ammonium hydroxide and benzoic acid

ammonium hydroxide has been researched along with benzoic acid in 65 studies

Research

Studies (65)

TimeframeStudies, this research(%)All Research%
pre-199036 (55.38)18.7374
1990's27 (41.54)18.2507
2000's1 (1.54)29.6817
2010's1 (1.54)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Holzknecht, RA; Mauer, SM; Summar, ML; Tuchman, M; Vnencak-Jones, CL1
Bachmann, C; Bordugo, A; Burlina, AB; Colombo, JP; Ferrari, V; Wermuth, B; Zacchello, F1
Allen, JT; Holton, JB; Walter, JH1
Bautista, NS; Dass, PD; Hardman, SH; Kurtz, I; Lawson, LR1
Hommes, FA; Koch, R; Pandya, AL; Williams, JC1
Sakuma, T1
Kalbag, SS; Palekar, AG2
Michalak, A; Qureshi, IA5
Barshop, BA; Breuer, J; Holm, J; Leslie, J; Nyhan, WL1
Cyr, DM; Tremblay, GC1
Oliver, RM; Raman, GV; Talbot, S1
Asai, K; Ichiki, T; Kidouchi, K; Sakuma, T; Sugiyama, N; Wada, Y1
Angulo, MA; Canas, JA; Castro-Magana, M; Kalbag, SS; Kim, SJ; Palekar, AG1
Costell, M; Grisolía, S; O'Connor, JE2
Bachmann, C; Baerlocher, K; Hochreutener, H; Issakainen, J1
Brusilow, SW; Rajantie, J; Simell, O; Sipilä, I; Valle, DL1
Harris, RA; Swartzentruber, MS1
Batshaw, ML; Monahan, PS1
Bachmann, C; Colombo, JP; Gradwohl, M; Pfister, U1
Batshaw, ML; Coyle, JT; Hyman, SL; Mellits, ED; Quaskey, S; Qureshi, IA; Robinson, MB1
Matsuda, I; Ohtani, Y; Ohyanagi, K; Yamamoto, S1
Marshall, L; Mendenhall, CL; Rouster, S; Weesner, R1
Cyr, DM; Griffith, AD; Maswoswe, SM; Tremblay, GC1
Deshmukh, DR; Thomas, PE1
Godard, M; Letarte, J; Ouellet, R; Qureshi, IA1
Heininger, J; McCormick, K; Robinson, B; Viscardi, RM1
Inoue, Y; Kuhara, T; Matsumoto, I; Matsumoto, M; Shinka, T1
Paris, S; Pouysségur, J1
Batshaw, M; Brusilow, SW; Burton, B; Danney, M; Levitsky, L; McKeethren, C; Roth, K; Waber, LJ; Ward, J1
Baxter, P; Bourgeois, J; Bureau, J; Guibaud, P; Louis, JJ1
Berger, R; Mooy, P; Teijema, HL; Van de Bor, M; van Gelderen, HH; van Zoeren, D1
Fujiwara, K; Kamoshita, S; Kodama, H; Motokawa, Y; Nose, O; Tajiri, H1
Hayakawa, C; Kato, T; Maehara, M; Mizutani, N; Suzuki, S; Watanabe, K1
Steele, RD1
Batshaw, ML; Brusilow, S; Letarte, J; Ouellet, R; Qureshi, IA1
Al-Naama, MM; Rowsell, EV; Rowsell, KV1
Kuroda, Y; Miyao, M; Naito, E; Takeda, E; Toshima, K; Watanabe, T1
Freese, DK; Green, TP; Marchessault, RP1
Kamoshita, S; Kodama, H; Motokawa, Y1
Batshaw, ML; Blom, W; Brubakk, AM; Brusilow, S; Burton, BK; Cann, HM; Kerr, D; Mamunes, P; Matalon, R; Myerberg, D; Schafer, IA; Waber, L1
Berger, R; Blom, W; Brubakk, AM; Teijema, LL1
Letarte, J; Ouellet, R; Qureshi, IA1
Igarashi, M; Iwasaki, H; Kawana, S; Namiki, A1
Cleary, MA; Walter, JH; Wraith, JE1
Dass, PD; Holmes, EW; Stuart, BP1
Butterworth, RF; Qureshi, IA; Ratnakumari, L2
Ishizaki, T; Kubota, K1
Qureshi, IA; Tremblay, GC1
Henry, BW; Lange, C; Matalon, R; Melnyk, AR; Zeller, WP1
Klinger, RJ; Lo, WD; Sloan, HR; Sotos, JF1
Bassett, SS; Brusilow, SW; Clissold, DB; Maestri, NE1
Dallaire, L; Feoli-Fonseca, JC; Lambert, M; Melançon, SB; Millington, DS; Mitchell, G; Qureshi, IA1
Bonocore, G; Buonocore, G; Ciani, F; Donati, MA; Pasquini, E; Shih, VE; Zammarchi, E1
del Rosario, M; Lauer, SJ; Werlin, SL1
Beaudet, AL; Dennis, JA; Frazer, M; Healy, PJ; Lee, B; Mull, B; O'Brien, WE; Patejunas, G; Reeds, PJ; Warman, AW; Yu, H1
Goda, M; Kobayashi, M; Shimizu, S1
Burlina, AB; Korall, H; Ogier, H; Trefz, FK1
Austin, S; Coon, JJ; Donohue, TJ; Higbee, A; Hodge, DB; Kontur, WS; Noguera, DR; Oshlag, JZ; Ulbrich, A; Zhang, W; Zhang, Y1

