ammonium hydroxide has been researched along with ornithine in 357 studies
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 222 (62.18) | 18.7374 |
| 1990's | 52 (14.57) | 18.2507 |
| 2000's | 37 (10.36) | 29.6817 |
| 2010's | 27 (7.56) | 24.3611 |
| 2020's | 19 (5.32) | 2.80 |
| Authors | Studies |
|---|---|
| Cooper, T; Gorski, M; Sumrada, R | 1 |
| Townsend, R | 1 |
| Kraus, H; Stubbe, P; von Berg, W | 1 |
| Meijer, AJ; van Woerkom, GM | 1 |
| Allen, MM; Chee, HL; Weathers, PJ | 1 |
| Mora, J; Vaca, G | 1 |
| Chase, HP; Glasgow, AM | 1 |
| Gatfield, PD; Haust, MD; Taller, E; Wolfe, DM | 1 |
| Gatfield, PD; Haust, MD | 1 |
| Bolivar, F; Galván, M; Martuscelli, J | 1 |
| Alfant, M; Crandall, DE; Knott, CE; Tremblay, GS | 1 |
| Anderson, PM | 2 |
| Visek, WJ | 1 |
| Ito, K; Koyama, K; Owada, Y; Sato, T; Watabe, S; Yamauchi, H | 1 |
| Freedland, RA; Story, DL; Triebwasser, KC | 1 |
| Beaufrand, MJ; Debry, G; Felber, JP; Gay, G; Villaume, C | 1 |
| Coll, KE; Wałajtys-Rode, E; Williamson, JR | 1 |
| Ha, YH; Milner, JA | 1 |
| Chainuvati, T; Plengvanit, U; Viranuvatti, V | 1 |
| Morris, JG; Rogers, QR | 2 |
| Deleeuw, G; Gimpel, JA; Meijer, AJ; Tager, JM; Tischler, ME; Williamson, JR | 1 |
| Hatchwell, LC; Milner, JA | 1 |
| Bakker, HD; Brink, M; de Bree, PK; Desplanque, J; van der Heiden, C; Wadman, SK | 1 |
| Russel, A; Statter, M | 1 |
| Fell, V; Pollitt, RJ | 1 |
| Blahíková, L; Horký, J; Marecková, O; Pechar, J; Vidlaková, M; Vosmík, J; Zvolánková, K | 1 |
| Katsunuma, T; Ohkubo, T; Saheki, T | 1 |
| Chiba, T; Minami, R; Nakao, T; Oyanagi, K; Sogawa, H | 1 |
| Imler, M | 1 |
| Gatfield, PD; Gordon, BA; Taller, E | 1 |
| Hayase, K; Yokogoshi, H; Yoshida, A | 1 |
| Freedland, RA; Triebwasser, KC | 1 |
| Glasgow, AM | 1 |
| Erb, W; Goldberg, P; Leinweber, W | 1 |
| Chi, MS; Speers, GM | 1 |
| Shih, VE | 2 |
| Amacher, AL; Bolton, RJ; Gatfield, PD | 1 |
| Henglein-Ottermann, D | 1 |
| Horisawa, S; Kato, T; Tanaka, E | 1 |
| Briggs, S; Freedland, RA | 1 |
| Cimino, F; Salvatore, F | 1 |
| Brandt, JT; Fausto, N; Kesner, L | 1 |
| Clancy, PE; Henley, KS; Laughrey, EG; Lyra, LG | 1 |
| Colombo, JP; Lavinha, F; Lowenthal, A; Terheggen, HG | 1 |
| Milner, JA; Visek, WJ | 1 |
| Read, LJ | 3 |
| Eskelin, LE; Perheentupa, J; Rapola, J; Simell, O; Visakorpi, JK | 1 |
| Hayaishi, O; Yamamoto, S; Yamauchi, T | 1 |
| Thaler, MM | 1 |
| Krebs, HA; Stubbs, M | 1 |
| Beaudry, MA; Collu, R; Dallairf, L; Ducharme, JR; Leboeuf, G; Letarte, J; Melancon, SB | 1 |
| Goto, I; Kobayashi, T; Shigeto, H; Yamada, T | 1 |
| Shimizu, H | 1 |
| Arbour, JF; Dubé, J; Flessas, J; Laberge, M; Lafleur, L; Lambert, MA; Lemay, JF; Mitchell, GA; Valle, D; Vanasse, M | 1 |
| Laframboise, R; Mandell, R; Pichette, J; Shih, VE | 1 |
| Brochu, P; Jasmin, G; Lambert, MA; Qureshi, IA; Seidman, EG; Smith, L | 1 |
| Baverel, G; Martin, G; Vincent, N | 1 |
| Hatase, O; Hosokawa, K; Itano, T; Janjua, NA; Kugoh, T; Matsui, H; Tokuda, M | 1 |
| Costello, M; Edwards, MR; O'Sullivan, WJ; Schofield, PJ | 2 |
| Knödgen, B; Sarhan, S; Seiler, N | 1 |
| Mitkov, D | 2 |
| Azuma, T; Higa, S; Kishimoto, S; Sakoda, S; Suzuki, T; Tsujino, S | 1 |
| Almond, MK; Cohen, RD; Flynn, G; Iles, RA; Smith, A | 1 |
| Knopman, DS; Shih, VE; Tuchman, M | 1 |
| Eto, Y; Maekawa, K; Shimizu, H | 1 |
| Inoue, I; Kuno, T; Miyazaki, S; Saheki, T | 1 |
| Botschner, J; Scriver, CR; Simell, O; Smith, DW | 1 |
| Alonso, E; García-España, A; Girbés, J; Rubio, V | 1 |
| Daune, G; Gerhart, F; Grauffel, C; Seiler, N | 1 |
| Hartung, HD | 1 |
| Bates, D; Dale, G; Shaw, PJ | 1 |
| Chorváth, B; Forgács, A; Horáková, K; Perényi, T; Valentová, N | 1 |
| Cheung, CW; Cohen, NS; Raijman, L | 1 |
| Bonnefont, JP; Chadefaux, B; Kamoun, P; Rabier, D; Saudubray, JM; Shih, VE | 1 |
| Zieve, L | 1 |
| Alme, A; Broch, H; Gjessing, LR; Lie, SO; Lunde, HA; Undrum, T | 1 |
| Alvarez, L; Coude, FX; Fabregas, I; Fernandez Alvarez, E; Grimber, G; Pineda, M; Ribes, A; Rodes, M | 1 |
| Bachmann, C; Colombo, JP; Dionisi Vici, C; Gambarara, M; Sabetta, G | 1 |
| Baska, RE; Harris, DJ; Siegel, C | 1 |
| Inoue, I; Kayanuma, K; Koike, R; Koura, M; Miyatake, T; Nakajima, M; Saheki, T; Takeshita, K; Uono, M; Yuasa, T | 1 |
| Oyanagi, K | 1 |
| Inoue, I; Kayanuma, K; Koike, R; Miyatake, T; Nakajima, M; Saheki, T; Sakoda, K; Takeshita, K; Uono, M; Yuasa, T | 1 |
| Hashiba, M; Noguchi, R; Shimoji, K; Tomita, Y | 1 |
| Akiyoshi, H; Ichihara, K; Inoue, I; Ishii, S; Mito, T; Nakajima, M; Saheki, T; Takakura, H; Takashima, S; Takeshita, K | 1 |
| Gordon, BA; Haust, MD | 2 |
| Fujimori, K; Koike, R; Miyatake, T; Yuasa, T | 1 |
| Gatfield, DP; Gordon, BA; Haust, MD | 1 |
| Fujimori, K; Inoue, I; Koike, R; Miyatake, T; Saheki, T; Yuasa, T | 1 |
| Halangk, W; Letko, G | 1 |
| Janssens, PA; Wilkes, GE | 1 |
| Biscoping, J; Hempelmann, G; Michaelis, G | 1 |
| Halpern, YS; Metzer, E; Shaibe, E | 1 |
| Barth, CA; de Vrese, M | 1 |
| Chandler, MD; McCandless, DW; Sears, ES | 1 |
| Dyken, PR; Hartlage, PL; Hommes, FA; Metoki, K; Roesel, RA | 1 |
| Rogers, QR; Visek, WJ | 1 |
| Rantamäki, P; Soini, J | 1 |
| Clow, CL; Mackenzie, S; Scriver, CR; Simell, O | 1 |
| Simell, O; Takki, K | 1 |
| Boswell, M; Hoogenraad, NJ; Thaler, MM | 1 |
| Katunuma, N; Nishii, Y; Okada, M | 1 |
| Charles, R | 1 |
| Joshi, PC; Pathak, HD | 1 |
| Veerkamp, JH | 1 |
| Ziegler, K | 1 |
| Estis, LF; Haschemeyer, RH; Meister, A; Trotta, PP | 1 |
| Haschemeyer, RH; Meister, A; Pinkus, LM; Trotta, PP | 1 |
| Chalupa, W; Clark, J; Lavker, R; Opliger, P | 1 |
| Omura, H; Osajima, Y; Tsukamoto, T | 1 |
| Hellebust, JA; Liu, MS | 1 |
| Brenton, DP; Cusworth, DC; Hartley, S; Kuzemko, JA; Lumley, S | 1 |
| Asafov, GB; Ekisenina, NI; Ivanova, LM; Lumel'skiĭ, VIa; Smagin, VG | 1 |
| Cohen, PP; Reddy, MK; Wixom, RL | 1 |
| Saheki, T | 1 |
| Ampola, MG | 1 |
| Szám, I | 1 |
| Causa, P; Perri, GC | 1 |
| Nordmann, J; Nordmann, R; Petit, MA | 1 |
| Girard, PF; Kopp, N; Trillet, M | 1 |
| Heinonen, H; Schreck-Purola, I; Setälä, K | 1 |
| Miertsch, HJ; Róka, L | 1 |
| Gamble, JG; Lehninger, AL | 1 |
| Pollitt, R; Wright, T | 1 |
| Antoniello, S; Cacciatore, L; De Ritis, F; Valentino, B | 1 |
| Hems, R; Krebs, HA; Lund, P | 1 |
| Fell, V; Pollitt, RJ; Sampson, GA; Wright, T | 1 |
| Hegedüs-Wein, I; Szám, I; Szentner, J; Szilárd, T; Vass, A | 1 |
| Poe, WE; Wilson, RP | 1 |
| Cathelineau, L; Polonovski, C; Saudubray, JM | 1 |
| Burgess, EA; Butler, LJ; Levin, B; Oberholzer, VG; Palmer, T | 1 |
| Colombo, JP | 2 |
| Cimino, F; Salvatore, F; Venuta, S | 1 |
| Hager, SE; Jones, ME | 1 |
| Barrio, A; Carlisky, NJ | 1 |
| Freeman, JM; Levy, HL; Lindenbaum, JE; Sunshine, P | 1 |
| Bergman, EN; Williams, HH; Wolff, JE | 1 |
| Dojcinov, D; Dorf, G; Gravagne, G; Hall, S; James, IM; MacDonell, L; Michel, H | 1 |
| Bungert, HJ; Leonhardt, H | 1 |
| Asmar, JA; Daghir, NJ; Sifri, M | 1 |
| Berenberg, W; Kang, ES | 1 |
| Anakura, M; Arashima, S; Matsuda, I; Nambu, H; Takekoshi, Y | 1 |
| Hornig, D; Weber, F; Wiss, O | 1 |
| Goldstein, L; McBean, RL | 1 |
| Biswas, SD; Kleinberg, I | 1 |
| Waldschmidt, M | 1 |
| Costa, AA; Ganc, AJ; Miszputen, SJ; Reibscheid, S; Vilela, MP | 1 |
| Melzer, H; Weber, D; Wotzka, R | 1 |
| Dietz, RW; Flipse, RJ | 1 |
| Schulman, JD; Shih, VE | 1 |
| Mille, T; Pastorino, G | 1 |
| Kekomäki, M; Pentikäinen, P; Schwartz, AL | 1 |
| Kajii, T; Matsuda, I; Sugai, M | 1 |
| Hermann, G | 1 |
| Cedrangolo, F; Cutinelli, L; Salvatore, F; Sorrentino, L; Tramonti, C | 1 |
| Bertrand, L; Michel, H; Ogé, P | 1 |
| Chen, CH; Koeppe, RE; Meghal, SK; O'Neal, RM; Reynolds, CS | 1 |
| Efron, ML; Shahidi, NT | 1 |
| Grossi, CE; Prytz, B; Rousselot, LM | 2 |
| Atarova, GT; Olenicheva, LS | 1 |
| Cavallo, F; Coghe, M; Grillo, MA | 1 |
| Charbonneau, R; Roberge, A | 2 |
| Stähler, F | 1 |
| Schäfer, W | 1 |
| Nordmann, R | 1 |
| Efron, ML; Moser, HW; Shih, VE | 1 |
| Bickel, H; Feist, D; Kekomäki, M; Müller, H; Quadbeck, G | 1 |
| Brady, CJ | 1 |
| Balestrieri, C; Cittadini, D; De Cristofaro, D | 1 |
| Estes, FL; Wetzel, RL | 1 |
| Dupuy, R; Thiroloix, J | 1 |
| Gray, RG; Hill, SE; Pollitt, RJ | 2 |
| Zollner, H | 1 |
| Yamashita, F; Yoshida, I | 1 |
| Applegarth, DA; Farrell, K; Kirby, LT; Verity, CM | 1 |
| Itakura, Y; Nakao, T; Oyanagi, K; Sakamoto, S; Sogawa, H; Tsuchiyama, A; Wagatsuma, K; Yachi, A | 1 |
| Ban, M; Kato, T; Mizutani, N | 2 |
| Hommes, FA; Metoki, K | 1 |
| Dyken, P; Hommes, FA; Kelloes, C; Metoki, K; Trefz, J | 1 |
| Cerra, FB; Goodman, MW; Konstantinides, FN; Zieve, L | 1 |
| Brusilow, SW | 1 |
| Blankenship, PR; Coryell, ME; Hommes, FA; Roesel, RA | 1 |
| Blok, IuE; Loginov, AS | 1 |
| Baker, DH; Czarnecki, GL | 1 |
| Carter, AL; Eller, AG; Evans, BA; Hommes, FA | 1 |
| Batshaw, ML; Brusilow, SW; Starrett, A; Thomas, GH; Wachtel, RC | 1 |
| Meijer, AJ; Van Roermund, CW; Wanders, RJ | 1 |
| Ferenci, P; Wewalka, F | 1 |
| Herzfeld, A; Mandell, R; Shih, VE | 2 |
| Cathelineau, L; Charpentier, C; Coude, FX; Frezal, J; Grimber, G; Ogier, H; Parvy, P; Saudubray, JM | 1 |
| Casanello-Ertl, D; Duducgian-Vartavarian, L; Jones, MR; Kopple, JD; Pardridge, WM | 1 |
| Leisinger, T; Meile, L; Soldati, L | 1 |
| Beemer, FA; Desplanque, J; Gerards, LJ; van der Heiden, C; van Dijk, HA | 1 |
| Blanding, JH; Tremblay, GC; Wendler, PA | 1 |
| Herlong, HF; Maddrey, WC; Walser, M | 1 |
| Cohen, PP | 1 |
| DeLong, GR; Glick, TH | 1 |
| Acquarone, N; Deferrari, G; Garibotto, G; Ghiggeri, GM; Robaudo, C; Tizianello, A | 1 |
| Kubota, K; Murakami, T; Yamashita, F; Yoshida, I; Yoshino, M | 1 |
| Cerri, C; Fici, F; Scarlato, G | 1 |
| Parks, JK; Stumpf, DA | 1 |
| Batshaw, ML; Brusilow, SW; Walser, M | 1 |
| Akaboshi, I; Katsuki, T; Matsuda, I; Nagata, N; Ohtsuka, H; Yamamoto, J | 1 |
| Gatfield, PD; Gordon, BA; Haust, MD | 1 |
| Smith, I | 1 |
| Batshaw, M; Stewart, PM; Valle, D; Walser, M | 1 |
| Bazer, FW; Tou, W; Wu, G | 1 |
| Gray, RG; Green, A; Hall, S; McKeown, C | 1 |
| Daune-Anglard, G; Grauffel, C; Knödgen, B; Sarhan, S; Seiler, N | 1 |
| Butterworth, RF; Knödgen, B; Sarhan, S; Seiler, N; Therrien, G | 1 |
| Hartman, WJ; Prior, RL; Torre, PM | 1 |
| Bébin, B; Candito, M; Chambon, P; Chazalette, JP; Ferraci, JP; Mathieu, M; Sebag, F; Vianey-Saban, C | 1 |
| Elzalabany, MM; Madina, H; Morsy, MR; Ramadan, MA; Sharaf, SA; Soliman, AT | 1 |
| Gustafson, LA; Meijer, AJ; Romp, N; van Woerkom, GM | 1 |
| Knoedgen, B; Sarhan, S; Seiler, N | 1 |
| Hornsperger, JM; Knoedgen, B; Sablone, M; Sarhan, S; Seiler, N | 1 |
| Flynn, NE; Knabe, DA; Wu, G | 1 |
| Daune-Anglard, G; Seiler, N | 1 |
| Beliveau Carey, G; Brusilow, S; Cheung, CW; Cohen, NS; Raijman, L | 1 |
| Wu, G | 1 |
| Callaghan, RC; Gil-Benso, R; Juan, G; O'Connor, JE | 1 |
| Donati, MA; Filippi, L; Resti, M; Zammarchi, E | 1 |
| Dewar, RA; Gatfield, DP; Gordon, BA; Haust, MD | 1 |
| Dallaire, L; Feoli-Fonseca, JC; Lambert, M; Melançon, SB; Millington, DS; Mitchell, G; Qureshi, IA | 1 |
| de Martinville, B; Demmer, LA; Dowton, SB; Kim, JM | 1 |
| Haust, MD | 1 |
| Boveé, WM; Chamuleau, RA; Karlsen, OT; Mass, MA; Vogels, BA | 1 |
| Flynn, NE; Wu, G | 1 |
| Jiménez, C; Lluch-Fernández, MD; Marchante-Serrano, C; Navarro-Quesada, FJ; Vaquero-Abellán, M | 1 |
| Seiler, N | 2 |
| Bonocore, G; Buonocore, G; Ciani, F; Donati, MA; Pasquini, E; Shih, VE; Zammarchi, E | 1 |
| Fukushige, T; Kakinoki, H; Kobayashi, K; Saheki, T | 1 |
| Nagao, M; Oyanagi, K | 1 |
| Britton, HG; Llorente, P; Rubio, V | 1 |
| Chowdhury, S; Christoffels, VM; Darlington, GJ; Iwase, K; Kimura, T; Lamers, WH; Matsuzaki, H; Mori, M; Takiguchi, M | 1 |
| Cynober, L; Farges, MC; Sarret, A; Vasson, MP | 1 |
| Arena, ME; Manca de Nadra, MC; Saguir, FM | 1 |
| Almashanu, S; Biery, B; Camacho, JA; Casey, R; Goodman, BK; Hu, CA; Lambert, M; Mitchell, GA; Obie, C; Steel, G; Valle, D | 1 |
| Fukushige, T; Kobayashi, K; Li, MX; Nakajima, T; Saheki, T; Seiler, N | 1 |
| Celli, M; Crifò, C; D'Eufemia, P; Finocchiaro, R; Giardini, O; Salerno, C | 1 |
| Arnold, M; Bitzi, R; Colombani, PC; Frey, W; Frey-Rindova, P; Langhans, W; Wenk, C | 1 |
| Eto, Y; Kanazawa, N; Kira, J; Ohashi, T; Saito, T; Tsujino, S; Yamada, T | 1 |
| Finazzi Agrò, A; Floris, G; Lorrai, A; Medda, R; Padiglia, A | 1 |
| Hotston-Moore, A; Lobley, GE; Milano, GD | 1 |
| Haynes, TE; Li, H; Meininger, CJ; Wu, G | 1 |
| Iwata, K; Kajimura, M; Sakamoto, T | 1 |
| Bauer, MF; Bieger, I; Gempel, K; Gerbitz, KD; Hofmann, S; Pontz, BF; Stadler, S | 1 |
| Lobley, GE; Milano, GD | 1 |
| Kanazawa, N; Miyamoto, T; Tsujino, S | 1 |
| Dehne, MG; Fuchs, M; Hempelmann, G; Mühling, J; Sablotzki, A; Spatz, J; Weiss, S | 1 |
| Hayakawa, C; Kanazawa, N; Miyamoto, T; Tsujino, S | 1 |
| Frick, NT; Wright, PA | 1 |
| Doutreleau, S; Geny, B; Lampert, E; Lonsdorfer, J; Mettauer, B; Piquard, F; Schaefer, A | 1 |
| Costa Rosa, LF; Lancha, AH; Mendonça, JR; Meneguello, MO | 1 |
| Antonelli, AC; dos Santos Michima, LE; Kitamura, SS; Maruta, CA; Mori, CS; Ortolani, EL; Sucupira, MC | 1 |
| Aalto, M; Lukkarinen, M; Näntö-Salonen, K; Pulkki, K; Simell, O | 1 |
| Ballantyne, JS; Chew, SF; Hiong, KC; Ip, YK; Loong, AM; Tam, WL; Wong, WP | 1 |
| DAVIDSON, CS; FAST, BB; STORMONT, JM; WOLFE, SJ | 1 |
| CAMPBELL, JW | 1 |
| CARACCIOLI, MD; CIMINO, F; CITTADINI, D; SALVATORE, F | 1 |
