adenylosuccinate has been researched along with aminoimidazole carboxamide in 11 studies
Studies (adenylosuccinate) | Trials (adenylosuccinate) | Recent Studies (post-2010) (adenylosuccinate) | Studies (aminoimidazole carboxamide) | Trials (aminoimidazole carboxamide) | Recent Studies (post-2010) (aminoimidazole carboxamide) |
---|---|---|---|---|---|
52 | 1 | 5 | 1,913 | 35 | 830 |
Timeframe | Studies, this research(%) | All Research% |
---|---|---|
pre-1990 | 2 (18.18) | 18.7374 |
1990's | 5 (45.45) | 18.2507 |
2000's | 3 (27.27) | 29.6817 |
2010's | 1 (9.09) | 24.3611 |
2020's | 0 (0.00) | 2.80 |
Authors | Studies |
---|---|
Jaeken, J; Van den Bergh, F; Van den Berghe, G; Vincent, MF | 4 |
Van den Berghe, G; Vincent, MF | 1 |
Holmes, EW; Patterson, D; Sabina, RL | 1 |
Domkin, VD; Lazebnik, TA; Smirnov, MN | 1 |
Marie, S; Race, V; Van den Berghe, G; Vincent, MF | 2 |
Colman, RF; Palenchar, JB | 1 |
Chen, BC; Duley, JA; Khoo, TB; McGown, IN; Ngu, LH; Pitt, J; Thong, MK; Yunus, ZM | 1 |
11 other study(ies) available for adenylosuccinate and aminoimidazole carboxamide
Article | Year |
---|---|
Adenylosuccinase activity and succinylpurine production in fibroblasts of adenylosuccinase-deficient children.
Topics: Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Cells, Cultured; Child; Fibroblasts; Humans; Kinetics; Purine-Pyrimidine Metabolism, Inborn Errors; Purines; Ribonucleotides | 1991 |
Radiochemical assay of adenylosuccinase: demonstration of parallel loss of activity toward both adenylosuccinate and succinylaminoimidazole carboxamide ribotide in liver of patients with the enzyme defect.
Topics: Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Animals; Carbon Radioisotopes; Chromatography, Thin Layer; Cold Temperature; Enzyme Stability; Fumarates; Humans; Liver; Male; Muscles; Rats; Rats, Inbred Strains; Ribonucleotides; Saccharomyces cerevisiae; Substrate Specificity | 1991 |
Influence of succinylpurines on the binding of adenosine to a particulate fraction of rat cerebral cortex.
Topics: Adenosine; Adenosine Monophosphate; Aminoimidazole Carboxamide; Animals; Cell Membrane; Cerebral Cortex; Imidazoles; Rats; Receptors, Purinergic; Ribonucleotides | 1989 |
5-Amino-4-imidazolecarboxamide riboside (Z-riboside) metabolism in eukaryotic cells.
Topics: Adenosine Monophosphate; Aminoimidazole Carboxamide; Animals; Cells, Cultured; Cricetinae; Cricetulus; Female; Fibroblasts; Imidazoles; Inosine Monophosphate; Ovary; Purine Nucleotides; Pyrimidine Nucleotides; Ribonucleosides; Ribonucleotides | 1985 |
A new diagnostic technique for adenylosuccinate lyase deficiency.
Topics: Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Chromatography, Ion Exchange; Humans; Infant; Infant, Newborn; Purine-Pyrimidine Metabolism, Inborn Errors; Ribonucleosides; Spectrophotometry, Ultraviolet | 1995 |
Residual adenylosuccinase activities in fibroblasts of adenylosuccinase-deficient children: parallel deficiency with adenylosuccinate and succinyl-AICAR in profoundly retarded patients and non-parallel deficiency in a mildly retarded girl.
Topics: Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Binding, Competitive; Cells, Cultured; Child; Chromatography, Ion Exchange; Female; Fibroblasts; Humans; Hydrogen-Ion Concentration; Intellectual Disability; Kinetics; Nucleotides; Potassium Chloride; Ribonucleotides; Substrate Specificity | 1993 |
Functional studies in fibroblasts of adenylosuccinase-deficient children.
Topics: Adenosine Monophosphate; Adenosine Triphosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Cells, Cultured; Child; Fibroblasts; Formates; Humans; Hypoxanthine; Hypoxanthines; Intellectual Disability; Ribonucleotides | 1993 |
Clinical, biochemical and molecular genetic correlations in adenylosuccinate lyase deficiency.
Topics: 5' Untranslated Regions; Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Chromatography, Gel; Electrophoresis, Polyacrylamide Gel; Fibroblasts; Genotype; Homozygote; Humans; Intellectual Disability; Kinetics; Metabolism, Inborn Errors; Mutation; Mutation, Missense; Recombinant Fusion Proteins; Recombinant Proteins; Ribonucleosides; Temperature; Time Factors | 2000 |
Adenylosuccinate lyase deficiency: from the clinics to molecular biology.
Topics: Adenosine; Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Enzyme Stability; Gene Expression; Heating; Humans; Recombinant Fusion Proteins; Ribonucleotides | 2000 |
Characterization of a mutant Bacillus subtilis adenylosuccinate lyase equivalent to a mutant enzyme found in human adenylosuccinate lyase deficiency: asparagine 276 plays an important structural role.
Topics: Adenosine Monophosphate; Adenylosuccinate Lyase; Amino Acid Sequence; Aminoimidazole Carboxamide; Arginine; Asparagine; Bacillus subtilis; Bacterial Proteins; Circular Dichroism; Enzyme Activation; Humans; Hydrogen-Ion Concentration; Kinetics; Molecular Sequence Data; Molecular Weight; Mutagenesis, Site-Directed; Point Mutation; Protein Structure, Secondary; Recombinant Proteins; Ribonucleotides; Substrate Specificity; Threonine | 2003 |
Adenylosuccinate lyase deficiency in a Malaysian patient, with novel adenylosuccinate lyase gene mutations.
Topics: Adenosine; Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Autistic Disorder; Biomarkers; Child Development; Chromatography, High Pressure Liquid; DNA Mutational Analysis; Genetic Predisposition to Disease; Genetic Testing; Heterozygote; Humans; Infant; Infant, Newborn; Malaysia; Male; Mutation; Myoclonus; Phenotype; Predictive Value of Tests; Psychomotor Disorders; Psychomotor Performance; Purine-Pyrimidine Metabolism, Inborn Errors; Ribonucleosides; Seizures; Spectrometry, Mass, Electrospray Ionization; Tandem Mass Spectrometry | 2010 |