carnitine and cysteine

carnitine has been researched along with cysteine in 36 studies

Research

Studies (36)

TimeframeStudies, this research(%)All Research%
pre-199010 (27.78)18.7374
1990's5 (13.89)18.2507
2000's7 (19.44)29.6817
2010's11 (30.56)24.3611
2020's3 (8.33)2.80

Authors

AuthorsStudies
Kako, KJ; Liu, MS1
Hauhart, RE; Thurston, JH1
Feller, A; Rudman, D1
Rudman, D; Williams, PJ1
Berry, CJ; Chawla, RK; Kutner, MH; Rudman, D1
Burgess, AH; Hendler, RW; Scharff, R1
Roskoski, R1
Leveille, GA; Romsos, DR; Tsai, AC1
Hodgson, E; Kumar, SS1
Neely, JR; Robishaw, JD; Vary, TC1
Hoffmann, H; Kirchner, E1
Briones, P; Camacho, JA; Farré, C; Mas, A; Vilaseca, MA1
Giangregorio, N; Indiveri, C; Palmieri, F; Tonazzi, A3
Ford, GD; Packer, L; Suzuki, YJ1
Artuch, R; Lambruschini, N; Moyano, D; Vilaseca, MA1
Andresen, BS; Campistol, J; Curcoy, A; Gregersen, N; Olsen, RK; Osorio, JH; Ribes, A; Trenchs, V; Vilaseca, MA1
Dai, J; Liu, H; Treber, M; Woldegiorgis, G; Zheng, G1
Celis, R; Cornejo, J; Cruz-Guzmán, M; Hermosín, MC; Koskinen, WC1
Blom, HJ; Heil, SG; Hogeveen, M; Kluijtmans, LA; Morava, E; van de Berg, GB; van Dijken, PJ1
Cárdenas, S; Carrillo-Carrión, C; Simonet, BM; Valcárcel, M1
Kolodziejczyk, J; Saluk-Juszczak, J; Wachowicz, B1
Al-Humadi, H; Almpani, M; Katsouni, E; Liapi, C; Skandali, N; Stolakis, V; Tsakiris, S; Voumvourakis, K; Zarros, A1
Giangregorio, N; Indiveri, C; Palmieri, F1
Eberini, I; Indiveri, C; Tonazzi, A1
Bucak, MN; Büyükleblebici, S; Cantürk, F; Sarıözkan, S; Tuncer, PB1
de Jesús Escalante-Padrón, F; de Jesús López-López, E; Hurtado-Torres, GF; Lima-Rogel, V; Romano-Moreno, S1
Bastin, J; Bennett, MJ; Chen, J; Doulias, PT; Ischiropoulos, H; Tenopoulou, M1
Console, L; Giangregorio, N; Indiveri, C; Tonazzi, A1
Console, L; De Palma, A; Giangregorio, N; Indiveri, C; Tonazzi, A1
Appel, LJ; Holmes, E; Loo, RL; Nicholson, JK; Zou, X1
Cai, YY; Li, J; Li, P; Liu, BL; Liu, Q; Pan, A; Qi, LW; Yang, L; Zhang, WS1
Cariou, B; Croyal, M; Gand, E; Goronflot, T; Hadjadj, S; Jacobi, D; Le May, C; Prieur, X; Ragot, S; Saulnier, PJ; Trochu, JN; Wargny, M1
Bugg, TDH; Cameron, AD; Chen, Y; Quareshy, M; Shanmugam, M1
Console, L; Giangregorio, N; Indiveri, C; Scalise, M; Tonazzi, A1

Reviews

1 review(s) available for carnitine and cysteine

ArticleYear
Nutrient deficiencies during total parenteral nutrition.
    Nutrition reviews, 1985, Volume: 43, Issue:1