Reviews

3 review(s) available for ammonium hydroxide and benzoic acid

ArticleYear
Treatment of urea cycle disorders.
    Enzyme, 1987, Volume: 38, Issue:1-4

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Benzoates; Benzoic Acid; Dietary Proteins; Humans; Nitrogen; Phenylacetates; Prognosis

1987
The biochemistry and toxicology of benzoic acid metabolism and its relationship to the elimination of waste nitrogen.
    Pharmacology & therapeutics, 1993, Volume: 60, Issue:1

    Topics: Ammonia; Animals; Benzoates; Benzoic Acid; Humans; Nitrogen; Urea

1993
Late clinical presentation of partial carbamyl phosphate synthetase I deficiency.
    American journal of diseases of children (1960), 1993, Volume: 147, Issue:3

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Biopsy; Body Height; Body Weight; Carbamoyl-Phosphate Synthase (Ammonia); Coma; Diagnosis, Differential; Dietary Proteins; Growth Disorders; Humans; Male; Pediatrics; Phenylacetates; Renal Dialysis

1993

Trials

3 trial(s) available for ammonium hydroxide and benzoic acid

ArticleYear
A new therapy for portal systemic encephalopathy.
    The American journal of gastroenterology, 1986, Volume: 81, Issue:7

    Topics: Aged; Ammonia; Benzoates; Benzoic Acid; Double-Blind Method; Drug Evaluation; Hepatic Encephalopathy; Humans; Male; Middle Aged; Phenylacetates; Random Allocation

1986
Long-term treatment of girls with ornithine transcarbamylase deficiency.
    The New England journal of medicine, 1996, Sep-19, Volume: 335, Issue:12

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Brain Diseases; Child; Child, Preschool; Drug Therapy, Combination; Female; Humans; Infant; Intelligence; Ornithine Carbamoyltransferase Deficiency Disease; Phenylacetates; Phenylbutyrates; Treatment Outcome

1996
Chronic sodium benzoate therapy in children with inborn errors of urea synthesis: effect on carnitine metabolism and ammonia nitrogen removal.
    Biochemical and molecular medicine, 1996, Volume: 57, Issue:1

    Topics: Adolescent; Adult; Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Carnitine; Child; Child, Preschool; Female; Humans; Male; Nitrogen; Ornithine; Retrospective Studies; Syndrome; Urea

1996

Other Studies

59 other study(ies) available for ammonium hydroxide and benzoic acid

ArticleYear
Prospective versus clinical diagnosis and therapy of acute neonatal hyperammonaemia in two sisters with carbamyl phosphate synthetase deficiency.
    Journal of inherited metabolic disease, 1992, Volume: 15, Issue:2

