Page last updated: 2024-09-05

beta-methylcrotonylglycine and biotin

beta-methylcrotonylglycine has been researched along with biotin in 10 studies

Compound Research Comparison

Studies
(beta-methylcrotonylglycine)
Trials
(beta-methylcrotonylglycine)
Recent Studies (post-2010)
(beta-methylcrotonylglycine)
Studies
(biotin)
Trials
(biotin)
Recent Studies (post-2010) (biotin)
270414,847953,882

Protein Interaction Comparison

ProteinTaxonomybeta-methylcrotonylglycine (IC50)biotin (IC50)
nonstructural protein 1Influenza A virus (A/California/07/2009(H1N1))0.2

Research

Studies (10)

TimeframeStudies, this research(%)All Research%
pre-19906 (60.00)18.7374
1990's1 (10.00)18.2507
2000's3 (30.00)29.6817
2010's0 (0.00)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Holme, E; Jacobson, CE; Kristiansson, B1
Mock, DM; Mock, NI; Weintraub, S1
Baker, H; Baswell, DL; Holman, RT; Mock, DM; Sweetman, L1
Greter, J; Holme, E; Koivikko, M; Lindstedt, S1
Bartlett, K; Leonard, JV; Ng, H1
Baker, H; Nyhan, WL; Peterson, RM; Surh, L; Sweetman, L1
Berry, SA; Nyhan, WL; Thuy, LP; Tuchman, M1
Mock, DM; Mock, NI1
Almashanu, S; Baumgartner, ER; Baumgartner, MR; Dantas, MF; Fowler, B; Friebel, D; Gebhardt, B; Giunta, C; Hoffmann, GF; Suormala, T; Valle, D1
Kluijtmans, LAJ; Koene, S; Mock, D; Morava, E; Pasch, M; Wevers, R1

Other Studies

10 other study(ies) available for beta-methylcrotonylglycine and biotin

ArticleYear
Biotin-responsive multiple carboxylase deficiency in an 8-year-old boy with normal serum biotinidase and fibroblast holocarboxylase-synthetase activities.
    Journal of inherited metabolic disease, 1988, Volume: 11, Issue:3

    Topics: Amidohydrolases; Biotin; Biotinidase; Carbon-Nitrogen Ligases; Child; Fibroblasts; Glycine; Humans; Kinetics; Ligases; Male; Multiple Carboxylase Deficiency; Valerates

1988
Abnormal organic aciduria in biotin deficiency: the rat is similar to the human.
    The Journal of laboratory and clinical medicine, 1988, Volume: 112, Issue:2

    Topics: Animals; Biotin; Disease Models, Animal; Gas Chromatography-Mass Spectrometry; Glycine; Male; Random Allocation; Rats; Rats, Inbred Strains; Valerates

1988
Biotin deficiency complicating parenteral alimentation: diagnosis, metabolic repercussions, and treatment.
    The Journal of pediatrics, 1985, Volume: 106, Issue:5

    Topics: Alopecia; Biotin; Citrates; Diagnosis, Differential; Erythema; Fatty Acids, Essential; Female; Glycine; Humans; Infant; Isomerism; Lactates; Lactic Acid; Male; Nervous System Diseases; Parenteral Nutrition; Valerates; Zinc

1985
Biotin-responsive 3-methylcrotonylglycinuria with biotinidase deficiency.
    Journal of inherited metabolic disease, 1985, Volume: 8 Suppl 2

    Topics: Amidohydrolases; Biotin; Biotinidase; Carbon-Carbon Ligases; Child, Preschool; Glycine; Humans; Ligases; Male

1985
A combined defect of three mitochondrial carboxylases presenting as biotin-responsive 3-methylcrotonyl glycinuria and 3-hydroxyisovaleric aciduria.
    Clinica chimica acta; international journal of clinical chemistry, 1980, Jan-15, Volume: 100, Issue:2

    Topics: Acidosis; Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Biotin; Butyrates; Carbon Dioxide; Carboxy-Lyases; Child, Preschool; Crotonates; Female; Fibroblasts; Glycine; Humans; Hydroxy Acids; Ligases; Mitochondria; Propionates; Pyruvate Carboxylase Deficiency Disease; Valerates

1980
Clinical and metabolic abnormalities in a boy with dietary deficiency of biotin.
    Pediatrics, 1981, Volume: 68, Issue:4

    Topics: Alopecia; Biotin; Carbon-Carbon Ligases; Carboxy-Lyases; Child; Citrates; Diet; Egg Proteins; Facial Dermatoses; Glycine; Humans; Hydroxy Acids; Ligases; Male; Methylmalonyl-CoA Decarboxylase; Propionates; Skin Diseases

1981
Partial methylcrotonyl-coenzyme A carboxylase deficiency in an infant with failure to thrive, gastrointestinal dysfunction, and hypertonia.
    Pediatrics, 1993, Volume: 91, Issue:3

    Topics: Biotin; Carbon-Carbon Ligases; Failure to Thrive; Gastrointestinal Diseases; Glycine; Humans; Infant; Ligases; Male; Metabolism, Inborn Errors; Muscle Hypertonia; Valerates

1993
Lymphocyte propionyl-CoA carboxylase is an early and sensitive indicator of biotin deficiency in rats, but urinary excretion of 3-hydroxypropionic acid is not.
    The Journal of nutrition, 2002, Volume: 132, Issue:7

    Topics: Animals; Biomarkers; Biotin; Carboxy-Lyases; Deficiency Diseases; Glycine; Lactic Acid; Lymphocytes; Male; Methylmalonyl-CoA Decarboxylase; Rats; Rats, Sprague-Dawley; Sensitivity and Specificity

2002
Isolated 3-methylcrotonyl-CoA carboxylase deficiency: evidence for an allele-specific dominant negative effect and responsiveness to biotin therapy.
    American journal of human genetics, 2004, Volume: 75, Issue:5

    Topics: Alleles; Base Sequence; Biotin; Carbon-Carbon Ligases; DNA Mutational Analysis; Dose-Response Relationship, Drug; Fibroblasts; Gene Expression; Genetic Vectors; Germany; Glycine; Greece; Humans; Infant, Newborn; Male; Mitochondrial Diseases; Molecular Sequence Data; Mutation; Reverse Transcriptase Polymerase Chain Reaction; Sequence Analysis, DNA; Transfection; Valerates

2004
Biotin-sensitive 3-methylcrotonylglycinuria in a patient with severe growth delay, ectodermal abnormalities, neonatal progeroid appearance, and developmental delay.
    Clinical dysmorphology, 2008, Volume: 17, Issue:3

    Topics: Abnormalities, Multiple; Aging, Premature; Biotin; Child, Preschool; Developmental Disabilities; Ectoderm; Female; Glycine; Growth Disorders; Humans; Metabolism, Inborn Errors

2008