    Topics: Adolescent; Adult; Aged; Animals; Biotin; Carnitine; Child; Choline Deficiency; Chromium; Copper; Cysteine; Deficiency Diseases; Dogs; Fatty Acids, Essential; Female; Folic Acid Deficiency; Guinea Pigs; Humans; Infant; Male; Middle Aged; Molybdenum; Parenteral Nutrition; Parenteral Nutrition, Total; Phosphates; Rats; Selenium; Sheep; Taurine; Tyrosine; Vitamin A Deficiency; Zinc

1985

Trials

1 trial(s) available for carnitine and cysteine

ArticleYear
Characterization of metabolic responses to healthy diets and association with blood pressure: application to the Optimal Macronutrient Intake Trial for Heart Health (OmniHeart), a randomized controlled study.
    The American journal of clinical nutrition, 2018, 03-01, Volume: 107, Issue:3

    Topics: Adult; Aged; Aged, 80 and over; Blood Pressure; Cardiovascular Diseases; Carnitine; Cholesterol; Cluster Analysis; Creatine; Cross-Over Studies; Cysteine; Diet, Healthy; Dietary Carbohydrates; Dietary Fats; Dietary Proteins; Female; Humans; Magnetic Resonance Spectroscopy; Male; Middle Aged; Risk Factors

2018

Other Studies

34 other study(ies) available for carnitine and cysteine

ArticleYear
Some properties and subcellular distribution of palmitoyl-CoA hydrolase and phosphatidate phosphohydrolase in rabbit hearts.
    Journal of molecular and cellular cardiology, 1975, Volume: 7, Issue:8

    Topics: Animals; Carnitine; Cattle; Cysteine; Dithiothreitol; Hydrogen-Ion Concentration; Hydrolysis; Male; Microsomes; Muscle Proteins; Myocardium; Palmitic Acids; Phospholipids; Phosphoric Monoester Hydrolases; Rabbits; Subcellular Fractions; Thiolester Hydrolases; Time Factors

1975
Amelioration of adverse effects of valproic acid on ketogenesis and liver coenzyme A metabolism by cotreatment with pantothenate and carnitine in developing mice: possible clinical significance.
    Pediatric research, 1992, Volume: 31, Issue:4 Pt 1

    Topics: Animals; Animals, Suckling; Carnitine; Coenzyme A; Cysteine; Ketone Bodies; Liver; Mice; Pantothenic Acid; Valproic Acid

1992
Evidence for deficiencies of conditionally essential nutrients during total parenteral nutrition.
    Journal of the American College of Nutrition, 1986, Volume: 5, Issue:2

    Topics: Carnitine; Choline Deficiency; Cysteine; Deficiency Diseases; Humans; Parenteral Nutrition, Total; Taurine; Tyrosine

1986
Plasma concentrations of transsulfuration pathway products during nasoenteral and intravenous hyperalimentation of malnourished patients.
    The American journal of clinical nutrition, 1985, Volume: 42, Issue:4

    Topics: Adolescent; Adult; Aged; Amino Acids; Blood Proteins; Carnitine; Choline; Creatine; Cysteine; Enteral Nutrition; Female; Glutathione; Humans; Liver Cirrhosis; Male; Middle Aged; Nutrition Disorders; Parenteral Nutrition, Total; Phosphatidylcholines; Protein Binding; Sulfur

1985
Respiration and protein synthesis in Escherichia coli membrane-envelope fragments. II. Effects of fatty acids and albumin on respiration.
    The Journal of cell biology, 1970, Volume: 44, Issue:2

    Topics: Adenosine Triphosphate; Carnitine; Cell-Free System; Coenzyme A; Cysteine; Electrodes; Escherichia coli; Fatty Acids; Hydrogen-Ion Concentration; Membranes; NAD; Oxidoreductases; Oxygen Consumption; Polarography; Serum Albumin, Bovine; Succinate Dehydrogenase; Succinates

1970
Choline acetyltransferase. Evidence for an acetyl-enzyme reaction intermediate.
    Biochemistry, 1973, Sep-11, Volume: 12, Issue:19

