Page last updated: 2024-09-03

adenylosuccinate and aminoimidazole carboxamide

adenylosuccinate has been researched along with aminoimidazole carboxamide in 11 studies

Compound Research Comparison

Studies
(adenylosuccinate)
Trials
(adenylosuccinate)
Recent Studies (post-2010)
(adenylosuccinate)
Studies
(aminoimidazole carboxamide)
Trials
(aminoimidazole carboxamide)
Recent Studies (post-2010) (aminoimidazole carboxamide)
52151,91335830

Research

Studies (11)

TimeframeStudies, this research(%)All Research%
pre-19902 (18.18)18.7374
1990's5 (45.45)18.2507
2000's3 (27.27)29.6817
2010's1 (9.09)24.3611
2020's0 (0.00)2.80

Authors

AuthorsStudies
Jaeken, J; Van den Bergh, F; Van den Berghe, G; Vincent, MF4
Van den Berghe, G; Vincent, MF1
Holmes, EW; Patterson, D; Sabina, RL1
Domkin, VD; Lazebnik, TA; Smirnov, MN1
Marie, S; Race, V; Van den Berghe, G; Vincent, MF2
Colman, RF; Palenchar, JB1
Chen, BC; Duley, JA; Khoo, TB; McGown, IN; Ngu, LH; Pitt, J; Thong, MK; Yunus, ZM1

Other Studies

11 other study(ies) available for adenylosuccinate and aminoimidazole carboxamide

ArticleYear
Adenylosuccinase activity and succinylpurine production in fibroblasts of adenylosuccinase-deficient children.
    Advances in experimental medicine and biology, 1991, Volume: 309B

    Topics: Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Cells, Cultured; Child; Fibroblasts; Humans; Kinetics; Purine-Pyrimidine Metabolism, Inborn Errors; Purines; Ribonucleotides

1991
Radiochemical assay of adenylosuccinase: demonstration of parallel loss of activity toward both adenylosuccinate and succinylaminoimidazole carboxamide ribotide in liver of patients with the enzyme defect.
    Analytical biochemistry, 1991, Mar-02, Volume: 193, Issue:2

    Topics: Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Animals; Carbon Radioisotopes; Chromatography, Thin Layer; Cold Temperature; Enzyme Stability; Fumarates; Humans; Liver; Male; Muscles; Rats; Rats, Inbred Strains; Ribonucleotides; Saccharomyces cerevisiae; Substrate Specificity

1991
Influence of succinylpurines on the binding of adenosine to a particulate fraction of rat cerebral cortex.
    Advances in experimental medicine and biology, 1989, Volume: 253B

    Topics: Adenosine; Adenosine Monophosphate; Aminoimidazole Carboxamide; Animals; Cell Membrane; Cerebral Cortex; Imidazoles; Rats; Receptors, Purinergic; Ribonucleotides

1989
5-Amino-4-imidazolecarboxamide riboside (Z-riboside) metabolism in eukaryotic cells.
    The Journal of biological chemistry, 1985, May-25, Volume: 260, Issue:10

    Topics: Adenosine Monophosphate; Aminoimidazole Carboxamide; Animals; Cells, Cultured; Cricetinae; Cricetulus; Female; Fibroblasts; Imidazoles; Inosine Monophosphate; Ovary; Purine Nucleotides; Pyrimidine Nucleotides; Ribonucleosides; Ribonucleotides

1985
A new diagnostic technique for adenylosuccinate lyase deficiency.
    Journal of inherited metabolic disease, 1995, Volume: 18, Issue:3

    Topics: Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Chromatography, Ion Exchange; Humans; Infant; Infant, Newborn; Purine-Pyrimidine Metabolism, Inborn Errors; Ribonucleosides; Spectrophotometry, Ultraviolet

1995
Residual adenylosuccinase activities in fibroblasts of adenylosuccinase-deficient children: parallel deficiency with adenylosuccinate and succinyl-AICAR in profoundly retarded patients and non-parallel deficiency in a mildly retarded girl.
    Journal of inherited metabolic disease, 1993, Volume: 16, Issue:2

    Topics: Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Binding, Competitive; Cells, Cultured; Child; Chromatography, Ion Exchange; Female; Fibroblasts; Humans; Hydrogen-Ion Concentration; Intellectual Disability; Kinetics; Nucleotides; Potassium Chloride; Ribonucleotides; Substrate Specificity

1993
Functional studies in fibroblasts of adenylosuccinase-deficient children.
    Journal of inherited metabolic disease, 1993, Volume: 16, Issue:2

    Topics: Adenosine Monophosphate; Adenosine Triphosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Cells, Cultured; Child; Fibroblasts; Formates; Humans; Hypoxanthine; Hypoxanthines; Intellectual Disability; Ribonucleotides

1993
Clinical, biochemical and molecular genetic correlations in adenylosuccinate lyase deficiency.
    Human molecular genetics, 2000, Sep-01, Volume: 9, Issue:14

    Topics: 5' Untranslated Regions; Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Chromatography, Gel; Electrophoresis, Polyacrylamide Gel; Fibroblasts; Genotype; Homozygote; Humans; Intellectual Disability; Kinetics; Metabolism, Inborn Errors; Mutation; Mutation, Missense; Recombinant Fusion Proteins; Recombinant Proteins; Ribonucleosides; Temperature; Time Factors

2000
Adenylosuccinate lyase deficiency: from the clinics to molecular biology.
    Advances in experimental medicine and biology, 2000, Volume: 486

    Topics: Adenosine; Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Enzyme Stability; Gene Expression; Heating; Humans; Recombinant Fusion Proteins; Ribonucleotides

2000
Characterization of a mutant Bacillus subtilis adenylosuccinate lyase equivalent to a mutant enzyme found in human adenylosuccinate lyase deficiency: asparagine 276 plays an important structural role.
    Biochemistry, 2003, Feb-25, Volume: 42, Issue:7

    Topics: Adenosine Monophosphate; Adenylosuccinate Lyase; Amino Acid Sequence; Aminoimidazole Carboxamide; Arginine; Asparagine; Bacillus subtilis; Bacterial Proteins; Circular Dichroism; Enzyme Activation; Humans; Hydrogen-Ion Concentration; Kinetics; Molecular Sequence Data; Molecular Weight; Mutagenesis, Site-Directed; Point Mutation; Protein Structure, Secondary; Recombinant Proteins; Ribonucleotides; Substrate Specificity; Threonine

2003
Adenylosuccinate lyase deficiency in a Malaysian patient, with novel adenylosuccinate lyase gene mutations.
    Journal of inherited metabolic disease, 2010, Volume: 33 Suppl 3

    Topics: Adenosine; Adenosine Monophosphate; Adenylosuccinate Lyase; Aminoimidazole Carboxamide; Autistic Disorder; Biomarkers; Child Development; Chromatography, High Pressure Liquid; DNA Mutational Analysis; Genetic Predisposition to Disease; Genetic Testing; Heterozygote; Humans; Infant; Infant, Newborn; Malaysia; Male; Mutation; Myoclonus; Phenotype; Predictive Value of Tests; Psychomotor Disorders; Psychomotor Performance; Purine-Pyrimidine Metabolism, Inborn Errors; Ribonucleosides; Seizures; Spectrometry, Mass, Electrospray Ionization; Tandem Mass Spectrometry

2010