alpha-methyl-beta-hydroxybutyrate has been researched along with isoleucine in 7 studies
| Studies (alpha-methyl-beta-hydroxybutyrate) | Trials (alpha-methyl-beta-hydroxybutyrate) | Recent Studies (post-2010) (alpha-methyl-beta-hydroxybutyrate) | Studies (isoleucine) | Trials (isoleucine) | Recent Studies (post-2010) (isoleucine) |
|---|---|---|---|---|---|
| 23 | 0 | 5 | 5,938 | 74 | 1,138 |
| Timeframe | Studies, this research(%) | All Research% |
|---|---|---|
| pre-1990 | 3 (42.86) | 18.7374 |
| 1990's | 1 (14.29) | 18.2507 |
| 2000's | 2 (28.57) | 29.6817 |
| 2010's | 1 (14.29) | 24.3611 |
| 2020's | 0 (0.00) | 2.80 |
| Authors | Studies |
|---|---|
| de Céspedes, C; Estrada, Y; Loria, AR; Nyhan, WL; Sweetman, L; Weyler, W | 1 |
| Aramaki, S; Lehotay, D; Middleton, B; Nyhan, WL; Sweetman, L; Winter, SC | 1 |
| Bartlett, K; Cannon, RA; Conde, C; Gomez Vazquez, J; Lipson, M; Middleton, B; Nyhan, WL; Romanos, A; Sweetman, L | 1 |
| Bartlett, K; Middleton, B | 1 |
| Fukao, T; Hazama, A; Kohno, Y; Kondo, M; Kondo, N; Kubo, T; Matsuo, N; Sakura, N; Shigematsu, Y; Yamaga, H; Yamaguchi, S; Zhang, GX | 1 |
| Forstner, R; Sass, JO; Sperl, W | 1 |
| de Almeida, IT; Diogo, L; Duran, M; Garcia, P; Ijlst, L; Luís, PB; Moedas, M; Ofman, R; Ruiter, JP; Silva, MF; Wanders, RJ | 1 |
7 other study(ies) available for alpha-methyl-beta-hydroxybutyrate and isoleucine
| Article | Year |
|---|---|
Abnormal metabolites of isoleucine in a patient with propionyl-CoA carboxylase deficiency.
Topics: Acetoacetates; Carboxy-Lyases; Child, Preschool; Consanguinity; Female; Glycine; Humans; Hydroxy Acids; Hydroxybutyrates; Isoleucine; Keto Acids; Pentanoic Acids; Propionates | 1978 |
Urinary excretion of 2-methylacetoacetate, 2-methyl-3-hydroxybutyrate and tiglylglycine after isoleucine loading in the diagnosis of 2-methylacetoacetyl-CoA thiolase deficiency.
Topics: Acetoacetates; Acetyl-CoA C-Acyltransferase; Butanones; Glycine; Humans; Hydroxybutyrates; Infant; Isoleucine; Male | 1991 |
3-Ketothiolase deficiency.
Topics: 3-Hydroxybutyric Acid; Acetyl Coenzyme A; Acetyl-CoA C-Acyltransferase; Acyl Coenzyme A; Acyltransferases; Child; Female; Fibroblasts; Glycine; Humans; Hydroxybutyrates; Infant; Isoleucine; Ketosis; Male; Valerates | 1986 |
The synthesis and characterisation of 2-methylacetoacetyl coenzyme A and its use in the identification of the site of the defect in 2-methylacetoacetic and 2-methyl-3-hydroxybutyric aciduria.
Topics: Acetoacetates; Acetyl-CoA C-Acetyltransferase; Acyl Coenzyme A; Amino Acid Metabolism, Inborn Errors; Cells, Cultured; Child, Preschool; Fibroblasts; Humans; Hydroxybutyrates; Isoleucine | 1983 |
The mitochondrial acetoacetyl-CoA thiolase (T2) deficiency in Japanese patients: urinary organic acid and blood acylcarnitine profiles under stable conditions have subtle abnormalities in T2-deficient patients with some residual T2 activity.
Topics: Acetoacetates; Acetyl-CoA C-Acetyltransferase; Amino Acid Metabolism, Inborn Errors; Carnitine; Humans; Hydroxybutyrates; Infant; Isoleucine; Ketone Bodies; Male; Mitochondria; Mutation | 2003 |
2-Methyl-3-hydroxybutyryl-CoA dehydrogenase deficiency: impaired catabolism of isoleucine presenting as neurodegenerative disease.
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Alcohol Oxidoreductases; Amino Acid Metabolism, Inborn Errors; Brain; Child, Preschool; Humans; Hydroxybutyrates; Infant; Infant, Newborn; Isoleucine; Magnetic Resonance Imaging; Neurodegenerative Diseases | 2004 |
Valproic acid utilizes the isoleucine breakdown pathway for its complete β-oxidation.
Topics: 3-Hydroxyacyl CoA Dehydrogenases; Acyl Coenzyme A; Alcohol Oxidoreductases; Cell Line; Enoyl-CoA Hydratase; Fibroblasts; Humans; Hydroxybutyrates; Isoleucine; Oxidation-Reduction; Substrate Specificity; Valproic Acid | 2011 |