    Topics: Acetyl Coenzyme A; Acetylcholine; Acetyltransferases; Animals; Binding Sites; Brain; Carbon Isotopes; Carnitine; Catalysis; Cattle; Choline; Chromatography, Gel; Coenzyme A; Cysteine; Drug Stability; Esters; Guanidines; Hydrogen-Ion Concentration; Organophosphorus Compounds; Pantothenic Acid; Sulfhydryl Compounds; Sulfides; Trichloroacetic Acid; Tritium

1973
Significance of dietary carnitine for growth and carnitine turnover in rats.
    The Journal of nutrition, 1974, Volume: 104, Issue:6

    Topics: Animal Nutritional Physiological Phenomena; Animals; Body Composition; Body Weight; Carbon Radioisotopes; Carnitine; Choline; Choline Deficiency; Cysteine; Diet; Dietary Fats; Half-Life; Liver; Male; Methionine; Muscles; Organ Size; Rats; Urine

1974
Partial purification and properties of choline kinase from the cockroach, Periplaneta americana.
    Comparative biochemistry and physiology, 1970, Mar-01, Volume: 33, Issue:1

    Topics: Adenosine Triphosphate; Amino Alcohols; Animals; Calcium Phosphates; Carbon Isotopes; Carnitine; Chemical Precipitation; Choline; Cysteine; Drug Stability; Hydrogen-Ion Concentration; Insecta; Kinetics; Magnesium; Methods; Nucleotides; Phosphotransferases; Quaternary Ammonium Compounds; Serine; Sulfates; Time Factors; Ultracentrifugation

1970
Control of myocardial levels of CoA and carnitine.
    Journal of molecular and cellular cardiology, 1982, Volume: 14 Suppl 3

    Topics: Animals; Biological Transport; Carnitine; Coenzyme A; Cysteine; Cytosol; Diabetes Mellitus, Experimental; Heart; Insulin; Kinetics; Male; Mitochondria, Heart; Myocardium; Rats; Rats, Inbred Strains

1982
[Studies in mice on diminishing acute toxicity of violamycin BI by combined therapy (author's transl)].
    Die Pharmazie, 1982, Volume: 37, Issue:5

    Topics: Aminoglycosides; Animals; Anti-Bacterial Agents; Ascorbic Acid; Carnitine; Cysteine; Dogs; Drug Interactions; Female; Folic Acid; Male; Methionine; Mice; Rabbits; Rats; Rats, Inbred Strains; Swine; Vitamin E

1982
Biochemical follow-up in late-treated nephropathic cystinosis.
    Journal of inherited metabolic disease, 1995, Volume: 18, Issue:2

    Topics: Carnitine; Creatinine; Cysteamine; Cysteine; Cystinosis; Disease Progression; Female; Follow-Up Studies; Humans; Infant; Infant, Newborn; Kidney Function Tests; Male; Oxidants

1995
Probing the active site of the reconstituted carnitine carrier from rat liver mitochondria with sulfhydryl reagents. A cysteine residue is localized in or near the substrate binding site.
    European journal of biochemistry, 1995, Mar-01, Volume: 228, Issue:2

    Topics: Animals; Binding Sites; Carnitine; Carrier Proteins; Cysteine; Disulfides; Mitochondria, Liver; Molecular Weight; Oxidation-Reduction; Phenanthrolines; Rats; Sulfhydryl Reagents

1995
Relationships between the effects of superoxide anion and palmitoyl-L-carnitine on the Ca(2+)-ATPase of vascular smooth muscle sarcoplasmic reticulum.
    Journal of molecular and cellular cardiology, 1993, Volume: 25, Issue:7

    Topics: Animals; Antioxidants; Calcium-Transporting ATPases; Carnitine; Cattle; Cysteine; Dose-Response Relationship, Drug; Free Radicals; Hypoxanthine; Hypoxanthines; Muscle, Smooth, Vascular; Oxidation-Reduction; Oxygen; Palmitoylcarnitine; Sarcoplasmic Reticulum; Superoxides; Xanthine Oxidase