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Carbamoyl-Phosphate Synthase (Ammonia); Female; Humans; Infant, Newborn; Kinetics; Pedigree; Peritoneal Dialysis; Phenylacetates; Polymorphism, Restriction Fragment Length; Pregnancy; Prenatal Diagnosis; Prospective Studies; Renal Dialysis

1992
Partial N-acetylglutamate synthetase deficiency: a new case with uncontrollable movement disorders.
    Journal of inherited metabolic disease, 1992, Volume: 15, Issue:3

    Topics: Acetyltransferases; Amino-Acid N-Acetyltransferase; Ammonia; Arginine; Benzoates; Benzoic Acid; Brain; Dietary Proteins; Female; Humans; Infant; Magnetic Resonance Imaging; Movement Disorders; Orotic Acid

1992
Arginosuccinate synthetase deficiency: good outcome despite severe neonatal hyperammonaemia.
    Journal of inherited metabolic disease, 1992, Volume: 15, Issue:2

    Topics: Ammonia; Arginine; Argininosuccinate Synthase; Benzoates; Benzoic Acid; Dietary Proteins; Humans; Infant, Newborn; Male

1992
Benzoate modulates renal and extrarenal nitrogen flow: metabolic mechanisms.
    Life sciences, 1991, Volume: 48, Issue:8

    Topics: Ammonia; Animals; Benzoates; Benzoic Acid; Glutamates; Glutamic Acid; Glutamine; Hippurates; Kidney Tubules, Proximal; Male; Nitrogen; Rats; Rats, Inbred Strains

1991
N-acetylglutamate synthetase deficiency: clinical and laboratory observations.
    Journal of inherited metabolic disease, 1991, Volume: 14, Issue:5

    Topics: Acetyltransferases; Amino-Acid N-Acetyltransferase; Ammonia; Arginine; Benzoates; Benzoic Acid; Citrulline; Dietary Proteins; Humans; Infant; Infant, Newborn; Liver; Male; Phenylacetates

1991
Alteration of urinary carnitine profile induced by benzoate administration.
    Archives of disease in childhood, 1991, Volume: 66, Issue:7

    Topics: Acetylcarnitine; Administration, Oral; Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Carnitine; Child, Preschool; Dose-Response Relationship, Drug; Hippurates; Humans; Male

1991
Amino acids in the rat liver and plasma and some metabolites in the liver after sodium benzoate treatment.
    Biochemical medicine and metabolic biology, 1991, Volume: 46, Issue:1

    Topics: Adenosine Triphosphate; Amino Acids; Ammonia; Animals; Benzoates; Benzoic Acid; Glycine; Liver; Male; Rats; Rats, Inbred Strains

1991
Plasma and urinary levels of carnitine in different experimental models of hyperammonemia and the effect of sodium benzoate treatment.
    Biochemical medicine and metabolic biology, 1990, Volume: 43, Issue:2

    Topics: Ammonia; Animals; Benzoates; Benzoic Acid; Carnitine; Mice; Mice, Mutant Strains

1990
Excretion of hippuric acid during sodium benzoate therapy in patients with hyperglycinaemia or hyperammonaemia.
    Journal of inherited metabolic disease, 1989, Volume: 12, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Child, Preschool; Female; Glycine; Hippurates; Humans; Infant; Infant, Newborn; Male; Metabolism, Inborn Errors

1989
On combination therapy with benzoate and piridoxilate.
    American journal of diseases of children (1960), 1989, Volume: 143, Issue:12

    Topics: Ammonia; Benzoates; Benzoic Acid; Drug Synergism; Humans; Metabolism, Inborn Errors; Pyridoxine

1989
Hyperammonaemic coma in ureterosigmoid urinary diversion.
    Postgraduate medical journal, 1989, Volume: 65, Issue:765

    Topics: Amino Acids; Ammonia; Benzoates; Benzoic Acid; Colon, Sigmoid; Coma; Female; Humans; Middle Aged; Phenylacetates; Urinary Diversion

1989
Identification of benzoylcarnitine in the urine of a patient of hyperammonemia.
    The Tohoku journal of experimental medicine, 1989, Volume: 159, Issue:2

