metabolism; Glucose; Glycine; Heart; Heart Rate; Hemodynamics; Hydrogen-Ion Concentration; Male; Myocardial Ischemia; Myocardial Reperfusion; Myocardium; Palmitic Acid; Palmitic Acids; Phosphates; Phosphocreatine; Rats; Rats, Sprague-Dawley; Ventricular Function, Left

1995
The detection of 3-methylglutarylcarnitine and a new dicarboxylic conjugate, 3-methylglutaconylcarnitine, in 3-methylglutaconic aciduria.
    Clinica chimica acta; international journal of clinical chemistry, 1994, Oct-14, Volume: 230, Issue:1

    Topics: Acidosis; Carnitine; Chromatography, Gas; Female; Fibroblasts; Glutarates; Glycine; Humans; Hydro-Lyases; Infant; Male; Spectrometry, Mass, Fast Atom Bombardment

1994
Involvement of erythrocyte calpain in glycine- and carnitine-treated isovaleric acidemia.
    Pediatric research, 1994, Volume: 36, Issue:2

    Topics: Calpain; Carnitine; Child; Erythrocytes; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids

1994
Cellular uncoupling induced by accumulation of long-chain acylcarnitine during ischemia.
    Circulation research, 1994, Volume: 74, Issue:1

    Topics: Animals; Carnitine; Carnitine O-Palmitoyltransferase; Electrophysiology; Epoxy Compounds; Glycine; Heart Conduction System; In Vitro Techniques; Myocardial Ischemia; Papillary Muscles; Rabbits; Time Factors

1994
Effect of treatment with glycine and L-carnitine in medium-chain acyl-coenzyme A dehydrogenase deficiency.
    The Journal of pediatrics, 1993, Volume: 122, Issue:4

    Topics: Acyl-CoA Dehydrogenase; Adult; Carnitine; Child; Dicarboxylic Acids; Fatty Acid Desaturases; Glycine; Humans; Time Factors

1993
Liquid chromatographic-atmospheric pressure chemical ionization mass spectrometric analysis of glycine conjugates and urinary isovalerylglycine in isovaleric acidemia.
    Journal of chromatography. B, Biomedical applications, 1995, Aug-18, Volume: 670, Issue:2

    Topics: Acidosis; Administration, Oral; Carnitine; Child, Preschool; Chromatography, Liquid; Female; Glucuronates; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Male; Mass Spectrometry; Pentanoic Acids

1995
3-Hydroxyisovalerylcarnitine in patients with deficiency of 3-methylcrotonyl CoA carboxylase.
    Clinica chimica acta; international journal of clinical chemistry, 1995, Aug-31, Volume: 240, Issue:1

    Topics: Carbon-Carbon Ligases; Carnitine; Child, Preschool; Female; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Ligases; Male; Valerates

1995
Benzoate therapy and carnitine deficiency in non-ketotic hyperglycinemia.
    American journal of medical genetics, 1995, Dec-04, Volume: 59, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Benzoates; Benzoic Acid; Carnitine; Drug Interactions; Female; Food Preservatives; Glycine; Humans; Infant; Infant, Newborn; Male

1995
Isolated (biotin-resistant) 3-methylcrotonyl-CoA carboxylase deficiency: four sibs devoid of pathology.
    Journal of inherited metabolic disease, 1995, Volume: 18, Issue:5

    Topics: Carbon-Carbon Ligases; Carnitine; Child; Child, Preschool; Dietary Proteins; Female; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Infant; Ligases; Male; Valerates

1995
Isovaleric acidemia: response to a leucine load after three weeks of supplementation with glycine, L-carnitine, and combined glycine-carnitine therapy.
    The Journal of pediatrics, 1996, Volume: 129, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Carnitine; Child; Female; Glycine; Hemiterpenes; Humans; Isovaleryl-CoA Dehydrogenase; Leucine; Oxidoreductases; Oxidoreductases Acting on CH-CH Group Donors; Pentanoic Acids

1996
Effect of carnitine administration on glycine metabolism in patients with isovaleric acidemia: significance of acetylcarnitine determination to estimate the proper carnitine dose.
    The Tohoku journal of experimental medicine, 1996, Volume: 179, Issue:2

    Topics: Acetylcarnitine; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Biomarkers; Carnitine; Child, Preschool; Female; Glycine; Hemiterpenes; Humans; Injections, Intravenous; Leucine; Male; Pentanoic Acids