| GERSHENOVITCH, ZS; KRICHEVSKAYA, AA; SHUGALEI, WS | 1 |
| GIULIANI, V | 1 |
| Hutchinson, JH; Jolley, RL; Labby, DH | 1 |
| Hutchinson, JH; Labby, DH | 1 |
| ANDERSON, RA; KIRKPATRICK, CH | 1 |
| CAMERON, JA; VINCENT, WF | 1 |
| CRAIG, LC; KING, TP; RUTTENBERG, MA | 1 |
| KAKIMOTO, M; KURAISHI, K; SHIOYA, A; TAMAMA, Y | 1 |
| CIMINO, F; CITTADINI, D; DAYELLO CARACCIOLO, M; SALVATORE, F | 1 |
| BARNES, RH; BRADFIELD, RB; LABADAN, BA; SIYAMOGLU, B | 1 |
| BROWN, H | 1 |
| LUCK, JM; MURRAY, K; NEUSTAEDTER, J; RASMUSSEN, PS | 1 |
| KESNER, L | 1 |
| KANTERS, A; KNAUFF, HG; SEYBOLD, D | 1 |
| ROBERTS, E; SIMONSEN, DG | 1 |
| Blachier, F; Mouillé, B; Robert, V | 1 |
| Baldwin, RL; Bequette, BJ; Oba, M; Owens, SL | 1 |
| Ball, RO; Pencharz, PB; Shoveller, AK; Urschel, KL | 1 |
| Bernier, NJ; Essex-Fraser, PA; Murray, BW; Steele, SL; Stevens, ED; Wright, PA | 1 |
| Berger, R; Besley, GT; Cleary, MA; de Koning, TJ; Dorland, L; Duran, M; Mandell, R; Olpin, SE; Poll-The, BT; Shih, VE | 1 |
| Biswas, K; Datta, S; Kharbuli, ZY; Saha, N; Sarma, D | 1 |
| Chew, SF; Hiong, KC; Ip, YK; Lee, SM; Loong, AM; Wong, WP | 1 |
| Al-Dirbashi, OY; Al-Hassnan, ZN; Rashed, MS | 1 |
| Djais, A; Hoshino, E; Sato, N; Uematsu, H | 1 |
| Chew, SF; Hiong, KC; Ip, YK; Lee, SJ; Lee, SM; Loong, AM; Tay, YL; Tng, YY; Wee, NL; Wilson, JM; Wong, WP | 1 |
| Ball, RO; Pencharz, PB; Urschel, KL; Wilkinson, CW | 1 |
| Bhattacharjee, A; Biswas, K; Datta, S; Kharbuli, ZY; Saha, N | 1 |
| Davies, NA; Hodges, SJ; Jalan, R; Wright, G | 1 |
| Aizawa, T; Hasegawa, I; Iwabuchi, N; Kimoto, KI; Kudo, T; Nakajima, M; Sasaki, S; Sumida, H; Sunairi, M; Suzuki, KI; Tamura, T; Ve, NB | 1 |
| Castillo, L; Erez, A; Lee, B; Marini, JC | 1 |
| Barańczyk-Kuźma, A; Chrzanowska, A; Graboń, W; Mielczarek-Puta, M | 1 |
| Eichinger-Öttl, U; Ertl, C; Haberlandt, E; Häberle, J; Heinz-Erian, P; Karall, D; Rostásy, K; Scholl-Bürgi, S; Sigl, SB | 1 |
| Davies, DC; Davies, NA; Fuskevåg, OM; Habtesion, A; Hodges, SJ; Jalan, R; Stadlbauer, V; Wright, G; Ytrebø, LM; Zwingmann, C | 1 |
| Cobos, MJ; Fuskevåg, OM; Jalan, R; Kalstad, T; Kristiansen, RG; Maehre, H; Revhaug, A; Rose, CF; Ytrebø, LM | 1 |
| Laberge, T; McDonald, MD; Walsh, PJ | 1 |
| Demura, S; Komatsu, M; Morishita, K; Yamada, T; Yamaji, S | 1 |
| Bazer, FW; Cudd, TA; Datta, S; Keisler, DH; Lassala, A; Satterfield, MC; Spencer, TE; Wu, G | 1 |
| Arranz, JA; Córdoba, J; Oria, M; Raguer, N; Riudor, E; Romero-Giménez, J | 1 |
| Balasubramaniyan, V; Davies, NA; Habtesion, A; Jalan, R; Mookerjee, RP; Sharifi, Y; Sharma, V; Wright, G | 1 |
| Choi, DE; Lee, KW; Na, KR; Shin, YT | 1 |
| Busanello, EN; Grings, M; Knebel, LA; Leipnitz, G; Lobato, VA; Moura, AP; Pettenuzzo, LF; Ritter, L; Tonin, AM; Vargas, CR; Viegas, CM; Wajner, M; Zanatta, A | 1 |
| Busanello, EN; Fernandes, CG; Leipnitz, G; Moura, AP; Seminotti, B; Tonin, AM; Viegas, CM; Wajner, M; Zanatta, A | 1 |
| Bak, LK; Dadsetan, S; Jalan, R; Keiding, S; Ott, P; Schousboe, A; Sørensen, M; Vilstrup, H; Waagepetersen, HS | 1 |
| LeMoine, CM; Walsh, PJ | 1 |
| Horiuchi, M; Kanesada, H; Kirisako, T; Kokubo, T; Miyata, T; Nishimura, A; Watanabe, K | 1 |
| Davies, N; Habtesion, A; Jalan, R; Jover-Cobos, M; Lee, K; Noiret, L; Romero-Gomez, M; Sharma, V | 1 |
| Banerjee, B; Bhuyan, G; Saha, N | 1 |
| Fuskevåg, OM; Jalan, R; Kristiansen, RG; Mæhre, H; Revhaug, A; Rose, CF; Ytrebø, LM | 1 |
| Hu, S; Li, X; McNeal, CJ; Meininger, CJ; Rezaei, R; Wu, G | 1 |
| Rahimi, RS; Rockey, DC | 1 |
| Sussman, NL | 1 |
| Andreola, F; Balasubramaniyan, V; De Chiara, F; Jalan, R; Khetan, V; Malago, M; Mookerjee, RP; Pinzani, M; Rombouts, K | 1 |
| Kristiansen, RG | 1 |
| Bailey, C; Cantor, NL; Ernst, SL; Gappmaier, E; Longo, N; Pasquali, M; Price, LB | 1 |
| Fernie, AR; Joshi, V | 1 |
| Arias, N; Hadjihambi, A; Jalan, R; Sheikh, M | 1 |
| Bukofzer, S; Clasen, K; Durkalski, V; Fontana, RJ; Ganger, D; Gottfried, M; Hameed, B; Hanje, AJ; Koch, D; Lee, WM; Little, L; Ravis, WR; Sherker, A; Stravitz, RT; Subramanian, RM | 1 |
| Hua, Q; Liu, L; Liu, Y; Nie, X; Yang, C; Zhang, H; Zhao, GP | 1 |
| Eto, K; Funahashi, A; Furuie, S; Furukawa, T; Gao, Q; Horiuchi, M; Kadowaki, T; Kuroda, E; Moriyama, M; Nakamura, Y; Saheki, T; Setogawa, Y; Sinasac, DS; Tai, YH; Takano, K; Ushikai, M; Yamamura, KI; Yasuda, I | 1 |
| Alsahhar, JS; Rahimi, RS | 1 |
| Bazer, FW; Gilbreath, KR; Nawaratna, GI; Satterfield, MC; Wickersham, TA; Wu, G | 1 |
| Ibayashi, Y; Lee, Y; Nagasaki, Y; Ngo, DN; Nishikawa, Y; Vong, LB | 1 |
| Banerjee, B; Hasan, R; Koner, D; Saha, N | 1 |
| Li, L; Wu, X; Yang, C; Zhang, H; Zhang, Y; Zhuang, N | 1 |
| Alimirah, M; Gordon, SC; Sadiq, O | 1 |
| Deelman-Driessen, C; Gaastra, BF; Pols, T; Poolman, B; Singh, S | 1 |
| Bazer, FW; Cleere, JJ; Gilbreath, KR; Satterfield, MC; Wu, G | 1 |
| Cai, YN; Jiang, MY; Li, XZ; Lin, YT; Liu, L; Mei, HF; Peng, MZ; Shao, YX; Sheng, HY; Su, L; Yin, X | 1 |
| Azad, AK; Mulik, S; Paidipally, P; Radhakrishnan, RK; Samten, B; Schlesinger, LS; Sivangala Thandi, R; Tripathi, D; Vankayalapati, R | 1 |
| Tapper, EB | 2 |
| Bémeur, C; Bosoi, CR; Clément, MA; Oliveira, MM; Rose, CF; Tremblay, M | 1 |
| Fukuyama, T; Hoshino, Y; Kaneko, T; Kodaira, M; Matsuno, A; Sekijima, Y; Takano, K; Yazaki, M | 1 |
| Vilchez, RA; Wang, X | 1 |
| Dalal, A; Jain, A; Kumar, A; Mahajan, B; Sachdeva, S; Sharma, BC; Sonika, U; Srivastava, S | 1 |
| Bajaj, JS; Bukofzer, S; Devarakonda, KR; Jamil, K; Potthoff, A; Pyrsopoulos, N; Rahimi, RS; Ram Bhamidimarri, K; Safadi, R; Thabut, D; Wang, L | 1 |
| Da, BL; Kovalic, AJ; Lee, TP | 1 |
| Fukui, K; Ishihara, N; Kakuma, T; Matsunari, H; Nagashima, H; Takahashi, T; Uchikura, A; Watanabe, M; Watanabe, Y; Yamashita, Y; Yoshino, M | 1 |
| Ji, X; Jiang, P; Li, Y; Yan, W; Yue, H | 1 |
| Chen, Y; Wang, G; Wang, Z; Yan, X; Zhang, L; Zhao, F; Zhou, M | 1 |
| Ding, Y; Koda, Y; Nagasaki, Y; Nishikawa, Y; Shashni, B; Takeda, N; Tanaka, N; Zhang, X | 1 |
26 review(s) available for ammonium hydroxide and ornithine
| Article | Year |
|---|---|
Ammonia metabolism, urea cycle capacity and their biochemical assessment.
Topics: Amino Acids; Ammonia; Animals; Arginine; Brain; Citric Acid Cycle; Humans; Nutritional Requirements; Ornithine; Orotic Acid; Polyamines; Quaternary Ammonium Compounds; Urea | 1979 |
Hyperornithinemia, hyperammonemia, homocitrullinuria (HHH) syndrome: presentation as acute liver disease with coagulopathy.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Blood Coagulation Disorders; Child, Preschool; Citrulline; Female; Humans; Liver Diseases; Liver Function Tests; Ornithine; Syndrome | 1992 |
Conditional deficiencies of ornithine or arginine.
Topics: Amino Acids; Amino Acids, Branched-Chain; Ammonia; Animals; Arginine; Citrulline; Female; Glycine; Hepatic Encephalopathy; Humans; Liver Cirrhosis; Lysine; Models, Biological; Ornithine; Orotic Acid; Pregnancy; Protein Deficiency; Urease | 1986 |
Regulation of the urea cycle and TCA cycle by ammonia.
Topics: Alanine Transaminase; Amino Acids; Ammonia; Amobarbital; Animals; Aspartate Aminotransferases; Aspartic Acid; Carbon Isotopes; Citrates; Citric Acid Cycle; Cytoplasm; Diabetes Mellitus, Experimental; Dietary Proteins; Glutamates; Hydrocortisone; In Vitro Techniques; Isoenzymes; Ketoglutaric Acids; Liver; Mice; Mitochondria, Liver; N-Glycosyl Hydrolases; Niacinamide; Nucleotides; Ornithine; Oxidoreductases; Oxygen Consumption; Pyrophosphatases; Pyruvates; Rats; Transaminases; Urea | 1966 |
[Regulatory conditions for urea biosynthesis--from the standpoint of organ level].
Topics: Amino Acids; Ammonia; Animals; Arginine; Aspartic Acid; Glutamates; Glutamine; In Vitro Techniques; Liver; Nitrogen; Nutritional Physiological Phenomena; Ornithine; Perfusion; Rats; Urea | 1972 |
Phenylketonuria and other disorders of amino acid metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Child, Preschool; Counseling; Cystathionine; Cystinosis; Cystinuria; Diet Therapy; Dietary Proteins; Family; Female; Hartnup Disease; Histidine; Homocystinuria; Humans; Hyperglycemia; Infant; Infant, Newborn; Lysine; Maple Syrup Urine Disease; Ornithine; Phenylketonurias; Pregnancy; Proline; Tyrosine | 1973 |
[Hyperammoniemia and its treatment].
Topics: Ammonia; Arginine; Aspartic Acid; Humans; Ketoglutaric Acids; Liver; Malates; Metabolism, Inborn Errors; Ornithine; Orotic Acid | 1973 |
[Hereditary enzyme defects of the urea cycle].
Topics: Adult; Ammonia; Arginase; Arginine; Child; Child, Preschool; Citrulline; Enzymes; Female; Humans; Infant; Infant, Newborn; Ligases; Lyases; Male; Metabolism, Inborn Errors; Ornithine; Ornithine Carbamoyltransferase; Phosphotransferases; Succinates; Transaminases; Urea | 1971 |
[Etiological mechanism of Reye's syndrome--from the viewpoint of metabolic disorders].
Topics: Ammonia; Animals; Aspirin; Child; Child, Preschool; Fatty Acids; Female; Humans; Infant; Male; Mitochondria; Mitochondria, Liver; Mitochondrial ADP, ATP Translocases; Ornithine; Rats; Reye Syndrome | 1984 |
The ornithine-urea cycle: biosynthesis and regulation of carbamyl phosphate synthetase I and ornithine transcarbamylase.
Topics: Ammonia; Animals; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Dietary Proteins; Glutamates; Kinetics; Ligases; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase; Urea | 1981 |
Some regulatory aspects of urea synthesis.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Carbamyl Phosphate; Citric Acid Cycle; Dietary Proteins; Female; Glutamates; Humans; Male; Ornithine; Proteins; Urea | 1981 |
Regulation of ornithine metabolism.
Topics: Ammonia; Animals; Biological Transport; Citrulline; Cytosol; Fibroblasts; Humans; Mitochondria; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase; Urea | 1981 |
Encephalopathy of Reye's syndrome: a review of pathogenetic hypotheses.
Topics: Acidosis; Ammonia; Animals; Brain; Citrulline; Fatty Acids, Nonesterified; Glucose; Humans; Insulin; Intracranial Pressure; Lactates; Mitochondria; Mitochondria, Liver; Nitrogen; Ornithine; Rabbits; Reye Syndrome | 1982 |
Endogenous ornithine in search for CNS functions and therapeutic applications.
Topics: Ammonia; Animals; Brain; Brain Diseases; gamma-Aminobutyric Acid; Humans; Ornithine; Ornithine-Oxo-Acid Transaminase; Polyamines | 1993 |
Ornithine aminotransferase as a therapeutic target in hyperammonemias.
Topics: Ammonia; Animals; Enzyme Inhibitors; Humans; Ornithine; Ornithine-Oxo-Acid Transaminase; Thioacetamide | 1997 |
[Hyperornithinemia-hyperammonemia-homocitrullinuria (H.H.H.) syndrome].
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Diagnosis, Differential; Humans; Infant, Newborn; Ornithine; Ornithine-Oxo-Acid Transaminase; Syndrome | 1998 |
Ornithine aminotransferase, a potential target for the treatment of hyperammonemias.
Topics: Ammonia; Animals; Biogenic Polyamines; Brain; Chorioretinitis; Enzyme Inhibitors; Humans; Hyperammonemia; Kidney; Liver; Mice; Ornithine; Ornithine-Oxo-Acid Transaminase; Thioacetamide; Urea | 2000 |
[Molecular genetic studies of mitochondrial ornithine transporter deficiency (HHH syndrome)].
Topics: Amino Acid Transport Systems, Basic; Ammonia; Animals; Base Sequence; Carrier Proteins; Citrulline; Humans; Membrane Transport Proteins; Mitochondria; Molecular Sequence Data; Mutation; Nervous System Diseases; Ornithine; Syndrome | 2001 |
[New insights into arginase. Part II. Role in physiology and pathology].
Topics: Ammonia; Animals; Arginase; Arginine; Glutamates; Humans; Ornithine; Polyamines | 2008 |
Novel Ammonia-Lowering Agents for Hepatic Encephalopathy.
Topics: Ammonia; Carbon; Gastrointestinal Agents; Glycerol; Hepatic Encephalopathy; Humans; Ornithine; Oxides; Phenylbutyrates; Polyethylene Glycols; Urea | 2015 |
Treatment of Overt Hepatic Encephalopathy.
Topics: Amino Acids, Branched-Chain; Ammonia; Arteriovenous Fistula; Dipeptides; Gastrointestinal Agents; Glycerol; Hepatic Encephalopathy; Humans; Lactulose; Liver Failure; Malnutrition; Ornithine; Phenylbutyrates; Probiotics; Rifamycins; Rifaximin | 2015 |
Current state of knowledge of hepatic encephalopathy (part I): newer treatment strategies for hyperammonemia in liver failure.
Topics: Ammonia; Animals; Glutamate-Ammonia Ligase; Health Knowledge, Attitudes, Practice; Hepatic Encephalopathy; Humans; Hyperammonemia; Liver Failure; Ornithine; Treatment Outcome | 2016 |
Citrulline metabolism in plants.
Topics: Adaptation, Physiological; Amino Acid Transport Systems; Ammonia; Animals; Arabidopsis; Argininosuccinate Synthase; Bacteria; Biological Transport; Carbamyl Phosphate; Citrulline; Cucurbitaceae; Fungi; Gene Expression Regulation, Plant; Humans; Ornithine; Ornithine Carbamoyltransferase; Stress, Physiological | 2017 |
Hepatic encephalopathy: a critical current review.
Topics: Albumins; Ammonia; Anti-Bacterial Agents; Bile Acids and Salts; Brain; Brain Edema; Cognitive Dysfunction; Dipeptides; Energy Metabolism; Gastrointestinal Agents; Hepatic Encephalopathy; Humans; Lactulose; Liver Cirrhosis; Ornithine; Portasystemic Shunt, Surgical; Prognosis; Psychometrics; Severity of Illness Index; Synaptic Transmission | 2018 |
Updates on the pathophysiology and therapeutic targets for hepatic encephalopathy.