1993
Plasma amino acids in anorexia nervosa.
    European journal of clinical nutrition, 1998, Volume: 52, Issue:9

    Topics: Adolescent; Amino Acids; Anorexia Nervosa; Carnitine; Chromatography, Ion Exchange; Cysteine; Female; Glycine; Humans; Insulin-Like Growth Factor I; Methionine; Phenylalanine; Reference Values; Tyrosine; Valine

1998
Late-onset form of beta-electron transfer flavoprotein deficiency.
    Molecular genetics and metabolism, 2003, Volume: 78, Issue:4

    Topics: Amino Acid Metabolism, Inborn Errors; Arginine; Carnitine; Cysteine; DNA Mutational Analysis; Electron-Transferring Flavoproteins; Electrons; Exons; Female; Fibroblasts; Gas Chromatography-Mass Spectrometry; Gene Deletion; Glutarates; Humans; Infant, Newborn; Iron-Sulfur Proteins; Lysine; Mutation, Missense; Oxidoreductases Acting on CH-NH Group Donors; Oxygen; Phenotype

2003
Cysteine-scanning mutagenesis of muscle carnitine palmitoyltransferase I reveals a single cysteine residue (Cys-305) is important for catalysis.
    The Journal of biological chemistry, 2005, Feb-11, Volume: 280, Issue:6

    Topics: Alanine; Amino Acid Sequence; Animals; Binding Sites; Blotting, Western; Carnitine; Carnitine O-Palmitoyltransferase; Catalysis; Cysteine; DNA Primers; Humans; Kinetics; Malonyl Coenzyme A; Models, Chemical; Molecular Sequence Data; Mutagenesis; Mutation; Myocardium; Palmitic Acid; Palmitoylcarnitine; Pichia; Protein Structure, Tertiary; Sequence Homology, Amino Acid; Serine

2005
Identification by site-directed mutagenesis and chemical modification of three vicinal cysteine residues in rat mitochondrial carnitine/acylcarnitine transporter.
    The Journal of biological chemistry, 2005, May-20, Volume: 280, Issue:20

    Topics: Amino Acid Sequence; Amino Acid Substitution; Animals; Arsenicals; Carnitine; Carnitine Acyltransferases; Cattle; Cysteine; Diamide; Enzyme Inhibitors; In Vitro Techniques; Kinetics; Liposomes; Mitochondria; Models, Molecular; Molecular Sequence Data; Mutagenesis, Site-Directed; Phenanthrolines; Rats; Recombinant Proteins; Sequence Homology, Amino Acid

2005
Adsorption of pesticides from water by functionalized organobentonites.
    Journal of agricultural and food chemistry, 2005, Sep-21, Volume: 53, Issue:19

    Topics: Adsorption; Bentonite; Carnitine; Cations; Cysteine; Pesticides; Spectroscopy, Fourier Transform Infrared; Thiamine; Water; X-Ray Diffraction

2005
Marfanoid features in a child with combined methylmalonic aciduria and homocystinuria (CblC type).
    Journal of inherited metabolic disease, 2007, Volume: 30, Issue:5

    Topics: Adolescent; Carnitine; Carrier Proteins; Child; Cysteine; Diagnosis, Differential; DNA Mutational Analysis; Exons; Female; Folic Acid; Genetic Testing; Heterozygote; Homocysteine; Homocystinuria; Humans; Male; Marfan Syndrome; Metabolism, Inborn Errors; Methylmalonic Acid; Mutation; Oxidoreductases; Pedigree; Phenotype; Treatment Outcome; Vitamin B 12; Vitamin B 6; Vitamins

2007
Conformation-dependent accessibility of Cys-136 and Cys-155 of the mitochondrial rat carnitine/acylcarnitine carrier to membrane-impermeable SH reagents.
    Biochimica et biophysica acta, 2007, Volume: 1767, Issue:11

    Topics: Animals; Biological Transport; Carnitine; Carnitine Acyltransferases; Cysteine; Dose-Response Relationship, Drug; Ethyl Methanesulfonate; Fluoresceins; Membrane Transport Proteins; Mesylates; Mitochondria; Models, Molecular; Mutant Proteins; Mutation; Permeability; Protein Conformation; Rats; Substrate Specificity; Sulfhydryl Reagents