1996
Comparison of in vitro carnitine and glycine conjugation with branched-side chain and cyclic side chain carboxylic acids in rats.
    Drug metabolism and disposition: the biological fate of chemicals, 1997, Volume: 25, Issue:2

    Topics: Animals; Benzoates; Benzoic Acid; Butyrates; Carboxylic Acids; Carnitine; Cells, Cultured; Cyclopropanes; Glycine; Isobutyrates; Kidney; Liver; Male; Rats; Rats, Sprague-Dawley

1997
Glycine-protected, hypoxic, proximal tubules develop severely compromised energetic function.
    Kidney international, 1997, Volume: 52, Issue:1

    Topics: 4-Aminobenzoic Acid; Adenosine Triphosphate; Aminobenzoates; Animals; Carnitine; Carrier Proteins; Cell Hypoxia; Cyclosporine; Dose-Response Relationship, Drug; Female; Glycine; Hydrogen-Ion Concentration; Immunohistochemistry; In Vitro Techniques; Kidney Tubules, Proximal; L-Lactate Dehydrogenase; Microfilament Proteins; Microscopy, Confocal; Microscopy, Fluorescence; para-Aminobenzoates; Phalloidine; Rabbits; Time Factors

1997
[Evaluation of the effect of long term valproic acid treatment on plasma levels of carnitine, ammonia and amino acids related to the urea cycle in pediatric epileptic patients].
    Revista de neurologia, 1997, Volume: 25, Issue:143

    Topics: Adolescent; Amino Acids; Ammonia; Anticonvulsants; Carnitine; Child; Child, Preschool; Epilepsy; Glutamine; Glycine; Humans; Infant; Infant, Newborn; Ornithine; Prospective Studies; Retrospective Studies; Urea; Valproic Acid

1997
[Effect of l-carnitine on the expression of glycine conjugates in rats in experimental B2-hypovitaminosis].
    Voprosy pitaniia, 1997, Issue:6

    Topics: Animals; Carnitine; Glycine; Rats; Rats, Wistar; Riboflavin Deficiency

1997
Effects of fasting, hypoxia, methylpalmoxirate and oxfenicine on the tissue-levels of long-chain acyl CoA and acylcarnitine in the rat atria.
    Archives of physiology and biochemistry, 1997, Volume: 105, Issue:6

    Topics: Acyl Coenzyme A; Aerobiosis; Animals; Carnitine; Carnitine O-Palmitoyltransferase; Cell Hypoxia; Enzyme Induction; Enzyme Inhibitors; Epoxy Compounds; Fasting; Female; Glycine; Heart Atria; Hypoxia; Male; Muscle Proteins; Propionates; Rats; Rats, Wistar

1997
Plasma amino acids in anorexia nervosa.
    European journal of clinical nutrition, 1998, Volume: 52, Issue:9

    Topics: Adolescent; Amino Acids; Anorexia Nervosa; Carnitine; Chromatography, Ion Exchange; Cysteine; Female; Glycine; Humans; Insulin-Like Growth Factor I; Methionine; Phenylalanine; Reference Values; Tyrosine; Valine

1998
Carnitine inhibits hydrolysis of inositol phospholipids induced by activation of metabotropic receptors.
    Neurochemical research, 1998, Volume: 23, Issue:12

    Topics: Animals; Carbachol; Carnitine; Catechols; Cycloleucine; Glycine; GTP-Binding Proteins; Hippocampus; Hydrolysis; Male; Neuroprotective Agents; Norepinephrine; Phosphatidylinositols; Rats; Rats, Wistar; Receptors, Metabotropic Glutamate; Type C Phospholipases

1998
Identification of new medium-chain acylcarnitines present in urine of a patient with medium-chain acyl-CoA dehydrogenase deficiency.
    Journal of inherited metabolic disease, 1999, Volume: 22, Issue:1

    Topics: Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenases; Carnitine; Child, Preschool; Female; Glucuronates; Glycine; Humans

1999
Carnitine alters binding of aflatoxin to DNA and proteins in rat hepatocytes and cell-free systems.
    The Journal of nutrition, 2001, Volume: 131, Issue:7

    Topics: Aflatoxin B1; Animals; Biomarkers; Carnitine; Cells, Cultured; Choline; DNA Adducts; Dose-Response Relationship, Drug; Glycine; Hepatocytes; Male; Microsomes, Liver; Rats; Rats, Sprague-Dawley; Sensitivity and Specificity