Topics: Amino Acids, Aromatic; Amino Acids, Branched-Chain; Ammonia; Dipeptides; Fecal Microbiota Transplantation; Frailty; Gastrointestinal Agents; Gastrointestinal Microbiome; Glycerol; Hepatic Encephalopathy; Humans; Hypertension, Portal; Lactulose; Liver Cirrhosis; Ornithine; Phenylbutyrates; Polyethylene Glycols; Probiotics; Rifaximin; Trace Elements; Zinc | 2019 |
Novel Therapies in Hepatic Encephalopathy.
Topics: Acetylcarnitine; Albumins; Ammonia; Dipeptides; Fecal Microbiota Transplantation; Flumazenil; GABA Modulators; Glycerol; Hepatic Encephalopathy; Humans; Nootropic Agents; Ornithine; Phenylbutyrates; Polyethylene Glycols; Probiotics; Surface-Active Agents | 2020 |
13 trial(s) available for ammonium hydroxide and ornithine
| Article | Year |
|---|---|
[Amino acids prevent hepatic encephalopathy. Ornithine-aspartate in hyperammonemia--results of a study].
Topics: Ammonia; Aspartic Acid; Clinical Trials as Topic; Double-Blind Method; Hepatic Encephalopathy; Humans; Ornithine | 1989 |
[On the therapy of liver diseases with ornithine aspartate].
Topics: Acute Disease; Alanine Transaminase; Ammonia; Aspartic Acid; Bilirubin; Cholangitis; Chronic Disease; Drug Tolerance; Fatty Liver; Hepatic Encephalopathy; Hepatitis; Humans; Iron; Liver Cirrhosis; Liver Diseases; Liver Function Tests; Ornithine; Sulfobromophthalein | 1969 |
The use of ornithine salts of branched-chain ketoacids in portal-systemic encephalopathy.
Topics: Adult; Aged; Amino Acids; Amino Acids, Branched-Chain; Ammonia; Calcium; Clinical Trials as Topic; Double-Blind Method; Electroencephalography; Female; Hepatic Encephalopathy; Humans; Keto Acids; Ketoglutaric Acids; Male; Middle Aged; Nitrogen; Ornithine | 1980 |
Chronic sodium benzoate therapy in children with inborn errors of urea synthesis: effect on carnitine metabolism and ammonia nitrogen removal.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Carnitine; Child; Child, Preschool; Female; Humans; Male; Nitrogen; Ornithine; Retrospective Studies; Syndrome; Urea | 1996 |
Chronic arginine aspartate supplementation in runners reduces total plasma amino acid level at rest and during a marathon run.
Topics: 3-Hydroxybutyric Acid; Adult; Amino Acids; Ammonia; Arginine; Aspartic Acid; Carbohydrates; Creatine Kinase; Cross-Over Studies; Dietary Supplements; Double-Blind Method; Fatty Acids; Glucagon; Glycerol; Human Growth Hormone; Humans; Hydrocortisone; Insulin; L-Lactate Dehydrogenase; Male; Ornithine; Respiratory Function Tests; Running; Urea | 1999 |
L-arginine reduces exercise-induced increase in plasma lactate and ammonia.
Topics: Adult; Ammonia; Arginine; Citrulline; Double-Blind Method; Exercise; Humans; Lactates; Male; Muscle, Skeletal; Nitric Oxide; Ornithine | 2002 |
The effect of L-ornithine hydrochloride ingestion on performance during incremental exhaustive ergometer bicycle exercise and ammonia metabolism during and after exercise.
Topics: Ammonia; Athletes; Athletic Performance; Cross-Over Studies; Dietary Supplements; Double-Blind Method; Exercise; Exercise Test; Glutamic Acid; Heart Rate; Humans; Lactic Acid; Male; Muscle Fatigue; Ornithine; Oxygen Consumption; Physical Endurance; Time Factors; Urea; Young Adult | 2010 |
Ornithine ingestion improved sleep disturbances but was not associated with correction of blood tryptophan ratio in Japanese Antarctica expedition members during summer.
Topics: Adult; Ammonia; Antarctic Regions; Creatine Kinase; Double-Blind Method; Expeditions; Humans; Japan; L-Lactate Dehydrogenase; Ornithine; Seasons; Sleep; Sleep Wake Disorders; Surveys and Questionnaires; Tryptophan | 2013 |
Anaplerotic therapy in propionic acidemia.
Topics: Amino Acids; Ammonia; Carbon-Carbon Ligases; Child; Child, Preschool; Citrates; Citric Acid; Citric Acid Cycle; Dietary Supplements; Female; Glutamine; Humans; Lactic Acid; Male; Ornithine; Propionic Acidemia; Treatment Outcome | 2017 |
Ruminal microbes of adult sheep do not degrade extracellular l-citrulline.
Topics: Ammonia; Animal Feed; Animals; Arginine; Bacteria; Citrulline; Diet; Dietary Supplements; Female; Glutamic Acid; Glutamine; Ornithine; Proline; Rumen; Sheep; Urea | 2020 |
L-ornithine L-aspartate in acute treatment of severe hepatic encephalopathy: A double-blind randomized controlled trial.
Topics: Ammonia; Aspartic Acid; Hepatic Encephalopathy; Humans; Lactulose; Liver Cirrhosis; Ornithine; Rifaximin; Tumor Necrosis Factor-alpha | 2022 |
Pharmacokinetics/pharmacodynamics of L-ornithine phenylacetate in overt hepatic encephalopathy and the effect of plasma ammonia concentration reduction on clinical outcomes.
Topics: Adult; Ammonia; Hepatic Encephalopathy; Humans; Ornithine; Phenylacetates | 2022 |
Letter to the editor: l-ornithine l-aspartate in acute treatment of severe hepatic encephalopathy: A double-blind randomized controlled trial.
Topics: Ammonia; Aspartic Acid; Dipeptides; Double-Blind Method; Hepatic Encephalopathy; Humans; Ornithine | 2022 |
318 other study(ies) available for ammonium hydroxide and ornithine
| Article | Year |
|---|---|
Urea transport-defective strains of Saccharomyces cerevisiae.
Topics: Acetamides; Allantoin; Ammonia; Biological Transport, Active; Carbonyl Cyanide m-Chlorophenyl Hydrazone; Cyanides; Cycloheximide; Dinitrophenols; Formamides; Glycolates; Hydrogen-Ion Concentration; Mutation; Ornithine; Saccharomyces cerevisiae; Urea | 1976 |
Arginine metabolism by spiroplasma citri.
Topics: Ammonia; Arginine; Citrulline; Fructose; Glucose; Hydrogen-Ion Concentration; Ornithine; Spiroplasma | 1976 |
Effects of arginine infusion in infants: increased urea synthesis associated with unchanged ammonia blood levels.
Topics: Ammonia; Arginine; Bicarbonates; Child; Humans; Hydrogen-Ion Concentration; Infant; Infant, Newborn; Ornithine; Urea | 1976 |
Relationship between intramitochondrial citrate and the activity of carbamoyl-phosphate synthase (ammonia).
Topics: Adenosine Triphosphate; Ammonia; Animals; Calcimycin; Carbamoyl-Phosphate Synthase (Ammonia); Citrates; Citrulline; Glutamates; Hydrogen-Ion Concentration; Magnesium; Malates; Mitochondria, Liver; Ornithine; Phosphotransferases; Rats | 1977 |
Arginine catabolism in Aphanocapsa 6308.
Topics: Adenosine Triphosphate; Aerobiosis; Ammonia; Arginase; Arginine; Carbon Dioxide; Citrulline; Cyanobacteria; Hydrolases; Ornithine; Urea; Urease | 1978 |
Nitrogen regulation of arginase in Neurospora crassa.
Topics: Ammonia; Arginase; Arginine; Enzyme Induction; Enzyme Repression; Glutamate Dehydrogenase; Glutamates; Glutamine; Mutation; Neurospora; Neurospora crassa; Nitrogen; Ornithine; Proline; Urease | 1977 |
Inhibition of urea synthesis by 4-pentenoic acid.
Topics: Ammonia; Animals; Aspartic Acid; Citrulline; Fatty Acids, Monounsaturated; Fatty Acids, Unsaturated; Glutamates; Liver; Ornithine; Phosphotransferases; Rats; Transferases; Urea; Valerates | 1975 |
Hyperornithinemia, hyperammonemia, and homocitrullinuria associated with decreased carbamyl phosphate synthetase I activity.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Biopsy; Carbamoyl-Phosphate Synthase (Ammonia); Child; Child, Preschool; Citrulline; Dietary Proteins; Female; Humans; Leukocytes; Liver; Lysine; Male; Microscopy, Electron; Mitochondria, Liver; Ornithine; Phosphotransferases | 1975 |
Proceedings: Hepatic ultrastructure in a child with carbamyl phosphate synthetase deficiency, hyperornithinaemia, hyperammonaemia, and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Carbamoyl-Phosphate Synthase (Ammonia); Child; Citrulline; Humans; Liver; Male; Ornithine; Phosphotransferases | 1975 |
Biochemical and genetic characterization of a carbamyl phosphate synthetase mutant of Escherichia coli K12.
Topics: Ammonia; Arginine; Carbamoyl-Phosphate Synthase (Ammonia); Carbamoyl-Phosphate Synthase (Glutamine-Hydrolyzing); Carbamyl Phosphate; Cell-Free System; Coliphages; Escherichia coli; Genes, Recessive; Glutamine; Mutagens; Mutation; Nitrosoguanidines; Ornithine; Ornithine Carbamoyltransferase; Phosphotransferases; Transduction, Genetic; Uracil Nucleotides | 1976 |
Orotic acid biosynthesis in rat liver: studies on the source of carbamoylphosphate.
Topics: Ammonia; Ammonium Chloride; Animals; Bicarbonates; Carbamates; Carbamoyl-Phosphate Synthase (Ammonia); Carbamyl Phosphate; Carbon Radioisotopes; Glutamine; Liver; Mitochondria, Liver; Ornithine; Orotic Acid; Phosphotransferases; Putrescine; Rats | 1977 |
Evidence that the catalytic and regulatory functions of carbamylphosphate synthetase from Escherichia coli are not dependent on oligomer formation.
Topics: Adenosine Triphosphate; Allosteric Regulation; Allosteric Site; Ammonia; Carbamoyl-Phosphate Synthase (Ammonia); Escherichia coli; Inosine Nucleotides; Macromolecular Substances; Magnesium; Ornithine; Phosphotransferases; Protein Binding | 1977 |
Ammonia metabolism in the rat liver in biliary obstruction.
Topics: Adenosine Triphosphate; Ammonia; Animals; Arginine; Cholestasis; In Vitro Techniques; Liver; Male; Ornithine; Rats; Urea | 1979 |
Arginine: an acutely essential amino acid for the near-adult cat.
Topics: Ammonia; Animal Nutritional Physiological Phenomena; Animals; Arginine; Cats; Growth Disorders; Ornithine | 1979 |
The effect of dietary o,p'-DDT on ureagenesis from ammonia by isolated rat hepatocytes.
Topics: Ammonia; Animals; Citrulline; DDT; In Vitro Techniques; Lactates; Liver; Male; Mitochondria, Liver; Ornithine; Rats; Urea | 1979 |
Effects of ornithine alphaketoglutarate on blood insulin, glucagon and aminoacids in alcoholic cirrhosis.
Topics: Amino Acids; Ammonia; Glucagon; Humans; Infusions, Parenteral; Insulin; Ketoglutaric Acids; Liver Cirrhosis, Alcoholic; Male; Middle Aged; Ornithine | 1979 |
Effects of branched chain alpha-ketoacids on the metabolism of isolated rat liver cells. II. Interactions with gluconeogenesis and urea synthesis.
Topics: Alanine; Ammonia; Animals; Gluconeogenesis; Humans; In Vitro Techniques; Keto Acids; Ketone Bodies; Kinetics; Lactates; Liver; Oleic Acids; Ornithine; Rats; Structure-Activity Relationship; Urea | 1979 |
Urea cycle operation in the arginine deficient rat.
Topics: Ammonia; Animals; Arginase; Arginine; Argininosuccinate Lyase; Argininosuccinate Synthase; Carbamoyl-Phosphate Synthase (Glutamine-Hydrolyzing); Citrulline; Liver; Male; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Rats; Urea | 1979 |
Ornicetil on encephalopathy. Effect of ornicetil (ornithine alpha-ketoglutarate) on encephalopathy in patients with acute and chronic liver disease.
Topics: Acute Disease; Adult; Ammonia; Chronic Disease; Drug Evaluation; Female; Hepatic Encephalopathy; Humans; Ketoglutaric Acids; Male; Middle Aged; Ornithine | 1977 |
Ammonia intoxication in the near-adult cat as a result of a dietary deficiency of arginine.
Topics: Amino Acids; Ammonia; Animal Nutritional Physiological Phenomena; Animals; Arginine; Cats; Female; Male; Ornithine; Time Factors | 1978 |
Interrelationships between gluconeogenesis and ureogenesis in isolated hepatocytes.
Topics: Ammonia; Animals; Aspartate Aminotransferases; Cycloserine; Gluconeogenesis; In Vitro Techniques; Kinetics; Liver; Male; Mitochondria, Liver; Ornithine; Pyruvates; Rats; Urea | 1978 |
Amino acid induced orotic aciduria.
Topics: Amino Acids; Ammonia; Animal Nutritional Physiological Phenomena; Animals; Arginine; Fasting; Male; Ornithine; Orotic Acid; Quaternary Ammonium Compounds; Rats; Urea; Urease | 1978 |
Attempted dietary treatment of a boy with hyperammonemia due to ornithine transferase deficiency.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Arginine; Child, Preschool; Citrates; Dietary Proteins; Humans; Lactulose; Male; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease | 1978 |
Competitive interrelationships between lysine and arginine in rat liver under normal conditions and in experimental hyperammonemia.
Topics: Alanine; Ammonia; Animals; Arginine; Drug Interactions; Liver; Lysine; Male; Ornithine; Rats; Urease | 1978 |
3-Aminopiperid-2-one, an unusual metabolite in the urine of a patient with hyperammonaemia, hyperornithinaemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Chromatography, Gas; Chromatography, Ion Exchange; Citrulline; Electrophoresis; Humans; Mass Spectrometry; Ornithine; Piperidines; Piperidones | 1978 |
[Effect of ornithine-ketoglutarate on provoked hyperammonaemia in patients with cirrhosis of the liver (author's transl)].
Topics: Ammonia; Humans; Hypertension, Portal; Ketoglutaric Acids; Liver Cirrhosis; Ornithine; Time Factors | 1978 |
Arginine: an essential amino acid for the cat.
Topics: Ammonia; Animal Nutritional Physiological Phenomena; Animals; Arginine; Cats; Hyperglycemia; Male; Nutritional Requirements; Ornithine; Rats; Spasm; Species Specificity; Vomiting | 1978 |
Regulation of urea synthesis in rat liver. Increase in the concentrations of ornithine and acetylglutamate in rat liver in response to urea synthesis stimulated by the injection of an ammonium salt.
Topics: Ammonia; Animals; Citrulline; Glutamates; Kinetics; Liver; Male; Ornithine; Quaternary Ammonium Compounds; Rats; Urea | 1978 |
The mechanism of hyperammonemia in congenital lysinuria.
Topics: Adolescent; Adult; Alanine; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Female; Humans; Lysine; Ornithine | 1979 |
[Present-day therapy of hepatic encephalopathy (author's transl)].
Topics: Acid-Base Imbalance; Ammonia; Anemia; Anti-Bacterial Agents; Exchange Transfusion, Whole Blood; Glucose; Hepatic Encephalopathy; Humans; Hypoxia; Intestinal Mucosa; Ketoglutaric Acids; Kidney; Lactulose; Liver Cirrhosis; Ornithine; Perfusion; Prognosis; Renal Dialysis | 1976 |
Ornithine methyl ester. An unusual metabolite encountered in the urine of patients with a urea cycle disorder characterized by hyperammonemia, hyperornithinemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Chromatography; Citrulline; Dansyl Compounds; Humans; Ornithine | 1977 |
Effect of supplementation of methionine and threonine to a protein free diet on urinary excretion of nitrogen and tissue free amino acids in rats.
Topics: Amino Acids; Ammonia; Animals; Drug Synergism; Female; Food, Fortified; Intestinal Mucosa; Liver; Male; Methionine; Muscles; Nitrogen; Ornithine; Protein Deficiency; Rats; Threonine; Urea | 1977 |
The effect of glucagon on ureagenesis from ammonia by isolated rat hepatocytes.
Topics: Ammonia; Animals; Citrulline; Glucagon; In Vitro Techniques; Kinetics; Liver; Male; Mitochondria, Liver; Ornithine; Rats; Urea | 1977 |
Potential hazard of therapy for Reye's syndrome with urea cycle intermediates.
Topics: Ammonia; Humans; Ornithine; Orotic Acid; Reye Syndrome; Urea | 1977 |
[Influence of ornithin-alpha-ketoglutaric acid on fatmetabolism in patients with cirrhosis of the liver (author's transl)].
Topics: Ammonia; Biotransformation; Cholesterol; Citric Acid Cycle; Endotoxins; Fatty Acids, Nonesterified; Humans; Hydroxybutyrates; Hypertension, Portal; Ketoglutaric Acids; Lipid Metabolism; Liver Cirrhosis; Ornithine; Phenols; Triglycerides; Urea | 1976 |
Effects of dietary protein and lysine levels on plasma amino acids, nitrogen retention and egg production in laying hens.
Topics: Amino Acids; Amino Acids, Essential; Ammonia; Animals; Chickens; Dietary Proteins; Dose-Response Relationship, Drug; Female; Lysine; Nitrogen; Ornithine; Oviposition; Taurine; Uric Acid | 1976 |
Congenital hyperammonemic syndromes.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinate Synthase; Argininosuccinic Aciduria; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Diagnosis, Differential; Humans; Hyperargininemia; Infant, Newborn; Infant, Newborn, Diseases; Lysine; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Syndrome; Urea | 1976 |
Hyperammonemia (ornithinemia) presenting as a unilateral cerebral mass lesion.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Astrocytes; Brain Diseases; Brain Neoplasms; Carbamoyl-Phosphate Synthase (Ammonia); Cerebral Cortex; Child, Preschool; Diagnosis, Differential; Functional Laterality; Glioma; Humans; Male; Ornithine; Syndrome | 1976 |
[Influence of ornithine aspartate on the experimentally induced hyperammoniemia. Clinico-experimental study].
Topics: Adult; Ammonia; Aspartic Acid; Humans; Liver Diseases; Ornithine | 1976 |
Hyperdibasicaminoaciduria and hyperammonemia in familial protein intolerance.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Diamino; Ammonia; Arginine; Child, Preschool; Cystinuria; Humans; Intestinal Absorption; Intestinal Mucosa; Lysine; Male; Ornithine; Renal Aminoacidurias | 1976 |
Effect of ornithine and lactate on urea synthesis in isolated hepatocytes.
Topics: Ammonia; Animals; Butyrates; Citrulline; In Vitro Techniques; Kinetics; Lactates; Liver; Male; Oleic Acids; Ornithine; Pyruvates; Rats; Starvation; Stimulation, Chemical; Urea | 1976 |
[Biochemical mechanisms of action of catalyzers of ureogenesis and their use in human therapy].
Topics: Ammonia; Arginine; Catalysis; Humans; Inactivation, Metabolic; Ketoglutaric Acids; Liver Diseases; Ornithine; Urea | 1976 |
Possible interactions between the urea cycle and synthesis of pyrimidines and polyamines in regenerating liver.
Topics: Adrenalectomy; Ammonia; Animals; Bicarbonates; Carbon Radioisotopes; Carboxy-Lyases; Hepatectomy; Liver; Liver Regeneration; Male; Ornithine; Orotic Acid; Polyamines; Pyrimidines; Rats; Urea; Urease | 1975 |
Nitrogen metabolism in the perfused cirrhotic liver of the rat.
Topics: Alanine; Ammonia; Animals; Diet; Ethanol; Glucose; Glutamates; Glutamine; Liver; Liver Cirrhosis, Experimental; Male; Nitrogen; Organ Size; Ornithine; Perfusion; Rats; Urea | 1975 |
Familial hyperargininaemia.