2007
Selective quantification of carnitine enantiomers using chiral cysteine-capped CdSe(ZnS) quantum dots.
    Analytical chemistry, 2009, Jun-15, Volume: 81, Issue:12

    Topics: Cadmium Compounds; Carnitine; Cysteine; Fluorescence Resonance Energy Transfer; Quantum Dots; Selenium Compounds; Spectrometry, Fluorescence; Stereoisomerism; Zinc Sulfate

2009
L-Carnitine protects plasma components against oxidative alterations.
    Nutrition (Burbank, Los Angeles County, Calif.), 2011, Volume: 27, Issue:6

    Topics: Adult; Antioxidants; Blood Proteins; Carnitine; Cysteine; Dietary Supplements; Glutathione; Homocysteine; Humans; Lipid Peroxides; Lipids; Male; Osmolar Concentration; Oxidants; Oxidation-Reduction; Oxidative Stress; Peroxynitrous Acid; Protein Carbonylation; Thiobarbituric Acid Reactive Substances; Tyrosine; Young Adult

2011
Experimentally-induced Wernicke's encephalopathy modifies crucial rat brain parameters: the importance of Na+, K+ -ATPase and a potentially neuroprotective role for antioxidant supplementation.
    Metabolic brain disease, 2013, Volume: 28, Issue:3

    Topics: Acetylcholinesterase; Animals; Antioxidants; Brain; Ca(2+) Mg(2+)-ATPase; Carnitine; Cysteine; Male; Neuroprotective Agents; Rats; Rats, Wistar; Sodium-Potassium-Exchanging ATPase; Thiamine Deficiency; Wernicke Encephalopathy

2013
Glutathione controls the redox state of the mitochondrial carnitine/acylcarnitine carrier Cys residues by glutathionylation.
    Biochimica et biophysica acta, 2013, Volume: 1830, Issue:11

    Topics: Animals; Biological Transport; Carnitine; Carrier Proteins; Cysteine; Glutaredoxins; Glutathione; Glutathione Disulfide; Mitochondria, Liver; Mutagenesis, Site-Directed; Oxidation-Reduction; Proteolipids; Rats

2013
Molecular mechanism of inhibition of the mitochondrial carnitine/acylcarnitine transporter by omeprazole revealed by proteoliposome assay, mutagenesis and bioinformatics.
    PloS one, 2013, Volume: 8, Issue:12

    Topics: Animals; Antiporters; Biological Assay; Biological Transport; Carnitine; Computational Biology; Cysteine; Kinetics; Membrane Transport Proteins; Mitochondria; Molecular Docking Simulation; Mutagenesis, Site-Directed; Mutant Proteins; Omeprazole; Proteolipids; Proton Pump Inhibitors; Rats; Substrate Specificity

2013
Influence of various antioxidants added to TCM-199 on post-thaw bovine sperm parameters, DNA integrity and fertilizing ability.
    Cryobiology, 2014, Volume: 68, Issue:1

    Topics: Animals; Antioxidants; Carnitine; Cattle; Cryopreservation; Cryoprotective Agents; Cysteine; DNA Fragmentation; Female; Fertilization; Glutamine; Male; Methionine; Pregnancy; Semen Preservation; Sperm Motility; Spermatozoa

2014
Aluminum Contamination in Parenteral Nutrition Admixtures for Low-Birth-Weight Preterm Infants in Mexico.
    JPEN. Journal of parenteral and enteral nutrition, 2016, Volume: 40, Issue:7

    Topics: Aluminum; Calcium Gluconate; Carnitine; Cysteine; Drug Contamination; Humans; Infant; Infant, Low Birth Weight; Infant, Premature; Mexico; Nutritional Requirements; Parenteral Nutrition Solutions; Phosphates; Potassium Compounds; United States; United States Food and Drug Administration

2016
Strategies for correcting very long chain acyl-CoA dehydrogenase deficiency.
    The Journal of biological chemistry, 2015, Apr-17, Volume: 290, Issue:16