2001
Compound heterozygosity in four asymptomatic siblings with medium-chain acyl-CoA dehydrogenase deficiency.
    Journal of inherited metabolic disease, 2001, Volume: 24, Issue:3

    Topics: Acyl-CoA Dehydrogenases; Caprylates; Carnitine; Child; Child, Preschool; Dicarboxylic Acids; DNA Mutational Analysis; Female; Glycine; Heterozygote; Humans; Infant, Newborn; Male; Mutation; Neonatal Screening

2001
Palmitate-induced cardiac apoptosis is mediated through CPT-1 but not influenced by glucose and insulin.
    American journal of physiology. Heart and circulatory physiology, 2002, Volume: 282, Issue:2

    Topics: Animals; Apoptosis; Carboxylic Acids; Carnitine; Carnitine O-Palmitoyltransferase; Cell Survival; Cells, Cultured; Chick Embryo; Decanoic Acids; DNA; Enzyme Inhibitors; Fumonisins; Glucose; Glycine; Heart Ventricles; Hypoglycemic Agents; Insulin; Lactic Acid; Myocardium; Palmitic Acid

2002
The importance of gut motility in the metabolic control of propionic acidemia.
    The Journal of pediatrics, 2004, Volume: 144, Issue:4

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Carnitine; Cathartics; Child; Child, Preschool; Gastrointestinal Motility; Glycine; Humans; Propionates; Prospective Studies; Senna Extract

2004
Medium-chain acyl-CoA dehydrogenase deficiency: genotype-biochemical phenotype correlations.
    Molecular genetics and metabolism, 2006, Volume: 87, Issue:1

    Topics: Acyl-CoA Dehydrogenase; Carnitine; DNA Mutational Analysis; Fibroblasts; Genetic Testing; Genetic Variation; Genotype; Glycine; Homozygote; Humans; Infant, Newborn; Mass Spectrometry; Phenotype; Statistics as Topic

2006
In vitro and in vivo studies on acyl-coenzyme A-dependent bioactivation of zomepirac in rats.
    Chemical research in toxicology, 2005, Volume: 18, Issue:11

    Topics: Acetyl Coenzyme A; Animals; Biotransformation; Carnitine; Chromatography, High Pressure Liquid; Glycine; Hepatocytes; Liver; Male; Mass Spectrometry; Rats; Rats, Sprague-Dawley; Taurine; Tolmetin

2005
Carnitine treatment inhibits increases in cerebral carnitine esters and glutamate detected by mass spectrometry after hypoxia-ischemia in newborn rats.
    Stroke, 2006, Volume: 37, Issue:2

    Topics: Animals; Animals, Newborn; Anions; Brain; Cardiolipins; Carnitine; Carnitine O-Acetyltransferase; Glutamates; Glutamic Acid; Glycine; Hypoxia; Hypoxia-Ischemia, Brain; Immunohistochemistry; Lipid Metabolism; Mass Spectrometry; Microscopy, Fluorescence; Mitochondria; Phospholipids; Rats; Rats, Wistar; Superoxides; Time Factors; Vitamin B Complex

2006
Influence of hematocrit and localisation of punch in dried blood spots on levels of amino acids and acylcarnitines measured by tandem mass spectrometry.
    Clinica chimica acta; international journal of clinical chemistry, 2006, Volume: 373, Issue:1-2

    Topics: Amino Acids; Blood Specimen Collection; Blood Stains; Carnitine; Glycine; Hematocrit; Humans; Sensitivity and Specificity; Tandem Mass Spectrometry

2006
The sigma factor RpoN (sigma54) is involved in osmotolerance in Listeria monocytogenes.
    FEMS microbiology letters, 2006, Volume: 263, Issue:1

    Topics: Bacterial Proteins; Betaine; Carnitine; Carrier Proteins; Culture Media; Gene Deletion; Genome, Bacterial; Glycine; Listeria monocytogenes; Membrane Transport Proteins; Mutation; Organic Cation Transport Proteins; Osmolar Concentration; Reverse Transcriptase Polymerase Chain Reaction; RNA Polymerase Sigma 54; Sodium Chloride

2006
Transport of butyryl-L-carnitine, a potential prodrug, via the carnitine transporter OCTN2 and the amino acid transporter ATB(0,+).
    American journal of physiology. Gastrointestinal and liver physiology, 2007, Volume: 293, Issue:5