    Topics: Ammonia; Benzoates; Benzoic Acid; Carbamoyl-Phosphate Synthase (Ammonia); Carnitine; Humans

1989
Failure of sodium benzoate to alleviate plasma and liver ammonia in rats.
    Biochemical medicine and metabolic biology, 1989, Volume: 41, Issue:1

    Topics: Ammonia; Animals; Benzoates; Benzoic Acid; Liver; Male; Rats; Rats, Inbred Strains

1989
Carbamyl glutamate prevents the potentiation of ammonia toxicity by sodium benzoate.
    European journal of pediatrics, 1989, Volume: 148, Issue:6

    Topics: Ammonia; Animals; Benzoates; Benzoic Acid; Drug Synergism; Glutamates; Mice; Urea

1989
[Carbamyl phosphate synthase deficiency: clinical symptoms, diagnosis and dietary-medicamentous treatment in the neonatal period and infancy].
    Helvetica paediatrica acta, 1989, Volume: 43, Issue:5-6

    Topics: Amino Acids; Ammonia; Arginine; Benzoates; Benzoic Acid; Carbamoyl-Phosphate Synthase (Ammonia); Carnitine; Citrulline; Combined Modality Therapy; Dietary Proteins; Female; Fetal Growth Retardation; Humans; Infant, Newborn; Male; Pregnancy

1989
Waste nitrogen excretion via amino acid acylation: benzoate and phenylacetate in lysinuric protein intolerance.
    Pediatric research, 1986, Volume: 20, Issue:11

    Topics: Acylation; Alanine; Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Benzoates; Benzoic Acid; Child; Child, Preschool; Creatinine; Glutamine; Hippurates; Humans; Lysine; Nitrogen; Orotic Acid; Phenylacetates; Urea

1986
Inhibition of metabolic processes by coenzyme-A-sequestering aromatic acids. Prevention by para-chloro- and para-nitrobenzoic acids.
    Biochemical pharmacology, 1987, Oct-01, Volume: 36, Issue:19

    Topics: 4-Aminobenzoic Acid; Ammonia; Animals; Benzoates; Benzoic Acid; Coenzyme A; Fatty Acids; Glucose; In Vitro Techniques; Liver; Male; Nitrobenzoates; Rats; Salicylates; Salicylic Acid; Valproic Acid

1987
Sodium benzoate inhibits fatty acid oxidation in rat liver: effect on ammonia levels.
    Biochemical medicine and metabolic biology, 1988, Volume: 40, Issue:2

    Topics: Acetyl Coenzyme A; Adenosine Triphosphate; Ammonia; Animals; Benzoates; Benzoic Acid; Caprylates; Coenzyme A; Fatty Acids; Liver; Mitochondria, Liver; Oxidation-Reduction; Oxygen Consumption; Palmitates; Rats; Rats, Inbred Strains

1988
Mitochondrial urea cycle enzymes in rats treated with sodium benzoate.
    Biochemical and biophysical research communications, 1988, Mar-15, Volume: 151, Issue:2

    Topics: Acetyltransferases; Amino-Acid N-Acetyltransferase; Ammonia; Animals; Benzoates; Benzoic Acid; Carbamoyl-Phosphate Synthase (Ammonia); Hippurates; Kinetics; Ligases; Male; Mitochondria, Liver; Ornithine Carbamoyltransferase; Rats; Rats, Inbred Strains; Urea; Urease

1988
Effect of sodium benzoate and sodium phenylacetate on brain serotonin turnover in the ornithine transcarbamylase-deficient sparse-fur mouse.
    Pediatric research, 1988, Volume: 23, Issue:4

    Topics: Administration, Oral; Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Benzoates; Benzoic Acid; Brain; Child; Citrulline; Humans; Injections, Intraperitoneal; Male; Mice; Mice, Mutant Strains; Ornithine Carbamoyltransferase Deficiency Disease; Phenylacetates; Serotonin

1988
Hyperammonemia related to carnitine metabolism with particular emphasis on ornithine transcarbamylase deficiency.
    Enzyme, 1987, Volume: 38, Issue:1-4

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Carnitine; Child; Dietary Proteins; Humans; Reye Syndrome