Topics: Amino Acids; Ammonia; Arginine; Athetosis; Child, Preschool; Chromatography; Cystinuria; Dietary Proteins; Erythrocytes; Female; Guanidines; Humans; Hyperargininemia; Infant; Infant, Newborn; Intellectual Disability; Metabolism, Inborn Errors; Muscle Spasticity; Ornithine; Umbilical Cord; Urea | 1975 |
Urinary metabolites characteristic of urea-cycle amino acid deficiency.
Topics: Amino Acids; Amino Acids, Essential; Ammonia; Animal Nutritional Physiological Phenomena; Animals; Arginine; Biotransformation; Body Weight; Carbamyl Phosphate; Citrates; Citrulline; Deficiency Diseases; Diet; Male; Nitrogen; Ornithine; Orotic Acid; Pyrimidines; Rats; Urea | 1975 |
Absence of ureogenic pathways in liver of the hagfish Bdellostoma cirrhatum.
Topics: Allantoin; Amidohydrolases; Ammonia; Animals; Arginase; Fasting; Fishes; Hagfishes; Liver; Ornithine; Purines; Urate Oxidase; Urea; Ureohydrolases | 1975 |
Lysinuric protein intolerance.
Topics: Adolescent; Adult; Alanine; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Arginine; Birth Weight; Child; Child, Preschool; Dietary Proteins; Eye Diseases; Female; Humans; Infant; Intellectual Disability; Intestinal Absorption; Liver; Lysine; Male; Nitrogen; Ornithine; Proteins; Renal Aminoacidurias; Urea | 1975 |
A possible involvement of sulfhydryl groups in the conversion of lysine monooxygenase to an oxidase.
Topics: Amines; Amino Acid Oxidoreductases; Ammonia; Arginine; Chloromercuribenzoates; Enzyme Activation; Ethylmaleimide; Kinetics; Lysine; Ornithine; Oxygen Consumption; Oxygenases; Sulfhydryl Compounds; Sulfhydryl Reagents | 1975 |
Pathogenesis of Reye's syndrome: A working hypothesis.
Topics: Ammonia; Arginine; Brain Diseases; Child; Humans; Ornithine; Reye Syndrome | 1975 |
The accumulation of aspartate in the presence of ethanol in rat liver.
Topics: Alanine; Ammonia; Ammonium Chloride; Animals; Aspartic Acid; Cytosol; Ethanol; Female; Gluconeogenesis; Glutamates; Ketoglutaric Acids; Lactates; Liver; Mitochondria, Liver; Ornithine; Rats; Urea | 1975 |
[Chronic hyperammonemia with orotic aciduria: evidence of pyrimidine pathway stimulation (author's transl)].
Topics: Alanine; Amino Acids; Ammonia; Child, Preschool; Dietary Proteins; Erythrocytes; Growth Disorders; Humans; Intellectual Disability; Leukocytes; Ornithine; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Orotate Phosphoribosyltransferase; Orotic Acid; Orotidine-5'-Phosphate Decarboxylase; Purine-Pyrimidine Metabolism, Inborn Errors; Pyrimidines; Seizures; Syndrome; Urea | 1975 |
[A case of hyperornithinemia-hyperammonemia-homocitrullinuria (HHH) syndrome with spastic paraparesis and severe distal muscle atrophy of lower limbs].
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Electromyography; Humans; Leg; Male; Muscular Atrophy; Ornithine; Paraparesis, Tropical Spastic; Spinal Cord; Syndrome | 1992 |
[The dibasic amino acid metabolic disorders].
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Blood Transfusion; Citrulline; Humans; Hyperargininemia; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Renal Dialysis | 1992 |
Hyperammonemia-hyperornithinemia-homocitrullinuria syndrome: neurologic, ophthalmologic, and neuropsychologic examination of six patients.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Child, Preschool; Citrulline; Eye Diseases; Female; Humans; Male; Nervous System Diseases; Neuropsychological Tests; Ornithine; Psychomotor Performance | 1992 |
Neonatal form of the hyperornithinaemia, hyperammonaemia, and homocitrullinuria (HHH) syndrome and prenatal diagnosis.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Cells, Cultured; Citrulline; Female; Gestational Age; Hepatitis B Surface Antigens; Humans; Hyaline Membrane Disease; Infant, Newborn; Male; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Ornithine-Oxo-Acid Transaminase; Pregnancy; Pregnancy Outcome; Prenatal Diagnosis; Syndrome | 1992 |
Glycine, a new regulator of glutamine metabolism in isolated rat-liver cells.
Topics: Ammonia; Ammonium Chloride; Animals; Carbon Dioxide; Dose-Response Relationship, Drug; Glucose; Glutaminase; Glutamine; Glycine; Liver; Male; Mitochondria, Liver; Ornithine; Rats; Rats, Wistar; Urea | 1992 |
Plasma urea and ammonia in epileptic patients and their relatives.
Topics: Adolescent; Adult; Amino Acids; Ammonia; Child; Citrulline; Epilepsy; Family; Female; Humans; Male; Middle Aged; Ornithine; Urea | 1992 |
Arginine metabolism during culture of Giardia intestinalis.
Topics: Ammonia; Animals; Arginine; Culture Media; Energy Metabolism; Giardia lamblia; Kinetics; Ornithine | 1992 |
Inhibition of ornithine aminotransferase by 5-fluoromethylornithine: protection against acute thioacetamide intoxication by elevated tissue ornithine levels.
Topics: Amino Acids; Ammonia; Animals; Biogenic Polyamines; Chemical and Drug Induced Liver Injury; Hemorrhage; Liver Diseases; Male; Mice; Ornithine; Ornithine-Oxo-Acid Transaminase; Pilot Projects; Poisoning; Thioacetamide | 1992 |
Effect of prostaglandin F2 alpha on urea synthesis and hepatic hemodynamics.
Topics: Ammonia; Animals; Dinoprost; In Vitro Techniques; Liver; Liver Circulation; Male; Ornithine; Rats; Urea | 1991 |
Hyperornithinemia, hyperammonemia and homocitrullinuria--a case report and study of ornithine metabolism using in vivo deuterium labelling.
Topics: Adult; Ammonia; Arginine; Chromatography, Liquid; Citrulline; Deuterium; Humans; Male; Mass Spectrometry; Ornithine | 1991 |
Substrate and pH effects on glutamine synthesis in rat liver. Consequences for acid-base regulation.
Topics: Acid-Base Equilibrium; Ammonia; Ammonium Chloride; Animals; Glucose; Glutamine; Hydrogen-Ion Concentration; Lactates; Lactic Acid; Liver; Male; Nitrogen; Ornithine; Portal Vein; Pyruvates; Pyruvic Acid; Rats; Rats, Inbred Strains | 1991 |
Effect of prostaglandin E2 on urea synthesis and hepatic hemodynamics in rat livers. An in vivo/in vitro study.
Topics: Ammonia; Animals; Blood Pressure; Dinoprostone; In Vitro Techniques; Liver; Liver Circulation; Ornithine; Oxygen; Portal Vein; Rats; Rats, Inbred Strains; Urea | 1990 |
Episodic hyperammonemia in adult siblings with hyperornithinemia, hyperammonemia, and homocitrullinuria syndrome.
Topics: Adult; Ammonia; Citrulline; Female; Fibroblasts; Glutamine; Humans; Leucine; Male; Metabolism, Inborn Errors; Ornithine; Phenylbutyrates; Recurrence; Syndrome; Urea | 1990 |
The arginine dihydrolase pathway is present in Giardia intestinalis.
Topics: Ammonia; Animals; Arginine; Giardia; Hydrolases; Ornithine | 1990 |
Abnormal urinary excretion of polyamines in HHH syndrome (hyperornithinemia associated with hyperammonemia and homocitrullinuria).
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Biogenic Polyamines; Citrulline; Diet; Humans; Male; Ornithine; Syndrome | 1990 |
Hyperammonemia caused by impaired mitochondrial ornithine transport in a patient with partial quantitative deficiency of ornithine carbamoyltransferase.
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Humans; Liver; Male; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease | 1990 |
Comparison of ornithine metabolism in hyperornithinaemia-hyperammonaemia-homocitrullinuria syndrome, lysinuric protein intolerance and gyrate atrophy fibroblasts.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Fibroblasts; Heterozygote; Homozygote; Humans; Lysine; Ornithine; Ornithine-Oxo-Acid Transaminase; Oxidation-Reduction; Proteins; Syndrome | 1989 |
Changes in urea cycle-related metabolites in the mouse after combined administration of valproic acid and an amino acid load.
Topics: Amino Acids; Ammonia; Animals; Carbamoyl-Phosphate Synthase (Glutamine-Hydrolyzing); Citrulline; Glutamates; Glutamine; Liver; Mice; Ornithine; Urea; Valproic Acid | 1989 |
Ornithine aminotransferase activity, liver ornithine concentration and acute ammonia intoxication.
Topics: Acetates; Administration, Oral; Ammonia; Animals; Arginine; Creatinine; Eflornithine; Female; Injections, Intraperitoneal; Liver; Mice; Ornithine; Ornithine-Oxo-Acid Transaminase; Orotic Acid; Transaminases; Urea | 1989 |
Familial lysinuric protein intolerance presenting as coma in two adult siblings.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Coma; Family; Family Health; Humans; Male; Ornithine | 1989 |
Study of metabolism and growth limitation of human leukemia cell lines.
Topics: Amino Acids; Ammonia; Cell Count; Cell Division; Cell Line; Culture Media; Glucose; Glutamine; Humans; Keto Acids; Leukemia; Ornithine; Pyruvates; Tumor Cells, Cultured | 1989 |
Channeling of urea cycle intermediates in situ in permeabilized hepatocytes.
Topics: Ammonia; Animals; Aspartic Acid; Bicarbonates; Cell Membrane Permeability; Liver; Ornithine; Rats; Urea | 1989 |
Potential for the prenatal diagnosis of hyperornithinemia, hyperammonemia, and homocitrullinuria syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Chorionic Villi Sampling; Citrulline; Female; Humans; Ornithine; Pregnancy; Pregnancy Trimester, First; Prenatal Diagnosis | 1989 |
A new patient with hyperornithinaemia, hyperammonaemia and homocitrullinuria treated early with low protein diet.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Citrulline; Dietary Proteins; Glutamine; Humans; Infant; Male; Ornithine; Pyrimidines | 1986 |
A new family affected by the syndrome of hyperornithinaemia, hyperammonaemia and homocitrullinuria.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Citrulline; Female; Humans; Male; Ornithine; Syndrome | 1987 |
Hyperornithinemia-hyperammonemia-homocitrullinuria syndrome: low creatine excretion and effect of citrulline, arginine, or ornithine supplement.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Child, Preschool; Citrulline; Creatine; Female; Humans; Lysine; Male; Ornithine; Orotic Acid; Syndrome | 1987 |
Transient hyperammonaemia.
Topics: Ammonia; Child, Preschool; Dietary Proteins; Female; Humans; Lysine; Metabolic Clearance Rate; Ornithine; Seizures | 1987 |
Abnormality of citrulline synthesis in liver mitochondria from patients with hyperornithinaemia, hyperammonaemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Humans; Kinetics; Mitochondria, Liver; Ornithine | 1987 |
[Hyperornithinemia, hyperammonemia and homocitrullinuria due to a defect of mitochondrial membrane transport].
Topics: Amino Acids; Ammonia; Biological Transport; Cells, Cultured; Citrulline; Fibroblasts; Humans; Mitochondria, Liver; Ornithine; Skin | 1988 |
Biochemical analysis of decreased ornithine transport activity in the liver mitochondria from patients with hyperornithinemia, hyperammonemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Biological Transport; Citrulline; Humans; Kinetics; Mitochondria, Liver; Ornithine | 1988 |
[Anesthesia for a patient with the hyperornithinemia-hyperammonemia-homocitrullinuria (HHH) syndrome].
Topics: Adult; Ammonia; Anesthesia; Citrulline; Humans; Male; Ornithine; Syndrome | 1988 |
Clinical, biochemical and ultrastructural study on the pathogenesis of hyperornithinemia-hyperammonemia-homocitrullinuria syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Brain; Child; Citrulline; Endoplasmic Reticulum; Humans; Liver Glycogen; Male; Mitochondria, Liver; Ornithine; Tomography, X-Ray Computed | 1988 |
Possible pathogenetic mechanism in hyperornithinemia, hyperammonemia, and homocitrullinuria syndrome.
Topics: Ammonia; Citrulline; Growth Disorders; Humans; Intellectual Disability; Liver; Lymphocytes; Mitochondria; Ornithine; Syndrome | 1987 |
[Hyperornithinemia, hyperammonemia and homocitrullinuria syndrome in a family].
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Electroencephalography; Humans; Male; Mitochondria; Ornithine; Syndrome | 1987 |
The hyperornithinemia, hyperammonemia, homocitrullinuria syndrome: an ornithine transport defect remediable with ornithine supplements.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Citrulline; Dietary Proteins; Fibroblasts; Humans; In Vitro Techniques; Male; Mitochondria; Ornithine; Oxidation-Reduction; Syndrome | 1987 |
Hyperornithinemia, hyperammonemia, and homocitrullinuria: case report and biochemical study.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Citrulline; Fibroblasts; Humans; Liver; Male; Ornithine; Reference Values; Skin | 1987 |
Effect of improved hydrogen supply on energy state, ureogenesis and gluconeogenesis in isolated hepatocytes.
Topics: Adenosine Diphosphate; Adenosine Triphosphate; Ammonia; Animals; Caprylates; Carbonyl Cyanide p-Trifluoromethoxyphenylhydrazone; Energy Metabolism; Gluconeogenesis; Hydrogen; Lactates; Lactic Acid; Liver; Ornithine; Phenazines; Urea | 1986 |
Physiological and metabolic changes associated with weaning in the tammar wallaby, Macropus eugenii.
Topics: Ammonia; Animal Nutritional Physiological Phenomena; Animals; Blood Glucose; Female; Gluconeogenesis; Glycogen; Glycolysis; Hexokinase; Hydrogen-Ion Concentration; Liver; Macropodidae; Marsupialia; Organ Size; Ornithine; Phosphoenolpyruvate Carboxykinase (GTP); Pyruvate Kinase; Urea; Urine; Weaning | 1986 |
[H-H-H syndrome: a rare disease also relevant in anesthesiology].
Topics: Adolescent; Ammonia; Anesthesia, General; Citrulline; Femoral Fractures; Fracture Fixation, Internal; Humans; Male; Ornithine; Postoperative Complications; Syndrome; Wound Healing | 1986 |
Support of respiration and citrulline synthesis by isolated hepatic mitochondria from Squalus acanthias by acyl-CoAs and other nitrogen-donating substrates.
Topics: Acyl Coenzyme A; Amino Acids; Ammonia; Animals; Bicarbonates; Citrulline; Dogfish; Glutamine; Kinetics; Mitochondria, Liver; Ornithine; Oxygen Consumption; Sharks | 1986 |
Control of utilization of L-arginine, L-ornithine, agmatine, and putrescine as nitrogen sources in Escherichia coli K-12.
Topics: Agmatine; Ammonia; Arginine; Escherichia coli; Genes; Genes, Bacterial; Genotype; Glucose; Glutamine; Guanidines; Nitrogen; Ornithine; Phenotype; Putrescine; Species Specificity; Succinates | 1985 |
Influence of lysine on urea cycle activity and orotate formation in the isolated perfused rat liver.
Topics: Ammonia; Animals; In Vitro Techniques; Kinetics; Liver; Lysine; Male; Ornithine; Orotic Acid; Perfusion; Rats; Rats, Inbred Strains; Urea | 1985 |
Disruption of the blood-brain barrier in hyperammonemic coma and the pharmacologic effects of dexamethasone and difluoromethyl ornithine.
Topics: Acetates; Ammonia; Animals; Blood-Brain Barrier; Coma; Dexamethasone; Eflornithine; Exploratory Behavior; Female; Grooming; Hepatic Encephalopathy; Mice; Mice, Inbred Strains; Ornithine | 1985 |
Studies on a case of HHH-syndrome (hyperammonemia, hyperornithinemia, homocitrullinuria).
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Biological Transport; Child, Preschool; Citrulline; Fibroblasts; Follow-Up Studies; Humans; Kinetics; Male; Ornithine; Psychomotor Disorders; Seizures; Syndrome | 1986 |
Metabolic role of urea cycle intermediates: nutritional and clinical aspects. Introduction.
Topics: Ammonia; Animals; Arginine; Body Weight; Citrulline; Intestine, Small; Kidney; Liver; Nutritional Physiological Phenomena; Ornithine; Proline; Rats; Urea | 1985 |
Free amino acid pattern in blue mussel (Mytilus edulis) exposed to crude oil.
Topics: Amino Acids; Ammonia; Animals; Bivalvia; Finland; Gills; Ornithine; Petroleum; Proteins; Time Factors; Urea; Water Pollutants; Water Pollutants, Chemical | 1985 |
Ornithine loading did not prevent induced hyperammonemia in a patient with hyperornithinemia-hyperammonemia-homocitrullinuria syndrome.
Topics: Alanine; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Child; Citrulline; Cytoplasm; Humans; Male; Ornithine; Orotic Acid; Syndrome | 1985 |
Raised plasma-ornithine and gyrate atrophy of the choroid and retina.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Aqueous Humor; Atrophy; Child; Choroid; Electroretinography; Eye Diseases; Female; Fundus Oculi; Humans; Male; Middle Aged; Ornithine; Retina; Retinal Degeneration; Syndrome; Transaminases | 1973 |
Editorial: Encephalopathy and fatty degeneration of viscera.
Topics: Age Factors; Ammonia; Arginine; Brain Diseases; Chickenpox; Child; Fatty Liver; Humans; Influenza, Human; Ornithine; Orthomyxoviridae; Reye Syndrome; Transaminases; Urea | 1974 |
Reye's syndrome due to a novel protein-tolerant variant of ornithine-transcarbamylase deficiency.
Topics: Ammonia; Brain Diseases; Child; Fatty Liver; Female; Hepatic Encephalopathy; Humans; Kinetics; Liver; Metabolism, Inborn Errors; Ornithine; Ornithine Carbamoyltransferase; Prothrombin Time; Reye Syndrome; Urea | 1974 |
Biochemical aspects of metamorphosis: a study of the isolation of intact frog-liver mitochondria.
Topics: Adenosine Triphosphatases; Ammonia; Animals; Anura; Cell Differentiation; Citrulline; Glutamates; Liver; Metamorphosis, Biological; Mitochondria, Liver; Ornithine; Oxygen Consumption | 1971 |
Effect of ultraviolet radiations on ornithine.
Topics: Alanine; Aminobutyrates; Ammonia; Bicarbonates; Chemical Phenomena; Chemistry; Chromatography; Indenes; Indicators and Reagents; Ketones; Ornithine; Proline; Radiation Effects; Spectrophotometry; Time Factors; Ultraviolet Rays | 1970 |
The structure of the cell wall peptidoglycan of Bifidobacterium bifidum var. pennsylvanicus.
Topics: Alanine; Amino Acids; Ammonia; Asparagine; Cell Wall; Chromatography, Gel; Chromatography, Paper; Cycloserine; Dinitrophenols; Electrophoresis; Fluorine; Glucosamine; Glutamine; Glycosaminoglycans; Hydrazines; Hydrolysis; Lactobacillus; Models, Structural; Muramidase; Nucleoside Diphosphate Sugars; Ornithine; Paper; Peptides; Polysaccharides, Bacterial; Serine; Species Specificity; Stereoisomerism; Uracil Nucleotides | 1971 |
[Current views on the therapy of hepatic coma].
Topics: Acute Kidney Injury; Adolescent; Amino Acids; Ammonia; Anti-Bacterial Agents; Arginine; Aspartic Acid; Coenzyme A; Diet Therapy; Exchange Transfusion, Whole Blood; Glutamates; Hepatic Encephalopathy; Humans; Malates; Male; NAD; Ornithine; Prednisone; Prognosis; Renal Dialysis; Thiamine Pyrophosphate; Thioctic Acid; Vasopressins | 1970 |
Self-association and allosteric properties of glutamine-dependent carbamyl phosphate synthetase. Reversible dissociation to monomeric species.