    Topics: Amino Acid Transport System A; Amino Acid Transport Systems; Biological Transport; Carnitine; Cell Line; Cloning, Molecular; Female; Glycine; Humans; Kinetics; Oocytes; Organic Cation Transport Proteins; Placenta; Pregnancy; Prodrugs

2007
3-Methylcrotonyl-CoA carboxylase deficiency: phenotypic variability in a family.
    Journal of child neurology, 2009, Volume: 24, Issue:4

    Topics: Adult; Brain; Carbon-Carbon Ligases; Carnitine; Cells, Cultured; Child, Preschool; DNA Mutational Analysis; Epilepsy; Fibroblasts; Gene Deletion; Genetic Predisposition to Disease; Genetic Testing; Genotype; Glycine; Humans; Infant; Language Development Disorders; Male; Mutation; Phenotype; Valerates

2009
Metabolomic analyses of plasma reveals new insights into asphyxia and resuscitation in pigs.
    PloS one, 2010, Mar-09, Volume: 5, Issue:3

    Topics: Animals; Animals, Newborn; Asphyxia; Blood Proteins; Carnitine; Female; Glycine; Hydrogen-Ion Concentration; Hypoxia; Lactates; Male; Metabolomics; Oxygen; Resuscitation; Swine

2010
Allelic diversity in MCAD deficiency: the biochemical classification of 54 variants identified during 5 years of ACADM sequencing.
    Molecular genetics and metabolism, 2010, Volume: 100, Issue:3

    Topics: Acyl-CoA Dehydrogenase; Adolescent; Adult; Alleles; Carnitine; Child; Child, Preschool; DNA Mutational Analysis; Exons; Genetic Association Studies; Genetic Carrier Screening; Genetic Variation; Genotype; Glycine; Humans; Infant, Newborn; Lipid Metabolism, Inborn Errors; Middle Aged; Mutation; Mutation, Missense; Neonatal Screening; Polymorphism, Single Nucleotide; Young Adult

2010
Useful second-tier tests in expanded newborn screening of isovaleric acidemia and methylmalonic aciduria.
    Journal of inherited metabolic disease, 2010, Volume: 33, Issue:Suppl 2

    Topics: Amino Acid Metabolism, Inborn Errors; Biomarkers; Blood Specimen Collection; Carnitine; Case-Control Studies; Chromatography, Liquid; False Positive Reactions; Gas Chromatography-Mass Spectrometry; Glycine; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Japan; Lactic Acid; Metabolism, Inborn Errors; Methylmalonic Acid; Neonatal Screening; Pilot Projects; Predictive Value of Tests; Retrospective Studies; Severity of Illness Index; Tandem Mass Spectrometry

2010
Beta-ketothiolase deficiency brought with lethargy: case report.
    Human & experimental toxicology, 2011, Volume: 30, Issue:10

    Topics: 3-Hydroxybutyric Acid; Acetyl-CoA C-Acyltransferase; Amino Acid Metabolism, Inborn Errors; Carnitine; Female; Glycine; Humans; Hydroxybutyrates; Infant; Ketosis; Lethargy

2011
Discovery of sexual dimorphisms in metabolic and genetic biomarkers.
    PLoS genetics, 2011, Volume: 7, Issue:8

    Topics: Adult; Aged; Aged, 80 and over; Amino Acids; Carnitine; Female; Genetic Markers; Genome-Wide Association Study; Glycine; Humans; Lipids; Male; Metabolome; Middle Aged; Polymorphism, Single Nucleotide; Sex Characteristics

2011
A single mutation in MCCC1 or MCCC2 as a potential cause of positive screening for 3-methylcrotonyl-CoA carboxylase deficiency.
    Molecular genetics and metabolism, 2012, Volume: 105, Issue:4

    Topics: Acyl Coenzyme A; Carbon-Carbon Ligases; Carnitine; Cells, Cultured; Child; Child, Preschool; DNA Mutational Analysis; Female; Fibroblasts; Glycine; Heterozygote; Humans; Infant; Infant, Newborn; Male; Mutation; Neonatal Screening; Real-Time Polymerase Chain Reaction; Skin; Urea Cycle Disorders, Inborn

2012
Quantification of acylglycines in human urine by HPLC electrospray ionization-tandem mass spectrometry and the establishment of pediatric reference interval in local Chinese.
    Talanta, 2012, Jan-15, Volume: 88