1987
The potentiation of ammonia toxicity by sodium benzoate is prevented by L-carnitine.
    Biochemical and biophysical research communications, 1987, Jun-15, Volume: 145, Issue:2

    Topics: Ammonia; Animals; Benzoates; Benzoic Acid; Carnitine; Drug Synergism; Glutamates; Male; Mice; Mitochondria, Liver; Urea

1987
The effect of sodium benzoate on ammonia toxicity in rats.
    Biochemical and biophysical research communications, 1986, Jul-16, Volume: 138, Issue:1

    Topics: Acetates; Acetyl Coenzyme A; Ammonia; Animals; Benzoates; Benzoic Acid; Drug Interactions; Fasting; Glycine; Hippurates; Male; Rats

1986
Effect of arginine-free diet on ammonia metabolism in young and adult ferrets.
    The Journal of nutrition, 1986, Volume: 116, Issue:4

    Topics: Aging; Ammonia; Animals; Arginine; Benzoates; Benzoic Acid; Brain; Brain Diseases; Diet; Ferrets; Male

1986
Chronic benzoate therapy in a boy with partial ornithine transcarbamylase deficiency.
    The Journal of pediatrics, 1985, Volume: 106, Issue:5

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Child; Humans; Male; Ornithine Carbamoyltransferase Deficiency Disease

1985
Partial pyruvate decarboxylase deficiency with profound lactic acidosis and hyperammonemia: responses to dichloroacetate and benzoate.
    American journal of medical genetics, 1985, Volume: 22, Issue:2

    Topics: Acidosis; Ammonia; Benzoates; Benzoic Acid; Carboxy-Lyases; Dichloroacetic Acid; Hippurates; Humans; Infant, Newborn; Lactates; Male; Pyruvate Decarboxylase

1985
Benzoylalanine: detection and identification of an alanine conjugate with benzoic acid in hyperammonemic patients treated with sodium benzoate.
    Clinica chimica acta; international journal of clinical chemistry, 1985, Oct-15, Volume: 151, Issue:3

    Topics: Alanine; Ammonia; Benzoates; Benzoic Acid; Carboxylic Acids; Child, Preschool; Chromatography, Gas; Female; Gas Chromatography-Mass Spectrometry; Humans; Infant; Infant, Newborn; Metabolism, Inborn Errors

1985
Growth factors activate the Na+/H+ antiporter in quiescent fibroblasts by increasing its affinity for intracellular H+.
    The Journal of biological chemistry, 1984, Sep-10, Volume: 259, Issue:17

    Topics: Amiloride; Ammonia; Animals; Benzoates; Benzoic Acid; Carbon Radioisotopes; Carrier Proteins; Cell Line; Cricetinae; Cricetulus; Fibroblasts; Growth Substances; Hydrogen-Ion Concentration; Kinetics; Lung; Sodium-Hydrogen Exchangers; Thrombin

1984
Treatment of episodic hyperammonemia in children with inborn errors of urea synthesis.
    The New England journal of medicine, 1984, Jun-21, Volume: 310, Issue:25

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Argininosuccinate Synthase; Benzoates; Benzoic Acid; Carbamoyl-Phosphate Synthase (Ammonia); Drug Administration Schedule; Humans; Infant; Injections, Intravenous; Male; Ornithine Carbamoyltransferase Deficiency Disease; Parenteral Nutrition, Total; Phenylacetates; Renal Dialysis; Urea

1984
Severe ornithine transcarbamylase deficiency. Two and a half years' survival with normal development.
    Archives of disease in childhood, 1984, Volume: 59, Issue:5

    Topics: Amino Acids; Ammonia; Benzoates; Benzoic Acid; Drug Therapy, Combination; Enteral Nutrition; Humans; Infant, Newborn; Keto Acids; Male; Mannitol; Ornithine Carbamoyltransferase Deficiency Disease

1984
Successful treatment of severe carbamyl phosphate synthetase I deficiency.
    Archives of disease in childhood, 1984, Volume: 59, Issue:12

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Carbamoyl-Phosphate Synthase (Ammonia); Dietary Proteins; Female; Humans; Infant, Newborn; Ligases; Phenylacetates

