alpha-methyl-beta-hydroxybutyrate has been researched along with tiglylglycine in 11 studies
| Studies (alpha-methyl-beta-hydroxybutyrate) | Trials (alpha-methyl-beta-hydroxybutyrate) | Recent Studies (post-2010) (alpha-methyl-beta-hydroxybutyrate) | Studies (tiglylglycine) | Trials (tiglylglycine) | Recent Studies (post-2010) (tiglylglycine) |
|---|---|---|---|---|---|
| 23 | 0 | 5 | 20 | 0 | 6 |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 5 (45.45) | 18.7374 |
| 1990's | 1 (9.09) | 18.2507 |
| 2000's | 2 (18.18) | 29.6817 |
| 2010's | 3 (27.27) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| Aramaki, S; Lehotay, D; Middleton, B; Nyhan, WL; Sweetman, L; Winter, SC | 1 |
| Leonard, JV; Middleton, B; Seakins, JW | 1 |
| Bartlett, K; Cannon, RA; Conde, C; Gomez Vazquez, J; Lipson, M; Middleton, B; Nyhan, WL; Romanos, A; Sweetman, L | 1 |
| Bennett, MJ; Littlewood, JM; MacDonald, A; Pollitt, RJ; Thompson, J | 1 |
| Condado, I; DelValle, JA; Garcia, MJ; Jiménez, A; López, O; Merinero, B; Solaguren, R; Ugarte, M | 1 |
| Middleton, B; Oorthuys, JW; Schutgens, RB; Tegelaers, WH; vd Blij, JF; Veder, HA; Vulsma, T | 1 |
| da C Ferreira, G; Dalcin, KB; de Assis, DR; Filho, CS; Latini, A; Leipnitz, G; Maria, RC; Perry, ML; Ribeiro, CA; Rosa, RB; Schuck, PF; Wajner, M; Wannmacher, CM; Wyse, AT | 1 |
| Baldellou, A; Briones, P; Campistol, J; Cortés, N; Delpiccolo, C; Fernández, C; Fons, C; Fuentes-Castelló, MA; García-Villoria, J; González, I; Hernández-Gonzalez, A; Messeguer, A; Navarro-Sastre, A; Pérez-Cerdá, C; Ribes, A | 1 |
| Arica, SG; Arica, V; Dag, H; Gülbayzar, S; Obut, O; Onur, H | 1 |
| Akiba, K; Aoyama, Y; Fukao, T; Goto, M; Hasegawa, Y; Hashimoto, T; Hori, T; Kuwayama, N; Morita, M; Moriyama, Y; Murayama, K; Ohtake, A; Shigematsu, Y; Usuda, N; Venkatesan, R; Wierenga, R | 1 |
| Bancel, LP; Dessein, AF; Germain, N; Guemann, AS; Joncquel Chevalier Curt, M | 1 |
11 other study(ies) available for alpha-methyl-beta-hydroxybutyrate and tiglylglycine
| Article | Year |
|---|---|
Urinary excretion of 2-methylacetoacetate, 2-methyl-3-hydroxybutyrate and tiglylglycine after isoleucine loading in the diagnosis of 2-methylacetoacetyl-CoA thiolase deficiency.
Topics: Acetoacetates; Acetyl-CoA C-Acyltransferase; Butanones; Glycine; Humans; Hydroxybutyrates; Infant; Isoleucine; Male | 1991 |
Acetoacetyl CoA thiolase deficiency presenting as ketotic hypoglycemia.
Topics: Acetoacetates; Acetyl-CoA C-Acetyltransferase; Acetyltransferases; Acidosis; Female; Glycine; Humans; Hydroxybutyrates; Hypoglycemia; Infant; Ketosis | 1987 |
3-Ketothiolase deficiency.
Topics: 3-Hydroxybutyric Acid; Acetyl Coenzyme A; Acetyl-CoA C-Acyltransferase; Acyl Coenzyme A; Acyltransferases; Child; Female; Fibroblasts; Glycine; Humans; Hydroxybutyrates; Infant; Isoleucine; Ketosis; Male; Valerates | 1986 |
A case of beta-ketothiolase deficiency.
Topics: Acetyl-CoA C-Acyltransferase; Acidosis; Acyltransferases; Dietary Proteins; Female; Glycine; Humans; Hydroxybutyrates; Infant | 1983 |
Late onset type of propionic acidaemia: case report and biochemical studies.
Topics: Acidosis; Amino Acid Metabolism, Inborn Errors; Carbon-Carbon Ligases; Female; Glycine; Humans; Hydroxybutyrates; Infant; Ketosis; Ligases; Propionates | 1981 |
Beta-ketothiolase deficiency in a family confirmed by in vitro enzymatic assays in fibroblasts.
Topics: Acetyl-CoA C-Acyltransferase; Acidosis; Acyltransferases; Adult; Child; Fibroblasts; Glycine; Humans; Hydroxybutyrates; Male; Metabolism, Inborn Errors | 1982 |
Inhibition of energy metabolism by 2-methylacetoacetate and 2-methyl-3-hydroxybutyrate in cerebral cortex of developing rats.
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Acetates; Acetoacetates; Acetyl-CoA C-Acyltransferase; Acidosis; Alcohol Oxidoreductases; Animals; Brain; Carbon Dioxide; Cerebral Cortex; Citrates; Creatine Kinase; Dose-Response Relationship, Drug; Electron Transport; Energy Metabolism; Glucose; Glutathione; Glycine; Hydroxybutyrates; In Vitro Techniques; Intellectual Disability; Lactic Acid; NG-Nitroarginine Methyl Ester; Oxygen; Rats; Rats, Wistar; Time Factors | 2005 |
Study of patients and carriers with 2-methyl-3-hydroxybutyryl-CoA dehydrogenase (MHBD) deficiency: difficulties in the diagnosis.
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Alcohol Oxidoreductases; Amino Acid Metabolism, Inborn Errors; Female; Glycine; Heredodegenerative Disorders, Nervous System; Humans; Hydroxybutyrates; Infant; Infant, Newborn; Male; Valerates | 2009 |
Beta-ketothiolase deficiency brought with lethargy: case report.
Topics: 3-Hydroxybutyric Acid; Acetyl-CoA C-Acyltransferase; Amino Acid Metabolism, Inborn Errors; Carnitine; Female; Glycine; Humans; Hydroxybutyrates; Infant; Ketosis; Lethargy | 2011 |
The first case in Asia of 2-methyl-3-hydroxybutyryl-CoA dehydrogenase deficiency (HSD10 disease) with atypical presentation.
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Acetyl-CoA C-Acetyltransferase; Base Sequence; Carnitine; Child; Diagnosis, Differential; DNA Mutational Analysis; Dyskinesias; Fibroblasts; Glycine; Humans; Hydroxybutyrates; Immunoblotting; Lipid Metabolism, Inborn Errors; Male; Mental Retardation, X-Linked; Mitochondria; Models, Molecular; Point Mutation; Protein Structure, Tertiary | 2014 |
Abnormal Ketone Bodies in a 22-Month-Old Boy Presenting with Recurrent Vomiting and Metabolic Acidosis.
Topics: Acetoacetates; Acetyl-CoA C-Acyltransferase; Acidosis; Amino Acid Metabolism, Inborn Errors; Glycine; Humans; Hydroxybutyrates; Infant; Ketone Bodies; Male; Vomiting | 2019 |