Topics: Allosteric Regulation; Ammonia; Barbiturates; Carbamates; Carbon Radioisotopes; Enzyme Activation; Escherichia coli; Glutamine; Guanidines; Kinetics; Macromolecular Substances; Ornithine; Osmolar Concentration; Phosphates; Phosphotransferases; Potassium; Potassium Chloride; Protein Conformation; Ultracentrifugation; Urea | 1974 |
Reversible dissociation of the monomer of glutamine-dependent carbamyl phosphate synthetase into catalytically active heavy and light subunits.
Topics: Adenosine Triphosphatases; Allosteric Regulation; Amino Acids; Ammonia; Binding Sites; Carbamates; Carbon Radioisotopes; Catalysis; Chromatography, Gel; Enzyme Activation; Escherichia coli; Glutaminase; Glutamine; Macromolecular Substances; Nucleotides; Ornithine; Phosphotransferases; Potassium; Thiocyanates; Ultracentrifugation | 1974 |
Detoxication of ammonia in sheep fed soy protein or urea.
Topics: Ammonia; Animals; Arginase; Arginine; Biotransformation; Carbamates; Depression, Chemical; Dietary Proteins; Feces; Glutamate Dehydrogenase; Glycine max; Ligases; Liver; Lyases; NAD; NADP; Nitrogen; Ornithine; Ornithine Carbamoyltransferase; Phosphotransferases; Plant Proteins; Sheep; Statistics as Topic; Succinates; Urea | 1970 |
Some properties of urea dehydrogenase in tissues of higher plants.
Topics: Adenine Nucleotides; Ammonia; Aspartic Acid; Carbon Isotopes; Chromatography; Chromatography, Paper; Flavin Mononucleotide; Flavin-Adenine Dinucleotide; Flavins; Hot Temperature; Hydrogen-Ion Concentration; Indicators and Reagents; NADP; Ornithine; Oxidoreductases; Phosphates; Plants; Quaternary Ammonium Compounds; Succinates; Sulfates; Urea | 1966 |
Utilization of amino acids as nitrogen sources, and their effects on nitrate reductase in the marine diatom Cyclotella cryptica.
Topics: Alanine; Amino Acids; Ammonia; Arginine; Asparagine; Cell-Free System; Chlorophyll; Eukaryota; Glutamates; Glutamine; Glycine; Isoleucine; Nitrate Reductases; Nitrates; Ornithine; Plant Proteins; Proline; Seawater; Urea; Water Microbiology | 1974 |
Argininosuccinicaciduria: clinical, metabolic and dietary study.
Topics: Affective Symptoms; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginase; Arginine; Ataxia; Child; Citrulline; Dietary Proteins; Electroencephalography; Epilepsy; Female; Humans; Intellectual Disability; Intelligence Tests; Male; Ornithine; Phenobarbital; Seizures; Succinates; Tremor | 1974 |
[Amino acid levels in the blood serum of patients with chronic colitis].
Topics: Adult; Alanine; Amino Acids; Ammonia; Arginine; Aspartic Acid; Betaine; Chronic Disease; Citrulline; Colitis; Glutamates; Glutamine; Glycine; Histidine; Humans; Middle Aged; Ornithine; Phenylalanine; Proline; Serine; Taurine; Threonine; Tryptophan; Tyrosine; Urea | 1974 |
A concerted response of the enzymes of urea biosynthesis during thyroxine-induced metamorphosis of Rana catesbeiana.
Topics: Adenosine Triphosphate; Ammonia; Animals; Anura; Arginase; Arginine; Aspartic Acid; Carbon Dioxide; Citrulline; Larva; Ligases; Liver; Lyases; Metamorphosis, Biological; Mitochondria, Liver; Organ Size; Ornithine; Ornithine Carbamoyltransferase; Phosphotransferases; Rana catesbeiana; Subcellular Fractions; Succinates; Thyroxine; Urea | 1972 |
[Experimental study of synergism and antagonism between the amino acids of the Krebs-Henseleit cycle].
Topics: Amino Acids; Ammonia; Animals; Arginine; Citric Acid Cycle; Citrulline; Drug Antagonism; Drug Interactions; Drug Synergism; Female; Male; Mice; Ornithine; Poisoning | 1972 |
[Mechanism of intrahepatic accumulation of dicarboxylic amino acids during ammonia poisoning].
Topics: Alanine; Amino Acids; Ammonia; Animals; Arginine; Aspartic Acid; Citrates; Citrulline; Dicarboxylic Acids; Glutamates; Glutaminase; Glutamine; Liver; Malates; Ornithine; Pyruvates; Rats; Seizures; Urea | 1972 |
[Correction by L-dopa of neurologic manifestations of a chronic portocaval encephalopathy].
Topics: Alcoholism; Ammonia; Brain Diseases; Dihydroxyphenylalanine; Electroencephalography; Humans; Ketoglutaric Acids; Lactulose; Liver Cirrhosis; Male; Middle Aged; Neurologic Manifestations; Ornithine; Prednisone; Silicosis; Tremor | 1972 |
Uraemic waste recovery. II. In vitro studies.
Topics: Allantoin; Ammonia; Arginine; Creatine; Culture Media; Fermentation; Glutamates; Guanidines; Humans; Nitrogen; Ornithine; Soil Microbiology; Temperature; Urea; Uremia; Uric Acid; Xanthines | 1972 |
[Study on di-L(+)-ornithine-alpha-ketoglutaric acid in the model of isolated perfused rat liver].
Topics: Ammonia; Animals; Chemical and Drug Induced Liver Injury; Female; Galactosamine; Glucose; Ketoglutaric Acids; Liver; Membranes; Models, Biological; Ornithine; Perfusion; Potassium; Rats; Urea | 1972 |
Transport of ornithine and citrulline across the mitochondrial membrane.
Topics: Ammonia; Animals; Biological Transport, Active; Carbamates; Carbon Isotopes; Citrulline; Electron Transport; In Vitro Techniques; Membrane Potentials; Mitochondria; Mitochondria, Liver; Mitochondria, Muscle; Mitochondrial Swelling; Myocardium; Oligomycins; Organ Specificity; Ornithine; Ornithine Carbamoyltransferase; Osmosis; Oxygen Consumption; Phosphotransferases; Rats; Uncoupling Agents; Valinomycin | 1973 |
Psychomotor retardation, epileptic and stuporous attacks, irritability and ataxia associated with ammonia intoxication, high blood ornithine levels and increased homocitruline in the urine.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Ataxia; Citrulline; Epilepsy; Female; Humans; Ornithine; Paralysis; Psychomotor Disorders | 1973 |
Free amino acids of plasma in the acute phase of experimental necrotic liver damage.
Topics: Amino Acids; Ammonia; Animals; Arginase; Arginine; Carbon Tetrachloride Poisoning; Liver Diseases; Male; Necrosis; Ornithine; Rats; Time Factors; Urea | 1973 |
Accumulation of amino acids by the perfused rat liver in the presence of ethanol.
Topics: Alanine; Amino Acids; Ammonia; Animals; Aspartic Acid; Ethanol; Gluconeogenesis; Glucose; In Vitro Techniques; Lactates; Liver; Oleic Acids; Ornithine; Oxygen Consumption; Pyruvates; Rats; Urea | 1973 |
Ornithinemia, hyperammonemia, and homocitrullinuria. A disease associated with mental retardation and possibly caused by defective mitochondrial transport.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Dietary Proteins; Female; Humans; Intellectual Disability; Lysine; Mitochondria; Ornithine; Ornithine Carbamoyltransferase; Proline; Transaminases | 1974 |
[Therapy of experimental and clinical hyperammonaemia with ornithine-alpha-ketoglutarate].
Topics: Amino Acids, Dicarboxylic; Ammonia; Animals; Drug Evaluation; Female; Hepatic Encephalopathy; Humans; Injections, Intravenous; Ketoglutaric Acids; Male; Middle Aged; Ornithine; Poisoning; Rats | 1974 |
Nitrogen metabolism in channel catfish, Ictalurus punctatus. 3. Relative pool sizes of free amino acids and related compounds in various tissues of the catfish.
Topics: Alanine; Amino Acids; Aminobutyrates; Aminoisobutyric Acids; Ammonia; Analysis of Variance; Animals; Autoanalysis; Brain; Fishes; Gills; Glutamine; Hydroxyproline; Intestinal Mucosa; Kidney; Liver; Myocardium; Organ Specificity; Ornithine; Spleen; Taurine; Urea | 1974 |
Heterogenous mutations of the structural gene of human ornithine carbamyltransferase as observed in five personal cases.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Carbamates; Female; Genes; Humans; Hydrogen-Ion Concentration; Intestines; Kinetics; Liver; Male; Mutation; Ornithine; Ornithine Carbamoyltransferase; Sex Chromosomes | 1974 |
Hyperammonaemia in 20 families. Biochemical and genetical survey, including investigations in 3 new families.
Topics: Alanine; Ammonia; Arginine; Child, Preschool; Citrulline; Female; Genes, Dominant; Genetic Linkage; Glutamates; Glutamine; Glycine; Humans; Leucine; Liver; Lysine; Male; Metabolism, Inborn Errors; Ornithine; Ornithine Carbamoyltransferase; Sex Chromosomes | 1974 |
A system for the study of urea synthesis in liver homogenates.
Topics: Adenine Nucleotides; Amino Acids; Ammonia; Animals; Aspartic Acid; Cell-Free System; Edetic Acid; In Vitro Techniques; Keto Acids; Liver; Magnesium; Male; Nitrogen; Ornithine; Plasma; Rats; Time Factors; Urea | 1969 |
Initial steps in pyrimidine synthesis in Ehrlich ascites carcinoma in vitro. II. The synthesis of carbamyl phosphate by a soluble, glutamine-dependent carbamyl phosphate synthetase.
Topics: Adenosine Triphosphate; Ammonia; Ammonium Chloride; Animals; Bicarbonates; Carbon Isotopes; Carcinoma, Ehrlich Tumor; Citrulline; Enterococcus faecalis; Glutamine; In Vitro Techniques; Magnesium; Ornithine; Ornithine Carbamoyltransferase; Phosphotransferases; Pyrimidines; Streptococcus; Time Factors | 1967 |
Nitrogen metabolism of the South American lungfish Lepidosiren paradoxa.
Topics: Acetates; Ammonia; Animals; Arginine; Aspartic Acid; Bicarbonates; Carbon Isotopes; Citrulline; Climate; Fasting; Fishes; Glutamates; Guanidines; Leucine; Liver; Manganese; Ornithine; Serine; Stereoisomerism; Urea | 1972 |
Hyperammonemia due to a defect in hepatic ornithine transcarbamylase.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Central Nervous System Diseases; Child; Child Behavior Disorders; Citrates; Coma; Diet Therapy; Dietary Proteins; Female; Gastrointestinal Diseases; Guanidines; Humans; Liver; Male; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Succinates; Urea | 1972 |
Net metabolism of plasma amino acids by liver and portal-drained viscera of fed sheep.
Topics: Alanine; Amino Acids; Ammonia; Animal Feed; Animals; Arginine; Aspartic Acid; Blood Flow Velocity; Dietary Proteins; Digestive System; Glutamates; Glutamine; Glycine; Isoleucine; Leucine; Liver; Liver Circulation; Nitrogen; Ornithine; Phenylalanine; Serine; Sheep; Tyrosine; Valine | 1972 |
Effect of ornithine alpha ketoglutarate on disturbances of brain metabolism caused by high blood ammonia.
Topics: Ammonia; Animals; Brain; Carbon Dioxide; Cerebrovascular Circulation; Dogs; Glucose; Hydrogen-Ion Concentration; Ketoglutaric Acids; Ornithine; Oxygen Consumption | 1972 |
[Therapy of severe hyperammonemia].
Topics: Adult; Aged; Ammonia; Anti-Bacterial Agents; Aspartic Acid; Diet Therapy; Enzyme Induction; Female; Hepatic Encephalopathy; Humans; Male; Middle Aged; Ornithine | 1972 |
Serum aminotransferase activities and plasma free amino acid concentration as criteria for pyridoxine nutritional status of chicks.
Topics: Alanine Transaminase; Amino Acids; Aminobutyrates; Ammonia; Animal Nutritional Physiological Phenomena; Animals; Asparagine; Aspartate Aminotransferases; Body Weight; Chickens; Cysteine; Diet; Feeding Behavior; Glutamine; Glycine; Male; Ornithine; Pyridoxal Phosphate; Pyridoxine; Serine; Taurine; Vitamin B 6 Deficiency | 1972 |
The congenital hyperammonemic syndrome.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Diet Therapy; Dietary Proteins; Female; Humans; Infant; Keto Acids; Ornithine; Ornithine Carbamoyltransferase; Phosphotransferases; Urea; Uric Acid | 1971 |
Hyperammonemia due to a mutant enzyme of ornithine transcarbamylase.
Topics: Amino Acids; Ammonia; Animals; Autopsy; Clinical Enzyme Tests; Culture Techniques; Female; Humans; Infant; Liver; Metabolism, Inborn Errors; Mutation; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Phosphotransferases; Rats; Threonine; Urea | 1971 |
The presence of high ornithine-urea cycle enzyme activity in the teleost Opsanus tau.
Topics: Acetates; Adenosine Triphosphate; Ammonia; Animals; Arginase; Arginine; Bicarbonates; Blood Urea Nitrogen; Carbamates; Enzyme Activation; Fishes; Glutamates; Ligases; Liver; Lyases; Magnesium; Manganese; Ornithine; Ornithine Carbamoyltransferase; Phosphoric Acids; Phosphotransferases; Quaternary Ammonium Compounds; Succinates; Sulfuric Acids; Urea | 1971 |
The effect of vitamin C depletion on the free amino acid content in blood plasma of the guinea pig.
Topics: Alanine; Amino Acids; Ammonia; Animals; Arginine; Ascorbic Acid Deficiency; Aspartic Acid; Citrulline; Cysteine; Glutamates; Glycine; Guinea Pigs; Histidine; Isoleucine; Lysine; Male; Methionine; Ornithine; Phenylalanine; Proline; Serine; Threonine; Time Factors; Tyrosine; Valine | 1971 |
Ornithine-urea cycle activity in xenopus laevis: adaptation in saline.
Topics: Adaptation, Physiological; Ammonia; Animals; Carbamoyl-Phosphate Synthase (Ammonia); Liver; Male; Ornithine; Sodium Chloride; Urea; Xenopus laevis | 1967 |
Effect of urea concentration on its utilization, on the pH and the formation of ammonia and carbon dioxide in a human salivary sediment system.
Topics: Amino Acids; Ammonia; Autoradiography; Carbohydrate Metabolism; Carbon; Carbon Dioxide; Carbon Isotopes; Chromatography, Paper; Humans; Hydrogen-Ion Concentration; Lactates; Nitrogen; Ornithine; Saliva; Succinates; Urea; Urease | 1971 |
[Urea-and ammonia content of the liver following irradiation in vivo].
Topics: Ammonia; Animals; Liver; Male; Ornithine; Radiation Effects; Rats; Urea | 1966 |
[Effects of the arginine-ornithine combination on the arterial ammonia levels in chronic liver diseases and hepatic coma].
Topics: Ammonia; Arginine; Chronic Disease; Hepatic Encephalopathy; Humans; Methods; Ornithine; Uremia | 1968 |
Metabolism of bovine semen. XX. Role of ammonia in interactions between the citric acid and urea cycles.
Topics: Amino Acids; Ammonia; Animals; Arginase; Arginine; Carbamates; Carbon Dioxide; Carbon Isotopes; Cattle; Cell Fractionation; Citric Acid Cycle; Citrulline; Male; Ornithine; Ornithine Carbamoyltransferase; Oxygen Consumption; Phosphotransferases; Proline; Pyruvates; Rabbits; Semen; Spermatozoa; Urea; Valerates | 1969 |
Ornithine-ketoacid transaminase activity in human skin and amniotic fluid cell culture.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Amniotic Fluid; Biopsy; Cell Line; Citrulline; Culture Techniques; Humans; Keto Acids; Ornithine; Skin; Transaminases | 1970 |
[The use of a detoxicant drug in the treatment of alcoholic toxicosis].
Topics: Adult; Alcoholic Intoxication; Alcoholism; Ammonia; Arginine; Citrulline; Female; Humans; Liver Function Tests; Male; Middle Aged; Nitrogen; Ornithine; Psychoses, Alcoholic; Transaminases | 1970 |
Rate of urea synthesis in normal and cirrhotic rat liver with reference to the arginine synthetase system.
Topics: Ammonia; Ammonium Chloride; Animals; Arginine; Blood Proteins; Blood Urea Nitrogen; Diet; Hydroxyproline; In Vitro Techniques; Ligases; Liver; Liver Cirrhosis, Experimental; Male; Ornithine; Rats; Urea | 1970 |
Ornithine loading test in Lowe's syndrome.
Topics: Abnormalities, Multiple; Amino Acids; Ammonia; Chromosome Aberrations; Chromosome Disorders; Eye Diseases; Growth Disorders; Humans; Intellectual Disability; Kidney Diseases; Ornithine | 1970 |
[Modification of experimentally induced endogenous hyperammoniemia by amino acids in the rat].
Topics: Amino Acids; Ammonia; Anesthesia, General; Animals; Arginine; Aspartic Acid; Citric Acid Cycle; Depression, Chemical; Disease Models, Animal; Ethyl Ethers; Male; Ornithine; Rats | 1970 |
Protection by ornithine-aspartate of the effects of physical exercise.
Topics: Adenine Nucleotides; Adenosine Triphosphate; Alanine Transaminase; Ammonia; Animals; Aspartate Aminotransferases; Aspartic Acid; Creatine; Depression, Chemical; Fatigue; Male; Ornithine; Physical Exertion; Rats; Stimulation, Chemical; Swimming | 1970 |
[Action of ornighine alpha-ketoglutarate on hyperammoniemia in the cirrhotic patient].
Topics: Ammonia; Humans; Injections, Intravenous; Ketoglutaric Acids; Liver Cirrhosis; Ornithine | 1971 |
The 'neurotoxicity' of L-2,4-diaminobutyric acid.
Topics: Aminobutyrates; Ammonia; Animals; Arginine; Aspartic Acid; Blood Glucose; Brain Chemistry; Chickens; Chromatography, Ion Exchange; Glutamates; Glutamine; In Vitro Techniques; Leucine; Liver; Lysine; Male; Ornithine; Ornithine Carbamoyltransferase; Potassium; Quaternary Ammonium Compounds; Rats; Sodium; Spectrophotometry; Time Factors; Urea; Urine | 1968 |
Excretion of delta-aminolevulinic acid in the absence of demonstrable erythropoiesis.
Topics: Adolescent; Amino Acids; Aminobutyrates; Ammonia; Anemia, Aplastic; Autoanalysis; Chemistry, Clinical; Child; Child, Preschool; Chromatography, Ion Exchange; Erythropoiesis; Heme; Histidine; Humans; Lead Poisoning; Levulinic Acids; Lysine; Middle Aged; Ornithine; Phenylalanine; Tyrosine | 1968 |
Metabolic buffers in hepatic failure.
Topics: Adenosine Triphosphate; Amino Acids; Ammonia; Animals; Blood Glucose; Blood Urea Nitrogen; Diet Therapy; Dogs; Glucose; Hepatic Encephalopathy; Keto Acids; Lactates; Liver Cirrhosis; Liver Diseases; Ornithine; Ornithine Carbamoyltransferase; Portacaval Shunt, Surgical | 1968 |
[On deamination of amino acids by plague microorganism].
Topics: Amino Acids; Ammonia; Aspartic Acid; Cell-Free System; Depression, Chemical; Genetics, Microbial; Guanidines; Histidine; Hydroxylamines; Isoniazid; Keto Acids; Ornithine; Species Specificity; Vaccines; Yersinia pestis | 1968 |
Effect of thyroid hormones on some enzymes of nitrogen metabolism.