1984
Activity of the glycine cleavage system in hyperammonemia treated with benzoate.
    The Tohoku journal of experimental medicine, 1983, Volume: 140, Issue:3

    Topics: Ammonia; Animals; Benzoates; Benzoic Acid; Female; Folic Acid; Glycine; Humans; Liver; Male; Mice; Mice, Mutant Strains; Ornithine Carbamoyltransferase Deficiency Disease; Pyridoxine

1983
Hyperargininemia: clinical course and treatment with sodium benzoate and phenylacetic acid.
    Brain & development, 1983, Volume: 5, Issue:6

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids; Ammonia; Arginine; Benzoates; Benzoic Acid; Child, Preschool; Dietary Proteins; Humans; Male; Phenylacetates

1983
Hyperammonemia and orotic aciduria in portacaval-shunted rats.
    The Journal of nutrition, 1984, Volume: 114, Issue:1

    Topics: Ammonia; Ammonium Chloride; Animals; Arginine; Benzoates; Benzoic Acid; Liver; Liver Diseases; Male; Nitrogen; Organ Size; Orotic Acid; Portacaval Shunt, Surgical; Rats; Rats, Inbred Strains; Spleen; Urea

1984
Treatment of hyperargininemia with sodium benzoate and arginine-restricted diet.
    The Journal of pediatrics, 1984, Volume: 104, Issue:3

    Topics: Adolescent; Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Benzoates; Benzoic Acid; Combined Modality Therapy; Female; Humans

1984
Glycine metabolism in rat kidney cortex slices.
    The Biochemical journal, 1982, Apr-15, Volume: 204, Issue:1

    Topics: Amino Acids; Ammonia; Animals; Benzoates; Benzoic Acid; Carbon Dioxide; Glycine; In Vitro Techniques; Kidney Cortex; Male; Rats; Rats, Inbred Strains; Serine; Tissue Distribution; Urea

1982
Effect of long-term administration of sodium benzoate to a patient with partial ornithine carbamoyl transferase deficiency.
    Clinical pediatrics, 1983, Volume: 22, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Child; Female; Humans; Male; Ornithine Carbamoyltransferase Deficiency Disease; Time Factors

1983
Disposition of sodium benzoate in newborn infants with hyperammonemia.
    The Journal of pediatrics, 1983, Volume: 102, Issue:5

    Topics: Ammonia; Benzoates; Benzoic Acid; Bilirubin; Female; Hippurates; Humans; Infant, Newborn; Infant, Newborn, Diseases; Kinetics; Male; Metabolic Clearance Rate

1983
Treatment of hyperammonemia with sodium benzoate.
    The Journal of pediatrics, 1983, Volume: 103, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Child; Female; Humans

1983
Treatment of inborn errors of urea synthesis: activation of alternative pathways of waste nitrogen synthesis and excretion.
    The New England journal of medicine, 1982, Jun-10, Volume: 306, Issue:23

    Topics: Amino Acid Metabolism, Inborn Errors; Amino Acids, Essential; Ammonia; Arginine; Argininosuccinate Synthase; Argininosuccinic Aciduria; Benzoates; Benzoic Acid; Carbamoyl-Phosphate Synthase (Ammonia); Child, Preschool; Citrulline; Coma; Female; Humans; Infant; Infant, Newborn; Infusions, Parenteral; Male; Nitrogen; Ornithine Carbamoyltransferase Deficiency Disease; Urea

1982
Successful treatment of severe OTC deficiency.
    The Journal of pediatrics, 1982, Volume: 100, Issue:6

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Benzoates; Benzoic Acid; Citrulline; Humans; Infant, Newborn; Male; Ornithine Carbamoyltransferase Deficiency Disease

1982
Spontaneous animal models of ornithine transcarbamylase deficiency: studies on serum and urinary nitrogenous metabolites.
    Advances in experimental medicine and biology, 1982, Volume: 153

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Benzoates; Benzoic Acid; Diet; Female; Glutamine; Heterozygote; Liver; Male; Mice; Mice, Mutant Strains; Ornithine Carbamoyltransferase; Ornithine Carbamoyltransferase Deficiency Disease; Orotic Acid