    Topics: 1-Butanol; Acylation; Adolescent; Asian People; Calibration; Carnitine; Child; Child, Preschool; Chromatography, High Pressure Liquid; Deuterium; Female; Glycine; Humans; Infant; Infant, Newborn; Male; Metabolism, Inborn Errors; Reference Values; Sensitivity and Specificity; Solid Phase Extraction; Spectrometry, Mass, Electrospray Ionization; Tandem Mass Spectrometry

2012
Oleoyl-L-carnitine inhibits glycine transport by GlyT2.
    British journal of pharmacology, 2013, Volume: 168, Issue:4

    Topics: Animals; Biological Transport; Carnitine; Dose-Response Relationship, Drug; Glycine; Glycine Plasma Membrane Transport Proteins; Molecular Structure; Oocytes; Patch-Clamp Techniques; Xenopus laevis

2013
Glycine propionyl l-carnitine attenuates d-Galactosamine induced fulminant hepatic failure in wistar rats.
    Chemico-biological interactions, 2014, May-05, Volume: 214

    Topics: Alanine Transaminase; Animals; Aspartate Aminotransferases; Ataxia Telangiectasia Mutated Proteins; Base Sequence; Carnitine; Comet Assay; DNA Primers; Galactosamine; Glutathione; Glycine; Lipid Peroxidation; Liver Failure, Acute; Male; Mitogen-Activated Protein Kinases; Rats; Rats, Wistar; Real-Time Polymerase Chain Reaction; Tumor Necrosis Factor-alpha

2014
Decreased cerebrospinal fluid levels of L-carnitine in non-apolipoprotein E4 carriers at early stages of Alzheimer's disease.
    Journal of Alzheimer's disease : JAD, 2014, Volume: 41, Issue:1

    Topics: Aged; Alzheimer Disease; Amyloid beta-Peptides; Apolipoprotein E4; Arginine; Biomarkers; Carnitine; Cognition Disorders; Cognitive Dysfunction; Creatine; Dicarboxylic Acids; Female; Glycine; Heterozygote; Humans; Male; Middle Aged; Neuropsychological Tests; Peptide Fragments; Sensitivity and Specificity; tau Proteins

2014
Metabolomics of asthma.
    The Journal of allergy and clinical immunology, 2014, Volume: 133, Issue:5

    Topics: Asthma; Carnitine; Ethanolamines; Female; Glycine; Humans; Male; Methylamines; Oxidative Stress; Serine; Sphingosine N-Acyltransferase; Threonine

2014
Reply: To PMID 24369803.
    The Journal of allergy and clinical immunology, 2014, Volume: 133, Issue:5

    Topics: Asthma; Carnitine; Ethanolamines; Female; Glycine; Humans; Male; Methylamines; Oxidative Stress; Serine; Sphingosine N-Acyltransferase; Threonine

2014
The first case in Asia of 2-methyl-3-hydroxybutyryl-CoA dehydrogenase deficiency (HSD10 disease) with atypical presentation.
    Journal of human genetics, 2014, Volume: 59, Issue:11

    Topics: 3-Hydroxyacyl CoA Dehydrogenases; Acetyl-CoA C-Acetyltransferase; Base Sequence; Carnitine; Child; Diagnosis, Differential; DNA Mutational Analysis; Dyskinesias; Fibroblasts; Glycine; Humans; Hydroxybutyrates; Immunoblotting; Lipid Metabolism, Inborn Errors; Male; Mental Retardation, X-Linked; Mitochondria; Models, Molecular; Point Mutation; Protein Structure, Tertiary

2014
Elevation of pivaloylcarnitine by sivelestat sodium in two children.
    Molecular genetics and metabolism, 2015, Volume: 116, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Cardiomyopathies; Carnitine; Child, Preschool; Chromatography, Liquid; Female; Glycine; Humans; Hyperammonemia; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Muscular Diseases; Neonatal Screening; Serine Proteinase Inhibitors; Sulfonamides; Tandem Mass Spectrometry

2015
Regression of fibrosis/cirrhosis by Glycine propionyl-l-carnitine treatment in d-Galactosamine induced chronic liver damage.
    Chemico-biological interactions, 2016, Dec-25, Volume: 260