    Topics: Acetylcysteine; Acyl-CoA Dehydrogenase; Acyl-CoA Dehydrogenase, Long-Chain; Amino Acid Sequence; Carnitine; Congenital Bone Marrow Failure Syndromes; Cysteine; Dose-Response Relationship, Drug; Fatty Acids; Fibroblasts; Genetic Therapy; Humans; Kinetics; Lipid Metabolism, Inborn Errors; Mitochondrial Diseases; Molecular Sequence Data; Muscular Diseases; Mutation; Oxidation-Reduction; Primary Cell Culture; Skin

2015
Mitochondrial carnitine/acylcarnitine translocase: insights in structure/ function relationships. Basis for drug therapy and side effects prediction.
    Mini reviews in medicinal chemistry, 2015, Volume: 15, Issue:5

    Topics: Amino Acid Sequence; Animals; Anti-Bacterial Agents; Bacterial Infections; Brain Diseases; Cardiovascular Diseases; Carnitine; Carnitine Acyltransferases; Computational Biology; Cysteine; Digestive System Diseases; Gastrointestinal Diseases; Humans; Hydrogen Peroxide; Mitochondria; Molecular Sequence Data; Mutagenesis, Site-Directed; Oxidative Stress; Proton Pump Inhibitors; Respiratory Distress Syndrome; Sequence Alignment

2015
Nitric oxide inhibits the mitochondrial carnitine/acylcarnitine carrier through reversible S-nitrosylation of cysteine 136.
    Biochimica et biophysica acta. Bioenergetics, 2017, Volume: 1858, Issue:7

    Topics: Amino Acid Sequence; Animals; Biological Transport; Carnitine; Carnitine Acyltransferases; Conserved Sequence; Cysteine; Dithioerythritol; Liposomes; Mitochondria; Models, Molecular; Nitric Oxide; Nitric Oxide Donors; Nitrogen; Oxidation-Reduction; Protein Conformation; Protein Processing, Post-Translational; Rats; S-Nitrosoglutathione; Sequence Alignment; Sequence Homology, Amino Acid

2017
American Ginseng and Asian Ginseng Intervention in Diet-Induced Obese Mice: Metabolomics Reveals Distinct Metabolic Profiles.
    The American journal of Chinese medicine, 2019, Volume: 47, Issue:4

    Topics: Animals; Carnitine; Chromatography, Liquid; Cysteine; Diet, High-Fat; Fatty Acids; Glucose; Linoleic Acid; Lipid Metabolism; Male; Mass Spectrometry; Metabolomics; Methionine; Mice, Inbred C57BL; Obesity; Panax; Phytotherapy; Plant Extracts; Taurine

2019
Nutritional biomarkers and heart failure requiring hospitalization in patients with type 2 diabetes: the SURDIAGENE cohort.
    Cardiovascular diabetology, 2022, 06-09, Volume: 21, Issue:1

    Topics: Aged; Betaine; Biomarkers; Carnitine; Choline; Cohort Studies; Cysteine; Diabetes Mellitus, Type 2; Female; Heart Failure; Homocysteine; Hospitalization; Humans; Male; Methionine; Middle Aged; Prospective Studies; Risk Factors

2022
Characterisation of an unusual cysteine pair in the Rieske carnitine monooxygenase CntA catalytic site.
    The FEBS journal, 2023, Volume: 290, Issue:11

    Topics: Carnitine; Catalytic Domain; Cysteine; Ecosystem; Humans; Mixed Function Oxygenases; Oxidation-Reduction; Phylogeny

2023
Inhibition of the Mitochondrial Carnitine/Acylcarnitine Carrier by Itaconate through Irreversible Binding to Cysteine 136: Possible Pathophysiological Implications.
    Biomolecules, 2023, 06-15, Volume: 13, Issue:6

    Topics: Carnitine; Cysteine; HeLa Cells; Humans; Membrane Transport Modulators; Membrane Transport Proteins; Mitochondria

2023