1982
[Anesthetic management for a patient with citrullinemia and liver cirrhosis].
    Masui. The Japanese journal of anesthesiology, 1995, Volume: 44, Issue:1

    Topics: Ammonia; Anesthesia, Spinal; Benzoates; Benzoic Acid; Citrulline; Female; Femoral Neck Fractures; Hepatic Encephalopathy; Hip Prosthesis; Humans; Liver Cirrhosis; Middle Aged; Preoperative Care

1995
Absence of acidosis in the initial presentation of propionic acidaemia.
    Archives of disease in childhood. Fetal and neonatal edition, 1995, Volume: 72, Issue:3

    Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Carnitine; Food Preservatives; Humans; Infant, Newborn; Liver Transplantation; Nervous System Diseases; Propionates

1995
Effects of benzoate and hippurate on the regulation of interorgan nitrogen flow: therapeutic benefits.
    Contributions to nephrology, 1994, Volume: 110

    Topics: Ammonia; Animals; Benzoates; Benzoic Acid; Glutamic Acid; Glutamine; Hippurates; Male; Mannitol; Nitrogen; Rats; Rats, Sprague-Dawley

1994
Effect of L-carnitine on cerebral and hepatic energy metabolites in congenitally hyperammonemic sparse-fur mice and its role during benzoate therapy.
    Metabolism: clinical and experimental, 1993, Volume: 42, Issue:8

    Topics: Adenosine Triphosphate; Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Benzoates; Benzoic Acid; Body Weight; Brain; Brain Chemistry; Carnitine; Coenzyme A; Dose-Response Relationship, Drug; Energy Metabolism; Genetic Linkage; Glutamates; Glutamic Acid; Glutamine; Hair Diseases; Ketoglutaric Acids; Lactates; Liver; Male; Mice; Mice, Mutant Strains; Ornithine Carbamoyltransferase; Pyruvates; Time Factors; Urea

1993
Effect of single oral dose of sodium benzoate on ureagenesis in healthy men and two patients with late onset citrullinaemia.
    European journal of clinical pharmacology, 1993, Volume: 45, Issue:5

    Topics: Administration, Oral; Adult; Ammonia; Argininosuccinate Synthase; Benzoates; Benzoic Acid; Citrulline; Drug Administration Schedule; Humans; Male; Time Factors; Urea

1993
[Profile of hepatic and muscular acylcarnitines in chronically hyperammonemic mice after an acute treatment with sodium benzoate: dose-response study].
    Annales de biologie clinique, 1993, Volume: 51, Issue:10-11

    Topics: Acetylcarnitine; Ammonia; Animals; Benzoates; Benzoic Acid; Carnitine; Dose-Response Relationship, Drug; Liver; Male; Mice; Mice, Mutant Strains; Muscles

1993
[Carnitine levels in muscle in mice with hyperammonemia: effect of treatment with sodium benzoate].
    Canadian journal of physiology and pharmacology, 1993, Volume: 71, Issue:7

    Topics: Ammonia; Animals; Benzoates; Benzoic Acid; Carnitine; Creatine Kinase; Female; Male; Mice; Mice, Inbred ICR; Muscles

1993
Prospective management of a child with neonatal citrullinemia.
    The Journal of pediatrics, 1993, Volume: 122, Issue:1

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Arginine; Argininosuccinate Synthase; Benzoates; Benzoic Acid; Child Development; Child, Preschool; Citrulline; Female; Humans; Infant; Infant, Newborn; Phenylacetates

1993
Effect of sodium benzoate on cerebral and hepatic energy metabolites in spf mice with congenital hyperammonemia.
    Biochemical pharmacology, 1993, Jan-07, Volume: 45, Issue:1

    Topics: Acetyl Coenzyme A; Adenosine Triphosphate; Ammonia; Animals; Benzoates; Benzoic Acid; Brain; Coenzyme A; Disease Models, Animal; Dose-Response Relationship, Drug; Glutamine; Liver; Male; Mice; Mice, Mutant Strains; Ornithine Carbamoyltransferase Deficiency Disease; Time Factors; Urea