Topics: Ammonia; Animals; Antithyroid Agents; Aspartic Acid; Dactinomycin; Depression, Chemical; Diet; Ethionine; Glutaminase; Glutamine; Hyperthyroidism; Hypothyroidism; Kidney; Ligases; Liver; Male; Ornithine; Phosphotransferases; Propylthiouracil; Puromycin; Rats; Stimulation, Chemical; Thyroid Hormones; Transaminases; Transferases; Urea | 1968 |
Metabolism of ammonia. I. Biochemical aspect of ammonia intoxication.
Topics: Ammonia; Animals; Arginine; Ascorbic Acid; Autoradiography; Bicarbonates; Blood-Brain Barrier; Carbon Isotopes; Chickens; Citrulline; Hydrogen-Ion Concentration; Injections, Intraperitoneal; Male; Mice; Ornithine; Phosphates; Poisoning; Rats; Sulfates; Time Factors | 1968 |
[Metabolites of urea synthesis following localized liver irradiation].
Topics: Ammonia; Animals; Arginine; Liver; Male; Methods; Ornithine; Radiation Effects; Rats; Urea | 1968 |
[Intravenous administration of ornithine aspartate to patients with hepatic diseases].
Topics: Ammonia; Aspartic Acid; Humans; Injections, Intravenous; Liver Diseases; Liver Function Tests; Ornithine | 1968 |
A study of ammonia and urea production and excretion in the fresh-water-adapted form of the Pacific lempry, Entosphenus tridentatus.
Topics: Ammonia; Animals; Arginase; Biological Evolution; Carbamates; Citrulline; Fishes; Gills; Hydrogen-Ion Concentration; Kidney; Kinetics; Liver; Manganese; Ornithine; Phosphotransferases; Seawater; Urea | 1968 |
[Therapy of hyperammoniemia].
Topics: Adenosine Triphosphate; Ammonia; Anti-Bacterial Agents; Arginine; Aspartic Acid; Citrulline; Dietary Proteins; Hepatic Encephalopathy; Humans; Intestines; Malates; Ornithine | 1969 |
Hyperornithinemia, hyperammonemia, and homocitrullinuria. A new disorder of amino acid metabolism associated with myoclonic seizures and mental retardation.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Ataxia; Child, Preschool; Citrulline; Diet Therapy; Humans; Intellectual Disability; Lysine; Male; Myoclonus; Ornithine; Ornithine Carbamoyltransferase; Seizures | 1969 |
Ornithinaemia. Another disorder of aminoacid metabolism associated with brain damage.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Brain Diseases; Child; Child, Preschool; Female; Humans; Male; Ornithine; Transaminases | 1969 |
[Metabolism of ammonia. 3. Effect in vitro of arginine on the physiological activity of the urea cycle enzymes during ammonia poisoning].
Topics: Ammonia; Animals; Arginase; Arginine; Citrulline; Epinephrine; Hormones; In Vitro Techniques; Ligases; Liver; Norepinephrine; Ornithine; Rats; Transferases; Urea | 1969 |
The redistribution of nitrogen in silage by lactic-acid-producing bacteria.
Topics: Amino Acids; Ammonia; Arginine; Food Microbiology; Hydrogen-Ion Concentration; Lactobacillus; Nitrogen; Ornithine; Pediococcus; Plants; Serine; Silage | 1966 |
Amino acids mixtures in prevention of acute ammonia intoxication in dogs.
Topics: Ammonia; Animals; Aspartic Acid; Blood Urea Nitrogen; Dogs; Hepatic Encephalopathy; Ornithine; Portal Vein | 1967 |
Effect of ornithine-aspartate mixture on 15N-ammonia incorporation into urea in intact mice.
Topics: Ammonia; Animals; Aspartic Acid; Injections, Intraperitoneal; Male; Mice; Nitrogen; Ornithine; Radioisotopes; Urea | 1967 |
The recovery of amino acids from acid hydrolysates of whole urine from patients with thermal burns.
Topics: Alanine; Amino Acids; Ammonia; Arginine; Aspartic Acid; Burns; Creatine; Glutamates; Glycine; Histidine; Humans; Hydroxyproline; Isoleucine; Leucine; Lysine; Ornithine; Phenylalanine; Proline; Serine; Taurine; Threonine; Tyrosine; Urea; Valine | 1967 |
[Critical study of venous blood ammonia in hepatic coma. Diagnosis, surveillance and treatment].
Topics: Adult; Aged; Ammonia; Female; Hepatic Encephalopathy; Humans; Male; Middle Aged; Ornithine | 1967 |
Reduced ornithine catabolism in cultured fibroblasts and phytohaemagglutinin-stimulated lymphocytes from a patient with hyperornithinaemia, hyperammonaemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Aspartate Ammonia-Lyase; Cells, Cultured; Citrulline; Fibroblasts; Glutamates; Glutamic Acid; Humans; Lymphocyte Activation; Lymphocytes; Ornithine; Phytohemagglutinins; Proline | 1982 |
Regulation of the n-acetylglutamate content of rat hepatocytes by the glutamate concentration.
Topics: Ammonia; Animals; Aspartic Acid; Citrulline; Diet; Glutamates; Glutamic Acid; Liver; Ornithine; Rats; Urea | 1982 |
The influence of anticonvulsants on fasting plasma ammonia and amino acid levels.
Topics: Amino Acids; Ammonia; Anticonvulsants; Carbamazepine; Child; Child, Preschool; Glutamine; Glycine; Humans; Infant; Ornithine; Phenobarbital; Valproic Acid | 1983 |
The mechanism of hyperammonaemia and hyperornithinaemia in the syndrome of hyperornithinaemia, hyperammonaemia with homocitrullinuria.
Topics: Ammonia; Citrulline; Fibroblasts; Humans; Liver; Male; Middle Aged; Mitochondria, Liver; Ornithine; Syndrome | 1983 |
Studies on the pathway from ornithine to proline in cultured skin fibroblasts with reference to the defect in hyperornithinaemia with hyperammonaemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Biological Transport; Cells, Cultured; Citrulline; Fibroblasts; Glutamine; Humans; Mitochondria; Ornithine; Proline; Proteins | 1983 |
Hyperammonemia in lysinuric protein intolerance.
Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Child; Cystinuria; Humans; Lysine; Male; Ornithine | 1984 |
The pH of mitochondria of fibroblasts from a hyperornithinaemia, hyperammonaemia, homocitrullinuria-syndrome patient.
Topics: Acid-Base Equilibrium; Ammonia; Citrulline; Cytosol; Fibroblasts; Humans; Hydrogen-Ion Concentration; Mitochondria; Ornithine; Syndrome | 1984 |
Ultrastructural changes in fibroblast mitochondria of a patient with HHH-syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Fibroblasts; Genes, Recessive; Humans; Intracellular Membranes; Microscopy, Electron; Mitochondria; Ornithine; Skin | 1984 |
Mechanism of arginine protection against ammonia intoxication in the rat.
Topics: Acetyltransferases; Amino-Acid N-Acetyltransferase; Ammonia; Animals; Arginine; Carbamoyl-Phosphate Synthase (Ammonia); Citrulline; Male; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase; Orotic Acid; Rats; Rats, Inbred Strains; Urea | 1984 |
Arginine, an indispensable amino acid for patients with inborn errors of urea synthesis.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Argininosuccinate Synthase; Argininosuccinic Aciduria; Blood Urea Nitrogen; Carbamoyl-Phosphate Synthase (Ammonia); Child, Preschool; Female; Glutamine; Humans; Infant; Infant, Newborn; Male; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Urea | 1984 |
Gamma-glutamylornithine excretion in patients with hyperornithinemia.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Atrophy; Choroid; Chromatography; Citrulline; Dipeptides; Humans; Ornithine; Retina; Retinal Diseases; Syndrome; Uveal Diseases | 1984 |
[Diagnosis and treatment of hyperazotemia in liver cirrhosis].
Topics: Ammonia; Drug Therapy, Combination; Female; Humans; Lactulose; Liver Cirrhosis; Liver Function Tests; Male; Middle Aged; Ornithine; Uremia | 1983 |
Urea cycle function in the dog with emphasis on the role of arginine.
Topics: Age Factors; Ammonia; Animals; Arginine; Blood Glucose; Citrulline; Dogs; Ornithine; Orotic Acid; Urea; Vomiting | 1984 |
Reconstitution of ornithine transport in liposomes with Lubrol extracts of mitochondria.
Topics: Amino Acid Transport Systems, Basic; Ammonia; Animals; Biological Transport, Active; Carrier Proteins; Cattle; Citrulline; Kinetics; Liposomes; Membrane Transport Proteins; Mitochondria, Liver; Ornithine; Polyethylene Glycols; Solubility; Syndrome | 1984 |
Arginine-responsive asymptomatic hyperammonemia in the premature infant.
Topics: Ammonia; Arginine; Female; Humans; Infant, Newborn; Infant, Premature, Diseases; Male; Ornithine | 1984 |
Analysis of the control of citrulline synthesis in isolated rat-liver mitochondria.
Topics: Acetazolamide; Ammonia; Animals; Bicarbonates; Carbamoyl-Phosphate Synthase (Ammonia); Carbamyl Phosphate; Citrulline; Male; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase; Rats; Rats, Inbred Strains; Valine | 1984 |
[Parenteral feeding of patients with liver cirrhosis with hepatic encephalopathy].
Topics: Amino Acids; Ammonia; Arginine; Hepatic Encephalopathy; Humans; Liver Cirrhosis; Ornithine; Parenteral Nutrition | 1980 |
Defective ornithine metabolism in the syndrome of hyperornithinaemia, hyperammonaemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Fibroblasts; Humans; Ornithine; Pyrroline Carboxylate Reductases | 1981 |
[Lysinuric protein intolerance: a severe hyperammonemia secondary to l-arginine deficiency (author's transl)]].
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Female; Humans; Infant; Lysine; Male; Ornithine; Time Factors | 1981 |
Arginine metabolism and urea synthesis in cultured rat skeletal muscle cells.
Topics: Ammonia; Animals; Arginase; Arginine; Cells, Cultured; Chromatography, Thin Layer; Creatine; Muscles; Ornithine; Rats; Serine; Urea | 1982 |
Regulation of proline catabolism in Pseudomonas aeruginosa PAO.
Topics: 1-Pyrroline-5-Carboxylate Dehydrogenase; Ammonia; Citrates; Enzyme Induction; Enzyme Repression; Mutation; Ornithine; Oxidoreductases Acting on CH-NH Group Donors; Proline; Proline Oxidase; Pseudomonas aeruginosa | 1982 |
Renal transport of lysine and arginine in lysinuric protein intolerance.
Topics: Adolescent; Ammonia; Arginine; Biological Transport; Humans; Kidney Tubules; Lysine; Male; Ornithine; Renal Aminoacidurias | 1982 |
A lethal neonatal variant of carbamoyl-phosphate synthetase deficiency in combination with an intermediate activity of L-ornithine: 2-oxoglutarate amino-transferase.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Carbamoyl-Phosphate Synthase (Ammonia); Female; Humans; Infant, Newborn; Ligases; Liver; Ornithine; Ornithine-Oxo-Acid Transaminase; Proline; Transaminases | 1983 |
Interaction between the urea cycle and the orotate pathway: studies with isolated hepatocytes.
Topics: Ammonia; Animals; Carbamoyl-Phosphate Synthase (Ammonia); Catalysis; In Vitro Techniques; Ligases; Liver; Male; Ornithine; Orotic Acid; Pyrimidines; Rats; Rats, Inbred Strains; Urea | 1983 |
Renal ammoniagenesis in an early stage of metabolic acidosis in man.
Topics: Acidosis; Adult; Amino Acids; Ammonia; Bicarbonates; Diuresis; Glutamine; Glycine; Humans; Kidney; Middle Aged; Ornithine; Time Factors | 1982 |
Defective ornithine metabolism in cultured skin fibroblasts from patients with the syndrome of hyperornithinemia, hyperammonemia and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Cells, Cultured; Citrulline; Fibroblasts; Humans; Models, Chemical; Ornithine; Proteins; Skin | 1982 |
Argininemia: report of a new case and mechanisms of orotic aciduria and hyperammonemia.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Child, Preschool; Female; Humans; Hyperargininemia; Ornithine; Orotic Acid; Purine-Pyrimidine Metabolism, Inborn Errors; Urea | 1982 |
alpha-Ketoglutarate induced transamination during ischemic exercise.
Topics: Adult; Amination; Ammonia; Citric Acid Cycle; Energy Metabolism; Humans; Ischemia; Ketoglutaric Acids; Lactates; Lactic Acid; Ornithine; Physical Exertion; Pyruvates; Pyruvic Acid | 1982 |
Urea cycle regulation: I. Coupling of ornithine metabolism to mitochondrial oxidative phosphorylation.
Topics: Adenosine Triphosphate; Ammonia; Animals; Citric Acid Cycle; Citrulline; Glutamate Dehydrogenase; Ketoglutaric Acids; Mitochondria, Liver; Ornithine; Ornithine-Oxo-Acid Transaminase; Oxidative Phosphorylation; Rats; Reye Syndrome; Urea | 1980 |
Plasma alpha-ketoglutarate in urea cycle enzymopathies and its role as a harbinger of hyperammonemic coma.
Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Argininosuccinate Synthase; Argininosuccinic Acid; Argininosuccinic Aciduria; Carbamoyl-Phosphate Synthase (Ammonia); Carbamyl Phosphate; Child; Child, Preschool; Coma; Female; Hepatic Encephalopathy; Humans; Infant; Infant, Newborn; Ketoglutaric Acids; Ligases; Lyases; Male; Middle Aged; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease | 1980 |
Ornithine transcarbamylase (OTC) in white blood cells.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Carbamyl Phosphate; Carbon Radioisotopes; Cattle; Cells, Cultured; Humans; Infant; Leukocytes; Liver; Ornithine; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Radioligand Assay | 1980 |
Ultrastructural changes in the mitochondria in disorders in ornithine metabolism.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Citrulline; Humans; Mitochondria, Liver; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease | 1980 |
Ultrastructure of hepatic mitochondria in a child with hyperornithinemia, hyperammonemia, and homocitrullinuria.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Child; Citrulline; Humans; Male; Microscopy, Electron; Mitochondria, Liver; Ornithine | 1981 |
The treatment of inborn errors of the urea cycle.
Topics: Ammonia; Arginine; Humans; Metabolism, Inborn Errors; Ornithine; Urea | 1981 |
Effects of arginine-free meals on ureagenesis in cats.
Topics: Acetyltransferases; Amino-Acid N-Acetyltransferase; Ammonia; Animals; Arginine; Cats; Citrulline; Food, Formulated; Kinetics; Liver; Mitochondria, Liver; Ornithine; Ornithine-Oxo-Acid Transaminase; Transaminases | 1981 |
Developmental changes of free amino acid concentrations in fetal fluids of pigs.
Topics: Aging; Allantois; Amino Acids; Ammonia; Amniotic Fluid; Animals; Arginine; Female; Fetal Blood; Gestational Age; Glutamine; Glycine; Male; Ornithine; Placenta; Pregnancy; Swine; Urea; Uterus | 1995 |
Prenatal exclusion of the HHH syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Amniotic Fluid; Cells, Cultured; Citrulline; Female; Humans; Ornithine; Pregnancy; Prenatal Diagnosis; Syndrome | 1995 |
Decreased hyperammonaemia and orotic aciduria due to inactivation of ornithine aminotransferase in mice with a hereditary abnormal ornithine carbamoyltransferase.
Topics: Amino Acids; Ammonia; Animals; Behavior, Animal; Female; Male; Metabolism, Inborn Errors; Mice; Mice, Mutant Strains; Mutation; Ornithine; Ornithine Carbamoyltransferase; Ornithine-Oxo-Acid Transaminase; Orotic Acid | 1994 |
Effects of ornithine aminotransferase inactivation by 5-fluoromethylornithine in rats following portacaval anastomosis.
Topics: Amino Acids; Ammonia; Animals; Body Weight; Brain; Liver; Male; Ornithine; Ornithine-Oxo-Acid Transaminase; Portacaval Shunt, Surgical; Rats; Rats, Sprague-Dawley | 1994 |
Dietary citrulline but not ornithine counteracts dietary arginine deficiency in rats by increasing splanchnic release of citrulline.
Topics: Alanine; Amino Acids; Ammonia; Animals; Arginine; Blood Flow Velocity; Body Weight; Citrulline; Creatinine; Diet; Food; Glutamic Acid; Glutamine; Male; Ornithine; Orotic Acid; Proline; Rats; Rats, Sprague-Dawley; Splanchnic Circulation; Urea | 1994 |
Lysinuric protein intolerance. Urinary amino acid excretion at 2 and 9 days of age.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Arginine; Citrulline; Humans; Infant, Newborn; Lysine; Male; Ornithine | 1994 |
Hyperammonemia in Marasmic children.
Topics: Alanine Transaminase; Ammonia; Arginine; Aspartate Aminotransferases; Citrulline; Humans; Infant; Ornithine; Protein-Energy Malnutrition; Urea | 1994 |
Carbamoyl phosphate and ureagenesis are not involved in amino-acid-stimulated glycogenesis.
Topics: Amino Acids; Ammonia; Animals; Carbamyl Phosphate; Cells, Cultured; Glucose; Glycogen; Hypotonic Solutions; Liver; Male; Ornithine; Phosphorylation; Picolinic Acids; Rats; Rats, Wistar; Urea | 1994 |
Protection against lethal ammonia intoxication: synergism between endogenous ornithine and L-carnitine.
Topics: Acetates; Amino Acids; Ammonia; Animals; Brain; Carnitine; Drug Synergism; Drug Therapy, Combination; Female; Mice; Ornithine; Poisoning | 1994 |
Enhanced endogenous ornithine concentrations protect against tonic seizures and coma in acute ammonia intoxication.
Topics: 3-Mercaptopropionic Acid; Ammonia; Animals; Brain Chemistry; Coma; Dialysis; Dizocilpine Maleate; Electroshock; Epilepsy, Generalized; Female; Glutamate-Ammonia Ligase; Methionine Sulfoximine; Mice; N-Methylaspartate; Ornithine; Ornithine-Oxo-Acid Transaminase; Pentylenetetrazole; Postural Balance; Putrescine; Strychnine | 1993 |
Synthesis of citrulline from glutamine in pig enterocytes.
Topics: Ammonia; Animals; Carbon-Nitrogen Ligases; Citrulline; Female; Glutaminase; Glutamine; Jejunum; Ligases; Male; Ornithine; Ornithine Carbamoyltransferase; Ornithine-Oxo-Acid Transaminase; Proline; Swine | 1994 |
Regulation of urea and citrulline synthesis under physiological conditions.
Topics: Amino Acids; Ammonia; Animals; Citrulline; Glutamates; Male; Mitochondria, Liver; Nitrogen; Ornithine; Rats; Rats, Sprague-Dawley; Urea | 1993 |
Urea synthesis in enterocytes of developing pigs.
Topics: Ammonia; Ammonium Chloride; Animals; Animals, Newborn; Animals, Suckling; Arginine; Argininosuccinate Lyase; Argininosuccinate Synthase; Carbamoyl-Phosphate Synthase (Ammonia); Carbamyl Phosphate; Chromatography, High Pressure Liquid; Citrulline; Glutamine; Intestinal Mucosa; Intestines; Ornithine; Ornithine Carbamoyltransferase; Swine; Urea; Weaning | 1995 |
Oxidative metabolism in a rat hepatoma (N13) and isolated rat hepatocytes: a flow cytometric comparative study.
Topics: Ammonia; Animals; Carnitine; Flow Cytometry; Glucose; Glycolysis; Liver; Liver Neoplasms, Experimental; Male; Oleic Acid; Oleic Acids; Ornithine; Oxidation-Reduction; Rats; Rats, Wistar; Rhodamine 123; Rhodamines; Succinates; Succinic Acid | 1996 |
Cryptogenic hepatitis masking the diagnosis of ornithine transcarbamylase deficiency.