    Topics: Actins; Animals; Body Weight; Carnitine; Chronic Disease; Collagen Type I; Galactosamine; Gene Expression Regulation; Glycine; Hydroxyproline; In Situ Nick-End Labeling; Interleukin-6; Liver; Liver Cirrhosis; Male; Oxidative Stress; Rats, Wistar; RNA, Messenger; Transforming Growth Factor beta; Tumor Necrosis Factor-alpha; Tyrosine

2016
Genotype and phenotype characterization in a Spanish cohort with isovaleric acidemia.
    Journal of human genetics, 2017, Volume: 62, Issue:3

    Topics: Acute Disease; Amino Acid Metabolism, Inborn Errors; Asymptomatic Diseases; Carnitine; Child; Child, Preschool; Chronic Disease; Creatinine; Female; Fibroblasts; Gene Expression; Genetic Association Studies; Genotype; Glycine; Hemiterpenes; Humans; Infant; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Male; Mutation; Neonatal Screening; Pentanoic Acids; Phenotype; Prevalence; Spain

2017
First-Trimester Maternal Serum Amino Acids and Acylcarnitines Are Significant Predictors of Gestational Diabetes.
    The review of diabetic studies : RDS, 2016,Winter, Volume: 13, Issue:4

    Topics: Adult; Arginine; Biomarkers; Carnitine; Case-Control Studies; Diabetes, Gestational; Down-Regulation; Female; Finland; Glycine; Hospitals, University; Humans; Maternal Serum Screening Tests; Predictive Value of Tests; Pregnancy; Pregnancy Trimester, First; Retrospective Studies; Risk; Sensitivity and Specificity; Up-Regulation

2016
Urinary and plasma metabolite differences detected by HPLC-ESI-QTOF-MS in systemic sclerosis patients.
    Journal of pharmaceutical and biomedical analysis, 2019, Jan-05, Volume: 162

    Topics: Acylation; Adult; Aged; Arachidonic Acids; Biomarkers; Carnitine; Case-Control Studies; Chromatography, High Pressure Liquid; Endocannabinoids; Female; Glycerides; Glycine; Humans; Male; Metabolomics; Middle Aged; Predictive Value of Tests; Prognosis; Reproducibility of Results; Scleroderma, Systemic; Spectrometry, Mass, Electrospray Ionization; Urinalysis

2019
Nutraceutical targeting of TLR4 signaling has potential for prevention of cancer cachexia.
    Medical hypotheses, 2019, Volume: 132

    Topics: 3-Hydroxybutyric Acid; Adipocytes; Biotin; Cachexia; Carnitine; Catechin; Coumaric Acids; Dietary Supplements; Fatty Acids, Omega-3; Glycine; Humans; Macrophages; Muscle, Skeletal; Neoplasms; Phycobilins; Phycocyanin; Signal Transduction; Tea; Toll-Like Receptor 4

2019
Eight novel mutations detected from eight Chinese patients with isovaleric acidemia.
    Clinica chimica acta; international journal of clinical chemistry, 2019, Volume: 498

    Topics: Alleles; Amino Acid Metabolism, Inborn Errors; Asian People; Carnitine; China; Female; Glycine; Humans; Infant, Newborn; Isovaleryl-CoA Dehydrogenase; Male; Mutation; Phenotype

2019
Post-mortem tissue analyses in a patient with succinic semialdehyde dehydrogenase deficiency (SSADHD). I. Metabolomic outcomes.
    Metabolic brain disease, 2020, Volume: 35, Issue:4

    Topics: Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Brain; Carnitine; Creatine; Creatinine; Developmental Disabilities; gamma-Aminobutyric Acid; Glycine; Humans; Male; Metabolomics; Succinate-Semialdehyde Dehydrogenase

2020
Effects of low and high doses of fenofibrate on protein, amino acid, and energy metabolism in rat.
    International journal of experimental pathology, 2020, Volume: 101, Issue:5

    Topics: Amino Acids; Amino Acids, Branched-Chain; Animals; Carnitine; Energy Metabolism; Fenofibrate; Glycine; Hepatomegaly; Humans; Hypolipidemic Agents; Leucine; Liver; Lysine; Male; Methionine; Muscle, Skeletal; Oxidation-Reduction; Proteins; Rats; Rats, Wistar

2020
Distinct lipid signatures are identified in the plasma of rats with chronic inflammation induced by estradiol benzoate and sex hormones.
    Metabolomics : Official journal of the Metabolomic Society, 2020, 09-07, Volume: 16, Issue:9