1993
Tissue acylcarnitine and acyl-coenzyme A profiles in chronically hyperammonemic mice treated with sodium benzoate and supplementary L-carnitine.
    Biomedicine & pharmacotherapy = Biomedecine & pharmacotherapie, 1995, Volume: 49, Issue:7-8

    Topics: Acetylcarnitine; Acyl Coenzyme A; Ammonia; Animals; Benzoates; Benzoic Acid; Carnitine; Chronic Disease; Creatine Kinase; Drug Therapy, Combination; Food Preservatives; Liver; Mice; Mice, Mutant Strains; Muscle, Skeletal

1995
Free and esterified coenzyme A in the liver and muscles of chronically hyperammonemic mice treated with sodium benzoate.
    Biochemical and molecular medicine, 1995, Volume: 54, Issue:2

    Topics: Acetyl Coenzyme A; Ammonia; Animals; Benzoates; Benzoic Acid; Chronic Disease; Coenzyme A; Disease Models, Animal; Dose-Response Relationship, Drug; Food Preservatives; Liver; Male; Mice; Mice, Inbred ICR; Muscle, Skeletal; Ornithine Carbamoyltransferase Deficiency Disease

1995
Neonatal onset of hyperornithinemia-hyperammonemia-homocitrullinuria syndrome with favorable outcome.
    The Journal of pediatrics, 1997, Volume: 131, Issue:3

    Topics: Amino Acid Metabolism, Inborn Errors; Ammonia; Benzoates; Benzoic Acid; Carnitine; Citrulline; Diet, Protein-Restricted; Humans; Infant, Newborn; Male; Ornithine

1997
Hyperammonemic encephalopathy after chemotherapy. Survival after treatment with sodium benzoate and sodium phenylacetate.
    Journal of clinical gastroenterology, 1997, Volume: 25, Issue:4

    Topics: Adolescent; Ammonia; Antimetabolites; Benzoates; Benzoic Acid; Brain Diseases; Drug-Related Side Effects and Adverse Reactions; Humans; Male; Phenylacetates

1997
Evaluation of gene therapy for citrullinaemia using murine and bovine models.
    Journal of inherited metabolic disease, 1998, Volume: 21 Suppl 1

    Topics: Adenoviruses, Human; Amino Acid Metabolism, Inborn Errors; Ammonia; Animals; Arginine; Argininosuccinate Synthase; Benzoates; Benzoic Acid; Cattle; Citrulline; Disease Models, Animal; Evaluation Studies as Topic; Gene Transfer Techniques; Genetic Therapy; Genetic Vectors; Liver; Mice; Nitrogen; Treatment Outcome; Urea

1998
The catalytic mechanism of amidase also involves nitrile hydrolysis.
    FEBS letters, 1998, Nov-20, Volume: 439, Issue:3

    Topics: Amidohydrolases; Ammonia; Benzoic Acid; Catalysis; Enzyme Inhibitors; Escherichia coli; Hydrolysis; Nitriles; Rhodococcus; Substrate Specificity

1998
Long-term treatment with sodium phenylbutyrate in ornithine transcarbamylase-deficient patients.
    Molecular genetics and metabolism, 2001, Volume: 72, Issue:4

    Topics: Adolescent; Ammonia; Benzoates; Benzoic Acid; Child; Child, Preschool; DNA Mutational Analysis; Drug Therapy, Combination; Female; Glutamine; Humans; Infant; Infant, Newborn; Male; Ornithine Carbamoyltransferase Deficiency Disease; Phenylbutyrates; Retrospective Studies; Treatment Outcome

2001
Metabolism of Multiple Aromatic Compounds in Corn Stover Hydrolysate by Rhodopseudomonas palustris.
    Environmental science & technology, 2015, Jul-21, Volume: 49, Issue:14

    Topics: Ammonia; Anaerobiosis; Benzoic Acid; Biodegradation, Environmental; Biomass; Biotransformation; Carbohydrates; Hydrocarbons, Aromatic; Hydrolysis; Lignin; Mutation; Rhodobacter sphaeroides; Rhodopseudomonas; Waste Products; Zea mays

2015