Topics: Absorption; Ammonia; Arginine; Child, Preschool; Citrulline; Diagnosis, Differential; Dietary Proteins; Female; Glutamine; Hepatitis; Humans; Infant; Lysine; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Urea | 1996 |
Hyperornithinemia-hyperammonemia-homocitrullinuria (HHH)-syndrome. Ultrastructural changes of mitochondria in cultured dermal fibroblasts of three patients.
Topics: Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Cells, Cultured; Child; Citrulline; Female; Fibroblasts; Humans; Male; Mitochondria; Ornithine; Skin; Syndrome | 1996 |
A novel missense mutation in the exon containing the putative ornithine-binding domain of the OTC enzyme in a female.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Binding Sites; Child, Preschool; Codon, Terminator; DNA Probes; Exons; Female; Humans; Mutation; Ornithine; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid | 1996 |
Ciliated cultured dermal fibroblasts in a patient with hyperornithinemia, hyperammonemia and homocitrullinuria (HHH) syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Cells, Cultured; Cilia; Citrulline; Endoplasmic Reticulum, Rough; Fibroblasts; Humans; Microscopy, Electron; Mitochondria; Ornithine; Skin; Syndrome; Urea | 1995 |
L-ornithine vs. L-ornithine-L-aspartate as a treatment for hyperammonemia-induced encephalopathy in rats.
Topics: Ammonia; Analysis of Variance; Animals; Brain; Brain Diseases; Dipeptides; Drug Therapy, Combination; Magnetic Resonance Spectroscopy; Male; Microdialysis; Nitrogen; Ornithine; Portacaval Shunt, Surgical; Protons; Rats; Rats, Wistar; Synaptic Transmission | 1997 |
Glucocorticoids play an important role in mediating the enhanced metabolism of arginine and glutamine in enterocytes of postweaning pigs.
Topics: Aging; Ammonia; Animals; Arginase; Arginine; Argininosuccinate Lyase; Argininosuccinate Synthase; Carbon Dioxide; Cells, Cultured; DNA; Enzyme Induction; Female; Glucocorticoids; Glutamine; Hydrocortisone; Jejunum; Male; Mifepristone; Ornithine; Proline; Receptors, Glucocorticoid; Swine; Urea; Weaning | 1997 |
[Evaluation of the effect of long term valproic acid treatment on plasma levels of carnitine, ammonia and amino acids related to the urea cycle in pediatric epileptic patients].
Topics: Adolescent; Amino Acids; Ammonia; Anticonvulsants; Carnitine; Child; Child, Preschool; Epilepsy; Glutamine; Glycine; Humans; Infant; Infant, Newborn; Ornithine; Prospective Studies; Retrospective Studies; Urea; Valproic Acid | 1997 |
Neonatal onset of hyperornithinemia-hyperammonemia-homocitrullinuria syndrome with favorable outcome.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Carnitine; Citrulline; Diet, Protein-Restricted; Humans; Infant, Newborn; Male; Ornithine | 1997 |
No increase of ornithine concentration in the liver of ornithine transcarbamylase-deficient spf-ash mice following intraperitoneal injection of ammonium chloride.
Topics: Ammonia; Ammonium Chloride; Animals; Arginine; Citrulline; Liver; Mice; Mice, Inbred Strains; Mice, Transgenic; Ornithine; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid; Peptones | 1997 |
Mechanism of carbamoyl phosphate synthetase from Escherichia coli--binding of the ATP molecules used in the reaction and sequestration by the enzyme of the ATP molecule that yields carbamoyl phosphate.
Topics: Adenosine Triphosphate; Ammonia; Bicarbonates; Carbamoyl-Phosphate Synthase (Ammonia); Carbamoyl-Phosphate Synthase (Glutamine-Hydrolyzing); Carbamyl Phosphate; Cations, Monovalent; Escherichia coli; Glutamine; Models, Chemical; Ornithine; Phosphates; Potassium | 1998 |
Hypoglycemia-associated hyperammonemia caused by impaired expression of ornithine cycle enzyme genes in C/EBPalpha knockout mice.
Topics: Ammonia; Animals; Blood Glucose; CCAAT-Enhancer-Binding Proteins; DNA-Binding Proteins; Genes, Lethal; Gluconeogenesis; Hypoglycemia; In Situ Hybridization; Liver; Mice; Mice, Knockout; Models, Biological; Nuclear Proteins; Ornithine; Urea | 1998 |
Free amino acid concentrations in milk: effects of microwave versus conventional heating.
Topics: Amino Acids; Ammonia; Animals; Cattle; Hot Temperature; Microwaves; Milk; Ornithine | 1998 |
Arginine dihydrolase pathway in Lactobacillus plantarum from orange.
Topics: Ammonia; Arginine; Beverages; Citrulline; Citrus; Colorimetry; Glucose; Hydrogen-Ion Concentration; Hydrolases; Lactobacillus; Ornithine; Spectrophotometry; Urea | 1999 |
Hyperornithinaemia-hyperammonaemia-homocitrullinuria syndrome is caused by mutations in a gene encoding a mitochondrial ornithine transporter.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acid Sequence; Amino Acid Substitution; Amino Acid Transport Systems, Basic; Ammonia; Animals; Canada; Carrier Proteins; Chromosome Mapping; Chromosomes, Human, Pair 13; Citrulline; Female; France; Genetic Carrier Screening; Humans; Karyotyping; Male; Membrane Transport Proteins; Mice; Mitochondria; Mitochondrial Membrane Transport Proteins; Molecular Sequence Data; Neurospora crassa; Ornithine; Point Mutation; Saccharomyces cerevisiae; Sequence Alignment; Sequence Deletion; Sequence Homology, Amino Acid; Skin; Syndrome; Transfection | 1999 |
Aberrations of ammonia metabolism in ornithine carbamoyltransferase-deficient spf-ash mice and their prevention by treatment with urea cycle intermediate amino acids and an ornithine aminotransferase inactivator.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Ammonium Chloride; Animals; Arginine; Citrulline; Enzyme Inhibitors; Injections, Intraperitoneal; Liver; Male; Mice; Mice, Transgenic; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Perfusion; Urea | 1999 |
Determination of urinary orotic acid and uracil by capillary zone electrophoresis.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Borates; Buffers; Citrulline; Dietary Proteins; Electrophoresis, Capillary; Humans; Hydrogen-Ion Concentration; Infant; Male; Ornithine; Orotic Acid; Syndrome; Uracil | 1999 |
Three novel mutations (G27E, insAAC, R179X) in the ORNT1 gene of Japanese patients with hyperornithinemia, hyperammonemia, and homocitrullinuria syndrome.
Topics: Amino Acid Metabolism, Inborn Errors; Amino Acid Sequence; Ammonia; Asian People; Biological Transport; Carrier Proteins; Citrulline; DNA Mutational Analysis; Exons; Humans; Japan; Mitochondria; Molecular Sequence Data; Mutation; Ornithine; Reverse Transcriptase Polymerase Chain Reaction; Syndrome | 2000 |
Arginine and ornithine oxidation catalyzed by lentil seedling copper-amine oxidase.
Topics: Amine Oxidase (Copper-Containing); Ammonia; Arginine; Fabaceae; Kinetics; Molecular Structure; Ornithine; Oxidation-Reduction; Oxygen Consumption; Plants, Medicinal; Spectrophotometry | 2000 |
Influence of hepatic ammonia removal on ureagenesis, amino acid utilization and energy metabolism in the ovine liver.
Topics: Amino Acids; Ammonia; Animals; Energy Metabolism; Liver; Male; Ornithine; Portal System; Sheep; Urea | 2000 |
Glutamine metabolism in endothelial cells: ornithine synthesis from glutamine via pyrroline-5-carboxylate synthase.
Topics: Alanine; Ammonia; Animals; Antimetabolites, Antineoplastic; Aorta; Asparagine; Aspartic Acid; Azaserine; Carbon Dioxide; Cattle; Cells, Cultured; Diazooxonorleucine; Endothelium, Vascular; Enzymes; Glutamic Acid; Glutamine; Humans; Microcirculation; Ornithine; Ornithine-Oxo-Acid Transaminase; Umbilical Veins; Venules | 2000 |
Functional ureogenesis in the gobiid fish Mugilogobius abei.
Topics: Amino Acid Sequence; Ammonia; Animals; Anti-Bacterial Agents; Carbon-Nitrogen Ligases; Citrulline; Female; Gills; Glutamate-Ammonia Ligase; Glutamine; Kinetics; Liver; Male; Molecular Sequence Data; Muscles; Nitrogen; Ornithine; Perciformes; RNA, Messenger; Seawater; Sequence Alignment; Skin; Urea; Uric Acid | 2000 |
Detection of neonatal argininosuccinate lyase deficiency by serum tandem mass spectrometry.
Topics: Amino Acid Sequence; Amino Acids; Ammonia; Arginine; Argininosuccinate Lyase; Argininosuccinic Acid; Argininosuccinic Aciduria; Base Sequence; Citrulline; Coma; Frameshift Mutation; Humans; Hyperammonemia; Infant, Newborn; Mass Spectrometry; Molecular Sequence Data; Neonatal Screening; Ornithine | 2001 |
Liver nitrogen movements during short-term infusion of high levels of ammonia into the mesenteric vein of sheep.
Topics: Amino Acids; Amino Acids, Branched-Chain; Ammonia; Analysis of Variance; Animals; Biological Transport; Cross-Over Studies; Glutamic Acid; Infusions, Intravenous; Liver; Male; Mesenteric Veins; Nitrogen; Ornithine; Sheep; Time Factors; Urea | 2001 |
Conscientious metabolic monitoring on a patient with hyperornithinemia-hyperammonemia-homocitrullinuria (HHH) syndrome undergoing anaesthesia.
Topics: Adult; Amino Acids; Ammonia; Anesthesia; Blood Coagulation Tests; Citrulline; Clinical Chemistry Tests; Female; Humans; Monitoring, Physiologic; Ornithine; Syndrome | 2001 |
A novel mutation, P126R, in a Japanese patient with HHH syndrome.
Topics: Adolescent; Ammonia; Base Sequence; Brain Diseases; Carrier Proteins; Cysts; DNA Primers; Exons; Gene Expression; Humans; Magnetic Resonance Imaging; Male; Metabolism, Inborn Errors; Methionine; Mitochondrial Diseases; Molecular Sequence Data; Ornithine; Point Mutation; Polymerase Chain Reaction; Polymorphism, Restriction Fragment Length; Septum Pellucidum; Syndrome; Tomography, X-Ray Computed | 2002 |
Nitrogen metabolism and excretion in the mangrove killifish Rivulus marmoratus II. Significant ammonia volatilization in a teleost during air-exposure.
Topics: Air; Amino Acids; Ammonia; Animals; Arginase; Carbon-Nitrogen Ligases; Fundulidae; Gills; Glutamic Acid; Glutamine; Nitrogen; Ornithine; Ornithine Carbamoyltransferase; Urea; Volatilization | 2002 |
Effect of arginine, ornithine and citrulline supplementation upon performance and metabolism of trained rats.
Topics: Ammonia; Animals; Arginine; Citrulline; Dietary Supplements; Glutamate-Ammonia Ligase; Glutamine; Glycogen; Liver; Male; Muscle, Skeletal; Ornithine; Rats; Rats, Wistar; Swimming; Urea | 2003 |
Treatment of ammonia intoxication in rats with urea cycle amino acids, furosemide and fluids.
Topics: Ammonia; Animals; Arginine; Citrulline; Diuretics; Fluid Therapy; Furosemide; Male; Ornithine; Poisoning; Rats; Rats, Wistar | 2003 |
Oral supplementation corrects plasma lysine concentrations in lysinuric protein intolerance.
Topics: Absorption; Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Female; Humans; Intestinal Absorption; Kidney Tubules; Kinetics; Lysine; Male; Nitrogen; Ornithine; Reference Values; Urea | 2003 |
The osmotic response of the Asian freshwater stingray (Himantura signifer) to increased salinity: a comparison with marine (Taeniura lymma) and Amazonian freshwater (Potamotrygon motoro) stingrays.
Topics: Acclimatization; Amino Acids; Ammonia; Analysis of Variance; Animals; Carbon-Nitrogen Ligases; Fresh Water; Glutamate-Ammonia Ligase; Ornithine; Seawater; Skates, Fish; Urea; Water-Electrolyte Balance | 2003 |
Treatment of hepatic coma: use of certain Krebs' urea cycle intermediates (L-arginine, DL-ornithine).
Topics: Amino Acids; Ammonia; Arginine; Citric Acid Cycle; Hepatic Encephalopathy; Humans; Ornithine; Urea | 1958 |
UREA FORMATION AND UREA CYCLE ENZYMES IN THE CESTODE, HYMENOLEPIS DIMINUTA.
Topics: Amino Acids; Ammonia; Animals; Arginase; Bicarbonates; Carbon Isotopes; Cestoda; Citrulline; Hymenolepis diminuta; Magnesium; Manganese; Metabolism; Ornithine; Research; Transferases; Urea | 1963 |
ON THE MECHANISM OF AMMONIA DETOXICATION BY L-ORNITHINE AND L-ASPARTATE.
Topics: Ammonia; Aspartic Acid; Blood Chemical Analysis; Enzyme Inhibitors; Ligases; Liver; Ornithine; Pharmacology; Rats; Research; Seizures; Toxicology; Urea | 1964 |
THE SYNTHESIS OF UREA IN THE BRAIN.
Topics: Alanine; Amino Acids; Aminobutyrates; Ammonia; Aspartic Acid; Brain; Carbon Isotopes; Citrulline; Ornithine; Proteins; Rats; Research; Tissue Culture Techniques; Urea | 1963 |
[INITIAL CLINICAL RESULTS FOLLOWING THE USE OF A NEW HEPATOPROTECTIVE AND ANTI-BLOOD AMMONIA PREPARATION].
Topics: Amino Acids; Ammonia; Arginine; Blood Chemical Analysis; Chemical and Drug Induced Liver Injury; Citrulline; Geriatrics; Hepatitis; Hepatitis A; Humans; Ornithine | 1963 |
STUDIES OF RAT LIVER AND KIDNEY ENZYMES. I. RESPONSE TO MASSIVE INTRAGASTRIC DOSES OF CHRONICALLY ADMINISTERED NITROGENOUS SUBSTANCES.
Topics: Alanine; Amino Acids; Ammonia; Arginine; Brain Diseases; Enzymes; Glutamates; Glutamine; Injections; Kidney; Liver; Liver Diseases; Nitrogen; Ornithine; Rats; Research; Stomach; Transaminases; Urea | 1964 |
STUDIES OF RAT LIVER AND KIDNEY ENZYMES. II. RESPONSE TO DIETARY PROTEIN DEFICIENCY AND REPLETION DURING CHRONIC ADMINISTRATION OF AMMONIUM ACETATE AND L-GLUTAMINE.
Topics: Acetates; Adaptation, Physiological; Ammonia; Arginine; Dietary Proteins; Enzymes; Glutamates; Glutamine; Hepatic Encephalopathy; Kidney; Kwashiorkor; Liver; Ornithine; Protein Deficiency; Rats; Research | 1964 |
A MODIFIED METHOD FOR THE SEPARATION OF BASIC AMINO ACIDS ON THE AUTOMATIC AMINO ACID ANALYZER.
Topics: Amino Acids; Amino Acids, Basic; Aminobutyrates; Ammonia; Arginine; Autoanalysis; Chromatography; Creatine; Creatinine; Hexosamines; Histidine; Lysine; Muscles; Ornithine; Peptides; Phenylalanine; Rabbits; Research; Tryptophan; Tyrosine | 1964 |
MEASUREMENT OF TISSUE ORNITHINE CARBAMOYLTRANSFERASE.
Topics: Ammonia; Animals; Citrulline; Colorimetry; Hydroxides; Liver; Mice; Ornithine; Ornithine Carbamoyltransferase; Research; Transferases | 1964 |
CLEAVAGE OF PEPTIDE PROLINE BONDS BY LITHIUM ALUMINUM HYDRIDE.
Topics: Aluminum Compounds; Amides; Amino Alcohols; Ammonia; Aspartic Acid; Autoanalysis; Chromatography; Countercurrent Distribution; Glutamates; Glycine; Indicators and Reagents; Leucine; Lithium Compounds; Ornithine; Peptides; Phenylalanine; Proline; Research; Tryptophan; Tyrothricin | 1964 |
PHARMACOLOGICAL STUDY ON L-ORNITHINE L-ASPARTATE.
Topics: Alanine Transaminase; Ammonia; Ammonium Chloride; Aspartate Aminotransferases; Aspartic Acid; Blood; Carbon Tetrachloride Poisoning; Chemical and Drug Induced Liver Injury; Clinical Enzyme Tests; D-Alanine Transaminase; Dogs; Hepatitis; Mice; Ornithine; Paralysis; Research; Sulfobromophthalein; Toxicology; Urea | 1964 |
MECHANISM OF THE PROTECTION BY L-ORNITHINE-L-ASPARTATE MIXTURE AND BY L-ARGININE IN AMMONIA INTOXICATION.
Topics: Ammonia; Arginine; Aspartic Acid; Chemical and Drug Induced Liver Injury; Dipeptides; Hepatitis; Ligases; Metabolism; Ornithine; Pharmacology; Rats; Research; Toxicology; Urea | 1964 |
EFFECTS OF EXERCISE AND ADMINISTRATION OF ASPARTIC ACID ON BLOOD AMMONIA IN THE RAT.
Topics: Ammonia; Aspartic Acid; Blood; Exercise; Fatigue; Metabolism; Ornithine; Pharmacology; Physical Exertion; Rats; Research | 1964 |
MECHANISM OF HEPATIC COMA IN SURGERY.
Topics: Ammonia; Blood; Hepatic Encephalopathy; Humans; Ligases; Liver; Liver Function Tests; Neurologic Manifestations; Ornithine; Ornithine Carbamoyltransferase; Portacaval Shunt, Surgical; Postoperative Complications | 1964 |
THE HYDROLYSIS OF ARGININE.
Topics: Ammonia; Arginine; Chromatography; Hydrochloric Acid; Hydrolysis; Hydroxides; Ion Exchange Resins; Ornithine; Piperidines; Research | 1965 |
THE EFFECT OF AMMONIA ADMINISTRATION ON OROTIC ACID EXCRETION IN RATS.
Topics: Ammonia; Ammonium Chloride; Antimetabolites; Arginine; Chromatography; Citrulline; Diet; Glutamine; Ornithine; Orotic Acid; Pharmacology; Rats; Research; Succinates; Urine | 1965 |
[FREE PLASMA AMINO ACIDS AND BLOOD AMMONIA FOLLOWING ORAL PROTEIN LOAD. STUDIES IN NORMAL PERSONS AND PATIENTS WITH LIVER CIRRHOSIS].
Topics: Amino Acids; Ammonia; Arginine; Aspartic Acid; Blood; Dietary Proteins; Glutamates; Humans; Liver Cirrhosis; Lysine; Methionine; Ornithine; Phenylalanine; Proteins; Tyrosine | 1965 |
STRUCTURAL REQUIREMENTS OF NITROGENOUS SUBSTANCES WHICH HAVE PROTECTIVE EFFECTS AGAINST ACUTE HYDRAZINE TOXICITY IN MICE.
Topics: Aminobutyrates; Ammonia; Antidotes; Arginine; Biotransformation; Chemical Phenomena; Chemistry; Hydrazines; Mice; Nitrogen; Ornithine; Pharmacology; Poisoning; Propionates; Research; Toxicology | 1965 |
Adaptative increase of ornithine production and decrease of ammonia metabolism in rat colonocytes after hyperproteic diet ingestion.
Topics: Adaptation, Physiological; Ammonia; Ammonium Chloride; Animals; Arginine; Body Weight; Citrulline; Colon; Dietary Proteins; Dose-Response Relationship, Drug; Eating; Feces; Hydrogen-Ion Concentration; Intestines; Male; Ornithine; Osmolar Concentration; Polyamines; Quaternary Ammonium Compounds; Rats; Rats, Inbred F344; Veins | 2004 |
Urea synthesis by ruminal epithelial and duodenal mucosal cells from growing sheep.