    Topics: Amino Acids; Animals; Biomarkers; Carnitine; Estradiol; Glycerophospholipids; Glycine; Gonadal Steroid Hormones; Humans; Inflammation; Lipids; Male; Metabolomics; Plasma; Prostatic Neoplasms; Prostatitis; Rats; Rats, Sprague-Dawley; Sphingomyelins

2020
Prospective analysis of circulating metabolites and endometrial cancer risk.
    Gynecologic oncology, 2021, Volume: 162, Issue:2

    Topics: Aged; Biomarkers, Tumor; Body Mass Index; Carnitine; Case-Control Studies; Endometrial Neoplasms; Female; Glycine; Humans; Metabolomics; Middle Aged; Prospective Studies; Risk Factors; Serine; Sphingomyelins

2021
Circulating Isovalerylcarnitine and Lung Cancer Risk: Evidence from Mendelian Randomization and Prediagnostic Blood Measurements.
    Cancer epidemiology, biomarkers & prevention : a publication of the American Association for Cancer Research, cosponsored by the American Society of Preventive Oncology, 2022, 10-04, Volume: 31, Issue:10

    Topics: Biomarkers, Tumor; Carnitine; Case-Control Studies; Genome-Wide Association Study; Glycine; Humans; Lung Neoplasms; Mendelian Randomization Analysis; Polymorphism, Single Nucleotide; Risk Factors

2022
Associations of plasma carnitine, lysine, trimethyllysine and glycine with incident ischemic stroke: Findings from a nested case-control study.
    Clinical nutrition (Edinburgh, Scotland), 2022, Volume: 41, Issue:9

    Topics: Carnitine; Case-Control Studies; Fabaceae; Glycine; Humans; Ischemic Stroke; Lysine; Stroke; Tandem Mass Spectrometry

2022
Dynamics of acylcarnitines, hypoglycin A, méthylènecyclopropylglycine and their metabolites in a Kladruber stallion with atypical myopathy.
    The veterinary quarterly, 2022, Volume: 42, Issue:1

    Topics: Acyl-CoA Dehydrogenases; Animals; Carnitine; Creatine Kinase; Cyclopropanes; Fatty Acids; Glycine; Horse Diseases; Horses; Hypoglycins; Male; Muscular Diseases

2022
Proline/Glycine residues of the PG-levels guide conformational changes along the transport cycle in the mitochondrial carnitine/acylcarnitine carrier (SLC25A20).
    International journal of biological macromolecules, 2022, Nov-30, Volume: 221

    Topics: Alanine; Carnitine; Carnitine Acyltransferases; Glycine; Proline

2022
Targeted Metabolomics Revealed a Sex-Dependent Signature for Metabolic Syndrome in the Mexican Population.
    Nutrients, 2022, Sep-06, Volume: 14, Issue:18

    Topics: Carnitine; Citrulline; Cohort Studies; Female; Glycine; Humans; Male; Metabolic Syndrome; Metabolomics

2022
Metabolic rewiring revealed by cell-specific rate analyses from nontargeted exometabolomics during simultaneous consumption of glucose and lactic acid in a CHO fed-batch process.
    Journal of biotechnology, 2022, Nov-20, Volume: 359

    Topics: Acetylcarnitine; Amino Acids; Animals; Antioxidants; Carnitine; CHO Cells; Cricetinae; Cricetulus; Glucose; Glutamates; Glutarates; Glutathione; Glycine; Lactic Acid; Mevalonic Acid; Phosphates; Pyridoxamine; Succinic Acid

2022
New gamma-hydroxybutyric acid (GHB) biomarkers: Development and validation of a liquid chromatography-tandem mass spectrometry method for the determination of GHB amino acid, carnitine, and fatty acid conjugates in urine.
    Drug testing and analysis, 2023, Volume: 15, Issue:4

    Topics: Amino Acids; Biomarkers; Carnitine; Chromatography, Liquid; Fatty Acids; Glycine; Humans; Hydroxybutyrates; Sodium Oxybate; Tandem Mass Spectrometry; Taurine

2023
Urinary concentrations of GHB and its novel amino acid and carnitine conjugates following controlled GHB administration to humans.
    Scientific reports, 2023, 06-02, Volume: 13, Issue:1

    Topics: Amino Acids; Carnitine; Chromatography, Liquid; Glycine; Humans; Hydroxybutyrates; Sodium Oxybate; Substance Abuse Detection; Tandem Mass Spectrometry

2023