Topics: Ammonia; Animals; Arginase; Arginine; Aspartic Acid; Carbamoyl-Phosphate Synthase (Ammonia); Cells, Cultured; Citrulline; Duodenum; Enzyme Activation; Epithelial Cells; Gastric Mucosa; Intestinal Mucosa; Ornithine; Rumen; Sheep; Urea | 2004 |
Arginine synthesis does not occur during first-pass hepatic metabolism in the neonatal piglet.
Topics: Amino Acids; Ammonia; Animal Feed; Animals; Animals, Newborn; Arginine; Blood Urea Nitrogen; Deuterium; Enteral Nutrition; Liver; Male; Ornithine; Proline; Random Allocation; Swine; Urea | 2005 |
Expression of four glutamine synthetase genes in the early stages of development of rainbow trout (Oncorhynchus mykiss) in relationship to nitrogen excretion.
Topics: Ammonia; Animals; Egg Yolk; Gene Expression; Glutamate-Ammonia Ligase; Glutamine; Isoenzymes; Larva; Liver; Muscle, Skeletal; Nitrogen; Oncorhynchus mykiss; Ornithine; RNA, Messenger; Urea | 2005 |
Ornithine aminotransferase deficiency: diagnostic difficulties in neonatal presentation.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Citrulline; Diagnosis, Differential; Female; Fibroblasts; Glutamine; Humans; Hyperammonemia; Infant, Newborn; Male; Mutation; Neonatal Screening; Ornithine; Ornithine-Oxo-Acid Transaminase; Orotic Acid | 2005 |
Expression of ornithine-urea cycle enzymes in early life stages of air-breathing walking catfish Clarias batrachus and induction of ureogenesis under hyper-ammonia stress.
Topics: Air; Ammonia; Animals; Carbon-Nitrogen Ligases; Catfishes; Egg Yolk; Embryo, Nonmammalian; Fertilization; Glutamate-Ammonia Ligase; Life Cycle Stages; Ornithine; Urea | 2006 |
Postprandial increases in nitrogenous excretion and urea synthesis in the Chinese soft-shelled turtle, Pelodiscus sinensis.
Topics: Ammonia; Animal Feed; Animals; Brain; Eating; Fatty Acids, Nonesterified; Gastric Mucosa; Glutamate-Ammonia Ligase; Glutamine; Intestinal Mucosa; Liver; Muscle, Skeletal; Nitrogen; Ornithine; Postprandial Period; Turtles; Urea | 2007 |
Determination of homocitrulline in urine of patients with HHH syndrome by liquid chromatography tandem mass spectrometry.
Topics: Ammonia; Chromatography, Liquid; Citrulline; Creatinine; Humans; Mass Spectrometry; Ornithine; Syndrome | 2006 |
Degradation of arginine by Slackia exigua ATCC 700122 and Cryptobacterium curtum ATCC 700683.
Topics: Ammonia; Arginine; Chromatography, High Pressure Liquid; Citrulline; Dental Pulp Necrosis; Eubacterium; Humans; Hydrolases; Ornithine; Periodontal Pocket | 2006 |
Active ammonia transport and excretory nitrogen metabolism in the climbing perch, Anabas testudineus, during 4 days of emersion or 10 minutes of forced exercise on land.
Topics: Amino Acids; Ammonia; Animal Migration; Animals; Biological Transport, Active; Energy Metabolism; Glutamate-Ammonia Ligase; Liver; Metabolic Networks and Pathways; Motor Activity; Nitrogen; Ornithine; Oxygen Consumption; Perches; Urea | 2006 |
Coadministration of ornithine and alpha-ketoglutarate is no more effective than ornithine alone as an arginine precursor in piglets enterally fed an arginine-deficient diet.
Topics: Administration, Oral; Ammonia; Animals; Arginine; Ketoglutaric Acids; Male; Ornithine; Swine; Urea | 2007 |
Air-breathing catfish, Clarias batrachus upregulates glutamine synthetase and carbamyl phosphate synthetase III during exposure to high external ammonia.
Topics: Ammonia; Animals; Carbamoyl-Phosphate Synthase (Ammonia); Catfishes; Fish Proteins; Gene Expression Regulation, Enzymologic; Glutamate-Ammonia Ligase; Hydrocortisone; Liver; Organ Specificity; Ornithine; Oxygen Consumption; Up-Regulation; Urea | 2007 |
L-Ornithine phenylacetate (OP): a novel treatment for hyperammonemia and hepatic encephalopathy.
Topics: Ammonia; Drug Therapy, Combination; Hepatic Encephalopathy; Humans; Hyperammonemia; Liver; Models, Biological; Muscle, Skeletal; Ornithine; Phenylacetates | 2007 |
Curtobacterium ammoniigenes sp. nov., an ammonia-producing bacterium isolated from plants inhabiting acidic swamps in actual acid sulfate soil areas of Vietnam.
Topics: Actinomycetales; Ammonia; Bacterial Typing Techniques; Cell Wall; DNA, Bacterial; DNA, Ribosomal; Eleocharis; Fatty Acids; Genes, rRNA; Molecular Sequence Data; Nucleic Acid Hybridization; Onagraceae; Ornithine; Peptidoglycan; Phylogeny; Quinones; RNA, Bacterial; RNA, Ribosomal, 16S; Sequence Analysis, DNA; Sequence Homology, Nucleic Acid; Spores, Bacterial; Vietnam; Wetlands | 2007 |
Interaction between murine spf-ash mutation and genetic background yields different metabolic phenotypes.
Topics: Alanine; Ammonia; Animals; Arginine; Citrulline; Disease Models, Animal; Female; Glycine; Injections, Intravenous; Intestinal Mucosa; Liver; Male; Mice; Mice, Inbred ICR; Mice, Inbred Strains; Mice, Mutant Strains; Models, Biological; Mutation; Nitric Oxide; Ornithine; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Phenotype; Phenylalanine; Urea | 2007 |
Amino acids in CSF and plasma in hyperammonaemic coma due to arginase1 deficiency.
Topics: Adult; Amino Acids; Ammonia; Arginine; Biomarkers; Chromatography, Ion Exchange; Coma; Glutamine; Humans; Hyperammonemia; Hyperargininemia; Lysine; Male; Ornithine | 2008 |
L-ornithine and phenylacetate synergistically produce sustained reduction in ammonia and brain water in cirrhotic rats.
Topics: Ammonia; Animals; Body Water; Brain; Drug Synergism; Liver Cirrhosis; Male; Ornithine; Phenylacetates; Phenylbutyrates; Rats; Rats, Sprague-Dawley | 2009 |
L-ornithine phenylacetate attenuates increased arterial and extracellular brain ammonia and prevents intracranial hypertension in pigs with acute liver failure.
Topics: Ammonia; Animals; Arteries; Brain; Drug Combinations; Extracellular Space; Intracranial Hypertension; Liver Failure, Acute; Ornithine; Phenylacetates; Swine | 2009 |
Effects of crowding on ornithine-urea cycle enzyme mRNA expression and activity in gulf toadfish (Opsanus beta).
Topics: Ammonia; Animals; Arginase; Batrachoidiformes; Carbon-Nitrogen Ligases; Glutamate-Ammonia Ligase; Hydrocortisone; Liver; Lyases; Ornithine; Ornithine Carbamoyltransferase; Population Density; RNA, Messenger; Urea | 2009 |
Parenteral administration of L-arginine enhances fetal survival and growth in sheep carrying multiple fetuses.
Topics: 3-Hydroxybutyric Acid; Ammonia; Animals; Arginine; Birth Weight; Body Weight; Cysteine; Female; Fetal Death; Fetal Growth Retardation; Injections, Intravenous; Ornithine; Pregnancy; Pregnancy Outcome; Pregnancy, Multiple; Proline; Random Allocation; Sheep, Domestic | 2011 |
Ornithine phenylacetate prevents disturbances of motor-evoked potentials induced by intestinal blood in rats with portacaval anastomosis.
Topics: Amino Acids; Ammonia; Animals; Brain; Disease Models, Animal; Evoked Potentials, Motor; Glutamine; Hepatic Encephalopathy; Male; Ornithine; Phenylacetates; Portacaval Shunt, Surgical; Rats; Rats, Sprague-Dawley | 2012 |
Ammonia reduction with ornithine phenylacetate restores brain eNOS activity via the DDAH-ADMA pathway in bile duct-ligated cirrhotic rats.
Topics: Amidohydrolases; Ammonia; Animals; Arginine; Bile Ducts; Brain; Ligation; Liver Cirrhosis; Male; NADPH Oxidases; Nitric Oxide Synthase Type III; Ornithine; Phenylacetates; Rats; Rats, Sprague-Dawley; Tumor Necrosis Factor-alpha | 2012 |
Hyperammonemia in a patient with late-onset ornithine carbamoyltransferase deficiency.
Topics: Age of Onset; Ammonia; Arginine; Citrulline; Humans; Hyperammonemia; Male; Middle Aged; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Pedigree; Renal Dialysis; Sodium Benzoate | 2012 |
Chronic postnatal ornithine administration to rats provokes learning deficit in the open field task.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Animals, Newborn; Avoidance Learning; Behavior, Animal; Citrulline; Cognition; Developmental Disabilities; Disease Models, Animal; Half-Life; Learning Disabilities; Maze Learning; Memory; Memory, Long-Term; Ornithine; Postural Balance; Rats; Rats, Wistar; Thiobarbituric Acid Reactive Substances | 2012 |
Impairment of brain redox homeostasis caused by the major metabolites accumulating in hyperornithinemia-hyperammonemia-homocitrullinuria syndrome in vivo.
Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Antioxidants; Brain; Catalase; Citrulline; Glutathione Peroxidase; Homeostasis; Injections, Intraperitoneal; Injections, Intraventricular; Male; Nitric Oxide; Ornithine; Oxidation-Reduction; Oxidative Stress; Protein Carbonylation; Rats; Rats, Wistar; Sulfhydryl Compounds; Thiobarbituric Acid Reactive Substances; Urease | 2012 |
Interorgan metabolism of ornithine phenylacetate (OP)--a novel strategy for treatment of hyperammonemia.
Topics: Acetates; Ammonia; Animals; Arteries; Bile Ducts; Drug Interactions; Female; Glutamine; Hyperammonemia; Kidney; Ligation; Liver; Liver Cirrhosis, Biliary; Muscle, Skeletal; Nitrogen Isotopes; Ornithine; Phenols; Rats; Rats, Wistar; Tissue Distribution | 2013 |
Ontogeny of ornithine-urea cycle gene expression in zebrafish (Danio rerio).
Topics: Aging; Ammonia; Animals; Base Sequence; Carbon-Nitrogen Ligases; Digoxigenin; Embryo, Nonmammalian; Gene Expression; Gene Silencing; In Situ Hybridization, Fluorescence; Molecular Sequence Data; Ornithine; Real-Time Polymerase Chain Reaction; RNA Probes; Urea; Zebrafish | 2013 |
Ornithine phenylacetate targets alterations in the expression and activity of glutamine synthase and glutaminase to reduce ammonia levels in bile duct ligated rats.
Topics: Ammonia; Animals; Bile Ducts; Disease Models, Animal; End Stage Liver Disease; Glutamate-Ammonia Ligase; Glutaminase; Ligation; Liver; Male; Ornithine; Rats; Rats, Sprague-Dawley | 2014 |
Influence of environmental hypertonicity on the induction of ureogenesis and amino acid metabolism in air-breathing walking catfish (Clarias batrachus, Bloch).
Topics: Air; Amino Acids; Ammonia; Animals; Catfishes; Diuretics, Osmotic; Environment; Hypertonic Solutions; Mannitol; Ornithine; Osmosis; Respiration; Urea; Walking | 2014 |
L-Ornithine phenylacetate reduces ammonia in pigs with acute liver failure through phenylacetylglycine formation: a novel ammonia-lowering pathway.
Topics: Ammonia; Animals; Biomarkers; Brain; Disease Models, Animal; Female; Glycine; Hyperammonemia; Kidney; Liver Failure, Acute; Ornithine; Random Allocation; Swine; Time Factors | 2014 |
Safety of long-term dietary supplementation with L-arginine in pigs.
Topics: Adipose Tissue, White; Alanine; Ammonia; Animals; Animals, Suckling; Arginine; Body Composition; Cholesterol; Dietary Supplements; Female; Glutamine; Glycine; Male; Muscle, Skeletal; Ornithine; Proline; Swine; Time Factors; Triglycerides; Weaning | 2015 |
Ammonia produces pathological changes in human hepatic stellate cells and is a target for therapy of portal hypertension.
Topics: Ammonia; Animals; Cell Proliferation; Cells, Cultured; Endoplasmic Reticulum; Hepatic Stellate Cells; Humans; Hypertension, Portal; Male; Ornithine; Rats; Rats, Sprague-Dawley; Reactive Oxygen Species | 2016 |
Safety, tolerability, and pharmacokinetics of l-ornithine phenylacetate in patients with acute liver injury/failure and hyperammonemia.
Topics: Acetates; Adolescent; Adult; Aged; Ammonia; Female; Glutamine; Humans; Hyperammonemia; Kidney Function Tests; Liver; Liver Failure, Acute; Male; Middle Aged; Ornithine; Phenols; Registries; Treatment Outcome; Young Adult | 2018 |
The cyanobacterial ornithine-ammonia cycle involves an arginine dihydrolase.
Topics: Ammonia; Arginine; Bacterial Proteins; Biomass; Carbon Dioxide; Citrulline; Cyanobacteria; Hydrolases; Mutation; Nitrogen; Nitrogen Isotopes; Ornithine; Oscillometry; Polyamines; Synechocystis; Urea | 2018 |
Pivotal role of inter-organ aspartate metabolism for treatment of mitochondrial aspartate-glutamate carrier 2 (citrin) deficiency, based on the mouse model.
Topics: Amino Acids; Ammonia; Ammonium Chloride; Animals; Aspartic Acid; Citrulline; Citrullinemia; Disease Models, Animal; Glycerolphosphate Dehydrogenase; Hyperammonemia; Intestine, Small; Lactates; Liver; Mice, Inbred C57BL; Mice, Knockout; Mitochondrial Membrane Transport Proteins; Organ Specificity; Ornithine; Perfusion; Portal Vein; Pyruvic Acid; Urea | 2019 |
Ruminal microbes of adult steers do not degrade extracellular L-citrulline and have a limited ability to metabolize extracellular L-glutamate1,2.
Topics: Amino Acids; Ammonia; Animals; Arginine; Bacteria; Cattle; Citrulline; Glutamic Acid; Glutamine; Male; Ornithine; Proline; Rumen | 2019 |
Poly(ornithine)-based self-assembling drug for recovery of hyperammonemia and damage in acute liver injury.
Topics: Acetaminophen; Ammonia; Animals; Cattle; Cell Survival; Chemical and Drug Induced Liver Injury; Chondroitin Sulfates; Disease Models, Animal; Drug Delivery Systems; Endothelial Cells; Hyperammonemia; Macrophages; Male; Mice; Mice, Inbred C57BL; Mice, Inbred ICR; Nanoparticles; Ornithine; RAW 264.7 Cells | 2019 |
Molecular characterization and ornithine-urea cycle genes expression in air-breathing magur catfish (Clarias magur) during exposure to high external ammonia.
Topics: Ammonia; Animals; Argininosuccinate Lyase; Argininosuccinate Synthase; Catfishes; Fish Proteins; Ornithine; Ornithine Carbamoyltransferase; Phylogeny; RNA, Messenger; Sequence Alignment; Sequence Analysis, Protein; Tissue Distribution; Urea | 2020 |
Crystal structures and biochemical analyses of the bacterial arginine dihydrolase ArgZ suggests a "bond rotation" catalytic mechanism.
Topics: Ammonia; Arginine; Carbon Dioxide; Catalysis; Crystallography, X-Ray; Hydrolases; Nitrogen; Ornithine; Protein Conformation; Synechocystis | 2020 |
Enzymology of the pathway for ATP production by arginine breakdown.
Topics: Adenosine Triphosphate; Amino Acid Transport Systems; Ammonia; Antiporters; Arginine; Bacterial Proteins; Carbon Dioxide; Energy Metabolism; Gene Expression Regulation, Bacterial; Hydrolases; Kinetics; Lactococcus lactis; Liposomes; Ornithine; Ornithine Carbamoyltransferase; Phosphatidylcholines; Phosphatidylethanolamines; Phosphatidylglycerols; Phosphotransferases (Carboxyl Group Acceptor); Recombinant Proteins | 2021 |
Clinical and biochemical characteristics of patients with ornithine transcarbamylase deficiency.
Topics: Adolescent; Adult; Ammonia; Arginine; Child; Child, Preschool; China; Creatine; Female; Humans; Hyperammonemia; Lysine; Male; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Urea; Young Adult | 2020 |
Ornithine-A urea cycle metabolite enhances autophagy and controls Mycobacterium tuberculosis infection.
Topics: Ammonia; Animals; Apoptosis; Arginase; Atropine; Autophagy; Cell Proliferation; Disease Progression; Female; Imidazoles; Kupffer Cells; Macrophages, Alveolar; Macrophages, Peritoneal; Mice; Mice, Inbred C57BL; Nitric Oxide; Ornithine; Phosphatidylserines; Reactive Oxygen Species; RNA, Small Interfering; Tuberculosis; Urea | 2020 |
A Trial of Ornithine Phenylacetate and the Arc of Ammonia's History in the Management of Overt Hepatic Encephalopathy.
Topics: Ammonia; Hepatic Encephalopathy; Humans; Ornithine | 2021 |
Bile-duct ligation renders the brain susceptible to hypotension-induced neuronal degeneration: Implications of ammonia.
Topics: Ammonia; Animals; Antigens, Nuclear; Anxiety; Apoptosis; Behavior, Animal; Bile Ducts; Caspase 3; Cerebrovascular Circulation; Disease Models, Animal; Hepatic Encephalopathy; Hyperammonemia; Hypotension; Ligation; Male; Nerve Tissue Proteins; Neurodegenerative Diseases; Neurons; Ornithine; Rats; Rats, Sprague-Dawley | 2021 |
Reply.
Topics: Ammonia; Hepatic Encephalopathy; Humans; Ornithine | 2021 |
Reversible Leukoencephalopathy in a Man with Childhood-onset Hyperornithinemia-Hyperammonemia-Homocitrullinuria Syndrome.
Topics: Ammonia; Child; Humans; Hyperammonemia; Leukoencephalopathies; Male; Middle Aged; Ornithine; Urea Cycle Disorders, Inborn | 2022 |
Population Pharmacokinetic Analysis to Assist Dose Selection of the L-Ornithine Salt of Phenylacetic Acid.
Topics: Adult; Ammonia; Clinical Trials as Topic; Hepatic Encephalopathy; Humans; Ornithine; Phenylacetates | 2022 |
Moving towards a novel therapeutic strategy for hyperammonemia that targets glutamine metabolism.
Topics: Ammonia; Animals; Fibroblasts; Glutamate Dehydrogenase; Glutamine; Hyperammonemia; Mice; Ornithine; Ornithine Carbamoyltransferase Deficiency Disease; Swine | 2022 |
New insights into the effect of bisphenol AF exposure on maternal mammary glands at various stages of gestation in mice.
Topics: Amino Acids; Ammonia; Animals; Benzhydryl Compounds; Female; Fluorocarbons; Mice; Ornithine; Phenylalanine; Pregnancy; Proline; RNA, Messenger; Threonine; Tyrosine; Valine | 2022 |
Metabolomic Analysis of Microcystis aeruginosa After Exposure to the Algicide L-Lysine.
Topics: Ammonia; Arginine; Citrulline; Cyanobacteria; Ecosystem; Herbicides; Humans; Lysine; Microcystins; Microcystis; Ornithine | 2022 |
An orally deliverable ornithine-based self-assembling polymer nanomedicine ameliorates hyperammonemia in acetaminophen-induced acute liver injury.
Topics: Acetaminophen; Ammonia; Animals; Hyperammonemia; Liver; Mice; Nanomedicine; Ornithine; Polyethylene Glycols; Polymers | 2023 |